# Tumor endócrino clássico do apêndice

> Página oficial: https://raras.org/doenca/tumor-endocrino-classico-do-apendice
> Fonte: Raras.org — Banco de Dados de Doenças Raras em Português (CC BY-NC-SA 4.0)
> Última atualização: 2026-05-07

## Identificadores

- **ORPHA**: 329977 — https://www.orpha.net/en/disease/detail/329977
- **CID-10**: D37.3

## Descrição clínica

Classic endocrine tumor of the appendix is a type of endocrine tumor of the appendix, seen twice as frequently in females than in males, and usually presenting before the fifth decade of life. Classic endocrine tumor of the appendix is usually asymptomatic when located in the tip of the appendix (without obstruction), but acute appendicitis is often associated.

## Epidemiologia e herança

- **Prevalência**: Unknown
- **Padrão de herança**: Not applicable

## Ensaios clínicos ativos (2)

- **NCT00020579** [COMPLETED]: MS-275 in Treating Patients With Advanced Solid Tumors or Lymphoma — https://clinicaltrials.gov/study/NCT00020579
- **NCT00049296** [COMPLETED]: Thalidomide and Docetaxel in Treating Patients With Advanced Cancer — https://clinicaltrials.gov/study/NCT00049296

## Importante

O Raras **não diagnostica e não prescreve**. Esta página é educativa e informativa.
Pacientes devem consultar profissionais de saúde qualificados para decisões clínicas.

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**Citação sugerida**: Raras.org — Tumor endócrino clássico do apêndice. Disponível em: https://raras.org/doenca/tumor-endocrino-classico-do-apendice
**Formato HTML**: https://raras.org/doenca/tumor-endocrino-classico-do-apendice
**Formato RDF/Turtle**: https://raras.org/api/rdf?orpha=329977
