Localized cystic dilatation of the intrahepatic bile ducts as a distinct subtype of Caroli disease: a case report.

Caroli disease associated with autosomal recessive polycystic kidney disease: CT imaging features of a case report.

Next-Generation Sequencing Defines a Molecularly Confirmed ARPKD Core Within the Broader PKHD1-Associated Disease Spectrum.

Intrahepatic Versus Extrahepatic Biliary Tree Cysts: Outcomes after Surgical Resection in a Multicentric Study.

Open resection of gastroduodenal artery aneurysm with fistulization into the duodenum 17 years after coil embolization in a patient with Caroli disease.

Recommendations for management of pregnancy complicated by Caroli disease: A case report and literature review.

Gallstone Ileus Causing Mechanical Bowel Obstruction in a Patient With Caroli's Disease: A Case Report.

Splenic artery embolization in a patient with advanced Caroli's syndrome complicated by portal hypertension: a case report.

A case of pregnancy complicated by caroli disease.

Prenatal diagnosis and molecular characterization of PKHD1 variants in two Chinese fetuses with Caroli disease/syndrome.

Prenatal Recurrence of Ductal Plate Malformations Leads to PKHD1 Variant Reclassification.

Non-infectious Hepatic Cystic Lesions: A Narrative Review.

Liver Transplantation in Childhood: A 2-Year Single Center Experience.

Hepatic Cyst Infection in a Hemodialysis Patient with Autosomal Dominant Polycystic Kidney Disease Complicated by Non-symptomatic Caroli Disease.

[Variant anatomy of the gallbladder].

[A case of congenital hepatic fibrosis accompanied with multiple system abnormalities].

Surgical management of Caroli disease in a low-mid income country: a single-center study and review of literature.

Hepatic cysts: a survival guide.

Recurrent kidney stones in a young man with Caroli disease.

Prenatal Diagnosis of Caroli's Disease by Ultrasound and MRI Imaging.

Cystic lesions and their mimics involving the intrahepatic bile ducts and peribiliary space: diagnosis, complications, and management.

AIRE mutation in an elderly Caroli's patient with cholangitis and sepsis: a case report.

Caroli disease incidentally discovered in a 23-years old male: A case report.

Optimal transplant strategy of pediatric liver transplantation for fibropolycystic liver disease: Multicenter retrospective study in Japan.

Heritable Chronic Cholestatic Liver Diseases: A Review.

Association of congenital hepatic fibrosis and Caroli's syndrome: Two illustrative cases.

Liver Transplantation for Diffuse Form of Caroli Disease with Chronic Hepatitis B: A Case Report.

A case report of intrahepatic bile duct dilatation caused by WDR19 gene mutation and presented as Caroli syndrome.

Caroli's disease misdiagnosed as bile duct cystadenoma: A case report.

Histopathology and molecular pathology confirmed a diagnosis of atypical Caroli's syndrome: a case report.

Short-Term Outcome of Isolated Kidney Transplantation in Children with Autosomal Recessive Polycystic Kidney Disease: A Case Series and Literature Review.

A Unique Case of Caroli Disease in Kenya's Medical Landscape.

Caroli disease combined with Banti syndrome in a woman: a case report.

Compound heterozygous WDR19 variants associated with nephronophthisis, Caroli disease, refractory epilepsy and congenital bilateral central blindness: Case report.

Caroli disease with subcutaneous hemorrhage as the sole clinical manifestation: A case report.

Autosomal Recessive Polycystic Kidney Disease: Diagnosis, Prognosis, and Management.

Atypical cystic hepatorenal disease in a 40-year-old female: What is the diagnosis? A nephrology zebra.

Efficacy of rehabilitation initiated in the early phase after simultaneous deceased donor liver and kidney transplantation: A case report.

Nirmatrelvir/ritonavir-induced elevation of blood tacrolimus levels in a patient in the maintenance phase post liver transplantation.

Clinical, histopathological, and immunohistochemical spectrum of hepatolithiasis: a tertiary care center-based study from north India.

[Caroli disease: optimizing the choice of surgical strategy using 3D modeling, 3D printing and therapy].

Caroli syndrome associated with atrial septal defect and polydactyly: a case report.

Liver transplantation for biliary cysts: perioperative and long-term outcomes.

AN 84-YEAR-OLD PATIENT WITH CAROLI SYNDROME: WHAT IS THE PROGNOSIS OF THIS CONDITION?

Findings of cholangitis in a kidney transplant patient with Caroli disease on FDG PET/CT and MRI.

Transjugular intrahepatic portosystemic shunt for portal hypertension in a patient with Caroli disease.

Role of Cholangioscopy in a Patient With Hepatolithiasis and Caroli Disease.

ABO-incompatible Pediatric Liver Transplantation With Antibody and B-cell Depletion-free Immunosuppressive Protocol in High Consanguinity Communities.

[Introduction to the recommendations from the European Association for the Study of the Liver clinical practice guidelines on the management of cystic liver disease].

Diagnosis and management of choledochal cysts.

Hypersplenism caused by Caroli's disease.

[Robotic Left Hepatectomy Using the Glissonean Pedicle Approach for the Treatment of Caroli's Syndrome].

Liver Cancer Study Group of Japan Clinical Practice Guidelines for Intrahepatic Cholangiocarcinoma.

Caroli syndrome in a patient with psoriasis: A case report.

Caroli's syndrome with autosomal recessive polycystic kidney disease on fetal MRI: A case report.

[A case of Caroli's disease associated with intrahepatic cholangiocarcinoma].

An update on ductal plate malformations and fibropolycystic diseases of the liver.

EASL Clinical Practice Guidelines on the management of cystic liver diseases.

Rare variants in PKHD1 associated with Caroli syndrome: Two case reports.

Caroli's disease incidentally discovered in a 16-years-old female: a case report.

Imaging of fibropolycystic liver disease.

Esophagogastric variceal bleeding as a debut of Caroli's syndrome.

Heterotopic pancreas in the liver: a rare cause of recurrent attacks of cholangitis mimicking Caroli's disease.

Immune-complex membranoproliferative glomerulonephritis in liver cirrhosis secondary to Caroli's disease: a multi-hit process?

Repeated epigastric pain caused by Caroli's disease.

Incidental Detection of Caroli Syndrome With Unusual Findings.

Right hepatectomy with a cholangiojejunostomy and hepaticojejunostomy for unilobar Caroli's syndrome.

Caroli disease: an update on pathogenesis.

Clinical features of autosomal recessive polycystic kidney disease in the Japanese population and analysis of splicing in PKHD1 gene for determination of phenotypes.

The rate of cholangiocarcinoma in Caroli Disease A German multicenter study.

Notch-Hes1 signaling activation in Caroli disease and polycystic liver disease.

Biliary Tree Cysts and Surgical Treatment: Outcomes in a Multicentric Study.

Diffuse Versus Localized Caroli Disease: A Comparative MRCP Study.

Imaging manifestations of Caroli disease with autosomal recessive polycystic kidney disease: a case report and literature review.

Fibrocystic liver disease: novel concepts and translational perspectives.

Multisystem inflammatory syndrome in children associated with SARS-CoV-2 in a solid organ transplant recipient.

[A case of Caroli's disease confirmed by pathology, atypical symptoms and images].

Laparoscopic liver resection in Caroli disease: A single-centre case series.

[Clinicopathological features of Caroli disease/Caroli syndrome: an analysis of 21 cases].

Factors contributing to diagnostic delay of Caroli syndrome: a single-center, retrospective study.

Type IV choledochal cyst with polycystic kidney disease: a case report.

Risk of malignancy in Caroli disease and syndrome: A systematic review.

Caroli Disease: A Presentation of Acute Pancreatitis and Cholangitis.

Pituitary stalk interruption syndrome broadens the clinical spectrum of the TTC26 ciliopathy.

A rare missense variant in APC interrupts splicing and causes AFAP in two Danish families.

Caroli's syndrome evaluated by ultrasound and magnetic resonance imaging during pregnancy.

Revisiting Caroli Syndrome in a Tanzanian Patient.

Liver transplantation for severe portopulmonary hypertension: A case report and literature review.

[Laparoscopic Left Hemihepatectoy Applying Intraoperative Indocyanine Green Fluorescence Detection Counter Perfusion Method for Visualization].

[Surgical approach to benign bile duct alterations].

Endoscopic therapy for gastro-oesophageal varices of Caroli's syndrome: a case report.

Giant choledochal cyst and infantile polycystic kidneys as prenatal sonographic features of Caroli syndrome.

Diagnosis of Congenital Hepatic Fibrosis in Adulthood.

Technique and outcome of domino liver transplantation from patients with maple syrup urine disease: Expanding the donor pool for live donor liver transplantation.

Hepatobiliary and Pancreatic: Caroli syndrome: Egg-like sign on CT.

[Congenital hepatic fibrosis associated with Caroli's disease: a case report].

Large-duct cholangiopathies: aetiology, diagnosis and treatment.

Pathobiology of inherited biliary diseases: a roadmap to understand acquired liver diseases.

Langerhans' Cell Histiocytosis Masquerading as Caroli's Disease.

Congenital Cystic Lesions of the Bile Ducts: Imaging-Based Diagnosis.

[A cough in a patient with cholangitis in the course of caroli's disease. Case report].

Caroli Syndrome in a 6-Year-Old Rottweiler Dog.

Caroli Disease Revisited: A Case of a Kidney Transplant Patient With Autosomal Polycystic Kidney Disease and Recurrent Episodes of Cholangitis.

Magnetic resonance imaging of fibropolycystic liver disease: the spectrum of ductal plate malformations.

Role of Transplant in Biliary Disease.

Evaluation of Underlying Liver Disease and Its Severity in Children Referred for Liver Transplant: a Single-Center Report From Nemazee Hospital of Shiraz.

Haemostatic radiation therapy for a bleeding intraductal papillary neoplasm of the biliary tree.

Medullary sponge kidney and Caroli's disease in a patient with stricture urethra: look for the hidden in presence of the apparent.

A human ciliopathy with polycystic ovarian syndrome and multiple subcutaneous cysts: A rare case report.

Cholangiolocellular Carcinoma With "Ductal Plate Malformation" Pattern May Be Characterized by ARID1A Genetic Alterations.

Caroli syndrome: a clinical case with detailed histopathological analysis.

A teenage patient with autosomal recessive polycystic kidney disease, a splenorenal shunt, and congenital hepatic fibrosis: a case report.

Surgical treatment for monolobular Caroli's disease ‒ Report of a 30-year single center case series.

Blockade of Hedgehog Signaling Attenuates Biliary Cystogenesis in the Polycystic Kidney (PCK) Rat.

Caroli's disease associated with biliary papillomatosis and cholangiolithiasis.

An unusual case of pregnancy in a patient with Caroli's syndrome.

Liver resection and transplantation in Caroli disease and syndrome.

[Genetic diagnosis of Caroli syndrome with autosomal recessive polycystic kidney disease: a case report and literature review].

Starry Night on Liver MRI: An Unexpected Incidental Finding in a Healthy Recruit.

Laparoscopic hepatectomy for the treatment of Caroli's disease: a case report.

Choledochal Malformations: Surgical Implications of Radiologic Findings.

β-Catenin and interleukin-1β-dependent chemokine (C-X-C motif) ligand 10 production drives progression of disease in a mouse model of congenital hepatic fibrosis.

[A case of Caroli disease in Tibet, China].

Congenital hepatic fibrosis in a 9-year-old female patient - a case report.

Hepatic morphology abnormalities: beyond cirrhosis.

[Upper abdominal pain and febrile episodes in a 44-year-old Filipino woman].

Identification of occult active infection using PET-CT in a combined liver-kidney transplant candidate.

Abernethy malformation associated with Caroli's syndrome in a patient with a PKHD1 mutation: a case report.

Prenatal Diagnosis of Caroli Disease Associated With Autosomal Recessive Polycystic Kidney Disease by 3-D Ultrasound and Magnetic Resonance Imaging.

Diffuse-Type Caroli Disease with Characteristic Central Dot Sign Complicated by Multiple Intrahepatic and Common Bile Duct Stones.

Diversity of renal phenotypes in patients with WDR19 mutations: Two case reports.

Transjugular intrahepatic portosystemic shunt in a patient with Caroli's disease and portal cavernoma.

Pediatric choledochal cysts: diagnosis and current management.

Factors associated with long-term survival after liver transplantation: A retrospective cohort study.

Unusual Indications for a Liver Transplant: A Single-Center Experience.

Intrahepatic Biliary Duct Dilatation With an Unusual Choledochoscope Image.

Canine Breed-Specific Hepatopathies.

Cholangiocarcinoma: Current Knowledge and New Developments.

Accessory gallbladder in an intrahepatic location mimicking a cystic tumor of the liver: A case report.

Recurrent Cholangitis in a Patient with Autosomal Dominant Polycystic Kidney Disease (ADPKD) and Caroli's Disease.

Pylephlebitis: Through These Portals Pass Bad Bugs.

Should Caroli's disease be in the Todani classification?

Autosomal recessive polycystic kidney disease diagnosed in a 39 year-old women with kidney failure and cramps.

Ductal Plate Malformation in the Liver of Boxer Dogs: Clinical and Histological Features.

Contrast-enhanced magnetic resonance cholangiography with gadoxetic-acid-disodium for the detection of biliary-cyst communication in Caroli disease.

Imaging of Von Meyenburg complexes.

Compound heterozygous PKHD1 variants cause a wide spectrum of ductal plate malformations.

Proposal for an algorithm for liver transplantation in Caroli's disease and syndrome: putting an uncommon effort into a common task.

Surgical Management of Caroli's Disease: Single Center Experience and Review of the Literature.

Hepatorenal fibrocystic diseases in children.

Caroli's disease misdiagnosed as intraductal papillary neoplasm of the bile duct.

Caroli's Syndrome with Incidental Fibrolamellar Carcinoma on Liver Explant.

Renal cystic disease and liver abnormalities: polycystic kidney and hepatic disease and the association with Caroli disease.

Image of the month: Caroli syndrome: central dot sign on CT.

What is this sign? The 'central dot sign', associated with Caroli's disease and Caroli's syndrome.

Nephronophthisis 13: implications of its association with Caroli disease and altered intracellular localization of WDR19 in the kidney.

Education and imaging. Hepatology: "central dot sign" of Caroli syndrome.

Segmental cholangiectasia clinically worrisome for cholangiocarcinoma: comparison with recurrent pyogenic cholangitis.