OBSOLETO. Qualquer uma das formas de neoplasia cardíaca que apresentam incidência rara.
Introdução
O que você precisa saber de cara
Visão geral
O termo tumor cardíaco refere-se a qualquer uma das formas de neoplasia cardíaca que apresentam incidência rara, correspondendo historicamente a uma classificação com termo considerado obsoleto na literatura especializada. Trata-se da denominação em inglês 'Rare cardiac tumor' mapeada formalmente pelo identificador MONDO:0015673.[1]
Conteúdo informativo gerado e mantido automaticamente a partir de fontes oficiais (Orphanet, HPO, OMIM, SUS). Não substitui avaliação médica.
O termo tumor cardíaco reúne diferentes tipos de lesões e neoplasias raras que surgem nas estruturas do coração. As manifestações e os impactos no organismo variam muito conforme o tipo histológico e a localização exata da lesão no órgão. Em muitos casos descritos pela literatura médica, a abordagem envolve avaliação detalhada e procedimentos de cirurgia cardíaca. Esta condição não consta na lista oficial de Protocolos Clínicos e Diretrizes Terapêuticas (PCDT) de doenças raras do Ministério da Saúde, devendo o paciente buscar acompanhamento na rede especializada.
OBSOLETO. Qualquer uma das formas de neoplasia cardíaca que apresentam incidência rara.
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Entender a doença
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Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Linha do tempo da pesquisa
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Genética e causas
O que está alterado no DNA e como passa nas famílias
Nenhum gene associado encontrado
Os dados genéticos desta condição ainda estão sendo catalogados.
Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
Remédios, cuidados de apoio e o que precisa acompanhar
Onde tratar no SUS
Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)
🇧🇷 Atendimento SUS — Tumor cardíaco
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Pesquisa ativa
Ensaios clínicos abertos e novidades científicas recentes
Pesquisa e ensaios clínicos
Nenhum ensaio clínico registrado para esta condição.
Publicações mais relevantes
Cardiac Myxoma in the right ventricle.
Right ventricular myxomas is rare cardiac tumor. We described a 35-year-old man who had a right ventricular myxomas. The mass was completely removed under cardiopulmonary bypass.This case illustrates the importance of multimodality imaging when establishing the primary diagnosis and determining the course of treatment.
Cardiac Fibroblastoma Presenting as NSTEMI.
Myocardial infarction with nonobstructive coronary arteries (MINOCA) represents ∼8% of acute myocardial infarctions, with causes including myocarditis, coronary spasm, and embolization from cardiac tumors. A 59-year-old woman presented with exertional chest pain and elevated troponins, consistent with non-ST-segment elevation myocardial infarction. Coronary angiography showed normal coronaries. Cardiac magnetic resonance imaging revealed a small ischemic infarct, prompting review of prior computed tomography, which identified a small aortic valve mass. Transesophageal echocardiography confirmed a mobile lesion. Surgical excision revealed a benign fibroblastoma, an extremely rare cardiac tumor. This case highlights the importance of thorough imaging review in MINOCA and expands the spectrum of cardiac tumors implicated in coronary embolization. This is to our knowledge one of the first reports of a cardiac fibroblastoma.
Cardiac Angiosarcoma as an Unexpected Cause of Palpitations: Case Report, Differential Diagnosis, and Current Therapeutic Approach to Cardiac Tumors.
We present a case of an 83-year-old woman who presented with palpitations, asthenia, and exertional dyspnea. The electrocardiogram showed atrial flutter, and echocardiography (UCG) revealed a large mass occupying the right atrial chamber. Contrast-enhanced computed tomography (CECT) and cardiac magnetic resonance (CMR) confirmed its origin and extension into the superior vena cava (SVC). A multidisciplinary medical committee considered palliative surgery as the best therapeutic option for the patient due to the impossibility of a complete surgical resection of the tumor. Primary malignant neoplasms of the heart are extremely rare. Their clinical behavior is aggressive, with high morbidity and mortality and frequent surgical limitations due to location and extent at diagnosis. Imaging techniques are essential for diagnosis such as UCG for initial detection, CMR for tissue characterization, and CT or positron emission tomography-computed tomography (PET-CT) for staging and therapeutic planning. Definitive diagnosis requires histologic study, although it is not free of significant complications. This is a case report of a rare cardiac tumor followed by review of literature on its diagnosis and therapeutic approach.
Left Atrial Epithelioid Angiosarcoma Presenting As Recurrent Stroke: A Case Report.
A 74-year-old man presented with recurrent cerebellar infarction and progressive anemia. The workup revealed a small jejunal tumor and a mobile mass in the left atrium. Urgent minimally invasive cardiac surgery was performed, and histopathology confirmed epithelioid angiosarcoma. Subsequent small bowel resection revealed a similar tumor. Despite chemotherapy and radiotherapy, bone metastases progressed, and the patient succumbed to the disease eight months postoperatively. The cardiac tumor was smaller than typically reported, suggesting early detection prompted by embolic events. Nevertheless, the clinical course was aggressive, highlighting the high malignancy of epithelioid angiosarcoma and the limited effectiveness of current therapies. Accumulation of further clinical experience is essential to improve outcomes in this rare cardiac tumor.
Papillary Fibroelastoma as a Cause of Cardioembolic Stroke in Young Adults: A Case Report.
Although ischaemic strokes are common worldwide, strokes in young adults are rare. Cardioembolism is a frequent cause of ischaemic strokes, often arising from atrial fibrillation or, less commonly, underlying structural heart defects. Primary cardiac tumours are commonly associated with embolic strokes. Although papillary fibroelastoma (PFE) is a rare cardiac tumor, it is one of the most common primary cardiac tumours that causes embolic strokes. We report the case of a 24-year-old woman who presented with sudden-onset right arm weakness. Subsequent investigations, including echocardiography, revealed a papillary mass consistent with PFE.
Publicações recentes
Cardiac Myxoma in the right ventricle.
Cardiac Fibroblastoma Presenting as NSTEMI.
🥉 Relato de casoCardiac Angiosarcoma as an Unexpected Cause of Palpitations: Case Report, Differential Diagnosis, and Current Therapeutic Approach to Cardiac Tumors.
Left Atrial Epithelioid Angiosarcoma Presenting As Recurrent Stroke: A Case Report.
Papillary Fibroelastoma as a Cause of Cardioembolic Stroke in Young Adults: A Case Report.
🥉 Relato de caso📚 EuropePMC28 artigos no totalmostrando 49
Cardiac Myxoma in the right ventricle.
The international journal of cardiovascular imagingCardiac Fibroblastoma Presenting as NSTEMI.
JACC. Case reportsCardiac Angiosarcoma as an Unexpected Cause of Palpitations: Case Report, Differential Diagnosis, and Current Therapeutic Approach to Cardiac Tumors.
CureusLeft Atrial Epithelioid Angiosarcoma Presenting As Recurrent Stroke: A Case Report.
CureusPapillary Fibroelastoma as a Cause of Cardioembolic Stroke in Young Adults: A Case Report.
CureusCardiac Hemangiomas: A Five-Year Systematic Review of Diagnosis, Treatment, and Outcomes.
CancersCardiac benign metastatic leiomyoma- a comprehensive review.
Cardio-oncology (London, England)Pulmonary Valve Fibroelastoma, Still a Very Rare Cardiac Tumor: Case Report and Literature Review.
Diagnostics (Basel, Switzerland)Endobronchial ultrasound-guided cryobiopsy of a rare epicardial tumour.
PulmonologyCardiac papillary fibroelastoma involving the mitral valve: A case report.
MedicineClinical and laboratory manifestations, ECG findings, and outcomes of right atrial myxoma: a systematic review of cases reported worldwide.
The Egyptian heart journal : (EHJ) : official bulletin of the Egyptian Society of CardiologyHamartoma of mature cardiac myocytes presenting as a polypoid epicardial tumor in the interatrial groove and with gene fusions by copy number anomalies of chromosome 7.
Cardiovascular pathology : the official journal of the Society for Cardiovascular PathologyRare Cardiac Tumor: Do We Know All About Cardiac Myxofibrosarcoma?
CureusPapillary fibroelastoma complicated by Streptococcus sanguinis bacteremia: a rare case of cardiac tumor with embolic events.
Archive of clinical casesPericardial hemangioma: An extremely rare cardiac tumor.
Kardiologia polskaLethal complication of a rare cardiac tumor.
Forensic science, medicine, and pathologyCardiac osteosarcoma: a case report and literature review.
Frontiers in cardiovascular medicineOperative management and outcomes in patients with myxomas: A single-center experience.
Frontiers in surgeryGiant left atrial myxoma causing acute ischemic stroke.
Future cardiologyClinical Characteristics and Surgical Outcomes of Right Heart Myxoma and Its Comparison with Left Heart Myxoma: A Single-Center Retrospective Study.
Anatolian journal of cardiologyCase report: The diagnostic challenge of primary cardiac intimal sarcoma.
Frontiers in cardiovascular medicineDiagnosis of rapidly progressed primary cardiac lymphoma in liver transplant recipient: A case report.
Frontiers in oncologyA Giant Cardiac Hemangioma Encroaching on the Right Coronary Artery.
The Annals of thoracic surgeryCase Report: Unusual Clinical Presentation of a Rare Cardiac Inflammatory Myofibroblastic Tumor in Children: The Differential Diagnosis With Pediatric Emergencies.
Frontiers in pediatricsSurgical Management of Primary Pulmonary Artery Sarcoma.
Seminars in thoracic and cardiovascular surgeryCalcified Amorphous Tumor of Left Ventricle: A Rare Cardiac Tumor.
CureusExcision of a rare cardiac tumor aided by endocardial electroanatomical mapping.
Journal of cardiac surgeryA rare cardiac tumor presenting with myxoma: Primary cardiac hemangioendothelioma.
Turk gogus kalp damar cerrahisi dergisiCancer Patient With Unusual Dyspnea in the COVID-19 Era: Challenging Management of a Rare Cardiac Tumor.
JACC. Case reportsSurgical excision of a rare cardiac tumor: Cardiac hibernoma.
Journal of cardiac surgeryHeartburn as the first symptom of rare cardiac tumor localization: is multimodality imaging a helpful approach?
Kardiologia polskaLeft Atrial Angiosarcoma: A Rare Cardiac Tumor at an Uncommon Site.
Journal of cardiovascular echographyFrom pathogenesis to treatment, a systemic review of cardiac lipoma.
Journal of cardiothoracic surgeryIntracardiac Teratoma in a Child: A Rare Site of a Common Tumor.
Journal of pediatric hematology/oncologyCase Report: Can we differentiate mesothelioma from inflammatory pericardial constriction preoperatively?
F1000ResearchListen to the Heart - Rare Cardiac Tumor in an Adolescent.
Klinische PadiatriePrimary cardiac angiosarcoma with right atrial wall rupture: A case report.
MedicineUnusual Presentation of Rare Cardiac Tumor: The Role of F-18-Fluorodeoxyglucose Positron Emission Tomography/Computed Tomography.
Indian journal of nuclear medicine : IJNM : the official journal of the Society of Nuclear Medicine, IndiaPapillary Fibroelastoma as a Cause of Cardiogenic Embolic Stroke in a β-Thalassemia Patient: Case Report and Literature Review.
Case reports in cardiologyA rare cardiac tumor: Bronchogenic cyst of interatrial septum.
Echocardiography (Mount Kisco, N.Y.)Multiple Fibroelastoma: Search and You Will Find.
The Journal of heart valve diseaseLeft atrial myxoma masquerading as viral flu.
Proceedings (Baylor University. Medical Center)Primary Cardiac T-Cell Lymphoma Localized in the Mitral Valve.
The Annals of thoracic surgerySuccessful Management of Primary Cardiac Lymphoma with Minimal Debulking Surgery Combined with Adjuvant Chemotherapy.
The heart surgery forumAcute Mesenteric Ischemia Caused by Rare Cardiac Tumor Embolus.
ACG case reports journalGiant Cardiac Cavernous Hemangioma.
The Annals of thoracic surgeryRare cause of a common symptom: primary cardiac lymphoma.
The American journal of emergency medicineLarge primary right ventricular teratoma in an adult.
The Annals of thoracic surgery[Unusual consequences of foam sclerotherapy].
Journal des maladies vasculairesAssociações
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Doenças relacionadas
Doenças com sintomas parecidos — ajudam quem ainda está buscando diagnóstico
Ainda não achamos doenças com sintomas parecidos o suficiente.
Perguntas frequentes
O que as famílias mais perguntam sobre esta doença — cada resposta com a fonte de onde saiu
É a denominação utilizada para qualquer forma de neoplasia do coração que tenha uma ocorrência rara. O grupo engloba lesões como mixomas, rabdomiomas e outras formações descritas na literatura médica.
Referências
Fontes citadas no texto, publicações do grafo e bases de dados usadas neste verbete
3 fontes citadas no texto · 5 publicações do grafo RarasNet (PubMed) · 3 bases de dados. Títulos, periódicos e PMIDs vêm direto da fonte, sem intermediação de IA.
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Citar este verbete
Raras. (2026). Tumor cardíaco. Em Raras — Enciclopédia de Doenças Raras do Brasil. https://raras.org/doenca/tumor-cardiaco
Formato APA. Conteúdo sob CC BY 4.0 — reuso livre com atribuição.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
Tumor cardíaco
📋 Origem dos dados
Esta página agrega dados de fontes públicas e oficiais. Dados sobre cobertura no SUS (PCDT, CEAF) são verificados ativamente por agente proativo (ver badge no infobox). Demais dados têm atribuição de fonte + data da última sincronização — clique para abrir o original.
- Doença rara (ontologia)
- fonte: Orphanet
- Identificador unificado
- fonte: MONDO
- Dado público estruturado
- fonte: Wikidata
