# Hipotensão intracraniana espontânea

> Página oficial: https://raras.org/doenca/hipotensao-intracraniana-espontanea
> Fonte: Raras.org — Banco de Dados de Doenças Raras em Português (CC BY-NC-SA 4.0)
> Última atualização: 2026-05-07

## Identificadores

- **ORPHA**: 443180 — https://www.orpha.net/en/disease/detail/443180
- **CID-10**: G96.0
- **OMIM**: none — https://omim.org/entry/none

## Descrição clínica

Dor de cabeça postural intensa, piora em pé e melhora ao deitar. Pode haver náuseas, vômitos e zumbido. Causada por perda de líquido cefalorraquidiano sem trauma aparente.

## Epidemiologia e herança

- **Prevalência**: 1-9 / 100 000
- **Padrão de herança**: Not applicable

## Ensaios clínicos ativos (5)

- **NCT06374524** [RECRUITING]: Greater Occipital Nerve Block for Spontaneous Intracranial Hypotension — https://clinicaltrials.gov/study/NCT06374524
- **NCT05922514** [RECRUITING]: A Clinical Registry of Spontaneous Intracranial Hypotension — https://clinicaltrials.gov/study/NCT05922514
- **NCT06805591** [ENROLLING_BY_INVITATION]: Pathophysiology and Treatment of Cerebrospinal Hypotension Exploration Study — https://clinicaltrials.gov/study/NCT06805591
- **NCT07283536** [NOT_YET_RECRUITING]: Blind Versus Targeted Epidural Patch With Autologous Platelet-rich Plasma for Spontaneous Intracranial Hypotension — https://clinicaltrials.gov/study/NCT07283536
- **NCT07085260** [NOT_YET_RECRUITING]: ONSD Changes and Treatment Response After Epidural Blood Patch in Spontaneous Intracranial Hypotension — https://clinicaltrials.gov/study/NCT07085260
- **NCT02261792** [COMPLETED]: Spontaneous Intracranial Hypotension Treatment "SIHT" — https://clinicaltrials.gov/study/NCT02261792
- **NCT03041441** [COMPLETED]: Non-invasive Estimation of CSF Pressure Using MRI in Patients With Spontaneous Intracranial Hypotension — https://clinicaltrials.gov/study/NCT03041441
- **NCT02603549** [SUSPENDED]: Pituitary Function and Spontaneous Intracranial Hypotension — https://clinicaltrials.gov/study/NCT02603549

## Importante

O Raras **não diagnostica e não prescreve**. Esta página é educativa e informativa.
Pacientes devem consultar profissionais de saúde qualificados para decisões clínicas.

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**Citação sugerida**: Raras.org — Hipotensão intracraniana espontânea. Disponível em: https://raras.org/doenca/hipotensao-intracraniana-espontanea
**Formato HTML**: https://raras.org/doenca/hipotensao-intracraniana-espontanea
**Formato RDF/Turtle**: https://raras.org/api/rdf?orpha=443180
