A síndrome da cimitarra é caracterizada por uma combinação de anomalias cardiopulmonares, incluindo conexão de retorno venoso pulmonar anômalo parcial do pulmão direito à veia cava inferior, levando à criação de um shunt da esquerda para a direita.
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A síndrome da cimitarra é caracterizada por uma combinação de anomalias cardiopulmonares, incluindo conexão de retorno venoso pulmonar anômalo parcial do pulmão direito à veia cava inferior, levando à criação de um shunt da esquerda para a direita.
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Os sinais que médicos procuram e os exames que confirmam
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Publicações mais relevantes
Exercise Capacity and Pulmonary Function in Pediatric Patients With Anomalous Pulmonary Venous Connection Post-Surgical Repair: A Retrospective Analysis.
Anomalous pulmonary venous connection (APVC), including total (TAPVC) and partial (PAPVC) forms, is a congenital heart defect with abnormal pulmonary vein drainage; and while surgical repair has improved survival, its long-term impact on cardiopulmonary function remains unclear. This retrospective study evaluated exercise capacity and pulmonary function in 26 pediatric APVC patients (17 TAPVC, 9 PAPVC) using cardiopulmonary exercise testing (CPET) and compared them with 63 age-matched healthy controls. Patients with complex defects or significant comorbidities were excluded. Results showed significantly lower anaerobic threshold VO2 (p = 0.03), peak VO2 (p < 0.001) and peak heart rate (p = 0.02) in the APVC group, indicating impaired exercise capacity; though no differences were found between TAPVC and PAPVC subgroups. Despite preserved resting lung function, these findings suggest that children with repaired APVC experience persistent exercise limitations, underscoring the importance of routine functional assessment and potential rehabilitation, with further studies needed to clarify underlying mechanisms and guide long-term care.
Partial Anomalous Pulmonary Venous Return in Lung Cancer Surgery: Diagnostic Challenges and Surgical Considerations in Two Cases.
Partial anomalous pulmonary venous return (PAPVR) is a rare congenital anomaly in which one or more pulmonary veins drain into the systemic venous system instead of the left atrium, in the absence of associated cardiac defects such as atrial septal defect. When only a single anomalous pulmonary vein is involved, the resulting shunt volume is typically small, allowing asymptomatic progression into advanced age. Consequently, such cases are often incidentally diagnosed or remain undetected. We report herein two cases of PAPVR that required pulmonary resection for primary or metastatic lung cancer. In Patient 1, PAPVR was successfully identified preoperatively using three-dimensional computed tomography in the lobe with cancer, enabling appropriate surgical planning for lobectomy. In Patient 2, segmentectomy was performed to preserve lung function: PAPVR was not recognized preoperatively on conventional two-dimensional computed tomography but only identified postoperatively, in a different lobe to the one with cancer. A deliberate awareness of the possible presence of PAPVR and accurate identification of PAPVR before surgery are essential in patients undergoing pulmonary resection. Segmentectomy may be a viable surgical option in select cases complicated by PAPVR because it potentially minimizes the reduction in pulmonary blood flow while preserving lung function.
Scimitar Syndrome Incidentally Identified During the Workup for Acute Appendicitis in a Young Adult Female: A Case Report.
While congenital pulmonary venolobar syndrome (CPVS), including Scimitar syndrome and horseshoe lung, is highly uncommon in adults, acute appendicitis is a common surgical emergency. This case report emphasizes the difficulties in diagnosing patients and the possibility of misdiagnosis, highlighting the significance of clinical awareness for the best possible care. A laparoscopic appendectomy was performed on a 21-year-old female patient who presented with symptoms of acute appendicitis. During the procedure, a suspicious cecal tumor and a subserosal, dilated retrocecal appendix were observed. The patient was identified as having right lung hypoplasia, cardiac dextroposition, and partial anomalous pulmonary venous return (PAPVR), indicating the presence of Scimitar syndrome along with horseshoe lung. These findings were confirmed by post-operative CT imaging. The appendix histopathology and colonoscopy were unremarkable, and the cardiac assessment, including the electrocardiogram and echocardiogram, was also normal. Incidental CPVS in adults requires diligent recognition for optimal management. This case contributes to the limited research on adult manifestations of Scimitar syndrome and associated abnormalities, which is expanded by this instance.
Unmasking an Anomalous Vein: Surgical Repair of Left Upper Pulmonary Vein Drainage into the Innominate Vein.
Partial anomalous pulmonary venous return (PAPVR) is a rare congenital anomaly characterized by one or more pulmonary veins draining into the systemic venous system. We present the case of a 51-year-old woman with PAPVR involving the left upper pulmonary vein (LUPV) draining into the left innominate vein via a vertical vein, diagnosed after investigation of progressive dyspnea and lower limb edema. The diagnosis was confirmed through contrast-enhanced CT and echocardiography. The patient underwent surgical correction of the anomalous return along with tricuspid valve repair. Postoperative recovery was uneventful. This case highlights the importance of recognizing PAPVR in adult patients presenting with unexplained right heart dilation or symptoms of right heart overload.
Computational Predictive Modeling of Surgical Outcomes in Total Anomalous Pulmonary Venous Connection: Assessing the Impact of Pulmonary Venous Confluence Size on Preoperative Planning.
To develop a predictive model for optimal anastomosis sizing in TAPVC surgery, focusing on the role of pulmonary venous confluence (PVC) size. A patient-specific fluid-structure interaction (FSI) model simulated blood flow through various anastomosis sizes. Key variables included body weight, anastomosis length, and PVC size. The model's predictions were validated against postoperative echocardiographic measurements from nine TAPVC cases. A strong positive correlation was found between flow velocity and the ratio of body weight to anastomosis length and PVC circumference. Including PVC size significantly improved predictive accuracy. No significant difference was observed between predicted and measured velocities. PVC size is a critical factor for planning TAPVC surgery. Incorporating it into computational models enhances the prediction of flow dynamics and supports personalized surgical decision-making.
Publicações recentes
Surgical and Catheter-Based Intervention in Pediatric Pulmonary Vein Stenosis.
[Scimitar Syndrome in a young adult with an arteriovenous fistula from the celiac trunk - A rare adult presentation].
Intra-atrial Baffling of an Infradiaphragmatic Scimitar Vein without Circulatory Arrest.
Discovery and management of accessory hemidiaphragm during video-assisted thoracoscopic segmentectomy for pulmonary nodule: a case report.
Early outcomes of a formal robotic congenital cardiac surgery program.
📚 EuropePMC616 artigos no totalmostrando 197
Partial Anomalous Pulmonary Venous Return in Lung Cancer Surgery: Diagnostic Challenges and Surgical Considerations in Two Cases.
The Tokai journal of experimental and clinical medicineScimitar Syndrome Incidentally Identified During the Workup for Acute Appendicitis in a Young Adult Female: A Case Report.
CureusUnmasking an Anomalous Vein: Surgical Repair of Left Upper Pulmonary Vein Drainage into the Innominate Vein.
Portuguese journal of cardiac thoracic and vascular surgeryComputational Predictive Modeling of Surgical Outcomes in Total Anomalous Pulmonary Venous Connection: Assessing the Impact of Pulmonary Venous Confluence Size on Preoperative Planning.
Journal of cardiovascular translational researchHorseshoe Lung Associated with Left-sided Scimitar Syndrome in an Infant with Complex Congenital Heart Disease.
Journal of cardiovascular echographyDon't Miss the Sword in the Lung: Unveiling a Previously Undiagnosed Congenital Syndrome in a Suspected Myocardial Infarction with Nonobstructive Coronary Arteries Patient.
Journal of cardiovascular echographyLeft Ventricular Rupture Due to Congenital Partial Defect of the Left Ventricular Free Wall.
Interdisciplinary cardiovascular and thoracic surgeryTranscatheter Management of Atypical Scimitar Syndromes With Dual Venous Drainage.
JACC. Case reportsTranscatheter resolution of a post-surgical "Iatrogenic" circular shunt in a child.
Cardiology in the youngEmbolización de secuestro pulmonar en paciente con síndrome de cimitarra: reporte de caso.
Archivos de cardiologia de MexicoAscending Vertical Vein Aneurysm.
Methodist DeBakey cardiovascular journal[Utility of Low-Dose CT Angiography in the Diagnosis of Neonatal Scimitar Syndrome].
RoFo : Fortschritte auf dem Gebiete der Rontgenstrahlen und der NuklearmedizinTotal Anomalous Pulmonary Venous Connections.
Clinics in perinatologyCardiac Magnetic Resonance Imaging in the Evaluation and Management of Scimitar Syndrome.
Annals of thoracic surgery short reportsMinimally Invasive Repair of Sinus Venosus Atrial Septal Defects and Anomalous Pulmonary Venous Connections via Vertical Right Axillary Thoracotomy.
Journal of cardiovascular development and disease[Agenesis of the left pulmonary artery with hypoplasia of the homolateral lung].
La Revue du praticienPractical Considerations for Endovascular Treatment of Pulmonary Sequestration-Induced Hemoptysis: Two Case Reports and Review of Literature.
Journal of the Korean Society of RadiologyScimitar Syndrome: A Rare Congenital Conundrum in a Child With Stridor.
Pediatric pulmonology'Congenitally corrected' Scimitar syndrome? An anomalous unilateral single pulmonary vein variant.
BMJ case reportsTranscatheter correction of the scimitar variant with dual pulmonary venous drainage-an international multicentre series.
Cardiology in the youngCongenital extrahepatic portosystemic shunt with partial anomalous pulmonary venous return and aneurysmal dilation of the pulmonary artery: successful management of a complex multisystem congenital anomaly.
Cardiology in the youngThe unconventional surgical management of an infant with rare Scimitar syndrome variant.
Cardiology in the youngAn Adult With Giant Vertical Vein in Total Anomalous Pulmonary Venous Connection Combined With Pulmonary Valve Stenosis.
Echocardiography (Mount Kisco, N.Y.)Left Atrial Mechanics in Isolated Total Anomalous Pulmonary Venous Connection after Repair.
Journal of the American Society of Echocardiography : official publication of the American Society of EchocardiographyExercise Capacity and Pulmonary Function in Pediatric Patients With Anomalous Pulmonary Venous Connection Post-Surgical Repair: A Retrospective Analysis.
The Kaohsiung journal of medical sciencesTotal Anomalous Pulmonary Venous Connection: A Case Series.
The Journal of the Association of Physicians of IndiaNationwide registry study of long term survival and comorbidities in total anomalous pulmonary venous connection in Denmark.
Scientific reportsSuccessful treat-and-repair strategy in a 5 year old with partial anomalous pulmonary venous connection, atrial septal defect, and severe pulmonary hypertension.
Cardiology in the youngMYRF gene mutation leading to coronary artery anomaly combined with 46,XY sex development disorder, a case report and literature review.
BMC pediatricsHemi-Senning baffle for scimitar syndrome correction.
JTCVS techniquesScimitar syndrome: Updated follow-up of the multipatch technique.
JTCVS techniquesPreference for double-patch technique in adult patients with partial anomalous pulmonary venous return.
Cardiovascular journal of AfricaCRB2-Related Syndrome in 2 New Patients: Three Novel Variants.
Molecular syndromologyThe Long Shadow of Repair: Late-Onset Atrioventricular Block and Atrial Arrhythmias After Scimitar Syndrome and Mitral Annuloplasty.
Reports (MDPI)Modified double-decker repair for pediatric scimitar syndrome.
JTCVS techniquesDuctus arteriosus obstruction induced by vertical vein stenting in single-ventricle physiology with supracardiac total anomalous pulmonary venous connection.
Cardiology in the youngInfracardiac total anomalous pulmonary venous drainage with concomitant hypoplastic aortic arch in a preterm neonate: a rare and complex surgical challenge.
Cardiology in the youngPartial anomalous pulmonary venous return: diagnostic challenges and successful correction in a patient with progressive pulmonary hypertension.
BMJ case reportsThe double scimitar sign.
Cardiology in the youngMultimodality Imaging in Presurgical Evaluation of Total Anomalous Pulmonary Venous Connection: Single-Center Practice Variability and a Systematic Review of Diagnostic Error.
Journal of the American Society of Echocardiography : official publication of the American Society of EchocardiographyIs There an Ideal Age or Weight for the Warden Procedure in Patients With Partial Anomalous Pulmonary Venous Return?
The Annals of thoracic surgeryAtrial Fibrillation-Induced Cardiomyopathy in Scimitar Syndrome With Electrically Silent Anomalous Pulmonary Vein: An Adult Case Report.
CJC pediatric and congenital heart diseasePostrepair Pulmonary Vein Stenosis: Addressing Anatomic and Patient Risk Factors to Improve Outcomes.
Seminars in thoracic and cardiovascular surgery. Pediatric cardiac surgery annualNeonatal Atrial Flutter: A Novel Triad for Immediate Electrocardiographic Diagnosis.
The journal of Tehran Heart CenterUnveiling the Mystery of Horseshoe Lung: A Case Report.
CureusRobotic approach for surgical correction of scimitar syndrome via direct anastomosis.
JTCVS techniquesPrognostic factors in pediatrics TAPVC: a 10-year retrospective study.
Scientific reportsOver 3,000 Minimally Invasive Thoracotomies From the European Congenital Heart Surgeons Association for Quality Repairs of the Most Common Congenital Heart Defects: Safe and Routine for Selected Repairs.
World journal for pediatric & congenital heart surgeryA "hybrid" approach to total anomalous pulmonary venous return repair.
Cardiology in the youngA bleeding sword: Scimitar syndrome in a child with hematemesis due to esophageal varices - a case report.
Annals of medicine and surgery (2012)Delayed Diagnosis of Partial Anomalous Pulmonary Venous Return in an Adult With Pulmonary Hypertension.
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Pediatric radiologyScimitar Syndrome: Unveiling the Complexities of a rare Congenital Cardiopulmonary Anomaly.
European journal of case reports in internal medicinePrenatal diagnosis of a de novo 17q25.3 microdeletion encompassing RAC3 and CSNK1D in a fetus associated with partial agenesis of the corpus callosum, small brain volume, micrognathia and total anomalous pulmonary venous return.
Taiwanese journal of obstetrics & gynecologyPredicting the Need for Pulmonary Venous Reintervention in Total Anomalous Pulmonary Venous Connection: The Role of Preoperative Echocardiographic Metrics.
Echocardiography (Mount Kisco, N.Y.)Scimitar syndrome: A case report.
Radiology case reportsAdult-type scimitar syndrome.
European heart journal. Cardiovascular ImagingA Case of Incomplete Scimitar Syndrome in a Quinquagenarian Male.
CureusTotal Anomalous Pulmonary Venous Drainage Caused by Malposition of Septum Primum in Adults.
Echocardiography (Mount Kisco, N.Y.)Comparison of different approaches applied for surgical correction of partial anomalous pulmonary venous connection.
Cardiology in the youngA rare case of mal-positioning of an internal jugular central venous catheter due to an anomalous right upper pulmonary venous return.
The journal of vascular accessA Rare Case of Anomalous Pulmonary Venous Return.
Echocardiography (Mount Kisco, N.Y.)Total Anomalous Pulmonary Venous Return, Marfan Syndrome, and Severe Combined Immunodeficiency: A Lethal Combination?
World journal for pediatric & congenital heart surgeryOutcomes in Late Presenting Obstructed Infracardiac Total Anomalous Pulmonary Venous Connection-Single Centre Experience.
World journal for pediatric & congenital heart surgeryThe Role of Fetal Echocardiography in Predicting Postnatal Pulmonary Venous Obstruction in Neonates with TAPVR: A Single Center Experience.
Pediatric cardiologyA Curious Case of Scimitar Syndrome That Defies Embryology.
Annals of thoracic surgery short reportsAnatomy vs. shunt fraction: haemodynamic consequences in atrial septal defects and partial anomalous pulmonary venous connection-a comprehensive CMR study.
European heart journal. Cardiovascular ImagingTranscatheter Embolization in Congenital Cardiovascular Malformations-Variable Use of Vascular Plugs.
Cardiovascular therapeuticsPercutaneous Transcatheter Approach to Partial Anomalous Pulmonary Venous Return: A Case Series.
The American journal of cardiologyFactor Analysis of the Missed Diagnosis of Total Anomalous Pulmonary Venous Connection in Prenatal Echocardiography.
Birth defects researchNew Fetal Sonographic Marker to Rule Out Total Anomalous Pulmonary Venous Return: Color Doppler Drainage From Pulmonary Vein to Atrium to Ventricle (CDDVAV).
Echocardiography (Mount Kisco, N.Y.)Prenatal MR Diagnosis of Total Anomalous Pulmonary Venous Connection and Related Brain Growth Changes.
Journal of magnetic resonance imaging : JMRIUnveiling the anomaly: Scimitar syndrome in a middle-aged female patient.
Radiology case reportsAn explainable deep learning model to predict partial anomalous pulmonary venous connection for patients with atrial septal defect.
BMC pediatricsSingle Meandering Right Pulmonary Vein With Potential Systemic Arterial Fistula: Serial Cardiac MRI Assessment With 4D Flow Characterization.
Circulation. Cardiovascular imagingAnalysis and Visualization of Inter-/Intra-surgeon Variability Using Surgical Simulation for Partial Anomalous Pulmonary Venous Connection Repair.
Pediatric cardiologyPseudo hepatic vein thrombosis in a newborn with infracardiac total anomalous pulmonary venous connection.
Pediatric radiologySuccessful repair of infracardiac total anomalous pulmonary venous connection with nonconfluent bilateral pulmonary veins.
Asian cardiovascular & thoracic annalsOutcomes of the Modified Warden Procedure for Partial Anomalous Pulmonary Venous Connection Drainage to a High Location in the Superior Vena Cava.
Heart, lung & circulationHybrid stage 1 Norwood combined with reverse Blalock-Taussig shunt and sutureless repair of total anomalous pulmonary venous connections.
Multimedia manual of cardiothoracic surgery : MMCTSImpact of the pulmonary venous entry site morphology on postoperative pulmonary vein stenosis in total anomalous pulmonary venous connection patients.
Journal of the Formosan Medical Association = Taiwan yi zhiScimitar Syndrome: A Thorough Diagnosis in a Pediatric Patient.
CureusOutcomes of Adults With Unrepaired Partial Anomalous Pulmonary Venous Return and Intact Atrial Septum.
Journal of the American Heart AssociationSurgical Repair of Total Anomalous Pulmonary Venous Connection into the Superior Vena Cava: A Case Report.
World journal for pediatric & congenital heart surgeryAtrial thrombus after total anomalous pulmonary venous connection repair.
Asian cardiovascular & thoracic annalsPrenatal diagnosis of scimitar syndrome.
Ginekologia polska[Mispositioned central line with catheterization of partial anomalous pulmonary venous return].
Revue medicale de LiegePercutaneous transcatheter treatment for partial anomalous pulmonary right venous connection to the superior caval vein without atrial septal defect.
Catheterization and cardiovascular interventions : official journal of the Society for Cardiac Angiography & InterventionsImages in Medicine: Inability to Advance Pulmonary Artery Catheter Unmasking Anomalous Infra-Cardiac Right Pulmonary Venous Return in a Middle-Aged Adult.
South Dakota medicine : the journal of the South Dakota State Medical AssociationClinical Outcomes, Predictors, and Surgical Management of Infracardiac Total Anomalous Pulmonary Venous Connection.
Pediatric cardiologyAdvancing prenatal diagnosis: Echocardiographic detection of Scimitar syndrome in China - A case series.
Open medicine (Warsaw, Poland)Scimitar Syndrome in Adulthood: Challenges in Management and Individualized Approaches.
CureusDiagnostic value of reversed differential cyanosis in (supra)cardiac total anomalous pulmonary venous return.
Pediatric researchScimitar syndrome in a four-month-old infant.
Ghana medical journalCongenital Lung Malformations: A Pictorial Review of Imaging Findings and a Practical Guide for Diagnosis.
Children (Basel, Switzerland)Long-Term Outcomes of Surgical Repair of Supracardiac Total Anomalous Pulmonary Venous Connection.
Pediatric cardiologyTAPVR: Molecular Pathways and Animal Models.
Advances in experimental medicine and biologyTotal Anomalous Pulmonary Venous Connections, Human Genetics.
Advances in experimental medicine and biologyAdult Partial Anomalous Pulmonary Venous Connection: Case Reports (Including a Case of Scimitar Syndrome).
The Journal of the Association of Physicians of IndiaInfracardiac total anomalous pulmonary venous connection with dual drainage into the hepatic and portal venous system.
Journal of cardiovascular computed tomographyFactors associated with early postoperative mortality after total anomalous pulmonary venous connection repair: A retrospective cohort study.
MedicineScimitar Syndrome in a Pediatric Cohort.
World journal for pediatric & congenital heart surgeryDual Drainage Total Anomalous Pulmonary Venous Connection With Infracardiac and Supracardiac Drainage.
World journal for pediatric & congenital heart surgeryValley Index as a Predictor of Prenatal Diagnosis of Total Anomalous Pulmonary Venous Connection.
Fetal diagnosis and therapyInfracardiac Total Anomalous Pulmonary Venous Connection.
Radiology. Cardiothoracic imagingAdvanced Imaging Guidance for Ductus Venosus Stenting in Obstructed Total Anomalous Pulmonary Venous Return.
World journal for pediatric & congenital heart surgeryUltrasound and computed tomography angiography diagnosis of fetal right atrial isomerism with cardiac total anomalous pulmonary venous connection and intestinal malrotation: a case report and literature review.
Pediatric radiologyScimitar syndrome with vein stenosis in an infant.
BMJ case reportsInsight into the research history and trends of total anomalous pulmonary venous connection: a bibliometric analysis.
Journal of cardiothoracic surgeryImaging spectrum of horseshoe lung: A series of four cases.
SA journal of radiologyPercutaneous closure of a sinus venosus defect with partial anomalous pulmonary venous return.
The Journal of invasive cardiologyEleven Years After Scimitar Syndrome Repair With the Lugones Technique: Usefulness of Four-Dimensional Flow Magnetic Resonance Imaging.
World journal for pediatric & congenital heart surgeryTotal Anomalous Pulmonary Venous Connection in Adults: Should We Offer Surgery?
World journal for pediatric & congenital heart surgeryClinical characteristics, imaging findings, management, and outcomes of patients with scimitar syndrome at a tertiary referral healthcare center in Colombia.
The international journal of cardiovascular imagingComplex pulmonary venous drainage pattern with obstructive partial anomalous pulmonary venous connection and associated meandering pulmonary vein.
Pediatric pulmonologyPartial Anomalous Pulmonary Venous Return Incidentally Detected at Lung Cancer Screening With Low-dose Thoracic CT.
Archivos de bronconeumologiaIsolated Partial Anomalous Pulmonary Veins: A 10-Year Experience at a Single Center.
The Journal of surgical researchALCAPA in Children with Complex Congenital Heart Disease: A Multicenter Study.
Pediatric cardiologyCongenital Pulmonary Lymphangiectasia Masked by Postoperative Pulmonary Venous Obstruction in an Infant with Total Anomalous Pulmonary Venous Connection.
International heart journalMultimodality assessment of a child with Turner syndrome and a late diagnosis of mixed partial anomalous pulmonary venous return without atrial septal defect. Case report.
Archivos de cardiologia de MexicoPrenatal diagnosis of total anomalous pulmonary venous connection with vertical vein branching into two.
Journal of medical ultrasonics (2001)Unveiling a Unique Case of Scimitar Syndrome: Clinical Significance and Multidisciplinary Management Challenges in Pakistan.
CureusRare case of total anomalous pulmonary venous return into the right atrium in situs solitus.
Cardiology in the youngDual drainage in "partial" anomalous pulmonary venous connection.
Journal of cardiovascular computed tomographyRight S3 segmentectomy for lung cancer with partial anomalous pulmonary venous return in the right upper pulmonary vein: A case report.
Thoracic cancerLeft sided Scimitar syndrome.
Annals of pediatric cardiologyUnilateral Anomalous Pulmonary Venous Return into Coronary Sinus.
Radiology. Cardiothoracic imagingA rare variant of scimitar syndrome characterised by right pulmonary vein drainage to portal vein with eventeration of diaphragm.
Cardiology in the youngA 15-Year Experience With Total Anomalous Pulmonary Venous Connection in Vietnam.
World journal for pediatric & congenital heart surgeryBronchial Asthma With Scimitar Syndrome: A Case Report.
CureusA rare case of scimitar syndrome with pulmonary arterial hypertension in an adult female.
Pulmonary circulationPersistent Patent Vertical Vein After Repair of Total Anomalous Pulmonary Venous Connection (TAPVR): A Rare Cause of Hypoxemia Post-Fontan Procedure.
Pediatric cardiologySTIC-HD live flow technology in the antenatal diagnosis of scimitar syndrome: A case report.
Echocardiography (Mount Kisco, N.Y.)An 8-year-old boy with Scimitar syndrome: Presentation with gastroesophageal reflux symptoms and concurrent associations, including ectopic herniated liver.
Pediatric pulmonologyScimitar syndrome, bronchiectasis, haemoptysis and a pneumonectomy.
Respirology case reportsThe Sword and the Crown: Echocardiography for the Detection of a Rare Combination of Congenital Heart Disease.
CASE (Philadelphia, Pa.)Partial anomalous pulmonary venous return: a casual finding in many cases.
Archivos de cardiologia de MexicoPrenatal diagnosis of isolated total anomalous pulmonary venous connection (TAPVC) to coronary sinus.
Ginekologia polskaScimitar syndrome with large atrial septal defect and a rare partial anomalous venous drainage in an adult: a case report.
European heart journal. Case reportsContemporary outcomes for functional single ventricle with total anomalous pulmonary venous connection.
The Journal of thoracic and cardiovascular surgery[Left Metastatic Lung Tumor for a Patient with Scimitar Syndrome:Report of a Case].
Kyobu geka. The Japanese journal of thoracic surgeryUnilateral bilobar pulmonary aplasia with anomalous pulmonary venous return: A rare combination of congenital airway and vascular anomalies.
Pediatric pulmonologyRisk factors associated with prolonged intensive care unit stay following surgery for total anomalous pulmonary venous connection: a retrospective study.
Journal of cardiothoracic surgeryLong-term outcomes of functional single ventricles associated with heterotaxy syndrome†.
European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic SurgeryModified L-shaped incision technique for supracardiac total anomalous pulmonary venous connection as an alternative to sutureless technique.
International journal of surgery (London, England)Clinical exome sequencing efficacy and phenotypic expansions involving anomalous pulmonary venous return.
European journal of human genetics : EJHGIntracardiac total anomalous pulmonary venous return or septum primum malposition? Complete repair in left atrial isomerism.
Multimedia manual of cardiothoracic surgery : MMCTSA rare cause of angina: scimitar syndrome case report.
European heart journal. Case reportsCase report: A unique quadruple coexisting anomaly-scimitar syndrome, atrial septal defect, vascular ring, and pulmonary sequestration.
Frontiers in pediatricsScimitar syndrome with hemi-cor triatriatum.
Acta cardiologicaNovel operative technique for Scimitar syndrome: Posterior flap technique.
Asian cardiovascular & thoracic annalsOutcomes and Risk Factors of Interventions for Pediatric Post-operative Pulmonary Vein Stenosis.
Pediatric cardiologyLong-Term Outcomes of Unrepaired Isolated Partial Anomalous Pulmonary Venous Connection With an Intact Atrial Septum.
The American journal of cardiologyWhale's tail sign in fetus with coronary sinus total anomalous pulmonary venous connection.
Ultrasound in obstetrics & gynecology : the official journal of the International Society of Ultrasound in Obstetrics and GynecologySurgical repair of mitral valve regurgitation with anomalous unilateral single pulmonary vein.
Journal of cardiology cases[Integrated management during the perinatal period for total anomalous pulmonary venous connection].
Zhongguo dang dai er ke za zhi = Chinese journal of contemporary pediatricsSuccessful Surgical Management of Incidentally Diagnosed Scimitar Syndrome With Anomalous Connection of the Left Hepatic Vein to Coronary Sinus and Persistent Left Superior Vena Cava.
CureusSutureless Repair of Extracardiac Univentricular Total Anomalous Pulmonary Venous Connection.
The Annals of thoracic surgeryMultimodality diagnostic imaging for anomalous pulmonary venous connections: a pictorial essay.
Pediatric radiologyA unique bizarre subtype of mixed total anomalous pulmonary venous connection.
Cardiology in the youngModification of the Warden Procedure for Surgical Repair of Partial Anomalous Pulmonary Venous Connection.
World journal for pediatric & congenital heart surgeryExtracardiac conduit as alternative repair for scimitar syndrome.
Annals of pediatric cardiologyRare case of horseshoe lung associated with scimitar syndrome in Palestine: a case report.
Annals of medicine and surgery (2012)Total or Partial? Rare Cases of Partial Anomalous Pulmonary Venous Return: Three Pulmonary Veins Connected to the Coronary Sinus.
Balkan medical journalUnrecognized Patent Foramen Ovale in Patient With Sinus Venosus-Type Atrial Septal Defect With Partial Anomalous Pulmonary Venous Return.
A&A practiceAnesthesia management of living donor liver transplantation in a patient with scimitar syndrome.
Saudi journal of anaesthesiaWorsening Dyspnea and New-Onset Atrial Fibrillation in a 79-Year-Old Woman.
JAMA cardiologyBetter Late Than Never - A Case of a Congenital Left Partial Anomalous Pulmonary Venous Drainage Diagnosed and Treated in The Sixth Decade of Life.
The heart surgery forumRepair of Partial Anomalous Pulmonary Venous Connection to the Azygous Vein via Right Thoracotomy.
World journal for pediatric & congenital heart surgeryRarer Components of a Rare Disease: Accessory Hemidiaphragm and Horseshoe Lung with Scimitar Syndrome; Two Case Reports.
Current medical imagingComparison of the effects of conventional method and primary sutureless techniques on early postoperative rhythm problems in patients with total abnormal pulmonary venous return anomaly.
Cardiology in the youngPalliation of a Heterotaxy Single Ventricle Neonate with Pulmonary Atresia and Obstructed TAPVR.
Pediatric cardiologyTotal Anomalous Pulmonary Venous Return.
RadiologyPartial anomalous pulmonary venous connection diagnosed prenatally.
Pediatrics international : official journal of the Japan Pediatric SocietyMidline crossing right pulmonary veins with dual drainage to the left atrium.
Cardiology in the youngRE: Wang et al. Diagnosis of fetal total anomalous pulmonary venous connection based on the post-left atrium space ratio using artificial intelligence.
Prenatal diagnosisSupracardiac total anomalous pulmonary venous connection type Ib: Morphology and outcomes.
The Journal of thoracic and cardiovascular surgeryInfracardiac obstructive total anomalous pulmonary venous return with ventricular septal defect: a rare anomaly.
Multimedia manual of cardiothoracic surgery : MMCTSProximal Interruption of Pulmonary Artery: Spectrum of Radiological Findings With Emphasis on Chest Radiograph and Contrast-Enhanced Computed Tomography (CECT).
CureusAdult congenital horseshoe lung with bilateral pulmonary sequestration: A case report.
Acta radiologica openTwo sisters with cardiac-urogenital syndrome secondary to pathogenic splicing variant in the MYRF gene with unaffected parents: A case of gonadal mosaicism?
Molecular genetics & genomic medicineReintervention and mortality risk after total anomalous pulmonary venous connection repair.
Cardiology in the young[Scimitar syndrome with pulmonary sequestration containing carcinoma: a case report].
Zhonghua jie he he hu xi za zhi = Zhonghua jiehe he huxi zazhi = Chinese journal of tuberculosis and respiratory diseasesAnatomical attention-based prediction of postoperative pulmonary venous obstruction via CTA images.
Computerized medical imaging and graphics : the official journal of the Computerized Medical Imaging SocietyPrimary sutureless repair concomitant with the Warden procedure.
Asian cardiovascular & thoracic annalsDuctus arteriosus banding to regulate excessive pulmonary blood flow in a neonate with necrotizing enterocolitis and complex congenital heart disease, including pulmonary atresia and total anomalous pulmonary venous return: a case report.
Journal of cardiothoracic surgeryEchocardiographic evaluation of supracardiac anomalous pulmonary venous connection in children: comparison with multilayer spiral CT.
The international journal of cardiovascular imagingHypogenetic right lung with partial anomalous pulmonary venous return and accessory diaphragm: a case of "scimitar lung".
Folia morphologicaTotal anomalous pulmonary venous connection with another major congenital cardiac defect in biventricular hearts.
Asian cardiovascular & thoracic annalsComplete transcatheter correction of variant scimitar syndrome-a case report.
European heart journal. Case reportsInfluenza vaccination during pregnancy and risk of selected major structural congenital heart defects, National Birth Defects Prevention Study 2006-2011.
Birth defects researchNovel marker for diagnosis of supracardiac total anomalous pulmonary venous connection in first trimester.
Ultrasound in obstetrics & gynecology : the official journal of the International Society of Ultrasound in Obstetrics and GynecologySurgical correction of partial anomalous left superior pulmonary venous connection to the innominate vein.
Multimedia manual of cardiothoracic surgery : MMCTSComputed Tomographic 3-Dimensional Virtual Dissection Aiding in Diagnosis and Surgical Planning of a Rare Form of Obstructed Supracardiac Total Anomalous Pulmonary Venous Connection With an Unusual Scimitar-Like Arrangement.
World journal for pediatric & congenital heart surgeryMinimally invasive versus sternotomy approach for double-patch repair of partial anomalous pulmonary venous connection and sinus venosus defect in pediatric and adult patients: Mid to long-term outcomes.
Journal of cardiac surgeryA rare case on anomalous pulmonary venous drainage in congenital cardiovascular disease.
Journal of cardiac surgeryThe Lugones Procedure for Scimitar Syndrome Repair Through Right Axillary Thoracotomy: Not Only a Cosmetically Superior Approach.
World journal for pediatric & congenital heart surgeryAssociações
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Comunidades
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Exercise Capacity and Pulmonary Function in Pediatric Patients With Anomalous Pulmonary Venous Connection Post-Surgical Repair: A Retrospective Analysis.
- Partial Anomalous Pulmonary Venous Return in Lung Cancer Surgery: Diagnostic Challenges and Surgical Considerations in Two Cases.
- Scimitar Syndrome Incidentally Identified During the Workup for Acute Appendicitis in a Young Adult Female: A Case Report.
- Unmasking an Anomalous Vein: Surgical Repair of Left Upper Pulmonary Vein Drainage into the Innominate Vein.
- Computational Predictive Modeling of Surgical Outcomes in Total Anomalous Pulmonary Venous Connection: Assessing the Impact of Pulmonary Venous Confluence Size on Preoperative Planning.
- Surgical and Catheter-Based Intervention in Pediatric Pulmonary Vein Stenosis.
- [Scimitar Syndrome in a young adult with an arteriovenous fistula from the celiac trunk - A rare adult presentation].
- Intra-atrial Baffling of an Infradiaphragmatic Scimitar Vein without Circulatory Arrest.
- Discovery and management of accessory hemidiaphragm during video-assisted thoracoscopic segmentectomy for pulmonary nodule: a case report.
- Early outcomes of a formal robotic congenital cardiac surgery program.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:185(Orphanet)
- MONDO:0015987(MONDO)
- GARD:18680(GARD (NIH))
- Busca completa no PubMed(PubMed)
- Q2557206(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
