# Tumor glioneuronal papilar

> Página oficial: https://raras.org/doenca/tumor-glioneuronal-papilar
> Fonte: Raras.org — Banco de Dados de Doenças Raras em Português (CC BY-NC-SA 4.0)
> Última atualização: 2026-05-07

## Identificadores

- **ORPHA**: 251962 — https://www.orpha.net/en/disease/detail/251962
- **CID-10**: D33.0

## Descrição clínica

A WHO grade I, indolent and relatively circumscribed brain tumor. Morphologically it is characterized by the presence of astrocytes that line vascular and hyalinized pseudopapillae. In between the pseudopapillae aggregates of neurocytes, large neurons, and ganglioid cells are present.

## Epidemiologia e herança


## Ensaios clínicos ativos (1)

- **NCT03975829** [ACTIVE_NOT_RECRUITING]: Pediatric Long-Term Follow-up and Rollover Study — https://clinicaltrials.gov/study/NCT03975829
- **NCT02684058** [COMPLETED]: Study of Efficacy and Safety of Dabrafenib in Combination With Trametinib in Pediatric Patients With BRAF V600 Mutation Positive LGG or Relapsed or Refractory HGG Tumors — https://clinicaltrials.gov/study/NCT02684058

## Importante

O Raras **não diagnostica e não prescreve**. Esta página é educativa e informativa.
Pacientes devem consultar profissionais de saúde qualificados para decisões clínicas.

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**Citação sugerida**: Raras.org — Tumor glioneuronal papilar. Disponível em: https://raras.org/doenca/tumor-glioneuronal-papilar
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**Formato RDF/Turtle**: https://raras.org/api/rdf?orpha=251962