# Neurocitoma extraventricular

> Página oficial: https://raras.org/doenca/neurocitoma-extraventricular
> Fonte: Raras.org — Banco de Dados de Doenças Raras em Português (CC BY-NC-SA 4.0)
> Última atualização: 2026-05-07

## Identificadores

- **ORPHA**: 251927 — https://www.orpha.net/en/disease/detail/251927
- **CID-10**: C72.9

## Descrição clínica

Extraventricular neurocytoma (EVN), a variant of central neurocytoma, is a rare neuronal neoplasm, composed of round cells with neuronal differentiation, which is located outside of the ventricular system, usually within the spinal cord or cerebral hemispheres and that manifests with headache, nausea, vomiting, complex partial seizures or focal neurological deficits. In some cases it may exhibit atypical features consistent with aggressive clinical behavior.

## Epidemiologia e herança


## Ensaios clínicos ativos (1)

- **NCT03975829** [ACTIVE_NOT_RECRUITING]: Pediatric Long-Term Follow-up and Rollover Study — https://clinicaltrials.gov/study/NCT03975829
- **NCT02684058** [COMPLETED]: Study of Efficacy and Safety of Dabrafenib in Combination With Trametinib in Pediatric Patients With BRAF V600 Mutation Positive LGG or Relapsed or Refractory HGG Tumors — https://clinicaltrials.gov/study/NCT02684058

## Importante

O Raras **não diagnostica e não prescreve**. Esta página é educativa e informativa.
Pacientes devem consultar profissionais de saúde qualificados para decisões clínicas.

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**Citação sugerida**: Raras.org — Neurocitoma extraventricular. Disponível em: https://raras.org/doenca/neurocitoma-extraventricular
**Formato HTML**: https://raras.org/doenca/neurocitoma-extraventricular
**Formato RDF/Turtle**: https://raras.org/api/rdf?orpha=251927