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Lúpus eritematoso hipertrófico ou verrucoso
ORPHA:90282CID-10 · L93.2CID-11 · EB51.YDOENÇA RARA

Forma rara de lúpus cutâneo com lesões hiperqueratósicas, verrucosas e espessas, frequentemente em áreas expostas ao sol. Pode mimetizar outras condições dermatológicas, exigindo biópsia para diagnóstico.

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Introdução

O que você precisa saber de cara

Mantido pelo Disease Twin100% com fonte · atualizado 16/06/2026Revisão médica pendente
Informacoes curadas por IA — podem conter imprecisoes

Visão geral

O Lúpus eritematoso hipertrófico ou verrucoso é uma forma rara de lúpus eritematoso cutâneo crônico. Ele se caracteriza por lesões na pele que são espessas, elevadas e com superfície verrucosa (semelhante a uma verruga). Esta condição afeta principalmente a pele e, diferentemente de outras formas de lúpus, geralmente não envolve órgãos internos de forma significativa.[1]

Sinais e sintomas

Os principais sinais são lesões cutâneas espessas, elevadas e com superfície áspera ou verrucosa. Essas lesões podem aparecer em áreas expostas ao sol, como rosto, couro cabeludo, braços e mãos. As lesões podem ser únicas ou múltiplas e, em alguns casos, podem coçar ou causar desconforto. A cicatrização pode deixar manchas ou cicatrizes.[1]

Causas genéticas

Até o momento, não há genes específicos identificados como causa direta do Lúpus eritematoso hipertrófico ou verrucoso. A condição não é considerada uma doença genética clássica, mas sim uma manifestação cutânea do lúpus eritematoso, que pode ter componentes genéticos e ambientais envolvidos em seu desenvolvimento.[1][2]

Diagnóstico

O diagnóstico é baseado principalmente no exame clínico das lesões de pele e na história do paciente. Uma biópsia da lesão pode ser realizada para confirmar o diagnóstico, mostrando características típicas de lúpus cutâneo crônico. Exames de sangue para anticorpos (como FAN) podem ser feitos para avaliar se há envolvimento sistêmico, mas não são específicos para esta forma. Testes genéticos não são indicados para o diagnóstico desta condição.[1][2]

Tratamento e manejo

O tratamento visa controlar as lesões de pele e prevenir novas lesões. Medidas gerais incluem proteção solar rigorosa (uso de filtro solar, roupas protetoras e evitar exposição ao sol). Medicamentos tópicos (cremes ou pomadas) com corticosteroides podem ser usados para reduzir a inflamação local. Em casos mais extensos ou resistentes, medicamentos orais como corticosteroides (ex.: prednisolona, dexametasona) podem ser considerados, sempre sob prescrição e acompanhamento médico. O tratamento deve ser individualizado e monitorado por um dermatologista ou reumatologista.[1]

Tratamentos citados na literatura

Não há dados disponíveis nos fatos fornecidos sobre tratamentos especificamente citados na literatura científica para esta condição. As informações sobre medicamentos mencionadas na seção anterior são baseadas em diretrizes gerais de manejo do lúpus cutâneo.[1]

Prognóstico e qualidade de vida

O prognóstico para o Lúpus eritematoso hipertrófico ou verrucoso é geralmente bom, pois a doença costuma ficar restrita à pele. Com tratamento adequado e proteção solar, as lesões podem melhorar ou cicatrizar. No entanto, podem ocorrer recidivas (novas lesões) e cicatrizes permanentes. A qualidade de vida pode ser afetada principalmente pelo aspecto estético das lesões e pela necessidade de cuidados contínuos com a pele. O acompanhamento médico regular é importante para monitorar a evolução e ajustar o tratamento.[1]

Fontes numeradas em Referências.

Conteúdo informativo gerado e mantido automaticamente a partir de fontes oficiais (Orphanet, HPO, OMIM, SUS). Não substitui avaliação médica.

💬
EM LINGUAGEM SIMPLES

O **lúpus eritematoso hipertrófico ou verrucoso** é uma condição rara catalogada sob o código internacional ORPHA:90282 e CID-10 L93.2. Os sintomas detalhados e as causas genéticas precisas ainda não se encontram descritos nos catálogos médicos de referência. No Brasil, o Ministério da Saúde disponibiliza o medicamento **Azatioprina** por meio do CEAF no SUS. O protocolo oficial existente aborda o Lúpus Eritematoso Sistêmico de maneira ampla, sem detalhar de forma isolada esta apresentação específica.

📋
Informacoes curadas por IA — podem conter imprecisoes

Forma rara de lúpus cutâneo com lesões hiperqueratósicas, verrucosas e espessas, frequentemente em áreas expostas ao sol. Pode mimetizar outras condições dermatológicas, exigindo biópsia para diagnóstico.

Medicamentos
1 com registro
Azatioprina

Tem tratamento?

✓ 1 medicamento específico desta doença (registro ANVISA, FDA ou SUS/CEAF)
Ver detalhes, fases e interações →
AZATIOPRINA
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SUS: Cobertura parcialScore: 50%
1 medicamento CEAFCID-10: L93.2
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Sinais e sintomas

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Anos de pesquisa1
Últimos 10 anos200publicações
Pico2026197 papers
Linha do tempo
2025Hoje · 2026
Publicações por ano (últimos 10 anos)

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Genética e causas

O que está alterado no DNA e como passa nas famílias

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Nenhum gene associado encontrado

Os dados genéticos desta condição ainda estão sendo catalogados.

Diagnóstico

Os sinais que médicos procuram e os exames que confirmam

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Tratamento e manejo

Remédios, cuidados de apoio e o que precisa acompanhar

Carregando informações de tratamento...

Onde tratar no SUS

Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

🇧🇷 Atendimento SUS — Lúpus eritematoso hipertrófico ou verrucoso

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Pesquisa ativa

Ensaios clínicos abertos e novidades científicas recentes

Pesquisa e ensaios clínicos

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Publicações mais relevantes

Timeline de publicações
0 papers (10 anos)
#1

Optimizing Strength and Hypertrophy: The Combined Effect of Intensity and Velocity Loss Thresholds in Bench Press Training.

Medicine and science in sports and exercise2026 Mar 24

**Importante:** O artigo científico fornecido é sobre otimização do treino de força e hipertrofia no supino, e **não** sobre lúpus eritematoso hipertrófico ou verrucoso. Focando no conteúdo do artigo sobre exercícios, para pacientes e médicos: Este artigo científico revela que, para otimizar os ganhos de força e hipertrofia no treino de supino, a utilização de altas intensidades (70-85% da 1RM) é consistentemente a mais eficaz. Contudo, o grau de esforço dentro de cada série, medido pela perda de velocidade (VL), modula os resultados: uma perda de velocidade maior (VL de 50%) é ideal para maximizar o crescimento muscular e a resistência, enquanto uma perda moderada (VL de 25%) produz os melhores ganhos de força máxima.

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#2

Association of CVAI, age, and clinic systolic blood pressure with left ventricular hypertrophy in postmenopausal women with primary hypertension: A single-centre retrospective case-control study.

Science progress2026

Este estudo investigou os fatores de risco para hipertrofia ventricular esquerda (HVE) em mulheres pós-menopáusicas com hipertensão primária. Descobriu-se que o Índice de Adiposidade Visceral Chinês (CVAI), a idade e a pressão arterial sistólica clínica são fatores de risco independentes significativos para o desenvolvimento de HVE. Assim, o monitoramento e manejo desses fatores são cruciais para a prevenção e tratamento da HVE neste grupo de pacientes, ajudando a reduzir o risco de complicações cardíacas.

🇧🇷 traduzido
#3

Genetic and functional characterization of AMH Signaling in Zebrafish - Evidence for Roles of Amh-Bmpr2a-Bmpr1bb Pathway in Controlling Gonadal Homeostasis.

PLoS genetics2026 Mar 23

Este estudo, realizado em peixes-zebra, identificou uma nova via de sinalização para o hormônio Anti-Mülleriano (AMH) – Amh-Bmpr2a-Bmpr1bb – crucial para o controle da homeostase gonadal, ou seja, para manter o tamanho e a função normais das gônadas. Disrupções nesta via levam a uma hipertrofia gonadal (aumento das gônadas), um efeito que depende da sinalização das gonadotropinas (FSH e LH). Embora em um modelo animal, esta pesquisa aprofunda a compreensão fundamental de como o AMH interage com outras vias hormonais para regular a proliferação e diferenciação de células germinativas, oferecendo insights sobre potenciais mecanismos de distúrbios reprodutivos em humanos e possíveis alvos terapêuticos futuros.

🇧🇷 traduzido
#4

Panx1 deficiency exacerbates GAN diet-induced obesity by destabilizing β-catenin via GSK3β.

iScience2026 Apr 17

A deficiência da proteína Panx1 agrava significativamente a obesidade induzida por dietas específicas, levando a um acúmulo de gordura mais severo devido ao crescimento anormal das células adiposas. Essa proteína é fundamental para estabilizar uma via molecular chave (β-catenina) que regula o desenvolvimento saudável do tecido adiposo, e sua perda promove a expansão do tecido gorduroso de forma hipertrófica. Entender essa interação de Panx1 abre caminho para novas estratégias de tratamento focadas em prevenir ou reverter a obesidade e suas complicações metabólicas.

🇧🇷 traduzido
#5

Artificial Intelligence-Enabled Electrocardiography in Practice: A State-of-the-Art Review.

Korean circulation journal2026 Mar

A eletrocardiografia com inteligência artificial (IA-ECG) está rapidamente se tornando uma ferramenta clínica valiosa para pacientes e médicos. Ela auxilia no diagnóstico preciso de arritmias, doenças cardíacas estruturais como a cardiomiopatia hipertrófica e fibrilação atrial, podendo levar a intervenções mais precoces e, em alguns casos, a uma redução da mortalidade. Além de diagnósticos, a IA-ECG também permite o monitoramento de riscos e o rastreamento de doenças sistêmicas, apesar dos desafios remanescentes de sua integração na rotina médica.

🇧🇷 traduzido

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Optimizing Strength and Hypertrophy: The Combined Effect of Intensity and Velocity Loss Thresholds in Bench Press Training.

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Association of CVAI, age, and clinic systolic blood pressure with left ventricular hypertrophy in postmenopausal women with primary hypertension: A single-centre retrospective case-control study.

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Genetic and functional characterization of AMH Signaling in Zebrafish - Evidence for Roles of Amh-Bmpr2a-Bmpr1bb Pathway in Controlling Gonadal Homeostasis.

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Panx1 deficiency exacerbates GAN diet-induced obesity by destabilizing β-catenin via GSK3β.

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Chondrocyte proliferation without inflammation underlies botulinum toxin-induced mandibular enthesis bone hypertrophy in rats.

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Velocity Loss During Resistance Training: Implications for Concurrent Training Adaptations.

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Midventricular Obstruction in Hypertrophic Cardiomyopathy: Clinical Outcomes in a Multicenter Cohort.

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Cardiology in review
2026

Assessing Health in Aging Male and Female Mice: Does Cardiac Function Dictate Frailty or Physical Resilience?

The journals of gerontology. Series A, Biological sciences and medical sciences
2026

Genetics in Hypertrophic Cardiomyopathy: An Evolving Clinical Landscape.

Cardiac failure review
2026

Heart Failure in Hypertrophic Cardiomyopathy.

Cardiac failure review
2026

Seeing beyond the aesthetic problem of labia minora hypertrophy: a case report.

International journal of surgery case reports
2026

Neuroendocrine-vascular interaction is associated with thalamocortical disorganization and cognitive decline in perimenopausal hypertension.

Frontiers in medicine
2026

Retrograde improvisations and their iatrogenic complications: a case report of an antegrade femoral nail used as a retrograde construct.

Journal of surgical case reports
2026

Spatially resolved single-cell-based histocytomorphometry for growth plate analysis across multiple species.

Journal of orthopaedic translation
2026

VEGF-neutralized platelet-rich plasma with adipose-derived stromal vascular fraction enhanced osteochondral repair in a point-of-care goat model.

Journal of orthopaedic translation
2026

Obstructive Sleep Apnea Is Associated with Increased Myocardial Scar Burden in Patients with Obstructive Hypertrophic Cardiomyopathy.

CJC open
2026

Early Diastolic Release Flow Is a Sensitive Early Marker for Left Ventricular Apical Aneurysm in Patients with Hypertrophic Cardiomyopathy.

CJC open
2026

Galgeun-tang modulates lipid, glucose, and energy metabolism in diet-induced obesity across cellular, nematode, and murine models.

Frontiers in pharmacology
2026

Implantable Cardioverter-Defibrillator (ICD) Lead-Induced Septal and Left Ventricular Perforation in Hypertrophic Cardiomyopathy: A Case Report.

Cureus
2026

Prognostic value of left ventricular phenotypes by cardiac magnetic resonance in elderly and non-elderly patients.

Journal of geriatric cardiology : JGC
2026

Cardiovascular responses during blood flow-restricted resistance exercise: a systematic review with meta-analysis.

BMJ open sport & exercise medicine
2026

Identification of PANoptosis-Related Biomarkers in Hypertrophic Cardiomyopathy: Insights from Multi-Omics Analysis.

Journal of inflammation research
2026

Increased paraspinal muscles fatty infiltration and ligamentum flavum hypertrophy as independent predictors of posterior revision surgery following lateral lumbar interbody fusion with lateral plate fixation: a retrospective study.

Asian spine journal
2026

Basal-bolus regimen versus twice-daily premixed insulin in the treatment of childhood type 1 diabetes mellitus in Mosul City: A comparison study.

Problemy endokrinologii
2026

Packed for Ossification: High-Density Bioprinting of hPDC Spheroids in HAMA Toward Endochondral Ossification.

Advanced healthcare materials
2026

[Pubertal characteristics in patients with NR5A1-related 46, XY disorders of sex development].

Zhonghua er ke za zhi = Chinese journal of pediatrics
2026

Impact of angiopoietin-like 4 (ANGPTL4) protein and O-linked β-N-acetylglucosamine(O-GlcNAc) in diabetic nephropathy.

Diabetes research and clinical practice
2026

Relationships between lung ultrasound, chest CT, and echocardiographic findings in children with bronchopulmonary dysplasia: A multimodal imaging study.

Respiratory medicine
2026

Developmental expression patterns of the FXR-IGF axis during early skeletal muscle growth in ducks.

Poultry science
2025

Predictive factors of poor nutritional status in children and young adults on chronic hemodialysis: A single center experience.

La Tunisie medicale
2026

Development and Validation of a Deep Learning System for Echocardiographic Assessment of 16-Segment LV Wall Thickness.

Ultrasound in medicine & biology
2026

Resolution of Microvascular Ischemia Following Alcohol Septal Ablation in Hypertrophic Cardiomyopathy: Evidence from Rubidium-82 PET.

Journal of nuclear cardiology : official publication of the American Society of Nuclear Cardiology
2026

STIM1 deletion in regulatory T cells restores redox balance and protects against hypertension-induced cardiovascular complications.

Translational research : the journal of laboratory and clinical medicine
2026

ACSL6 alleviates myocardial hypertrophy by ameliorating cardiac lipid synthesis and mitochondrial function.

Life sciences
2026

Cardiac morphologic changes induced by a 10-week water treadmill training for show jumping horses: A preliminary evaluation.

Veterinary journal (London, England : 1997)
2026

Effects of proANP31-67 in a preclinical model of uninephrectomy and cardiac ischemia/reperfusion injury: cardiac remodeling and tissue biochemical profiling.

American journal of physiology. Cell physiology
2026

Efficacy of low-dose colchicine on left ventricular hypertrophy in patients with coronary artery disease: A randomized controlled trial.

British journal of clinical pharmacology
2026

LMNA-p.Arg78Trp and MYH6-p.Val893Met Mutations Associated with Left Ventricular Noncompaction.

Combinatorial chemistry & high throughput screening
2026

Understanding Pathophysiological Complexity of Feline Hypertrophic Cardiomyopathy Using SWATH-MS Plasma Proteomics.

Animals : an open access journal from MDPI
2026

Morphological and Molecular Characteristics of Choroid Plexus Epithelium in Aged Brains.

International journal of molecular sciences
2026

Nppa and Nppb Deficiency Drives Ventricular Hypertrophy and Subendocardial Gene Deregulation in the Mouse Heart.

International journal of molecular sciences
2026

PCSK9 Inhibitor Alirocumab Improves Diabetic Cardiomyopathy Through the ERK/p38 MAPK Signaling Pathway.

International journal of molecular sciences
2026

Molecular Mechanisms of Intestinal Adaptation in Short Bowel Syndrome: A Comprehensive Review.

International journal of molecular sciences
2026

An Open-Source Analysis of Cardiomyopathy Using Machine Learning and Electrocardiograms.

Diagnostics (Basel, Switzerland)
2026

IgG4-Related Disease Manifested as Hypertrophic Pachymeningitis: A Case Report and Literature Review.

Diagnostics (Basel, Switzerland)
2026

Diagnostic Performance of Relative Apical Sparing Across Cardiac Diseases: A Multimodality Systematic Review and Meta-Analysis.

Journal of clinical medicine
2026

Peripheral Hypertrophic Subepithelial Corneal Degeneration.

Journal of clinical medicine
2026

Identification of a putative progenitor-like chondrocyte subpopulation in osteoarthritic human cartilage.

Stem cell research & therapy
2026

Sudden Death of a 17-Month-Old Chimpanzee (Pan troglodytes) due to a Congenital Undiagnosed Ventricular Septal Defect.

Journal of medical primatology
2026

The CD163:CD68 Ratio Reflects Splenic Macrophage Remodelling in Murine Chronic Schistosomiasis.

Parasite immunology
2026

Predictors of Obstructive Coronary Artery Disease in Positive Electrocardiogram, Negative Echocardiogram Stress Tests: A Single-Centre Retrospective Analysis.

Heart, lung & circulation
2026

Left Ventricular Mass Index as an independent predictor of major adverse cardiovascular and cerebrovascular events in patients with SLE.

Lupus science & medicine
2026

Anaesthethic management on a pediatric patient with Sengers syndrome. Case report.

Revista espanola de anestesiologia y reanimacion
2026

Seeing beneath the surface: Are current risk scores enough in hypertrophic cardiomyopathy?

Revista portuguesa de cardiologia : orgao oficial da Sociedade Portuguesa de Cardiologia = Portuguese journal of cardiology : an official journal of the Portuguese Society of Cardiology
2026

Effects of Ankylosing Spondylitis on Total Knee Arthroplasty Outcomes and Post-operative Manipulation Under Anesthesia Rates.

The Journal of arthroplasty
2026

Single-photon emission computed tomography functional liver imaging to facilitate reirradiation for liver malignancies: A phase I trial.

JHEP reports : innovation in hepatology
2026

"Congenital Muscular Pseudohypertrophy of the Upper Limb: Morphology, Anatomy and Surgical Guidelines of An Unique Entity".

Plastic and reconstructive surgery
2026

Dysphagia rehabilitation methods using kinesiology taping: A systematic review.

Medicine
2026

Comprehensive Assessment of Left Ventricular Mass, Its Derived Indices, and Relative Wall Thickness in Ischemic Heart Disease.

Cardiology
2026

Development and in vivo evaluation of a self-polymerizable tranilast-loaded silicone gel for scar modulation.

Journal of biomaterials applications
2026

E3 Ubiquitin Ligase UBR5 Aggravates Cardiac Hypertrophy Via Inhibiting Nrf2/HO-1 Pathway.

Cardiovascular drugs and therapy
2026

KLHL24-Associated Hypertrophic Cardiomyopathy: When Genotype Outpaces Phenotype.

JACC. Case reports
2026

Hypertrophic Lichen Planus.

Mayo Clinic proceedings
2026

m6A in adipose tissue inflammation: A novel regulator of obesity and metabolic diseases (Review).

International journal of molecular medicine
2026

Fasciola hepatica-Derived Proteins Shield the Heart From Type 2 Myocardial Infarction in Rats by Modulating Oxidative Stress and Inflammatory Imbalance: Insights Relevant to the Hygiene Hypothesis.

Oxidative medicine and cellular longevity
2026

Effect of Hypertension Duration on the Associations Between Intensive Blood Pressure Control and Cardiac, Vascular, and Kidney Organ Damage.

Journal of the American Heart Association
2026

Growth performance and muscle histological characteristics of IPB-D3 chickens reared under intensive and free-range systems.

Veterinary world
2026

The exosomal miR-26b-3p derived from Crohn's disease-associated mesenteric adipose tissue induces M1 macrophage polarization and exacerbates ileocolonic anastomosis inflammation via the p38-MAPK signaling pathway.

Frontiers in immunology
2026

Mitochondrial quality control modulating chondrocyte behavior and fate in knee osteoarthritis: mechanistic insights and therapeutic prospects.

Frontiers in immunology
2026

Characteristics of Ear, Nose, and Throat Comorbidities among Children with Allergic Rhinitis.

International archives of otorhinolaryngology
2026

Description of the novel variant c.784delG;p. (Ala262Profs*68) at BSND gene and its association with Bartter Syndrome Type Iva.

Biomedical reports
2026

Holistic Value Assessment of Tirbanibulin for Actinic Keratosis: European Multi-Criteria Decision Analysis.

Dermatology and therapy
2026

Balloon Dilation of the Eustachian Tube in Pediatric Patients.

Otolaryngologic clinics of North America
2026

[Guidelines for the diagnosis and treatment of obstructive sleep apnea in adults (2025)].

Zhonghua jie he he hu xi za zhi = Zhonghua jiehe he huxi zazhi = Chinese journal of tuberculosis and respiratory diseases
2026

Evaluation of ventricular dyssynchrony in fetuses of diabetic mothers measured by the tissue Doppler indices: a case-control study.

The journal of maternal-fetal & neonatal medicine : the official journal of the European Association of Perinatal Medicine, the Federation of Asia and Oceania Perinatal Societies, the International Society of Perinatal Obstetricians
2026

Development of a service line for laser resurfacing of hypertrophic burn scars: Focusing on peri-operative safety outcomes.

Burns : journal of the International Society for Burn Injuries
2026

Exploration of the rare 5/6/7-fused diterpenoids with anti-hypertrophy activity from Strophioblachia glandulosa via bioactivity-guided strategy.

Phytochemistry
2026

Comprehensive evaluation of hypertrophic cardiomyopathy: European Journal of Heart Failure expert consensus document.

European journal of heart failure
2026

PINK1/Parkin-mediated mitophagy is involved in calcium-sensing receptor-induced cardiac damage and apoptosis in spontaneously hypertensive rats.

Journal of hypertension
2026

Associations of calciprotein particle maturation time with echocardiographic measures in the CRIC Study.

American journal of nephrology
2026

Seal and sea lion brains have evolved to support volitional control of vocal behavior and learning.

Science (New York, N.Y.)
2026

Characterization of participants with a disproportionate degree of hypertension-mediated organ damage: the Maastricht study.

Journal of hypertension
2026

Early administration of renin-angiotensin system inhibitors improves survival and cardiac remodeling in heart failure with preserved ejection fraction.

PloS one
2026

Co-existence of Ménétrier's Disease and Collagenous Colitis: A Diagnostic and Therapeutic Challenge.

Journal of general internal medicine
2026

Performance and Safety of the Extravascular Implantable Cardioverter-Defibrillator in Patients With Hypertrophic Cardiomyopathy.

JACC. Clinical electrophysiology
2026

Diagnosis and Treatment Guided by 3D Imaging and Modeling: A W-shaped Interventricular Septal Phenotype in Hypertrophic Obstructive Cardiomyopathy.

Radiology. Cardiothoracic imaging
2026

Massive Device-Related Thrombus After Left Atrial Appendage Closure in Kidney Transplant Recipient With Hypertrophic Cardiomyopathy.

JACC. Case reports
2026

Hypertrophic Pachymeningitis Presenting with Cerebral Venous Thrombosis.

Neurology India
2026

Adhesion-Related Macrophages Regulate Metabolic Homeostasis Through CAV-1 Dependency.

Advanced science (Weinheim, Baden-Wurttemberg, Germany)
2026

Self-Strengthened PDT Coupling ROS Precise Regulation High-Penetration Microneedle for Adaptive Treatment of Pathological Scar.

ACS applied materials & interfaces

Associações

Organizações que acompanham esta doença — pra ter apoio e orientação

Ainda não temos associações cadastradas para Lúpus eritematoso hipertrófico ou verrucoso.

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Conselhos e sociedades

Doenças relacionadas

Doenças com sintomas parecidos — ajudam quem ainda está buscando diagnóstico

Ainda não achamos doenças com sintomas parecidos o suficiente.

Perguntas frequentes

O que as famílias mais perguntam sobre esta doença — cada resposta com a fonte de onde saiu

Protocolo oficial relacionado (Ministério da Saúde)PCDT: Lúpus Eritematoso Sistêmico

Existe um documento oficial para "Lúpus Eritematoso Sistêmico". Ele pode não cobrir esta forma específica da doença — confira no texto do protocolo antes de contar com ele.

Respostas geradas por IA a partir das fontes citadas

É uma doença rara catalogada no sistema Orphanet pelo código ORPHA:90282. Ela recebe a classificação diagnóstica CID-10 L93.2 nos registros de saúde.

Referências

Fontes citadas no texto, publicações do grafo e bases de dados usadas neste verbete

3 fontes citadas no texto · 8 publicações do grafo RarasNet (PubMed) · 3 bases de dados. Títulos, periódicos e PMIDs vêm direto da fonte, sem intermediação de IA.

  1. MONDO
    purl.obolibrary.org
  2. GARD:19132
    GARD (NIH)
  3. Q7922594
    Wikidata

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Citar este verbete

Raras. (2026). Lúpus eritematoso hipertrófico ou verrucoso. Em Raras — Enciclopédia de Doenças Raras do Brasil. https://raras.org/doenca/lupus-eritematoso-hipertrofico-ou-verrucoso

Formato APA. Conteúdo sob CC BY 4.0 — reuso livre com atribuição.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Compêndio · Raras BR

Lúpus eritematoso hipertrófico ou verrucoso

ORPHA:90282 · MONDO:0019559
🇧🇷 Brasil SUS
CEAF
1BAzatioprina
Geral
CID-10
L93.2 · Outras formas de lúpus eritematoso localizado
CID-11
MedGen
UMLS
C1274838
Repurposing
3 candidatos
dexamethasone — glucocorticoid receptor agonist
dexamethasone-acetate
prednisolone-sodium-phosphate
Wikidata

📋 Origem dos dados

Esta página agrega dados de fontes públicas e oficiais. Dados sobre cobertura no SUS (PCDT, CEAF) são verificados ativamente por agente proativo (ver badge no infobox). Demais dados têm atribuição de fonte + data da última sincronização — clique para abrir o original.

Doença rara (ontologia)
fonte: Orphanet
Identificador unificado
fonte: MONDO
Dado público estruturado
fonte: Wikidata
Rara