Em audiologia, perda auditiva periférica é um déficit auditivo de etiologia multifatorial que pode sofrer influência de fatores ambientais ou genéticos, que se manifesta em duas classificações principais, perda condutiva e perda neurosensorial, que tem como origem porções específicas do sistema audiorreceptor. Além disso, atualmente também adota-se a caracterização para a perda auditiva mista, perda auditiva funcional e por deficiência auditiva central.
Introdução
O que você precisa saber de cara
Malformação congênita rara das vias aéreas pulmonares, tipo 4, caracterizada por cistos múltiplos e difusos, frequentemente associados a anomalias vasculares e prognóstico reservado. Pode apresentar-se com dificuldade respiratória neonatal ou ser assintomática.
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Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Linha do tempo da pesquisa
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Genética e causas
O que está alterado no DNA e como passa nas famílias
Nenhum gene associado encontrado
Os dados genéticos desta condição ainda estão sendo catalogados.
Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
Remédios, cuidados de apoio e o que precisa acompanhar
Onde tratar no SUS
Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)
🇧🇷 Atendimento SUS — Malformação congênita das vias aéreas pulmonares, tipo 4
Centros de Referência SUS
24 centros habilitados pelo SUS para Malformação congênita das vias aéreas pulmonares, tipo 4
Centros para Malformação congênita das vias aéreas pulmonares, tipo 4
Detalhes dos centros
Hospital Universitário Prof. Edgard Santos (HUPES)
R. Dr. Augusto Viana, s/n - Canela, Salvador - BA, 40110-060 · CNES 0003808
Serviço de Referência
Hospital Infantil Albert Sabin
R. Tertuliano Sales, 544 - Vila União, Fortaleza - CE, 60410-794 · CNES 2407876
Serviço de Referência
Hospital de Apoio de Brasília (HAB)
AENW 3 Lote A Setor Noroeste - Plano Piloto, Brasília - DF, 70684-831 · CNES 0010456
Serviço de Referência
Hospital Estadual Infantil e Maternidade Alzir Bernardino Alves (HIABA)
Av. Min. Salgado Filho, 918 - Soteco, Vila Velha - ES, 29106-010 · CNES 6631207
Serviço de Referência
Hospital das Clínicas da UFG
Rua 235 QD. 68 Lote Área, Nº 285, s/nº - Setor Leste Universitário, Goiânia - GO, 74605-050 · CNES 2338424
Serviço de Referência
Hospital Universitário da UFJF
R. Catulo Breviglieri, Bairro - s/n - Santa Catarina, Juiz de Fora - MG, 36036-110 · CNES 2297442
Atenção Especializada
Hospital das Clínicas da UFMG
Av. Prof. Alfredo Balena, 110 - Santa Efigênia, Belo Horizonte - MG, 30130-100 · CNES 2280167
Serviço de Referência
Hospital Universitário Julio Müller (HUJM)
R. Luis Philippe Pereira Leite, s/n - Alvorada, Cuiabá - MT, 78048-902 · CNES 2726092
Atenção Especializada
Hospital Universitário João de Barros Barreto
R. dos Mundurucus, 4487 - Guamá, Belém - PA, 66073-000 · CNES 2337878
Serviço de Referência
Hospital Universitário Lauro Wanderley (HULW)
R. Tabeliao Estanislau Eloy, 585 - Castelo Branco, João Pessoa - PB, 58050-585 · CNES 0002470
Atenção Especializada
Instituto de Medicina Integral Prof. Fernando Figueira (IMIP)
R. dos Coelhos, 300 - Boa Vista, Recife - PE, 50070-902 · CNES 0000647
Serviço de Referência
Hospital Pequeno Príncipe
R. Des. Motta, 1070 - Água Verde, Curitiba - PR, 80250-060 · CNES 3143805
Serviço de Referência
Hospital Universitário Regional de Maringá (HUM)
Av. Mandacaru, 1590 - Parque das Laranjeiras, Maringá - PR, 87083-240 · CNES 2216108
Atenção Especializada
Hospital de Clínicas da UFPR
R. Gen. Carneiro, 181 - Alto da Glória, Curitiba - PR, 80060-900 · CNES 2364980
Serviço de Referência
Hospital Universitário Pedro Ernesto (HUPE-UERJ)
Blvd. 28 de Setembro, 77 - Vila Isabel, Rio de Janeiro - RJ, 20551-030 · CNES 2280221
Serviço de Referência
Instituto Nacional de Saúde da Mulher, da Criança e do Adolescente Fernandes Figueira (IFF/Fiocruz)
Av. Rui Barbosa, 716 - Flamengo, Rio de Janeiro - RJ, 22250-020 · CNES 2269988
Serviço de Referência
Hospital São Lucas da PUCRS
Av. Ipiranga, 6690 - Jardim Botânico, Porto Alegre - RS, 90610-000 · CNES 2232928
Serviço de Referência
Hospital de Clínicas de Porto Alegre (HCPA)
Rua Ramiro Barcelos, 2350 Bloco A - Av. Protásio Alves, 211 - Bloco B e C - Santa Cecília, Porto Alegre - RS, 90035-903 · CNES 2237601
Serviço de Referência
Hospital Universitário da UFSC (HU-UFSC)
R. Profa. Maria Flora Pausewang - Trindade, Florianópolis - SC, 88036-800 · CNES 2560356
Serviço de Referência
Hospital das Clínicas da FMUSP
R. Dr. Ovídio Pires de Campos, 225 - Cerqueira César, São Paulo - SP, 05403-010 · CNES 2077485
Serviço de Referência
Hospital de Base de São José do Rio Preto
Av. Brg. Faria Lima, 5544 - Vila Sao Jose, São José do Rio Preto - SP, 15090-000 · CNES 2079798
Atenção Especializada
Hospital de Clínicas da UNICAMP
R. Vital Brasil, 251 - Cidade Universitária, Campinas - SP, 13083-888 · CNES 2748223
Serviço de Referência
Hospital de Clínicas de Ribeirão Preto (HCRP-USP)
R. Ten. Catão Roxo, 3900 - Vila Monte Alegre, Ribeirão Preto - SP, 14015-010 · CNES 2082187
Serviço de Referência
UNIFESP / Hospital São Paulo
R. Napoleão de Barros, 715 - Vila Clementino, São Paulo - SP, 04024-002 · CNES 2688689
Serviço de Referência
Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.
Pesquisa ativa
Ensaios clínicos abertos e novidades científicas recentes
Pesquisa e ensaios clínicos
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Publicações mais relevantes
Mostrando amostra de 79 publicações de um total de 459
Pulmonary Malignancies in Adults With Congenital Lung Malformations: A Scoping Review.
We aimed to synthesize current knowledge on pulmonary malignancies in adults with congenital lung malformations (CLMs), focusing on clinical presentation, treatment approaches, and outcomes. We performed a scoping review according to the Preferred Reporting Items for Systematic Reviews and Meta-Analyses extension for scoping reviews. A systematic search was conducted in January 2025 across three databases. References were included if they described patients aged 17 years or older with a CLM and a coexisting pulmonary malignancy. Data were extracted on patient demographics, CLM and malignancy type, symptoms, treatment, and outcomes. Findings were summarized using descriptive statistics and narrative synthesis. A total of 65 references met the inclusion criteria, comprising 85 adult patients with CLM and pulmonary malignancies. Pulmonary adenocarcinoma was most frequently observed (66%), particularly within congenital pulmonary airway malformations (89% of malignancies in that subgroup). The median age at lung cancer diagnosis was 43.5 years. Respiratory symptoms were the most common presentation (67%), with 18% of patients being asymptomatic at the time of pulmonary malignancy diagnosis. Surgical resection was performed in 94% of patients, with lobectomy being the most frequently performed surgery type (68% of operated patients). More than half of malignancies (57%) were definitively diagnosed postoperatively. Follow-up data were incomplete; however, most reported patients were alive without disease recurrence at last follow-up with a median follow-up time of 14 months. The young median age at cancer diagnosis, the presence of pulmonary malignancies in asymptomatic patients, and the high proportion of malignancy diagnoses established only postoperatively underscore the need for proactive and tailored surveillance strategies in adults with known CLM. A multidisciplinary approach with longitudinal follow-up is crucial to refine risk assessment and optimize long-term care.
Challenges with Congenital Lung Cysts: When to Consider DICER1 Testing? A Narrative Review.
Congenital pulmonary airway malformations (CPAMs), according to the Stocker classification, comprise five types, two of which are non-cystic in nature (types 0 and 3) whereas the others present as cystic lung lesions (types 1, 2 and 4). While there is consensus that symptomatic lesions should be managed surgically, the asymptomatic cases are more problematic in terms of therapeutic intervention. The dilemma is further complicated by CPAM types 1 and 4 and their preneoplastic potential. In the case of CPAM type 1, there are reports of lipidic adenocarcinoma arising from the mucinous component. Type 4 has been equated to type I or cystic pleuropulmonary blastoma (PPB), a proposition that has been challenged in the past. Pleuropulmonary blastoma is associated with a heterozygous germline or somatic variants in DICER1. It was recognized that the earliest stage of the sarcomatous progression of PPB was a multicystic lesion in the periphery of the lung whose architectural features were identical to CPAM type 4. This narrative review addresses key aspects of the pathogenetic and diagnostic issues of type I PPB/CPAM type 4, as well as the association of DICER1 and PPB, offering valuable insights for pediatricians and clinicians caring for young adults who are impacted by the presence of a germline DICER1 variant.
Perioperative Care for Pediatric Patients Undergoing Lung Surgery: Retrospective Single Center Review.
Procedures involving lung surgery in the pediatric population are relatively uncommon and tend to be centralized in a limited number of institutions. Anesthesia literature is also sparse. To have a clear overview of frequency, underlying pathologies, ICU and hospital stay, anesthetic techniques, one lung ventilation, and perioperative analgesia. We conducted a retrospective review in a single-center tertiary hospital, from January 2014 to 2023. We included children aged 0-16 years who underwent major lung surgery and received anesthesia managed by the pediatric anesthesia team. Patients with congenital diaphragmatic hernia, esophageal atresia, or those undergoing surgery for pectus excavatum were excluded. Our main outcome measures include the type of underlying pathology and surgical procedure, ICU and hospital stay, methods of one-lung ventilation, source of perioperative analgesia, and the incidence of (postoperative) complications. We included 73 patients, 55% male and 45% female. The median age was 2.8 years and the median weight was 12.9 kg. Congenital pulmonary airway malformation was diagnosed in 43%, and 45% underwent a (partial) lobectomy. The proportion of video-assisted thoracoscopic surgery was comparable to that of open thoracotomy. One-lung ventilation (OLV) was used in 81%, primarily facilitated by a bronchial blocker. Epidural catheterization with ropivacaine for perioperative pain management was used in 71%. The proportion of patients receiving intravenous morphine on postoperative Days 1, 2, 3, 4, and 5 was 40%, 34%, 19%, 15%, and 11%, respectively. Insufficient pain control was reported in 14%. 70% were admitted to the ICU for one night. The average length of hospital stay was 8 days. We addressed the anesthetic care of pediatric lung surgery procedures. OLV was required in the majority of the population and a bronchial blocker was the preferred method. Epidural analgesia was the preferred choice to tackle perioperative pain.
Congenital Lung Malformations: A Comprehensive Overview of Current Knowledge-Narrative Review.
Congenital lung malformations (CLMs) encompass a range of developmental anomalies, including congenital pulmonary airway malformation (CPAM), bronchopulmonary sequestration (BPS), congenital lobar overinflation (CLO), bronchogenic cysts (BC), and bronchial atresia (BA). These lesions present with varying severity, from incidental findings to severe neonatal respiratory distress. Advances in prenatal imaging, such as ultrasound and fetal magnetic resonance image (MRI), have significantly improved early detection, aiding in better management planning. CLMs arise from abnormalities during specific stages of lung development. CPAMs are categorized by cyst size and histological type, while BPS is characterized by systemic arterial supply. CLO and BA are associated with air trapping and hyperinflation, and BCs are typically fluid-filled, well defined, and compressive. Postnatal diagnosis is based on high-resolution computed tomography (CT) and occasionally MRI for detailed evaluation. Surgical resection is recommended for symptomatic lesions, while management of asymptomatic cases remains debated. Elective surgery may help prevent complications like infection or rare malignancy, particularly in CPAM Types 1 and 4 and BCs. However, some lesions remain stable or regress, supporting conservative management in selected cases. Long-term outcomes are generally positive, with children undergoing early resection often maintaining good lung function due to compensatory lung growth, though subtle functional deficits may persist. Risk stratification using imaging and genetic markers, such as DICER1 mutations, is gaining importance for guiding treatment decisions. Management should be individualized, involving a multidisciplinary approach and shared decision-making with families. Further research is needed to clarify the natural history of CLMs, optimize the timing of interventions, and standardize long-term surveillance strategies.
Congenital Pulmonary Hybrid Lesions: Clinical Presentation, Surgical Management, and Outcomes.
Congenital pulmonary airway malformation (CPAM) lesion with an aberrant systemic blood supply is considered a "hybrid" lesion (HL). The aim of the study was to report authors' experience in the presentation, surgical management, and outcomes of HL. A retrospective cohort study of HL patients followed from 2000 to 2022 in a single institution was done. Clinical and radiographic data were collected from the medical records. Over the study period, 39 patients with HL were identified. HL with CPAM type 2 was more common than type 1 (74% vs. 26%), and intralobar sequestrations were more prevalent than extralobar sequestrations (ELS) (79.5% vs. 20.5%). HL with CPAM type 2 had higher rates of co-morbidities and higher likelihood to present with respiratory symptoms after birth. HL with ELS had smaller feeding vessels (all < 4 mm) which resulted in lower rates of open thoracotomy approach for resection. The variability in HL patient presentation and outcomes is correlated with the size and the hybrid composition.
Publicações recentes
Rising detection of congenital pulmonary airway malformations and a pragmatic institutional algorithm: a four-patient thoracoscopic case series.
Delayed surgical management of extensive bilateral multilobar congenital pulmonary airway malformation.
🥉 Relato de casoLobectomy vs. sublobar resection for congenital pulmonary airway malformations: a 10-year NSQIP-pediatric review.
Congenital pulmonary airway malformation or pulmonary sequestration with ipsilateral foregut cyst-inevitable association or coincidence?
Diagnostic Challenges in a Hybrid Congenital Pulmonary Airway Malformation: A Case Report.
📚 EuropePMC253 artigos no totalmostrando 79
Pulmonary Malignancies in Adults With Congenital Lung Malformations: A Scoping Review.
JTO clinical and research reportsChallenges with Congenital Lung Cysts: When to Consider DICER1 Testing? A Narrative Review.
Acta medica portuguesaPerioperative Care for Pediatric Patients Undergoing Lung Surgery: Retrospective Single Center Review.
Paediatric anaesthesiaLaser therapy for type III fetal congenital cystic adenomatoid malformation.
Ceska gynekologieCongenital Lung Malformations: A Comprehensive Overview of Current Knowledge-Narrative Review.
Archivos de bronconeumologiaType III Congenital Pulmonary Airway Malformation: A Case Report.
Iranian journal of pathologyType 2 Congenital Pulmonary Airway Malformation in Tetralogy of Fallot with Absent Pulmonary Valve Syndrome.
The Indian journal of radiology & imagingMultiple congenital pulmonary malformations in a black-capped Bolivian squirrel monkey (Saimiri boliviensis boliviensis).
Journal of comparative pathologyComputed tomography (CT)-based classification and management pathways for hybrid lesions in children: a comparative analysis of congenital pulmonary airway malformation (CPAM) and bronchopulmonary sequestration (BPS).
Clinical radiologyCongenital Pulmonary Airway Malformations: Experience of a Tunisian Tertiary Referral Center Over a Five-Year Period.
Pediatric pulmonologyCongenital Pulmonary Airway Malformation with Pulmonary Arteriovenous Malformation in Adulthood: A Case Report.
Surgical case reportsCongenital lung malformations: Do preoperative symptoms have an impact in surgical outcomes?
Anales de pediatriaCharacterization of 45 cases of congenital lung malformation and association of inflammation with symptomatology.
Scientific reportsNeonatal Surgery for Congenital Lung Malformations: Indications, Outcomes and Association With Malignancy.
Journal of pediatric surgeryCongenital Pulmonary Hybrid Lesions: Clinical Presentation, Surgical Management, and Outcomes.
Indian journal of pediatrics[Clinical and morphological characteristics of lung sequestration].
Arkhiv patologiiThe ten-year evaluation of clinical characteristics in congenital lung anomaly in pediatrics; a retrospective study in North of Iran.
BMC pediatricsComplicated Congenital Pulmonary Adenomatoid Malformation Type I following Right Lower Lobectomy: A Case Report.
JNMA; journal of the Nepal Medical Association[Clinicopathological and genetic characteristics of congenital cystic adenomatoid malformation of lung and its associated lung cancer in adults].
Zhonghua bing li xue za zhi = Chinese journal of pathologyExperience of video-assisted thoracic surgery treatment of congenital pulmonary airway malformation in infants less than 3 months of age.
Translational pediatricsThe Effect of Steroids on Prenatally Diagnosed Lung Lesions.
Journal of pediatric surgeryInfantile type I pleuropulmonary blastoma presenting with dyspnea due to compression by pneumothorax and an occupying tumor: a case report.
Surgical case reportsPrenatal Array-CGH Detection of 3q26.32q26.33 Interstitial Deletion Encompassing the SOX2 Gene: Ultrasound, Pathological, and Cytogenetic Findings.
Fetal and pediatric pathologyCongenital pulmonary malformations in children in a pediatric hospital in Peru, 2010-2020.
Boletin medico del Hospital Infantil de MexicoA pleuropulmonary blastoma type III in a 4-month-old infant: First case report in Syria.
International journal of surgery case reportsCongenital pulmonary airway malformation manifesting with severe respiratory distress and pneumothorax in a neonate.
Indian journal of thoracic and cardiovascular surgeryCongenital Pulmonary Airway Malformations With a Reconsideration and Current Perspective on the Stocker Classification.
Pediatric and developmental pathology : the official journal of the Society for Pediatric Pathology and the Paediatric Pathology SocietyCongenital pleuropulmonary blastoma in a newborn with a variant of uncertain significance in DICER1 evaluated by RNA-sequencing.
Maternal health, neonatology and perinatologyThe Role of Bone Morphogenetic Protein 4 in Lung Diseases.
Current molecular medicineThe long-term outcome following thoraco-amniotic shunting for congenital lung malformations.
Journal of pediatric surgeryType II congenital pulmonary airway malformation with primary ciliary dyskinesia in a 4-year-old child: A case report.
Pediatric pulmonologyCongenital cystic adenomatoid malformations of the lung: a retrospective study of diagnosis, treatment strategy and postoperative morbidity in surgically treated patients.
European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic SurgeryModified thoracoscopic wedge resection of limited peripheral lesions in S10 for children with congenital pulmonary airway malformation: Initial single-center experience.
Frontiers in pediatricsThoracoscopic segmentectomy for congenital pulmonary airway malformation arising in a lung with an accessory fissure: A case report.
Asian journal of endoscopic surgeryVascular Anatomy in Congenital Lung Lesions-Description and Classification.
Frontiers in pediatricsAtypical Antenatal Presentation of an Unusual Nonmucinous Papillary Variant of Giant Congenital Pulmonary Airway Malformation Masquerading as Congenital Diaphragmatic Hernia with Volvulus.
Journal of medical ultrasound18FDG PET-Positive Congenital Pulmonary Airway Malformation Mimicking Lung Cancer.
Clinical nuclear medicineNeonatal congenital pulmonary airway malformation associated with mucinous adenocarcinoma and KRAS mutations.
Journal of pediatric surgeryCongenital Pulmonary Airway Malformation - A Histomorphological Spectrum of 15 Cases: A 5-Year Study from a Tertiary Care Center.
Journal of Indian Association of Pediatric SurgeonsCongenital pulmonary airway malformation (cpam) mimicking an spontaneous pneumothorax in a newborn.
Cirugia pediatrica : organo oficial de la Sociedad Espanola de Cirugia PediatricaAn adult with episodic retrosternal chest pain: an unusual presentation of congenital pulmonary airway malformation - case report.
Journal of cardiothoracic surgeryMucinous Adenocarcinoma With Intrapulmonary Metastasis Harboring KRAS and GNAS Mutations Arising in Congenital Pulmonary Airway Malformation.
American journal of clinical pathologySingle-cell transcriptome profiling reveals the mechanism of abnormal proliferation of epithelial cells in congenital cystic adenomatoid malformation.
Experimental cell researchMucinous adenocarcinoma arising in congenital pulmonary airway malformation: clinicopathological analysis of 37 cases.
HistopathologyThoracoscopic Resection in the Treatment of Spontaneous Pneumothorax.
Sisli Etfal Hastanesi tip bulteniPleuropulmonary blastoma type I and congenital pulmonary airway malformation type 4: distinct entities or sides of the same coin?
Virchows Archiv : an international journal of pathologyComputed tomography features can distinguish type 4 congenital pulmonary airway malformation from other cystic congenital pulmonary airway malformations.
European journal of radiologyPleuropulmonary blastoma type I might arise in congenital pulmonary airway malformation type 4 by acquiring a Dicer 1 mutation.
Virchows Archiv : an international journal of pathologyAnalysis of Wnt7B and BMP4 expression patterns in congenital pulmonary airway malformation.
Pediatric pulmonologyCongenital Cystic Adenomatoid Malformation of the Lung Tipe II: Three Cases Report.
Translational medicine @ UniSaObstetric and neonatal outcomes in pregnancies complicated by fetal lung masses: does final histology matter?
The journal of maternal-fetal & neonatal medicine : the official journal of the European Association of Perinatal Medicine, the Federation of Asia and Oceania Perinatal Societies, the International Society of Perinatal ObstetriciansType I pleuropulmonary blastoma presenting as congenital pulmonary airway malformation: A report of two cases.
Indian journal of pathology & microbiologyValue of routine ultrasound examination at 35-37 weeks' gestation in diagnosis of fetal abnormalities.
Ultrasound in obstetrics & gynecology : the official journal of the International Society of Ultrasound in Obstetrics and GynecologyCongenital Cystic Adenomatoid Malformation Volume Ratio in Prenatal Assessment of Prognosis of Fetal Pulmonary Sequestrations.
Current medical scienceEsophageal duplication cyst presenting with stridor in a child with congenital pulmonary airway malformation: A case report and literature review.
MedicineCystic and pseudocystic pulmonary malformations in children: Clinico-pathological correlation.
Annals of diagnostic pathologyEarly vs late resection of asymptomatic congenital lung malformations.
Journal of pediatric surgeryFetal Congenital Peripheral Bronchial Atresia Diagnosed by Magnetic Resonance Imaging: Two Case Reports.
AJP reportsAn investigation on clinical differences between congenital pulmonary airway malformation and bronchial atresia.
Journal of pediatric surgery[Pulmonary lobectomy in children: the sooner the better?].
Cirugia pediatrica : organo oficial de la Sociedad Espanola de Cirugia PediatricaCongenital cystic adenomatoid malformation - diagnostic and therapeutic procedure: 8-year experience of one medical centre.
Kardiochirurgia i torakochirurgia polska = Polish journal of cardio-thoracic surgeryTypes II and III congenital pulmonary airway malformation with hydrops treated in utero with percutaneous sclerotherapy.
Prenatal diagnosis[Pulmonary sequestration associated with congenital pulmonary airway malformation].
Boletin medico del Hospital Infantil de MexicoCongenital pulmonary airway malformations: state-of-the-art review for pediatrician's use.
European journal of pediatricsAn Atypical Presentation of Congenital Pulmonary Airway Malformation (CPAM): A Rare Case with Antenatal Ultrasound Findings and Review of Literature.
Polish journal of radiologyCongenital Cystic Adenomatoid Malformation: A Tertiary Care Hospital Experience.
Journal of clinical and diagnostic research : JCDRAssociation between Congenital Lung Malformations and Lung Tumors in Children and Adults: A Systematic Review.
Journal of thoracic oncology : official publication of the International Association for the Study of Lung CancerPulmonary Kirsten Rat Sarcoma Virus Mutation Positive Mucinous Adenocarcinoma Arising in a Congenital Pulmonary Airway Malformation, Mixed Type 1 and 2.
The Annals of thoracic surgeryOutcome of infants operated on for congenital pulmonary malformations.
Pediatric pulmonologyFetal MRI as Complementary Study of Congenital Cystic Adenomatoid Malformation During Pregnancy: A Single Case Report.
CureusPulmonary Arteriovenous Fistula: Clinical and Histologic Spectrum of Four Cases.
Journal of pathology and translational medicineRetrospective Evaluation of Children with Congenital Pulmonary Airway Malformation: A Single Center Experience of 20 Years.
Fetal and pediatric pathologyNasoethmoidal meningocele in a child presenting bilateral congenital cystic adenomatoid malformation: Evidence for a new entity or consequence of gestational exposures?
Birth defects research. Part A, Clinical and molecular teratology[Pediatric lung lesions: a clinicopathological study of 215 cases].
Zhonghua bing li xue za zhi = Chinese journal of pathologyCan congenital pulmonary airway malformation be distinguished from Type I pleuropulmonary blastoma based on clinical and radiological features?
Journal of pediatric surgeryCongenital Pulmonary Airway Malformation in an Adult Male: A Case Report with Literature Review.
Case reports in pulmonologyExtralobar sequestration of lung associated with congenital diaphragmatic hernia and malrotation of gut.
Lung India : official organ of Indian Chest Society[Congenital pulmonary airway malformation of lung in fetus: a clinicopathological analysis].
Zhonghua bing li xue za zhi = Chinese journal of pathologySurgical management of bronchopulmonary malformations.
The Journal of surgical researchAssociações
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Pulmonary Malignancies in Adults With Congenital Lung Malformations: A Scoping Review.
- Challenges with Congenital Lung Cysts: When to Consider DICER1 Testing? A Narrative Review.
- Perioperative Care for Pediatric Patients Undergoing Lung Surgery: Retrospective Single Center Review.
- Congenital Lung Malformations: A Comprehensive Overview of Current Knowledge-Narrative Review.
- Congenital Pulmonary Hybrid Lesions: Clinical Presentation, Surgical Management, and Outcomes.
- Rising detection of congenital pulmonary airway malformations and a pragmatic institutional algorithm: a four-patient thoracoscopic case series.
- Delayed surgical management of extensive bilateral multilobar congenital pulmonary airway malformation.
- Lobectomy vs. sublobar resection for congenital pulmonary airway malformations: a 10-year NSQIP-pediatric review.
- Congenital pulmonary airway malformation or pulmonary sequestration with ipsilateral foregut cyst-inevitable association or coincidence?
- Diagnostic Challenges in a Hybrid Congenital Pulmonary Airway Malformation: A Case Report.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:280854(Orphanet)
- MONDO:0017252(MONDO)
- GARD:21097(GARD (NIH))
- Busca completa no PubMed(PubMed)
- Q55786940(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
