cAMP/PKA signaling in endocrine hypertension: genetic mechanisms and pathophysiological insights.

A urologic manifestation of carney complex: Bilateral Sertoli tumors and scrotal myxoma in an adolescent male.

Case Reports: Exploring the Varied Presentations and Clinical Features of Carney Complex, A Detailed Report on Three Distinct Cases.

Orbitoconjunctival Myxoma: A Case Report and a Brief Literature Review.

Familial hereditary cardiac myxoma: report of three cases and literature review.

PRKACA constitutional duplication: a specific cause of primary pigmented nodular adrenocortical disease.

From misclassified AIP variant to carney complex: a case report and retrospective evaluation of PRKAR1A in pituitary tumor predisposition.

ST-Segment Elevation Myocardial Infarction From Carney Complex Familial Myxoma Embolization.

Sinonasal Tract Osteochondromyxoma: Future Directions Beyond Morphologic Description.

Large Right Atrial Myxoma With Endocrine Abnormalities as a Possible Case of a Syndromic Disease: A Case Report.

Perioperative Care of a Patient With Carney Complex.

Dermatologic Features of Endocrine Tumor Syndromes-Systematic Review and Meta-Analysis.

Right Atrial Myxoma in a Young Patient with a DSG-2 Genetic Mutation: A Case Report.

Carney Complex During Six-Year Follow-Up and Its Association With Attention-Deficit Hyperactivity Disorder: A Case Report.

Sinonasal Tract Osteochondromyxoma: An Underrecognized Tumor Easily Mistaken for Nasal Chondromesenchymal Hamartoma.

A RARE CAUSE OF CUSHING'S SYNDROME: BILATERAL PRIMARY PIGMENTED MICRONODULAR ADRENAL DISEASE.

Case Report: The carney complex led to the tragic passing of a young girl in the prime of her life.

Familial Carney complex with embolic ischemic stroke: a case report and literature review.

Keeping Up With Carney Complex: A Case of Recurrent Cardiac Myxomas.

Cushing's syndrome due to Carney complex in two siblings.

Cyclic Cushing syndrome and endocrine disorders in two children with Carney complex.

A Case of Carney Complex with Pontine Glioma.

A Case of Myxoid Malignant Peripheral Nerve Sheath Tumor in a Patient With Carney Complex.

Recurrent Atrial Myxoma in a Patient With Carney Complex 26 Years After Heart Transplantation.

Isolated Myxoma of the External Auditory Canal: A Rare Case Report.

The Role of the Surgical Pathologist in the Recognition of Hereditary Mesenchymal Neoplasms.

Uncharted Territory: The First Case of Cardiac Myxoma in a Patient With NF2.

Cardiac Complications in Carney Complex: Right Ventricular Outflow Tract Obstruction and Pulmonary Hypertension.

Unilateral Adrenalectomy for Pediatric Cyclical Cushing Syndrome with Novel PRKAR1A Variant Associated Carney Complex.

Recurrent Cardiac Myxoma: Insights From a Fourth Recurrence.

Case Report: Cardiac myxomas and Carney complex: a case of recurrent embolic strokes and intracranial tumor growth.

Superficial angiomyxoma affecting the buccal mucosa: A detailed immunohistochemical study and literature review.

Updated Recommendations for Pediatric Surveillance in Hereditary Endocrine Neoplasia Syndromes: Multiple Endocrine Neoplasias, Hyperparathyroidism-Jaw Tumor Syndrome, and Carney Complex.

Sporadic Coexistence of Parathyroid Adenoma, Papillary Thyroid Carcinoma, Pheochromocytoma, and Cardiac Myxoma: A Multidisciplinary Approach to an Extremely Rare Tumor Constellation.

Right Ventricle Myxoma Masquerading as a Thrombus in a Pediatric Patient.

Child With Painful Purpuric Rash of the Hands and Feet.

Carney complex: A rare diagnosis at hand.

Subtle Symptoms of Large Biatrial Myxomas: A Case Study and Surgical Insights.

Oncocytic Tumors in the Familial and Syndromic Contexts: A Tri-Focal Review - Integrated Cytopathological, Pathological, and Molecular Perspectives.

Nonmalignant Adrenocorticotrophic Hormone-Independent Cushing's Syndrome in Pediatric Patients: A Retrospective Observational Cohort Study.

Cardiac myxoma: a comprehensive review.

A Rare Case of PRKACA Duplication-Associated Childhood-Onset Primary Pigmented Nodular Adrenocortical Disease.

Hybrid nerve sheath tumor of the spinal canal and neurofibromatosis-2, where the twain shall meet-a case report and review of literature.

Detection of PRKAR1A gene mutations in sporadic cardiac myxomas: a study of 24 cases.

A Case of Recurrent Eyelid Cutaneous Myxoma With Basaloid Proliferation in a Child.

Synchronous bilateral adrenalectomy for ACTH-independent Cushing's syndrome in children: multidisciplinary management.

[Superficial angiomyxoma in the scrotum].

Right Atrial Myxoma Removal Followed by COVID-19 Infection and Possibly Related Late Pericardial Effusion in a 31-Year-Old Male.

The "Pigmented Side" of Nerve Sheaths: Malignant Melanotic Nerve Sheath Tumor.

Carney complex was diagnosed following the recurrence of cardiac myxoma: A case report.

Total resection via right mini-thoracotomy for left atrial myxoma in juvenile Carney complex: a case report.

Male Infertility associated with a Novel PRKAR1A Mutation in Carney Complex.

The molecular genetics of adrenal cushing.

Challenging Diagnostic Workup of a 22-year-old Patient With Primary Pigmented Nodular Adrenocortical Disease.

Cushing syndrome in paediatric population: who and how to screen.

Recurrent left ventricular myxoma with Carney complex.

Solitary Superficial Angiomyxoma in an Uncommon Location: A Case Report and Literature Review.

Germline mutations in a G protein identify signaling cross-talk in T cells.

From cortisol-producing adrenal adenoma to atrial myxoma, through nivolumab-induced hypophysitis: a complicated case report of Carney Complex.

Surgical recurrence of cardiac myxomas in patients with the Carney complex condition: A literature review.

Myxoma: An Unusual Aggressive Orbital Lesion.

Cardiac Myxomas in Carney Complex: Single Institution Multidecade Experience.

Nasal Osteochondromyxoma Without Carney Complex: A Case Report and a Literature Review.

[Superficial angiomyxoma on the sole of the foot].

Adrenal Cushing Syndrome: Diagnosis and Management in a 10-Year-Old Boy with Carney Complex.

[Molecular genetic abnormalities in ACTH-secreting pituitary tumors (corticotropinomas): fundamental research and prospects for use in clinical practice].

Right atrial cardiac myxoma with malignant transformation to undifferentiated sarcoma: A case report.

Novel PRKAR1A mutation in Carney complex: a case report and literature review.

Squamous Metaplasia in a Schwannoma: A Unique Histologic Finding.

The clinical characteristics and pathogenic variants of primary pigmented nodular adrenocortical disease in 210 patients: a systematic review.

Right ventricular myxoma and pulmonary embolism in an adolescent with Carney complex.

Bilateral Adrenocortical Nodular Disease and Cushing's Syndrome.

Diagnosis and cardiac transplantation of a Carney syndrome-induced cardiac myxoma combined with dilated cardiomyopathy: a case report.

Carney complex: a case report of bilateral breast myxoid fibroadenomas.

Recurrent, polycystic myxoma in a Carney complex patient undergoing medical control of acromegaly.

The Spectrum of GH Excess in Carney Complex and Genotype-phenotype Correlations.

Familial syndromes associated with testicular and paratesticular neoplasms: a comprehensive review.

Pulmonary embolism from right ventricular myxoma in a child with undiagnosed Carney complex.

Frequent protein kinase A regulatory subunit A1 mutations but no GNAS mutations as potential driver in sporadic cardiac myxomas.

Sudden Death in a Child With Ocular Lesions.

Lipodystrophy in methylmalonic acidemia associated with elevated FGF21 and abnormal methylmalonylation.

Carney Complex with Left Atrial Myxoma - A Vasculitis Mimicker.

Carney complex predisposes to breast cancer: prospective study of 50 women.

Superficial Angiomyxoma in an Uncommon Area: A Case Report.

Molecular characterization of large cell calcifying sertoli cell tumors: A multi-institutional study of 6 benign and 2 malignant tumors.

Recurrent Biatrial Myxomas in Carney Complex with a Spinal Melanotic Schwannoma: Advocacy for a Rigorous Multidisciplinary Follow-Up.

The benign nature and rare occurrence of cardiac myxoma as a possible consequence of the limited cardiac proliferative/ regenerative potential: a systematic review.

Bilateral large cell calcifying Sertoli cell tumours: A testicular preservation approach in a young male.

Atypical Presentation and Course of ACTH-Independent Cushing’s Syndrome in Two Families.

Carney Complex and Its Association With Thyroid Cancer, Molecular Pathway, and Treatment.

Superficial Angiomyxoma of Axilla: A Case Report.

Carney complex: A clinicopathologic study on a single family from several Canadian provinces.

Osteochodromyxoma presenting as case of congenital nasolacrimal duct obstruction.

Genetic Testing in Hereditary Pituitary Tumors.

Germline PRKACA amplification-associated primary pigmented nodular adrenocortical disease: a case report and literature review.

Pigmented epithelioid melanocytoma arising from a teratoma of a Carney complex patient.

Newly Recognized Genetic Tumor Syndromes of the CNS in the 5th WHO Classification: Imaging Overview with Genetic Updates.

Surgical management of malignant melanotic nerve sheath tumors: an institutional experience and systematic review of the literature.

[Schwannoma, Neurofibromatosis Type 2, and Schwannomatosis in the 2021 WHO Classification of Tumors of the Central Nervous System].

Cardiac myxomas: causes, presentations, diagnosis, and management.

Whole genome sequencing resolves 10 years diagnostic odyssey in familiar myxoma.

A rare case of cutaneous myxoma with trichofolliculoma-like features.

Brain and/or Spinal Cord Tumors Accompanied with Other Diseases or Syndromes.

[Rare forms of hereditary endocrine neoplasia: co-existence of pituitary adenoma and pheochromocytoma/paraganglioma].

Multiple cardiac myxomas and cutaneous pigmentation revealing carney complex.

Malignant melanotic nerve sheath tumor with PRKAR1A, KMT2C, and GNAQ mutations.

Case Report: Atrial myxoma combined with hyperthyroidism in an adolescent with literature review.

Fourth Recurrence of Cardiac Myxoma in a Patient with Carney Complex.

Cardiac myxoma in a teenager with Carney complex.

Pituitary Tumorigenesis-Implications for Management.

Case of Bilateral Atrial Myxomas in Carney Syndrome.

Laparoscopic right adrenalectomy in a patient with Carney syndrome: A case report.

Large cell calcifying Sertoli cell tumour: molecular and immunohistochemical assessment of a series comprising non-metastasising and metastasising neoplasms.

Superficial angiomyxoma of the breast in a 25-year-old woman without Carney complex.

Atrial myxoma and associated Cushing syndrome: Carney complex.

A case report and literature review of Carney complex with atrial adenomyxoma.

An adolescent case of sellar osteochondromyxoma in the setting of spondyloepiphyseal dysplasia.

Angiomyxoma of the Breast: A Clinicopathologic Analysis of 40 Cases.

Recurrent multi-cameral cardiac myxomas in a child with Carney complex.

A 14-Year-Old Saudi Boy with Gynecomastia, Cushing Syndrome, Large-Cell Calcifying Sertoli Cell Tumor of the Testis, and Carney Complex.

Carney complex presenting as subclinical Cushing syndrome in a child due to a novel Phosphodiesterase 11A mutation.

Surgical Outcomes of Cardiac Myxoma Resection Through Right Mini-Thoracotomy.

Key changes in WHO classification 2022 of testicular tumors.

Unusual Findings in a Patient With Carney Complex due to a Novel PRKAR1A Mutation.

The Spectrum of Familial Pituitary Neuroendocrine Tumors.

Bilateral tympanic myxoma: A CARE case report.

The cAMP-signaling cancers: Clinically-divergent disorders with a common central pathway.

Abnormal Fibroblasts Drive Pigmentary Skin Lesions in a Mouse Model of Carney Complex.

Carney complex- why thorough medical history taking is so important - report of three cases and review of the literature.

New Onset Cardiac Murmur and Exertional Dyspnea in an Apparently Healthy Child: A Rare Localization of Obstructive Myxoma in the Right Ventricle Outflow Tract without Pulmonary Embolization-A Case Report and Literature Review.

Association between subclinical hyperthyroidism and a PRKAR1A gene variant in Carney complex patients: A case report and systematic review.

A Novel Missense PRKAR1A Variant Causes Carney Complex.

Efficacy of aromatase inhibitor therapy in a case with large cell calcifying Sertoli cell tumour-associated prepubertal gynaecomastia.

Trigeminal Nerve Melanotic Schwannoma in Carney Complex.

Cardiac myxoma presenting with multisystem involvement.

Genetic and clinical phenotypic analysis of carney complex with external auditory canal myxoma.

Unilateral or bilateral adrenalectomy in PPNAD: six cases from a single family followed up over 40 years.

Conjunctival myxoma masquerading as conjunctival lymphoma: A case report.

Carney complex with multiple breast tumours including breast cancer: a case report.

Phenotypic Variability in a Family with Carney Complex Accompanied by a Novel Mutation Involving PRKAR1A.

Spotty skin pigmentation in Carney complex.

Genetic Alterations in Benign Adrenal Tumors.

Gastrointestinal: Melanotic schwannoma of the pancreas associated with Carney complex: A cause of acute neoplastic symptom.

Cardiac myxomas: A narrative review.

Steroidogenic Factor-1 Lineage Origin of Skin Lesions in Carney Complex Syndrome.

Molecular genetic testing in the management of pituitary disease.

A review of multiomics platforms in pituitary adenoma pathogenesis.

Conjunctival myxoid stromal tumor of the palpebral conjunctiva: A case report.

A Case Presentation Based on Incidental Diagnosis of Atrial Myxoma in a Patient Presenting With Atrial Fibrillation and Suspected Carney Complex.

Thorahcic SMARCA4-deficient undifferentiated tumors with ganglioneuroma and enchondroma: implications for SLC7A11 and ARID1A expression: a case report.

A novel 8.57-kb deletion of the upstream region of PRKAR1A in a family with Carney complex.

Case Report: Two Myxomas of Different Echodensities on Transthoracic Echocardiography in One Patient.

Carney Complex Complicated with Primary Pigmented Nodular Adrenocortical Disease without Cushing's Syndrome Recurrence for Five Years after Unilateral Adrenalectomy.

Novel CD63-PRKCB fusion in a case of pigmented epithelioid melanocytoma.

A clinicopathologic analysis of 54 cases of cutaneous myxoma.

Large Cell Calcifying Sertoli Cell Tumor: A Clinicopathologic Study of 18 Cases With Comprehensive Review of the Literature and Reappraisal of Prognostic Features.

Superficial Angiomyxomas Frequently Demonstrate Loss of Protein Kinase A Regulatory Subunit 1 Alpha Expression: Immunohistochemical Analysis of 29 Cases and Cutaneous Myxoid Neoplasms With Histopathologic Overlap.

Bloody nipple discharge in Carney complex: A case report.

Protein kinase A drives paracrine crisis and WNT4-dependent testis tumor in Carney complex.

Large cell calcifying Sertoli cell tumour: a contemporary multi-institutional case series highlighting the diagnostic utility of PRKAR1A immunohistochemistry.

Dermatologic manifestations of pediatric cardiovascular diseases: Skin as a reflection of the heart.

Case Report: An Atypical Case of Carney Complex.

Bilateral Adrenal Hyperplasia: Pathogenesis and Treatment.

[Carney complex characterized by jugular foramen myxoma: a case report].

Gαs-Protein Kinase A (PKA) Pathway Signalopathies: The Emerging Genetic Landscape and Therapeutic Potential of Human Diseases Driven by Aberrant Gαs-PKA Signaling.

Peutz-Jeghers syndrome: Skin manifestations and endocrine anomalies (Review).

Diagnosis of Carney complex following multiple recurrent cardiac myxomas.

Dermatological and endocrine elements in Carney complex (Review).

A novel PRKAR1A gene mutation in Carney complex.

Sporadic superficial angiomyxomas demonstrate loss of PRKAR1A expression.

Ultrasonographic features of cutaneous myxomas in a patient with Carney complex.

Conjunctival myxoma: A systematic review of a rare tumor.

Multimodality Cardiac Imaging Enhances Diagnosis and Management of Recurrent Atrial Myxomas in Carney Complex.

PRKAR1A and Thyroid Tumors.

L3 rootlet recurrent melanocytic schwannoma - case report and literature review.

Carney complex: left atrial myxoma in a patient with past pituitary microadenoma and lentiginosis.

Incidentally discovered myelolipomatous adrenal adenomas, including six cases presenting with hypercortisolism.

Imaging features of Carney complex with external auditory canal myxoma.

Loss of PKA regulatory subunit 1α aggravates cardiomyocyte necrosis and myocardial ischemia/reperfusion injury.

A most versatile kinase: The catalytic subunit of PKA in T-cell biology.

Checkpoint inhibitors and radiotherapy in refractory malignant melanocytic schwannoma with Carney complex: first evidence of efficacy.

Vulvar Cutaneous Myxoma in a Patient With Carney Complex: Avoiding Pitfalls of Myxoid Lesions of the Vulva.

Noncanonical protein kinase A activation by oligomerization of regulatory subunits as revealed by inherited Carney complex mutations.

Hemorrhagic spinal melanotic schwannoma presenting as acute chest pain: A case report and literature review.

A novel mutation in PRKAR1A gene in a patient with Carney complex presenting with pituitary macroadenoma, acromegaly, Cushing's syndrome and recurrent atrial myxoma.

Carney complex: a curious case of a rare cancer syndrome caused by a novel pathogenic mutation in the PRKAR1A gene.

Genetics of Acromegaly and Gigantism.

Molecular Genetic and Genomic Alterations in Cushing's Syndrome and Primary Aldosteronism.

Multiple cardiac myxomas and acromegaly revealing carney complex.

Schwannoma with Psammoma Body.

Psammomatous melanotic schwannoma - a rare neck lump.

[Cancer-associated genodermatoses].

First Somatic PRKAR1A Defect Associated With Mosaicism for Another PRKAR1A Mutation in a Patient With Cushing Syndrome.

Genetic and Epigenetic Causes of Pituitary Adenomas.

The clinical aspects of pituitary tumour genetics.

Inherited Follicular Epithelial-Derived Thyroid Carcinomas: From Molecular Biology to Histological Correlates.

Recurrent cardiac and skin myxomas along with acromegaly: A case report of carney complex.

MANAGEMENT OF ENDOCRINE DISEASE: Carney complex: clinical and genetic update 20 years after the identification of the CNC1 (PRKAR1A) gene.

Carney triad: A case report, characteristics and literature review of this rare entity.

Newborn infant with congenital lentigines as a manifestation of Carney Complex.