# Amiloidose cutânea, forma nodular

> Página oficial: https://raras.org/doenca/amiloidose-cutanea-forma-nodular
> Fonte: Raras.org — Banco de Dados de Doenças Raras em Português (CC BY-NC-SA 4.0)
> Última atualização: 2026-05-07

## Identificadores

- **ORPHA**: 137810 — https://www.orpha.net/en/disease/detail/137810
- **CID-10**: E85.4+

## Descrição clínica

Primary localized cutaneous nodular amyloidosis (PLCNA) is the most rare form of primary cutaneous amyloidosis, a skin disease characterized by the accumulation of amyloid deposits in the dermis, characterized clinically by yellowish waxy crusted nodules and papules on the face, lower extremities, trunk, scalp, and genitalia and histologically by the localized deposition of immunoglobulin-derived amyloid in the papillary dermis and subcutis. PLCNA can be associated with connective tissue disorders such as SjC6grenBs syndrome and CREST syndrome.

## Epidemiologia e herança


## Importante

O Raras **não diagnostica e não prescreve**. Esta página é educativa e informativa.
Pacientes devem consultar profissionais de saúde qualificados para decisões clínicas.

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**Citação sugerida**: Raras.org — Amiloidose cutânea, forma nodular. Disponível em: https://raras.org/doenca/amiloidose-cutanea-forma-nodular
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**Formato RDF/Turtle**: https://raras.org/api/rdf?orpha=137810