Raras
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Coroidopatia interna punctiforme
ORPHA:580951CID-10 · H31.0CID-11 · 9B65.0DOENÇA RARA

Doença oftalmológica rara caracterizada por lesões coriorretinianas pontilhadas do pólo posterior tipicamente bilaterais, assimétricas, amareladas, formando um padrão de ramificação linear e progredindo para cicatrizes atróficas. Membranas neovasculares sub-retinianas ocorrem na maioria dos casos. Vitritis está sempre ausente. Os doentes podem apresentar visão turva, escotoma, moscas volantes, fotopsia e metamorfopsia. A formação da membrana neovascular coroidal e a fibrose sub-retiniana são as principais causas da perda visual. A condição ocorre predominantemente em mulheres jovens com miopia.

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Introdução

O que você precisa saber de cara

📋

Doença oftalmológica rara caracterizada por lesões coriorretinianas pontilhadas do pólo posterior tipicamente bilaterais, assimétricas, amareladas, formando um padrão de ramificação linear e progredindo para cicatrizes atróficas. Membranas neovasculares sub-retinianas ocorrem na maioria dos casos. A vitrite está sempre ausente. Os pacientes podem apresentar visão turva, escotoma, moscas volantes, fotopsia e metamorfopsia. A formação da membrana neovascular coroidal e da fibrose sub-retiniana são as principais causas da perda visual. Uma condição ocorre predominantemente em mulheres jovens com miopia.

Publicações científicas
224 artigos
Último publicado: 2026 Mar 13

Escala de raridade

CLASSIFICAÇÃO ORPHANET · BRASIL 2024
1-9 / 1 000 000
Ultra-rara
<1/50k
Muito rara
1/20k
Rara
1/10k
Pouco freq.
1/5k
Incomum
1/2k
Prevalência
0.0
Worldwide
Início
Adult
🏥
SUS: Sem cobertura SUSScore: 0%
CID-10: H31.0
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Sinais e sintomas

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Linha do tempo da pesquisa

Publicações por ano — veja quando o interesse científico cresceu
Anos de pesquisa1desde 2026
Total histórico224PubMed
Últimos 10 anos133publicações
Pico202219 papers
Linha do tempo
2026Hoje · 2026🧪 2010Primeiro ensaio clínico📈 2022Ano de pico
Publicações por ano (últimos 10 anos)

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Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

🇧🇷 Atendimento SUS — Coroidopatia interna punctiforme

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Publicações mais relevantes

Timeline de publicações
135 papers (10 anos)
#1

Choroidal neovascularization secondary to punctate inner choroidopathy after resolution of multiple evanescent white dot syndrome: A case report.

Medicine2026 Mar 06

White dot syndromes include multiple evanescent white dot syndrome (MEWDS) and punctate inner choroidopathy (PIC), which are rarely reported to coexist or occur sequentially in a single eye. The co-occurrence increases diagnostic complexity, and there are no previous reports of choroidal neovascularization (CNV) secondary to PIC following the resolution of MEWDS. This case report aims to supplement clinical evidence for the pathogenesis and treatment of such sequential ocular diseases. A 42-year-old healthy female presented with blurred vision in her right eye for 3 days initially; 2 months later, her right eye vision worsened further, and 2.5 months after that, she developed blurred vision again with decreased visual acuity. At the first visit, the patient was diagnosed with MEWDS in her right eye based on fundus examination, fundus autofluorescence, fundus fluorescein angiography, visual field test, and optical coherence tomography (OCT) findings. Two months later, she was diagnosed with PIC in the same eye due to new peripapillary yellow-white lesions and corresponding OCT changes. Another 2.5 months later, she was diagnosed with CNV secondary to PIC based on subretinal hemorrhage, abnormal vascular flow on OCT angiography, and fundus fluorescein angiography confirmation. No treatment was given at the initial diagnosis of MEWDS. After the diagnosis of PIC, the patient received oral prednisone (1 mg/kg per day for 5 days, followed by gradual reduction over 6-8 weeks). For CNV secondary to PIC, intravitreal anti-vascular endothelial growth factor (VEGF) therapy (Ranibizumab, 0.5 mg/0.1 mL, once a month, twice in total) was administered. After 2 intravitreal anti-VEGF injections, the best-corrected visual acuity of the patient's right eye improved to 20/20, fundic hemorrhage resolved, and OCT demonstrated complete resolution of CNV. During 2 years of follow-up, no recurrence of CNV or PIC was observed, and best-corrected visual acuity remained stable at 20/20. MEWDS and PIC may share common etiological and pathogenetic mechanisms. PIC may develop sequentially after MEWDS in the same eye, and CNV may be a complication of PIC. A combination of oral corticosteroid therapy for PIC and timely intravitreal anti-VEGF injections for secondary CNV can achieve favorable long-term clinical outcomes. Regular follow-up is necessary for patients with MEWDS to monitor for potential progression to PIC and CNV.

#2

Progressive development of dome-shaped macula and subsequent onset of punctate inner choroidopathy in a highly myopic patient: a 7-year follow-up case report.

American journal of ophthalmology case reports2026 Jun

To describe the development of dome-shaped macula (DSM) in a highly myopic patient, followed by the subsequent onset of punctate inner choroidopathy (PIC). A 46-year-old man with high myopia, with a systemic history of psoriatic arthritis and an ocular history of Acanthamoeba keratitis resulted in two penetrating keratoplasties (PK) in his right eye, was followed up regularly at our center for a 7-year period. During the follow-up, the left eye remained stable until the fifth year. However, at the seventh year, a routine fundus examination revealed the asymptomatic appearance of lacquer cracks, which had been absent at baseline. Multimodal imaging evaluation further identified the incidental development of a horizontal oriented DSM and active and inactive PIC foci localized near the newly detected lacquer cracks. This case report provides new insights into the formation of DSM, supporting the hypothesis that macular bulge may result from differential elongation of the peri-dome region. Additionally, it highlights that DSM can coexist with PIC.

#3

ROLE OF INFLAMMATION IN ATROPHY DEVELOPMENT AND PROGRESSION IN PATHOLOGIC MYOPIA.

Retina (Philadelphia, Pa.)2026 Mar 01

To describe the progression of atrophy in pathologic myopia eyes with prior retinal inflammatory lesions consistent with punctate inner choroidopathy. Retrospective case series of 21 eyes with pathologic myopia and resolved retinal inflammatory lesions compared with 26 noninflamed controls (14 fellow eyes; 12 external myopic eyes with pre-existing patchy atrophy). The primary outcome was annual atrophy-area change (mm2/year) on multimodal imaging. Secondary outcomes included incident/enlarging atrophy, multifocal versus unifocal appearance, and META-PM category progression. Group comparisons used Welch t tests and Fisher exact tests; an age-adjusted linear regression examined independent associations. Over 5.2 ± 3.2 years in inflamed eyes and 5.3 ± 2.4 years in controls, patchy atrophy progressed faster with inflammation (0.76 ± 0.67 vs. 0.38 ± 0.47 mm2/year; P = 0.03). Among eyes starting in myopic macular degeneration Category 1 to 2, incident atrophy occurred in 14 of 14 (100%) inflamed versus 4 of 11 (36.4%) controls (P < 0.01). Overall atrophy activity (new or enlarging) was 21 of 21 (100%) in inflamed eyes versus 19 of 26 (73.1%) controls (P < 0.01). Multifocal atrophy was more frequent with inflammation (15/21, 71.4%) than in controls (6/26, 23.1%; P < 0.01). In age-adjusted regression, inflammation remained independently associated with faster atrophy expansion (β = 0.41 mm2/year; 95% CI, 0.04-0.78; P = 0.033). In pathologic myopia, prior retinal inflammation is independently associated with more frequent multifocal involvement, higher risk of incident atrophy, and a substantially faster atrophy-expansion. Beyond mechanical factors, inflammation seems to be a key driver of atrophic progression in this population.

#4

Revisiting pathologic myopia: imaging evidence of an inflammatory component in the pathogenesis of myopic degeneration.

Frontiers in medicine2026

Pathologic myopia has traditionally been viewed as a degenerative disorder caused by mechanical stretching and choroidal ischemia. However, converging clinical, molecular, and imaging data increasingly suggest that chronic low-grade inflammation contributes to both the onset and progression of myopic retinal degeneration. Recent studies have identified inflammatory patterns-including multifocal choroiditis/punctate inner choroidopathy (MFC/PIC)-like lesions, periatrophic inflammatory "plumes," and secondary Multiple Evanescent White Dots Syndrome (MEWDS)-often localized at sites of retinal pigment epithelium-Bruch's membrane disruption. Parallel laboratory evidence indicates dysregulation of cytokines, activation of the complement cascade, and engagement of intracellular signaling pathways such as JAK-STAT within the myopic eye. Together, these findings support a model in which mechanical stress and hypoxia act as triggers for sustained immune activation, promoting extracellular-matrix remodeling, choroidal thinning, and progressive atrophy. Recognizing inflammation as an integral component of the pathophysiology of pathologic myopia may open new therapeutic perspectives, including immunomodulatory or complement-targeting approaches.

#5

Sex-Related Effects on the Clinical Presentation of Uveitis.

American journal of ophthalmology2026 Feb

The primary aim of this study was to determine sex-related patterns of uveitic entities. Secondary aims included sex-related patterns of uveitic complications. Retrospective clinical cohort study. 5703 participants presenting with uveitis from January 2009 to December 2023 were included. uveitis entities and complications. 2870 (50.3%) participants were female and 2831 (49.6%) were male. Males presented at a significantly younger age than females (42.2 vs 45.0). Significant sex-based differences were observed in the prevalence of specific uveitic conditions. Females were more likely to develop multifocal choroiditis (female: male ratio 1.818:1), Vogt-Koyanagi-Harada syndrome (female: male ratio 2.136:1), birdshot chorioretinopathy (female: male ratio 2.800:1, punctate inner choroidopathy (female: male ratio 6.571:1), drug-induced uveitis (female: male ratio 2.833:1), Crohn's disease (female: male ratio 3.714:1) and multiple evanescent white dot syndrome (female: male ratio 5.000:1). In contrast, males were more likely to develop acute posterior multifocal placoid pigment epitheliopathy (female: male ratio 0.364:1), sympathetic ophthalmia (female: male ratio 0.353:1) and syphilis (female: male ratio 0.404:1). Cataract was significantly more common in females, and this remained significant after adjusting for age at presentation, anatomical location and bilaterality. Cystoid macular edema and epiretinal membrane were more frequent in females, whereas retinal detachment occurred more often in males. Bilateral vision loss occurred in 238 patients (4.2%) and was significantly more common in females (4.9% vs 3.5%). Sex appears to be a key factor influencing the underlying etiology and clinical course of uveitis. These findings underscore the importance of considering sex as a biological variable in the diagnosis, monitoring, and management of uveitis.

Publicações recentes

Ver todas no PubMed

📚 EuropePMC142 artigos no totalmostrando 133

2026

Choroidal neovascularization secondary to punctate inner choroidopathy after resolution of multiple evanescent white dot syndrome: A case report.

Medicine
2026

Progressive development of dome-shaped macula and subsequent onset of punctate inner choroidopathy in a highly myopic patient: a 7-year follow-up case report.

American journal of ophthalmology case reports
2026

ROLE OF INFLAMMATION IN ATROPHY DEVELOPMENT AND PROGRESSION IN PATHOLOGIC MYOPIA.

Retina (Philadelphia, Pa.)
2026

Revisiting pathologic myopia: imaging evidence of an inflammatory component in the pathogenesis of myopic degeneration.

Frontiers in medicine
2026

Sex-Related Effects on the Clinical Presentation of Uveitis.

American journal of ophthalmology
2026

En Face Optical Coherence Tomography and OCT Angiography in the Pathoanatomy of Inflammatory Macular Disease.

American journal of ophthalmology
2026

Differences in epiretinal macrophage-like cells and associated retinochoroidal changes between multifocal choroiditis and punctate inner choroidopathy observed using widefield optical coherence tomography angiography.

Photodiagnosis and photodynamic therapy
2026

Near-Infrared Autofluorescence in Non-Infectious Uveitis: A Review.

Ocular immunology and inflammation
2025

Retinal phlebitis complicated by punctate inner choroidopathy-like lesions: a case report.

American journal of ophthalmology case reports
2026

Idiopathic Multifocal Choroiditis/Punctate Inner Choroidopathy as a Secondary Inflammatory Reaction to Lacquer Cracks: A Structural and Temporal Analysis.

American journal of ophthalmology
2025

Punctate Inner Choroidopathy Complicated by Multifocal Neovascularization and Schlaegel Lines.

Retina (Philadelphia, Pa.)
2026

Macular Complications Predict Visual Decline in Punctate Inner Choroidopathy.

Ophthalmology
2026

AI-Driven Optical Coherence Tomography Biomarkers for Choroidal Neovascularization Assessment in Punctate Inner Choroidopathy and Multifocal Choroiditis.

American journal of ophthalmology
2025

Minimum Imaging Sets for Diagnosis, Activity Assessment, and Complications in Noninfectious Posterior Uveitis - Multimodal Imaging in Uveitis (MUV) Task Force Report 9.

American journal of ophthalmology
2025

Noninfectious Uveitis Syndromes.

Advances in experimental medicine and biology
2025

Systemic Immunosuppression and Secondary Choroidal Neovascularisation in Patients with Punctate Inner Chorioretinopathy.

Ocular immunology and inflammation
2026

Punctate Inner Pachychoroidopathy Associated with Choroidal Neovascularization. A Case Report.

Ceska a slovenska oftalmologie : casopis Ceske oftalmologicke spolecnosti a Slovenske oftalmologicke spolecnosti
2025

Systematic Review of Clinical Utility of Multimodal Imaging in Noninfectious Posterior Uveitis: MUV Project Report 3.

American journal of ophthalmology
2025

Prevalence and clinical characteristics of ocular sarcoidosis among non-infectious uveitis in a Chinese tertiary ophthalmic center: a retrospective observational study.

BMC ophthalmology
2025

Long-term prognosis of punctate inner choroidopathy lesions in pathologic myopia and their relationship to lacquer cracks.

Scientific reports
2025

Choroidal Hyperreflective Foci Represent a Common Finding Across Different Types of Macular Atrophy.

Investigative ophthalmology &amp; visual science
2025

Choroidal neovascularization secondary to punctate inner choroidopathy vs myopia: clinical outcomes after 1-year of treatment.

Graefe's archive for clinical and experimental ophthalmology = Albrecht von Graefes Archiv fur klinische und experimentelle Ophthalmologie
2026

PUNCTATE INNER CHOROIDOPATHY-LIKE REACTION IN STAGE 3 EXTENSIVE MACULAR ATROPHY WITH PSEUDODRUSEN-LIKE APPEARANCE.

Retinal cases &amp; brief reports
2024

An update of multimodal imaging in white dot syndrome.

Oman journal of ophthalmology
2025

Infrared Autofluorescence to Identify Activity in Punctate Inner Choroidopathy.

Ophthalmic surgery, lasers &amp; imaging retina
2024

Atypical choroidal neovascular membrane.

American journal of ophthalmology case reports
2024

91-month follow-up of solitary punctate chorioretinitis in a Chinese patient.

BMC ophthalmology
2025

PUNCTATE INNER CHOROIDOPATHY AFTER PARS PLANA VITRECTOMY FOR HIGH MYOPIC FULL-THICKNESS MACULAR HOLE.

Retinal cases &amp; brief reports
2024

EXPLORING THE CHALLENGES OF DISTINGUISHING PUNCTATE INNER CHOROIDOPATHY FROM MULTIFOCAL CHOROIDITIS AND PANUVEITIS.

Retina (Philadelphia, Pa.)
2025

Schlaegel Lines 360 Degrees in Punctate Inner Choroidopathy.

Ophthalmology. Retina
2025

Recurrent Choroidal Neovascular Membrane as the Initial Presentation of Mycobacterium chimaera-Associated Serpiginoid Choroiditis.

Ocular immunology and inflammation
2024

Punctate Inner Choroidopathy (PIC) disease recurrence with inflammatory choroidal neovascular membrane (iCNVM) post-COVID-19 vaccine.

European journal of ophthalmology
2024

Clinical features and possible pathogenesis of multiple evanescent white dot syndrome with different retinal diseases and events: a narrative review.

International journal of ophthalmology
2024

Diagnostic Challenges in Inflammatory Choroidal Neovascularization.

Medicina (Kaunas, Lithuania)
2024

White Dot Syndromes: Report of Three Cases.

Case reports in ophthalmology
2024

Chorioretinopathy Post COVID-19: A Systematic Review and Prevalence Assessment, Unveiling Insights into an Emerging Ocular Entity.

Seminars in ophthalmology
2025

SEVERE RECURRENCE AND RETINAL INFLAMMATORY INFILTRATION AFTER CESSATION OF IMMUNOSUPPRESSION FOR MULTIFOCAL CHOROIDITIS AND PANUVEITIS.

Retinal cases &amp; brief reports
2024

Punctate inner choroidopathy: A review of the current diagnostic and therapeutic approaches.

Progress in retinal and eye research
2024

The multimodal imaging features and outcomes of multifocal choroiditis/punctate inner choroidopathy lesion with multiple evanescent white dot syndrome-like features: a retrospective study.

BMC ophthalmology
2024

Differential diagnosis of myopic choroidal neovascularization (mCNV): insights from multimodal imaging and treatment implications.

Graefe's archive for clinical and experimental ophthalmology = Albrecht von Graefes Archiv fur klinische und experimentelle Ophthalmologie
2025

TRANSDIFFERENTIATION AND INTRACHOROIDAL MIGRATION OF MELANOTIC RETINAL PIGMENT EPITHELIUM IN PUNCTATE INNER CHOROIDITIS.

Retinal cases &amp; brief reports
2023

PUNCTATE INNER PACHYCHOROIDOPATHY: Demographic and Clinical Features of Inner Choroidal Inflammation in Eyes with Pachychoroid Disease.

Retina (Philadelphia, Pa.)
2023

Punctate inner choroidopathy in common variable immunodeficiency associated with a pathogenic variant in the tumour necrosis factor receptor superfamily 13b (TNFRSF13B) gene - Case report and review of the literature.

Clinical immunology (Orlando, Fla.)
2023

SOLITARY PUNCTATE CHORIORETINITIS: A Unique Subtype of Punctate Inner Choroidopathy.

Retina (Philadelphia, Pa.)
2023

Challenges in posterior uveitis-tips and tricks for the retina specialist.

Journal of ophthalmic inflammation and infection
2023

Latest advances in white spot syndromes: New findings and interpretations.

Progress in retinal and eye research
2023

Association of Risk Variants in the CFH Gene With Elevated Levels of Coagulation and Complement Factors in Idiopathic Multifocal Choroiditis.

JAMA ophthalmology
2023

PRIMARY MULTIPLE EVANESCENT WHITE DOT SYNDROME AND MULTIPLE EVANESCENT WHITE DOT SYNDROME SECONDARY TO MULTIFOCAL CHOROIDITIS/PUNCTATE INNER CHOROIDOPATHY: A Comparative Study.

Retina (Philadelphia, Pa.)
2024

Corticosteroids Decrease the Incidence and Activity of Choroidal Neovascularization in Patients with Punctuate Inner Choroidopathy or Multifocal Choroiditis.

Ocular immunology and inflammation
2024

RECURRENCE OF ACUTE RETINOPATHY IN PSEUDOXANTHOMA ELASTICUM.

Retinal cases &amp; brief reports
2023

Adalimumab Biosimilar-Induced Autoimmunity-Related Sweet-Like Neutrophilic Dermatosis.

The American Journal of dermatopathology
2023

Similarities in the histological mouse model of early herpes simplex retinopathy with punctate inner choroidopathy and Ebola virus disease retinopathy.

European journal of ophthalmology
2022

MULTIMODAL IMAGING OF MULTIFOCAL CHOROIDITIS WITH ADAPTIVE OPTICS OPHTHALMOSCOPY.

Retinal cases &amp; brief reports
2022

PUNCTATE INNER CHOROIDOPATHY-LIKE REACTIONS IN UNRELATED RETINAL DISEASES.

Retina (Philadelphia, Pa.)
2023

Outcomes in PIC-Related CNV: Pooled Analysis of Individual Participant Data.

Ocular immunology and inflammation
2022

Spectrally resolved autofluorescence imaging in posterior uveitis.

Scientific reports
2022

Idiopathic Multifocal Choroiditis and Punctate Inner Choroidopathy - Evaluation of Risk Factors for Increased Relapse Rate: A 2-Year Prospective Observational Cohort Study.

Ophthalmologica. Journal international d'ophtalmologie. International journal of ophthalmology. Zeitschrift fur Augenheilkunde
2022

Punctate inner choroidopathy immediately after COVID-19 infection: a case report.

BMC ophthalmology
2022

Multimodal imaging of multiple areas of choroidal neovascularization in punctate inner choroidopathy.

Journal francais d'ophtalmologie
2021

Key Multimodal Fundus Imaging Findings to Recognize Multifocal Choroiditis in Patients With Pathological Myopia.

Frontiers in medicine
2022

ROLE OF OPTICAL COHERENCE TOMOGRAPHY ANGIOGRAPHY IN DETECTING AND MONITORING INFLAMMATORY CHOROIDAL NEOVASCULARIZATION.

Retina (Philadelphia, Pa.)
2021

Optical Coherence Tomography Findings of Underlying Choroidal Neovascularization in Punctate Inner Choroidopathy.

Frontiers in medicine
2022

Outcomes of adalimumab therapy in refractory punctate inner choroidopathy and multifocal choroiditis.

Graefe's archive for clinical and experimental ophthalmology = Albrecht von Graefes Archiv fur klinische und experimentelle Ophthalmologie
2022

PREVALENCE AND CHARACTERISTICS OF MULTIFOCAL CHOROIDITIS/PUNCTATE INNER CHOROIDOPATHY IN PATHOLOGIC MYOPIA EYES WITH PATCHY ATROPHY.

Retina (Philadelphia, Pa.)
2021

RPE disruption and hyper-transmission are early signs of secondary CNV with punctate inner choroidopathy in structure-OCT.

BMC ophthalmology
2021

Central Multifocal Choroiditis: Platelet Granularity as a Potential Marker for Treatment With Steroid-Sparing Immunomodulatory Therapy.

Frontiers in ophthalmology
2022

CORRELATION BETWEEN FOCAL CHOROIDAL EXCAVATION AND UNDERLYING RETINOCHOROIDAL DISEASE: A Pathological Hypothesis From Clinical Observation.

Retina (Philadelphia, Pa.)
2021

Inflammatory Choroidal Neovascular Membranes: Clinical Profile, Treatment Effectiveness, and Visual Prognosis.

Journal of ophthalmology
2022

Distinct Patterns of Choroidal Lesions in Punctate Inner Choroidopathy and Multifocal Choroiditis Determined by Heatmap Analysis.

Ocular immunology and inflammation
2022

Punctate inner choroidopathy reactivation following COVID-19: A case report.

European journal of ophthalmology
2022

Multifocal Evanescent White Dot Syndrome-like Phenotypes Associated with Inflammatory and Myopic Choroidal Neovascularization.

Ocular immunology and inflammation
2022

Idiopathic multifocal choroiditis and punctate inner choroidopathy: an evaluation in pregnancy.

Acta ophthalmologica
2021

Swept Source-Optical Coherence Tomography Angiography for Management of Secondary Choroidal Neovascularization in Punctate Inner Choroidopathy.

Case reports in ophthalmology
2022

Chorioretinal Atrophy in Punctate Inner Choroidopathy/multifocal Choroiditis: A Five-year Follow-up Study.

Ocular immunology and inflammation
2021

Punctate inner choroidopathy with atypical presentation.

Arquivos brasileiros de oftalmologia
2022

Use of Short-wave Blue Fundus Autofluorescence to Detect and Monitor Acute Regional Outer Retinopathy in Punctate Inner Choroidopathy.

Ocular immunology and inflammation
2022

OCTA versus dye angiography for the diagnosis and evaluation of neovascularisation in punctate inner choroidopathy.

The British journal of ophthalmology
2021

Patchy hyperautofluorescence as a predictive factor for the recurrence of punctate inner choroidopathy.

Photodiagnosis and photodynamic therapy
2022

Characteristics of punctate inner choroidopathy complicated by choroidal neovascularisation on Multispectral Imaging in comparison with other imaging modalities.

Ocular immunology and inflammation
2021

Multiple Evanescent White Dot Syndrome Presenting in a Patient With Punctate Inner Choroidopathy.

Journal of vitreoretinal diseases
2021

Efficacy and safety of certolizumab pegol in pregnant women with uveitis. Recommendations on the management with immunosuppressive and biologic therapies in uveitis during pregnancy.

Clinical and experimental rheumatology
2020

Occult inflammation detected by autofluorescence May Be the cause of idiopathic choroidal neovascularization.

American journal of ophthalmology case reports
2020

Rapid and spontaneous resolution of hemorrhagic macular hole retinal detachment and subretinal hemorrhages in an eye with pathologic myopia: a case report.

BMC ophthalmology
2022

Distribution and Progression of Inflammatory Chorioretinal Lesions Related to Multifocal Choroiditis and Their Correlations with Clinical Outcomes at 24 Months.

Ocular immunology and inflammation
2020

Merging Information From Infrared and Autofluorescence Fundus Images for Monitoring of Chorioretinal Atrophic Lesions.

Translational vision science &amp; technology
2021

DIFFERENTIAL RESPONSE TO GLUCOCORTICOID IMMUNOSUPPRESSION OF TWO DISTINCT INFLAMMATORY SIGNS ASSOCIATED WITH PUNCTATE INNER CHOROIDOPATHY.

Retina (Philadelphia, Pa.)
2021

[Choroidal neovascularization due to a punctate inner choroidopathy visualized by optical coherence tomography angiography].

Der Ophthalmologe : Zeitschrift der Deutschen Ophthalmologischen Gesellschaft
2021

The "Sponge sign": A novel feature of inflammatory choroidal neovascularization.

European journal of ophthalmology
2021

Optical Coherence Tomography Angiography Changes in Choroidal Vasculature following Treatment in Punctate Inner Choroidopathy.

Ocular immunology and inflammation
2020

Differentiating Multifocal Choroiditis and Punctate Inner Choroidopathy: A Cluster Analysis Approach.

American journal of ophthalmology
2020

Presence or absence of choroidal hyper-transmission by SD-OCT imaging distinguishes inflammatory from neovascular lesions in myopic eyes.

Graefe's archive for clinical and experimental ophthalmology = Albrecht von Graefes Archiv fur klinische und experimentelle Ophthalmologie
2021

Long-term Outcome of Zonal Outer Retinopathy in Punctate Inner Choroidopathy or Multifocal Choroiditis.

Ocular immunology and inflammation
2019

[White dot syndromes : Principles, diagnostics, and treatment].

Der Ophthalmologe : Zeitschrift der Deutschen Ophthalmologischen Gesellschaft
2019

Using optical coherence tomography angiography to guide the treatment of pathological myopic patients with submacular hemorrhage.

Photodiagnosis and photodynamic therapy
2020

Intraretinal Cystoid Spaces in Regression of Punctate Inner Choroidopathy Lesions.

Ocular immunology and inflammation
2019

Two-Year Outcome of Aflibercept for the Treatment of Choroidal Neovascularization in Punctate Inner Choroidopathy.

Case reports in ophthalmology
2020

Long-Term Outcome of Punctate Inner Choroidopathy or Multifocal Choroiditis with Active Choroidal Neovascularization Managed with Intravitreal Bevacizumab.

Ocular immunology and inflammation
2020

Punctate Inner Choroidopathy and Choroidal Neovascularization in Korean Patients.

Ocular immunology and inflammation
2020

Development of Secondary Choroidal Neovascularization in Focal Choroidal Excavation of Punctate Inner Choroidopathy.

Ocular immunology and inflammation
2019

Immunosuppressants and/or antivascular endothelial growth factor inhibitors in punctate inner choroidopathy? Follow-up results with optical coherence tomography angiography.

The British journal of ophthalmology
2018

Treatment of Punctate Inner Choroidopathy with Choroidal Neovascularization Using Corticosteroid and Intravitreal Ranibizumab.

BioMed research international
2018

An update on inflammatory choroidal neovascularization: epidemiology, multimodal imaging, and management.

Journal of ophthalmic inflammation and infection
2019

Etiologies and Characteristics of Choroidal Neovascularization in Young Chinese Patients.

Ophthalmologica. Journal international d'ophtalmologie. International journal of ophthalmology. Zeitschrift fur Augenheilkunde
2018

Long-term results of intravitreal bevacizumab and dexamethasone for the treatment of punctate inner choroidopathy associated with choroidal neovascularization: A case series.

SAGE open medical case reports
2019

Optical coherence tomography angiography in comparison with other multimodal imaging techniques in punctate inner choroidopathy.

The British journal of ophthalmology
2017

Optical Coherence Tomography Angiography of Punctate Inner Choroidopathy.

Case reports in ophthalmological medicine
2017

Optical Coherence Tomography Angiography Findings in Punctate Inner Choroidopathy.

Ophthalmic surgery, lasers &amp; imaging retina
2018

Risk Factors for Developing Choroidal Neovascular Membrane and Visual Loss in Punctate Inner Choroidopathy.

Ophthalmology
2017

Efficacy and safety of conbercept as a primary treatment for choroidal neovascularization secondary to punctate inner choroidopathy.

BMC ophthalmology
2017

Inflammatory choroidal neovascularization in Indian eyes: Etiology, clinical features, and outcomes to anti-vascular endothelial growth factor.

Indian journal of ophthalmology
2018

Intravitreal anti-VEGF treatment for choroidal neovascularization secondary to punctate inner choroidopathy.

International ophthalmology
2017

Multi-modal imaging and anatomic classification of the white dot syndromes.

International journal of retina and vitreous
2017

How to Differentiate Myopic Choroidal Neovascularization, Idiopathic Multifocal Choroiditis, and Punctate Inner Choroidopathy Using Clinical and Multimodal Imaging Findings.

Ophthalmic surgery, lasers &amp; imaging retina
2017

Observation and Clinical Pattern in Patients with White Dot Syndromes: The Role of Color Photography in Monitoring Ocular Changes in Long-Term Observation.

Medical science monitor : international medical journal of experimental and clinical research
2016

Idiopathic Multifocal Choroiditis.

Journal of ophthalmic &amp; vision research
2016

Optical Coherence Tomography Angiography for Detecting Choroidal Neovascularization Secondary to Punctate Inner Choroidopathy.

Ophthalmic surgery, lasers &amp; imaging retina
2017

Punctate inner choroidopathy: A review.

Survey of ophthalmology
2016

Combined treatment in punctate inner choroidopathy.

Therapeutics and clinical risk management
2017

Punctate inner choroidopathy complicated with exudative neurosensory detachment: A favourable response to treatment with systemic corticosteroids and intravitreal ranibizumab.

Archivos de la Sociedad Espanola de Oftalmologia
2017

Choroidal neovascularisation on optical coherence tomography angiography in punctate inner choroidopathy and multifocal choroiditis.

The British journal of ophthalmology
2016

Etiology and treatment of choroidal neovascularization in pediatric patients.

European journal of ophthalmology
2016

[Punctate Inner Choroidopathy].

Ceska a slovenska oftalmologie : casopis Ceske oftalmologicke spolecnosti a Slovenske oftalmologicke spolecnosti
2016

Adjunctive use of systematic retinal thickness map analysis to monitor disease activity in punctate inner choroidopathy.

Journal of ophthalmic inflammation and infection
2015

Choroidal Neovascularization Associated with Punctate Inner Choroidopathy: Combination of Intravitreal Anti-VEGF and Systemic Immunosuppressive Therapy.

Case reports in ophthalmology
2015

OPTICAL COHERENCE TOMOGRAPHY ANGIOGRAPHY AND WIDEFIELD FUNDUS AUTOFLUORESCENCE IN PUNCTATE INNER CHOROIDOPATHY.

Retinal cases &amp; brief reports
2015

The Fundus Autofluorescence Spectrum of Punctate Inner Choroidopathy.

Journal of ophthalmology
2016

Clinical Characteristics of Inflammatory Choroidal Neovascularization in a Chinese Population.

Ocular immunology and inflammation
2015

Punctate Inner Choroidopathy.

Case reports in ophthalmological medicine
2015

Clinical characteristics and antivascular endothelial growth factor effect of choroidal neovascularization in younger patients in Taiwan.

Taiwan journal of ophthalmology
2014

Punctate inner choroidopathy: a systematic review.

Medical hypothesis, discovery &amp; innovation ophthalmology journal
2015

Focal Choroidal Excavation in Multifocal Choroiditis and Punctate Inner Choroidopathy.

Ophthalmology
2015

Punctate inner choroidopathy in systemic lupus.

Journal francais d'ophtalmologie
2015

Spectral-domain optical coherence tomographic features of choroidal neovascular membranes in multifocal choroiditis and punctate inner choroidopathy.

Graefe's archive for clinical and experimental ophthalmology = Albrecht von Graefes Archiv fur klinische und experimentelle Ophthalmologie
Ver todos os 142 no EuropePMC

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Grupos ativos de quem convive com esta doença aqui no Raras

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Doenças relacionadas

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Referências e fontes

Bases de dados externas citadas neste artigo

Publicações científicas

Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.

  1. Choroidal neovascularization secondary to punctate inner choroidopathy after resolution of multiple evanescent white dot syndrome: A case report.
    Medicine· 2026· PMID 41790663mais citado
  2. Progressive development of dome-shaped macula and subsequent onset of punctate inner choroidopathy in a highly myopic patient: a 7-year follow-up case report.
    American journal of ophthalmology case reports· 2026· PMID 41716621mais citado
  3. ROLE OF INFLAMMATION IN ATROPHY DEVELOPMENT AND PROGRESSION IN PATHOLOGIC MYOPIA.
    Retina (Philadelphia, Pa.)· 2026· PMID 41701337mais citado
  4. Revisiting pathologic myopia: imaging evidence of an inflammatory component in the pathogenesis of myopic degeneration.
    Frontiers in medicine· 2026· PMID 41647512mais citado
  5. Sex-Related Effects on the Clinical Presentation of Uveitis.
    American journal of ophthalmology· 2026· PMID 41642701mais citado
  6. MEWDS-like Presentation Unmasking Sequential Bilateral Multifocal Choroiditis: Insights from Longitudinal Multimodal Imaging.
    Biomedicines· 2026· PMID 41898295recente

Bases de dados e fontes oficiais

Identificadores e referências canônicas usadas para montar este verbete.

  1. ORPHA:580951(Orphanet)
  2. MONDO:0035584(MONDO)
  3. GARD:7503(GARD (NIH))
  4. Busca completa no PubMed(PubMed)

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Coroidopatia interna punctiforme
Compêndio · Raras BR

Coroidopatia interna punctiforme

ORPHA:580951 · MONDO:0035584
Prevalência
1-9 / 1 000 000
CID-10
H31.0 · Cicatrizes coriorretinianas
CID-11
Início
Adult
Prevalência
0.0 (Worldwide)
MedGen
UMLS
C0730321
EuropePMC
Papers 10a
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