O cor triatriatum sinister (CTS) resulta quando o átrio esquerdo é dividido em dois compartimentos por uma membrana. A membrana pode variar em tamanho e formato e pode ter uma ou mais aberturas. Casos graves de cor triatriatum sinister geralmente se apresentam na infância e frequentemente estão associados a outros defeitos cardíacos. Em casos menos graves, o diagnóstico pode não ser feito até fases posteriores da vida. Os sintomas específicos dependem do grau em que a membrana obstrui o fluxo sanguíneo e da presença ou não de defeitos cardíacos adicionais. Os sintomas podem variar desde falta de ar leve durante o exercício até sinais de insuficiência cardíaca e congestão pulmonar. Algumas pessoas com CTS podem não apresentar sintomas. O tratamento varia de acordo com a gravidade dos sintomas. Para pacientes sintomáticos, a cirurgia é geralmente considerada o curso definitivo de terapia.
Introdução
O que você precisa saber de cara
Visão geral
O cor triatriatum sinister (CTS) é uma condição cardíaca congênita que ocorre quando o átrio esquerdo é dividido em dois compartimentos por uma membrana. Essa membrana anatômica pode apresentar variações tanto em seu tamanho quanto em seu formato, contendo uma ou mais aberturas. Em classificações nosológicas internacionais, a condição é catalogada sob o código CID-10 Q24.2 e identificada pelo identificador MONDO:0020430.[1][2]
Sinais e sintomas
As manifestações clínicas do cor triatriatum dependem diretamente do grau de obstrução do fluxo sanguíneo causado pela membrana e da presença ou não de defeitos cardíacos associados. Casos graves frequentemente se apresentam na infância e estão comumente associados a outras cardiopatias. Em situações menos graves, o quadro pode permanecer não diagnosticado até etapas posteriores da vida, e algumas pessoas com a alteração podem ser completamente assintomáticas.[1]
Nos indivíduos que manifestam sintomas, o quadro clínico pode variar desde uma falta de ar leve durante a realização de exercícios físicos até sinais francos de insuficiência cardíaca e congestão pulmonar.[1]
Diagnóstico
O momento do diagnóstico é variável: casos com obstrução expressiva tendem a ser identificados ainda na infância, enquanto indivíduos com alterações menos severas podem ter o diagnóstico estabelecido apenas na idade adulta ou em fases mais tardias da vida, devido à menor intensidade ou ausência de sintomas obstrutivos iniciais.[1]
Tratamento e manejo
A abordagem terapêutica para o cor triatriatum varia em função da gravidade dos sintomas apresentados pelo paciente. Para as pessoas sintomáticas, o procedimento cirúrgico é geralmente considerado o curso definitivo de terapia com o objetivo de corrigir o fluxo sanguíneo intracardíaco.[1]
Conteúdo informativo gerado e mantido automaticamente a partir de fontes oficiais (Orphanet, HPO, OMIM, SUS). Não substitui avaliação médica.
O cor triatriatum é uma alteração congênita rara em que o átrio esquerdo do coração fica dividido em dois espaços por uma membrana. Dependendo de quanto essa membrana bloqueia a circulação, a pessoa pode não sentir nada ou ter falta de ar aos esforços e congestão pulmonar. Quando os sintomas aparecem e prejudicam a função do coração, a cirurgia para retirar a membrana costuma ser a opção definitiva de tratamento. A doença não possui protocolo clínico (PCDT) próprio no Ministério da Saúde, mas o SUS oferece atendimento e acompanhamento de reabilitação na sua rede especializada.
O cor triatriatum sinister (CTS) resulta quando o átrio esquerdo é dividido em dois compartimentos por uma membrana. A membrana pode variar em tamanho e formato e pode ter uma ou mais aberturas. Casos graves de cor triatriatum sinister geralmente se apresentam na infância e frequentemente estão associados a outros defeitos cardíacos. Em casos menos graves, o diagnóstico pode não ser feito até fases posteriores da vida. Os sintomas específicos dependem do grau em que a membrana obstrui o fluxo sanguíneo e da presença ou não de defeitos cardíacos adicionais. Os sintomas podem variar desde falta de ar leve durante o exercício até sinais de insuficiência cardíaca e congestão pulmonar. Algumas pessoas com CTS podem não apresentar sintomas. O tratamento varia de acordo com a gravidade dos sintomas. Para pacientes sintomáticos, a cirurgia é geralmente considerada o curso definitivo de terapia.
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Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Linha do tempo da pesquisa
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Genética e causas
O que está alterado no DNA e como passa nas famílias
Nenhum gene associado encontrado
Os dados genéticos desta condição ainda estão sendo catalogados.
Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
Remédios, cuidados de apoio e o que precisa acompanhar
Onde tratar no SUS
Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)
🇧🇷 Atendimento SUS — Cor triatriatum
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Ensaios clínicos abertos e novidades científicas recentes
Pesquisa e ensaios clínicos
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Publicações mais relevantes
Atrioventricular septal defect with cor triatriatum sinister.
Anatomical and electrophysiological characteristics of the intra-atrial membranous structure in a patient with cor triatriatum sinister undergoing atrial fibrillation catheter ablation.
Cor Triatriatum Sinister and Eustachian Valve Mimicking Vena Cava Inferior Stenosis: Coexistent Remnant Membranes.
A giant coronary artery aneurysm with right atrium fistula mimicking a cor triatriatum sinister.
One-stop procedure for persistent atrial fibrillation with cor triatriatum sinister under intracardiac echocardiography guidance: a case report.
This case report describes the treatment of a 76-year-old male patient diagnosed with persistent atrial fibrillation (AF) and cor triatriatum sinister (CTS). The patient presented with palpitations and shortness of breath for four years, exacerbated over two weeks. Cardiac ultrasound and computed tomography angiography (CTA) confirmed Bank II type complete CTS, with all four pulmonary veins draining into an accessory atrium. The patient also had lacunar stroke and heart failure, with a CHA2DS2-VASc score of 5 and HAS-BLED score of 2, indicating high stroke risk and moderate bleeding risk. Given the anatomical abnormalities and clinical characteristics, we performed a one-stop procedure under intracardiac echocardiography (ICE) guidance, combining AF radiofrequency ablation and left atrial appendage closure (LAAC). Post-procedure recovery was uneventful, and follow-up transesophageal echocardiography showed no residual shunt or thrombus around the occluder. An antithrombotic regimen of rivaroxaban 15 mg once daily for three months followed by aspirin 100 mg once daily long-term was prescribed. This case highlights the critical role of ICE technology in complex cardiac anatomy and the importance of personalized antithrombotic strategies in high-risk AF patients.
Publicações recentes
Percutaneous Closure of Patent Foramen Ovale in a Patient With Incomplete Cor Triatriatum Sinister: A Case Report.
Case Report: Cor triatriatum sinister presenting as acute decompensated heart failure in an adolescent.
Atrioventricular septal defect with cor triatriatum sinister.
📖 RevisãoAnatomical and electrophysiological characteristics of the intra-atrial membranous structure in a patient with cor triatriatum sinister undergoing atrial fibrillation catheter ablation.
Cor Triatriatum Sinister and Eustachian Valve Mimicking Vena Cava Inferior Stenosis: Coexistent Remnant Membranes.
🥉 Relato de caso📚 EuropePMC196 artigos no totalmostrando 141
Atrioventricular septal defect with cor triatriatum sinister.
Anales de pediatriaAnatomical and electrophysiological characteristics of the intra-atrial membranous structure in a patient with cor triatriatum sinister undergoing atrial fibrillation catheter ablation.
HeartRhythm case reportsCor Triatriatum Sinister and Eustachian Valve Mimicking Vena Cava Inferior Stenosis: Coexistent Remnant Membranes.
The Annals of thoracic surgeryThe feasibility and safety of cryoballoon ablation in an elderly patient with cor triatriatum sinister and persistent atrial fibrillation: A case report and a review.
HeartRhythm case reportsOne-stop procedure for persistent atrial fibrillation with cor triatriatum sinister under intracardiac echocardiography guidance: a case report.
Frontiers in cardiovascular medicinePerinatal Stroke and Cor Triatriatum Sinister: A Case Report.
CureusCor Triatriatum Sinister in a 34-Year-Old Woman.
CASE (Philadelphia, Pa.)Partial AVSD with cortriatriatum sinister with unroofed coronary sinus in an adult.
Annals of pediatric cardiologyCor Triatriatum Sinister in Adulthood: A Rare Clinical Encounter.
CureusUsing 3D Heart Printing for Planning to Repair a Complex Congenital Heart Disease via Minimal Invasive Thoracotomy.
JACC. Case reportsCor Triatriatum Sinister With a Patent Foramen Ovale Presenting With Embolic Stroke.
JACC. Case reportsDivided left atrium (cor triatriatum sinister) with atresia of the right pulmonary veins in a cat.
Journal of veterinary cardiology : the official journal of the European Society of Veterinary CardiologyA Case Report of Cor Triatriatum Sinister (CTS) in an Asymptomatic Adult with Chronic Adhesive Pericarditis.
Current medical imagingIncomplete Shone's complex with cor triatriatum sinister and interrupted aortic arch: Prenatal diagnosis of a rare association.
Annals of pediatric cardiologyAnte-mortem diagnosis of unilateral pulmonary vein stenosis in a cat: a case report.
Acta veterinaria ScandinavicaCor triatriatum sinister with partial atrioventricular septal defect in a cat.
Veterinarni medicinaRadiofrequency catheter ablation of persistent atrial fibrillation in a patient with cor triatriatum sinister.
Heart rhythm O2Successfully repaired adult cor triatriatum with mitral regurgitation and atrial fibrillation: a case report.
General thoracic and cardiovascular surgery casesCor Triatriatum: an uncommon congenital anomaly - the experience of a tertiary care center in a developing country.
Frontiers in cardiovascular medicineA giant coronary artery aneurysm with right atrium fistula mimicking a cor triatriatum sinister.
European heart journal. Cardiovascular ImagingIncidental Discovery of Forme Fruste Cor Triatriatum Sinister in an Adult Presenting for Emergent Coronary Artery Bypass Graft Surgery.
Journal of cardiothoracic and vascular anesthesiaAn uncommon cardiovascular abnormality: Case report of core triatriatum associated with persistent left superior vena cava and coronary sinus dilation.
Radiology case reportsCor triatriatum sinister in an elderly woman patient with successful conservative treatment.
Oxford medical case reportsSuccessful left atrial catheter ablation in a patient with cor triatriatum sinister navigated by 3D volume rendering technique computed tomography.
European heart journal. Case reportsSuccessful catheter ablation in an octogenarian with persistent atrial fibrillation complicated by cor triatriatum sinister: a case report.
European heart journal. Case reportsPercutaneous balloon angioplasty as a treatment for cor triatriatum sinister in a cat.
Journal of veterinary cardiology : the official journal of the European Society of Veterinary CardiologyCor Triatriatum Sinister With a Decompressing Levoatriocardinal Vein: A Rare Association.
CureusA 10-year-old female with Cor triatriatum sinister (CTS): a rare case report and literature review from Syria.
Annals of medicine and surgery (2012)Identification of novel compound heterozygous variants of the ALMS1 gene in a child with Alström syndrome by whole genome sequencing.
GeneClinical case of Cor triatriatum sinister, a dilemma of anticoagulation: A case report and literature review.
Clinical case reportsCor Triatriatum Sinister: A Rare Congenital Phenomenon in our Everyday Clinical-Surgical Practice.
Heart, lung & circulationCor Triatriatum Sinister in a Young Adult: An Unusual Cause of Syncope.
CureusExploring new frontiers: a rare case of catheter ablation for persistent atrial fibrillation in a patient with cor triatriatum sinister guided by intracardiac echocardiography.
Journal of cardiothoracic surgeryTransapical balloon dilation of cor triatriatum sinister in a cat.
Journal of veterinary cardiology : the official journal of the European Society of Veterinary CardiologyA Case of Persistent Junctional Reciprocating Tachycardia Coincident With Cor Triatriatum Sinister.
World journal for pediatric & congenital heart surgeryLabyrinthine cor triatriatum sinister in fetal hypoplastic left heart syndrome is associated with poor outcomes.
Prenatal diagnosisMultimodality Imaging of a Mass Arising from a Cor Triatriatum Sinister Membrane.
Radiology. Cardiothoracic imagingCardiac MR imaging of cor triatriatum sinister in an elderly man: A rare case report.
Radiology case reportsMultimodality imaging approach to an adult case with cor triatriatum sinister.
Cardiology journalObstructed Supramitral Inflow: Cor Triatriatum Sinister Presentation in Adulthood.
Journal of cardiothoracic and vascular anesthesiaDecoding the Enigma of Cor Triatriatum Sinister Manifesting in Adulthood.
Journal of cardiothoracic and vascular anesthesiaCor Triatriatum: A Review.
Cardiology in reviewEvaluation of Pulmonary Hypertension with Exercise Right Heart Catheterization in an Adult Patient with Cor Triatriatum Sinister.
Turk Kardiyoloji Dernegi arsivi : Turk Kardiyoloji Derneginin yayin organidirCor triatriatum sinister with dextrocardia in association with ostium secundum atrial septal defect, subpulmonary ventricular septal defect and bicuspid pulmonary valve in a pig.
Journal of comparative pathologyCor Triatriatum Sinister Associated with Total Anomalous Pulmonary Venous Connection.
Zeitschrift fur Geburtshilfe und NeonatologieStunning tornado: severe pulmonary hypertension due to cor triatriatum sinister.
European heart journalRight Aortic Arch with Isolated Left Subclavian Artery in Association with Double Outlet Right Ventricle and Cor Triatriatum Sinister: Hitherto Unreported Association.
The Indian journal of radiology & imaging[Cor triatriatum sinister, case report].
Archivos peruanos de cardiologia y cirugia cardiovascularCor triatriatum dexter as an incidental finding due to symptomatic bicuspid aortic valve stenosis.
PerfusionA retrospective study of congenital cardiac malformations in 29 goats.
Journal of veterinary diagnostic investigation : official publication of the American Association of Veterinary Laboratory Diagnosticians, IncThe Multilayered Atrium: An Unusual Case of a Life-Threatening Cor Triatriatum With Persistent Levotrial Cardinal Vein in a 2-Month-Old Infant.
Journal of investigative medicine high impact case reportsPersistent left superior vena cava without right superior vena cava during fetal life.
Cardiology in the youngCorrected Transposition of Great Arteries with Cor Triatriatum and Atrial Septal Defect-Case Report.
The heart surgery forumHidden problems in a case of atrial fibrillation.
Echocardiography (Mount Kisco, N.Y.)The Mashadi-Narasimhan-Said Classification for Cor Triatriatum Sinister: Applicable to All.
Journal of chest surgeryCor triatriatum simulating a left atrial mass in adult patient.
Radiology case reportsCor Triatriatum Sinister Presenting as Cardioembolic Stroke in a Young Woman.
Diagnostics (Basel, Switzerland)Cardiac Computed Tomography Pictorial Equivalent of Angiographic Gooseneck Sign in a Case of Atrioventricular Septal Defect with Cor Triatriatum Sinister.
Heart views : the official journal of the Gulf Heart AssociationA 3D transesophageal echocardiography-facilitated diagnosis and cryoballoon ablation of paroxysmal atrial fibrillation in a patient with cor triatriatum sinister.
Kardiologia polskaCor triatriatum sinister diagnosed in a patient with postoperative cerebral infarction after beach chair position: A case report.
Echocardiography (Mount Kisco, N.Y.)Cor triatriatum sinister: Long-term surgical outcomes in children and a proposal for a new classification.
Journal of cardiac surgeryPrenatal diagnosis of cor triatriatum sinister.
Ultrasound in obstetrics & gynecology : the official journal of the International Society of Ultrasound in Obstetrics and GynecologyDo we really need a new classification for cor triatriatum sinister?
Journal of cardiac surgeryCase report: The impact of percutaneous atrial septal defect closure in pulmonary hypertension with co-existing cor triatriatum sinister and multiple cardiac comorbidities.
Frontiers in cardiovascular medicineCatheter ablation for persistent atrial fibrillation in an elderly patient with cor triatriatum sinister.
HeartRhythm case reportsAsymptomatic Coarctation of the Aorta in Adults with Preserved Exercise Capacity.
Internal medicine (Tokyo, Japan)A case report of atrial fibrillation in early adulthood: dig deeper.
European heart journal. Case reportsAtrial Fibrillation Ablation in a Patient with Cor Triatriatum Sinister and Left Common Pulmonary Vein: Impact of Left Atrium Anatomy on Ablation Approach.
Life (Basel, Switzerland)Supravalvular mitral stenosis in a cat: clinical, diagnostic and pathologic findings.
Journal of ultrasoundCoexistence of Cor Triatriatum Sinister, Fibroelastoma and Pulmonary Veins Ostial Anatomy Variant as Incidental Findings in Coronary Computed Tomography Angiography.
Diagnostics (Basel, Switzerland)Correspondence on Surgical Outcomes of Cor Triatriatum Sinister.
Journal of chest surgerySuccessful Repair of Cor Triatriatum Sinistrum in Childhood: A Single-Institution Experience of Two Cases.
CureusDivided left atrium with totally anomalous drainage of normally connected pulmonary veins.
Cardiology in the youngCor triatriatum sinister with unusual pulmonary venous return.
European heart journal. Case reportsSurgical Outcomes of Cor Triatriatum Sinister: A Single-Center Experience.
Journal of chest surgeryA six-chambered heart: cor triatriatum sinister with double-chambered right ventricle in association with ventricular septal defect.
The Egyptian heart journal : (EHJ) : official bulletin of the Egyptian Society of CardiologyNever Too Old for Congenital Heart Disease: A Case of Cor Triatriatum Sinistrum and Mitral Valve Prolapse.
CureusCatheter ablation of atrial fibrillation in patients with cor triatriatum sinister; case series and review of literature.
Pacing and clinical electrophysiology : PACEA case of "acquired" cor triatriatum.
Indian journal of thoracic and cardiovascular surgerySurgical management of divided atrial chambers.
Journal of cardiac surgeryAdult Obstructive Cor Triatriatum with Severe Mitral Regurgitation: A Case Report.
The heart surgery forumPrenatal diagnosis of cor triatriatum sinister associated with early pericardial effusion: A case report.
World journal of clinical casesCor triatriatum sinister: out of the Lucas-Schmidt classification.
Revista espanola de cardiologia (English ed.)Successful radiofrequency perforation and balloon decompression of cor triatriatum sinister using novel technique, a case series.
Catheterization and cardiovascular interventions : official journal of the Society for Cardiac Angiography & InterventionsCardiac Anomalies in Two White-Tailed Eagles (Haliaeetus albicilla) in Sweden.
Journal of wildlife diseasesMultimodality Imaging of Cor Triatriatum Sinister in an Adult.
Radiology. Cardiothoracic imagingSuccessful catheter ablation of atrial tachycardia in cor triatriatum sinister: A figure-of-8 reentry in the left atrial membrane.
HeartRhythm case reportsDeep Inside Pathology of Cor Triatriatum Sinister.
The Annals of thoracic surgeryComputed tomography features of cor triatriatum: an institutional review.
The British journal of radiologyLoeffler's group 2 cor triatriatum sinistrum with mobile left atrial thrombus - a case report and literature review.
Cardiology in the youngEarly Results of Robotically Assisted Congenital Cardiac Surgery: Analysis of 242 Patients.
The Annals of thoracic surgeryA Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation.
Case reports in pediatricsCor triatriatum sinister with left anomalous pulmonary venous drainage to innominate vein: what to do with the vertical vein?
General thoracic and cardiovascular surgerySupracardiac total anomalous pulmonary venous connection with cor triatriatum sinister: A rare diagnosis confirmed by saline contrast echocardiography.
Echocardiography (Mount Kisco, N.Y.)Three-dimensional visualization of the left atrium by intracardiac echocardiography facilitates trans-septal catheterization and atrial fibrillation catheter ablation in cor triatriatum sinister: A case report and literature review.
Journal of cardiology casesCardioembolic stroke in a young male with cor triatriatum sinister: a case report.
European heart journal. Case reportsA Rare Case of Cor Triatriatum Sinister in Adulthood with Atypical Manifestation.
Heart internationalEndoscopic Repair of Obstructive Cor Triatriatum.
CASE (Philadelphia, Pa.)Anesthetic experience during a laparoscopic appendectomy in a pregnant patient with isolated cor triatriatum sinister.
Saudi journal of anaesthesiaCor Triatriatum Sinister (Divided Left Atrium): Histopathologic Features and Clinical Management.
The Annals of thoracic surgeryCor triatriatum sinister mimicking mitral stenosis.
Turk gogus kalp damar cerrahisi dergisiA Systematic Review of a Long-forgotten Cause of Atrial Fibrillation and Stroke: Cor Triatriatum.
CureusA Rare Case of Cardiogenic Shock: Cor Triatriatum With Anomalous Pulmonary Venous Return.
World journal for pediatric & congenital heart surgerySurgical experience with cor triatriatum repair beyond infancy.
Journal of cardiac surgeryCor triatriatum sinister in a dog.
Journal of veterinary cardiology : the official journal of the European Society of Veterinary Cardiology[Adult Cor Triatriatum Found by Chance at the Onset of Myocardial Infarction].
Kyobu geka. The Japanese journal of thoracic surgeryConcurrent cor triatriatum sinister and levoatriocardinal vein in an 11-year-old boy presenting with foudroyant pulmonary edema after appendectomy: A living tribute to the mal-incorporation theory.
Anatolian journal of cardiologyCor triatriatum sinister with left anomalous pulmonary venous return to innominate vein.
Cardiology in the youngMinimally Invasive Periareolar Approach to Cor Triatriatum Repair.
Innovations (Philadelphia, Pa.)Cor Triatriatum: Case Report of Emergency Department Diagnosis.
Clinical practice and cases in emergency medicineCor Triatriatum Sinister with Secundum Atrial Septal Defect.
CASE (Philadelphia, Pa.)Outcomes in patients with cor triatriatum sinister.
Congenital heart diseaseIt's Crowded Here - A Case of Cor Triatriatum Sinister.
South Dakota medicine : the journal of the South Dakota State Medical AssociationA Very Rare Case of Cor Triatriatum with Severe Mitral Regurgitation.
Open access Macedonian journal of medical sciencesCor Triatriatum Sinister: An Unusual Cause of Atrial Fibrillation in Adults.
Case reports in cardiologyCor triatriatum sinister.
Clinical research in cardiology : official journal of the German Cardiac SocietyAcquired Cor Triatriatum Sinister After the Fontan Operation and Successful Resection in a Child.
The Annals of thoracic surgery[Cardiac arrest in a fitness trainer with apical hypertrophic cardiomyopathy associated with cor triatriatum sinister].
Medizinische Klinik, Intensivmedizin und NotfallmedizinCor triatriatum sinister with an intact interatrial septum and a decompressing vein in a toddler.
Cardiology in the youngMutations in HYAL2, Encoding Hyaluronidase 2, Cause a Syndrome of Orofacial Clefting and Cor Triatriatum Sinister in Humans and Mice.
PLoS geneticsTotally Endoscopic Robotic Correction of Cor Triatriatum Sinister Coexisting With Atrial Septal Defect.
Innovations (Philadelphia, Pa.)A Very Rare Case of Co-Existence of Cor Triatriatum Sinister and Left Pulmonary Vein Atresia.
Acta Cardiologica SinicaCatheter-Based Palliation in an Infant With Obstructed Cor Triatriatum.
The Canadian journal of cardiologyAn interatrial tunnel: a rare form of atrial septal defects.
Echocardiography (Mount Kisco, N.Y.)Cor triatriatum sinister with severe obstruction: a rare presentation in an adult.
BMJ case reports[Subtotal cor triatriatum sinister associated with bilateral partial anomalous pulmonary venous return].
Turk Kardiyoloji Dernegi arsivi : Turk Kardiyoloji Derneginin yayin organidirCor triatriatum sinister: a rare underlying cause of pulmonary hemosiderosis.
SpringerPlusMapping and surgical ablation of persistent atrial fibrillation in cor triatriatum sinister.
European heart journalHyaluronidase 2 deficiency is a molecular cause of cor triatriatum sinister in mice.
International journal of cardiologyCor triatriatum sinister: a case series.
Turk Kardiyoloji Dernegi arsivi : Turk Kardiyoloji Derneginin yayin organidirWong's anomaly - a rare variant of cor triatriatum.
Indian heart journalCor Triatriatum Sinister - Source of Unusual Thrombogenesis in Mitral Stenosis.
Circulation journal : official journal of the Japanese Circulation SocietyDifferent Cardiac Anomalies in Mother and Son with 4q-Syndrome.
Case reports in geneticsSurgical Treatment of Cor Triatriatum Sinister in a Cat Under Cardiopulmonary Bypass.
Veterinary surgery : VSCor triatriatum sinister: Is it less sinister in older patients?
The Journal of thoracic and cardiovascular surgeryHemoptysis as a rare presentation of cor triatriatum sinister.
The Journal of thoracic and cardiovascular surgeryTranscatheter intervention in cor triatriatum sinister.
The Canadian journal of cardiologyAtrial fibrillation and cor triatriatum sinister: a case report.
The Permanente journalProfile and outcome of congenital heart diseases in children: a preliminary experience from a tertiary center in sokoto, north Western Nigeria.
The Nigerian postgraduate medical journalCor triatriatum: a reversible cause of severe pulmonary hypertension.
The Canadian journal of cardiologyCor triatriatum sinister identified after new onset atrial fibrillation in an elderly man.
Case reports in medicineAssociações
Organizações que acompanham esta doença — pra ter apoio e orientação
Ainda não temos associações cadastradas para Cor triatriatum.
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Doenças relacionadas
Doenças com sintomas parecidos — ajudam quem ainda está buscando diagnóstico
Ainda não achamos doenças com sintomas parecidos o suficiente.
Perguntas frequentes
O que as famílias mais perguntam sobre esta doença — cada resposta com a fonte de onde saiu
A anomalia decorre da presença de uma membrana que divide o átrio esquerdo do coração durante o desenvolvimento. Genes causais específicos em seres humanos ainda não foram catalogados nos registros médicos oficiais.
Referências
Fontes citadas no texto, publicações do grafo e bases de dados usadas neste verbete
3 fontes citadas no texto · 7 publicações do grafo RarasNet (PubMed) · 4 bases de dados. Títulos, periódicos e PMIDs vêm direto da fonte, sem intermediação de IA.
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Citar este verbete
Raras. (2026). Cor triatriatum. Em Raras — Enciclopédia de Doenças Raras do Brasil. https://raras.org/doenca/cor-triatriatum
Formato APA. Conteúdo sob CC BY 4.0 — reuso livre com atribuição.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
Cor triatriatum
📋 Origem dos dados
Esta página agrega dados de fontes públicas e oficiais. Dados sobre cobertura no SUS (PCDT, CEAF) são verificados ativamente por agente proativo (ver badge no infobox). Demais dados têm atribuição de fonte + data da última sincronização — clique para abrir o original.
- Doença rara (ontologia)
- fonte: Orphanet
- Identificador unificado
- fonte: MONDO
- Codificação WHO/SUS
- fonte: WHO ICD-10 / DATASUS
- CID-11 (futuro)
- fonte: WHO ICD-11
- NIH/GARD
- fonte: GARD (NIH)
- Dado público estruturado
- fonte: Wikidata
