Raras
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Schwannoma vestibular
ORPHA:252175CID-10 · D33.3CID-11 · 2A02.3DOENÇA RARA

O potencial evocado miogênico vestibular ou vestibular evoked myogenic potentials (VEMP) é um exame que avaliar que avalia os órgãos otolíticos, sendo testes complementares que pode ser utilizado para avaliar e inferir informações sobre a via do reflexo vestíbuloespinal e do reflexo vestíbulo ocular.

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Introdução

O que você precisa saber de cara

📋

Tumor benigno que se origina nos nervos vestibulares, responsáveis pelo equilíbrio e audição. Pode causar perda auditiva unilateral, zumbido e tontura.

Pesquisas ativas
20 ensaios
99 total registrados no ClinicalTrials.gov
Publicações científicas
4.751 artigos
Último publicado: 2026 Apr 15

Escala de raridade

CLASSIFICAÇÃO ORPHANET · BRASIL 2024
1-9 / 100 000
Ultra-rara
<1/50k
Muito rara
1/20k
Rara
1/10k
Pouco freq.
1/5k
Incomum
1/2k
Prevalência
2.0
Denmark
🏥
SUS: Sem cobertura SUSScore: 0%
CID-10: D33.3
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Sinais e sintomas

O que aparece no corpo e com que frequência cada sintoma acontece

Linha do tempo da pesquisa

Publicações por ano — veja quando o interesse científico cresceu
Anos de pesquisa1desde 2026
Total histórico4.751PubMed
Últimos 10 anos200publicações
Pico2026101 papers
Linha do tempo
2026Hoje · 2026🧪 1999Primeiro ensaio clínico
Publicações por ano (últimos 10 anos)

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Tratamento e manejo

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Onde tratar no SUS

Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

🇧🇷 Atendimento SUS — Schwannoma vestibular

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Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.

Pesquisa ativa

Ensaios clínicos abertos e novidades científicas recentes

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99 ensaios clínicos encontrados, 20 ativos.

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Ver todos no ClinicalTrials.gov
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Publicações mais relevantes

Timeline de publicações
3.159 papers (10 anos)

Mostrando amostra de 200 publicações de um total de 3.159

#1

Electromagnetic exposure changes human Schwann cell motility and transcriptomic profile of hearing-loss-related genes.

iScience2026 Mar 20

Schwann cells (SCs) are glial cells of the peripheral nervous system with functional plasticity in physio-pathological conditions, such as injury and oncotransformation. Interestingly, human SCs seem to develop, mature, and respond differently to other species to environmental challenges. Recently, concerns have been raised about the expansion of environmental electromagnetic fields (EMFs) and the increasing incidence of vestibular schwannoma (VS). We previously demonstrated that SCs respond to EMF by acquiring a state prone to oncotransformation. However, the biodependence of such transformation on the species (rodents versus humans) deserves clarification. Here, we obtained and characterized human SCs, showing that EMF affects proliferation, migration, and transcriptomic profile. The expression of motility proteins increased, while that of cell-to-cell adhesion proteins decreased. The functional clustering of genes differentially expressed matched those involved in hearing loss. In summary, we provide insights into the effects of chronic EMF on human SCs, highlighting its potential role in VS onset.

#2

Radiation-induced cavernous malformation in the brainstem after Gamma Knife radiosurgery for vestibular schwannoma: A case report and literature review.

Brain &amp; spine2026

Radiation-induced cavernous malformation (RICM) is an uncommon late complication of radiation therapy. There are even fewer cases reported after stereotactic radiosurgery (SRS). In this study, we investigated the clinical characteristics, management considerations, and outcomes of RICM following SRS. What are the clinical characteristics, management considerations, and outcomes of RICM following SRS? We describe a case of a 50-year-old woman previously treated with Gamma Knife® radiosurgery for a vestibular schwannoma. Almost two decades later, brain magnetic resonance imaging revealed a brainstem cavernous malformation in the brainstem, in the dose fall-off region adjacent to the target volume. A literature review was subsequently conducted to identify comparable cases, associated therapeutic strategies, and clinical outcomes. We identified 32 reported cases of RICM following SRS in the literature. The mean age at SRS was 65 years, with 57% being female. Mean latency to RICM development was 7.3 years. Our case demonstrated one of the longest latency periods reported for this complication. The patient had mild symptoms and was managed conservatively with surveillance imaging. Literature review revealed that 78% of cases underwent surgical management, predominantly those presenting with hemorrhage or progressive neurological symptoms. RICM represents a rare but clinically significant late complication of SRS that can occur after extended latency periods, even in adults. Management should be individualized based on symptoms, hemorrhage history, and lesion location. Further research is needed to develop more evidence-based management of RICM, and to better define the true incidence through long-term follow-up studies.

#3

Health-related quality of life in patients with vestibular schwannoma managed with observation, stereotactic radiosurgery or microsurgery: a systematic review and single-arm meta-analysis.

Journal of neurology2026 Mar 07

Health-related quality of life (HRQoL) is a key outcome in the management of vestibular schwannoma (VS). Although wait-and-scan (W&S), stereotactic radiosurgery (SRS), and microsurgery (MS) are established management strategies, their comparative effects on HRQoL remain unclear. This systematic review and meta-analysis aimed to synthesize HRQoL outcomes using the Penn Acoustic Neuroma Quality of Life (PANQOL) questionnaire and to pool PANQOL scores for W&S, SRS, and MS. A systematic search of PubMed and Embase was conducted up to February 2025. Eligible studies included patients with unilateral sporadic VS managed with W&S, SRS, or MS, with HRQoL assessed by PANQOL at least one year after diagnosis or intervention. Pooled mean PANQOL scores were calculated using single-arm meta-analyses. Minimal clinically important differences (MCIDs) were applied to assess relevance. 16 studies including 3745 patients were analyzed. The pooled PANQOL total score was 69.1 (95% CI 66.0-72.2) for W&S (n = 1,430), 66.9 (95% CI 62.7-71.2) for SRS (n = 864), and 61.3 (95% CI 57.2-65.4) for MS (n = 1451). Across domains, scores were the lowest for hearing and energy and the highest for facial function and anxiety. None of the between-strategy differences in total or domain scores exceeded established MCID thresholds. Substantial heterogeneity was present across all analyses (I2 > 75%). Patients with unilateral VS report broadly comparable HRQoL following W&S, SRS, or MS. Although numerical differences in PANQOL scores exist, they are not clinically meaningful. The observed heterogeneity highlights the need for standardized, prospective studies and international collaboration to better inform patient-centered decision-making.

#4

Prior surgical resection is a predictor of facial nerve function decrement after radiosurgery for vestibular schwannomas.

Clinical neurology and neurosurgery2026 May

Gamma Knife radiosurgery (GKRS) can serve as adjunctive treatment for vestibular schwannomas (VS) for residual or recurrent tumor after surgical resection. However, it is poorly understood whether prior surgical resection influences the risk of facial nerve injury from GKRS. An institutional database of GKRS treating adult VS was queried for patients with > 2 years of follow-up post-GKRS. Two cohorts were identified: patients with surgical resection prior to GKRS and patients receiving only GKRS. Facial nerve function was graded with the House-Brackmann (HB) scale pre-GKRS and until last follow-up. There were 31 patients in the surgery-GKRS cohort and 107 in the GKRS-only cohort. The surgery-GKRS cohort had a significantly lower median age (57.1 vs 63.6 years) and higher median tumor volume at time of GKRS (1.96 vs 0.84 cm3). Facial nerve function worsened within 2 years post-GKRS in 7/31 (22.6 %) of surgery-GKRS patients and 7/107 (6.5 %) of GKRS-only patients. At last follow-up, facial nerve function worsened in 5/31 (16.1 %) of surgery-GKRS patients and 3/107 (2.8 %) of GKRS-only patients. After controlling for patient, tumor, and radiosurgical parameters, prior surgical resection was significantly predictive of facial nerve function decrement after GKRS within 2 years and at last follow-up. Larger tumor volume was predictive of facial nerve function decrement at last follow-up. Pre-GK HB score was not predictive of new/worsened facial palsy. Patients with prior surgical resection may be at increased risk of new or worsened facial paresis after adjuvant or salvage GKRS compared to patients receiving upfront GKRS.

#5

Correlation of mastoid pneumatization and pneumatization of the posterior lip of internal auditory meatus and its implications during retrosigmoid craniotomy.

Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia2026 Feb 26

This study aimed to evaluate the relationship between the degree of mastoid pneumatization and the pneumatization of the posterior lip of the internal auditory meatus (IAM) in patients with vestibular schwannoma (VS). A retrospective analysis was performed on 224 patients who underwent retrosigmoid approach for VS excision (2011 to 2021). Mastoid pneumatization was graded based on Han et al classification on computed tomography (CT). Presence of pneumatization of the posterior lip of the IAM was assessed, and its correlation with mastoid and frontal sinus pneumatization, dominance of sigmoid sinus and jugular bulb position was analyzed. Pneumatization of the posterior lip of the IAM was observed in 39 patients (17.4%). Higher grades of mastoid pneumatization corresponding to grade 3 or 4 were found in 156 (69.6%) of patients. On univariate analysis, Manjila et al type 3 or 4 jugular bulb and higher grade of mastoid pneumatization were associated with pneumatization of the posterior lip of IAM. On multivariate analysis, only higher grade of mastoid pneumatization was independently associated with a pneumatization of the posterior lip of the IAM (OR, p = 0.003). Higher grades of mastoid pneumatization increased the risk of mastoid air cell entry during craniotomy (p = 0.0001) and was linked to postoperative cerebrospinal fluid (CSF) oto-rhinorrhoea. The degree of mastoid pneumatization has a strong independent correlation with pneumatization of the posterior lip of the IAM. Preoperative thin-slice temporal bone CT is essential in cases of extensive mastoid pneumatization to assess the posterior lip of the IAM for potential pneumatization.

Publicações recentes

Ver todas no PubMed

📚 EuropePMC2.900 artigos no totalmostrando 195

2026

Bicentric analysis of repeated retrosigmoid approach for recurrent vestibular schwannoma: facial nerve function and risk of second recurrence.

Journal of neuro-oncology
2026

Facial Nerve Tractography of Vestibular Schwannomas: A Systematic Review of MR Acquisition and Analysis Pipelines.

Journal of neuroimaging : official journal of the American Society of Neuroimaging
2026

Electromagnetic exposure changes human Schwann cell motility and transcriptomic profile of hearing-loss-related genes.

iScience
2026

Hemorrhagic Transformation of Postradiation Vestibular Schwannoma Presenting With Facial Paralysis.

The Laryngoscope
2026

Nerve dissection technique to optimize functional outcome: resection of cystic vestibular schwannoma: how I do it.

Acta neurochirurgica
2026

Salvage stereotactic radiosurgery following primary microsurgical resection for vestibular schwannomas: A systematic review & meta-analysis.

Neurosurgical review
2026

Advances in imaging modalities and tumor classification for vestibular schwannomas.

Journal of neuro-oncology
2026

Identification and synthesis of decision-making factors in vestibular schwannoma treatment.

European archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery
2026

Case Report: Somatic NF2 mutation in a vestibular schwannoma arising in a patient with neurofibromatosis type 1.

Frontiers in oncology
2026

Deep Learning-Based Inner Ear Subregion Segmentation in 3D T2-Weighted MRI Using Label-Preserving Data Augmentation.

NMR in biomedicine
2026

Radiation-induced cavernous malformation in the brainstem after Gamma Knife radiosurgery for vestibular schwannoma: A case report and literature review.

Brain &amp; spine
2026

Emerging systemic treatment strategies for vestibular schwannoma.

Journal of neuro-oncology
2026

Surgical Management Strategy for Large Cystic Vestibular Schwannoma Based on the Cyst Classification.

Neurologia medico-chirurgica
2026

Integrating GPT-4o Into Data Mining in Neurosurgery: Feasibility and Proof-of-Concept Study.

JMIR formative research
2026

Incidence and Prognosis of Delayed Facial Nerve Palsy After Vestibular Schwannoma Resection: Systematic Review and Meta-analysis.

Journal of neurological surgery. Part B, Skull base
2026

Vestibular Schwannomas in Pregnancy: A Case Series.

Journal of neurological surgery. Part B, Skull base
2026

Large Sporadic Vestibular Schwannoma Causing Brainstem Compression and Obstructive Hydrocephalus in a Young Adult.

Cureus
2026

Leveling the Playing Field in Vestibular Schwannoma Outcome Reporting: A Survey of Variance and Bias in Published Research.

Otology &amp; neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
2026

Characterizing Tumor-Induced Ataxia in a Vestibular Schwannoma Mouse Model.

Journal of visualized experiments : JoVE
2026

No surgery, but headache exists? Quality of life with vestibular schwannoma.

European archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery
2026

Lateral Skull Base Pseudomeningoceles: Diagnosis, Prevention, and Treatment.

Otolaryngologic clinics of North America
2026

Health-related quality of life in patients with vestibular schwannoma managed with observation, stereotactic radiosurgery or microsurgery: a systematic review and single-arm meta-analysis.

Journal of neurology
2026

Utility of Artificial Intelligence in Stereotactic Radiosurgery for Vestibular Schwannomas: A Systematic Review.

Asian journal of neurosurgery
2026

Single-cell multi-omic techniques highlight the diverse composition and intercellular interactions of the vestibular schwannoma tumor microenvironment.

Neuro-oncology advances
2026

Facial nerve outcomes following vestibular schwannoma surgery: Multivariate analysis of possible prognostic factors.

Acta otorrinolaringologica espanola
2026

Prior surgical resection is a predictor of facial nerve function decrement after radiosurgery for vestibular schwannomas.

Clinical neurology and neurosurgery
2026

Correlation of mastoid pneumatization and pneumatization of the posterior lip of internal auditory meatus and its implications during retrosigmoid craniotomy.

Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia
2026

Magnetic resonance imaging and the evaluation of vestibular schwannomas: a systematic review.

Neuroradiology
2026

N-Cadherin Dynamically Regulates Schwannoma Migration and Represents a Novel Therapeutic Target in NF2-Related Schwannomatosis.

Research square
2026

Two-Week Interval Hypofractionated Stereotactic Radiosurgery for Benign Intracranial Tumors: Volumetric Kinetics and Radiobiological Rationale.

Cancers
2026

Vestibular schwannoma microsurgery peculiarities for better functional outcome and result comparison.

Brain &amp; spine
2026

Microsurgical Outcomes of Medial Sporadic Vestibular Schwannoma: A Matched Cohort Study of 40 Cases and 120 Referents.

Otology &amp; neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
2026

Birds on a wire: Gamma Knife radiosurgery for two schwannomas along the same cranial nerve. Illustrative case.

Journal of neurosurgery. Case lessons
2026

Obsessive-compulsive disorder onset and clinical course in the context and treatment of pineal region germinoma and obstructive hydrocephalus: a case report.

Frontiers in child and adolescent psychiatry
2026

The effect of sex on vestibular schwannoma incidence varies across the lifespan and modifies associations with race/ethnicity.

Journal of neuro-oncology
2026

Unique characteristics of pediatric sporadic vestibular schwannoma.

American journal of otolaryngology
2026

Bilateral Blindness in a Patient With Vestibular Schwannoma and Empty Sella Syndrome: A Case Report.

Cureus
2026

Understanding the Translabyrinthine Approach for Neurosurgery Residents: Operative and Educational Video.

Journal of neurological surgery reports
2026

Translabyrinthine versus middle fossa approaches for vestibular schwannoma surgery: a systematic review and comparative meta-analysis.

Neuro-Chirurgie
2026

An orthotopic vestibular schwannoma mouse model to study tumor-host interactions and mechanism of sensorineural hearing loss.

Journal of neuroscience methods
2026

Diagnostic and management challenge of a pediatric H3K27-altered glioma masquerading as vestibular schwannoma.

Pediatric radiology
2026

Composition of Immune Cells in Sporadic Vestibular Schwannomas with Different Tumor Volumes.

Cancers
2026

Nonconventional Imaging Modalities for Vestibular Schwannoma Prognosis: A Scoping Review.

Otology &amp; neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
2026

A rare constellation of bilateral progressive visual and auditory loss in neurofibromatosis type 2: a multimodal diagnostic approach.

Annals of medicine and surgery (2012)
2026

Matrix Metalloproteinase‑9 (MMP-9) Activatable Gold Nanoparticles for In Situ Zymography and Diagnostics of Neurofibromatosis Type 2 (NF2) Tumors.

ACS applied nano materials
2026

Facial nerve preservation following gamma knife radiosurgery for vestibular schwannomas in neurofibromatosis type 2: a systematic review and meta-analysis of 552 tumors.

Neurosurgical review
2026

Results of TcMEP guided vestibular schwannoma surgery; long term follow-up and progression free survival.

Neurosurgical review
2026

The role of salvage stereotactic radiosurgery for tumor progression following incomplete microsurgical resection of vestibular schwannoma.

Journal of neurosurgery
2026

A decade later - assessing hearing preservation in vestibular schwannoma patients post middle cranial fossa surgery.

Acta oto-laryngologica
2025

Early post-operative hydrocephalus following retrosigmoid vestibular schwannoma resection: Incidence, clinical patterns, and outcomes.

Brain &amp; spine
2026

Cavernous Hemangioma of the Cerebellopontine Angle With Remarkable Enlargement of the Internal Auditory Canal in a Child.

Cureus
2026

A marked decrease in speech intelligibility is no longer a major characteristic of vestibular schwannoma in the current era.

Clinical and experimental otorhinolaryngology
2026

Preoperative interventions to improve clinical results in patients with vestibular schwannoma: A systematic review.

Journal of vestibular research : equilibrium &amp; orientation
2026

Persistent Hypercalcemia: Diagnostic Complexity With Multiglandular Hyperparathyroidism, Renal Cell Carcinoma, and Hereditary Tumor Features.

Cureus
2026

CyberKnife Stereotactic Radiosurgery for Vestibular Schwannomas: Systematic Review and Meta-Analysis of Long-Term Tumor Control and Hearing Preservation Outcomes.

Neurosurgery practice
2025

Use of venovenous extra-corporal membrane oxygenation in acute respiratory distress syndrome secondary to surgical air embolism: A favorable outcome case report.

Surgical neurology international
2026

Present Electrically Evoked Compound Action Potentials and Lack of Auditory Sensation Through a Cochlear Implant After Vestibular Schwannoma Resection.

Otology &amp; neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
2026

Hearing preservation and restoration surgery in NF2-related schwannomatosis.

Familial cancer
2026

Pre-operative blood-based inflammatory indices and long-term facial nerve outcomes following vestibular schwannoma resection.

Journal of neuro-oncology
2026

Rate of Hearing Preservation After Stereotactic Radiosurgery for Treatment of Vestibular Schwannoma: Analysis of Patients With 100% Word Recognition Scores.

Otology &amp; neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
2025

Adenoid cystic carcinoma of the external auditory canal with metastasis to the cerebellopontine angle mimicking vestibular schwannoma: a case report and literature review.

Frontiers in oncology
2026

MRI-Based Prediction of Vestibular Schwannoma: Systematic Review.

Cancers
2026

Candida albicans Meningoencephalitis After Vestibular Schwannoma Surgery: An Autopsy-Confirmed Case Report.

Diagnostics (Basel, Switzerland)
2026

High-risk morphology in cystic vestibular schwannomas: an imaging-based scoring system for facial nerve outcomes.

Journal of neuro-oncology
2026

Intralabyrinthine MRI FLAIR as a predictive marker for hearing loss in vestibular schwannomas in Neurofibromatosis Type 2.

Journal of neuro-oncology
2025

Facial Nerve Conduction Block during Vestibular Schwannoma Surgery: A Rare and Unclarified Transient Neural Dysfunction.

NMC case report journal
2026

Ganglioglioma mimicking a vestibular schwannoma: A rare entity of the cerebellopontine angle.

Neurocirugia
2026

Minimal important differences to assess cross-sectional differences among groups and minimal important changes to assess longitudinal within-patient changes for the Mayo Clinic Vestibular Schwannoma Quality of Life Index.

Journal of neurosurgery
2026

Long-term tumor control after Gamma Knife radiosurgery for sporadic vestibular schwannoma.

Journal of neurosurgery
2026

Defining clinically significant tumor size in sporadic vestibular schwannoma to inform timing of radiosurgery during wait-and-scan management: further evidence supporting size threshold surveillance.

Journal of neurosurgery
2026

Diverse NF2 alterations in cranial schwannomas: a two-case series of germline whole-gene deletion and somatic in-frame deletion.

Brain tumor pathology
2026

Vestibular dose predicts toxicity in stereotactic radiosurgery for vestibular schwannomas.

Clinical and translational radiation oncology
2025

Bilateral Cerebellopontine Angle Masses in a 72-Year-Old Woman With Prior Malignant Melanoma and a Cochlear Implant: A Diagnostic and Management Challenge.

Cureus
2026

Management of High Jugular Bulb in Retrosigmoid Surgery for Vestibular Schwannoma: Analysis of 590 Consecutive Cases.

Operative neurosurgery (Hagerstown, Md.)
2026

Angiogenesis PET/MRI predicts initial growth of sporadic vestibular schwannomas: a prospective study with follow-up in 29 patients using [68Ga]Ga-NODAGA-E[c(RGDyK)]2.

EJNMMI research
2026

Fully endoscopic retrosigmoid keyhole approach versus traditional microscopic microsurgery for small-to-medium vestibular schwannomas: a retrospective matched-cohort study.

Journal of neuro-oncology
2025

Extra-Axial Cerebellopontine Angle Low Grade Glioma - Unusual Occurrence in a 43-year-old Woman.

Pakistan journal of medical sciences
2026

Molecular and genetic insights into vestibular schwannoma.

Journal of neuro-oncology
2026

Artificial intelligence for personalized management of vestibular schwannoma: a multidisciplinary clinical implementation study.

JAMIA open
2026

Multimodal biomarker landscape in vestibular schwannoma.

Current opinion in neurology
2025

Microsurgery Versus Radiosurgery for Vestibular Schwannoma: Which Approach Yields Better Long-Term Results?

Cureus
2025

Volumetric and Linear Imaging Response After Stereotactic Radiotherapy for Vestibular Schwannoma.

Cureus
2026

Long-term hearing and facial nerve outcomes after hearing preservation surgery for vestibular schwannoma: a systematic review and meta-analysis.

Neurosurgical review
2025

Combined subtotal resection and stereotactic radiosurgery for large vestibular schwannomas: A systematic review and meta-analysis.

Neuro-oncology advances
2025

Can intraoperative facial nerve motor evoked potential monitoring predict postoperative facial synkinesis following vestibular schwannoma surgery? A retrospective study.

Journal of neuro-oncology
2026

Computer-aided prediction of growth in vestibular schwannomas based on both structural and dynamic contrast-enhanced MR imaging.

Medical physics
2026

Polymethylmethacrylate Versus Autologous Bone Flap Reconstruction After Retrosigmoid Vestibular Schwannoma Surgery: Impact on Wound Healing and Patient Satisfaction.

World neurosurgery
2026

Tumor Control After Radiosurgery in Sporadic and Neurofibromatosis Type 2 Vestibular Schwannomas.

Cancer medicine
2025

Systematic review of disease-specific quality of life in patients with sporadic vestibular schwannoma.

Journal of neuro-oncology
2025

Multidisciplinary Management of Cerebellopontine Angle Tumors with Brainstem Involvement.

Audiology research
2025

The tumour immune microenvironment is enriched but suppressed in vestibular schwannoma compared to meningioma: therapeutic implications for NF2-related schwannomatosis.

Acta neuropathologica communications
2025

Predictors of postoperative gustatory disturbance and gustatory recovery following microsurgical resection of vestibular schwannoma.

Journal of neuro-oncology
2025

Incidental finding of a lipoma of the internal auditory canal in a 12-year-old patient.

Archivos argentinos de pediatria
2025

Predictors of long-term postoperative tinnitus outcomes in vestibular schwannoma patients.

Scientific reports
2025

Surgery in NF2-Schwannomatosis.

Familial cancer
2025

Optimizing Cochlear Implant Position for Magnetic Resonance Imaging of Vestibular Schwannoma.

Laryngoscope investigative otolaryngology
2025

Evolution of vestibular schwannoma management in the 21st century: A national database study.

Surgical neurology international
2026

The Lived Experience of Facial Paralysis: Impact of Etiology on Patient Perceptions.

Otolaryngology--head and neck surgery : official journal of American Academy of Otolaryngology-Head and Neck Surgery
2026

Centralization of Surgical Care for Vestibular Schwannomas: A Scoping Review.

Otology &amp; neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
2025

Distinguishing pseudoprogression from true tumor growth after stereotactic surgery in vestibular schwannoma: a volumetric and clinical trajectory analysis.

Radiation oncology (London, England)
2026

[ACOUNEU-radiosurgery or hypofractionated radiotherapy for sporadic vestibular schwannoma].

Strahlentherapie und Onkologie : Organ der Deutschen Rontgengesellschaft ... [et al]
2025

Outcomes of Repeat Stereotactic Radiosurgery for Recurrent or Progressive Sporadic Vestibular Schwannoma: A Multicenter International Study.

Neurosurgery
2025

The Acoustic Neuroma-7 Score: An Externally Validated Tool Predicting Facial Nerve Outcome After Vestibular Schwannoma Surgery.

Neurosurgery
2025

[Long-term outcomes of the endoscopic transcanal transpromontorial approach for vestibular schwannoma].

Lin chuang er bi yan hou tou jing wai ke za zhi = Journal of clinical otorhinolaryngology head and neck surgery
2025

A deep learning model to reduce agent dose for contrast-enhanced MRI of the cerebellopontine angle cistern.

European radiology
2026

Gyroscopic Radiosurgery: Clinical Experience and Prospective Analysis of over 500 Treated Tumors.

World neurosurgery
2025

Exploring the Association between Diagnostic and Therapeutic Radiation and the Incidence of Vestibular Schwannoma: A Case-Control Study.

Journal of neurological surgery reports
2025

Evaluating Large Language Models in Interpreting MRI Reports and Recommending Treatment for Vestibular Schwannoma.

Diagnostics (Basel, Switzerland)
2025

Immunohistopathology of Cochleovestibular Schwannoma in Human Temporal Bone Specimens.

Biology
2025

Predicting the Consistency of Vestibular Schwannoma and Its Implication in the Retrosigmoid Approach: A Single-Center Analysis.

Current oncology (Toronto, Ont.)
2025

Variable Schwann cell merlin inactivation is targetable with TEAD1 inhibition in schwannomas.

bioRxiv : the preprint server for biology
2025

A deep learning pipeline for detecting vestibular schwannoma patients with unilateral vestibular loss based on kinematic data.

Scientific reports
2025

Recovery and Discharge Disposition After Retrosigmoid Versus Translabyrinthine Approaches for Vestibular Schwannoma Resection: A Retrospective Review of 301 Patients.

Neurosurgery
2025

Influence of tumor vascularization in surgical outcomes of patients with Grade IV Vestibular Schwannomas: Role of CD34, Perfusion rates, and VEGF.

Neurosurgical review
2025

Vestibular schwannoma presenting as vestibular neuritis-like attack during the COVID-19 pandemic: A case report.

Medicine
2025

Comparative Evaluation of Deep Learning Models for 3D Segmentation and Volumetry of Vestibular Schwannomas Using Large Heterogeneous Datasets with External Validation.

AJNR. American journal of neuroradiology
2025

Continuous and componentized facial palsy measurement alignment and clinical interpretable model.

NPJ digital medicine
2025

Comparative analysis of plan quality between two SRS systems for stereotactic irradiation in treating Vestibular Schwannoma.

Journal of applied clinical medical physics
2026

The Association Between Age and Outcomes of Bevacizumab Treatment in NF2-Related Schwannomatosis.

Otology &amp; neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
2025

Deep Learning Models for Radiomics-Based Segmentation of Vestibular Schwannoma on Magnetic Resonance Imaging: A Systematic Review and Meta-analysis.

Journal of imaging informatics in medicine
2026

Whole Genome Sequencing of Sporadic Vestibular Schwannoma Reveals Novel Genetic Changes.

Otology &amp; neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
2026

Proteomic Analysis Identifies Novel Plasma Biomarkers in Patients With Vestibular Schwannoma.

Otology &amp; neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
2026

Automated Segmentation of Bilateral Vestibular Schwannoma in Neurofibromatosis 2 (NF2).

Otology &amp; neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
2026

Malignant peripheral nerve sheath tumors in schwannomatosis: systematic review and meta-analysis.

Journal of neurosurgery
2026

Malignant peripheral nerve sheath tumors in schwannomatosis: a case series.

Journal of neurosurgery
2025

Vestibular schwannoma clinical prognostic factors and nomogram construction using SEER database.

Discover oncology
2026

Assessing vestibular function in patients with vestibular schwannoma: a comprehensive multi-test vestibular evaluation.

European archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery
2025

Deciphering oxidative stress contributions in vestibular schwannoma: A bioinformatics approach to novel therapeutic pathways.

PloS one
2025

Hearing Preservation and Complications of the Middle Cranial Fossa Approach for Otolaryngological Diseases: Twelve-Year Single-Center Experience.

Journal of clinical medicine
2025

Machine learning model for predicting hearing preservation after vestibular schwannoma surgery: A meta-analysis.

American journal of otolaryngology
2026

Loss of Enhancement in Vestibular Schwannomas Post Stereotactic Radiosurgery: Impact on Tumor Control and Serviceable Hearing.

Otology &amp; neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
2025

Chemokine receptor-4-targeted imaging with [68Ga]Ga-Pentixafor PET: unveiling its diagnostic and prognostic potential across cancers: a systematic review.

Nuclear medicine communications
2025

Real-world vestibular schwannoma management: treatment trends, facial weakness and disparities in a large US network analysis.

The Journal of laryngology and otology
2026

Feasibility of an Endoscopic-Assisted Retrolabyrinthine Approach for Intracanalicular Vestibular Schwannoma-A Radiographic Morphometric Study.

Otology &amp; neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
2026

Hearing outcome after Cyberknife® radiotherapy for vestibular Schwannoma.

European archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery
2025

Radiation-induced cavernous malformation within a vestibular schwannoma: A case report.

SAGE open medical case reports
2025

Collagen Matrix Dural Repair for the Internal Auditory Canal in Retrosigmoid Vestibular Schwannoma Surgery.

World neurosurgery
2026

Frailty, Surgical Time, and Surgical Complications Increase Length of Stay Following Large Vestibular Schwannoma Resection.

Otolaryngology--head and neck surgery : official journal of American Academy of Otolaryngology-Head and Neck Surgery
2025

Global Growth and Distribution of CyberKnife Stereotactic Radiosurgery: A Bibliometric Analysis.

Neurosurgery practice
2025

The relationship between extent of resection, tumor recurrence, and facial nerve outcomes in vestibular schwannoma surgery: a single-institution experience and systematic review.

Journal of neuro-oncology
2025

History and clinical epidemiology of NF2-related schwannomatosis.

Familial cancer
2025

Hearing preservation of post-radiotherapy for acoustic neuroma-a systematic review and meta-analysis.

Frontiers in neurology
2025

Application of Video Head Impulse Test in the Diagnosis and Follow-Up of Vestibular Schwannoma: Case Series, Narrative Literature Review and Clinical Practice Implications.

Journal of clinical medicine
2025

Nuances in the surgical treatment of gangliocytomas of the spinal cord: illustrative cases.

Journal of neurosurgery. Case lessons
2026

Letter: Scoring System Assessing Risks of Growth in Sporadic Vestibular Schwannoma.

Neurosurgery
2025

British Skull Base Society Consensus on Vestibular Schwannoma Surveillance.

Journal of neurological surgery. Part B, Skull base
2025

Radiomic Applications in Skull Base Pathology: A Systematic Review of Potential Clinical Uses.

Journal of neurological surgery. Part B, Skull base
2025

A Survey of 251 Facial Paralysis Patients to Assess Their Educational Preparedness and Symptom Management after Treatment of Vestibular Schwannoma.

Journal of neurological surgery. Part B, Skull base
2026

Pneumocephalus after posterior fossa surgery in the lounging position: risk analysis of intracranial air collections and clinical outcome by voxel-based volumetry.

Journal of neurosurgery
2025

Facial Nerve Outcomes After Resection of Aggressive Vestibular Schwannomas That Failed Initial Stereotactic Radiosurgery.

Neurosurgery
2025

Vestibular Function and Complaints in Patients With Untreated Unilateral Vestibular Schwannoma.

Otology &amp; neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
2025

A case of neurofibromatosis type 1 with neurofibromatosis type 1-related and neurofibromatosis type 1-unrelated tumors: a case report.

Journal of medical case reports
2025

Nodular Growths of NF2-Related Schwannomatosis Vestibular Schwannoma: Clinical and Therapeutical Consequences.

Neurosurgery
2026

Near-total resection in sporadic vestibular schwannoma: is there a volumetric threshold for a win-win scenario?

Journal of neurosurgery
2026

Assessment of auditory pathway microstructure in vestibular schwannoma patients: a quantitative diffusion tensor tractography study.

Journal of neurosurgery
2026

An Assessment of the Binaural Benefits of Concurrent Cochlear Implantation and Vestibular Schwannoma Resection.

Otology &amp; neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
2025

The role of artificial intelligence in predicting the clinical outcomes associated with different therapeutic approaches for vestibular schwannoma: A systematic review and meta-analysis.

Neurosurgical review
2025

A Case of Hypervascular Vestibular Schwannoma with Ventricular Enlargement Improved by the Tumor Volume Reduction Effect of Preoperative Embolization.

Journal of neuroendovascular therapy
2025

Complications of Cerebral Venous Thrombosis After Cerebellopontine Angle Tumor Resection: A STROBE Retrospective Observational Cohort Study.

Neurosurgery
2025

Efficacy of first line of bevacizumab in patients with neurofibromatosis 2-related vestibular schwannomas.

European archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery
2025

Vestibular schwannoma imaging and differential diagnosis.

Handbook of clinical neurology
2025

Clinical evaluation and investigation of vestibular schwannoma in NF2-related schwannomatosis.

Handbook of clinical neurology
2025

Clinical evaluation and investigation of patients with a sporadic vestibular schwannoma.

Handbook of clinical neurology
2025

Vestibular schwannomas: Key research questions and priorities.

Handbook of clinical neurology
2025

Genomics of vestibular schwannoma.

Handbook of clinical neurology
2025

Pathology and tumor microenvironment of vestibular schwannoma.

Handbook of clinical neurology
2025

Tinnitus and its management in patients with vestibular schwannoma.

Handbook of clinical neurology
2025

Dizziness in vestibular schwannomas.

Handbook of clinical neurology
2025

Prevention and rehabilitation of facial palsy in patients with vestibular schwannomas.

Handbook of clinical neurology
2025

Hearing rehabilitation in patients with vestibular schwannomas.

Handbook of clinical neurology
2025

Secondary trigeminal neuralgia due to vestibular schwannoma.

Handbook of clinical neurology
2025

Vestibular schwannoma: Global perspectives.

Handbook of clinical neurology
2025

The role of the clinical nurse specialist in managing vestibular schwannoma.

Handbook of clinical neurology
2025

Quality of life after treatment of vestibular schwannomas.

Handbook of clinical neurology
2025

Subtotal vs gross total excision of vestibular schwannomas.

Handbook of clinical neurology
2025

Management of vestibular schwannoma in the elderly.

Handbook of clinical neurology
2025

Decision-making in sporadic vestibular schwannoma.

Handbook of clinical neurology
2025

Proton therapy for vestibular schwannomas.

Handbook of clinical neurology
2025

Fractionated radiotherapy for vestibular schwannoma.

Handbook of clinical neurology
2025

LINAC stereotactic radiosurgery for vestibular schwannomas.

Handbook of clinical neurology
2025

Gamma Knife radiosurgery for vestibular schwannomas.

Handbook of clinical neurology
2025

Anesthesia for excision of vestibular schwannoma.

Handbook of clinical neurology
2025

Complications of vestibular schwannoma surgery and how to minimize them.

Handbook of clinical neurology
2025

Hearing preservation surgery for vestibular schwannoma.

Handbook of clinical neurology
2025

Outcomes following vestibular schwannoma surgery.

Handbook of clinical neurology
2025

Vestibular schwannoma microsurgical technique.

Handbook of clinical neurology
2025

Applied anatomy in vestibular schwannoma.

Handbook of clinical neurology
2025

Endoscopic vestibular schwannoma surgery.

Handbook of clinical neurology
2025

The retrolabyrinthine approach.

Handbook of clinical neurology
2025

Middle fossa approach to vestibular schwannomas.

Handbook of clinical neurology
2025

Retrosigmoid approach to vestibular schwannoma.

Handbook of clinical neurology
2025

Translabyrinthine approach to the cerebellopontine angle.

Handbook of clinical neurology
2025

Medical therapy for vestibular schwannoma.

Handbook of clinical neurology
2025

Surveillance management of vestibular schwannoma: Present and future strategies.

Handbook of clinical neurology
2025

Clinical epidemiology of NF2-related schwannomatosis.

Handbook of clinical neurology
Ver todos os 2.900 no EuropePMC

Associações

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Doenças relacionadas

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Ainda não achamos doenças com sintomas parecidos o suficiente.

Referências e fontes

Bases de dados externas citadas neste artigo

Publicações científicas

Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.

  1. Electromagnetic exposure changes human Schwann cell motility and transcriptomic profile of hearing-loss-related genes.
    iScience· 2026· PMID 41858877mais citado
  2. Radiation-induced cavernous malformation in the brainstem after Gamma Knife radiosurgery for vestibular schwannoma: A case report and literature review.
    Brain &amp; spine· 2026· PMID 41815645mais citado
  3. Health-related quality of life in patients with vestibular schwannoma managed with observation, stereotactic radiosurgery or microsurgery: a systematic review and single-arm meta-analysis.
    Journal of neurology· 2026· PMID 41794963mais citado
  4. Prior surgical resection is a predictor of facial nerve function decrement after radiosurgery for vestibular schwannomas.
    Clinical neurology and neurosurgery· 2026· PMID 41759480mais citado
  5. Correlation of mastoid pneumatization and pneumatization of the posterior lip of internal auditory meatus and its implications during retrosigmoid craniotomy.
    Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia· 2026· PMID 41759238mais citado
  6. Temporal patterns of facial nerve palsy after microsurgical resection of vestibular schwannoma: immediate vs. delayed onset, management, and outcomes.
    Neurosurg Rev· 2026· PMID 41984336recente
  7. Cochlear Implantation and Vestibular Schwannoma Removal: The Gruppo Otologico Experience in 73 Consecutive Cases.
    Otol Neurotol· 2026· PMID 41981748recente
  8. Recurrence After Subtotal Resection of NF-2-Associated Versus Sporadic Vestibular Schwannomas: A Matched-Cohort Analysis.
    Otolaryngol Head Neck Surg· 2026· PMID 41979396recente
  9. Association Between Intraoperative Fluid Therapy and Postoperative Complications in Posterior Fossa Surgery: A Retrospective Analysis of Vestibular Schwannoma Resections in the Semi-sitting Position.
    J Neurosurg Anesthesiol· 2026· PMID 41979034recente
  10. Prediction of postoperative facial nerve function with preoperative magnetic resonance imaging in patients with vestibular schwannoma.
    Quant Imaging Med Surg· 2026· PMID 41972030recente

Bases de dados e fontes oficiais

Identificadores e referências canônicas usadas para montar este verbete.

  1. ORPHA:252175(Orphanet)
  2. MONDO:0001569(MONDO)
  3. GARD:223(GARD (NIH))
  4. Busca completa no PubMed(PubMed)
  5. Artigo Wikipedia(Wikipedia)
  6. Q423965(Wikidata)

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Schwannoma vestibular
Compêndio · Raras BR

Schwannoma vestibular

ORPHA:252175 · MONDO:0001569
Prevalência
1-9 / 100 000
CID-10
D33.3 · Neoplasia benigna dos nervos cranianos
CID-11
Ensaios
20 ativos
Prevalência
2.0 (Denmark)
MedGen
UMLS
C0027859
EuropePMC
Wikidata
Wikipedia
Papers 10a
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