# Pancreatite autoimune

> Página oficial: https://raras.org/doenca/pancreatite-autoimune
> Fonte: Raras.org — Banco de Dados de Doenças Raras em Português (CC BY-NC-SA 4.0)
> Última atualização: 2026-05-07

## Identificadores

- **ORPHA**: 103919 — https://www.orpha.net/en/disease/detail/103919

## Descrição clínica

Autoimmune pancreatitis (AIP) is a rare pancreatic disease characterized by chronic non-alcoholic pancreatitis that presents with abdominal pain, steatorrhea, obstructive jaundice and responds well to steroid therapy and is seen in two subforms: type 1 AIP which affects elderly males, involves other organs and has increased immunoglobin G4 (IgG4) levels and type 2 AIP which affects both sexes equally but presents at a younger age and has no other organ involvement or increased IgG4 levels.

## Epidemiologia e herança


## Ensaios clínicos ativos (4)

- **NCT07015580** [RECRUITING]: The Characteristics of Oral Microbiota in Chronic Pancreatitis and Autoimmune Pancreatitis — https://clinicaltrials.gov/study/NCT07015580
- **NCT06369909** [RECRUITING]: Study on AI-assisted Multimodal Diagnosis System of Autoimmune Pancreatitis — https://clinicaltrials.gov/study/NCT06369909
- **NCT07536841** [NOT_YET_RECRUITING]: Ambispective Validation of the Odesa Criteria 2026 (OC26): A Flexible Point-Based System for Diagnosis of Autoimmune Pancreatitis. — https://clinicaltrials.gov/study/NCT07536841
- **NCT06753318** [NOT_YET_RECRUITING]: Validation of Joint-AI in Diagnosing Pancreatic Solid Lesions — https://clinicaltrials.gov/study/NCT06753318
- **NCT06358001** [COMPLETED]: EchoTip AcuCore Post-Market Clinical Study — https://clinicaltrials.gov/study/NCT06358001
- **NCT04834505** [COMPLETED]: To Differentiate Focal Autoimmune Pancreatitis From Pancreatic Cancer by Endoscopic Ultrasound — https://clinicaltrials.gov/study/NCT04834505
- **NCT04397731** [COMPLETED]: Prospective Study on the Role of Eus-fnb in the Diagnosis of Autoimmune Pancreatitis — https://clinicaltrials.gov/study/NCT04397731
- **NCT06699667** [COMPLETED]: CT Findings in Surgically Treated Focal Pancreatic Disease- A Retrospective Study — https://clinicaltrials.gov/study/NCT06699667
- **NCT05476978** [COMPLETED]: Artificial Intelligence in EUS for Diagnosing Pancreatic Solid Lesions — https://clinicaltrials.gov/study/NCT05476978
- **NCT06328101** [UNKNOWN]: Autoimmune Pancreatitis, Pancreatic and Extrapancreatic cAnceR (AiPPEAR) — https://clinicaltrials.gov/study/NCT06328101

## Importante

O Raras **não diagnostica e não prescreve**. Esta página é educativa e informativa.
Pacientes devem consultar profissionais de saúde qualificados para decisões clínicas.

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**Citação sugerida**: Raras.org — Pancreatite autoimune. Disponível em: https://raras.org/doenca/pancreatite-autoimune
**Formato HTML**: https://raras.org/doenca/pancreatite-autoimune
**Formato RDF/Turtle**: https://raras.org/api/rdf?orpha=103919
