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Anotia
ORPHA:93976CID-10 · Q16.1CID-11 · LA22.1DOENÇA RARA

Microtia é uma deformidade congênita, na qual o pavilhão auricular é subdesenvolvido. Uma orelha completamente subdesenvolvida é referida como anotia. Devido ao fato de microtia e anotia terem a mesma origem, a condição pode ser chamada genericamente de microtia-anotia. A microtia pode ser unilateral ou bilateral. A microtia ocorre em cerca de 1 a cada 8.000 a 10.

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Introdução

O que você precisa saber de cara

📋

Anotia é a ausência congênita total de uma ou ambas as orelhas externas. Geralmente associada a outras anomalias craniofaciais, pode afetar a audição e a estética.

Pesquisas ativas
1 ensaio
4 total registrados no ClinicalTrials.gov
Publicações científicas
203 artigos
Último publicado: 2025 Dec 3

Escala de raridade

CLASSIFICAÇÃO ORPHANET · BRASIL 2024
<1 / 1 000 000
Ultra-rara
<1/50k
Muito rara
1/20k
Rara
1/10k
Pouco freq.
1/5k
Incomum
1/2k
Prevalência
0.03
Specific population
Início
Infancy
+ neonatal
🏥
SUS: Cobertura mínimaScore: 15%
CID-10: Q16.1
🇧🇷Dados SUS / DATASUS
PROCEDIMENTOS SIGTAP (5)
0202010503
Cariótipo — bandas G, Q ou Rgenetic_test
0202010600
Pesquisa de microdeleções/microduplicações por FISHlab_test
0202010694
Sequenciamento completo do exoma (WES)rehabilitation
0202010260
Dosagem de alfa-fetoproteína
0301070040
Atendimento em reabilitação — doenças raras
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Entender a doença

Do básico ao detalhe, leia no seu ritmo

Preparando trilha educativa...

Sinais e sintomas

O que aparece no corpo e com que frequência cada sintoma acontece

Linha do tempo da pesquisa

Publicações por ano — veja quando o interesse científico cresceu
Anos de pesquisa1desde 2026
Total histórico203PubMed
Últimos 10 anos94publicações
Pico202317 papers
Linha do tempo
2026Hoje · 2026🧪 2013Primeiro ensaio clínico📈 2023Ano de pico
Publicações por ano (últimos 10 anos)

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Genética e causas

O que está alterado no DNA e como passa nas famílias

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Nenhum gene associado encontrado

Os dados genéticos desta condição ainda estão sendo catalogados.

Diagnóstico

Os sinais que médicos procuram e os exames que confirmam

Carregando...

Tratamento e manejo

Remédios, cuidados de apoio e o que precisa acompanhar

Pipeline de tratamentos
Pipeline regulatório — de medicamentos já aprovados a drogas em pesquisa exploratória.
·Pré-clínico3
Medicamentos catalogadosEnsaios clínicos· 0 medicamentos · 3 ensaios
Carregando informações de tratamento...

Onde tratar no SUS

Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

🇧🇷 Atendimento SUS — Anotia

🗺️

Selecione um estado ou use sua localização para ver resultados.

Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.

Pesquisa ativa

Ensaios clínicos abertos e novidades científicas recentes

🟢 Recrutando agora

1 pesquisa recrutando participantes. Converse com seu médico sobre a possibilidade de participar.

Outros ensaios clínicos

4 ensaios clínicos encontrados, 1 ativos.

Distribuição por fase
Ver todos no ClinicalTrials.gov
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Publicações mais relevantes

Timeline de publicações
96 papers (10 anos)
#1

Total Ear Reconstruction with Costal Cartilage in Challenging Cases: Silicone-Induced Vascularized Capsule Technique.

Plastic and reconstructive surgery2026 Feb 01

Total ear reconstruction using an autogenous costal cartilage framework within a mastoid skin pocket becomes challenging when suboptimal mastoid skin prevents complete framework embedding. Twelve patients with suboptimal mastoid skin underwent a silicone-induced vascularized capsule technique. Eight patients had congenital dystopic lobule-remnant microtia or anotia, accompanied by a severely low hairline, hemifacial microsomia, or both. Three patients had lobule-remnant congenital microtia requiring revision, and 1 patient had posttraumatic microtia. In 7 cases, hair-bearing mastoid skin was treated preoperatively with laser depilation. During the first stage, silicone blocks were placed in the recessed area of the cartilage framework-either the concha (11 patients) or scapha (1 patient)-to promote formation of a vascularized capsule between the silicone and bare cartilage, enhancing skin-to-framework contact. The second stage involved framework elevation to achieve ear projection. In the third stage, silicone blocks were removed, and skin grafts were applied. Two patients were excluded because of incomplete final-stage surgery. Nine patients developed well-vascularized capsules, enabling full-thickness skin grafting, without tissue loss. One had partial capsule loss from silicone exposure through a scar, but the remaining capsule supported successful grafting. During the 10-month to 4-year follow-up, grafted skin remained stable, with well-preserved contours. The capsule provided additional coverage of 227 mm 2 to 841 mm 2 (mean, 553 mm 2 ). All patients reported high satisfaction. This technique offers a reliable option for total ear reconstruction in patients with suboptimal mastoid skin, allowing tension-free coverage and stable long-term outcomes.

#2

A Modified Method for Ear Projection in Auricular Reconstruction: Split-Thickness Skin Graft Combined with Retroauricular Fascia Flap.

Plastic and reconstructive surgery2026 Feb 01

The 2-stage Nagata technique is one of the most prevalent methods for auricular reconstruction. Nevertheless, in the second stage, the use of a temporoparietal fascial flap usually requires an additional incision, and the procurement of donor skin from the groin or chest area can result in extra scarring, which may reduce patients' satisfaction with the surgical outcomes. The authors propose a refined method using a retroauricular fascia flap combined with a split-thickness skin graft for postauricular coverage, which can avoid additional scarring in the temporoparietal and donor skin area. From April of 2019 to January of 2024, auricular reconstructions on 337 ears across 324 patients were performed using this novel technique. The classification of microtia, duration of surgery, and postoperative complications were recorded. The authors finally evaluated the scar condition and patient satisfaction with surgery outcomes in the 1- to 2-year postoperative period. In the authors' study, 154 patients were diagnosed with lobule-type microtia, 53 patients were diagnosed with small concha-type microtia, 62 patients were diagnosed with concha-type microtia, and 55 patients were diagnosed patients with anotia. The average duration of the second-stage surgery was 2.8 hours. Patients who underwent this modified technique exhibited no noticeable long-term postoperative scarring and no instances of flap necrosis, framework deformation, cartilage exposure, infection, or mismatched skin color following the procedure. Furthermore, 94% of the patients reported satisfaction with the surgical outcomes. The use of continuous split-thickness skin grafts, combined with a retroauricular fascial flap, offers a safe, effective, and aesthetically pleasing solution for second-stage auricular projection.

#3

An Overview of the Currently Used Congenital Auricular Anomalies (CAA) Classifications for Surgical Reconstruction: A Scoping Review.

The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association2026 Apr

BackgroundCAAs are congenital malformations of the auricle ranging from ear underdevelopment to anotia, lacks standardized classification, impacting our outcome of different reconstruction approaches. This scoping review aimed to explore which CAA classifications are most used in current ear reconstruction practices.MethodsWe conducted a scoping review following the PRISMA guidelines, searching MEDLINE and Embase databases on November 1st, 2023. Studies on CAA reconstruction that included clear descriptions of the used classification published in the past 5 years were included. Studies were appraised using the Joanna Briggs Institute checklist.ResultsOut of 293 screened studies, 45 met inclusion criteria, encompassing 19 case series and 5 cohort studies. Findings revealed a predominant use of the Nagata classification across rib cartilage and alloplastic material reconstructions, despite noted application inconsistencies. Other systems like Marx's, Weerda's, and Meurman's remain underutilized.ConclusionMost studies used the Nagata's classification. Its widespread use underscores the necessity for an easy to use, but standardized classification to improve surgical outcome reporting and assessment accuracy. Further investigation and standardization efforts regarding the Nagata system are recommended.

#4

A systematic review of congenital external ear anomalies and their associated factors.

Frontiers in pediatrics2025

External ear anomalies may lead to conductive hearing loss with significant childhood disability, psychological distress, anxiety, social avoidance, and behavioral problems. The aim of this study is to compile and review published literature on the frequency of isolated and non-isolated external ear anomalies, their associated factors, and associated malformations/deformations in non-isolated cases. We conducted a systematic review in PubMed, Google Scholar, and Science Direct searching for any type of article (excluding reviews and meta-analyses) reporting isolated and non-isolated external ear anomalies in humans. Two authors extracted the information according to the main variables of interest according to PICO criteria. Details of studied population and main findings were also obtained (malformation type, unilateral or bilateral malformations and associated factors). Twenty-six studies met eligibility criteria to be included in this review. Anotia/microtia was the most reported malformation, more frequently found in males, mostly unilateral; being the right ear the most affected, and more frequent in Hispanic population. Associated factors for external ear anomalies included parental age, maternal education, multiple pregnancies, high maternal body mass index and diabetes, pregnancy, and perinatal complications (low birth weight, prematurity, threatened abortion, etc.), twining, and chemical/drug exposure. The most reported malformations and syndromes associated with congenital external ear defects included: skull/face anomalies, cleft lip/palate, congenital heart defects, musculoskeletal malformations of skull, face and jaw, Treacher-Collins, OAVS (oculo-auriculo-vertebral spectrum), and trisomy 18, 13 and 21. Congenital external ear anomalies can occur isolated or associated with other malformations or syndromes. Environmental, socioeconomic, and cultural factors may partially explain the variation across populations for congenital external ear anomalies. Depending on their type and severity, they can lead to speech impediments and childhood disability, particularly in bilateral cases, highlighting the relevance of early detection and repair to avoid childhood disability.

#5

Association between maternal occupation as a cleaner/maid/janitor during early pregnancy and selected birth defects in the National Birth Defects Prevention Study.

Occupational and environmental medicine2025 Dec 03

Cleaning work involves potential exposures to physical, chemical, biological and psychosocial hazards, which might increase the risk of birth defects. Yet, there is limited research focused on maternal occupation in cleaning jobs and the risk of birth defects. We investigated the association between maternal occupation in cleaning-related jobs during early pregnancy and selected birth defects in the National Birth Defects Prevention Study, a case-control study from 1997 to 2011. Mothers self-reported job details, which were classified by occupational epidemiologists into cleaner or non-cleaner occupations. Cases were live births or stillbirths with at least one of 19 eligible birth defects ascertained from state surveillance systems, while controls were randomly selected live births without structural defects. We estimated adjusted ORs with 95% CIs from multivariable logistic regression for associations between maternal cleaning occupations and birth defects, controlling for eight covariates identified a priori. Of the 28 936 mothers, 1109 (868 cases/241 controls) were assigned a primary occupational code as a cleaner during early pregnancy. In total, 9 of the 19 included birth defects had elevated ORs (>1.5), ranging from 1.58 for anophthalmia/microphthalmia to 2.65 for oesophageal atresia/stenosis; six had CIs that excluded the null (anencephaly, glaucoma, anotia/microtia, cleft lip and palate, oesophageal atresia/stenosis, small intestinal atresia/stenosis). We observed that maternal occupation in cleaning-related jobs was associated with several specific birth defects in various body systems. Future studies should explore specific chemical and physical exposures under these cleaning occupations and the association with birth defects.

Publicações recentes

Ver todas no PubMed

📚 EuropePMC55 artigos no totalmostrando 92

2025

Association between maternal occupation as a cleaner/maid/janitor during early pregnancy and selected birth defects in the National Birth Defects Prevention Study.

Occupational and environmental medicine
2025

Non-recurrent duplications on chromosome 4p16.1 involving cis-regulatory elements affecting neural crest development in patients with isolated bilateral microtia.

Human genetics
2025

A new species of Anotia Westwood from Bonaire and Curaao (Fulgoromorpha: Fulgoroidea: Derbidae: Otiocerini).

Zootaxa
2026

Total Ear Reconstruction with Costal Cartilage in Challenging Cases: Silicone-Induced Vascularized Capsule Technique.

Plastic and reconstructive surgery
2026

A Modified Method for Ear Projection in Auricular Reconstruction: Split-Thickness Skin Graft Combined with Retroauricular Fascia Flap.

Plastic and reconstructive surgery
2025

The Relationship Between Microtia and Complex Chronic Conditions: A Comprehensive Analysis of 20 000 Patients.

The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association
2025

Racial, Ethnic, and Socioeconomic Trends in Microtia and Anotia Care.

The Journal of craniofacial surgery
2025

A systematic review of congenital external ear anomalies and their associated factors.

Frontiers in pediatrics
2025

Microtia Reconstruction: 30-Day Outcomes for Autograft Versus Implant Reconstruction in a National Surgical Database.

The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association
2025

Epidemiological Characteristics and Maternal Risk Factors of Microtia and Aural Atresia in Kazakhstan.

International archives of otorhinolaryngology
2026

An Overview of the Currently Used Congenital Auricular Anomalies (CAA) Classifications for Surgical Reconstruction: A Scoping Review.

The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association
2025

Genetics of Nonsyndromic Microtia and Congenital Aural Atresia: A Scoping Review.

Otolaryngology--head and neck surgery : official journal of American Academy of Otolaryngology-Head and Neck Surgery
2024

Temporal trends in the prevalence of major birth defects in China: a nationwide population-based study from 2007 to 2021.

World journal of pediatrics : WJP
2024

Comparison of total prevalence, perinatal prevalence, and livebirth prevalence of birth defects in Hunan Province, China, 2016-2020.

Frontiers in public health
2024

Hemifacial Microsomia Surgical Approach and Anotia Reconstruction: A Case Report.

In vivo (Athens, Greece)
2024

Complex Presentation of Goldenhar Syndrome in a Preterm Neonate: A Case Report.

Cureus
2024

Early Non-Surgical Treatment For Microtia Types 1 and 2.

The Journal of craniofacial surgery
2024

Tissue Engineering Auricular Cartilage: A Review of Auricular Cartilage Characteristics and Current Techniques for Auricular Reconstruction.

The Journal of craniofacial surgery
2023

A new species of planthopper in the genus Anotia (Hemiptera: Auchenorrhyncha: Derbidae) from the Los Angeles cloud forest in Costa Rica.

Zootaxa
2024

Genetic basis of ear length in sheep breeds sampled across the region from the Middle East to the Alps.

Animal genetics
2023

Severe Unilateral Microtia with Aural Atresia, Hair White Patch, Stereotypes in a Young Boy with De novo 16p13.11 Deletion: Reasons for a New Genotype-Phenotype Correlation.

Global medical genetics
2023

Phenotypic and Genomic Characterization of the Comune di Sicilia Goat: Towards the Conservation of an Endangered Local Breed.

Animals : an open access journal from MDPI
2023

Strengthening capacity of health workers to diagnose birth defects in Ugandan hospitals from 2015 to 2021.

BMC medical education
2024

Early Postoperative Complications in Microtia Reconstruction: An Analysis of the NSQIP-P Database.

The Laryngoscope
2023

Bilateral Anotia In A Preterm Neonate After Maternal Retinoic Acid Exposure.

Klinische Padiatrie
2023

Goldenhar Syndrome: An Atypical Presentation With Developmental and Speech Delay.

Cureus
2023

Oculo auriculo vertebral spectrum and CHARGE association.

BMJ case reports
2023

Hospital Length of Stay and Surgery among European Children with Rare Structural Congenital Anomalies-A Population-Based Data Linkage Study.

International journal of environmental research and public health
2023

Geospatiotemporal and Causal Inferential Study of European Epidemiological Patterns of Cannabis- and Substance-Related Congenital Orofacial Anomalies.

Journal of xenobiotics
2023

3D printed bionic ear and microtia-anotia: Medical and forensic implications.

Congenital anomalies
2023

The Alberta Congenital Anomalies Surveillance System: a 40-year review with prevalence and trends for selected congenital anomalies, 1997-2019.

Health promotion and chronic disease prevention in Canada : research, policy and practice
2023

Patterns of co-occurring birth defects in children with anotia and microtia.

American journal of medical genetics. Part A
2023

Prevalence and characteristics of microtia in Oman: 37 Years analysis.

Journal of plastic, reconstructive &amp; aesthetic surgery : JPRAS
2023

Factors associated with nonsyndromic anotia and microtia, Texas, 1999-2014.

Birth defects research
2023

Assessing associations between residential proximity to greenspace and birth defects in the National Birth Defects Prevention Study.

Environmental research
2023

Contribution of Preterm Birth to Mortality Among Neonates with Birth Defects.

The Journal of pediatrics
2022

Retroposition of the Vestigial Cartilage in Patients With Microtia: A Novel Technique to Enhance Projection of the Reconstructed Ear.

The Journal of craniofacial surgery
2023

Search for a genetic cause in children with unilateral isolated microtia and congenital aural atresia.

European archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery
2022

Barriers to Pediatric Osseointegrated Bone-Conduction Hearing Devices.

Otology &amp; neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
2021

The effects of Goldenhar Syndrome on hearing and speech development.

The Medical journal of Malaysia
2022

A homozygous missense variant in laminin subunit beta 1 as candidate causal mutation of hemifacial microsomia in Romagnola cattle.

Journal of veterinary internal medicine
2021

Multicorrection Goldenhar syndrome (facio-auriculo-vertebral dysplasia): a rare follow-up case of 12-year-old female.

The Pan African medical journal
2021

Ten-year trends in the incidence of microtia: a nationwide population-based study from Taiwan.

European archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery
2022

Maternal occupation as a nail technician or hairdresser during pregnancy and birth defects, National Birth Defects Prevention Study, 1997-2011.

Occupational and environmental medicine
2022

Does Prematurity Play a Role in Newborn Microtia-Anotia?

The Annals of otology, rhinology, and laryngology
2021

Birth prevalence of congenital anomalies in Argentina, according to socioeconomic level.

Journal of community genetics
2021

Berry-Treacher Collins Syndrome With Congenital Bell's Palsy and Unilateral Anotia: Tongue-Tie Release Under General Anesthesia.

Cureus
2021

Congenital heart defects in patients with isolated microtia: evaluation using colour Doppler echocardiographic image.

Cardiology in the young
2020

Hemifacial Microsomia Review: Recent Advancements in Understanding the Disease.

The Journal of craniofacial surgery
2020

A new species of planthopper in the genus Anotia Kirby (Hemiptera: Auchenorrhyncha: Derbidae) from coconut palm in Costa Rica.

Zootaxa
2021

Improving In Vitro Cartilage Generation by Co-Culturing Adipose-Derived Stem Cells and Chondrocytes on an Allograft Adipose Matrix Framework.

Plastic and reconstructive surgery
2020

Atypical presentation of Cat Eye Syndrome in an infant with Peters anomaly and microphthalmia with cyst.

Ophthalmic genetics
2020

[TOTAL RECONSTRUCTION OF CONGENITAL MICROTIA - OUR EXPERIENCE WITH 150 PATIENTS].

Harefuah
2020

Management of Congenital Auricular Anomalies.

Plastic and reconstructive surgery
2020

Review of 602 Microtia Reconstructions: Revisions and Specific Recommendations for Each Subtype.

Plastic and reconstructive surgery
2020

Duplication in ECR Near HMX1 and a SNP in GATA6 Genes Regulate Microtia in Awassi Sheep.

Genes
2020

Acculturation and selected birth defects among non-Hispanic Blacks in a population-based case-control study.

Birth defects research
2020

Review of Preferential Suspicious Genes in Microtia Patients Through Various Approaches.

The Journal of craniofacial surgery
2020

Birth prevalence of congenital anomalies in the City of Buenos Aires, Argentina, according to socioeconomic level.

Journal of community genetics
2019

Genome-wide association studies of structural birth defects: A review and commentary.

Birth defects research
2019

A hospital-based birth defects surveillance system in Kampala, Uganda.

BMC pregnancy and childbirth
2019

Reconstruction of Congenital Microtia and Anotia: Analysis of Practitioner Epidemiology and Postoperative Outcomes.

Plastic and reconstructive surgery. Global open
2019

Cardiofacial Syndrome: A Rare Case Report.

Mymensingh medical journal : MMJ
2019

Otoplasty and Auricular Reconstruction.

Facial plastic surgery : FPS
2019

Selected acculturation factors and birth defects in the National Birth Defects Prevention Study, 1997-2011.

Birth defects research
2019

Sociodemographic, health behavioral, and clinical risk factors for anotia/microtia in a population-based case-control study.

International journal of pediatric otorhinolaryngology
2019

Evaluation of prenatal diabetes mellitus and other risk factors for craniofacial microsomia.

Birth defects research
2019

Computer guided temporomandibular joint reconstruction of Kaban III hemifacial microsomia with anotia: A case report.

International journal of surgery case reports
2019

Cochlear implantation via middle fossa approach - a case report.

Cochlear implants international
2019

Preferential Associated Malformation in Patients With Anotia and Microtia.

The Journal of craniofacial surgery
2018

Population-based birth defects data in the United States, 2011-2015: A focus on eye and ear defects.

Birth defects research
2018

Study of selected birth defects among American Indian/Alaska Native population: A multi-state population-based retrospective study, 1999-2007.

Birth defects research
2018

Genome-wide association study reveals the locus responsible for microtia in Valle del Belice sheep breed.

Animal genetics
2018

Antenatal Diagnosis of Fetal Retinoid Syndrome at 20 Weeks of Gestation: A Case Report.

Fetal and pediatric pathology
2018

Co-culture of adipose-derived stem cells and chondrocytes on three-dimensionally printed bioscaffolds for craniofacial cartilage engineering.

The Laryngoscope
2018

Osseointegrated implants for auricular prostheses: An alternative to autologous repair.

The Laryngoscope
2017

Retinoic Acid Embryopathy.

International journal of applied &amp; basic medical research
2017

Baha Attract: Our Experience.

Indian journal of otolaryngology and head and neck surgery : official publication of the Association of Otolaryngologists of India
2017

Our Experience of Treating Wide Spectrum of External Ear Canal Atresia of Different Etiologies in Pediatric Patients.

Indian journal of otolaryngology and head and neck surgery : official publication of the Association of Otolaryngologists of India
2017

Cost analysis of microtia treatment in the Netherlands.

Journal of plastic, reconstructive &amp; aesthetic surgery : JPRAS
2017

Maxillofacial features and systemic malformations in expanded spectrum Hemifacial Microsomia.

American journal of medical genetics. Part A
2016

Genetic Advances in the Understanding of Microtia.

Journal of pediatric genetics
2016

Newborn with congenital facial palsy and bilateral anotia/atresia of external auditory canal: Rare occurrence.

Journal of pediatric neurosciences
2016

Associated anomalies in cases with anotia and microtia.

European journal of medical genetics
2017

Mycophenolate mofetil embryopathy: A newly recognized teratogenic syndrome.

European journal of medical genetics
2016

Bone and Skin-Supported Stereolithographic Surgical Guides for Cranio-Facial Implant Placement.

Journal of maxillofacial and oral surgery
2016

Residential agricultural pesticide exposures and risks of selected birth defects among offspring in the San Joaquin Valley of California.

Birth defects research. Part A, Clinical and molecular teratology
2016

Epidemiologic characteristics and time trend in the prevalence of anotia and microtia in China.

Birth defects research. Part A, Clinical and molecular teratology
2015

Congenital Auricular Malformations: Description of Anomalies and Syndromes.

Facial plastic surgery : FPS
2015

Congenital malformations caused by Stryphnodendron fissuratum (Leg. Mimosoideae) in guinea pigs (Cavia porcellus).

Toxicon : official journal of the International Society on Toxinology
2015

Auricular reconstruction of congenital microtia: personal experience in 225 cases.

Acta otorhinolaryngologica Italica : organo ufficiale della Societa italiana di otorinolaringologia e chirurgia cervico-facciale
2015

Maternal occupational exposure to ionizing radiation and major structural birth defects.

Birth defects research. Part A, Clinical and molecular teratology

Associações

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Comunidades

Grupos ativos de quem convive com esta doença aqui no Raras

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Doenças relacionadas

Doenças com sintomas parecidos — ajudam quem ainda está buscando diagnóstico

Ainda não achamos doenças com sintomas parecidos o suficiente.

Referências e fontes

Bases de dados externas citadas neste artigo

Publicações científicas

Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.

  1. Total Ear Reconstruction with Costal Cartilage in Challenging Cases: Silicone-Induced Vascularized Capsule Technique.
    Plastic and reconstructive surgery· 2026· PMID 40690331mais citado
  2. A Modified Method for Ear Projection in Auricular Reconstruction: Split-Thickness Skin Graft Combined with Retroauricular Fascia Flap.
    Plastic and reconstructive surgery· 2026· PMID 40663787mais citado
  3. An Overview of the Currently Used Congenital Auricular Anomalies (CAA) Classifications for Surgical Reconstruction: A Scoping Review.
    The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association· 2026· PMID 39846418mais citado
  4. A systematic review of congenital external ear anomalies and their associated factors.
    Frontiers in pediatrics· 2025· PMID 40342890mais citado
  5. Association between maternal occupation as a cleaner/maid/janitor during early pregnancy and selected birth defects in the National Birth Defects Prevention Study.
    Occupational and environmental medicine· 2025· PMID 41266119mais citado
  6. Non-recurrent duplications on chromosome 4p16.1 involving cis-regulatory elements affecting neural crest development in patients with isolated bilateral microtia.
    Hum Genet· 2025· PMID 41143892recente
  7. A new species of Anotia Westwood from Bonaire and Curaao (Fulgoromorpha: Fulgoroidea: Derbidae: Otiocerini).
    Zootaxa· 2025· PMID 41119237recente

Bases de dados e fontes oficiais

Identificadores e referências canônicas usadas para montar este verbete.

  1. ORPHA:93976(Orphanet)
  2. MONDO:0019780(MONDO)
  3. GARD:16835(GARD (NIH))
  4. Busca completa no PubMed(PubMed)
  5. Q15057288(Wikidata)

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Anotia
Compêndio · Raras BR

Anotia

ORPHA:93976 · MONDO:0019780
Prevalência
<1 / 1 000 000
CID-10
Q16.1 · Ausência, atresia e estreitamento congênitos do conduto auditivo (externo)
CID-11
Ensaios
1 ativos
Início
Infancy, Neonatal
Prevalência
0.03 (Specific population)
MedGen
UMLS
C0702139
EuropePMC
Wikidata
Papers 10a
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