O arco aórtico, também referida como crossa da aorta, está localizado no tronco e é a saída comum do sangue bombeado pelo coração. Situa-se logo após a válvula aórtica.
Introdução
O que você precisa saber de cara
Arco aórtico direito é uma anomalia congênita rara onde a aorta emerge do coração e se curva para a direita em vez de para a esquerda. Pode ser assintomático ou causar compressão de estruturas adjacentes, como a traqueia e o esôfago.
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Entender a doença
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Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Linha do tempo da pesquisa
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Genética e causas
O que está alterado no DNA e como passa nas famílias
Nenhum gene associado encontrado
Os dados genéticos desta condição ainda estão sendo catalogados.
Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
Remédios, cuidados de apoio e o que precisa acompanhar
Onde tratar no SUS
Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)
🇧🇷 Atendimento SUS — Arco aórtico direito
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Publicações mais relevantes
Compression of the Left Brachiocephalic Vein by a Type II Right Aortic Arch: A Rare Vascular Anomaly With Unique Clinical Presentation.
Right-sided aortic arch (RAA) is an uncommon anatomical variation of the thoracic vasculature, occurring in approximately 0.1% of adults. In nearly half of these instances, the left subclavian artery follows an abnormal course. The left subclavian artery typically emerges from a tapered dilation at its origin from the aorta, referred to as Kommerell's diverticulum (KD). Based on available literature, only a few cases have been documented. We describe a 62-year-old female patient who presented with a painless chest bump persisting for four weeks. She reported no symptoms such as cough, shortness of breath, fainting, or difficulty swallowing. Upon chest inspection, the middle of the chest exhibited a mild protrusion. Her vital signs were stable, and both pulmonary and cardiovascular examinations were normal. After an initial workup, a CT angiogram of the chest was performed and revealed the presence of a RAA compressing the left brachiocephalic vein (LBCV ) in addition to an aberrant left subclavian artery (ALSA). In adults, right-sided aortic arch with an aberrant left subclavian artery originating from KD is a rare but typically silent anomaly. However, it can become clinically significant if complications arise, such as severe aneurysmal changes or compression of nearby mediastinal structures. Patients may then present with chest pain or dyspnea, coughing, and swallowing issues. In this case, the anomaly led to compression of the left brachiocephalic vein, resulting in its dilation and visible protrusion. Although standardized treatment guidelines are lacking, it is important to educate patients about the nature and potential risks of this condition. For those without symptoms, regular monitoring may be appropriate, with surgical intervention considered if complications emerge.
Isolated left common carotid artery: steal syndrome and neurological complications.
Isolated left common carotid artery (ILCCA) is a rare cardiovascular malformation. Its core imaging feature is the anomalous connection of the left common carotid artery (LCCA) to the pulmonary artery, rendering it the rarest subtype of right aortic arch malformation. Reversed blood flow in the LCCA has been identified in the vast majority of reported cases. This malformation induces a left-to-right shunt via the common carotid artery and the circle of Willis, which subsequently leads to LCCA-steal syndrome. To date, no studies have reported the composition of this left-to-right shunt nor the neurological complications secondary to LCCA-steal syndrome. This case report elucidates the composition of the left-to-right shunt and the underlying mechanism by which the malformation elicits the steal syndrome.
Outcomes of surgical repair of congenital vascular rings in children.
Vascular rings are rare anomalies of congenital cardiovascular. This study aimed to assess the outcome of surgical repair of congenital vascular rings in children. This retrospective study reviewed data from 237 patients with congenital vascular rings who underwent surgical division from January 2008 to October 2022. The mean age of patients was 12 months (Interquartile range, IQR, 6, 32 months) and their mean weight was 9.5 kg (IQR, 8, 14 kg). The data revealed that 153 patients (65%) were boys. The complete vascular rings consisted of a Double aortic arch (DAA, 33%), Right aortic arch (RAA) with left ligamentum arteriosum (LLA, 39%), and circumflex aorta (0.8%). The incomplete vascular rings consisted of a pulmonary artery sling (PAS, 26%), innominate artery compression syndrome (0.4%), and Left aortic arch (LAA) with Aberrant right subclavian artery (ARSCA, 0.8%). There were 3 hospital deaths (1.3%) and only one late death during the study. The overall mortality was 1.7% (4 patients). Eighteen patients underwent reintervention for complications. The overall survival rates at 1, 5, and 10 years were 98.3%, 98.3%, and 98.3%, respectively. The rate of freedom from residual symptoms at 1, 5, and 10 years was 97%, 91.3%, and 86.2%, respectively. The results show that surgical repair of congenital vascular rings in pediatric patients yields excellent outcomes: most patients' symptoms improved and only a small proportion required reintervention. Although the pulmonary artery sling forms an incomplete vascular ring, it is associated with a higher incidence of tracheal stenosis and an increased risk of persistent postoperative respiratory symptoms. These observations suggest that more proactive intraoperative management of tracheal stenosis should be considered during the primary operation.
Supernumerary transitional cervicothoracic vertebra and interrupted left subclavian artery reconstituted by a left vertebral arteria lusoria crossing a foramen transversarium.
We report an observation of a right aortic arch with an isolated left subclavian artery (Edwards III-C) occurring in association with a supernumerary transitional cervicothoracic vertebra. As a unique feature, reconstitution of the left subclavian artery involved a left vertebral arteria lusoria, resulting in the formation of a composite anomalous vessel that mimicked an aberrant subclavian artery, followed a retroesophageal course, and passed through the foramen transversarium of the supernumerary vertebra.
Neonatal Kommerell diverticulum with mid-ductal aneurysmal patent ductus arteriosus: serial imaging documentation of early natural history.
We report an exceptionally early diagnosis of a Kommerell diverticulum on the first day of life, distinguished by unusual mid-ductal aneurysmal dilatation of the patent ductus arteriosus. Serial echocardiography documented the serial evolution of spontaneous ductal closure and thrombosis formation. CT confirmed a right aortic arch with a retroesophageal Kommerell diverticulum. The infant remains asymptomatic under close surveillance. This case represents one of the youngest reported cases with serial imaging documentation, providing unique insights into the early natural history and highlighting management challenges in asymptomatic neonatal patients.
Publicações recentes
Outcomes of Staged Repair Following Systemic-to-Pulmonary Artery Shunt in Pulmonary Atresia with Ventricular Septal Defect.
Atypical cardiovocal syndrome associated with right aortic arch and Kommerell diverticulum.
"Migrant" Ductal Tissue in the Aortic Arch: A Substrate for Prostaglandin-Responsive Coarctation.
Compression of the Left Brachiocephalic Vein by a Type II Right Aortic Arch: A Rare Vascular Anomaly With Unique Clinical Presentation.
Isolated left common carotid artery: steal syndrome and neurological complications.
📚 EuropePMC743 artigos no totalmostrando 198
Compression of the Left Brachiocephalic Vein by a Type II Right Aortic Arch: A Rare Vascular Anomaly With Unique Clinical Presentation.
CureusIsolated left common carotid artery: steal syndrome and neurological complications.
Surgical and radiologic anatomy : SRAOutcomes of surgical repair of congenital vascular rings in children.
Journal of cardiothoracic surgeryRight aortic arch with cervical origin of left subclavian artery: Unusual arch anomaly associated with tetralogy of Fallot.
Annals of pediatric cardiologySupernumerary transitional cervicothoracic vertebra and interrupted left subclavian artery reconstituted by a left vertebral arteria lusoria crossing a foramen transversarium.
Surgical and radiologic anatomy : SRARight aortic arch with left innominate artery compression syndrome: An unusual vascular aetiology of stridor in a neonate with complex CHD.
Turk gogus kalp damar cerrahisi dergisiNeonatal Kommerell diverticulum with mid-ductal aneurysmal patent ductus arteriosus: serial imaging documentation of early natural history.
Cardiology in the youngHistological investigation of persistent fifth aortic arch with arch obstruction in a neonate.
Journal of cardiology casesRecurrent left internal carotid artery stenosis in a patient with intrathoracic carotid bifurcation and right aortic arch.
NeuroradiologyComprehensive defect detection in mouse embryos and the heart by combining automated phenotyping with novel population averages and atlases.
Differentiation; research in biological diversityPrenatal and postnatal determinants of clinical outcomes in congenital heart diseases: A 15-year retrospective cohort study.
Taiwanese journal of obstetrics & gynecologyTranscatheter aortic valve replacement in right aortic arch with mirror image branching.
BMC cardiovascular disordersRight Aortic Arch With Bilateral Ductus Arteriosus, Aberrant Left Subclavian Artery, Interrupted Left Carotid Artery.
Echocardiography (Mount Kisco, N.Y.)The Cardiovascular Anatomy of the Green Iguana (Iguana iguana): Heart Structure, Major Vessels, and Coelomic Circulation.
Anatomia, histologia, embryologiaVirtual Reality to Enhance Understanding of Congenital Heart Disease.
Journal of cardiovascular development and diseaseFrom stridor to symptom relief; management of pediatric Kommerell's diverticulum and vascular rings in Palestine [2016-2024]: a single center cohort study.
Frontiers in pediatricsEndovascular repair of the right arch and right descending with Kommerell diverticulum: a case report.
Journal of cardiothoracic surgeryDiagnostic and surgical challenges in atypical forms of esophageal atresia: A case series.
Pediatrics and neonatologyCongenital Isolation of a Common Carotid Artery: A Review of Cases, Phenotypes, and Embryology of a Rare Anomaly of the Aortic Arch System.
Pediatric cardiologyCoarctation on a right aortic arch: Minimally invasive imaging and management.
Radiology case reportsAnatomical variations in the branches of the aortic arch in Japanese patients.
Anatomical science internationalPrenatal Diagnosis of Isolated Right Aortic Arch: A Collaborative Approach to Management of Postnatal Aerodigestive Symptoms.
Pediatric pulmonologyAortic atresia, interrupted hypoplastic right aortic arch, single ventricle and bilateral arterial duct - a unique anatomy with surgical palliation.
Journal of cardiothoracic surgeryTracheal Compression on Chest X-ray Leading to the Diagnosis of Right Aortic Arch in 22q11.2 Deletion Syndrome.
CureusAbnormal fetal genitalia: two- and three-dimensional ultrasound assessment.
Journal of perinatal medicineRight aortic arch with a unique branching pattern, coarctation of the aorta, and vascular ring: a management conundrum.
Cardiology in the young[Two-stage Repair of Kommerell Diverticulum with Right Aortic Arch and Aberrant Left Subclavian Artery:Report of a Case].
Kyobu geka. The Japanese journal of thoracic surgeryDuctal stenting for hypoplastic left heart syndrome with right aortic arch associated with 20q11.2 microdeletion syndrome.
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Pediatric cardiologyThoracic Vascular Anomalies: Insights from Embryology and Imaging.
Radiographics : a review publication of the Radiological Society of North America, IncVascular rings in the current era: is this a new disease requiring a new approach?
Archives of disease in childhood. Education and practice editionCommon types of vascular rings: a pictorial guide.
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CureusIncidental Kommerell diverticulum with aberrant left subclavian artery and right aortic arch: a single-center observational study.
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The Annals of thoracic surgeryRobot-Assisted Laparoscopic Hiatal Hernia Repair in a Patient With Right Aortic Arch: Implications for Surgical Planning and Symptom Resolution.
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BMC pregnancy and childbirthAortopexy With Plication of Kommerell Diverticulum Is an Effective Alternative to Diverticulum Resection and Reimplantation of the Aberrant Left Subclavian Artery for Surgical Management of Vascular Rings in Children.
World journal for pediatric & congenital heart surgeryMechanical Thrombectomy for Acute Medium Vessel Occlusion Because of Paradoxical Cerebral Embolism in a Patient with a Right Aortic Arch: A Case Report.
Journal of neuroendovascular therapyCase report and literature review: fetal diagnosis of vascular ring with circumflex right aortic arch and unique aortic arch branching pattern.
Frontiers in cardiovascular medicinePersistent Fourth Right Aortic Arch in a White-Tailed Deer (Odocoileus virginianus ustus).
Anatomia, histologia, embryologiaRight Aortic Arch With Kommerell Diverticulum and a Rare Type of Isolated Left Subclavian Artery.
Echocardiography (Mount Kisco, N.Y.)Are all rings created equal? A single centre experience of fetal and paediatric vascular rings.
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Frontiers in cardiovascular medicineCase report: Innovative approach to esophageal cancer with right aortic arch: neoadjuvant immunotherapy and 3D reconstruction.
Frontiers in oncologyAortopathy in repaired tetralogy of Fallot and David procedure.
Cardiovascular diagnosis and therapyEndovascular single-branched stent graft to treat complicated type B aortic dissection involving aortic arch anomalies.
European journal of medical researchAnatomic characteristics of the right aortic arch with aberrant left subclavian artery in patients who do and do not undergo vascular ring repair.
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The journal of maternal-fetal & neonatal medicine : the official journal of the European Association of Perinatal Medicine, the Federation of Asia and Oceania Perinatal Societies, the International Society of Perinatal ObstetriciansDifferentiating Closely Resembling Fetal Aortic Arch Abnormalities Using Conventional and Four-Dimensional Echocardiography: A Pictorial Essay With Postnatal Outcomes.
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Cardiology in the youngA Unique Association of Right-Sided Aortic Arch With Kommerell's Diverticulum, Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia, and Typical Carcinoid: A Case Report.
CureusPrenatal diagnosis in fetal right aortic arch using chromosomal microarray analysis and whole exome sequencing: a Chinese single-center retrospective study.
Molecular cytogeneticsOutcomes of Patients Undergoing Surgery for Complete Vascular Rings.
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Frontiers in medicineAnalysis of prognostic risk factors and development of a predictive model for fetuses with right aortic arch with mirror-image branching: a prognostic evaluation method based on ultrasound parameter features.
Quantitative imaging in medicine and surgeryCT Angiography for Aortic Arch Anomalies: Prevalence, Diagnostic Efficacy, and Illustrative Findings.
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Diagnostics (Basel, Switzerland)Chronic regurgitation, weight loss, and lethargy in a 3-month-old intact female German Shepherd Dog.
Journal of the American Veterinary Medical AssociationRelationship Between Quantitative Tracheal Geometry and Clinical Course in Various Types of Vascular Ring.
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CureusAnomalous Origin of Left Pulmonary Artery From the Left Carotid Artery With a Right Aortic Arch and Aberrant Left Subclavian Artery in a Neonate With DiGeorge Syndrome.
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Open medicine (Warsaw, Poland)Implications of right aortic arch prenatal diagnosis: the multicentric nationwide ARCADE cohort.
Archives of disease in childhood. Fetal and neonatal editionDouble aortic arch: a comparison of fetal cardiovascular magnetic resonance, postnatal computed tomography and surgical findings.
Journal of cardiovascular magnetic resonance : official journal of the Society for Cardiovascular Magnetic ResonanceIsolation of the left innominate artery: When to operate?
Annals of pediatric cardiologyA case of right aortic arch type II combined with Kommerell's diverticulum and left innominate vein beneath the aortic arch.
Echocardiography (Mount Kisco, N.Y.)Right-Sided Aortic Arch: A Computed Tomography Angiography Investigation, A Systematic Review with Meta-Analysis.
Journal of clinical medicineClinical Presentation and Therapy of Tetralogy of Fallot and Double-Outlet Right Ventricle.
Advances in experimental medicine and biologyRight-Sided Aortic Arch With Isolated Left Subclavian Artery, Subclavian Steal Syndrome, and Right Bronchial Compression: A Case Report.
CureusPrenatal aortic arch development in double aortic arch: Understanding postnatal closure of left aortic arch: A case report.
Radiology case reportsAssociation of right aortic arch and agenesis of ductus arteriosus in prenatal tetralogy of Fallot spectrum and its clinical implications.
Prenatal diagnosisPrenatal echocardiography diagnosis of a novel combination of bilateral ductus arteriosus and cardiovascular anomalies: a case report and literature review.
Frontiers in cardiovascular medicine[Aortic Arch:Embryology and Remodeling].
No shinkei geka. Neurological surgeryTetralogy of Fallot With Aortic Origin of the Pulmonary Artery and Uncorrected Right Aortic Arch.
JACC. Case reportsRecurrent Pediatric Respiratory Distress From a Challenging Vascular Anomaly: The Uncrossing Operation for Circumflex Aorta.
JACC. Case reportsSurgical Management of Norwood Procedure for Atypical Aortic Arch.
World journal for pediatric & congenital heart surgerySevere hypotension in a dog undergoing persistent right aortic arch correction surgery after serratus plane block.
Journal of the American Veterinary Medical AssociationNavigating the Unexpected: Right Aortic Arch Unveiled During Left Heart Catheterization.
CureusCase Report: Right aortic arch with isolation of left brachiocephalic artery and ventricular septal defect.
Frontiers in cardiovascular medicine[Esophageal stenosis as a result of a right aortic arch in 2 cats].
Tierarztliche Praxis. Ausgabe K, Kleintiere/HeimtiereA case of Kommerell diverticulum in adolescence presented with dysphagia.
Surgical case reportsClarifying the Anatomy of Tetralogy of Fallot with S-shaped Ascending Aorta.
Pediatric cardiologyResolution of chronic regurgitation in an 8 month old Babydoll sheep by thoracoscopic treatment of a vascular ring anomaly.
Veterinary surgery : VS[Right aortic arch with mirror image branching : a rare cause of dysphagia].
Revue medicale de LiegeAdvances in Minimally Invasive Procedures of the Thoracic Cavity.
The Veterinary clinics of North America. Small animal practiceBovine Aortic Arch with an Aberrant Left Vertebral Artery in a 3-Year-Old Boy with VACTERL Association: A Case Report.
The American journal of case reportsDysplastic aberrant left subclavian artery originating from a thoracic intersegmental artery associated with a right aortic arch.
Surgical and radiologic anatomy : SRAPerioperative and Anesthetic Considerations in Vascular Rings and Slings.
Seminars in cardiothoracic and vascular anesthesiaRight-sided aortic arch with isolation of the left innominate artery and hypoplasia of the left internal carotid artery.
Surgical and radiologic anatomy : SRAContralateral Thoracotomy With Extracorporeal Circulation for Reoperative Resection of a Kommerell Diverticulum.
World journal for pediatric & congenital heart surgeryTetralogy of Fallot with vertebral defect and left aberrant subclavian artery: a rare occurrence.
The Egyptian heart journal : (EHJ) : official bulletin of the Egyptian Society of Cardiology[Right-sided upper lobectomy in a patient with right aortic arch: a case report and literature review].
KhirurgiiaAssociated Anomalies and Outcome in Patients with Prenatal Diagnosis of Aortic Arch Anomalies as Aberrant Right Subclavian Artery, Right Aortic Arch and Double Aortic Arch.
Diagnostics (Basel, Switzerland)[Genetic diagnosis and analysis of eight cases with central 22q11.2 deletion syndrome].
Zhonghua yi xue yi chuan xue za zhi = Zhonghua yixue yichuanxue zazhi = Chinese journal of medical geneticsPrenatal diagnosis of right aortic arch: associated anomalies and fetal prognosis according to different subtypes.
Journal of perinatal medicineIncreased Pulmonary-Aortic Interspace in Fetal Right Aortic Arch: A Matched Case-Control Study.
Fetal diagnosis and therapySurgical treatment for right-side aortic arch concomitant with Kommerell's diverticulum: techniques selection and follow-up results.
European journal of medical researchCase Report: Kommerell's diverticulum and left aberrant subclavian artery stenosis hybrid treatment with branched aortic stent-graft.
Frontiers in cardiovascular medicinePersistence of aerodigestive symptoms after vascular ring repair.
American journal of otolaryngology[Thoracoscopic Right Upper Lobectomy in a Patient with a Right Aortic Arch:Report of a Case].
Kyobu geka. The Japanese journal of thoracic surgeryCarotid-subclavian bypass and endovascular aortic repair of Kommerell's diverticulum with aberrant left subclavian artery: A case report.
World journal of clinical cases[Non-A Non-B Aortic Dissection Complicated with Right Aortic Arch Treated by Extended Thoracic Aortic Repair].
Kyobu geka. The Japanese journal of thoracic surgeryManagement of esophageal cancer in patients with a right aortic arch or double aortic arch: a case series of 34 cases.
Surgical endoscopyTotal arch replacement with frozen elephant trunk technique for Kommerell's diverticulum with a right-sided aortic arch and aberrant left subclavian artery.
Journal of cardiothoracic surgeryNarrowing Down the Symptomatology of Isolated Vascular Rings in Children.
Pediatric cardiologyRight Aortic Arch with Bicarotid Trunk and Isolated Left Subclavian Artery: Hitherto Unreported Pattern.
The Indian journal of radiology & imagingRare Combination of Right Aortic Arch, Aberrant Left Subclavian Artery and Absent Left Pulmonary Artery in a Boy with Tetralogy of Fallot.
International medical case reports journalUtility of the Angle between the Right Aortic Arch and First Branch for Detecting Double Aortic Arch via Fetal Echocardiography.
Fetal diagnosis and therapyIncremental value of fetal spatiotemporal image correlation echocardiography in the diagnosis of tetralogy of Fallot with disconnected pulmonary arteries with ductus arteriosus supplying the left pulmonary artery.
Annals of pediatric cardiologyThoracoscopic esophagectomy for thoracic esophageal cancer with right aortic arch and Kommerell diverticulum: a case report and literature review.
Frontiers in oncologyAssociation and Repair of Right Aortic Arch With Aberrant Left Subclavian Artery With Subclavian Stenosis.
World journal for pediatric & congenital heart surgery3D modeling and comparative analysis of the double arcus aorta case.
The international journal of cardiovascular imagingTreatment of a posterior cerebral artery aneurysm in the context of complex cardio-cerebrovascular variations using the Tubridge flow diverter.
Journal of cerebrovascular and endovascular neurosurgeryRare Vascular Anomalies in an Adult: Absent Left Pulmonary Artery With a Right-Sided Aortic Arch.
CureusA neonatal case of vascular ring with Alagille syndrome.
SAGE open medical case reportsRecurrent Inferior Laryngeal Nerve Preservation During Thyroid Surgery in a Patient with Right Aortic Arch: A Case Report.
The LaryngoscopeCommon arterial trunk (Van Praagh type A3), absent right pulmonary artery and right aortic arch in a cyanotic child.
Indian journal of thoracic and cardiovascular surgeryUnusual Vascular Ring in the Fetus.
Pediatric cardiologyExploring the Role of Modified Vascular Anatomical Molding (MVAM) in Prenatal Diagnosis Teaching and Prognosis Prediction of Fetal Complex Congenital Heart Disease (CCHD): A Preliminary Study.
International journal of general medicine[The image is the key: unilateral absence of a branch of the pulmonary artery].
Andes pediatrica : revista Chilena de pediatriaChallenges During Esophagectomy in Presence of Thoracic Anatomical Anomalies: A Report of Three Cases.
Anticancer researchClinical characteristics of tetralogy of Fallot with left pulmonary artery acute angulation on computed tomography.
Heart and vessels[Prenatally detected aortic arch anomalies and their consequences after birth].
Orvosi hetilapMultidisciplinary approach to vascular rings and vascular-related aerodigestive compression: a clinical practice review.
Translational pediatricsThe aortic uncrossing procedure.
The Journal of thoracic and cardiovascular surgeryRight Aortic Arch with Isolated Left Subclavian Artery in Association with Double Outlet Right Ventricle and Cor Triatriatum Sinister: Hitherto Unreported Association.
The Indian journal of radiology & imagingCarotid artery direct access for intracranial stenting of a stroke patient with an aberrant left common carotid artery and right aorta.
Journal of neurointerventional surgeryContemporary Outcomes in Fetuses Diagnosed with Vascular Rings.
Pediatric cardiologyThe prenatal diagnosis and prognosis of fetal right aortic arch and double aortic arch malformation: A single-center study.
The journal of obstetrics and gynaecology researchSubclavian steal syndrome in a right aortic arch with aberrant left subclavian artery atresia.
SAGE open medical case reportsKommerell's Diverticulum in a Right-Sided Aortic Arch With an Aberrant Left Subclavian Artery Hybrid Repair.
Vascular and endovascular surgeryComputed tomographic features of double aortic arch in six dogs.
Veterinary radiology & ultrasound : the official journal of the American College of Veterinary Radiology and the International Veterinary Radiology AssociationStrategies for Transcatheter Aortic Valve Replacement in Patients With a Right Aortic Arch.
Structural heart : the journal of the Heart TeamThe Subtlety of 22q11.2 Deletion Syndrome in a Preterm Neonate.
Neonatal network : NNSurgical treatment of a persistent right aortic arch with concurrent patent ductus arteriosus in a 4-month-old German shepherd dog.
Veterinary medicine and scienceInternational Multi-Institutional Experience with Presentation and Management of Aortic Arch Laterality in Aberrant Subclavian Artery and Kommerell's Diverticulum.
Annals of vascular surgeryA novel homozygous variant of TMEM260 induced cardiac malformation and neurodevelopmental abnormality: case report and literature review.
Frontiers in medicineHybrid Norwood for Hypoplastic Left Heart Syndrome With Rare Aortic Arch Anatomy.
World journal for pediatric & congenital heart surgeryImpact on the trachea in children with prenatally diagnosed vascular ring formed by a right aortic arch.
Pediatric pulmonologyPrenatal ultrasound findings, genetic testing, and literature review of Isolated left subclavian artery.
Echocardiography (Mount Kisco, N.Y.)Right Aortic Arch with Bicarotid Trunk and Aberrant Left Subclavian Artery.
The Indian journal of radiology & imagingUtility of fetal cardiovascular magnetic resonance imaging in assessing the fetuses with complete vascular ring.
Frontiers in pediatrics[A Case of Recurrent Lung Adenocarcinoma with Right Aortic Arch Treated with Pembrolizumab].
Gan to kagaku ryoho. Cancer & chemotherapyThe Impact of Prenatal Diagnosis on Clinical Outcomes of Isolated Vascular Rings From a Statewide Paediatric Cardiology Tertiary Service.
Heart, lung & circulationRetroaortic Innominate Vein in Association With Pulmonary Atresia/Major Aortopulmonary Collaterals.
Annals of thoracic surgery short reportsRight Subclavian Artery With Kommerell's Diverticulum: A Rare Cause of Dysphagia.
CureusPrenatal phenotype features and genetic etiology of the Williams-Beuren syndrome and literature review.
Frontiers in pediatricsSurgical Experience With Nine Cases of Obstructed Right Aortic Arch.
World journal for pediatric & congenital heart surgeryPost-operative Outcomes for Vascular Rings: A Systematic Review and Meta-analysis.
Journal of pediatric surgeryRight cervical aortic arch associated with anomaly of epiaortic vessels and haemodynamically significant obstruction between ascending and descending aorta. Extra-anatomic bypass graft between ascending and descending aorta and long-term follow-up.
Cardiology in the youngA rare adult case of asymptomatic double aortic arch accompanied by the right vertebral artery directly originating from the aortic arch.
Surgical and radiologic anatomy : SRADouble aortic arch: implications of antenatal diagnosis, differential growth of arches during pregnancy, associated abnormalities and postnatal outcome.
Ultrasound in obstetrics & gynecology : the official journal of the International Society of Ultrasound in Obstetrics and GynecologyTetralogy of Fallot Associated With Right Aortic Arch and Isolated Left Brachiocephalic Artery.
World journal for pediatric & congenital heart surgeryFive cases of endoscopically noted esophageal stenosis due to abnormal aortic angiogenesis.
Clinical journal of gastroenterologySingle-incision, off-pump repair of a right aortic arch with an aberrant left subclavian artery and diverticulum of Kommerell in an adult.
Multimedia manual of cardiothoracic surgery : MMCTS[Hybrid treatment of Kommerell diverticulum and giant aneurysm of intra-thoracic segment of aberrant left subclavian artery].
KhirurgiiaA natural systemic to pulmonary artery shunt.
Indian journal of thoracic and cardiovascular surgeryShort-term outcome after the prenatal diagnosis of right aortic arch.
Prenatal diagnosis[Total Arch Replacement using the Frozen Elephant Trunk for Kommerell Diverticulum with Right Aortic Arch:Report of a Case].
Kyobu geka. The Japanese journal of thoracic surgery[Staged Hybrid Repair of Extensive Thoracic Aortic Aneurysm with Right Aortic Arch and Isolated Left Subclavian Artery:Report of a Case].
Kyobu geka. The Japanese journal of thoracic surgerySubclavian steal syndrome associated with right aortic arch: A case report.
Frontiers in surgeryRight anterolateral thoracotomy with partial sternotomy for chronic type B aortic dissection with right aortic arch and Kommerell's diverticulum.
Asian cardiovascular & thoracic annalsA novel ZIC3 mutation in a Chinese family with heterotaxy and multiple types of congenital heart defect.
Prenatal diagnosisRetracted: Cases of Ultrasound-Diagnosed Right Aortic Arch with Right Arterial Duct and the Treatment.
Computational and mathematical methods in medicineGround-glass opacity in a patient with right aortic arch and no left pulmonary artery.
Journal of cardiothoracic surgerySubclavian Artery Access for Transcatheter Aortic Valve Replacement in a Right Aortic Arch.
JACC. Cardiovascular interventions3D black blood cardiovascular magnetic resonance atlases of congenital aortic arch anomalies and the normal fetal heart: application to automated multi-label segmentation.
Journal of cardiovascular magnetic resonance : official journal of the Society for Cardiovascular Magnetic ResonanceClinically diverse and perinatally lethal syndromes with urorectal septum malformation sequence.
American journal of medical genetics. Part AIncidental Vascular Findings in Computed Tomography Performed in the Qualification for the TAVI Procedure.
Diagnostics (Basel, Switzerland)Right aortic arch with common origin of right carotid and left innominate artery: A case report.
Clinical case reportsPrenatally diagnosed 16p11.2 copy number variations by SNP Array: A retrospective case series.
Clinica chimica acta; international journal of clinical chemistryIsolated Right Common Carotid Artery Arising from the Right Pulmonary Artery.
Radiology. Cardiothoracic imagingPersistent Patent Arterial Duct Rather Than a Ligament in the Setting of Diverticulum of Kommerell.
JACC. Case reportsDetermination of the best surgical strategy for thoracic esophageal resection concurrent with double aortic arch using a three-dimensional model: a case report.
Translational cancer researchDetection of Coronary Artery and Aortic Arch Anomalies in Patients with Tetralogy of Fallot Using CT Angiography.
Journal of clinical medicineAortic Arch Laterality in Chromosome 22q11.2 Deletion Syndrome: Male-Female Difference.
Clinical pediatricsSubclavian Steal Phenomenon Associated With Vascular Ring in an Infant Who Had a Prenatally Diagnosed Right Aortic Arch With an Atretic Aberrant Left Subclavian Artery.
Texas Heart Institute journalCongenital Anomalies of Aortic Arch: A Pictorial Essay.
The Indian journal of radiology & imagingRare association of absent pulmonary valve syndrome, complete atrioventricular canal defect, double outlet right ventricle, right aortic arch, and aberrant right subclavian artery in a fetal case.
Echocardiography (Mount Kisco, N.Y.)Thoracic endovascular aortic repair for chronic aortic dissection after total arch replacement for aberrant right subclavian artery: A case report.
SAGE open medical case reportsSuccessful Management in an Infant Patient of PHACE Syndrome with a Complicated Aortic Arch Anomaly.
Case reports in pediatricsSingle-stage repair of complex aortic arch anomaly with aortic regurgitation.
Indian journal of thoracic and cardiovascular surgeryThe Case of a 44-Year-Old Survivor of Unrepaired Tetralogy of Fallot, Right Aortic Arch and Abdominal Aortopulmonary Collateral Vessels.
Medicina (Kaunas, Lithuania)Case report: A rare combination of right aortic arch with right patent ductus arteriosus and right tracheal bronchus causing impaired respiratory function.
Frontiers in cardiovascular medicineClinical findings, surgical treatment and long-term outcome of dogs and cats with double aortic arch: four cases (2005-2022).
The Journal of small animal practiceManagement of prenatally detected vascular rings: a United Kingdom national survey.
Cardiology in the youngA rare case report: Tetralogy of Fallot, right aortic arch, isolated left subclavian from patent ductus arteriosus, neonatal aortopulmonary window, and hypoplastic right pulmonary artery.
JTCVS techniquesInterrupted Right Aortic Arch With Anomalous Origin of Left Pulmonary Artery From Ascending Aorta and Isolation of Left Subclavian Artery.
The Canadian journal of cardiologyUltrasound Evaluation of Subclavian Artery and Internal Thoracic Artery Before Coronary Artery Bypass Grafting as Part of Preoperative Vascular Assessment.
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Compression of the Left Brachiocephalic Vein by a Type II Right Aortic Arch: A Rare Vascular Anomaly With Unique Clinical Presentation.
- Isolated left common carotid artery: steal syndrome and neurological complications.
- Outcomes of surgical repair of congenital vascular rings in children.
- Supernumerary transitional cervicothoracic vertebra and interrupted left subclavian artery reconstituted by a left vertebral arteria lusoria crossing a foramen transversarium.
- Neonatal Kommerell diverticulum with mid-ductal aneurysmal patent ductus arteriosus: serial imaging documentation of early natural history.
- Outcomes of Staged Repair Following Systemic-to-Pulmonary Artery Shunt in Pulmonary Atresia with Ventricular Septal Defect.
- Atypical cardiovocal syndrome associated with right aortic arch and Kommerell diverticulum.
- "Migrant" Ductal Tissue in the Aortic Arch: A Substrate for Prostaglandin-Responsive Coarctation.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:99081(Orphanet)
- MONDO:0020417(MONDO)
- GARD:19640(GARD (NIH))
- Busca completa no PubMed(PubMed)
- Q7333452(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
