Raras
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Pancreatite autoimune
ORPHA:103919CID-11 · DC33DOENÇA RARA

Pancreatite é a inflamação do pâncreas. O pâncreas é um órgão volumoso na parte posterior do estômago que produz enzimas digestivas e uma série de hormonas. Existem dois tipos principais: pancreatite aguda e pancreatite crónica. Os sinais e sintomas de pancreatite mais comuns são dor na parte superior do abdómen, náuseas e vómitos. Em muitos casos a dor espalha-se para as costas e é geralmente muito intensa. Na pancreatite aguda, pode ocorrer febre e os sintomas geralmente desaparecem ao fim de alguns dias.

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Introdução

O que você precisa saber de cara

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Doença inflamatória crônica do pâncreas, onde o sistema imunológico ataca o órgão. Pode causar dor abdominal, icterícia e perda de peso, mimetizando câncer de pâncreas.

Pesquisas ativas
4 ensaios
27 total registrados no ClinicalTrials.gov
Publicações científicas
2.950 artigos
Último publicado: 2026 Apr 16
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SUS: Sem cobertura SUSScore: 0%
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Anos de pesquisa1desde 2026
Total histórico2.950PubMed
Últimos 10 anos200publicações
Pico2025151 papers
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2026Hoje · 2026🧪 2002Primeiro ensaio clínico📈 2025Ano de pico
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Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

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27 ensaios clínicos encontrados, 4 ativos.

Distribuição por fase
NCT07536841 · Ambispective Validation of the Odesa Criteria 2026 (OC26): A…Em breve
NCT06753318 · Validation of Joint-AI in Diagnosing Pancreatic Solid Lesion…Em breve
NA
NCT06358001 · EchoTip AcuCore Post-Market Clinical StudyConcluído
NCT04834505 · To Differentiate Focal Autoimmune Pancreatitis From Pancreat…Concluído
NCT04397731 · Prospective Study on the Role of Eus-fnb in the Diagnosis of…Concluído
NCT06699667 · CT Findings in Surgically Treated Focal Pancreatic Disease- …Concluído
NCT05476978 · Artificial Intelligence in EUS for Diagnosing Pancreatic Sol…Concluído
NCT06328101 · Autoimmune Pancreatitis, Pancreatic and Extrapancreatic cAnc…UNKNOWN
NCT05171517 · Study on Microflora Characteristics of Pancreatic Solid Lesi…Concluído
NCT05565066 · A Real-world Comparison of FNB and FNA in IHC-required Lesio…Concluído
NCT05095831 · EUS Shear Wave for Solid Pancreatic Lesions.UNKNOWN
NCT03753815 · Diagnostic Yield of FNA Needle and FNB Needle for Autoimmune…UNKNOWN
NA
NCT02797665 · Treatment of Obstructive Jaundice in Autoimmune Pancreatitis…UNKNOWN
NA
NCT02705638 · Treatment of IgG4-Related Disease With Revlimid and Rituxima…Concluído
PHASE1
NCT01845467 · Efficacy of Secretin MRCP in the Diagnosis and Follow up of …Cancelado
NCT03241797 · Evaluation of EUS-guided FNA for Diagnosing Autoimmune Pancr…Concluído
NA
NCT01584388 · Rituximab in IgG4-RD: A Phase 1-2 TrialConcluído
PHASE1, PHASE2
NCT02766842 · Evaluation of a New EUS Guided Biopsy Needle (SharkCore) Com…Cancelado
PHASE2
Ver todos no ClinicalTrials.gov
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Publicações mais relevantes

Timeline de publicações
1.505 papers (10 anos)

Mostrando amostra de 200 publicações de um total de 1.505

#1

Clinicopathological features of localized-type IgG4-related cholecystitis: a nationwide multicenter study in Japan.

Journal of gastroenterology2026 Feb 25

Immunoglobulin G4 (IgG4)-related cholecystitis represents gallbladder involvement in IgG4-related disease (IgG4-RD). However, localized-type IgG4-related cholecystitis is rare and remains poorly characterized. We conducted a nationwide, multicenter study to clarify the clinicopathological features of localized-type IgG4-related cholecystitis in Japan. We collected clinical information, imaging data, and tissue slides from suspected cases of IgG4-related cholecystitis for central review, and evaluated their clinicopathological features. Fifteen patients were diagnosed with localized-type IgG4-related cholecystitis. The incidence of localized-type IgG4-related cholecystitis was 0.59% (15/2560) among all IgG4-related gastroenterological diseases across 30 institutions. The median age was 62 years (range, 54-70 years), and 10 patients were men. Elevated serum IgG4 levels and other IgG4-RD lesions were observed in all 15 patients. Imaging findings demonstrated subepithelial lesions (SELs) of the gallbladder in all patients, and cystic lesions within SELs suggestive of adenomyomatosis (ADM) in nine patients. Among the 11 patients with available histopathological analyses, two distinct types of mass-forming lesions (inflammatory pseudotumors) characterized by storiform fibrosis and obliterative phlebitis were identified: ADM-type in six cases and mural hypertrophy-type in three cases. Eleven patients underwent surgery and four received glucocorticoids therapy. Within 2-4 weeks of initiating glucocorticoid therapy, complete resolution was achieved in one patient, and partial improvement in three patients. Localized-type IgG4-related cholecystitis is characterized by imaging findings of SELs. It shares histopathological features of IgG4-RD, and often has unique lesions centered around ADM. It responds to glucocorticoid therapy.

#2

Multicenter Validation Study of the Clinical Diagnostic Criteria for IgG4-Related Sclerosing Cholangitis 2020 in Japan.

Journal of hepato-biliary-pancreatic sciences2026 Jan 07

The diagnostic performance of clinical diagnostic criteria for IgG4-related sclerosing cholangitis 2020 (IgG4-SC2020) has not been fully validated since its proposal as a revision of the 2012 criteria (IgG4-SC2012). We conducted a multicenter validation study to evaluate the diagnostic performance of IgG4-SC2020 using clinical data collected from 1034 patients with IgG4-SC and 447 patients with mimickers, including 143 with pancreatic cancer, 157 with primary sclerosing cholangitis, and 147 with cholangiocarcinoma in Japan. The sensitivity of IgG4-SC2020 was significantly higher than that of IgG4-SC2012 (99.0% vs. 89.1%; p < 0.001). The specificities of both IgG4-SC2020 and IgG4-SC2012 were 100% for pancreatic cancer and cholangiocarcinoma. For primary sclerosing cholangitis, the specificities of IgG4-SC2020 and IgG4-SC2012 were 97.5% and 100%, respectively, with no significant difference (p = 0.123). A total of 113 patients who could not be diagnosed according to the IgG4-SC2012 were successfully diagnosed using IgG4-SC2020. These diagnostic improvements were attributed to the inclusion of MRCP findings (n = 97), the absence of neoplastic cells on histology (n = 15), and the presence of IgG4-related kidney lesions (n = 1). This Japanese multicenter validation study demonstrated that the diagnostic performance of IgG4-SC2020 was superior to that of IgG4-SC2012. UMIN Clinical Trials Registry (UMIN-CTR), UMIN000052984.

#3

Clinical features, responses to therapy and prognosis of 107 patients with IgG4-related cholangitis: a retrospective study.

BMC gastroenterology2026 Jan 07

IgG4-related cholangitis (IRC) is an important hepatobiliary manifestation of IgG4-related diseases (IRD), frequently accompanied by other organ involvement of IRD especially autoimmune pancreatitis (AIP). Diagnosis of IRC requires comprehensive evaluation. The patients respond well to glucocorticosteroids and have good long-term prognosis regardless of relapse. This retrospective observational study described the clinical features, responses to therapy and prognosis of patients with IRC. The aim of our study was to describe and analyze the clinical features, responses to treatment and prognosis of 107 patients with IRC at our hospital, exploring the difficulties and clinical experience in the diagnosis and treatment of IRC. We conducted a retrospective study of 107 patients with IRC (88 males and 19 females; mean age, 60.8 years) treated at Peking Union Medical College Hospital between January 2013 and April 2023. Data on demographic, clinical, serologic, pathologic and imaging characteristics as well as treatment responses and prognosis were collected and analyzed. Statistical Package for Social Sciences software (SPSS, version 25.0) and Python (version 3.11) were used for the data analysis. Survival was assessed using Kaplan–Meier curves. Univariate and multivariate logistic regression analysis was used to analyze risk factors of relapse. A two-sided probability P < 0.05 was considered statistically significant. Receiver operating characteristic (ROC) curve was used to predict the value of steroid maintenance duration for relapse. The most common symptoms at presentation were jaundice (76.6%) and weight loss (72.9%). AIP was the most prevalent comorbidity (96.3%). Serum IgG4 levels were elevated in 99% of the patients, and isolated stenosis of the lower part of the common bile duct (type 1 IRC) was the most common imaging finding (49.5%). Nearly 90% of the patients were treated with steroids, and all presented with an excellent response. A relapse rate of 37.5% was observed during the follow-up period, most of which occurred after steroid withdrawal (47.2%). Steroid maintenance duration was the significant independent risk factor of relapse in patients with IRC (P = 0.001) (odds ratio, 0.875; 95% CI, 0.811–0.944). The patients were followed up for a median of 63.8 months. Four patients (4.0%) died, and none of them had cholangiocarcinoma. Overall 5-year and 10-year survival rates were 97.0% and 96.0%, respectively. The disease-specific survival rate was 100%. Among the 107 patients examined, IRC was found to be benign and exhibited an excellent response to steroid treatment. No patient progressed to cholangiocarcinoma, and relapse had no impact on the overall survival rate. The online version contains supplementary material available at 10.1186/s12876-025-04598-0.

#4

Metachronic development of cholangiocarcinoma during treatment for IgG4-related sclerosing cholangitis.

Clinical journal of gastroenterology2026 Feb

We report a case of obstructive jaundice due to recurrent distal biliary stricture during 3 years of treatment for immunoglobulin G4 (IgG4)-related sclerosing cholangitis (IgG4-SC) associated with autoimmune pancreatitis. Although a relapse of IgG4-SC was initially suspected, imaging findings, laboratory tests, and histopathological examinations led to the diagnosis of metachronous cholangiocarcinoma. The patient underwent pancreaticoduodenectomy, and no cancer recurrence was noted 6 months postoperatively. Distal cholangiocarcinoma and IgG4-SC remission were observed in the resected specimen. In patients with recurrent biliary strictures during IgG4-SC treatment, comprehensive evaluations are essential because of the risk of disease relapse and development of metachronous cholangiocarcinoma.

#5

Peripancreatic Vascular Involvement and Gastric Varices in Autoimmune Pancreatitis: A Multicenter Retrospective Study.

Clinical gastroenterology and hepatology : the official clinical practice journal of the American Gastroenterological Association2026 Apr

Autoimmune pancreatitis (AIP) could induce peripancreatic vascular involvement, such as portal system stenosis, through inflammatory extension, resulting in the development of collateral vessels. In severe cases, gastric varices may develop, leading to a life-threatening risk of variceal rupture. However, these complications remain underrecognized and are not explicitly addressed in the current clinical guidelines. This study aimed to evaluate the frequency of vascular involvement in AIP, assess therapeutic effects of glucocorticoids, and identify key vessels associated with gastric varices. This multicenter retrospective study included 230 patients diagnosed with AIP at 17 institutions in Japan between 2010 and 2021. We analyzed clinical data, contrast-enhanced computed tomography images, and endoscopy findings. All images were evaluated individually by 3 professionals at a central facility. The primary outcome was the frequency of peripancreatic vascular involvement. At diagnosis, 51.3% of the patients exhibited peripancreatic vascular involvement, primarily in the splenic vein (48.3%), superior mesenteric vein (23.9%), and portal vein (9.6%). Collateral vessel formation was observed in 40.0% of patients, with 24.3% being severe; 2 gastric variceal ruptures occurred prior to therapy. Glucocorticoid therapy significantly improved venous stenosis (response rates: 95.6%, 93.8%, and 93.1% in the splenic, portal, and superior mesenteric veins, respectively). Additionally, 80.9% of patients exhibited collateral vessel improvement. Among 55 patients who underwent upper endoscopy, 10.9% had gastric varices strongly associated with severe splenic vein stenosis. Peripancreatic vascular involvement represents a common complication of AIP and significantly responds to glucocorticoid therapy, underscoring the importance of careful monitoring to prevent potentially fatal outcomes.

Publicações recentes

Ver todas no PubMed

📚 EuropePMC1.892 artigos no totalmostrando 195

2026

Elevated CA19-9 in IgG4-Related Autoimmune Pancreatitis: A Single-Center Retrospective Cohort Study.

International journal of general medicine
2026

Type 1 Autoimmune Pancreatitis with Associated Ulcerative Colitis in a 65-year-old Male.

Digestive diseases and sciences
2025

Case Report: jaundice in the young: the complexity of rare diseases beyond cholangiopathies.

Frontiers in gastroenterology (Lausanne, Switzerland)
2026

Clinico-pathological and immunohistochemical profile of plasma cell rich variants of chronic cholecystitis.

Annals of diagnostic pathology
2026

Endoscopic retrograde biliary drainage plus glucocorticoids versus glucocorticoid alone for autoimmune pancreatitis with significant obstructive jaundice: study protocol for a multicenter, open-label, non-inferiority randomized controlled trial.

Trials
2026

Effectiveness and Safety of Immunosuppressive Therapy in Recurrent Autoimmune Pancreatitis.

Internal medicine (Tokyo, Japan)
2026

Clinicopathological features of localized-type IgG4-related cholecystitis: a nationwide multicenter study in Japan.

Journal of gastroenterology
2026

Type 1 autoimmune pancreatitis: clinical features and independent predictors of histopathological confirmation via EUS-guided fine-needle aspiration/fine-needle biopsy.

BMC gastroenterology
2026

A Systematic Review of Erdheim-Chester Disease and IgG4-Related Disease: Building a Diagnostic Framework for the Rheumatologist.

Journal of clinical rheumatology : practical reports on rheumatic &amp; musculoskeletal diseases
2026

IgG4-related sclerosing cholangitis: navigating diagnostic dilemmas and the challenge of relapse.

Frontiers in medicine
2026

Simultaneous improvement of immunoglobulin G4-related disease complicated by nontuberculous mycobacteria infection by anti-infective therapy alone: a case-based literature review.

Rheumatology international
2026

A rare case of pediatric autoimmune pancreatitis and autoimmune hepatitis in a patient with sickle cell disease.

JPGN reports
2026

Diagnostic Challenges in Autoimmune Pancreatitis: A Case of Progressive Painless Jaundice With an Uncertain Etiology.

Cureus
2026

Development and validation of a clinical-radiomics nomogram for the differential diagnosis of focal pancreatic solid lesions: a retrospective cohort study.

Translational cancer research
2026

Hypertransaminasemia in a Patient with Acute Abdominal Pain: An Unusual Case Report.

European journal of case reports in internal medicine
2026

Diagnosis and treatment strategies for autoimmune pancreatitis combined with pancreatic neuroendocrine tumors.

World journal of surgical oncology
2026

Cutaneous Lesions of IgG4-related Disease.

Internal medicine (Tokyo, Japan)
2026

Lobularity in Autoimmune Pancreatitis Was A Steroid-Therapy Responding Endoscopic Ultrasound Finding.

The Kurume medical journal
2025

Case Report: IgG4-RD-related autoimmune pancreatitis combined with monoclonal gammopathy of undetermined significance.

Frontiers in immunology
2026

Bifidobacterium Infantis Promotes FOSL1-Mediated Transcriptional Repression of VDR to Accelerate Autoimmune Pancreatitis Progression Through Activation of Oxidative Stress.

Inflammation
2026

Clinical characteristics, disease course, and chronic organ damage in a real-world cohort of IgG4-related disease: Insights from an Interdisciplinary Unit.

Medicina clinica
2026

Immunoglobulin G4-related disease with multi-organ involvement: A case report.

Medicine
2026

A Case of Multiple Metastases in the Gastric Wall Due to Needle Tract Seeding after Endoscopic Ultrasound-Guided Tissue Acquisition for Pancreatic Tail Cancer.

Surgical case reports
2026

Steroid-Resistant Relapse of Autoimmune Pancreatitis with Marked Main Pancreatic Duct Dilatation Mimicking Multifocal Pancreatic Cancer.

Internal medicine (Tokyo, Japan)
2025

IgG4 Pancreatitis Presenting as a Mass: Unraveling a Diagnostic Illusion.

Cureus
2025

A Case of Thiazide-Induced Pancreatitis.

Cureus
2026

[Rational diagnostics and differential diagnosis in IgG4-related disease].

Zeitschrift fur Rheumatologie
2026

Multicenter Validation Study of the Clinical Diagnostic Criteria for IgG4-Related Sclerosing Cholangitis 2020 in Japan.

Journal of hepato-biliary-pancreatic sciences
2026

Clinical features, responses to therapy and prognosis of 107 patients with IgG4-related cholangitis: a retrospective study.

BMC gastroenterology
2025

Auto-Immune Pancreatitis with Pseudo-Tumoral Mass Induced by Pembrolizumab in a Woman suffering from Metastatic Urothelial Carcinoma: Case Report and Literature survey.

Acta gastro-enterologica Belgica
2025

Roles of chemokines in pancreatitis: A review.

World journal of gastrointestinal pathophysiology
2025

Advances in endoscopic ultrasound-guided shear wave elastography: A comprehensive review of its clinical applications.

World journal of gastroenterology
2025

Diagnostic challenge of autoimmune pancreatitis in children: Utility of endoscopic ultrasound-guided biopsy.

Revista de gastroenterologia de Mexico (English)
2025

Ophthalmological Findings in Cases of Autoimmune Pancreatitis: Changes in Long-term Corticosteroid Therapy.

Journal of gastrointestinal and liver diseases : JGLD
2025

Tumor-associated Pancreatitis Mimicking Autoimmune Pancreatitis in a Young Male: A Case of Main Duct IPMC.

Internal medicine (Tokyo, Japan)
2026

18 F-FAPI-42 PET/CT Finding in a Patient With Pancreatic Ductal Adenocarcinoma Encapsulated by Immunoglobulin G4-related Autoimmune Pancreatitis Located at the Pancreatic Body.

Clinical nuclear medicine
2025

Diffuse Intense Pancreatic Uptake on 99mTc-HYNIC-TOC SPECT/CT in a Rare Case of Diffuse Pancreatic Neuroendocrine Tumor.

Clinical nuclear medicine
2025

IgG4-Related Disease in Urological Practice: A Case Series of Mistaken Malignancies.

Indian journal of surgical oncology
2025

A Rare Case of Multifocal Autoimmune Pancreatitis.

Clinical gastroenterology and hepatology : the official clinical practice journal of the American Gastroenterological Association
2026

Type 1 Autoimmune Pancreatitis in a Teenager With Ulcerative Colitis: A Case Report.

Gastro hep advances
2025

The Diagnostic and Follow-Up Value of Contrast-Enhanced Ultrasound of IgG4-Associated Hepatic Inflammatory Pseudotumor: A Case Report and Review.

Journal of clinical ultrasound : JCU
2025

Pancreatic fallout: autoimmune pancreatitis post-mRNA COVID-19 vaccination.

The New Zealand medical journal
2026

GLP-1 agonists-induced autoimmune pancreatitis.

Drug and therapeutics bulletin
2025

IgG4-Related disease: From diagnosis to remission.

Best practice &amp; research. Clinical rheumatology
2025

Necrotising Pancreatitis in a Patient with Crest Syndrome: A Rare Autoimmune Gastrointestinal Complication.

European journal of case reports in internal medicine
2025

High vs. Low Initial Steroid Dose in Autoimmune Pancreatitis: Multicenter Cohort Study on Efficacy and Diabetes Worsening.

Diagnostics (Basel, Switzerland)
2025

Association between age groups and relapse of type 1 autoimmune pancreatitis: a large-scale retrospective cohort study.

Journal of autoimmunity
2025

Diagnostic delay in type I autoimmune pancreatitis: clinical, imaging, endoscopic and histologic predictors of timely diagnosis.

Translational gastroenterology and hepatology
2025

Endoscopic Ultrasound With Fine Needle Biopsy Confirming a Diagnosis of Immune Checkpoint Inhibitor-Related Type 3 Autoimmune Pancreatitis.

Case reports in gastrointestinal medicine
2025

The dual role of endoscopic ultrasonography in the diagnosis and treatment of autoimmune pancreatitis with gastric variceal bleeding: A case report and literature review.

The Journal of international medical research
2026

Endoscopic Ultrasound-guided Fine-Needle Biopsy With End-Cutting Needles in Autoimmune Pancreatitis: A Systematic Review and Meta-Analysis.

DEN open
2026

IgG4-related disease: findings from a retrospective cohort in Colombia.

Reumatismo
2025

Single-cell multi-omics analysis revealed the expansion of age-associated B cells in the pancreas of type 1 autoimmune pancreatitis patients.

Genome medicine
2025

[Type 2 autoimmune pancreatitis: a clinicopathological analysis].

Zhonghua bing li xue za zhi = Chinese journal of pathology
2025

CT findings in surgically treated focal pancreatic disease - a retrospective study.

Annals of medicine and surgery (2012)
2025

EXTRA-PANCREATIC MANIFESTATION IN AUTOIMMUNE PANCREATITIS VERSUS CONVENTIONAL PANCREATITIS: AN EGYPTIAN COHORT.

Arquivos de gastroenterologia
2025

Bach2-deficient mice are prone to autoimmune pancreatitis but protected from high-fat diet-induced fatty liver disease.

Frontiers in immunology
2025

Roles of Deubiquitinases OTUD3 and OTUD5 in Inflammatory Bowel Diseases.

International journal of molecular sciences
2025

A rare culprit: Acute pancreatitis associated with anisakiasis.

IDCases
2025

Isolated IgG4-related sclerosing cholangitis mimicking hilar cholangiocarcinoma: A case report and review.

Hepatology forum
2025

Clinical Profile and Predictors of Repeated Relapse in Type 1 Autoimmune Pancreatitis: A Multicenter Observational Study.

Journal of gastroenterology and hepatology
2025

Genetic Association in Immunoglobulin G4-Related Disease: A Systematic Review.

International archives of allergy and immunology
2026

Immune Checkpoint Inhibitor-Induced Pancreatic Injury: An Emerging Form of Immune-Mediated Pancreatitis.

Pancreas
2025

Case Report: A 14-year-old boy with recurrent pancreatitis and autism-response to steroid and rituximab therapy.

Frontiers in pediatrics
2025

A retrospective study on pancreatic and extra-pancreatic characteristics of IgG4-related disease.

Clinical rheumatology
2025

Dual Malignancies in IgG4-Related Disease: A Diagnostic and Therapeutic Challenge.

ACR open rheumatology
2025

Acute Pancreatitis in Inflammatory Bowel Disease: Results from the European Pandora Study.

Medicina (Kaunas, Lithuania)
2025

Clinicopathological Pearls and Diagnostic Pitfalls in IgG4-Related Disease: Challenging Case Series and Literature Review.

Diagnostics (Basel, Switzerland)
2025

Pancreatitis Preceding the Diagnosis of IBD in Children: A Retrospective Observational Study.

Children (Basel, Switzerland)
2025

Role of endoscopic ultrasound in diagnosis and management of autoimmune pancreatitis.

Indian journal of gastroenterology : official journal of the Indian Society of Gastroenterology
2025

Pancreatic biopsy for indeterminate autoimmune pancreatitis: closer to eliminating misdiagnosis.

Gastrointestinal endoscopy
2025

A Rare Case of Diffuse Neuroendocrine Tumor of the Pancreas Diagnosed by 68Ga-DOTANOC PET CT Study.

Clinical nuclear medicine
2025

Autoimmune Pancreatitis Not Otherwise Specified (AIP-NOS): The Importance of Gastroenterology Consultation When Clinical Findings Are Concerning for Pancreatic Cancer.

Case reports in gastrointestinal medicine
2025

Cavitating Mesenteric Lymph Node Syndrome With Autoimmune Pancreatitis and Hepatitis: A Case Report and Literature Review.

Cureus
2025

Maintenance Treatment for Type 1 Autoimmune Pancreatitis: Effectiveness and Development of the PrescrAIP Relapse Prediction Model.

Clinical gastroenterology and hepatology : the official clinical practice journal of the American Gastroenterological Association
2025

Burden of Metabolic Bone Disease in Patients with Immunoglobulin G4-Related Disease With and Without Autoimmune Pancreatitis: A Cross-Sectional Study.

Clinical and translational gastroenterology
2025

Vitamin A deficiency enhances susceptibility to experimental autoimmune pancreatitis through activation of CD4+ T cells expressing CXCR3 and secreting CCL25.

Clinical and experimental immunology
2025

Smoking, alcohol consumption, and new-onset impaired glucose metabolism in male patients with type 1 autoimmune pancreatitis: a retrospective cohort study.

Therapeutic advances in chronic disease
2026

Metachronic development of cholangiocarcinoma during treatment for IgG4-related sclerosing cholangitis.

Clinical journal of gastroenterology
2025

Endoscopic Diagnostics for IgG4-Related Pancreatobiliary Diseases: Current Modalities and Clinical Perspectives.

Diagnostics (Basel, Switzerland)
2025

Pancreatic Inflammation Induced by Immune Checkpoint Inhibitors in Melanoma Treatment: A Case Report.

The American journal of case reports
2025

Comparative analysis of clinical features in diffuse and focal enlargement of IgG4-related autoimmune pancreatitis: a single-center retrospective study.

Clinical rheumatology
2026

Alteration of Apolipoprotein A2 Isoforms is Associated With the Progression of Chronic Pancreatitis.

Pancreas
2025

A case of multiorgan IgG4-related disease with coronary artery vasculitis: Review of the 2019 Rheumatologic Classification Guidelines and what radiologists need to know.

Radiology case reports
2026

Effectiveness and safety of rituximab across the four phenotypes of IgG4-related disease: a European multi-center cohort study.

European journal of internal medicine
2025

IgG4-Related Autoimmune Pancreatitis With Pancreatic Honeycomb-Like Cystic Lesions: A Case Report.

Journal of digestive diseases
2025

Effective Extracellular Volume Fraction Determined by Equilibrium Contrast-Enhanced CT for Differentiating Autoimmune Pancreatitis from Pancreatic Ductal Adenocarcinoma.

Diagnostics (Basel, Switzerland)
2026

Diffusion-weighted Whole-body Imaging with Background Body Signal Suppression Enables Simultaneous Whole-body Assessments of IgG4-related Diseases.

Internal medicine (Tokyo, Japan)
2025

Pancreatic Doppelgängers: A Case of Misdiagnosed Identity.

ACG case reports journal
2025

Severe Metformin-Associated Lactic Acidosis Managed Without Dialysis in an Elderly Patient With Multiple Comorbidities: A Case Report.

Cureus
2025

Elevated CA19-9 in IgG4-related disease.

Annals of clinical biochemistry
2026

Peripancreatic Vascular Involvement and Gastric Varices in Autoimmune Pancreatitis: A Multicenter Retrospective Study.

Clinical gastroenterology and hepatology : the official clinical practice journal of the American Gastroenterological Association
2025

Predictive Factors for Relapse in Autoimmune Pancreatitis.

Clinical and translational gastroenterology
2025

[Type 1 autoimmune pancreatitis combined with pancreatic cysts: a report of four cases].

Zhonghua nei ke za zhi
2025

Risk of Pancreatic Cancer in Inflammatory Pancreatic Diseases.

The Korean journal of gastroenterology = Taehan Sohwagi Hakhoe chi
2025

Endoscopic ultrasound-guided fine-needle aspiration value in suspected autoimmune pancreatitis malignancy diagnosis.

CytoJournal
2025

Adherence to United European Gastroenterology Guidelines on Diagnosis and Therapy of Immunoglobulin-G4-Related Digestive Disease.

United European gastroenterology journal
2025

The Overlap of Autoimmune Pancreatitis and Pancreatic Cancer: A Clinical Challenge.

ACG case reports journal
2025

Pancreatic Cancer Mimicking Relapse of Autoimmune Pancreatitis: Case Reports.

Surgical case reports
2025

Autoimmune pancreatitis masquerading as a pancreatic neoplasm: A case report.

Medicine
2025

IgG4-related cholangitis - distinguishing from other benign biliary strictures: clinical features, imaging, and response to treatment: a retrospective study.

BMC gastroenterology
2025

Autoimmune Pancreatitis Presenting as a Pancreatic Mass in a Child-A Case Report.

Journal of paediatrics and child health
2025

Clinicopathological features of type 1 autoimmune pancreatitis without elevated serum IgG4 level.

Scientific reports
2025

Solid pancreatic lesions: etiology, morphology and utility of macroscopic on-site evaluation in predicting good yield of endoscopic ultrasound-guided biopsy.

Przeglad gastroenterologiczny
2025

IgG4-related disease - focus on digestive system involvement.

Frontiers in immunology
2025

A Rare Case of Hereditary Pancreatitis Unveiling Systemic Lupus Erythematosus in a Young Female Patient.

Cureus
2025

A comprehensive review of IgG4-related pancreatitis: pathogenesis, diagnosis, and therapeutic advances.

Frontiers in immunology
2025

Global research trends and emerging focus areas in IgG4-related disease: a bibliometric and visual analysis.

Hereditas
2025

The dual role of IgG4 in immunity: bridging pathophysiology and therapeutic applications.

Gut
2025

19-Gauge Versus 22-Gauge Franseen Needles, Comparison of the Histological Diagnostic Capability of Endoscopic Ultrasound-Guided Fine-Needle Biopsy for Autoimmune Pancreatitis: A Multicenter Retrospective Cohort Study.

Diagnostics (Basel, Switzerland)
2025

The Prevalence and Characteristics of Autoimmune Pancreatitis Among Patients Presenting With Pancreatitis to a Quaternary Referral Center in Melbourne, Australia.

Pancreas
2025

CT Coronary Angiogram in Diagnosing IgG4 of Coronary Arteries Presenting as Acute Coronary Syndrome: A Case Report with Review of Literature.

The Indian journal of radiology &amp; imaging
2025

Atypical Presentation of Pancreatic Cancer Mimicking IgG4-Related Disease.

Cureus
2025

Case Report: 18F-FDG PET/CT revealed diffuse pancreatic metastasis in paranasal sinuses rhabdomyosarcoma after treatment improvement.

Frontiers in medicine
2025

A Case of Type 2 Autoimmune Pancreatitis Suggesting Two Potential Disease Activity Markers.

Gastro hep advances
2025

[Ulcerative colitis complicated with type 2 autoimmune pancreatitis: a case report].

Zhonghua nei ke za zhi
2025

Uncovering novel exosome-specific miRNA markers and potential molecular mechanisms in autoimmune pancreatitis.

Genomics
2025

Prevalence and risk factors of skeletal muscle loss and sarcopenia in patients with autoimmune pancreatitis.

Hepatobiliary &amp; pancreatic diseases international : HBPD INT
2025

Granulomatosis with Polyangiitis Presenting as Pancreatic Pseudotumor and Peripancreatic Lymphadenitis: Diagnostic Challenges and Review of 55 Cases.

The American journal of case reports
2025

A new era for autoimmune pancreatitis diagnosis: fine-needle biopsy outperforms fine-needle aspiration in endoscopic ultrasound-guided tissue acquisition.

Clinical endoscopy
2025

Defining pancreatic damage and symptom burden in IgG4-related autoimmune pancreatitis: A cross-sectional study of 118 patients from a single-center registry.

Seminars in arthritis and rheumatism
2025

Autoimmune Pancreatitis: A Review.

Journal of clinical medicine
2025

Sustained Clinical Remission in Relapsing IgG4-related Autoimmune Pancreatitis With Dupilumab.

Clinical gastroenterology and hepatology : the official clinical practice journal of the American Gastroenterological Association
2025

IgG4-Related Cholangitis.

Seminars in liver disease
2025

Pancreaticobiliary maljunction (PBM)-associated pancreatitis: a case report and a new treatment strategy proposed for PBM.

Translational gastroenterology and hepatology
2025

Autoimmune Pancreatitis in Children: A Case Report.

Case reports in gastroenterology
2025

Differentiation of Autoimmune Pancreatitis From Pancreatic Ductal Adenocarcinoma by Diffusion-Weighted Magnetic Resonance Imaging With Weighted Diffusion Subtraction.

Cureus
2025

CA19-9/DBil: a promising indicator to distinguish between CA19-9-elevated pancreatic head-type autoimmune pancreatitis and pancreatic head cancer.

BMC gastroenterology
2025

Endoscopic diagnosis of immunoglobulin G4-related sclerosing cholangitis.

Digestive endoscopy : official journal of the Japan Gastroenterological Endoscopy Society
2025

Differences in the Fecal Metabolome of Autoimmune Pancreatitis Patients.

United European gastroenterology journal
2025

Rate of Decrease in Serum Autotaxin Can Predict Relapse of Type 1 Autoimmune Pancreatitis After Initial Steroid Therapy.

Pancreas
2025

Cytology-Radiology Correlation Series: Pancreatic cytopathology.

Cancer cytopathology
2025

Clinical features and long-term prognosis of type 1 autoimmune pancreatitis based on the location of bile duct lesions.

Journal of hepato-biliary-pancreatic sciences
2025

The impact of the novel EUS scope and ultrasonographic system for diagnosis and therapy in patients with pancreatobiliary diseases (videos).

Journal of hepato-biliary-pancreatic sciences
2025

Evaluating the Usefulness of the Blood Apolipoprotein A2 Isoform Index for Pancreatic Cancer Diagnosis.

Cancers
2025

Potential relationship between Helicobacter pylori infection and autoimmune disorders: A narrative review.

Microbial pathogenesis
2025

Abdominal Inflammatory Lesions Mimicking Malignancy: Imaging Pitfalls and Clues.

Seminars in ultrasound, CT, and MR
2025

Pediatric Autoimmune Pancreatitis: Clinical Findings and Outcomes in Sweden.

United European gastroenterology journal
2025

Avoiding Unnecessary Surgery in Autoimmune Pancreatitis: Lessons From a Four-Patient Case Series and Literature Review.

Cureus
2025

Somatosensory profiling to differentiate distinct painful diseases of the pancreas-a quantitative sensory testing case-control study.

Pain
2025

Clinicopathologic Characteristics of Immune Checkpoint Inhibitor-related Pancreatitis.

The American journal of surgical pathology
2025

Management of IgG4-related cholangitis: diagnosis, therapy, and long-term surveillance.

Gastroenterology report
2025

IgG4-Related Disease (IgG4-RD) Autoimmune Pancreatitis (AIP) as an Initial Presentation of Systemic Lupus Erythematosus (SLE).

Clinical case reports
2025

Facing the challenges of autoimmune pancreatitis diagnosis: The answer from artificial intelligence.

World journal of gastroenterology
2025

Pancreatic and extra-pancreatic transabdominal ultrasound findings of type 1 autoimmune pancreatitis.

Quantitative imaging in medicine and surgery
2025

Pancreatitis-related benign biliary strictures: a review of imaging findings and evolving endoscopic management.

Abdominal radiology (New York)
2025

Predictive factors for the diagnosis of autoimmune pancreatitis using endoscopic ultrasound-guided tissue acquisition: a retrospective study in Japan.

Clinical endoscopy
2025

Treatment Strategies for Chronic Pancreatitis (CP).

Pharmaceuticals (Basel, Switzerland)
2025

IgG4-related disease revealed by acute pancreatitis: A case report and literature review.

Radiology case reports
2025

Plasma Cell-rich Nephritis with a Systemic Polyclonal Lymphoproliferative Disorder, Mimicking Idiopathic Multicentric Castleman Disease, Systemic Lupus Erythematosus, and IgG4-related Disease.

Internal medicine (Tokyo, Japan)
2025

Effects of Steroid Therapy on Pancreatic Endocrine Function in IgG4-related AIP: Evaluation by Arginine Stimulation Test.

JCEM case reports
2025

Reconsidering invasive diagnostics in asymptomatic atypical autoimmune pancreatitis: a case-inspired discussion.

Clinical journal of gastroenterology
2025

Autoimmune Pancreatitis Presenting as Multifocal Masses: A Rare Case Report.

Cureus
2025

Longitudinal Pancreatojejunostomy for Pancreaticodigestive Reconstruction in the Resection of Pancreatic Head Malignancy with Chronic Pancreatitis: A Case Report.

Surgical case reports
2025

IgG4-related disease: lessons from the first 20 years.

Rheumatology (Oxford, England)
2025

Panniculitis of the Lower Extremities Caused by Acute Deterioration of Autoimmune Pancreatitis.

Journal of gastroenterology and hepatology
2025

Gut Microbiota Involved in the Immunopathogenesis of Autoimmune Pancreatitis.

Gut and liver
2025

[Diagnosis and treatment of serum IgG4-negative type 1 autoimmune pancreatitis].

Zhonghua nei ke za zhi
2025

[Two cases of type 1 autoimmune pancreatitis diagnosed by duodenal papilla biopsy].

Zhonghua nei ke za zhi
2025

[A case of primary biliary cholangitis combined with autoimmune pancreatitis and autoimmune gastritis].

Zhonghua nei ke za zhi
2025

Case report: Upper gastrointestinal bleeding associated with pancreatic segmental portal hypertension: six case reports and literature review.

Frontiers in medicine
2025

Differentiating pancreatic ductal adenocarcinoma and autoimmune pancreatitis using a machine learning model based on ultrasound clinical features.

Frontiers in oncology
2025

Unicentric Castleman Disease Coexisting With Type 2 Autoimmune Pancreatitis: A Case Report Mimicking Pancreatic Cancer and Near-Whipple Surgery.

ACG case reports journal
2025

Sequential activation of conventional and plasmacytoid dendritic cells in autoimmune pancreatitis and systemic lupus erythematosus: similarities and dissimilarities.

Frontiers in immunology
2025

Impact of EUS-guided fine-needle biopsy sampling on International Consensus Diagnostic Criteria for diagnosing autoimmune pancreatitis: a prospective multicenter study.

Gastrointestinal endoscopy
2025

Usefulness and Safety of Endoscopic Nasobiliary Drainage for Type 1 Autoimmune Pancreatitis.

Pancreas
2025

Autoimmune Pancreatitis Mimicking a Pancreatic Neuroendocrine Tumor: A Case Report with a Literature Review.

International journal of molecular sciences
2025

Autoimmune pancreatitis, pancreatic and extrapancreatic cancer (AIPPEAR): a multicentre, retrospective study protocol.

BMJ open
2025

A clinicopathological study of IgG4-related autoimmune hepatitis and IgG4-hepatopathy.

Journal of gastroenterology
2025

Clear Cell Carcinoma of the Uterine Cervix in a 14-Year-Old Girl: A Case Report.

Cureus
2025

Unraveling the Microenvironment and the Pathogenic Axis of HIF-1α-Visfatin-Fibrosis in Autoimmune Pancreatitis Using a Single-Cell Atlas.

Advanced science (Weinheim, Baden-Wurttemberg, Germany)
2025

What Is the Latest in Autoimmune Pancreatitis.

Gastroenterology clinics of North America
2024

EUS-guided fine-needle biopsy versus fine-needle aspiration for histopathological evidence for type 1 autoimmune pancreatitis: A single-center retrospective study in China.

Endoscopic ultrasound
2025

Aberrant Methylation of RUNX1 is Associated with the Pathogenesis of Autoimmune Pancreatitis.

International journal of surgical pathology
2024

An Unusual Case of Overlapping Immunoglobulin G4-Related Disease and Systemic Lupus Erythematosus.

Cureus
2025

Hepatobiliary and pancreatic manifestations in inflammatory bowel disease: an umbrella review of meta-analyses.

Therapeutic advances in gastroenterology
2024

Autoimmune pancreatitis as a risk factor of pancreatic cancer.

Klinicka onkologie : casopis Ceske a Slovenske onkologicke spolecnosti
2025

Discriminative features of immunoglobulin G4-related disease (IgG4-RD) and associated autoimmune rheumatic diseases (ARDs) in a nationwide observational cohort: study from the Egyptian College of Rheumatology.

Clinical rheumatology
2025

Ultrasound-guided percutaneous core-needle biopsy for the diagnosis of type 1 autoimmune pancreatitis.

Abdominal radiology (New York)
2025

IgG4-related Disease Manifesting as Autoimmune Pancreatitis, Sialadenitis, and Cholangitis: Case Report.

Acta medica Lituanica
2025

Update on Autoimmune Pancreatitis and IgG4-Related Disease.

United European gastroenterology journal
2024

Mass-forming type 2 autoimmune pancreatitis with upstream dilatation of the main pancreatic duct dilatation: a case report.

Journal of medical case reports
2025

Diffuse large B-cell lymphoma with rapid kidney enlargement after induction of hemodialysis in a patient with IgG4-related disease.

CEN case reports
2024

A Rare Case of Autoimmune Pancreatitis in a 9-Year-Old Male Patient: A Comprehensive Diagnosis and Successful Treatment.

Case reports in gastrointestinal medicine
2025

Letter to Editor regarding "Autoimmune pancreatitis associated with severe postoperative pneumonia".

Pancreatology : official journal of the International Association of Pancreatology (IAP) ... [et al.]
2024

Eccrine Chromhidrosis and Bilioptysis in Type 1 Autoimmune Pancreatitis.

Cureus
2024

IgG4-related disease for the hematologist.

Hematology. American Society of Hematology. Education Program
2025

Serum IgG4-negative and IgG4-positive type 1 autoimmune pancreatitis present with different clinicopathological features: An analysis of a nationwide survey in Japan.

Pancreatology : official journal of the International Association of Pancreatology (IAP) ... [et al.]
2025

Endoscopic ultrasound-guided fine-needle biopsy needle can facilitate histological diagnosis of type 1 autoimmune pancreatitis.

Journal of hepato-biliary-pancreatic sciences
2024

Relationship between pancreatic morphological changes and diabetes in autoimmune pancreatitis: Multimodal medical imaging assessment has important potential.

World journal of radiology
2024

Pancreatic volume change using three dimensional-computed tomography volumetry and its relationships with diabetes on long-term follow-up in autoimmune pancreatitis.

World journal of radiology
2025

Neutrophil extracellular DNA traps activate the TLR9 signaling pathway of pancreatic ductal epithelial cells in patients with type 2 autoimmune pancreatitis.

International immunopharmacology
2025

Clinical profile of IgG4-related disease in Japan based on the rare disease data registry.

Immunological medicine
2024

Journey to diagnosis: An unfinished exploration of IgG4-related sclerosing cholangitis.

World journal of clinical cases
2024

Dexamethasone's Clinical Efficacy in Experimental Autoimmune Pancreatitis Correlates with a Unique Transcriptomic Signature, Whilst Kinase Inhibitors Are Not Effective.

Biomedicines
Ver todos os 1.892 no EuropePMC

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Doenças relacionadas

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Referências e fontes

Bases de dados externas citadas neste artigo

Publicações científicas

Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.

  1. Clinicopathological features of localized-type IgG4-related cholecystitis: a nationwide multicenter study in Japan.
    Journal of gastroenterology· 2026· PMID 41739155mais citado
  2. Multicenter Validation Study of the Clinical Diagnostic Criteria for IgG4-Related Sclerosing Cholangitis 2020 in Japan.
    Journal of hepato-biliary-pancreatic sciences· 2026· PMID 41500843mais citado
  3. Clinical features, responses to therapy and prognosis of 107 patients with IgG4-related cholangitis: a retrospective study.
    BMC gastroenterology· 2026· PMID 41495676mais citado
  4. Metachronic development of cholangiocarcinoma during treatment for IgG4-related sclerosing cholangitis.
    Clinical journal of gastroenterology· 2026· PMID 40889100mais citado
  5. Peripancreatic Vascular Involvement and Gastric Varices in Autoimmune Pancreatitis: A Multicenter Retrospective Study.
    Clinical gastroenterology and hepatology : the official clinical practice journal of the American Gastroenterological Association· 2026· PMID 40774591mais citado
  6. Differentiating IgG4-related Sclerosing Cholangitis from Primary Sclerosing Cholangitis: A Comprehensive Systematic Review and Meta-analysis of Diagnostic Features.
    Am J Gastroenterol· 2026· PMID 41989037recente
  7. Pancreatic adenosquamous carcinoma mimicking autoimmune pancreatitis.
    Hepatobiliary Surg Nutr· 2026· PMID 41983198recente
  8. Anteroposterior diameter of the pancreas in the diagnosis of autoimmune pancreatitis and acute pancreatitis on MRI.
    Abdom Radiol (NY)· 2026· PMID 41973201recente
  9. Autoantibodies are useful in monitoring disease activity and predicting relapses in autoimmune pancreatitis.
    Digestion· 2026· PMID 41961744recente
  10. Drug cross-reactivity between methimazole and propylthiouracil causing recurrent pancreatitis in thyroid storm.
    Endocrinol Diabetes Metab Case Rep· 2026· PMID 41946385recente

Bases de dados e fontes oficiais

Identificadores e referências canônicas usadas para montar este verbete.

  1. ORPHA:103919(Orphanet)
  2. MONDO:0015175(MONDO)
  3. GARD:10911(GARD (NIH))
  4. Busca completa no PubMed(PubMed)
  5. Q2267451(Wikidata)

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Pancreatite autoimune
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Pancreatite autoimune

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MedGen
UMLS
C2609129
Repurposing
3 candidatos
camostat-mesilateprotease inhibitor
gabexateserine protease inhibitor
methanthelineacetylcholine receptor antagonist
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