# Amiloidose macular

> Página oficial: https://raras.org/doenca/amiloidose-macular
> Fonte: Raras.org — Banco de Dados de Doenças Raras em Português (CC BY-NC-SA 4.0)
> Última atualização: 2026-05-07

## Identificadores

- **ORPHA**: 137814 — https://www.orpha.net/en/disease/detail/137814
- **CID-10**: E85.4+

## Descrição clínica

Macular amyloidosis (MA) is a rare chronic form of cutaneous amyloidosis, a skin disease characterized by the accumulation of amyloid deposits in the dermis, clinically characterized by pruritic hyperkeratotic gray-brown macules that give a rippled or reticulated pattern of pigmentation usually in the upper back and extensor sites of arms, forearms and legs, and histologically by the deposition of amyloid in the upper dermis and close to the basal cell layer of the epidermis. MA is commonly associated with other skin diseases, such as atopic dermatitis.

## Epidemiologia e herança


## Ensaios clínicos ativos (1)

- **NCT07360860** [NOT_YET_RECRUITING]: Microneedling Alone vs Microneedling With PRP in the Treatment of Macular Amyloidosis; a Split Face Comparative Study — https://clinicaltrials.gov/study/NCT07360860
- **NCT00353392** [COMPLETED]: Q-Switched Nd:YAG in Macular Amyloidosis — https://clinicaltrials.gov/study/NCT00353392

## Importante

O Raras **não diagnostica e não prescreve**. Esta página é educativa e informativa.
Pacientes devem consultar profissionais de saúde qualificados para decisões clínicas.

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**Citação sugerida**: Raras.org — Amiloidose macular. Disponível em: https://raras.org/doenca/amiloidose-macular
**Formato HTML**: https://raras.org/doenca/amiloidose-macular
**Formato RDF/Turtle**: https://raras.org/api/rdf?orpha=137814
