# Displasia da válvula pulmonar

> Página oficial: https://raras.org/doenca/displasia-da-valvula-pulmonar
> Fonte: Raras.org — Banco de Dados de Doenças Raras em Português (CC BY-NC-SA 4.0)
> Última atualização: 2026-05-07

## Identificadores

- **ORPHA**: 99054 — https://www.orpha.net/en/disease/detail/99054
- **CID-10**: Q22.1

## Descrição clínica

A congenital cardiovascular malformation of the pulmonary valve in which there is narrowing or stricture (obstruction to flow).

## Epidemiologia e herança


## Ensaios clínicos ativos (5)

- **NCT06822400** [RECRUITING]: Investigation of Tetralogy of Fallot in Neonates — https://clinicaltrials.gov/study/NCT06822400
- **NCT06768008** [RECRUITING]: An Integrated Prenatal and Postnatal Treatment Model for the Treatment of Newborns With Critical Congenital Heart Disease — https://clinicaltrials.gov/study/NCT06768008
- **NCT05452720** [RECRUITING]: MASA Valve Early Feasibility Study — https://clinicaltrials.gov/study/NCT05452720
- **NCT03983512** [ACTIVE_NOT_RECRUITING]: PULSTA Transcatheter Pulmonary Valve Pre-Approval Study — https://clinicaltrials.gov/study/NCT03983512
- **NCT03441971** [ACTIVE_NOT_RECRUITING]: Evaluation of the GORE PV1 Device in Patients With Pulmonary Valve Dysfunction — https://clinicaltrials.gov/study/NCT03441971
- **NCT02987387** [COMPLETED]: COMPASSION XT PAS - Post-approval Study of the SAPIEN XT THV in Patients With Pulmonary Valve Dysfunction — https://clinicaltrials.gov/study/NCT02987387
- **NCT03110861** [COMPLETED]: Pulsta® Transcatheter Pulmonary Valve Korean Multicenter Study — https://clinicaltrials.gov/study/NCT03110861
- **NCT04452188** [COMPLETED]: Targeting Normoxia in Neonates With Cyanotic Congenital Heart Disease in the Intra-operative and Immediate Post-operative Period — https://clinicaltrials.gov/study/NCT04452188
- **NCT05748431** [UNKNOWN]: The Outcome of Percutaneous Balloon Pulmonary Valvuloplasty in Pediatrics — https://clinicaltrials.gov/study/NCT05748431
- **NCT02555319** [COMPLETED]: A Feasibility Study to Evaluate the Safety and Short-term Effectiveness of Transcatheter Pulmonary Valve (TPV) — https://clinicaltrials.gov/study/NCT02555319

## Importante

O Raras **não diagnostica e não prescreve**. Esta página é educativa e informativa.
Pacientes devem consultar profissionais de saúde qualificados para decisões clínicas.

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