Advanced Lung Cancer Inflammation Index (ALI) as an Independent Predictor for Bronchiectasis Exacerbation Risks.

Jugular Vein Occlusion-Induced Intracranial Hypertension Mimicking Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Modulator-Associated Intracranial Hypertension: A Diagnostic Pitfall.

Microbial signatures and host immune responses associated with the development of ventilator-associated pneumonia among patients with neurological injuries.

Targeting PI3Kγ anchoring enhances CFTR membrane localization and modulator efficacy via PKD1.

Effectiveness of exercise training in people with non-cystic fibrosis bronchiectasis with and without COPD.

Development of CpG-Depleted CFTR Plasmid-Based Nanoparticles for Nonviral Gene Therapy in Lung Cystic Fibrosis Disease.

Inhalable gene and RNA therapy for cystic fibrosis: perspectives and progress in clinical development.

Iloprost-loaded inhalable Nano into Micro (NiM) formulations for treating hyper-inflammation in a pre-clinical model of cystic fibrosis airway epithelial cells.

Recalibration: Exploring the Impact of Elexacaftor/Tezacaftor/Ivacaftor on Self-Concept for Adults with Cystic Fibrosis.

Colistin-stabilized antisolvent precipitation enables engineering of microcrystalline niclosamide for inhalable composite powders.

Genome-wide association study reveals two novel genetic loci associated with chronic lung allograft dysfunction.

Evaluation of the methodology of independent Community Advisory Boards in health products research and development: a mixed-methods cross-sectional survey study.

Determinants of early Elexacaftor-Tezacaftor-Ivacaftor use in adults with cystic fibrosis and preserved lung function: insights from a European multicenter survey.

Changes to serum lipids, BMI and body composition in adults with cystic fibrosis on Elexacaftor/Tezacaftor/Ivacaftor (ETI): A scoping review.

Apical hyperosmotic challenge upregulates aquaporin-3 in human airway epithelia.

Rhinovirus Infection Promotes Suppression of Sphingosine and Enhanced Bacterial Infection in Cystic Fibrosis Airways.

The challenges of detecting neutrophil CFTR.

One Size May Not Fit All: A Case Series.

Antimicrobial Pharmacokinetic and Pharmacodynamic Considerations in Special Populations: A Call to Action.

Bowel preparation for colonoscopy in children: a survey of the Italian society of pediatric gastroenterology, hepatology and nutrition.

Safety of inhaled levofloxacin in people with cystic fibrosis: Data from UK and German Registries.

[Allergic bronchopulmonary aspergillosis in internal medicine].

Validity of Alfred Step Test Exercise Protocol (A-STEP) as a Surrogate VO2Max Cardiopulmonary Exercise Test (CPET) to Cycle Ergometry in Adults With Cystic Fibrosis.

Hyperammonemia syndrome due to Pluralibacter gergoviae bacteremia in an immunocompromised patient: case report.

Microbiological outcomes associated with Burkholderia species in people with cystic fibrosis receiving CFTR modulator therapy.

Documentation practices of cystic fibrosis (CF) pharmacists: An opportunity for discipline-wide quality improvement.

Intestinal Ultrasound Scan in Acute Severe Ulcerative Colitis in children: a multicenter prospective study on behalf of the Porto IBD Working Group of ESPGHAN.

Inhibition of MAPK p38α overcomes the cancer immunosurveillance defect caused by FPR1 loss-of-function mutation.

Harnessing metabolomics and proteomics in a clinical trial for pulmonary arterial hypertension: insights from post-hoc analysis of the REHAB-PH trial.

Effect of Elexacaftor/Tezacaftor/Ivacaftor Treatment on Extrapulmonary Complications of Cystic Fibrosis.

[Transition and transfer from pediatrics to adult medicine].

Bioengineered 3D hPSC-Cholangiocyte Ducts With Physiological Signals for Biliary Disease Modeling.

Global Collaboration in Cystic Fibrosis: Lessons From the COVID-19 Pandemic for Low- and Middle-Income Countries.

Interkingdom signaling elicited by bacterial extracellular vesicles in human cystic fibrosis airway epithelium and neutrophils.

Long-term impact of elexacaftor/tezacaftor/ivacaftor on small and large airways in people with cystic fibrosis aged ≥6 years: 24-month real-world evidence from the German Cystic Fibrosis Registry.

Clinical profile and in-hospital outcomes of patients hospitalised for bronchiectasis exacerbation.

Evaluation of ATP12A and NFKBIZ as potential markers of inflammatory status in cystic fibrosis airway epithelial cells.

Advancements in Sweat Testing Techniques for Cystic Fibrosis: From Classical to Novel Methods.

The Human Cost of Respiratory Care: Professional Quality of Life and Burnout across Multidisciplinary Cystic Fibrosis Teams.

Safety and efficacy of elexacaftor/tezacaftor/ivacaftor in adolescents and adults with cystic fibrosis and F508del-gating and F508del-residual function genotypes: Results from an open-label extension study.

N-acetylglucosamine utilization and impact on antibiotic susceptibility, oxidative stress tolerance, and swimming in Stenotrophomonas maltophilia.

Complete genome sequences of Pseudomonas aeruginosa clone C strains 8277, PT31M, and SG50M isolated from the urinary tract and anthropogenic water environments.

Renal Function Decline in Adults with Cystic Fibrosis Experiencing Pulmonary Exacerbations.

Beta cell function and insulin sensitivity during elexacaftor/tezacaftor/ivacaftor therapy in people with cystic fibrosis.

The natural human adaptive IgG-specific immune response is skewed towards non-protective tail domains of DNABII proteins.

Development and Validation of an Electronic Health Record Algorithm to Predict the Presence of Chronic Obstructive Pulmonary Disease.

Research Progress on the Mechanisms of High Mucus Secretion in the Airway: A Scoping Review.

Stopping an outbreak of Pseudomonas aeruginosa ST111 by temporarily blocking the siphon to disinfect it before the transition to the wastewater drain.

Capsaicinoids prevent intestinal fluid secretion and motility by inhibiting chloride channels.

Mucus and inflammation in the HEMT Era: Persistent barriers to complete airway normalization in cystic fibrosis.

Relationships between lung ultrasound, chest CT, and echocardiographic findings in children with bronchopulmonary dysplasia: A multimodal imaging study.

Current State of Clinical Care of People With Cystic Fibrosis.

Density fluctuations of Burkholderia and Achromobacter in cystic fibrosis sputum.

Fetal Transplacental Therapy to Mitigate Consequences of Cystic Fibrosis.

Determining the Minimal Clinically Important Difference of the 40-Item Smell Identification Test in People With Cystic Fibrosis.

Prevalence of Overweight and Obesity in the Era of CFTR Modulators in Patients with Cystic Fibrosis.

Early Life Nutrition: The First 1000 Days and Healthy Aging in Cystic Fibrosis.

A Diagnostic Dilemma: Concurrent Diagnosis of Cystic Fibrosis and Definitive Kabuki Syndrome Type 1.

Antenatal CFTR Modulators to Treat a Healthy Pregnant Woman with a Fetus Affected by Cystic Fibrosis Complicated by Meconium Ileus and Intestinal Volvulus: From a Suspicion of the Disease to a Targeted Treatment in Utero: Case Report and Narrative Review.

Cerebral Desaturation in Cystic Fibrosis Patients Undergoing Double Lung Transplantation.

Optimizing Reproductive Autonomy in Cystic Fibrosis: The Role of Oocyte Cryopreservation.

The Multidisciplinary Support To Access living donor Kidney Transplant (MuST AKT) intervention: A Pilot Randomized Controlled Trial.

Muscle Dysfunction and Bone Loss in a Woman With Cystic Fibrosis and Obesity Treated With Glucagon-Like Peptide 1 Agonist: A Case Report.

Brachial artery flow-mediated dilation is less repeatable in children with a chronic inflammatory disease compared to their healthy peers.

Effect of an airway clearance technique on nebulized drug delivery in patients with CF: A randomized cross-over trial.

Outcomes of SARS-CoV-2 infection post-solid organ transplantation in the cystic fibrosis population.

Association of proteins involved in fetal lung development with respiratory outcomes in infancy.

Evidence of sex-related differences in vascular health among people with cystic fibrosis.

Innovative methodologies for elucidating bushfire smoke-induced pathophysiological mechanism.

Draft genome sequences of 109 gut bacteria isolated from colonoscopy samples of individuals with and without cystic fibrosis.

Hypochloremic Hypokalemic Metabolic Alkalosis as a Manifestation of CFTR-Related Disorder.

Etiologies of chronic cough in children: a two-year experience from a tertiary pediatric pulmonology center.

[Evolution of thoracic computed tomography after therapy with elexacaftor, tezacaftor, and ivacaftor in patients with cystic fibrosis].

Improved Quality of Life in Children With Cystic Fibrosis Who Received Transmembrane Conductance Regulator Modulators.

CRISPR-Cas9 genome editing in the parental iPSC line PCIi033-A to introduce the homozygous mutation p.F508del (c.1521_1523del) in the CFTR gene.

The impact of progressive expansion of elexacaftor-tezacaftor-ivacaftor availability on lung transplant for cystic fibrosis in France.

Discussing the potential health impacts of carrying a single CF-causing CFTR mutation during consult with people with CF who are planning a pregnancy.

Year in review: "Best" papers in pediatric pulmonary and sleep medicine in 2025.

Evaluation of the effect of modulator therapies on medication complexity in adult cystic fibrosis patients.

Long-Term Adherence to Elexacaftor/Tezacaftor/Ivacaftor in People with Cystic Fibrosis.

The interplay between temperature and growth phase shapes the transcriptional landscape of Pseudomonas aeruginosa.

Mechanisms of thermoregulation in Pseudomonas aeruginosa.

Post-marketing safety profile of lumacaftor/ivacaftor in cystic fibrosis treatment: a pharmacovigilance analysis based on FAERS.

Decoding liver injury in cystic fibrosis: How to tell drug-induced liver injury from cystic fibrosis liver disease.

Untargeted Metabolomic and Lipidomic Profiling in Cystic Fibrosis Patients Using UPLC-QTOF-MS.

Genetic and clinical characteristics of pediatric patients with cystic fibrosis: a single-center retrospective study in China.

Adherence to guidelines, pitfalls, and emerging technologies in endoscopic practice for celiac disease: a nationwide SIGENP survey.

Single-cell RNAseq identifies persistent epithelial and immune dysfunction in PwCF by mitigating inter-individual sampling heterogeneity.

Integrating cognitive behavioral therapy into specialty care for adolescents with cystic fibrosis: a feasibility trial.

Organoids for Metabolic Disease Modeling.

CFTR Modulators in Brazil: Not for Everyone-A Comparison of Ineligibility Across Different Regions.

Advancing Mental Healthcare for Individuals With Cystic Fibrosis in Low- and Middle-Income Countries.

Loss of Potassium and Chloride Transport Changes PM-Induced Epithelial Dysfunction.

'The Hero's journey': Narratives on the transition to motherhood with cystic fibrosis.

A longitudinal evaluation of localised chronic Pseudomonas aeruginosa infection in cystic fibrosis rat models.

Multiple virulence attenuating strategies against Pseudomonas aeruginosa: Natural, synthetic, and synergistic approaches.

Transcriptional regulation of the pneumococcal capsule can dictate serotype-specific infection.

Gegen Qinlian decoction alleviates bacterial diarrhea via Lactobacillus amylovorus-modulated restoration of colonic water transport through the cAMP/CFTR/AQP3 pathway.

mSphere of Influence: Rethinking microbial identity through variability.

Glycoside hydrolases enhance antibiotic activity against Pseudomonas aeruginosa biofilms from cystic fibrosis airways.

Co-Design of a Novel Telehealth Exercise Model of Care for Adults With Cystic Fibrosis.

Contemporary outcomes of isolated liver and combined liver-lung transplantation for cystic fibrosis in children.

Burkholderia cepacia Bacteremia Complicated by Acute Parotid Abscess in a Poorly Controlled Diabetic Patient With Community-Acquired Pneumonia: A Case Report.

Disparities in Access to Cystic Fibrosis Therapy Across Countries.

KRAS-elicited PDIA6 blocks PERK-dependent immunogenic cell death in pancreatic carcinoma.

CFTR knock-out mice exhibit impaired renal compensation to dietary NaCl depletion.

Assessing Dietary Patterns and Composition Among Adults With Cystic Fibrosis Taking Highly Effective Modulator Therapy.

MLPA-Detected CFTR Exon Deletions in Children With Inconclusive CFTR Sequencing: A Single-Center Experience From Türkiye.

Integrating the Glycemia Risk Index Into Clinical Practice and Research: A Consensus Report.

Peripheral muscle oxygenation during upper extremity functional exercise and balance in pediatric patients with cystic fibrosis: a cross-sectional study.

Outcomes of Kidney Transplantation in Cystic Fibrosis.

CFTR modulators-induced acne: Case series and analysis of pharmacovigilance databases.

Qualitative analysis of genomic mutations and antibiotic susceptibility testing of Pseudomonas aeruginosa isolates from chronic lung infections.

Craniofacial development in children with cystic fibrosis.

Bacterial EVs contain small RNAs and transfer RNAs that regulate inflammation in lung infections.

Therapies for bronchiectasis: mechanisms and potential effects.

Urinary System Involvement in Children With Cystic Fibrosis: A Single-Center Retrospective Cohort.

Assessing the reversibility of bronchiectasis with deep learning - Authors' reply.

Assessing the reversibility of bronchiectasis with deep learning.

Identification of CD164 as an essential entry receptor for divergent adeno-associated viruses.

Pseudomonas aeruginosa gene expression changes during established biofilm infection in a cystic fibrosis lung model.

WTC 2025 Highlights: Infectious Disease.

Longitudinal observation of severe asthma comorbidities and oral corticosteroids use from SANI and ISAR registries.

Sex Differences in Muscle-Respiratory Function Relationship in Lung Transplant Patients: A Longitudinal Study.

Outcomes of beta-blocker use in people living with chronic obstructive pulmonary disease and a co-existent beta-blocker indicated cardiovascular disease. Insights from a global federated network.

Predicting pulmonary exacerbations in cystic fibrosis subpopulations and implications for clinical trial design.

Cystic fibrosis year in review 2025.

Neutralization of acyl-CoA-binding protein attenuates glucocorticoid-mediated suppression of cancer immunosurveillance.

Functional analysis of purM in Burkholderia cenocepacia using a trimethoprim-selectable allelic exchange and mini-Tn7 complementation approach.

Epithelial plasma membrane transporters as drug targets.

When Recurrent Pancreatitis Is Not Pancreatitis: Cyclic Vomiting Syndrome Masquerading as Acute Pancreatitis in a Young Adult.

ERS Congress 2025: highlights from the Respiratory Infections Assembly.

CFTR activity in nasal potential difference of adults with idiopathic bronchiectasis.

Impact of Elexacaftor-Tezacaftor-Ivacaftor on fungal colonisation in children and adolescents with cystic fibrosis.

Clinical and epidemiological characteristics of nontuberculous mycobacteria pulmonary infections in the healthcare area of Virgen del Rocío University Hospital in Seville (2020-2023).

Ultraprocessed Food Consumption and Behavioral Outcomes in Canadian Children.

Implementing Genomic Medicine in Primary Care: A Convergent Mixed Method Case Study.

Aquagenic Wrinkling of the Palms as a Screening Indicator for Cystic Fibrosis Beyond Infancy.

A Narrative Review of Gene-Environment Interactions in Pediatric Pulmonology.

Harm reduction in paediatric off-label therapy: ethical analysis of early CFTR modulator use in an infant with cystic fibrosis.

Lipopolysaccharide-targeting treatments for multidrug-resistant Pseudomonas aeruginosa.

Towards functional precision medicine? Evidence standards of organoids as patient-specific models.

Phage isolation and functional characterization reveal strong antibiofilm activity against Pseudomonas aeruginosa in a cystic fibrosis sputum model.

Pseudomonas aeruginosa Biofilms in Cystic Fibrosis: Interactions, Methods, and Therapeutic Strategies.

Feasibility of electrical impedance tomography-guided PEP in children with CF and TBM.

Unraveling the Complexities of Kartagener's Syndrome: A Case of Bronchiectasis, Isolated Dextrocardia, and Primary Ciliary Dyskinesia in an Adult With Chronic Respiratory Symptoms.

[MUC1 and SIGIRR as Negative Regulators of TLR Signaling: Expression, Function, and Anti-inflammatory Augmentation].

Prolactin signaling in the highly osmotolerant Mozambique tilapia, Oreochromis mossambicus.

Opportunistic thoracic CT scan over bone densitometry in CF care: Is it possible to screen for osteoporosis using a CT scan?

Effect of vanzacaftor/tezacaftor/ivacaftor on cystic fibrosis nasal epithelial cells and intestinal organoids compared to elexacaftor/tezacaftor/ivacaftor.

Beyond readthrough: ataluren restores mitochondrial function and reduces oxidative stress in FANCA-mutated cells via mTOR-DRP1 modulation.

[Hearing impairment in children with cystic fibrosis].

In Utero CFTR Modulator Therapy in Fetuses With Cystic Fibrosis.

L-ascorbic acid exerts anti-microbial and anti-virulence effects against multi-drug resistant Burkholderia cepacia complex.

Genetic strategies for negative or variant of uncertain significance findings in exome sequencing in hereditary bronchiectasis: a case series.

Large variations in total and allele-specific transcript expression in a disease mutation-independent manner.

Author Correction: Phage therapy with nebulized cocktail BX004-A for chronic Pseudomonas aeruginosa infections in cystic fibrosis: a randomized first-in-human trial.

The effectiveness and value of brensocatib for the treatment of non-cystic fibrosis bronchiectasis.

Successful Management of Chronic Achromobacter xylosoxidans Bronchial Infection With Nebulized Levofloxacin in a Patient With Non-cystic Fibrosis Bronchiectasis.

Different States of Lung Allograft Injury Assessed by Plasma Donor-Derived and Total Cell-Free DNA.

Does it matter how cystic fibrosis transmembrane conductance regulator modulators reduce inflammation in cystic fibrosis?

A state of the union on alpha-1 antitrypsin deficiency at the Veterans Health Administration.

Activation of farnesoid X receptor inhibits TMEM16A-mediated chloride secretion in renal collecting duct cells and retards renal cyst progression.

Deciphering microbial biofilm: mechanism, infection, and advanced approaches for control.

Uncovering Cystic Fibrosis Carrier: Insights From a Heterozygous CFTR-F508del Rabbit Model.

The regional landscape of the human colon culturome in health and cystic fibrosis.

Streptococcus sanguinis antagonizes Prevotella melaninogenica in the context of the cystic fibrosis respiratory microbiome.

Normal Values for Respiratory Oscillometry in Pediatrics: An Argument for a Local Control Population.

Parental Experiences and Coping Strategies of Families Caring for a Child With Cystic Fibrosis.

Challenges and Practical Solutions in the Management of Cystic Fibrosis in Resource-Limited Countries: The Indian Experience.

The archaic CUP pilus SMF-1 utilizes a specific antiparallel bundling mechanism to initiate biofilm formation.

Lung retransplantation after initial single lung transplantation.

"No Words for Feelings": Alexithymia in Children With Cystic Fibrosis and Their Caregivers.

The Relationship Between Peripheral Eosinophilia, Lower Respiratory Tract Pathogens, Age at First Pneumonia, and Malnutrition in Children with Non-cystic Fibrosis Bronchiectasis.

Inhaled Antibiotic and Biologic Formulations Targeting Pseudomonas aeruginosa.

Recent Advances in Inhalation Therapy: An Overview.

Biofilm Formation in Aspergillus fumigatus: A Comparative Study of Strains from Different Origins.

From Promise to Practice: Harmonizing Telemedicine in Pediatric Chronic Respiratory Diseases.

Cystic Fibrosis: A Disease with a New Face.

The Prognostic Significance of Bronchoalveolar Lavage Cellular Analysis in Evaluating Disease Burden in Non-Cystic Fibrosis Bronchiectasis.

Restoration of Defective CFTR in Human Nasal Respiratory Epithelial Cells by CFTR Modulators and mRNA Transfection.

Special Issue "Inflammatory Airway Diseases: Diagnosis, Pathology, Molecular Mechanisms and Treatment Options".

Phage-Based Approaches to Chronic Pseudomonas aeruginosa Lung Infection in Cystic Fibrosis.

Simulation-Driven Annotation-Free Deep Learning for Automated Detection and Segmentation of Airway Mucus Plugs on Non-Contrast CT Images.

Drugs Associated with Pediatric Cataracts: A Real-World Pharmacovigilance Study.

Cystic fibrosis-related diabetes is associated with reduced airway microbial diversity.

Kidney care at NICU discharge and follow-up recommendations for preterm infants<34 weeks.

Alterations of bile acid composition in children with cystic fibrosis compared to healthy controls.

Novel translational pulmonary MRI in pediatrics: A Review of the last 10 years.

Pathology of the Human Temporal Bone in a Rare Case of Combined Usher Syndrome and Cystic Fibrosis.

Role of Iron Availability in Modulating Pseudomonas aeruginosa's Antifungal Effects on Planktonic and Biofilm Growth of Scedosporium/Lomentospora Under Cystic Fibrosis-Mimicking Conditions.

Metabolic Syndrome Predisposes Ossabaw Minipig Retina to an Early Neurodegenerative Milieu.

Beyond BMI: Nutritional Recovery and Functional Implications of CFTR Modulators in Cystic Fibrosis.

Towards accurate artificial intelligence models for strain-level phage-host prediction.