Raras
Buscar doenças, sintomas, genes...
Arco aórtico direito
ORPHA:99081CID-10 · Q25.4CID-11 · LA8B.2YDOENÇA RARA

O arco aórtico, também referida como crossa da aorta, está localizado no tronco e é a saída comum do sangue bombeado pelo coração. Situa-se logo após a válvula aórtica.

Mantido por Agente Raras·Colaborar como especialista →

Introdução

O que você precisa saber de cara

📋

Arco aórtico direito é uma anomalia congênita rara onde a aorta emerge do coração e se curva para a direita em vez de para a esquerda. Pode ser assintomático ou causar compressão de estruturas adjacentes, como a traqueia e o esôfago.

Pesquisas ativas
1 ensaio
2 total registrados no ClinicalTrials.gov
Publicações científicas
1.441 artigos
Último publicado: 2026 Apr 9
🏥
SUS: Cobertura mínimaScore: 15%
CID-10: Q25.4
🇧🇷Dados SUS / DATASUS
PROCEDIMENTOS SIGTAP (5)
0202010503
Cariótipo — bandas G, Q ou Rgenetic_test
0202010600
Pesquisa de microdeleções/microduplicações por FISHlab_test
0202010694
Sequenciamento completo do exoma (WES)rehabilitation
0202010260
Dosagem de alfa-fetoproteína
0301070040
Atendimento em reabilitação — doenças raras
Você se identifica com essa condição?
O Raras está aqui pra te apoiar — com ou sem diagnóstico

Encontrou um erro ou informação desatualizada? Sugira uma correção →

Entender a doença

Do básico ao detalhe, leia no seu ritmo

Preparando trilha educativa...

Sinais e sintomas

O que aparece no corpo e com que frequência cada sintoma acontece

Linha do tempo da pesquisa

Publicações por ano — veja quando o interesse científico cresceu
Anos de pesquisa1desde 2026
Total histórico1.441PubMed
Últimos 10 anos200publicações
Pico202462 papers
Linha do tempo
2026Hoje · 2026🧪 2019Primeiro ensaio clínico📈 2024Ano de pico
Publicações por ano (últimos 10 anos)

Encontrou um erro ou informação desatualizada? Sugira uma correção →

Genética e causas

O que está alterado no DNA e como passa nas famílias

🧬

Nenhum gene associado encontrado

Os dados genéticos desta condição ainda estão sendo catalogados.

Diagnóstico

Os sinais que médicos procuram e os exames que confirmam

Carregando...

Tratamento e manejo

Remédios, cuidados de apoio e o que precisa acompanhar

Pipeline de tratamentos
Pipeline regulatório — de medicamentos já aprovados a drogas em pesquisa exploratória.
·Pré-clínico2
Medicamentos catalogadosEnsaios clínicos· 0 medicamentos · 2 ensaios
Carregando informações de tratamento...

Onde tratar no SUS

Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

🇧🇷 Atendimento SUS — Arco aórtico direito

🗺️

Selecione um estado ou use sua localização para ver resultados.

Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.

Pesquisa ativa

Ensaios clínicos abertos e novidades científicas recentes

🟢 Recrutando agora

1 pesquisa recrutando participantes. Converse com seu médico sobre a possibilidade de participar.

Outros ensaios clínicos

2 ensaios clínicos encontrados, 1 ativos.

Distribuição por fase
Ver todos no ClinicalTrials.gov
🧪 Está conduzindo uma pesquisa?
Divulgue para pacientes e familiares que acompanham esta doença.
Divulgar pesquisa →

Publicações mais relevantes

Timeline de publicações
571 papers (10 anos)
#1

Compression of the Left Brachiocephalic Vein by a Type II Right Aortic Arch: A Rare Vascular Anomaly With Unique Clinical Presentation.

Cureus2026 Feb

Right-sided aortic arch (RAA) is an uncommon anatomical variation of the thoracic vasculature, occurring in approximately 0.1% of adults. In nearly half of these instances, the left subclavian artery follows an abnormal course. The left subclavian artery typically emerges from a tapered dilation at its origin from the aorta, referred to as Kommerell's diverticulum (KD). Based on available literature, only a few cases have been documented. We describe a 62-year-old female patient who presented with a painless chest bump persisting for four weeks. She reported no symptoms such as cough, shortness of breath, fainting, or difficulty swallowing. Upon chest inspection, the middle of the chest exhibited a mild protrusion. Her vital signs were stable, and both pulmonary and cardiovascular examinations were normal. After an initial workup, a CT angiogram of the chest was performed and revealed the presence of a RAA compressing the left brachiocephalic vein (LBCV ) in addition to an aberrant left subclavian artery (ALSA). In adults, right-sided aortic arch with an aberrant left subclavian artery originating from KD is a rare but typically silent anomaly. However, it can become clinically significant if complications arise, such as severe aneurysmal changes or compression of nearby mediastinal structures. Patients may then present with chest pain or dyspnea, coughing, and swallowing issues. In this case, the anomaly led to compression of the left brachiocephalic vein, resulting in its dilation and visible protrusion. Although standardized treatment guidelines are lacking, it is important to educate patients about the nature and potential risks of this condition. For those without symptoms, regular monitoring may be appropriate, with surgical intervention considered if complications emerge.

#2

Isolated left common carotid artery: steal syndrome and neurological complications.

Surgical and radiologic anatomy : SRA2026 Mar 16

Isolated left common carotid artery (ILCCA) is a rare cardiovascular malformation. Its core imaging feature is the anomalous connection of the left common carotid artery (LCCA) to the pulmonary artery, rendering it the rarest subtype of right aortic arch malformation. Reversed blood flow in the LCCA has been identified in the vast majority of reported cases. This malformation induces a left-to-right shunt via the common carotid artery and the circle of Willis, which subsequently leads to LCCA-steal syndrome. To date, no studies have reported the composition of this left-to-right shunt nor the neurological complications secondary to LCCA-steal syndrome. This case report elucidates the composition of the left-to-right shunt and the underlying mechanism by which the malformation elicits the steal syndrome.

#3

Outcomes of surgical repair of congenital vascular rings in children.

Journal of cardiothoracic surgery2026 Mar 02

Vascular rings are rare anomalies of congenital cardiovascular. This study aimed to assess the outcome of surgical repair of congenital vascular rings in children. This retrospective study reviewed data from 237 patients with congenital vascular rings who underwent surgical division from January 2008 to October 2022. The mean age of patients was 12 months (Interquartile range, IQR, 6, 32 months) and their mean weight was 9.5 kg (IQR, 8, 14 kg). The data revealed that 153 patients (65%) were boys. The complete vascular rings consisted of a Double aortic arch (DAA, 33%), Right aortic arch (RAA) with left ligamentum arteriosum (LLA, 39%), and circumflex aorta (0.8%). The incomplete vascular rings consisted of a pulmonary artery sling (PAS, 26%), innominate artery compression syndrome (0.4%), and Left aortic arch (LAA) with Aberrant right subclavian artery (ARSCA, 0.8%). There were 3 hospital deaths (1.3%) and only one late death during the study. The overall mortality was 1.7% (4 patients). Eighteen patients underwent reintervention for complications. The overall survival rates at 1, 5, and 10 years were 98.3%, 98.3%, and 98.3%, respectively. The rate of freedom from residual symptoms at 1, 5, and 10 years was 97%, 91.3%, and 86.2%, respectively. The results show that surgical repair of congenital vascular rings in pediatric patients yields excellent outcomes: most patients' symptoms improved and only a small proportion required reintervention. Although the pulmonary artery sling forms an incomplete vascular ring, it is associated with a higher incidence of tracheal stenosis and an increased risk of persistent postoperative respiratory symptoms. These observations suggest that more proactive intraoperative management of tracheal stenosis should be considered during the primary operation.

#4

Supernumerary transitional cervicothoracic vertebra and interrupted left subclavian artery reconstituted by a left vertebral arteria lusoria crossing a foramen transversarium.

Surgical and radiologic anatomy : SRA2026 Feb 19

We report an observation of a right aortic arch with an isolated left subclavian artery (Edwards III-C) occurring in association with a supernumerary transitional cervicothoracic vertebra. As a unique feature, reconstitution of the left subclavian artery involved a left vertebral arteria lusoria, resulting in the formation of a composite anomalous vessel that mimicked an aberrant subclavian artery, followed a retroesophageal course, and passed through the foramen transversarium of the supernumerary vertebra.

#5

Neonatal Kommerell diverticulum with mid-ductal aneurysmal patent ductus arteriosus: serial imaging documentation of early natural history.

Cardiology in the young2026 Feb 13

We report an exceptionally early diagnosis of a Kommerell diverticulum on the first day of life, distinguished by unusual mid-ductal aneurysmal dilatation of the patent ductus arteriosus. Serial echocardiography documented the serial evolution of spontaneous ductal closure and thrombosis formation. CT confirmed a right aortic arch with a retroesophageal Kommerell diverticulum. The infant remains asymptomatic under close surveillance. This case represents one of the youngest reported cases with serial imaging documentation, providing unique insights into the early natural history and highlighting management challenges in asymptomatic neonatal patients.

Publicações recentes

Ver todas no PubMed

📚 EuropePMC743 artigos no totalmostrando 198

2026

Compression of the Left Brachiocephalic Vein by a Type II Right Aortic Arch: A Rare Vascular Anomaly With Unique Clinical Presentation.

Cureus
2026

Isolated left common carotid artery: steal syndrome and neurological complications.

Surgical and radiologic anatomy : SRA
2026

Outcomes of surgical repair of congenital vascular rings in children.

Journal of cardiothoracic surgery
2025

Right aortic arch with cervical origin of left subclavian artery: Unusual arch anomaly associated with tetralogy of Fallot.

Annals of pediatric cardiology
2026

Supernumerary transitional cervicothoracic vertebra and interrupted left subclavian artery reconstituted by a left vertebral arteria lusoria crossing a foramen transversarium.

Surgical and radiologic anatomy : SRA
2026

Right aortic arch with left innominate artery compression syndrome: An unusual vascular aetiology of stridor in a neonate with complex CHD.

Turk gogus kalp damar cerrahisi dergisi
2026

Neonatal Kommerell diverticulum with mid-ductal aneurysmal patent ductus arteriosus: serial imaging documentation of early natural history.

Cardiology in the young
2025

Histological investigation of persistent fifth aortic arch with arch obstruction in a neonate.

Journal of cardiology cases
2026

Recurrent left internal carotid artery stenosis in a patient with intrathoracic carotid bifurcation and right aortic arch.

Neuroradiology
2026

Comprehensive defect detection in mouse embryos and the heart by combining automated phenotyping with novel population averages and atlases.

Differentiation; research in biological diversity
2026

Prenatal and postnatal determinants of clinical outcomes in congenital heart diseases: A 15-year retrospective cohort study.

Taiwanese journal of obstetrics & gynecology
2026

Transcatheter aortic valve replacement in right aortic arch with mirror image branching.

BMC cardiovascular disorders
2026

Right Aortic Arch With Bilateral Ductus Arteriosus, Aberrant Left Subclavian Artery, Interrupted Left Carotid Artery.

Echocardiography (Mount Kisco, N.Y.)
2026

The Cardiovascular Anatomy of the Green Iguana (Iguana iguana): Heart Structure, Major Vessels, and Coelomic Circulation.

Anatomia, histologia, embryologia
2025

Virtual Reality to Enhance Understanding of Congenital Heart Disease.

Journal of cardiovascular development and disease
2025

From stridor to symptom relief; management of pediatric Kommerell's diverticulum and vascular rings in Palestine [2016-2024]: a single center cohort study.

Frontiers in pediatrics
2025

Endovascular repair of the right arch and right descending with Kommerell diverticulum: a case report.

Journal of cardiothoracic surgery
2025

Diagnostic and surgical challenges in atypical forms of esophageal atresia: A case series.

Pediatrics and neonatology
2025

Congenital Isolation of a Common Carotid Artery: A Review of Cases, Phenotypes, and Embryology of a Rare Anomaly of the Aortic Arch System.

Pediatric cardiology
2026

Coarctation on a right aortic arch: Minimally invasive imaging and management.

Radiology case reports
2025

Anatomical variations in the branches of the aortic arch in Japanese patients.

Anatomical science international
2025

Prenatal Diagnosis of Isolated Right Aortic Arch: A Collaborative Approach to Management of Postnatal Aerodigestive Symptoms.

Pediatric pulmonology
2025

Aortic atresia, interrupted hypoplastic right aortic arch, single ventricle and bilateral arterial duct - a unique anatomy with surgical palliation.

Journal of cardiothoracic surgery
2025

Tracheal Compression on Chest X-ray Leading to the Diagnosis of Right Aortic Arch in 22q11.2 Deletion Syndrome.

Cureus
2025

Abnormal fetal genitalia: two- and three-dimensional ultrasound assessment.

Journal of perinatal medicine
2025

Right aortic arch with a unique branching pattern, coarctation of the aorta, and vascular ring: a management conundrum.

Cardiology in the young
2025

[Two-stage Repair of Kommerell Diverticulum with Right Aortic Arch and Aberrant Left Subclavian Artery:Report of a Case].

Kyobu geka. The Japanese journal of thoracic surgery
2025

Ductal stenting for hypoplastic left heart syndrome with right aortic arch associated with 20q11.2 microdeletion syndrome.

Cardiology in the young
2025

Challenges of Long-Gap Esophageal Atresia Repair in a Patient With Tetralogy of Fallot and Right Aortic Arch.

Cureus
2025

Kommerell's Diverticulum Masquerading in a Right Aortic Arch: A Vascular Surprise.

Methodist DeBakey cardiovascular journal
2026

A Rare Case of Posterior Malalignment VSD with Interrupted Right Arch and Isolated Left Common Carotid Artery.

Pediatric cardiology
2025

Thoracic Vascular Anomalies: Insights from Embryology and Imaging.

Radiographics : a review publication of the Radiological Society of North America, Inc
2026

Vascular rings in the current era: is this a new disease requiring a new approach?

Archives of disease in childhood. Education and practice edition
2026

Common types of vascular rings: a pictorial guide.

Archives of disease in childhood. Education and practice edition
2025

Ligamentum Arteriosum Calcification Associated With Kommerell Diverticulum Mimicking a Foreign Body in the Esophagus: A Case Report.

Cureus
2025

Incidental Kommerell diverticulum with aberrant left subclavian artery and right aortic arch: a single-center observational study.

Quantitative imaging in medicine and surgery
2025

A rare case of right aortic arch with mirror-image branching and vascular ring in an adult patient.

Radiology case reports
2025

Early Resection of Kommerell Diverticulum and Revascularization in Children With Right Aortic Arch and Aberrant Left Subclavian Artery.

The Annals of thoracic surgery
2025

Robot-Assisted Laparoscopic Hiatal Hernia Repair in a Patient With Right Aortic Arch: Implications for Surgical Planning and Symptom Resolution.

Cureus
2024

[MÖB-03] Extra-Pericardial Modified Blalock-Taussig Shunt Via Sternotomy in Patients with A Right Aortic Arch.

Turk gogus kalp damar cerrahisi dergisi
2025

Endovascular treatment of a descending thoracic aorta aneurysm in a patient with right sided aortic arch: a case report.

CVIR endovascular
2025

Right aortic arch with aberrant left subclavian artery and anomalous Circle of Willis supply.

Radiology case reports
2025

Anomalous drainage of the ductus venosus into the coronary sinus: prenatal ultrasound diagnosis utilizing two-dimensional and three-dimensional imaging techniques and differential diagnosis.

BMC pregnancy and childbirth
2025

Aortopexy With Plication of Kommerell Diverticulum Is an Effective Alternative to Diverticulum Resection and Reimplantation of the Aberrant Left Subclavian Artery for Surgical Management of Vascular Rings in Children.

World journal for pediatric & congenital heart surgery
2025

Mechanical Thrombectomy for Acute Medium Vessel Occlusion Because of Paradoxical Cerebral Embolism in a Patient with a Right Aortic Arch: A Case Report.

Journal of neuroendovascular therapy
2025

Case report and literature review: fetal diagnosis of vascular ring with circumflex right aortic arch and unique aortic arch branching pattern.

Frontiers in cardiovascular medicine
2025

Persistent Fourth Right Aortic Arch in a White-Tailed Deer (Odocoileus virginianus ustus).

Anatomia, histologia, embryologia
2025

Right Aortic Arch With Kommerell Diverticulum and a Rare Type of Isolated Left Subclavian Artery.

Echocardiography (Mount Kisco, N.Y.)
2025

Are all rings created equal? A single centre experience of fetal and paediatric vascular rings.

Cardiology in the young
2026

Postnatal Outcomes in Prenatally Detected Vascular Rings.

Pediatric cardiology
2025

Prenatal ultrasound diagnosis, associated anomalies and pregnancy outcomes of fetal right aortic arch.

Frontiers in cardiovascular medicine
2024

Case report: Innovative approach to esophageal cancer with right aortic arch: neoadjuvant immunotherapy and 3D reconstruction.

Frontiers in oncology
2024

Aortopathy in repaired tetralogy of Fallot and David procedure.

Cardiovascular diagnosis and therapy
2024

Endovascular single-branched stent graft to treat complicated type B aortic dissection involving aortic arch anomalies.

European journal of medical research
2025

Anatomic characteristics of the right aortic arch with aberrant left subclavian artery in patients who do and do not undergo vascular ring repair.

Journal of cardiovascular computed tomography
2024

Combined fetal echocardiographic views improved prenatal differential diagnosis between right aortic arch and double aortic arch: a multicenter research.

The journal of maternal-fetal & neonatal medicine : the official journal of the European Association of Perinatal Medicine, the Federation of Asia and Oceania Perinatal Societies, the International Society of Perinatal Obstetricians
2025

Differentiating Closely Resembling Fetal Aortic Arch Abnormalities Using Conventional and Four-Dimensional Echocardiography: A Pictorial Essay With Postnatal Outcomes.

Journal of ultrasound in medicine : official journal of the American Institute of Ultrasound in Medicine
2024

Double innominate vein in a case with double aortic arch: a case report.

Journal of cardiothoracic surgery
2024

Very high take-off the right coronary artery with double outlet right ventricle.

Cardiology in the young
2024

A Unique Association of Right-Sided Aortic Arch With Kommerell's Diverticulum, Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia, and Typical Carcinoid: A Case Report.

Cureus
2024

Prenatal diagnosis in fetal right aortic arch using chromosomal microarray analysis and whole exome sequencing: a Chinese single-center retrospective study.

Molecular cytogenetics
2024

Outcomes of Patients Undergoing Surgery for Complete Vascular Rings.

Journal of the American College of Cardiology
2024

Evaluation of tracheal diameter and angles in fetuses with double aortic arch using prenatal ultrasound: implications for postnatal management.

Frontiers in medicine
2024

Analysis of prognostic risk factors and development of a predictive model for fetuses with right aortic arch with mirror-image branching: a prognostic evaluation method based on ultrasound parameter features.

Quantitative imaging in medicine and surgery
2024

CT Angiography for Aortic Arch Anomalies: Prevalence, Diagnostic Efficacy, and Illustrative Findings.

Diagnostics (Basel, Switzerland)
2024

Vascular Ring Surgical Repair: Re-Implantation of the Left Subclavian Artery into the Left Carotid Artery in a Pediatric Patient.

Diagnostics (Basel, Switzerland)
2025

Chronic regurgitation, weight loss, and lethargy in a 3-month-old intact female German Shepherd Dog.

Journal of the American Veterinary Medical Association
2025

Relationship Between Quantitative Tracheal Geometry and Clinical Course in Various Types of Vascular Ring.

Pediatric cardiology
2024

Multiple Major Aortopulmonary Collateral Arteries With Tetralogy of Fallot and Other Congenital Cardiac Disorders Detected in the Fourth Decade: A Report of a Rare Case.

Cureus
2024

Anomalous Origin of Left Pulmonary Artery From the Left Carotid Artery With a Right Aortic Arch and Aberrant Left Subclavian Artery in a Neonate With DiGeorge Syndrome.

Circulation. Cardiovascular imaging
2024

Advancing prenatal diagnosis: Echocardiographic detection of Scimitar syndrome in China - A case series.

Open medicine (Warsaw, Poland)
2025

Implications of right aortic arch prenatal diagnosis: the multicentric nationwide ARCADE cohort.

Archives of disease in childhood. Fetal and neonatal edition
2024

Double aortic arch: a comparison of fetal cardiovascular magnetic resonance, postnatal computed tomography and surgical findings.

Journal of cardiovascular magnetic resonance : official journal of the Society for Cardiovascular Magnetic Resonance
2024

Isolation of the left innominate artery: When to operate?

Annals of pediatric cardiology
2024

A case of right aortic arch type II combined with Kommerell's diverticulum and left innominate vein beneath the aortic arch.

Echocardiography (Mount Kisco, N.Y.)
2024

Right-Sided Aortic Arch: A Computed Tomography Angiography Investigation, A Systematic Review with Meta-Analysis.

Journal of clinical medicine
2024

Clinical Presentation and Therapy of Tetralogy of Fallot and Double-Outlet Right Ventricle.

Advances in experimental medicine and biology
2024

Right-Sided Aortic Arch With Isolated Left Subclavian Artery, Subclavian Steal Syndrome, and Right Bronchial Compression: A Case Report.

Cureus
2024

Prenatal aortic arch development in double aortic arch: Understanding postnatal closure of left aortic arch: A case report.

Radiology case reports
2024

Association of right aortic arch and agenesis of ductus arteriosus in prenatal tetralogy of Fallot spectrum and its clinical implications.

Prenatal diagnosis
2024

Prenatal echocardiography diagnosis of a novel combination of bilateral ductus arteriosus and cardiovascular anomalies: a case report and literature review.

Frontiers in cardiovascular medicine
2024

[Aortic Arch:Embryology and Remodeling].

No shinkei geka. Neurological surgery
2024

Tetralogy of Fallot With Aortic Origin of the Pulmonary Artery and Uncorrected Right Aortic Arch.

JACC. Case reports
2024

Recurrent Pediatric Respiratory Distress From a Challenging Vascular Anomaly: The Uncrossing Operation for Circumflex Aorta.

JACC. Case reports
2024

Surgical Management of Norwood Procedure for Atypical Aortic Arch.

World journal for pediatric & congenital heart surgery
2024

Severe hypotension in a dog undergoing persistent right aortic arch correction surgery after serratus plane block.

Journal of the American Veterinary Medical Association
2024

Navigating the Unexpected: Right Aortic Arch Unveiled During Left Heart Catheterization.

Cureus
2024

Case Report: Right aortic arch with isolation of left brachiocephalic artery and ventricular septal defect.

Frontiers in cardiovascular medicine
2024

[Esophageal stenosis as a result of a right aortic arch in 2 cats].

Tierarztliche Praxis. Ausgabe K, Kleintiere/Heimtiere
2024

A case of Kommerell diverticulum in adolescence presented with dysphagia.

Surgical case reports
2025

Clarifying the Anatomy of Tetralogy of Fallot with S-shaped Ascending Aorta.

Pediatric cardiology
2024

Resolution of chronic regurgitation in an 8 month old Babydoll sheep by thoracoscopic treatment of a vascular ring anomaly.

Veterinary surgery : VS
2024

[Right aortic arch with mirror image branching : a rare cause of dysphagia].

Revue medicale de Liege
2024

Advances in Minimally Invasive Procedures of the Thoracic Cavity.

The Veterinary clinics of North America. Small animal practice
2024

Bovine Aortic Arch with an Aberrant Left Vertebral Artery in a 3-Year-Old Boy with VACTERL Association: A Case Report.

The American journal of case reports
2024

Dysplastic aberrant left subclavian artery originating from a thoracic intersegmental artery associated with a right aortic arch.

Surgical and radiologic anatomy : SRA
2024

Perioperative and Anesthetic Considerations in Vascular Rings and Slings.

Seminars in cardiothoracic and vascular anesthesia
2024

Right-sided aortic arch with isolation of the left innominate artery and hypoplasia of the left internal carotid artery.

Surgical and radiologic anatomy : SRA
2024

Contralateral Thoracotomy With Extracorporeal Circulation for Reoperative Resection of a Kommerell Diverticulum.

World journal for pediatric & congenital heart surgery
2024

Tetralogy of Fallot with vertebral defect and left aberrant subclavian artery: a rare occurrence.

The Egyptian heart journal : (EHJ) : official bulletin of the Egyptian Society of Cardiology
2024

[Right-sided upper lobectomy in a patient with right aortic arch: a case report and literature review].

Khirurgiia
2024

Associated Anomalies and Outcome in Patients with Prenatal Diagnosis of Aortic Arch Anomalies as Aberrant Right Subclavian Artery, Right Aortic Arch and Double Aortic Arch.

Diagnostics (Basel, Switzerland)
2024

[Genetic diagnosis and analysis of eight cases with central 22q11.2 deletion syndrome].

Zhonghua yi xue yi chuan xue za zhi = Zhonghua yixue yichuanxue zazhi = Chinese journal of medical genetics
2024

Prenatal diagnosis of right aortic arch: associated anomalies and fetal prognosis according to different subtypes.

Journal of perinatal medicine
2024

Increased Pulmonary-Aortic Interspace in Fetal Right Aortic Arch: A Matched Case-Control Study.

Fetal diagnosis and therapy
2024

Surgical treatment for right-side aortic arch concomitant with Kommerell's diverticulum: techniques selection and follow-up results.

European journal of medical research
2023

Case Report: Kommerell's diverticulum and left aberrant subclavian artery stenosis hybrid treatment with branched aortic stent-graft.

Frontiers in cardiovascular medicine
2024

Persistence of aerodigestive symptoms after vascular ring repair.

American journal of otolaryngology
2023

[Thoracoscopic Right Upper Lobectomy in a Patient with a Right Aortic Arch:Report of a Case].

Kyobu geka. The Japanese journal of thoracic surgery
2023

Carotid-subclavian bypass and endovascular aortic repair of Kommerell's diverticulum with aberrant left subclavian artery: A case report.

World journal of clinical cases
2023

[Non-A Non-B Aortic Dissection Complicated with Right Aortic Arch Treated by Extended Thoracic Aortic Repair].

Kyobu geka. The Japanese journal of thoracic surgery
2024

Management of esophageal cancer in patients with a right aortic arch or double aortic arch: a case series of 34 cases.

Surgical endoscopy
2023

Total arch replacement with frozen elephant trunk technique for Kommerell's diverticulum with a right-sided aortic arch and aberrant left subclavian artery.

Journal of cardiothoracic surgery
2024

Narrowing Down the Symptomatology of Isolated Vascular Rings in Children.

Pediatric cardiology
2023

Right Aortic Arch with Bicarotid Trunk and Isolated Left Subclavian Artery: Hitherto Unreported Pattern.

The Indian journal of radiology & imaging
2023

Rare Combination of Right Aortic Arch, Aberrant Left Subclavian Artery and Absent Left Pulmonary Artery in a Boy with Tetralogy of Fallot.

International medical case reports journal
2024

Utility of the Angle between the Right Aortic Arch and First Branch for Detecting Double Aortic Arch via Fetal Echocardiography.

Fetal diagnosis and therapy
2023

Incremental value of fetal spatiotemporal image correlation echocardiography in the diagnosis of tetralogy of Fallot with disconnected pulmonary arteries with ductus arteriosus supplying the left pulmonary artery.

Annals of pediatric cardiology
2023

Thoracoscopic esophagectomy for thoracic esophageal cancer with right aortic arch and Kommerell diverticulum: a case report and literature review.

Frontiers in oncology
2024

Association and Repair of Right Aortic Arch With Aberrant Left Subclavian Artery With Subclavian Stenosis.

World journal for pediatric & congenital heart surgery
2022

3D modeling and comparative analysis of the double arcus aorta case.

The international journal of cardiovascular imaging
2024

Treatment of a posterior cerebral artery aneurysm in the context of complex cardio-cerebrovascular variations using the Tubridge flow diverter.

Journal of cerebrovascular and endovascular neurosurgery
2023

Rare Vascular Anomalies in an Adult: Absent Left Pulmonary Artery With a Right-Sided Aortic Arch.

Cureus
2023

A neonatal case of vascular ring with Alagille syndrome.

SAGE open medical case reports
2024

Recurrent Inferior Laryngeal Nerve Preservation During Thyroid Surgery in a Patient with Right Aortic Arch: A Case Report.

The Laryngoscope
2023

Common arterial trunk (Van Praagh type A3), absent right pulmonary artery and right aortic arch in a cyanotic child.

Indian journal of thoracic and cardiovascular surgery
2024

Unusual Vascular Ring in the Fetus.

Pediatric cardiology
2023

Exploring the Role of Modified Vascular Anatomical Molding (MVAM) in Prenatal Diagnosis Teaching and Prognosis Prediction of Fetal Complex Congenital Heart Disease (CCHD): A Preliminary Study.

International journal of general medicine
2023

[The image is the key: unilateral absence of a branch of the pulmonary artery].

Andes pediatrica : revista Chilena de pediatria
2023

Challenges During Esophagectomy in Presence of Thoracic Anatomical Anomalies: A Report of Three Cases.

Anticancer research
2023

Clinical characteristics of tetralogy of Fallot with left pulmonary artery acute angulation on computed tomography.

Heart and vessels
2023

[Prenatally detected aortic arch anomalies and their consequences after birth].

Orvosi hetilap
2023

Multidisciplinary approach to vascular rings and vascular-related aerodigestive compression: a clinical practice review.

Translational pediatrics
2024

The aortic uncrossing procedure.

The Journal of thoracic and cardiovascular surgery
2023

Right Aortic Arch with Isolated Left Subclavian Artery in Association with Double Outlet Right Ventricle and Cor Triatriatum Sinister: Hitherto Unreported Association.

The Indian journal of radiology & imaging
2024

Carotid artery direct access for intracranial stenting of a stroke patient with an aberrant left common carotid artery and right aorta.

Journal of neurointerventional surgery
2024

Contemporary Outcomes in Fetuses Diagnosed with Vascular Rings.

Pediatric cardiology
2023

The prenatal diagnosis and prognosis of fetal right aortic arch and double aortic arch malformation: A single-center study.

The journal of obstetrics and gynaecology research
2023

Subclavian steal syndrome in a right aortic arch with aberrant left subclavian artery atresia.

SAGE open medical case reports
2023

Kommerell's Diverticulum in a Right-Sided Aortic Arch With an Aberrant Left Subclavian Artery Hybrid Repair.

Vascular and endovascular surgery
2023

Computed tomographic features of double aortic arch in six dogs.

Veterinary radiology & ultrasound : the official journal of the American College of Veterinary Radiology and the International Veterinary Radiology Association
2023

Strategies for Transcatheter Aortic Valve Replacement in Patients With a Right Aortic Arch.

Structural heart : the journal of the Heart Team
2023

The Subtlety of 22q11.2 Deletion Syndrome in a Preterm Neonate.

Neonatal network : NN
2023

Surgical treatment of a persistent right aortic arch with concurrent patent ductus arteriosus in a 4-month-old German shepherd dog.

Veterinary medicine and science
2023

International Multi-Institutional Experience with Presentation and Management of Aortic Arch Laterality in Aberrant Subclavian Artery and Kommerell's Diverticulum.

Annals of vascular surgery
2023

A novel homozygous variant of TMEM260 induced cardiac malformation and neurodevelopmental abnormality: case report and literature review.

Frontiers in medicine
2023

Hybrid Norwood for Hypoplastic Left Heart Syndrome With Rare Aortic Arch Anatomy.

World journal for pediatric & congenital heart surgery
2023

Impact on the trachea in children with prenatally diagnosed vascular ring formed by a right aortic arch.

Pediatric pulmonology
2023

Prenatal ultrasound findings, genetic testing, and literature review of Isolated left subclavian artery.

Echocardiography (Mount Kisco, N.Y.)
2023

Right Aortic Arch with Bicarotid Trunk and Aberrant Left Subclavian Artery.

The Indian journal of radiology & imaging
2023

Utility of fetal cardiovascular magnetic resonance imaging in assessing the fetuses with complete vascular ring.

Frontiers in pediatrics
2023

[A Case of Recurrent Lung Adenocarcinoma with Right Aortic Arch Treated with Pembrolizumab].

Gan to kagaku ryoho. Cancer & chemotherapy
2023

The Impact of Prenatal Diagnosis on Clinical Outcomes of Isolated Vascular Rings From a Statewide Paediatric Cardiology Tertiary Service.

Heart, lung & circulation
2023

Retroaortic Innominate Vein in Association With Pulmonary Atresia/Major Aortopulmonary Collaterals.

Annals of thoracic surgery short reports
2023

Right Subclavian Artery With Kommerell's Diverticulum: A Rare Cause of Dysphagia.

Cureus
2023

Prenatal phenotype features and genetic etiology of the Williams-Beuren syndrome and literature review.

Frontiers in pediatrics
2023

Surgical Experience With Nine Cases of Obstructed Right Aortic Arch.

World journal for pediatric & congenital heart surgery
2023

Post-operative Outcomes for Vascular Rings: A Systematic Review and Meta-analysis.

Journal of pediatric surgery
2023

Right cervical aortic arch associated with anomaly of epiaortic vessels and haemodynamically significant obstruction between ascending and descending aorta. Extra-anatomic bypass graft between ascending and descending aorta and long-term follow-up.

Cardiology in the young
2023

A rare adult case of asymptomatic double aortic arch accompanied by the right vertebral artery directly originating from the aortic arch.

Surgical and radiologic anatomy : SRA
2023

Double aortic arch: implications of antenatal diagnosis, differential growth of arches during pregnancy, associated abnormalities and postnatal outcome.

Ultrasound in obstetrics & gynecology : the official journal of the International Society of Ultrasound in Obstetrics and Gynecology
2023

Tetralogy of Fallot Associated With Right Aortic Arch and Isolated Left Brachiocephalic Artery.

World journal for pediatric & congenital heart surgery
2023

Five cases of endoscopically noted esophageal stenosis due to abnormal aortic angiogenesis.

Clinical journal of gastroenterology
2023

Single-incision, off-pump repair of a right aortic arch with an aberrant left subclavian artery and diverticulum of Kommerell in an adult.

Multimedia manual of cardiothoracic surgery : MMCTS
2023

[Hybrid treatment of Kommerell diverticulum and giant aneurysm of intra-thoracic segment of aberrant left subclavian artery].

Khirurgiia
2023

A natural systemic to pulmonary artery shunt.

Indian journal of thoracic and cardiovascular surgery
2023

Short-term outcome after the prenatal diagnosis of right aortic arch.

Prenatal diagnosis
2023

[Total Arch Replacement using the Frozen Elephant Trunk for Kommerell Diverticulum with Right Aortic Arch:Report of a Case].

Kyobu geka. The Japanese journal of thoracic surgery
2023

[Staged Hybrid Repair of Extensive Thoracic Aortic Aneurysm with Right Aortic Arch and Isolated Left Subclavian Artery:Report of a Case].

Kyobu geka. The Japanese journal of thoracic surgery
2022

Subclavian steal syndrome associated with right aortic arch: A case report.

Frontiers in surgery
2023

Right anterolateral thoracotomy with partial sternotomy for chronic type B aortic dissection with right aortic arch and Kommerell's diverticulum.

Asian cardiovascular & thoracic annals
2023

A novel ZIC3 mutation in a Chinese family with heterotaxy and multiple types of congenital heart defect.

Prenatal diagnosis
2022

Retracted: Cases of Ultrasound-Diagnosed Right Aortic Arch with Right Arterial Duct and the Treatment.

Computational and mathematical methods in medicine
2022

Ground-glass opacity in a patient with right aortic arch and no left pulmonary artery.

Journal of cardiothoracic surgery
2022

Subclavian Artery Access for Transcatheter Aortic Valve Replacement in a Right Aortic Arch.

JACC. Cardiovascular interventions
2022

3D black blood cardiovascular magnetic resonance atlases of congenital aortic arch anomalies and the normal fetal heart: application to automated multi-label segmentation.

Journal of cardiovascular magnetic resonance : official journal of the Society for Cardiovascular Magnetic Resonance
2023

Clinically diverse and perinatally lethal syndromes with urorectal septum malformation sequence.

American journal of medical genetics. Part A
2022

Incidental Vascular Findings in Computed Tomography Performed in the Qualification for the TAVI Procedure.

Diagnostics (Basel, Switzerland)
2022

Right aortic arch with common origin of right carotid and left innominate artery: A case report.

Clinical case reports
2023

Prenatally diagnosed 16p11.2 copy number variations by SNP Array: A retrospective case series.

Clinica chimica acta; international journal of clinical chemistry
2022

Isolated Right Common Carotid Artery Arising from the Right Pulmonary Artery.

Radiology. Cardiothoracic imaging
2022

Persistent Patent Arterial Duct Rather Than a Ligament in the Setting of Diverticulum of Kommerell.

JACC. Case reports
2022

Determination of the best surgical strategy for thoracic esophageal resection concurrent with double aortic arch using a three-dimensional model: a case report.

Translational cancer research
2022

Detection of Coronary Artery and Aortic Arch Anomalies in Patients with Tetralogy of Fallot Using CT Angiography.

Journal of clinical medicine
2023

Aortic Arch Laterality in Chromosome 22q11.2 Deletion Syndrome: Male-Female Difference.

Clinical pediatrics
2022

Subclavian Steal Phenomenon Associated With Vascular Ring in an Infant Who Had a Prenatally Diagnosed Right Aortic Arch With an Atretic Aberrant Left Subclavian Artery.

Texas Heart Institute journal
2022

Congenital Anomalies of Aortic Arch: A Pictorial Essay.

The Indian journal of radiology & imaging
2022

Rare association of absent pulmonary valve syndrome, complete atrioventricular canal defect, double outlet right ventricle, right aortic arch, and aberrant right subclavian artery in a fetal case.

Echocardiography (Mount Kisco, N.Y.)
2022

Thoracic endovascular aortic repair for chronic aortic dissection after total arch replacement for aberrant right subclavian artery: A case report.

SAGE open medical case reports
2022

Successful Management in an Infant Patient of PHACE Syndrome with a Complicated Aortic Arch Anomaly.

Case reports in pediatrics
2022

Single-stage repair of complex aortic arch anomaly with aortic regurgitation.

Indian journal of thoracic and cardiovascular surgery
2022

The Case of a 44-Year-Old Survivor of Unrepaired Tetralogy of Fallot, Right Aortic Arch and Abdominal Aortopulmonary Collateral Vessels.

Medicina (Kaunas, Lithuania)
2022

Case report: A rare combination of right aortic arch with right patent ductus arteriosus and right tracheal bronchus causing impaired respiratory function.

Frontiers in cardiovascular medicine
2022

Clinical findings, surgical treatment and long-term outcome of dogs and cats with double aortic arch: four cases (2005-2022).

The Journal of small animal practice
2023

Management of prenatally detected vascular rings: a United Kingdom national survey.

Cardiology in the young
2022

A rare case report: Tetralogy of Fallot, right aortic arch, isolated left subclavian from patent ductus arteriosus, neonatal aortopulmonary window, and hypoplastic right pulmonary artery.

JTCVS techniques
2022

Interrupted Right Aortic Arch With Anomalous Origin of Left Pulmonary Artery From Ascending Aorta and Isolation of Left Subclavian Artery.

The Canadian journal of cardiology
2023

Ultrasound Evaluation of Subclavian Artery and Internal Thoracic Artery Before Coronary Artery Bypass Grafting as Part of Preoperative Vascular Assessment.

Academic radiology
Ver todos os 743 no EuropePMC

Associações

Organizações que acompanham esta doença — pra ter apoio e orientação

Ainda não temos associações cadastradas para Arco aórtico direito.

É de uma associação que acompanha esta doença? Fale com a gente →

Comunidades

Grupos ativos de quem convive com esta doença aqui no Raras

Ainda não existe comunidade no Raras para Arco aórtico direito

Pacientes, familiares e cuidadores se organizam em comunidades pra compartilhar experiências, fazer perguntas e se apoiar. Você pode ser o primeiro.

Tire suas dúvidas

Perguntas, dicas e experiências compartilhadas aqui na página

Participe da discussão

Faça login para postar dúvidas, compartilhar experiências e interagir com especialistas.

Fazer login

Doenças relacionadas

Doenças com sintomas parecidos — ajudam quem ainda está buscando diagnóstico

Ainda não achamos doenças com sintomas parecidos o suficiente.

Referências e fontes

Bases de dados externas citadas neste artigo

Publicações científicas

Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.

  1. Compression of the Left Brachiocephalic Vein by a Type II Right Aortic Arch: A Rare Vascular Anomaly With Unique Clinical Presentation.
    Cureus· 2026· PMID 41846622mais citado
  2. Isolated left common carotid artery: steal syndrome and neurological complications.
    Surgical and radiologic anatomy : SRA· 2026· PMID 41838163mais citado
  3. Outcomes of surgical repair of congenital vascular rings in children.
    Journal of cardiothoracic surgery· 2026· PMID 41772630mais citado
  4. Supernumerary transitional cervicothoracic vertebra and interrupted left subclavian artery reconstituted by a left vertebral arteria lusoria crossing a foramen transversarium.
    Surgical and radiologic anatomy : SRA· 2026· PMID 41711954mais citado
  5. Neonatal Kommerell diverticulum with mid-ductal aneurysmal patent ductus arteriosus: serial imaging documentation of early natural history.
    Cardiology in the young· 2026· PMID 41680967mais citado
  6. Outcomes of Staged Repair Following Systemic-to-Pulmonary Artery Shunt in Pulmonary Atresia with Ventricular Septal Defect.
    J Thorac Cardiovasc Surg· 2026· PMID 41966476recente
  7. Atypical cardiovocal syndrome associated with right aortic arch and Kommerell diverticulum.
    SA J Radiol· 2026· PMID 41959685recente
  8. "Migrant" Ductal Tissue in the Aortic Arch: A Substrate for Prostaglandin-Responsive Coarctation.
    JACC Case Rep· 2026· PMID 41954535recente

Bases de dados e fontes oficiais

Identificadores e referências canônicas usadas para montar este verbete.

  1. ORPHA:99081(Orphanet)
  2. MONDO:0020417(MONDO)
  3. GARD:19640(GARD (NIH))
  4. Busca completa no PubMed(PubMed)
  5. Q7333452(Wikidata)

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Arco aórtico direito
Compêndio · Raras BR

Arco aórtico direito

ORPHA:99081 · MONDO:0020417
CID-10
Q25.4 · Outras malformações congênitas da aorta
CID-11
Ensaios
1 ativos
MedGen
UMLS
C0035615
EuropePMC
Wikidata
Papers 10a
DiscussaoAtiva

Nenhuma novidade ainda. O agente esta monitorando.

0membros
0novidades