Imunidade humoral é a parte da imunidade que é mediada por macromoléculas, que se encontram nos fluidos extracelulares e podem ser anticorpos, proteínas do sistema complemento ou certos péptidos antimicrobianos. A imunidade humoral é assim designada porque depende de substâncias que se encontram nos humores do corpo.
Introdução
O que você precisa saber de cara
Doença renal IgG4-relacionada é uma condição inflamatória crônica que afeta os rins, frequentemente associada a outras manifestações sistêmicas como pancreatite e linfadenite. Caracteriza-se por infiltração de plasmócitos IgG4+ nos órgãos afetados, podendo levar à insuficiência renal progressiva.
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<1/50kMuito rara
1/20kRara
1/10kPouco freq.
1/5kIncomum
1/2k
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Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Partes do corpo afetadas
+ 30 sintomas em outras categorias
Características mais comuns
Os sintomas variam de pessoa para pessoa. Abaixo estão as 59 características clínicas mais associadas, ordenadas por frequência.
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Genética e causas
O que está alterado no DNA e como passa nas famílias
Nenhum gene associado encontrado
Os dados genéticos desta condição ainda estão sendo catalogados.
Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
Remédios, cuidados de apoio e o que precisa acompanhar
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Publicações mais relevantes
The Effectiveness of Lesion Detection for Immunoglobulin G4-Related Kidney Diseases by Diffusion-Weighted Imaging.
The aim of the study was to compare the efficacy of magnetic resonance imaging (MRI) with that of plain or contrast-enhanced computed tomography (CT) in the detection of renal parenchymal and pelvic lesions of immunoglobulin G4-related kidney disease (IgG4-RKD). Patients with IgG4-RKD and controls, who performed plain, contrast-enhanced CT and MRI around the kidney region in our hospital, were enrolled. The diagnosis of IgG4-RKD was made by definite cases of IgG4-RKD diagnostic criteria in 2020. Five blinded observers independently assessed image datasets by confidence scores to assess diagnostic accuracy, sensitivity, specificity, areas under the receiver operating characteristic curve (AUROC), and Cronbach's alpha coefficient. A total of 31 patients were included in the study. Fourteen (45.2%) had IgG4-RKD. Five patients with IgG4-RKD had parenchymal lesions, 5 had renal pelvic lesions, and 4 had both. In the parenchymal lesions, there was no significant difference in diagnostic performance between contrast-enhanced CT and diffusion-weighted imaging (DWI)-b800. The AUROC and sensitivity were higher in DWI-b800 than in plain CT (p < 0.05). Cronbach's alpha coefficient was 0.44 for plain CT and over 0.80 for contrast-enhanced CT and DWI-b800. In the pelvic lesions, there were fewer differences in the performance among each sequence. Cronbach's alpha coefficient was over 0.80 for plain CT, contrast-enhanced CT, and DWI-b800. Plain MRI, especially in DWI-b800, can effectively detect renal parenchymal lesions in IgG4-RKD. In cases where the use of a contrast agent of CT is difficult, DWI-b800 can be an alternative for the screening of IgG4-RKD.
Urinary β2-microglobulin as a Potential Biomarker for Early Treatment Selection: A Patient with Severe IgG4-related Tubulointerstitial Nephritis.
This case report describes an 80-year-old man with severe immunoglobulin G4-related tubulointerstitial nephritis (IgG4-TIN), characterized by storiform fibrosis with diffuse lymphocytic and plasma cell infiltration observed on a renal biopsy. Steroid pulse therapy administered immediately after confirming a remarkable increase in urinary β2-microglobulin (100,948 μg/L) along with no evidence of malignancy significantly improved the renal function and reduced the urinary β2-microglobulin levels. This study highlights the potential utility of urinary β2-microglobulin as a biomarker for early treatment selection in severe IgG4-TIN and emphasizes the need for timely intervention to prevent irreversible kidney damage.
Clinical features and outcomes of immunoglobulin G4-related kidney disease and immunoglobulin G4-related retroperitoneal fibrosis in Korea.
Immunoglobulin G4 (IgG4)-related disease (RD) is a newly recognized disease, and a few epidemiologic studies about this disorder have been published. This research aimed to demonstrate the clinical features and outcomes of IgG4-related kidney disease (RKD) and IgG4-related retroperitoneal fibrosis (RPF) compared to other organs' involvement. Patients who were diagnosed with IgG4-RD from January 2009 to July 2019 at three medical institutions in South Korea were included. They were classified into three groups: RKD, RPF, and Others groups. The differences in symptoms, laboratory, histological and radiological findings, treatment, and outcomes among the three groups were evaluated. Of 94 patients, 13 (13.8%) and 22 patients (23.4%) were classified into the RKD and RPF groups, respectively. There were older (p = 0.004) and more asymptomatic patients (p = 0.02) in the RKD and RPF groups. In the RKD group, hypocomplementemia (p = 0.003) and eosinophilia (p = 0.001) were more frequently identified. In logistic regression analysis, hypocomplementemia (odds ratio [OR], 14.04; 95% confidence interval [CI], 1.38-142.95) and decreased renal function at the time of diagnosis (OR, 0.95; 95% CI, 0.91-0.98) were associated with renal involvement. Older age (OR, 1.05; 95% CI, 1.00-1.11), male (OR, 6.11; 95% CI, 1.41-26.61), and higher serum IgG4 levels (OR, 1.00; 95% CI, 1.00-1.00) were associated with retroperitoneal involvement. The treatment duration was longer in the RKD and RPF groups (p = 0.01) with glucocorticoids. Renal and retroperitoneal involvement in IgG4-RD presented clinical features that distinguish it from other organs' involvement, such as incidental diagnosis, hypocomplementemia, eosinophilia, and the need for a longer duration of maintenance treatment.
Ultrasonographic features of IgG4-related kidney disease: diagnostic value and correlation with clinical-pathological findings.
To systematically characterize the ultrasonographic features of biopsy-proven IgG4-related kidney disease (IgG4-RKD) and to evaluate their correlation with key clinicopathological parameters. In this retrospective study, the ultrasonographic, clinical, laboratory, and pathological data of 15 patients with biopsy-confirmed IgG4-RKD were analyzed. Key sonographic features, including renal size, parenchymal echotexture, focal lesions, and resistive index, were evaluated and correlated with clinicopathological findings. The cohort consisted of predominantly older males (86.7%) with frequent multi-organ involvement (60.0%). The most common ultrasonographic pattern included bilateral involvement (93.3%), increased or heterogeneous echogenicity (73.3%/60.0%), multiple hypoechoic areas (46.7%), and enlargement of at least one kidney (>12 cm) in 40.0% of patients. Increased renal length showed a significant positive correlation with serum IgG4 levels (r = 0.63, 95% confidence interval (CI) [0.17, 0.86], p < 0.05), and parenchymal thickness showed a significant negative correlation with serum C3 levels (r = -0.58, 95% CI [-0.84, -0.10], p < 0.05). Furthermore, parenchymal thickness was moderately correlated with serum creatinine (r = 0.51, n = 15, 95% CI [0.00, 0.81], p < 0.05). Ultrasound also effectively monitored therapeutic response, with 83.3% of followed patients showing structural improvement. Ultrasonography in IgG4-RKD reveals a characteristic pattern of findings that not only serve a descriptive role but also quantitatively correlate with serological disease activity and renal dysfunction. Therefore, ultrasound is a valuable, non-invasive tool for initial assessment, guiding diagnosis, and monitoring therapeutic response in the clinical management of IgG4-RKD.
IgG4-related kidney disease: from renal histopathology and immunopathogenesis to novel pharmacological interventions.
Immunoglobulin G4 (IgG4)-related disease (IgG4-RD) is a rare and chronic fibroinflammatory condition hallmarked by tumefactive lesions that can affect nearly any organ of the body and lead to fibrotic organ destruction. Parenchymal and non-parenchymal affection of the kidney and urogenital tract are subsumed under the umbrella term IgG4-related kidney disease (IgG4-RKD), which is a severe and quite common organ manifestation in IgG4-RD. The immunopathogenesis in IgG4-RD is depicted by a complex interplay of distinct B- and T-cell subsets, excessive antibody production, a unique cytokine environment and the development of exuberant fibrosis. Scientific advancements over the last two decades have fostered to explore a broad repertoire of pharmacological interventions starting from B-cell depleting agents and extending to modulators of T-cell co-stimulation. The aim of this review is to a) provide an overview of the current knowledge on IgG4-RKD with an emphasis on the unique properties of renal histopathology and immunopathogenesis and b) overview novel pharmacological interventions targeting B cells, T cells, and beyond. Speculating on a potential scenario that dominates IgG4-RD's treatment reality in 5 years, the advent of integrative treatment strategies combining both B- and T-cell targeting agents is conceivable.
Publicações recentes
IgG4-Related Kidney Disease With Hypocomplementemia and Circulating Immune Complex Containing IgG3 Presenting as Rapidly Progressive Glomerulonephritis: A Case Report.
Ultrasonographic features of IgG4-related kidney disease: diagnostic value and correlation with clinical-pathological findings.
IgG4-related kidney disease: from renal histopathology and immunopathogenesis to novel pharmacological interventions.
The Effectiveness of Lesion Detection for Immunoglobulin G4-Related Kidney Diseases by Diffusion-Weighted Imaging.
Concurrent IgG4-related membranous nephropathy and proliferative diabetic kidney disease: a diagnostic dilemma and therapeutic strategy in long-standing diabetes.
📚 EuropePMC81 artigos no totalmostrando 136
Ultrasonographic features of IgG4-related kidney disease: diagnostic value and correlation with clinical-pathological findings.
Frontiers in medicineIgG4-related kidney disease: from renal histopathology and immunopathogenesis to novel pharmacological interventions.
Expert review of clinical immunologyThe Effectiveness of Lesion Detection for Immunoglobulin G4-Related Kidney Diseases by Diffusion-Weighted Imaging.
NephronConcurrent IgG4-related membranous nephropathy and proliferative diabetic kidney disease: a diagnostic dilemma and therapeutic strategy in long-standing diabetes.
BMC nephrologyUrinary β2-microglobulin as a Potential Biomarker for Early Treatment Selection: A Patient with Severe IgG4-related Tubulointerstitial Nephritis.
Internal medicine (Tokyo, Japan)Case Report: Two cases of IgG4-related kidney disease with monoclonal gammopathy.
Frontiers in immunologyClinicopathological findings of tubulointerstitial nephritis: a cross-sectional analysis of the Japan Renal Biopsy Registry (J-RBR).
Clinical and experimental nephrologyCollapsing Focal Segmental Glomerulosclerosis With Concurrent IgG4 Nephropathy.
CureusClinical features and outcomes of immunoglobulin G4-related kidney disease and immunoglobulin G4-related retroperitoneal fibrosis in Korea.
Kidney research and clinical practiceAn Atypical Cystic Renal Mass in a Patient with IgG4-Related Kidney Disease.
Internal medicine (Tokyo, Japan)IgG4-Related Kidney Disease.
Clinical journal of the American Society of Nephrology : CJASNCoexistence of immunoglobulin G4-related kidney disease and acute hematogenous disseminated pulmonary tuberculosis: a case report.
Frontiers in immunologyProgression to end-stage renal disease due to IgG4-related nephritis: a case report.
Oxford medical case reportsA Challenging Case of IgG4-Related Kidney Disease Accompanied With Positive Serologic Tests of Lupus Erythematosus.
Nephrology (Carlton, Vic.)An Unusual Case of Overlapping Immunoglobulin G4-Related Disease and Systemic Lupus Erythematosus.
CureusDiffuse large B-cell lymphoma with rapid kidney enlargement after induction of hemodialysis in a patient with IgG4-related disease.
CEN case reportsA Case of IgG4-Related Disease Manifesting as Extensive Abdominal Periarteritis and Membranous Nephropathy, Successfully Controlled with Low-Dose Steroid Therapy without Relapse or Complications.
NephronRelationship between MRI findings and renal histopathology in IgG4-related tubulointerstitial nephritis.
Modern rheumatologyClinicopathologic Features of IgG4-Related Kidney Disease.
Kidney international reportsIgG4-related disease complicated by PLA2R-associated membranous nephropathy: A case report.
Open life sciencesRenal Manifestations of IgG4-Related Disease: A Concise Review.
International journal of nephrologyTubulointerstitial nephritis with storiform fibrosis in a patient with angioimmunoblastic T-cell lymphoma.
CEN case reportsA case of immunoglobulin G4-related kidney disease manifesting after dipeptidyl peptidase-4 inhibitor treatment.
CEN case reportsImmunoglobulin G4-related disease presenting with nephrotic syndrome due to minimal change disease: a case report.
Journal of medical case reportsIgG4-Related Membranous Nephropathy After COVID-19 Vaccination: A Case Report.
CureusIgG4-Related Kidney Disease: A Diagnostic Conundrum Successfully Treated With Steroids and Rituximab.
CureusImproved Renal Function in Initial Treatment Improves Patient Survival, Renal Outcomes, and Glucocorticoid-Related Complications in IgG4-Related Kidney Disease in Japan.
Kidney international reportsIgG4-related kidney disease: Clinicopathologic features, differential diagnosis, and mimics.
Seminars in diagnostic pathologyA pictorial review of genitourinary infections and inflammations.
Clinical imagingCase Report: IgG4-related kidney disease complicated by interstitial pneumonia.
F1000ResearchIgG4-Related Membranous Nephropathy with Acute Nephrotic Syndrome During Successful Steroid Maintenance Treatment for Type 1 Autoimmune Pancreatitis.
The American journal of case reportsClinical and Prognostic Factors in Patients with IgG4-Related Kidney Disease.
Clinical journal of the American Society of Nephrology : CJASNA case of IgG4-related interstitial nephritis with ureteral obstruction: case report and literature review.
BMC urologyProgression to End-Stage Renal Disease Due to IgG4-Related Nephritis Refractory to Rituximab.
CureusIgG4-related kidney disease complicated with retroperitoneal fibrosis: A case report.
World journal of clinical cases[When a rear-end collision turns out to be a revelation: a case of IgG4 related kidney desease].
Giornale italiano di nefrologia : organo ufficiale della Societa italiana di nefrologiaA Case of IgG4-Related Disease and Membranous Nephropathy Associated with Thrombospondin Type-1 Domain-Containing 7A.
Glomerular diseasesImportance of Awareness and Careful Follow-Up of Suspected IgG4-Related Periaortitis.
International heart journalImmunoglobulin G4-related Tubulointerstitial Nephritis with Simultaneous Resolution of Plasma Cell Infiltration and Fibrosis after Steroid Treatment.
Internal medicine (Tokyo, Japan)Immunoglobulin G4-Related Kidney Disease.
Saudi journal of kidney diseases and transplantation : an official publication of the Saudi Center for Organ Transplantation, Saudi ArabiaDiagnostic Dilemma: Cardiorenal Syndrome As an Unusual Presentation of IgG4-Related Disease.
Indian journal of nephrologyComparison of clinicopathological features between patients with and without hypocomplementemia in IgG4-related kidney disease.
Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal AssociationRenal biopsy diagnosis of IgG4-related kidney disease with minor hematuria and mild renal dysfunction: lessons for the clinical nephrologist.
Journal of nephrologyRecent advances in IgG4-related kidney disease.
Modern rheumatologyCase Report: Atypical Manifestations Associated With FOXP3 Mutations. The "Fil Rouge" of Treg Between IPEX Features and Other Clinical Entities?
Frontiers in immunologyIgG4-Related Kidney Disease Associated With End-Stage Kidney Disease, Renal Pseudotumor, and Renal Vein Thrombosis.
CureusNationwide epidemiological survey of immunoglobulin G4-related disease with malignancy in Japan.
Journal of gastroenterology and hepatologyA Case of M-Type Phospholipase A2 Receptor-Associated Membranous Nephropathy With IgG4-Positive Cells Infiltration in the Interstitium.
Clinical medicine insights. Case reportsConcurrent IgG4-Related disease and clear cell renal cell carcinoma.
Urology case reports[Clinicopathological characteristics and prognosis of IgG4-related kidney disease].
Zhonghua yi xue za zhiIgG4 Related Kidney Disease with Extra-Renal Involvement Demonstrated on FDG PET/CT.
Indian journal of nuclear medicine : IJNM : the official journal of the Society of Nuclear Medicine, IndiaIgG4 tubulointerstitial nephritis - An uncommon enemy!
Indian journal of pathology & microbiologyA Case of IgG4-Related Kidney Disease Developing While on Steroid Treatment for Autoimmune IgG4 Pancreatitis.
Journal of investigative medicine high impact case reportsVasculitic neuropathy associated with IgG4-related kidney disease: A case report and literature review.
Clinical nephrologyDisparities between IgG4-related kidney disease and extrarenal IgG4-related disease in a case-control study based on 450 patients.
Scientific reportsRenal Involvement in IgG4-Related Disease: From Sunlight to Twilight.
Frontiers in medicineIgG4-related kidney disease: Pathogenesis, diagnosis, and treatment.
Clinical nephrologyMasquerader in oncology: IgG4-related kidney disease presenting as right upper ureteric mass.
Indian journal of cancerIgG4-related kidney disease with systemic Epstein-Barr virus infection: A case report.
Clinical nephrologyValidation of the 2019 ACR/EULAR criteria for IgG4-related disease in a Japanese kidney disease cohort: a multicentre retrospective study by the IgG4-related kidney disease working group of the Japanese Society of Nephrology.
Annals of the rheumatic diseasesTertiary lymphoid tissue in early-stage IgG4-related tubulointerstitial nephritis incidentally detected with a tumor lesion of the ureteropelvic junction: a case report.
BMC nephrologyIgG4-related nephritis and interstitial pulmonary disease complicated by invasive pulmonary fungal infection: a case report.
BMC nephrology[Computed Tomography Imaging Features of IgG4-related Nephropathy].
Zhongguo yi xue ke xue yuan xue bao. Acta Academiae Medicinae SinicaeValidation of the diagnostic criteria for IgG4-related kidney disease (IgG4-RKD) 2011, and proposal of a new 2020 version.
Clinical and experimental nephrologyA case of eosinophilic granulomatosis with polyangiitis as a mimicker of IgG4-related disease.
Modern rheumatology case reportsIdiopathic membranous nephropathy in a patient diagnosed with IgG4-related disease: A case report.
MedicineClinicopathological features of IgG4-related kidney disease .
Clinical nephrologyRisks and characteristics of pancreatic cancer and pancreatic relapse in autoimmune pancreatitis patients.
Journal of gastroenterology and hepatologyLow-density lipoprotein apheresis for PLA2R-related membranous glomerulonephritis accompanied by IgG4-related tubulointerstitial nephritis.
CEN case reportsIgG4-related kidney disease: experience from a Mexican cohort.
Clinical rheumatologyClinical and imaging features of IgG4-related kidney disease.
Abdominal radiology (New York)Hypocomplementemia is related to elevated serum levels of IgG subclasses other than IgG4 in IgG4-related kidney disease.
Modern rheumatologyAn overlap of antineutrophil cytoplasmic antibody (ANCA)-associated glomerulonephritis and IgG4-related kidney disease.
Clinica chimica acta; international journal of clinical chemistryAcute Tubulointerstitial Nephritis as a Sole Manifestation of Immunoglobulin G4-Related Disease.
Journal of medical cases[A Case of Laparoscopic Resection of Cecal Carcinoma Complicated with IgG4-Related Disease].
Gan to kagaku ryoho. Cancer & chemotherapyProgressive Renal Dysfunction due to IgG4-Related Kidney Disease Refractory to Steroid Therapy: A Case Report.
Case reports in nephrology and dialysisIgG4-related disease in the Japanese population: a genome-wide association study.
The Lancet. RheumatologyImaging findings of IgG4-related kidney disease without extrarenal organ involvement: A case report.
MedicineIgG4-related kidney disease (IgG4-RKD) with membranous nephropathy as its initial manifestation: report of one case and literature review.
BMC nephrologyIgG4-Related Kidney Disease: A Curious Case of Interstitial Nephritis with Hypocomplementemia.
Case reports in nephrology and dialysisClinical characteristics of autoimmune pancreatitis with IgG4 related kidney disease.
Advances in medical sciencesKidney Involvement in Patients with Type 1 Autoimmune Pancreatitis.
Journal of clinical medicineSimultaneous occurrence of IgG4-related Tubulointerstitial nephritis and colon adenocarcinoma with hepatic metastasis: a case report and literature review.
BMC nephrologyA case of immunoglobulin G4-related inflammatory pseudotumor mimicking renal cell carcinoma.
Abdominal radiology (New York)Clinical Manifestations and Long-term Outcomes of IgG4-Related Kidney and Retroperitoneal Involvement in a United Kingdom IgG4-Related Disease Cohort.
Kidney international reportsImmunoglobulin G4-Related Disease Arising from the Bladder Wall.
Urologia internationalisIgG4-related kidney disease and retroperitoneal fibrosis: An update.
Modern rheumatologyAn IgA1-lambda-type monoclonal immunoglobulin deposition disease associated with membranous features in a patient with IgG4-related kidney disease: a case report.
BMC nephrologyAntineutrophil cytoplasmic antibody and/or antiglomerular basement membrane antibody associated crescentic glomerulonephritis in combination with IgG4-related tubulointerstitial nephritis.
Clinical and experimental rheumatologyImmunoglobulin G4-related Kidney Disease Associated With Autoimmune Hemolytic Anemia.
Iranian journal of kidney diseasesA case of IgG4-related kidney disease with predominantly unilateral renal atrophy.
CEN case reportsRole of complement system in patients with biopsy-proven immunoglobulin G4-related kidney disease.
Human pathologySpectrum of IgG4-related Kidney Disease at a Tertiary Care Center.
Indian journal of nephrologyPerirenal capsule and scrotal involvement in immunoglobulin G4-related kidney disease: case-based review.
Rheumatology internationalIgG4-related kidney disease: the effects of a Rituximab-based immunosuppressive therapy.
OncotargetA Refractory Case of Secondary Membranous Nephropathy Concurrent with IgG4-related Tubulointerstitial Nephritis.
Internal medicine (Tokyo, Japan)[IgG4-related kidney disease: Urologist trap?].
Progres en urologie : journal de l'Association francaise d'urologie et de la Societe francaise d'urologieImmunoglobulin G4-related kidney disease: Pathogenesis, diagnosis, and treatment.
Chronic diseases and translational medicineCrescentic Glomerulonephritis With Immunoglobulin G4-Related Disease.
The American journal of the medical sciencesIgG4-Related Kidney Disease: Report of a Case Presenting as a Renal Mass.
Case reports in surgeryIgG4-Related Disease Manifesting as Interstitial Nephritis Accompanied by Hypophysitis.
The American journal of case reportsIgG4-related membranous glomerulonephritis and generalized lymphadenopathy without pancreatitis: a case report.
BMC nephrologyBilateral renal hilar tumors in IgG4-related disease.
Clinical and experimental nephrology[A CASE OF IgG4-RELATED DISEASE WITH THICKENING OF THE RENAL PELVIS AT LEFT RENAL HILUM DIAGNOSED BY OBTURATOR LYMPH NODE DISSECTION].
Nihon Hinyokika Gakkai zasshi. The japanese journal of urologyFactors related to renal cortical atrophy development after glucocorticoid therapy in IgG4-related kidney disease: a retrospective multicenter study.
Arthritis research & therapyA case of IgG4-related tubulointerstitial nephritis and membranous glomerulonephritis during the clinical course of gastric cancer: Imaging features of IgG4-related kidney disease.
Modern rheumatologyCoexistence of Acute Crescent Glomerulonephritis and IgG4-Related Kidney Disease.
Case reports in nephrology and dialysisIgG4-Related Kidney Disease and IgG4-Related Retroperitoneal Fibrosis.
Seminars in liver diseaseRecognizing IgG4-related tubulointerstitial nephritis.
Canadian journal of kidney health and diseaseDistribution and components of interstitial inflammation and fibrosis in IgG4-related kidney disease: analysis of autopsy specimens.
Human pathologyIgG4-Related Kidney Disease in a Patient With History of Breast Cancer: Findings on 18F-FDG PET/CT.
Clinical nuclear medicineEstimation of the number of histological diagnosis for IgG4-related kidney disease referred to the data obtained from the Japan Renal Biopsy Registry (J-RBR) questionnaire and cases reported in the Japanese Society of Nephrology Meetings.
Clinical and experimental nephrologyIgG4-related nephropathy.
Journal of nephrology[IgG4-related kidney disease: what the nephrologist needs to know].
Giornale italiano di nefrologia : organo ufficiale della Societa italiana di nefrologiaIgG4-related Kidney Disease Mimicking Malignant Ureter Tumor: Case Report and Literature Review.
MedicineIgG4-related tubulointerstitial nephritis associated with only lymphadenopathy and without elevated serum IgG4 or renal imaging abnormalities: a case report and literature review.
International journal of clinical and experimental medicineA case of IgG4-related kidney disease complicated by eosinophilic lung disease.
CEN case reportsMembranoproliferative glomerulonephritis with predominant IgG2 and IgG3 deposition in a patient with IgG4-related disease.
BMC nephrologyIgG4-related stomach muscle lesion with a renal pseudotumor and multiple renal rim-like lesions: A rare manifestation of IgG4-related disease.
Modern rheumatologyImmunoglobulin G4-Related Kidney Disease: A Comprehensive Pictorial Review of the Imaging Spectrum, Mimickers, and Clinicopathological Characteristics.
Korean journal of radiologyIgG4-related kidney disease--A review.
Pathology, research and practiceImmunoglobulin G4-related Kidney Disease as a Cause of Acute Renal Insufficiency.
Iranian journal of kidney diseases[112th Scientific Meeting of the Japanese Society of Internal Medicine: Symposium: Recent Progress in IgG4-related Disease: IgG4-related Kidney Disease・IgG4-related Retroperitoneal Fibrosis].
Nihon Naika Gakkai zasshi. The Journal of the Japanese Society of Internal MedicineRecovery of renal function after glucocorticoid therapy for IgG4-related kidney disease with renal dysfunction.
Clinical and experimental nephrologyOrgan Correlation in IgG4-Related Diseases.
Journal of Korean medical scienceAn Overlapping Case of Lupus Nephritis and IgG4-Related Kidney Disease.
Journal of clinical medicine researchIgG4-related kidney disease from the renal pelvis that mimicked urothelial carcinoma: a case report.
BMC urologyIgG4-related Kidney Disease in Which the Urinalysis, Kidney Function and Imaging Findings Were Normal.
Internal medicine (Tokyo, Japan)A Case of IgG4-Related Hypophysitis Presented with Hypopituitarism and Diabetes Insipidus.
Clinical medicine insights. Case reportsDistinct cytokine mRNA expression pattern in immunoglobulin G4-related kidney disease associated with renal cell carcinoma.
Clinical kidney journalAcute Interstitial Nephritis and Membranous Nephropathy in the Context of IgG4-Related Disease.
Case reports in nephrology and dialysisImmunoglobulin G4-related tubulointerstitial nephritis associated with interstitial pulmonary disease: Report of a case with review of literature.
Indian journal of nephrology[IgG4-related kidney disease. Diagnosis and treatment].
Nihon Rinsho Men'eki Gakkai kaishi = Japanese journal of clinical immunologyUltrastructural studies of IgG4-related kidney disease.
Internal medicine (Tokyo, Japan)A case developing minimal change disease during the course of IgG4-related disease.
Modern rheumatologyIgG4-related kidney disease--an update.
Current opinion in nephrology and hypertensionAssociações
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- The Effectiveness of Lesion Detection for Immunoglobulin G4-Related Kidney Diseases by Diffusion-Weighted Imaging.
- Urinary β2-microglobulin as a Potential Biomarker for Early Treatment Selection: A Patient with Severe IgG4-related Tubulointerstitial Nephritis.
- Clinical features and outcomes of immunoglobulin G4-related kidney disease and immunoglobulin G4-related retroperitoneal fibrosis in Korea.
- Ultrasonographic features of IgG4-related kidney disease: diagnostic value and correlation with clinical-pathological findings.
- IgG4-related kidney disease: from renal histopathology and immunopathogenesis to novel pharmacological interventions.
- IgG4-Related Kidney Disease With Hypocomplementemia and Circulating Immune Complex Containing IgG3 Presenting as Rapidly Progressive Glomerulonephritis: A Case Report.
- Concurrent IgG4-related membranous nephropathy and proliferative diabetic kidney disease: a diagnostic dilemma and therapeutic strategy in long-standing diabetes.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:449395(Orphanet)
- MONDO:0018671(MONDO)
- GARD:21882(GARD (NIH))
- Busca completa no PubMed(PubMed)
- Q55788248(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
