# Leiomioma da órbita

> Página oficial: https://raras.org/doenca/leiomioma-da-orbita
> Fonte: Raras.org — Banco de Dados de Doenças Raras em Português (CC BY-NC-SA 4.0)
> Última atualização: 2026-05-07

## Identificadores

- **ORPHA**: 52994 — https://www.orpha.net/en/disease/detail/52994
- **CID-10**: D31.6

## Descrição clínica

Orbital leiomyoma is a rare benign smooth muscle tumor arising from the walls of orbital vessels characterized by its slow growth and well encapsulated nature. It is usually located in an extraconal position, commonly manifesting with painless proptosis. The tumor is composed of spindle cells arranged in a fibrous stroma rich in dilated sinusoidal capillaries. The nuclei of tumor cells are oval with blunted ends and there are no mitotic figures. Orbital leiomyoma when excised has excellent prognosis for vision and life. One case of orbital leiomyosarcoma that possibly represents sarcomatous change in an orbital leiomyoma following radiation treatment has been reported.

## Epidemiologia e herança

- **Prevalência**: <1 / 1 000 000
- **Casos conhecidos**: 26
- **Padrão de herança**: Unknown

## Importante

O Raras **não diagnostica e não prescreve**. Esta página é educativa e informativa.
Pacientes devem consultar profissionais de saúde qualificados para decisões clínicas.

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**Citação sugerida**: Raras.org — Leiomioma da órbita. Disponível em: https://raras.org/doenca/leiomioma-da-orbita
**Formato HTML**: https://raras.org/doenca/leiomioma-da-orbita
**Formato RDF/Turtle**: https://raras.org/api/rdf?orpha=52994