A Drenagem Anômala Total das Veias Pulmonares (DATVP) é uma condição do coração presente desde o nascimento. Nela, todas as veias que trazem o sangue oxigenado dos pulmões, em vez de levarem esse sangue para o lado esquerdo do coração (como deveriam), o desviam para o lado direito do coração ou para outros vasos que se conectam a ele. Isso pode levar a diversos problemas, como cansaço, falta de ar ao se esforçar, pressão alta nas artérias dos pulmões, coloração azulada da pele (cianose) e insuficiência cardíaca progressiva (quando o coração vai perdendo a capacidade de bombear o sangue de forma eficiente).
Introdução
O que você precisa saber de cara
A Drenagem Anômala Total das Veias Pulmonares (DATVP) é uma condição do coração presente desde o nascimento. Nela, todas as veias que trazem o sangue oxigenado dos pulmões, em vez de levarem esse sangue para o lado esquerdo do coração (como deveriam), o desviam para o lado direito do coração ou para outros vasos que se conectam a ele. Isso pode levar a diversos problemas, como cansaço, falta de ar ao se esforçar, pressão alta nas artérias dos pulmões, coloração azulada da pele (cianose) e insuficiência cardíaca progressiva (quando o coração vai perdendo a capacidade de bombear o sangue de forma eficiente).
Escala de raridade
<1/50kMuito rara
1/20kRara
1/10kPouco freq.
1/5kIncomum
1/2k
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Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Partes do corpo afetadas
+ 15 sintomas em outras categorias
Características mais comuns
Os sintomas variam de pessoa para pessoa. Abaixo estão as 42 características clínicas mais associadas, ordenadas por frequência.
Linha do tempo da pesquisa
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Genética e causas
O que está alterado no DNA e como passa nas famílias
Nenhum gene associado encontrado
Os dados genéticos desta condição ainda estão sendo catalogados.
Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
Remédios, cuidados de apoio e o que precisa acompanhar
Onde tratar no SUS
Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)
🇧🇷 Atendimento SUS — Anomalia do retorno venoso pulmonar congênita total
Centros de Referência SUS
24 centros habilitados pelo SUS para Anomalia do retorno venoso pulmonar congênita total
Centros para Anomalia do retorno venoso pulmonar congênita total
Detalhes dos centros
Hospital Universitário Prof. Edgard Santos (HUPES)
R. Dr. Augusto Viana, s/n - Canela, Salvador - BA, 40110-060 · CNES 0003808
Serviço de Referência
Hospital Infantil Albert Sabin
R. Tertuliano Sales, 544 - Vila União, Fortaleza - CE, 60410-794 · CNES 2407876
Serviço de Referência
Hospital de Apoio de Brasília (HAB)
AENW 3 Lote A Setor Noroeste - Plano Piloto, Brasília - DF, 70684-831 · CNES 0010456
Serviço de Referência
Hospital Estadual Infantil e Maternidade Alzir Bernardino Alves (HIABA)
Av. Min. Salgado Filho, 918 - Soteco, Vila Velha - ES, 29106-010 · CNES 6631207
Serviço de Referência
Hospital das Clínicas da UFG
Rua 235 QD. 68 Lote Área, Nº 285, s/nº - Setor Leste Universitário, Goiânia - GO, 74605-050 · CNES 2338424
Serviço de Referência
Hospital Universitário da UFJF
R. Catulo Breviglieri, Bairro - s/n - Santa Catarina, Juiz de Fora - MG, 36036-110 · CNES 2297442
Atenção Especializada
Hospital das Clínicas da UFMG
Av. Prof. Alfredo Balena, 110 - Santa Efigênia, Belo Horizonte - MG, 30130-100 · CNES 2280167
Serviço de Referência
Hospital Universitário Julio Müller (HUJM)
R. Luis Philippe Pereira Leite, s/n - Alvorada, Cuiabá - MT, 78048-902 · CNES 2726092
Atenção Especializada
Hospital Universitário João de Barros Barreto
R. dos Mundurucus, 4487 - Guamá, Belém - PA, 66073-000 · CNES 2337878
Serviço de Referência
Hospital Universitário Lauro Wanderley (HULW)
R. Tabeliao Estanislau Eloy, 585 - Castelo Branco, João Pessoa - PB, 58050-585 · CNES 0002470
Atenção Especializada
Instituto de Medicina Integral Prof. Fernando Figueira (IMIP)
R. dos Coelhos, 300 - Boa Vista, Recife - PE, 50070-902 · CNES 0000647
Serviço de Referência
Hospital Pequeno Príncipe
R. Des. Motta, 1070 - Água Verde, Curitiba - PR, 80250-060 · CNES 3143805
Serviço de Referência
Hospital Universitário Regional de Maringá (HUM)
Av. Mandacaru, 1590 - Parque das Laranjeiras, Maringá - PR, 87083-240 · CNES 2216108
Atenção Especializada
Hospital de Clínicas da UFPR
R. Gen. Carneiro, 181 - Alto da Glória, Curitiba - PR, 80060-900 · CNES 2364980
Serviço de Referência
Hospital Universitário Pedro Ernesto (HUPE-UERJ)
Blvd. 28 de Setembro, 77 - Vila Isabel, Rio de Janeiro - RJ, 20551-030 · CNES 2280221
Serviço de Referência
Instituto Nacional de Saúde da Mulher, da Criança e do Adolescente Fernandes Figueira (IFF/Fiocruz)
Av. Rui Barbosa, 716 - Flamengo, Rio de Janeiro - RJ, 22250-020 · CNES 2269988
Serviço de Referência
Hospital São Lucas da PUCRS
Av. Ipiranga, 6690 - Jardim Botânico, Porto Alegre - RS, 90610-000 · CNES 2232928
Serviço de Referência
Hospital de Clínicas de Porto Alegre (HCPA)
Rua Ramiro Barcelos, 2350 Bloco A - Av. Protásio Alves, 211 - Bloco B e C - Santa Cecília, Porto Alegre - RS, 90035-903 · CNES 2237601
Serviço de Referência
Hospital Universitário da UFSC (HU-UFSC)
R. Profa. Maria Flora Pausewang - Trindade, Florianópolis - SC, 88036-800 · CNES 2560356
Serviço de Referência
Hospital das Clínicas da FMUSP
R. Dr. Ovídio Pires de Campos, 225 - Cerqueira César, São Paulo - SP, 05403-010 · CNES 2077485
Serviço de Referência
Hospital de Base de São José do Rio Preto
Av. Brg. Faria Lima, 5544 - Vila Sao Jose, São José do Rio Preto - SP, 15090-000 · CNES 2079798
Atenção Especializada
Hospital de Clínicas da UNICAMP
R. Vital Brasil, 251 - Cidade Universitária, Campinas - SP, 13083-888 · CNES 2748223
Serviço de Referência
Hospital de Clínicas de Ribeirão Preto (HCRP-USP)
R. Ten. Catão Roxo, 3900 - Vila Monte Alegre, Ribeirão Preto - SP, 14015-010 · CNES 2082187
Serviço de Referência
UNIFESP / Hospital São Paulo
R. Napoleão de Barros, 715 - Vila Clementino, São Paulo - SP, 04024-002 · CNES 2688689
Serviço de Referência
Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.
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Publicações mais relevantes
Exercise Capacity and Pulmonary Function in Pediatric Patients With Anomalous Pulmonary Venous Connection Post-Surgical Repair: A Retrospective Analysis.
Anomalous pulmonary venous connection (APVC), including total (TAPVC) and partial (PAPVC) forms, is a congenital heart defect with abnormal pulmonary vein drainage; and while surgical repair has improved survival, its long-term impact on cardiopulmonary function remains unclear. This retrospective study evaluated exercise capacity and pulmonary function in 26 pediatric APVC patients (17 TAPVC, 9 PAPVC) using cardiopulmonary exercise testing (CPET) and compared them with 63 age-matched healthy controls. Patients with complex defects or significant comorbidities were excluded. Results showed significantly lower anaerobic threshold VO2 (p = 0.03), peak VO2 (p < 0.001) and peak heart rate (p = 0.02) in the APVC group, indicating impaired exercise capacity; though no differences were found between TAPVC and PAPVC subgroups. Despite preserved resting lung function, these findings suggest that children with repaired APVC experience persistent exercise limitations, underscoring the importance of routine functional assessment and potential rehabilitation, with further studies needed to clarify underlying mechanisms and guide long-term care.
Left Ventricular Rupture Due to Congenital Partial Defect of the Left Ventricular Free Wall.
A neonate who underwent corrective surgery for cardiac-type total anomalous pulmonary venous connection (TAPVC) was suspected of having a pseudoaneurysm of the left ventricular (LV) free wall on transthoracic echocardiography (TTE) on postoperative day 11. Emergency surgery was performed the following day, revealing LV rupture due to a congenital partial defect of the LV free wall. The defect was successfully repaired using double-patch closure reinforced with BioGlue. The postoperative course was uneventful. This case highlights that left ventricular rupture may occur due to an unrecognized congenital defect after neonatal cardiac surgery, particularly in conditions such as TAPVC, where the left ventricle is underfilled preoperatively.
Importance of clinical practice guidelines for specialized delivery room resuscitation of newborns with prenatally diagnosed critical congenital heart disease.
Perinatal transition is uniquely complex in newborns with critical congenital heart disease (CCHD), whose cardiopulmonary physiology often diverges from the standard neonatal resuscitation framework. We developed lesion-specific clinical practice guidelines (CPGs) for delivery room (DR) management of six high-risk CCHD diagnoses - hypoplastic left heart syndrome, dextro- transposition of the great arteries, Ebstein anomaly, congenital complete heart block, total anomalous pulmonary venous return, and tetralogy of Fallot with absent pulmonary valve. Developed collaboratively between neonatologists, cardiologists, and cardiac intensivists, these guidelines standardize DR stabilization for high-risk, low frequency events, promote a shared mental model among multidisciplinary teams, and provide structured escalation thresholds for oxygen, respiratory support, intubation, and medication use. Beyond clinical standardization, these CPGs enhance provider education, team preparedness, and family counseling. They offer a scalable framework adaptable to centers with or without on-site cardiac care, bridging physiologic principles with practical implementation.
High risk and low incidence diseases: Cyanotic critical congenital heart disease.
Cyanotic critical congenital heart disease (CCHD) is a serious condition associated with high rate of morbidity and mortality. This review highlights key aspects of CCHD, including presentation, diagnosis, and management in the emergency department (ED), based on current evidence. CCHD encompasses several conditions, including truncus arteriosus, dextro-transposition of the great arteries (d-TGA), tricuspid atresia, tetralogy of Fallot (TOF), total anomalous pulmonary venous return (TAPVR), Ebstein's anomaly, critical pulmonary stenosis, and hypoplastic left heart syndrome (HLHS). These conditions should be considered in critically ill neonates presenting with shock and cyanosis. Evaluation involves a thorough assessment of the patient's cardiovascular and respiratory status. Diagnostic tools include pulse oximetry, laboratory testing, electrocardiogram, chest radiography, and ultrasonography. Management requires prompt recognition and hemodynamic stabilization, which may involve the administration of antibiotics, prostaglandins, vasoactive/inotropic agents, and airway management. Expert consultation and coordination of transfer to a tertiary or quaternary care center are crucial. Surgical repair serves as the definitive treatment. A thorough understanding of cyanotic congenital heart disease is essential for emergency clinicians to effectively diagnose and manage this potentially life-threatening condition.
A De Novo Loss-of-Function NCKAP1 Variant in a Boy with Neurodevelopmental Delay and Congenital Heart Defect.
Background: Neurodevelopmental disorders (NDDs), such as autism spectrum disorder (ASD), intellectual disability (ID), and global developmental delay (GDD), frequently have underlying genetic causes. NCKAP1, a gene essential for actin cytoskeleton remodeling and neuronal development, has recently gained recognition as a promising candidate gene in NDDs. While not yet linked to a defined Mendelian disorder, damaging NCKAP1 variants have been identified in individuals with NDDs. NCKAP1 is also expressed in cardiac tissue, with emerging evidence supporting its potential involvement in cardiac development. Here, we present a case of a patient with neurodevelopmental delay and congenital heart disease (CHD) harboring a novel damaging NCKAP1 variant. Methods: Comprehensive clinical evaluations and trio exome sequencing (proband and parents) were conducted on a patient with complex cardiac and neurodevelopmental phenotypes. Results: We identified a de novo heterozygous frameshift variant in NCKAP1, NM_205842.3:c.2956_2959del p.(Ser986Hisfs*34), predicted to result in loss of function through nonsense-mediated mRNA decay. The patient's clinical features included neonatally diagnosed and surgically repaired infradiaphragmatic total anomalous pulmonary venous return (TAPVR), intellectual disability, speech delay, and autistic traits. His NDD phenotypes and variant type align well with previously described NCKAP1-associated NDD, while the cardiac anomaly adds evidence to the gene's expanding phenotypic spectrum. This represents the fourth reported case linking NCKAP1 variants to CHD and/or neurodevelopmental delay. Conclusions: This case strengthens the growing recognition of NCKAP1 in both neurodevelopment and cardiac formation. It highlights the importance of genetic testing for individuals with overlapping developmental and cardiac conditions. Further research is warranted to elucidate the role of NCKAP1 in cardiac development and its contribution to CHD.
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📚 EuropePMCmostrando 196
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World journal for pediatric & congenital heart surgeryOutcomes of the Warden Procedure for Partial Anomalous Pulmonary Venous Drainage.
Pediatric cardiologyTrends in Infant Mortality After TAPVR Repair over 18 Years in Texas and Impact of Hospital Surgical Volume.
Pediatric cardiologyd-Transposition of Great Arteries and Total Anomalous Pulmonary Venous Connection With Left Ventricular Regression-A Rarity.
World journal for pediatric & congenital heart surgeryAssessing the recently noted surgical outcome of isolated total anomalous pulmonary venous connection repair: A single-secondary center experience.
Journal of cardiac surgeryA Rare Case of Cardiogenic Shock: Cor Triatriatum With Anomalous Pulmonary Venous Return.
World journal for pediatric & congenital heart surgeryA Wide Comparison of Techniques for Repair of PAPVCs: One Institution's 20-Year Experience.
The Thoracic and cardiovascular surgeonClinical outcomes after the endovascular treatments of pulmonary vein stenosis in patients with congenital heart disease.
Cardiology in the youngPrenatal diagnosis and prevalence of critical congenital heart defects: an international retrospective cohort study.
BMJ openA new palliative surgical technique for high risk Total anomalous pulmonary venous connection (Sarmast-Takriti shunt).
Journal of cardiothoracic surgeryInfracardiac total anomalous pulmonary venous return in a patient with Williams syndrome: A case report.
MedicineLong-term Outcomes of the Fontan Operation in Patients With Total Anomalous Pulmonary Venous Drainage.
The Annals of thoracic surgeryComputed Tomography Angiography and Magnetic Resonance Angiography of Congenital Anomalies of Pulmonary Veins.
Journal of computer assisted tomographyDiagnosis and Management of the Unligated Vertical Vein in Repaired Total Anomalous Pulmonary Venous Connection.
World journal for pediatric & congenital heart surgeryA rare association of left pulmonary artery sling with right pulmonary hypoplasia and total anomalous pulmonary venous connection.
Cardiology in the youngTotal Anomalous Pulmonary Venous Connection Beyond the First Decade of Life.
World journal for pediatric & congenital heart surgerySuccessful Surgical Management of a Rare Case of Mixed Type of Total Anomalous Pulmonary Venous Connection in a Very Low Birth Weight Preterm Child Using a Novel Surgical Technique.
World journal for pediatric & congenital heart surgeryTotal anomalous pulmonary vein drainage in a 60-year-old woman diagnosed in an ECG-gated multidetector computed tomography - a case report and review of literature.
Polish journal of radiologyEvaluation of the post-LA space index in the normal fetus.
Prenatal diagnosisA Novel Mouse Model for Cilia-Associated Cardiovascular Anomalies with a High Penetrance of Total Anomalous Pulmonary Venous Return.
Anatomical record (Hoboken, N.J. : 2007)Surgical results of total anomalous pulmonary venous connection repair in 256 patients.
Interactive cardiovascular and thoracic surgeryIs Sutureless Technique Beneficial in the Primary Repair of Total Anomalous Pulmonary Venous Connection? A Systematic Review and Meta-Analysis.
Pediatric cardiologyPrevalence of congenital cardiac anomalies in patients with cleft lip and palate - Its implications in surgical management.
Journal of oral biology and craniofacial researchFamilial total anomalous pulmonary venous return with 15q11.2 (BP1-BP2) microdeletion.
Journal of human geneticsSingle Ventricle and Total Anomalous Pulmonary Venous Connection: Implications of Prenatal Diagnosis.
World journal for pediatric & congenital heart surgeryComputed tomography findings and preoperative risk factors for mortality of total anomalous pulmonary venous connection.
The international journal of cardiovascular imagingMaternal Obesity as a Risk Factor for the Development of Total Anomalous Pulmonary Venous Connection in Their Offspring.
Archives of medical researchSutureless technique versus conventional surgery in the primary treatment of total anomalous pulmonary venous connection: a systematic review and meta-analysis.
Journal of cardiothoracic surgeryPostoperative Obstruction of the Pulmonary Veins in Mixed Total Anomalous Pulmonary Venous Connection.
Pediatric cardiologyNeonatal Outcomes in Total Anomalous Pulmonary Venous Return: The Role of Prenatal Diagnosis and Pulmonary Venous Obstruction.
Pediatric cardiologyDual drainage total anomalous pulmonary venous connection: a rare mixed variant.
Asian cardiovascular & thoracic annalsPulmonary vein obstruction after primary sutureless pericardial repair of a total anomalous pulmonary venous connection.
Interactive cardiovascular and thoracic surgeryBeating the odds: a rare case of supracardiac total anomalous pulmonary venous return (TAPVR) in an adult patient.
BMJ case reportsLong-term outcomes of total correction for isolated total anomalous pulmonary venous connection: lessons from 50-years' experience.
Interactive cardiovascular and thoracic surgerySuperior Approach for Supracardiac Total Anomalous Pulmonary Venous Connection.
The Annals of thoracic surgeryCongenital heart defects in Williams syndrome.
The Turkish journal of pediatricsMorphological dilemma: Anomalous pulmonary venous confluence or cor triatriatum-does it matter?
Journal of the Saudi Heart AssociationPrenatal diagnosis of total anomalous pulmonary venous connection by 2D and 3D fetal echocardiography.
Echocardiography (Mount Kisco, N.Y.)Outcomes of Surgery for Mixed Total Anomalous Pulmonary Venous Drainage in Children.
Seminars in thoracic and cardiovascular surgeryA rare variant of intracardiac total anomalous pulmonary venous connection.
Revista portuguesa de cardiologia : orgao oficial da Sociedade Portuguesa de Cardiologia = Portuguese journal of cardiology : an official journal of the Portuguese Society of CardiologyRetroesophageal Infracardiac Total Anomalous Pulmonary Venous Drainage.
World journal for pediatric & congenital heart surgeryPrenatal diagnosis of total and partial anomalous pulmonary venous connection: multicenter cohort study and meta-analysis.
Ultrasound in obstetrics & gynecology : the official journal of the International Society of Ultrasound in Obstetrics and GynecologyTotal anomalous pulmonary venous connection (TAPVC): A familial cluster of 3 siblings.
Echocardiography (Mount Kisco, N.Y.)Prenatal diagnosis of isolated total anomalous systemic venous connection to the left atrium.
Cardiology in the youngTotal Anomalous Pulmonary Venous Connection in Children: Preoperative Evaluation with Low-Dose Multidetector Computed Tomographic Angiography.
Texas Heart Institute journalWhole-exome sequencing identifies SGCD and ACVRL1 mutations associated with total anomalous pulmonary venous return (TAPVR) in Chinese population.
OncotargetType IV Total Anomalous Pulmonary Venous Connection.
World journal for pediatric & congenital heart surgeryObstructed Infradiaphragmatic Total Anomalous Pulmonary Venous Return in a 13-Day-Old Infant Presenting Acutely to the Emergency Department: A Case Report.
The Journal of emergency medicinePrenatal diagnoses of an uncommon isolated obstructed supracardiac total anomalous pulmonary venous connection: Case report and review of the literature (CARE compliant).
MedicineSurgical Considerations in Total Anomalous Pulmonary Venous Connection.
Seminars in cardiothoracic and vascular anesthesiaAnomalous pulmonary venous connection: An underestimated entity.
Revista portuguesa de cardiologia : orgao oficial da Sociedade Portuguesa de Cardiologia = Portuguese journal of cardiology : an official journal of the Portuguese Society of CardiologyContinuous Cardiopulmonary Bypass During the Repair of Total Anomalous Pulmonary Venous Return.
World journal for pediatric & congenital heart surgeryTotal Anomalous Pulmonary Venous Connection: Preoperative Anatomy, Physiology, Imaging, and Interventional Management of Postoperative Pulmonary Venous Obstruction.
Seminars in cardiothoracic and vascular anesthesiaMultidetector Computed Tomographic Angiography Imaging of Congenital Pulmonary Venous Anomalies: A Pictorial Review.
Canadian Association of Radiologists journal = Journal l'Association canadienne des radiologistesPerioperative and Anesthetic Considerations in Total Anomalous Pulmonary Venous Connection.
Seminars in cardiothoracic and vascular anesthesia[Tetralogy of Fallow with Total Anomalous Pulmonary Vein Return and Atrial Septal Defect;Successful Two-staged Surgical Management;Report of a Case].
Kyobu geka. The Japanese journal of thoracic surgeryUnusual presentation of total anomalous systemic venous connection.
Asian cardiovascular & thoracic annalsDescending aortic flow reversal in obstructed total anomalous pulmonary venous connection.
Cardiology in the youngBodily isomerism is an independent risk factor for pulmonary hypertension in adults with congenital heart disease.
Therapeutic advances in respiratory diseaseTotal anomalous pulmonary venous connection with ventricular septal defects.
Asian cardiovascular & thoracic annalsEarly- and intermediate-term results of surgical correction in 122 patients with total anomalous pulmonary venous connection and biventricular physiology.
Journal of cardiothoracic surgeryModified Senning Procedure for Correction of Atrioventricular Discordance With Total Anomalous Pulmonary Venous Return, Atrial Situs Inversus, Dextrocardia, and Bilateral Superior Venae Cavae.
The Annals of thoracic surgeryMagnetic resonance imaging in the assessment of anomalous pulmonary venous connections.
RadiologiaPortal Vein Thrombosis of a Newborn with Corrected Total Anomalous Pulmonary Venous Return.
Turkish journal of haematology : official journal of Turkish Society of Haematology[Total Anomalous Pulmonary Venous Connection].
Kyobu geka. The Japanese journal of thoracic surgery[Total isolated anomalous pulmonary venous return: Are there any clues for prenatal screening?].
Gynecologie, obstetrique & fertiliteRepair Type Influences Mode of Pulmonary Vein Stenosis in Total Anomalous Pulmonary Venous Drainage.
The Annals of thoracic surgeryShared Segment Analysis and Next-Generation Sequencing Implicates the Retinoic Acid Signaling Pathway in Total Anomalous Pulmonary Venous Return (TAPVR).
PloS oneProfile and outcome of congenital heart diseases in children: a preliminary experience from a tertiary center in sokoto, north Western Nigeria.
The Nigerian postgraduate medical journalAdult Scimitar Syndrome: A Surgical Approach.
Heart, lung & circulationTotal anomalous pulmonary venous return in siblings.
Journal of cardiovascular ultrasoundAssociações
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Exercise Capacity and Pulmonary Function in Pediatric Patients With Anomalous Pulmonary Venous Connection Post-Surgical Repair: A Retrospective Analysis.
- Left Ventricular Rupture Due to Congenital Partial Defect of the Left Ventricular Free Wall.
- Importance of clinical practice guidelines for specialized delivery room resuscitation of newborns with prenatally diagnosed critical congenital heart disease.Journal of perinatology : official journal of the California Perinatal Association· 2026· PMID 41490934mais citado
- High risk and low incidence diseases: Cyanotic critical congenital heart disease.
- A De Novo Loss-of-Function NCKAP1 Variant in a Boy with Neurodevelopmental Delay and Congenital Heart Defect.
- Left superior vena cava or left vertical vein in supracardiac total anomalous pulmonary venous drainage - Does it make a difference?
- Determination of anomalous pulmonary venous return with high-pitch low-dose computed tomography in paediatric patients.
- Neonatal repair of truncus arteriosus with "scimitar-like" mixed total pulmonary venous return.
- Atresia of the common pulmonary vein.
- Stenting of the vertical vein in obstructed total anomalous pulmonary venous return as rescue procedure in a neonate.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:99125(Orphanet)
- OMIM OMIM:106700(OMIM)
- MONDO:0007130(MONDO)
- GARD:16896(GARD (NIH))
- Busca completa no PubMed(PubMed)
- Q2557206(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
