# Astrocitoma subependimário de células gigantes

> Página oficial: https://raras.org/doenca/astrocitoma-subependimario-de-celulas-gigantes
> Fonte: Raras.org — Banco de Dados de Doenças Raras em Português (CC BY-NC-SA 4.0)
> Última atualização: 2026-05-07

## Identificadores

- **ORPHA**: 251618 — https://www.orpha.net/en/disease/detail/251618
- **CID-10**: D43.2

## Descrição clínica

A benign, slowly growing tumor (WHO grade I) typically arising in the wall of the lateral ventricles and composed of large ganglioid astrocytes. It is the most common CNS neoplasm in patients with tuberous sclerosis complex and typically occurs during the first two decades of life. (WHO)

## Epidemiologia e herança


## Ensaios clínicos ativos (19)

- **NCT01165632** [COMPLETED]: Fluorine F 18 Fluorodopa-Labeled PET Scan in Planning Surgery and Radiation Therapy in Treating Patients With Newly Diagnosed High- or Low-Grade Malignant Glioma — https://clinicaltrials.gov/study/NCT01165632
- **NCT02186509** [COMPLETED]: Alisertib and Fractionated Stereotactic Radiosurgery in Treating Patients With Recurrent High Grade Gliomas — https://clinicaltrials.gov/study/NCT02186509
- **NCT02654340** [TERMINATED]: Biomarkers for Tuberous Sclerosis Complex (BioTuScCom) — https://clinicaltrials.gov/study/NCT02654340
- **NCT00823459** [COMPLETED]: Everolimus in Treating Patients With Recurrent Low-Grade Glioma — https://clinicaltrials.gov/study/NCT00823459
- **NCT02194452** [WITHDRAWN]: Efficacy of 68Ga-DOTATOC Positron Emission Tomography (PET) CT in Children and Young Adults With Brain Tumors — https://clinicaltrials.gov/study/NCT02194452
- **NCT02175745** [TERMINATED]: 18F-FDOPA PET/CT or PET/MRI in Measuring Tumors in Patients With Newly-Diagnosed or Recurrent Gliomas — https://clinicaltrials.gov/study/NCT02175745
- **NCT00326664** [COMPLETED]: AZD2171 in Treating Young Patients With Recurrent, Progressive, or Refractory Primary CNS Tumors — https://clinicaltrials.gov/study/NCT00326664
- **NCT00789828** [COMPLETED]: Efficacy and Safety of Everolimus (RAD001) in Patients of All Ages With Subependymal Giant Cell Astrocytoma Associated With Tuberous Sclerosis Complex (TSC)(EXIST-1) — https://clinicaltrials.gov/study/NCT00789828
- **NCT01119599** [COMPLETED]: RO4929097, Temozolomide, and Radiation Therapy in Treating Patients With Newly Diagnosed Malignant Glioma — https://clinicaltrials.gov/study/NCT01119599
- **NCT01462695** [COMPLETED]: Sunitinib Malate in Treating Younger Patients With Recurrent, Refractory, or Progressive Malignant Glioma or Ependymoma — https://clinicaltrials.gov/study/NCT01462695

## Importante

O Raras **não diagnostica e não prescreve**. Esta página é educativa e informativa.
Pacientes devem consultar profissionais de saúde qualificados para decisões clínicas.

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**Citação sugerida**: Raras.org — Astrocitoma subependimário de células gigantes. Disponível em: https://raras.org/doenca/astrocitoma-subependimario-de-celulas-gigantes
**Formato HTML**: https://raras.org/doenca/astrocitoma-subependimario-de-celulas-gigantes
**Formato RDF/Turtle**: https://raras.org/api/rdf?orpha=251618