Neurossarcoidose se refere a um tipo de sarcoidose, uma doença imunomediada caracterizada por inflamação granulomatosa dos órgãos afectados. Granulomas epitelioides compactos, bem formados, coalescentes, não necrosantes ou minimamente necrosantes, com linfócitos dispersos, são as características patológicas da doença. Os órgãos mais frequentemente afectados incluem os pulmões (90%), a pele (∼15%), os olhos (10-30%), o fígado (20-30%) e os gânglios linfáticos (10%-20%).
Introdução
O que você precisa saber de cara
A neuropatia axonal motora aguda (AMAN) é uma forma pura motora axonal do síndrome de Guillain-Barré (GBS; ver este termo).
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🇧🇷 Atendimento SUS — Neuropatia motora axonal, aguda (AMAN)
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Publicações mais relevantes
Patterns of Seasonality and Subtype-Linked Outcomes of Pediatric Guillain-Barré Syndrome ICU Admissions: A 10-Year Audit from Southern India.
To evaluate the seasonal variation in Guillain-Barré Syndrome (GBS) subtype distribution and its association with clinical outcomes in pediatric patients requiring intensive care unit (ICU) admission. An audit of pediatric patients with GBS admitted to the neuro-ICU of a tertiary center in Southern India between 2008 and 2018 was conducted. Seasonal distribution was defined as per meteorological classification: summer (March-May), monsoon (June-September), post-monsoon (October-November), and winter (December-February). Clinical subtypes, treatment, and outcomes, including length of mechanical ventilation (LOMV), ICU stay (LOIS), hospital stay (LOHS), and Hughes disability scores, were analyzed across seasons. Among 75 patients, the highest admissions occurred during the monsoon (n = 29). Acute motor axonal neuropathy (AMAN) was more frequent in monsoon, while acute inflammatory demyelinating polyneuropathy (AIDP) was common in winter and summer. Across the full cohort, no statistically significant seasonal differences were found in the outcomes. However, within the AMAN subtype, LOHS was significantly longer in summer compared to post-monsoon (P = 0.005). Axonal variants showed higher rates of intubation and severe disability (Hughes disability score > 3), while AIDP had milder outcomes. Seasonal clustering of GBS subtypes was observed, with axonal variants more common during the monsoon. However, seasonal variation did not significantly impact the overall clinical outcomes in pediatric ICU patients.
Immunotherapies on Guillain-Barré syndrome and other acute autoimmune neuropathies.
Guillain-Barré syndrome (GBS) and other acute autoimmune neuropathies are rare but severe immune-mediated diseases of the peripheral nervous system. Early diagnosis is important for adequate monitoring and treatment, but it can be complicated by the rarity, heterogeneity in clinical presentation, and extensive differential diagnosis. The current proven effective treatments for GBS are intravenous immunoglobulins administered within 2 weeks and plasma exchange within 4 weeks from the onset of weakness. These therapies are immunomodulatory and aim to prevent further damage of peripheral nerves during the acute stage of the disease. Here we provide an overview of the early presentation of GBS and the required diagnostic workup to discriminate GBS from other causes, including other acute forms of autoimmune polyneuropathies. In addition, the current evidence-based immunotherapies for GBS are discussed along with the presumed pathophysiologic mechanisms of action and practical recommendations for the treatment in clinical practice. Despite current treatment, a substantial proportion of patients with GBS have a poor clinical course and outcome. We will present the latest developments regarding potential new treatments that are currently being evaluated and discuss various opportunities to optimize the design of future treatment trials toward a more effective and personalized treatment of GBS.
Fine Motor Outcomes in Children with Guillain-Barré Syndrome.
To study the motor outcomes at 6-mo and 1-y follow-up of children with Guillain-Barré syndrome (GBS). This study was an ambispective study of 12 mo duration including children with GBS. The motor outcomes were assessed using Hughes Guillain-Barré Syndrome Disability Score (GBSDS) and Overall Neuropathy Limitations Scale (ONLS) at discharge, 6-mo, and 1-y follow-up. Of 56 patients enrolled, 52 children were included in the study. The median (IQR) age at presentation was 8 (4-11) y. Acute motor axonal neuropathy (AMAN) was the most common variant (50%) in the study. At discharge, all the children had GBSDS ≥ 2, with 51.9% (27/52) patients at 6-mo follow-up, and 19.2% (10/52) had GBSDS ≥ 2 at 1-y follow-up, signifying the need for assistance. On ONLS assessment, 46.2% (24/52) had an arm score of > 2, and 86.5% (45/52) had a leg score of > 2 at discharge. At 6-mo follow-up, 26.9% (14/52) had an arm score > 2, and 19.2% (10/52) had a leg score > 2. At 1-y follow-up, 7.7% (4/52) had an arm score of > 2, and 9.7% (5/52) had a leg score > 2. There was no mortality in the index study. Though most children with GBS recover completely, there can still be long-term impairments of fine motor movements required for daily activities. Early recognition and monitoring of persistent motor deficits as long-term sequelae of GBS is of utmost importance to improve the quality of life of these children.
Axonal Versus Demyelinating Guillain-Barré Syndrome Subtypes in Critically Ill Children: Clinical and Autonomic Profiles.
Electrophysiological subtypes of Guillain-Barré Syndrome (GBS) vary in pathophysiology and clinical presentation, but comparative data on their intensive care needs in critically ill children remain limited. In this retrospective cohort study, we analyzed 224 children (1 month to 12 years) diagnosed with GBS and admitted to the Pediatric Intensive Care Unit of a tertiary care hospital in North India from January 2010 to December 2022. GBS was subtyped based on nerve conduction studies into acute motor axonal neuropathy (AMAN), acute inflammatory demyelinating polyradiculoneuropathy (AIDP), acute motor-sensory axonal neuropathy (AMSAN), inexcitable, or equivocal patterns. Clinical features, intensive care interventions, and outcomes were compared across subtypes. AMAN was the most common subtype (61.6%), followed by AIDP (20.1%) and AMSAN (8%). A prodromal illness was reported in 47.3% of cases. Mechanical ventilation was required in 54.9%, and tracheostomy in 24.2% of children. AMSAN was associated with a significantly longer duration of symptoms at presentation (P = 0.006). Autonomic instability, particularly hypertension (P = 0.04), was significantly more frequent in the AIDP group. However, Hughes disability scores, respiratory and cranial nerve involvement, and intensive care needs were similar across subtypes. AMAN was the predominant GBS subtype in critically ill children. While AMSAN was associated with delayed presentation and AIDP with greater autonomic dysfunction, overall intensive care needs and short-term outcomes were comparable across subtypes.
Fusion of molecular mimicry, epigenetic predisposition, and new onset GBS: a narrative review of current understanding and future directions.
Guillain-Barré syndrome (GBS) is a severe immune-driven polyneuropathy marked by the acute onset of flaccid paralysis, areflexia, and in severe cases, life-threatening autonomic or respiratory failure. Although the clinical presentation and diagnostic criteria are widely established, the precise mechanisms underlying GBS are complex and poorly understood. This review summarizes current literature on the interplay of post-infectious triggers, molecular mimicry, and host susceptibility as influenced by genetic and epigenetic variables. Infectious pathogens such as Campylobacter jejuni, cytomegalovirus, Epstein-Barr virus, and, more recently, Zika and SARS-CoV-2 operate as initiators via molecular mimicry, in which pathogen antigens imitate peripheral nerve components, triggering the formation of autoreactive antibody and T-cell responses. Acute inflammatory demyelinating polyneuropathy (AIDP) is characterized by demyelination and inflammatory cytokine responses, whereas acute motor axonal neuropathy (AMAN) is associated with ganglioside-targeting antibodies and axonal loss. Genetic polymorphisms, such as those in HLA, TLR4, MMP9, and CD1A, influence vulnerability to the disease and its progression. Given that many patients experience persistent sensory, motor, and autonomic dysfunction despite treatment, the identification of long-term complications highlights the necessity of customized rehabilitation and long-term follow-up. Traditional therapeutic techniques, such as plasma exchange and intravenous immunoglobulin, remain in use, but current trials on complement inhibitors, antibody-degrading enzymes, and mesenchymal stem cell therapies indicate a move toward mechanism-driven approaches. Despite these advances, significant knowledge gaps remain regarding predictors of poor outcomes and underlying causes of persistent disabilities and complications, highlighting the need for continued translational and clinical research.
Publicações recentes
Re-evaluation of different electrophysiological criteria for Guillain-Barré syndrome in a single cohort from China.
Fusion of molecular mimicry, epigenetic predisposition, and new onset GBS: a narrative review of current understanding and future directions.
Clinical and Electrophysiological Spectrum of Guillain-Barré Syndrome in Syria: A Prospective Cohort Study Highlighting Atypical Presentations.
Challenges in managing prolonged intensive care unit stay for Guillain-Barré syndrome-acute motor axonal neuropathy variant.
📚 EuropePMC139 artigos no totalmostrando 199
Fusion of molecular mimicry, epigenetic predisposition, and new onset GBS: a narrative review of current understanding and future directions.
Annals of medicine and surgery (2012)Clinical and Electrophysiological Spectrum of Guillain-Barré Syndrome in Syria: A Prospective Cohort Study Highlighting Atypical Presentations.
NeuroepidemiologyChallenges in managing prolonged intensive care unit stay for Guillain-Barré syndrome-acute motor axonal neuropathy variant.
SAGE open medical case reportsPlasma exchange following immunoglobulins for Guillain-Barré-Syndrome: a persisting problematic practice?
Frontiers in neurologyPatterns of Seasonality and Subtype-Linked Outcomes of Pediatric Guillain-Barré Syndrome ICU Admissions: A 10-Year Audit from Southern India.
Indian pediatricsImmunotherapies on Guillain-Barré syndrome and other acute autoimmune neuropathies.
Handbook of clinical neurologyUtility of the "Modified Erasmus GBS Respiratory Insufficiency Score" in Axonal and Demyelinating Guillain-Barré Syndrome.
Journal of the peripheral nervous system : JPNSRapidly Progressive Guillain-Barré Syndrome (GBS) as a Critical Predictor of Early Mechanical Ventilation and Prolonged Hospitalization: An Observational Study at a Tertiary Care Hospital.
CureusAtypical Acute Motor Axonal Neuropathy (AMAN) Presenting Concurrently With Community-Acquired Pneumonia and Respiratory Failure: A Case Report.
CureusIn cases of immunoglobulin failure in acute motor axonal neuropathy and Miller Fisher syndrome, plasma exchange should be performed early.
Internal medicine (Tokyo, Japan)Dengue virus infection and Guillain-Barré syndrome: a systematic review of clinical characteristics, outcomes, and predictors of severity.
BMC infectious diseasesFine Motor Outcomes in Children with Guillain-Barré Syndrome.
Indian journal of pediatricsMeningoencephalitis as a presentation of primary Sjögren's syndrome: a case report.
Journal of medical case reportsAxonal Versus Demyelinating Guillain-Barré Syndrome Subtypes in Critically Ill Children: Clinical and Autonomic Profiles.
Pediatric neurologySYK regulates Schwann cell metabolic reprogramming to promote axonal regeneration in immune-mediated neuropathy.
Journal of neuroinflammationGuillain-Barré Syndrome After Inactivated Poliovirus Vaccination: A Rare Clinical Case Report.
Annals of medicine and surgery (2012)Guillain-Barré Syndrome and Variants.
Neurologic clinicsHyperacute Guillain-Barré Syndrome Reaching Clinical Nadir Within 16 Hours: A Case Report.
Internal medicine (Tokyo, Japan)Guillain-Barré Syndrome as an Initial Manifestation of Systemic Lupus Erythematous: Rare Case Report.
Journal of investigative medicine high impact case reportsGuillain-Barré Syndrome Mimicking Autoimmune Hepatitis: A Rare Entity.
ACG case reports journalDKA with negative DM-autoantibodies, complicated by GBS and RESLES: a case report and literature review.
Frontiers in immunologyNeurofilament Light Chain Levels as Diagnostic and Prognostic Biomarkers in Guillain-Barré Syndrome: An Updated Systematic Review and Meta-Analysis.
Neurology and therapyGuillain-barré syndrome following brainstem infarction: a case report and pathophysiological hypothesis.
Frontiers in immunologyCharacterization of Autonomic Involvement in Various Subtypes of Guillain-Barré Syndrome and Association With Electrophysiological Parameters.
Muscle & nerveGuillain-Barré Syndrome Secondary to Snake Bite: A Report of a Rare and Fatal Case.
The American journal of case reportsA Guillain Barre Syndrome (GBS): a case report.
International journal of emergency medicineA case report of zoster-induced Guillain-Barré syndrome: diagnostic challenges and potential role of pulse prednisone.
Annals of medicine and surgery (2012)Safety assessment of dexmedetomidine: Real-world adverse event analysis from the Food and Drug Administration Adverse Events Reporting System public dashboard.
Indian journal of pharmacologyNMDA Receptors Coordinate Metabolic Reprogramming and Mitophagy in Schwann Cells to Promote Peripheral Nerve Regeneration.
Research (Washington, D.C.)Hyperreflexia and Preserved Reflexes in Pediatric Guillain-Barré Syndrome: A Case Report and Literature Review.
CureusPlasma periaxin is a biomarker of peripheral nerve demyelination.
Brain : a journal of neurologyIntegrated treatment approach to Miller Fisher syndrome, a variant of Guillain-Barre syndrome - A case report.
Journal of Ayurveda and integrative medicineSerial Serum Immunoglobulin G Levels and Correlation with Outcomes in Children with Guillain Barre Syndrome.
Indian journal of pediatricsAxonal Guillain-Barré Syndrome After Leptospirosis Contracted in a Cave or While Packrafting-A Case Report.
Wilderness & environmental medicineRapid Paralysis and Hidden Malignancy: Acute Motor Axonal Neuropathy Revealing Pleomorphic Liposarcoma.
European journal of case reports in internal medicineEvaluation and Comparison of Treatment Response and In-Hospital Prognosis of COVID-19-Related Guillain-Barre Syndrome with Non-COVID-19 Patients.
Medical journal of the Islamic Republic of IranClinico-epidemiological profile and prediction of outcome in children with Guillain-Barre syndrome.
Italian journal of pediatricsGuillain-Barré Syndrome Induced by Mycoplasma Pneumoniae: A Non-classical Presentation.
CureusEvolving understanding of Guillain-Barré syndrome pathophysiology and the central role of the classical complement pathway in axonal injury.
Frontiers in neurologyGuillain-Barré Syndrome During the Outbreak of Omicron in Southern China: A Multicenter Case-Control Study.
Journal of inflammation researchImpact of COVID-19 on Guillain Barre Syndrome (GBS) insights from an Iranian referral center.
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Annals of intensive careSOD1-ALS mimicking an inflammatory neuropathy: a case report.
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Pediatric neurologyAcute Hepatic Porphyria Presenting as Guillain-Barré Syndrome: Importance of Early Recognition and Screening.
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BMC neurologyEBV and Concomitant Acute Motor and Sensory Axonal Neuropathy in a Healthy 15-Year-Old Female.
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Radiology case reports[A case of anti-ganglioside antibody-positive Guillain-Barré syndrome with asymmetrical muscle weakness throughout the course of the disease].
Rinsho shinkeigaku = Clinical neurologyResolution of acute motor axonal neuropathy in a patient after treatment with efgartigimod: A case report.
MedicinePotential advantage of therapeutic plasma exchange over intravenous immunoglobulin in children with axonal variant of Guillain-Barré syndrome: A report of six paediatric cases.
Transfusion clinique et biologique : journal de la Societe francaise de transfusion sanguine[Epidemiological and clinical aspects of Guilain-Barré syndrome, 2012-2022].
Revista medica del Instituto Mexicano del Seguro SocialA rare kind of Guillain-Barre syndrome triggered by acute hepatitis A infection in a pediatric patient: a case report and review of literature.
Journal of neurovirologyPrognostic Value of Early Nerve Conduction Studies in Suspected Guillain-Barré Syndrome in Pediatric Age Group: An Observational Study.
CureusClinical characteristics and functional outcomes of pediatric Guillain-Barré syndrome admitted to the Neuro-intensive care unit: a decade-long retrospective observational study.
Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical NeurophysiologyPostpartum Guillain-Barré Syndrome Presenting as Acute Motor Axonal Neuropathy in a Young Female: A Report of a Rare Case.
CureusAcute hepatitis A and hepatitis C co-infection triggering Guillain-Barre syndrome.
Tropical doctorClaw Hand in Acute Motor Axonal Neuropathy Variant.
The Journal of the Association of Physicians of IndiaTemporal Pattern of Individual Neurological Function Recovery in Guillain-Barré Syndrome.
Journal of clinical medicineGuillain-Barrè Syndrome-Retrospective Analysis of Data from a Cohort of Patients Referred to a Tertiary Care Pediatric Neuromuscular Center from 2000 to 2017: Electrophysiological Findings, Outcomes, and a Brief Literature Review.
Medicina (Kaunas, Lithuania)Dexmedetomidine: a real-world safety analysis based on FDA adverse event reporting system database.
Frontiers in pharmacologyOpisthotonic posturing in Guillian-Barre syndrome.
The International journal of neuroscienceIntegrated Approach to Severe Dengue Complicated by Guillain-Barré Syndrome and Multi-organ Failure.
CureusImprovement of Functional Mobility Using a Hip-Wearable Exoskeleton Robot in Guillain-Barré Syndrome With Residual Gait Disturbance: A Case Report.
CureusComplete genome sequence of Edwardsiella tarda strain GBS0709 isolated from a Japanese patient with the acute motor axonal neuropathy subtype of Guillain-Barré syndrome.
Microbiology resource announcementsClinical adverse events to dexmedetomidine: a real-world drug safety study based on the FAERS database.
Frontiers in pharmacologyExploring the Efficacy of Physiotherapy in Guillain-Barré Syndrome Through Virtual Reality-Based Rehabilitation: A Case Report.
CureusGuillain-Barré syndrome: History, pathogenesis, treatment, and future directions.
European journal of neurologyAMAN with Ophthalmoparesis: A Rare Presentation.
The Journal of the Association of Physicians of IndiaThe sural-sparing pattern in clinical variants and electrophysiological subtypes of Guillain-Barré syndrome.
Arquivos de neuro-psiquiatriaAcute Motor Axonal Neuropathy in Lupus Nephritis.
CureusGuillain-Barre syndrome of acute motor axonal neuropathy (AMAN) type associated with herpes zoster: a case report.
BMC neurologyEffectiveness of Symptomatic Physiotherapy in Enhancing the Psychological Parameters of a Patient With Guillain-Barré Syndrome: A Case Report.
CureusAntiganglioside antibody frequency in routine clinical care settings.
European journal of neurologyEfficacy and safety of intravenous immunoglobulin retreatment amongst Guillain-Barré syndrome patients who poorly responded to initial IVIG cycle: a systematic review.
Acta neurologica BelgicaA Rare Presentation of Non-systemic Vasculitic Neuropathy Mimicking Guillain-Barré Syndrome: A Case Report.
CureusRehabilitation of a Chronic Guillain-Barré Syndrome Patient With Vibratory Motor Stimulation of Dorsiflexors: A Case Report.
CureusTREM2 deficiency impairs the energy metabolism of Schwann cells and exacerbates peripheral neurological deficits.
Cell death & diseaseA study on the role of serum uric acid in differentiating acute inflammatory demyelinating polyneuropathy from acute-onset chronic inflammatory demyelinating polyneuropathy.
European journal of neurologyGuillain-Barré syndrome post-SARS-CoV-2 vaccine: a systematic review and data analysis on its clinical, laboratory, electrophysiological, and radiological features.
Frontiers in neurologyEffectiveness of Physiotherapy Intervention in Guillain Barre Syndrome: A Case Report.
CureusA Case of Intractable Hypophosphatemia in a Patient with Guillain-Barré Syndrome and Encephalitis after SARS-CoV-2 Infection.
Endocrine, metabolic & immune disorders drug targetsThe pathophysiological role of endoneurial inflammatory edema in early classical Guillain-Barré syndrome.
Clinical neurology and neurosurgeryEvaluating yield and utilization of ganglioside antibody testing in clinical practice.
Journal of the neurological sciencesFactors Associated with Respiratory Insufficiency in Children with Guillain-Barré Syndrome.
NeuropediatricsThe characteristics of Guillain-Barre syndrome in children in pre-COVID-19 and during the COVID-19 pandemic: A cross-sectional study.
Health science reportsGuillain-Barré Syndrome Presenting as Symmetrical Proximal Muscle Weakness: An Atypical Presentation.
CureusGuillain-Barré Syndrome Presenting With Masticatory Disturbance and Reduction in Bite Force.
CureusPractice of gait training using lower-limb orthosis and body weight-supported walker for severe acute motor axonal neuropathy: a case report.
Japanese journal of comprehensive rehabilitation scienceGuillain-Barré Syndrome Following Hand, Foot, and Mouth Disease in an Adult Patient.
CureusRefining the Pulmonary and Functional Competencies in a Male Patient With Guillain-Barré Syndrome.
CureusAcute motor axonal neuropathy associated with the Pfizer SARS-CoV-2 vaccine.
Neurology perspectivesGuillain-Barré Syndrome in Adults in a Decade: The Largest, Single-Center, Cross-Sectional Study From the Kingdom of Saudi Arabia.
CureusClinical characteristics and management outcomes of Guillain-Barré syndrome: eight-year experience at a tertiary center in jordan - a retrospective cohort study.
Annals of medicine and surgery (2012)Markedly Prolonged Latency of Patellar Tendon Reflex in a Patient With Apparent Acute Motor Axonal Neuropathy.
Journal of clinical neurology (Seoul, Korea)Relation of Neutrophil-Lymphocyte Ratio with Clinical Severity in Patients with Guillain-Barre Syndrome.
Mymensingh medical journal : MMJPathology explains various mechanisms of auto-immune inflammatory peripheral neuropathies.
Brain pathology (Zurich, Switzerland)Immune-mediated polyneuropathy in cats: Clinical description, electrodiagnostic assessment, and treatment.
Journal of veterinary internal medicineConcurrence of Guillain-Barré syndrome and primary biliary cholangitis not related to SARS-CoV-2: Case report.
MedwaveThe Association of Acute Motor Axonal Neuropathy (Guillain-Barre' Syndrome Variant) with Coronavirus (SARS-Cov-2) in a Child: A Case Report.
Iranian journal of child neurologyHyperbaric oxygen therapy improves recovery at acute motor axonal neuropathy case.
Journal of neurosciences in rural practiceAssociation between hyperCKemia and axonal degeneration in Guillain-Barré syndrome.
BMC neurologyLeptomeningeal carcinomatosis presenting with acute motor axonal neuropathy.
Indian journal of cancerConcomitant Occurrence of Acute Motor Axonal Neuropathy in Systemic Lupus Erythematosus.
American journal of physical medicine & rehabilitationGuillain-Barré syndrome associated with COVID-19: A systematic review.
Brain, behavior, & immunity - healthComplement inhibition prevents glial nodal membrane injury in a GM1 antibody-mediated mouse model.
Brain communicationsNationwide survey of childhood Guillain-Barré syndrome, Fisher syndrome, and Bickerstaff brainstem encephalitis in Japan.
Brain & developmentIdentical late motor responses in early Guillain-Barré syndrome: A-waves and repeater F-waves.
Journal of the peripheral nervous system : JPNSTriggers of Guillain-Barré Syndrome: Campylobacter jejuni Predominates.
International journal of molecular sciencesGuillain-Barré Syndrome in Northern China: A Retrospective Analysis of 294 Patients from 2015 to 2020.
Journal of clinical medicinePrognostic Significance of Serial Nerve Conduction in GB Syndrome.
Neurology IndiaAcute motor axonal neuropathy following SARS-CoV-2 infection in the third trimester of pregnancy.
Proceedings (Baylor University. Medical Center)Reversible conduction failure in acute inflammatory demyelinating polyneuropathy.
Scientific reportsGuillain-Barré syndrome (GBS) complicated by rhabdomyolysis (RML): Case reports of 2 children and literature review.
Frontiers in pediatricsElevated monocyte to high-density lipoprotein cholesterol ratio correlates with clinical severity in acute inflammatory demyelinating polyradiculoneuropathy patients.
Frontiers in neurology[Finger drop variant of Guillain-Barré syndrome: a case report].
Rinsho shinkeigaku = Clinical neurologySural Sparing Pattern and Sensory Ratio as Electrodiagnostic and Prognostic Markers in Pediatric Guillain-Barré Syndrome.
NeuropediatricsConcomitant Guillain-Barré Syndrome in a young Sri Lankan male with severe ulcerative colitis.
BMC gastroenterology[Guillain-Barré syndrome and other autoimmune neurophaties: current therapy].
MedicinaAssessment of neurological sequelae and new-onset symptoms in the long-term follow-up of paediatric Guillain-Barre syndrome: A longitudinal study from India.
Journal of paediatrics and child healthPrognostic Implications of Early Albuminocytological Dissociation in Guillain-Barré Syndrome.
The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiquesThe acute motor axonal neuropathy variant of Guillain-Barré Syndrome diagnosed after ankle trauma.
Turkish journal of emergency medicineGuillain-Barré syndrome in children - High occurrence of Miller Fisher syndrome in East Asian region.
Brain & development[Guillain Barre syndrome associated with coronavac vaccine. Report of one case].
Revista medica de ChileOutcome of Guillain-Barré syndrome following intravenous immunoglobulin compared to natural course.
European journal of neurologyAutoimmune glial fibrillary acidic protein astrocytopathy overlapping with immunoglobulin G anti-GM1 antibody-associated acute motor axonal neuropathy.
Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical NeurophysiologySARS-CoV-2 vaccinations reduce the prevalence of post-COVID Guillain-Barre syndrome.
Clinics (Sao Paulo, Brazil)A Rare Case of COVID-19-Induced Chronic Demyelinating Polyneuropathy.
CureusLesion Localization and Prognosis Using Electrodiagnostic Studies in Facial Diplegia: A Rare Variant of Guillain-Barre Syndrome.
CureusNodopathies in the Early Diagnosis of Axonal Forms of Guillain-Barré Syndrome.
Frontiers in neurologyNeurophysiological Aspects in SARS-CoV-2-Induced Acute Respiratory Distress Syndrome.
Frontiers in neurologyFinger Drop-Dominant Variant of Guillain-Barre Syndrome in a Patient With COVID-19: A Case Report.
Journal of Korean medical scienceAre Miller Fisher syndrome and CANDA due to a paranodopathy?
Journal of the neurological sciencesPost malaria acute motor axonal neuropathy.
Journal of travel medicineGuillain-Barré Syndrome Related and Unrelated to COVID-19: Clinical Follow-Up in the COVID-19 Era.
Physical therapyPosterior Reversible Encephalopathy Syndrome in Guillain-Barré Syndrome: Just a Problem of Immunoglobulins? Controversy From Two Atypical Case Reports.
Frontiers in neurologyFrequency of exposure to arboviruses and characterization of Guillain Barré syndrome in a clinical cohort of patients treated at a tertiary referral center in Brasília, Federal District.
Revista da Sociedade Brasileira de Medicina TropicalCollaborative studies of U.S.-China neurologists on acute motor axonal neuropathy.
Pediatric investigation[A case suspected Sensory Guillain-Barré syndrome subsequent to Campylobacter jejuni enteritis].
Rinsho shinkeigaku = Clinical neurologyCOVID-19-Associated Autoimmune Disease: A Rare First Case Report of Acute Motor Axonal Neuropathy Variant of Guillain-Barre Syndrome in a Woman Patient in New York City.
CureusGuillain-Barré Syndrome in Mexico: An Updated Review Amid the Coronavirus Disease 2019 ERA.
Revista de investigacion clinica; organo del Hospital de Enfermedades de la NutricionPost COVID-19 vaccination Guillain-Barre syndrome: three cases.
Human vaccines & immunotherapeuticsTherapeutic plasma exchange in a patient with acute motor axonal neuropathy subtype of Guillain-Barre syndrome and systemic lupus erythematosus.
Journal of clinical apheresisPredictors of Mechanical Ventilation in Guillain-Barré Syndrome with Axonal Subtypes.
The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiquesMultiple Cranial Nerve Enhancement in Guillain-Barre Syndrome With Clinicoradiological Dissociation.
Journal of clinical neuromuscular diseaseRegional Differences of Guillain-Barré Syndrome in China: From South to North.
Frontiers in aging neuroscienceElectrophysiological Pattern and Predictors of Functional Outcome of Patients with Guillain Barre Syndrome at a Tertiary Care Hospital in Pakistan.
Journal of the College of Physicians and Surgeons--Pakistan : JCPSPComparison of the effects of different doses of Glucocorticoids on distinct subtypes of Guillain-Barré syndrome in Southern China.
BMC neurologyCOVID-19 Neuromuscular Involvement in Post-Acute Rehabilitation.
Brain sciencesSevere Acute Motor Axonal Neuropathy associated with Influenza-A (H1N1) Infection and Prolonged Respiratory Failure - A Case Report.
Journal of critical care medicine (Universitatea de Medicina si Farmacie din Targu-Mures)Pearls & Oy-sters: Delayed Diagnosis of Acute Motor Axonal Neuropathy With Cardiac Arrest.
NeurologyMultifocal motor neuropathy occurring after acute motor axonal neuropathy: two stages of the same disease?
Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical NeurophysiologyProtective Effect of Hyperbaric Oxygen Treatment on Axon Degeneration after Acute Motor Axonal Neuropathy.
Autoimmune diseasesElectrophysiologic findings in patients with COVID-19 and quadriparesia in the northwest of Iran, A case series study and literature review.
Caspian journal of internal medicineCovid-19 associated Guillain-Barré syndrome: A series of a relatively uncommon neurological complication.
Diabetes & metabolic syndromeComparison of Five Different Electrophysiological Criteria for Childhood Guillain Barre Syndrome.
Annals of Indian Academy of NeurologyBilateral Facial Palsy and Hyperreflexia as the Main Clinical Presentation in Guillain-Barré Syndrome.
The American journal of case reportsPerioperative Bilateral Medial Medullary Infarction With "Snake Eyes Appearance": A Case Report.
Frontiers in medicineGuillain Barre Syndrome associated with COVID-19 Infection: A Case Report.
JNMA; journal of the Nepal Medical AssociationPain in acute motor axonal neuropathy.
Muscle & nerveAn unusual case of acute motor axonal neuropathy (AMAN) complicating dengue fever.
Drug discoveries & therapeuticsGuillain-Barré Syndrome-Like Polyneuropathy Associated with Immune Checkpoint Inhibitors: A Systematic Review of 33 Cases.
BioMed research internationalAcute motor axonal neuropathy after ipilimumab and nivolumab treatment in melanoma brain metastases: A case report and review of the literature.
SAGE open medical case reportsElevated blood and cerebrospinal fluid glucose levels affect the severity and short-term prognosis of Guillain-Barré syndrome.
Neurological researchUnclassified subtype of Guillain-Barré syndrome is associated with quick recovery.
Journal of clinical neuroscience : official journal of the Neurosurgical Society of AustralasiaDevelopment of Acute Inflammatory Demyelinating Polyneuropathy 11 Days after Spinal Surgery: A Case Report and Literature Review.
Case reports in medicineCosts of Guillain-Barré Syndrome in the Brazilian Federal District: the patients' perspective.
Transactions of the Royal Society of Tropical Medicine and HygieneNerve ultrasound evaluation of Guillain-Barré syndrome subtypes in northern China.
Muscle & nerveEpidemiological and clinical aspects of Guillain-Barré syndrome and its variants.
Arquivos de neuro-psiquiatriaClinical features and outcome of Guillain-Barre syndrome in Saudi Arabia: a multicenter, retrospective study.
BMC neurologyGenetic basis of Guillain-Barre syndrome.
Journal of neuroimmunologyEmerging infectious diseases, vaccines and Guillain-Barré syndrome.
Clinical & experimental neuroimmunologyClinical features and real-world outcomes of Guillain-Barré syndrome in the Philippines.
Neurological researchEmerging Infection, Vaccination, and Guillain-Barré Syndrome: A Review.
Neurology and therapyElectrophysiological characteristics of patients with nitrous oxide abuse.
Neurological researchClinical and Electrophysiological Factors Predicting Prolonged Recovery in Children with Guillain-Barré Syndrome.
Indian journal of pediatricsSystematic review of cases of acute myelitis in individuals with COVID-19.
European journal of neurologyAcute Transverse Myelitis (ATM):Clinical Review of 43 Patients With COVID-19-Associated ATM and 3 Post-Vaccination ATM Serious Adverse Events With the ChAdOx1 nCoV-19 Vaccine (AZD1222).
Frontiers in immunologyMacrophages and Autoantibodies in Demyelinating Diseases.
CellsAxonal Guillain-Barre syndrome associated with SARS-CoV-2 infection in a child.
Journal of medical virologyThe value of sensory nerve conduction studies in the diagnosis of Guillain-Barré syndrome.
Clinical neurophysiology : official journal of the International Federation of Clinical NeurophysiologyGuillain-Barre Syndrome Associated With COVID-19 Infection: A Case Report With Review of Literature.
CureusAcute Motor Axonal Neuropathy Improvement 20 Days After Hyperbaric Oxygen Therapy.
International medical case reports journalClinical Characteristics and Predictors of Short-Term Outcome in Mexican Adult Patients with Guillain-Barré Syndrome.
Neurology IndiaClinical Profile and Outcome of Guillain-Barre Syndrome in Pediatric Patients Admitted to a Tertiary Care Centre: A Retrospective Study.
Neurology IndiaTherapeutic plasma exchange as a first-choice therapy for axonal Guillain-Barré syndrome: A case-based review of the literature (Review).
Experimental and therapeutic medicineElevated cerebrospinal fluid levels of beta-2-microglobulin in patients with Guillain-Barré syndrome and their correlations with clinical features.
Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical NeurophysiologyGuillain-Barré syndrome triggered by surgery in a Chinese population: a multicenter retrospective study.
BMC neurologyChanges in motor nerve excitability in acute phase Guillain-Barré syndrome.
Muscle & nerveAntiglycolipid antibodies in Guillain-Barré and Fisher syndromes: discovery, current status and future perspective.
Journal of neurology, neurosurgery, and psychiatryClinical Profile and Predictors of Mechanical Ventilation in Guillain-Barre Syndrome in North Indian Children.
Journal of child neurologyAcute Sensory-Motor Axonal Neuropathy in a 57-Year-Old Male Presenting With Paresthesia and Distal Muscle Weakness.
CureusIncreased Cerebrospinal Fluid Uric Acid Levels in Guillain-Barré Syndrome.
Frontiers in neurologyClinical characteristics of Epstein-Barr virus infection in the pediatric nervous system.
BMC infectious diseasesFinger drop sign as a new variant of acute motor axonal neuropathy.
Muscle & nerveAcute Motor Axonal Neuropathy Related to COVID-19 Infection: A New Diagnostic Overview.
Journal of clinical neuromuscular diseaseRelapsing Pattern of Acute Motor Axonal Neuropathy.
Journal of clinical neuromuscular diseaseNodal conduction block: A unifying concept.
Muscle & nerveAssociações
Organizações que acompanham esta doença — pra ter apoio e orientação
Ainda não temos associações cadastradas para Neuropatia motora axonal, aguda (AMAN).
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Comunidades
Grupos ativos de quem convive com esta doença aqui no Raras
Ainda não existe comunidade no Raras para Neuropatia motora axonal, aguda (AMAN)
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Patterns of Seasonality and Subtype-Linked Outcomes of Pediatric Guillain-Barré Syndrome ICU Admissions: A 10-Year Audit from Southern India.
- Immunotherapies on Guillain-Barré syndrome and other acute autoimmune neuropathies.
- Fine Motor Outcomes in Children with Guillain-Barré Syndrome.
- Axonal Versus Demyelinating Guillain-Barré Syndrome Subtypes in Critically Ill Children: Clinical and Autonomic Profiles.
- Fusion of molecular mimicry, epigenetic predisposition, and new onset GBS: a narrative review of current understanding and future directions.
- Re-evaluation of different electrophysiological criteria for Guillain-Barré syndrome in a single cohort from China.
- Clinical and Electrophysiological Spectrum of Guillain-Barré Syndrome in Syria: A Prospective Cohort Study Highlighting Atypical Presentations.
- Reply to The outcome of severe Guillain-Barré syndrome after robotic or conventional rehabilitation also depends on the triggering agent and the neurophysiological subtype.
- Challenges in managing prolonged intensive care unit stay for Guillain-Barré syndrome-acute motor axonal neuropathy variant.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:98918(Orphanet)
- MONDO:0020349(MONDO)
- GARD:19602(GARD (NIH))
- Busca completa no PubMed(PubMed)
- Q4677934(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
