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Neurocitoma central
ORPHA:73256CID-10 · D33.0CID-11 · 2A00.3DOENÇA RARA

Neurocitoma central é um tipo muito raro de tumor cerebral que afeta principalmente jovens adultos (com pouco mais de 100 casos registrados em todo o mundo). Ele costuma aparecer nos ventrículos laterais do cérebro e, às vezes, no terceiro ventrículo. Os sintomas são causados pelo aumento da pressão dentro da cabeça: dor de cabeça, náuseas (enjoos) e vômitos, sonolência, problemas de visão e alterações mentais. A remoção completa do tumor é o tratamento mais indicado. O prognóstico após a cirurgia geralmente é bom.

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Introdução

O que você precisa saber de cara

📋

Neurocitoma central é um tipo muito raro de tumor cerebral que afeta principalmente jovens adultos (com pouco mais de 100 casos registrados em todo o mundo). Ele costuma aparecer nos ventrículos laterais do cérebro e, às vezes, no terceiro ventrículo. Os sintomas são causados pelo aumento da pressão dentro da cabeça: dor de cabeça, náuseas (enjoos) e vômitos, sonolência, problemas de visão e alterações mentais. A remoção completa do tumor é o tratamento mais indicado. O prognóstico após a cirurgia geralmente é bom.

Pesquisas ativas
1 ensaio
3 total registrados no ClinicalTrials.gov
Publicações científicas
530 artigos
Último publicado: 2026

Escala de raridade

CLASSIFICAÇÃO ORPHANET · BRASIL 2024
Unknown
Ultra-rara
<1/50k
Muito rara
1/20k
Rara
1/10k
Pouco freq.
1/5k
Incomum
1/2k
Prevalência
0.0
Worldwide
Casos conhecidos
500
pacientes catalogados
Início
Adolescent
+ adult, childhood
🏥
SUS: Sem cobertura SUSScore: 0%
CID-10: D33.0
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Entender a doença

Do básico ao detalhe, leia no seu ritmo

Preparando trilha educativa...

Sinais e sintomas

O que aparece no corpo e com que frequência cada sintoma acontece

Partes do corpo afetadas

🧠
Neurológico
4 sintomas
👂
Ouvidos
1 sintomas
👁️
Olhos
1 sintomas
🫃
Digestivo
1 sintomas

+ 12 sintomas em outras categorias

Características mais comuns

100%prev.
Hidrocefalia
90%prev.
Lesão cística intracraniana
Muito frequente (99-80%)
90%prev.
Fenótipo celular anormal
Muito frequente (99-80%)
90%prev.
Anormalidade do ventrículo lateral
Muito frequente (99-80%)
55%prev.
Cefaleia
Frequente (79-30%)
55%prev.
Anormalidade da visão
Frequente (79-30%)
19sintomas
Muito frequente (4)
Frequente (8)
Ocasional (7)

Os sintomas variam de pessoa para pessoa. Abaixo estão as 19 características clínicas mais associadas, ordenadas por frequência.

HidrocefaliaHydrocephalus
Muito frequente100%
Lesão cística intracranianaIntracranial cystic lesion
Muito frequente (99-80%)90%
Fenótipo celular anormalAbnormal cellular phenotype
Muito frequente (99-80%)90%
Anormalidade do ventrículo lateralAbnormality of lateral ventricle
Muito frequente (99-80%)90%
CefaleiaHeadache
Frequente (79-30%)55%

Linha do tempo da pesquisa

Publicações por ano — veja quando o interesse científico cresceu
Anos de pesquisa1desde 2026
Total histórico530PubMed
Últimos 10 anos182publicações
Pico202022 papers
Linha do tempo
2026Hoje · 2026🧪 1996Primeiro ensaio clínico📈 2020Ano de pico
Publicações por ano (últimos 10 anos)

Encontrou um erro ou informação desatualizada? Sugira uma correção →

Genética e causas

O que está alterado no DNA e como passa nas famílias

🧬

Nenhum gene associado encontrado

Os dados genéticos desta condição ainda estão sendo catalogados.

Diagnóstico

Os sinais que médicos procuram e os exames que confirmam

Carregando...

Tratamento e manejo

Remédios, cuidados de apoio e o que precisa acompanhar

Pipeline de tratamentos
Pipeline regulatório — de medicamentos já aprovados a drogas em pesquisa exploratória.
Aprovado1
2Fase 21
Medicamentos catalogadosEnsaios clínicos· 0 medicamentos · 2 ensaios
Carregando informações de tratamento...

Onde tratar no SUS

Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

🇧🇷 Atendimento SUS — Neurocitoma central

🗺️

Selecione um estado ou use sua localização para ver resultados.

Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.

Pesquisa ativa

Ensaios clínicos abertos e novidades científicas recentes

Pesquisa e ensaios clínicos

3 ensaios clínicos encontrados, 1 ativos.

Distribuição por fase
Ver todos no ClinicalTrials.gov
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Publicações mais relevantes

Timeline de publicações
184 papers (10 anos)
#1

Epidemiology and Long-Term Treatment Outcome of Central Neurocytoma: A Retrospective National Study from Saudi Arabia.

World neurosurgery2026 Feb

To describe the clinical features, management, and long-term outcomes of central neurocytoma (CNC). A retrospective cohort included all histopathologically confirmed CNC cases treated at 11 tertiary centers in Saudi Arabia from 1996 to 2021. Overall survival (OS) and progression-free survival (PFS) were estimated with Kaplan-Meier and compared with the log-rank test. Postoperative radiation was modeled as a time-dependent exposure to address immortal time bias. Functional outcomes were assessed with the modified Rankin Scale. A total of 104 patients were identified (mean age 26.9 years, 51.9% male), corresponding to an annual incidence of 14.4 cases per 100 million persons. Most tumors were intraventricular (92.2%). Gross total resection was achieved in 41.3%, subtotal resection in 55.8%, and biopsy only in 2.9%. Postoperative radiation was performed in 40% of cases, with a median interval of 98 days after surgery. The 5-year and 10-year OS were 91.7% and 88.9%, respectively, and PFS were 80.1% and 69.4%, respectively. Neither extent of resection nor postoperative radiation was significantly associated with OS or PFS. Tumors larger than 36.3 cm3 were associated with poorer OS (P = 0.018) and functional outcomes (P = 0.002). At last follow-up, 81.7% of patients maintained functional independence (modified Rankin Scale ≤ 2). CNC offers favorable long-term survival and functional outcomes. Maximal safe resection remains the mainstay of treatment, while the benefit of postoperative radiation appears limited. Tumor size remains a key determinant of outcome.

#2

Diffuse midline glioma, H3K27-altered, mimicking central neurocytoma on MRI: A case report.

Radiology case reports2026 Jan

Diffuse midline glioma (DMG), H3K27-altered, is an aggressive central nervous system tumor that usually arises in midline structures such as the pons, thalamus, or spinal cord. We present a rare case of intraventricular DMG, H3K27-altered in a 35-year-old woman. MRI showed a soap-bubble appearance, initially suggestive of central neurocytoma, but histopathological and immunohistochemical analyses confirmed the final diagnosis of DMG, H3K27-altered. This is the first reported intraventricular DMG, H3K27-altered with a soap-bubble appearance, underscoring the importance of including this tumor in the differential diagnosis of intraventricular masses.

#3

Improved tumor control with adjuvant radiotherapy in patients with central neurocytoma: a multicenter study.

Journal of neuro-oncology2026 Mar 23
#4

Transfrontal Endoscopic Endoport Approach for Gross Total Resection of a Panventricular Central Neurocytoma: 2-Dimensional Operative Video.

Operative neurosurgery (Hagerstown, Md.)2026 Feb 01
#5

Central Neurocytoma in the Fourth Ventricle: A Case Report and Review of Cases With This Unusual Presentation Site.

Cureus2025 Nov

Central neurocytoma (CN) is classified as a grade 2 neuronal tumor and is mostly located in the lateral ventricles. In this report, we present the case of a 40-year-old female patient who was admitted due to vertigo and a holocranial headache. Magnetic resonance imaging (MRI) revealed a lesion in the fourth ventricle that appeared heterogeneous and hyperintense. In the T2/fluid attenuated inversion recovery (FLAIR) sequence, numerous cystic areas were observed. Light microscopic examination showed a neoplasm with a neuronal phenotype; areas with neoplastic cells exhibiting a ganglionic appearance were noted, along with immunohistochemical expression of neuronal markers. Currently, the patient is showing clinical improvement.

Publicações recentes

Ver todas no PubMed

📚 EuropePMC349 artigos no totalmostrando 176

2026

Improved tumor control with adjuvant radiotherapy in patients with central neurocytoma: a multicenter study.

Journal of neuro-oncology
2026

Epidemiology and Long-Term Treatment Outcome of Central Neurocytoma: A Retrospective National Study from Saudi Arabia.

World neurosurgery
2025

Central Neurocytoma in the Fourth Ventricle: A Case Report and Review of Cases With This Unusual Presentation Site.

Cureus
2026

Diffuse midline glioma, H3K27-altered, mimicking central neurocytoma on MRI: A case report.

Radiology case reports
2025

Long-Term Quality of Life and Functional Outcome Analysis of Surgically Managed Central Neurocytoma Patients: Results of a Multicenter Study.

Neurosurgery
2025

The clinical spectrum of central neurocytomas ranges from benign to leptomeningeal disseminating disease: a single institutional surgical series of 33 patients.

Frontiers in surgery
2025

Treatment of Central Neurocytoma.

Cancers
2025

Imaging characteristics of central neurocytomas according to Ki-67 proliferation index.

Frontiers in oncology
2025

Outcome-associated factors in a molecularly defined cohort of central neurocytoma.

Acta neuropathologica
2025

Lateral ventricle central neurocytoma with lipidization: a case report of an underrecognized presentation.

Arquivos de neuro-psiquiatria
2025

Chordoid glioma of right lateral ventricle in young male: a case report.

Annals of medicine and surgery (2012)
2026

Transfrontal Endoscopic Endoport Approach for Gross Total Resection of a Panventricular Central Neurocytoma: 2-Dimensional Operative Video.

Operative neurosurgery (Hagerstown, Md.)
2025

The Possible Role of Wnt/β-Catenin Pathway in Central Neurocytoma.

World neurosurgery
2025

A Young Adult With Persistent Headache: A Case of Central Neurocytoma.

Cureus
2025

Utility of Surgical Simulation for Tubular Retractor Surgery Using Three-Dimensional Printed Intraventricular Tumor Models: Case Series.

World neurosurgery
2024

Central Neurocytoma in a Teenager, a Rare Cause of Hemiplegia, and a Diagnostic Dilemma in a Resource-Poor Setting.

Case reports in pathology
2024

Intraoperative Cytologic Diagnosis of Central Neurocytoma Mimicking as Oligodendroglioma.

Indian journal of surgical oncology
2024

Shunt, endoscopic, and microsurgical management of trapped temporal horn following resection of lateral ventricle trigonal or peritrigonal tumors: A retrospective multicenter study.

European journal of surgical oncology : the journal of the European Society of Surgical Oncology and the British Association of Surgical Oncology
2024

Central Neurocytoma Diagnosis on Squash Cytology.

Journal of cytology
2024

A Patient Diagnosed With Rare Central Neurocytoma: A Case Report.

Neurology India
2024

How I do it? Resection of left ventricular central neurocytoma via trans-sulcal approach.

Acta neurochirurgica
2024

Radiotherapy for central neurocytoma: A multicentric retrospective study in France.

Cancer radiotherapie : journal de la Societe francaise de radiotherapie oncologique
2024

Freiburg Neuropathology Case Conference : Mild Disorientation and Mild Anomic Aphasia in a 79-Year-Old Female.

Clinical neuroradiology
2024

Molecular and clinical characterization of atypical central neurocytomas: implications for diagnosis and treatment strategies.

Discover oncology
2024

Revealing subependymal giant cell astrocytoma with multimodal positron emission tomography: illustrative cases.

Journal of neurosurgery. Case lessons
2024

Central Neurocytoma: A Case Report With Literature Review.

Cureus
2024

Navigating the Diagnostic and Therapeutic Challenges of Central Neurocytoma: A Case Report.

Cureus
2024

Clinical effects of neuroendoscopic infratentorial supracerebellar approach surgical technique for resecting pineal tumors: a retrospective study.

Neuro-Chirurgie
2024

Long-term outcomes of central neurocytoma - an institutional experience.

Journal of neuro-oncology
2024

Central Neurocytoma Treated Using Supratentorial Ventricle Radiotherapy: A Single-Institution Analysis of Five Cases in Adjuvant or Salvage Settings After Surgery.

Cureus
2024

Central neurocytoma exhibits radial glial cell signatures with FGFR3 hypomethylation and overexpression.

Experimental &amp; molecular medicine
2024

Adult Central Neurocytomas: Clinical Features and Long-Term Treatment Outcomes in Different Age Groups.

World neurosurgery
2024

Gamma Knife radiosurgery for central neurocytoma: a quantitative systematic review and metanalysis.

Neurosurgical review
2023

Analysis of a pituitary tumour with histological features of central neurocytoma points towards the emergence of a new entity recognizable by a specific epigenetic signature.

Neuropathology and applied neurobiology
2023

Intraventricular central neurocytoma molecularly defined as extraventricular neurocytoma: a case representing the discrepancy between clinicopathological and molecular classifications.

Brain tumor pathology
2023

Central Neurocytoma with Extensive Intratumoral Hemorrhage: A Case Report.

The American journal of case reports
2023

Pediatric atypical extraventricular neurocytoma: Clinical features and survival outcomes.

Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery
2023

Simplified anterior transpetrosal approach without superior petrosal sinus and tentorial incision for lesions centered in Meckel's cave.

Acta neurochirurgica
2023

Epigenetic Alteration of H3K27me3 as a Possible Oncogenic Mechanism of Central Neurocytoma.

Laboratory investigation; a journal of technical methods and pathology
2023

Primary papillary epithelial tumor of the sella and posterior pituitary tumor show similar (epi)genetic features and constitute a single neuro-oncological entity.

Neuro-oncology
2023

Central neurocytoma-positive and differential diagnosis: An example through a case report.

SAGE open medical case reports
2023

Episodic Headache, Periorbital Pain, and Multifocal Paresthesias as Presenting Symptoms of Central Neurocytoma: A Case Report.

Cureus
2023

Central neurocytomas: research trends, most cited papers, and scientometrics analysis to date.

Neurosurgical review
2022

Clinical prognostic factors for central neurocytoma and subgroup analysis of different treatment measures: A SEER database-based retrospective analysis from 2003 to 2019.

Frontiers in oncology
2023

Machine learning-based multiparametric magnetic resonance imaging radiomics model for distinguishing central neurocytoma from glioma of lateral ventricle.

European radiology
2022

The role of single fraction Gamma Knife radiosurgery for intraventricular central neurocytomas and the utility of F-18 fluroethyltyrosine: two case reports.

Journal of medical case reports
2022

Clinical application of 3D Slicer combined with Sina/MosoCam multimodal system in preoperative planning of brain lesions surgery.

Scientific reports
2022

Comparison of surgery with or without adjuvant radiotherapy in treating central neurocytoma: a single-center retrospective real-world study.

Journal of neuro-oncology
2022

Malignant transformation of central neurocytoma with dissemination 17 years after initial treatment: illustrative case.

Journal of neurosurgery. Case lessons
2023

Central neurocytomas in children: Clinicopathologic features and long-term surgical outcomes.

Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery
2022

Diffuse GFAP Immunopositivity in the Oligodendrocyte-like Component of Pilocytic Astrocytoma Distinguishes It from Mimickers.

Diagnostics (Basel, Switzerland)
2022

A 22-Year Course of a Case with Central Neurocytoma.

Neurology India
2022

Clinical Outcomes and Prognostic Analysis of 101 Patients of Central Neurocytoma: A 10-Year Treatment Experience at a Single Institution.

Frontiers in oncology
2022

A Clinicopathological and Molecular Analysis of Sellar/Suprasellar Neurocytoma Mimicking Pituitary Adenoma.

Frontiers in endocrinology
2022

Uncommon Glioneuronal Tumors: A Radiologic and Pathologic Synopsis.

AJNR. American journal of neuroradiology
2022

Extraventricular neurocytoma at the sellar region: Report of 8 cases and literature review.

Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia
2022

Central Neurocytoma with Hemorrhagic Presentation Case Report and Review of the Literature.

Case reports in surgery
2022

The Diagnostic Value of Pan-Trk Expression to Detect Neurotrophic Tyrosine Receptor Kinase (NTRK) Gene Fusion in CNS Tumours: A Study Using Next-Generation Sequencing Platform.

Pathology oncology research : POR
2022

Extraventricular Neurocytoma: Clinical Investigation of Heterogenous Prognosis.

Brain tumor research and treatment
2021

Corpus Callosum Swelling after Resection of Intraventricular Central Neurocytoma.

NMC case report journal
2021

Clinical Outcome After Microsurgical Resection of Central Neurocytoma: A Single-Centre Analysis of 15 Years.

Frontiers in neurology
2021

MRI features of an atypical case of extraventricular neurocytoma: A case report.

Medicine
2021

Refined Temporal-to-Frontal Horn Shunt for Treatment of Trapped Temporal Horn After Surgery of Peri- or Intraventricular Tumor: A Case Series Study.

Frontiers in oncology
2022

TTF-1: A Well-Favored Addition to the Immunohistochemistry Armamentarium as a Diagnostic Marker of SEGA.

World neurosurgery
2022

Primary intraventricular tumors - Imaging characteristics, post-treatment changes and relapses.

Clinical imaging
2021

A Rare Case of Isolated Intraventricular Primary Central Nervous System Lymphoma in an 85-Year-Old Man.

Asian journal of neurosurgery
2021

Immunohistochemical expression of Olig2, CD99, and EMA to differentiate oligodendroglial-like neoplasms.

Folia neuropathologica
2021

Organic bipolar disorder secondary to central neurocytoma resection: a case report.

Actas espanolas de psiquiatria
2021

Impact of Adjuvant Radiotherapy in Patients with Central Neurocytoma: A Multicentric International Analysis.

Cancers
2021

The last decade's experience of management of central neurocytomas: Treatment strategies and new options.

Surgical neurology international
2021

Large lateral intraventricular tumors - Outcome of radical surgery.

Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia
2021

Tumor Spheroids of an Aggressive Form of Central Neurocytoma Have Transit-Amplifying Progenitor Characteristics with Enhanced EGFR and Tumor Stem Cell Signaling.

Experimental neurobiology
2021

[Central neurocytomas: long-term treatment outcomes].

Zhurnal voprosy neirokhirurgii imeni N. N. Burdenko
2021

A rare diagnosis of an extraventricular neurocytoma.

Surgical neurology international
2021

Lateral ventricular liponeurocytoma: Review of literature and case illustration.

Neuro-Chirurgie
2021

Gamma Knife radiosurgery for the treatment of central neurocytoma: a single-institution experience of 25 patients.

Neurosurgical review
2021

Clinico-radiological characteristics, histo-pathological features and long-term survival outcomes in central neurocytoma: A single-institutional audit.

Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia
2021

Differential Diagnosis of Central Neurocytoma: Two Cases.

Journal of neurological surgery. Part A, Central European neurosurgery
2021

Transcortical Approach to Deep-Seated Intraventricular and Intra-axial Tumors Using a Tubular Retractor System: A Technical Note and Review of the Literature.

Journal of neurological surgery. Part A, Central European neurosurgery
2020

Intraventricular neuroepithelial tumors: surgical outcome, technical considerations and review of literature.

BMC cancer
2021

Atypical Central Neurocytoma: An Investigation of Prognostic Factors.

World neurosurgery
2020

Antibiotic-induced black hairy tongue: two case reports and a review of the literature.

The Journal of international medical research
2020

Long-term follow-up of lateral ventricular central neurocytoma treated with subtotal resection followed by concurrent chemoradiotherapy and add on chemotherapy - Case report from a Tertiary Kenyan Cancer Hospital.

Surgical neurology international
2020

Individual Treatment Decisions for Central Neurocytoma.

Frontiers in neurology
2021

The importance of staged surgery for giant atypical central neurocytoma.

Acta neurologica Belgica
2020

[Choice optimisation of radiation therapy technique for central neurocytomas from literature data].

Cancer radiotherapie : journal de la Societe francaise de radiotherapie oncologique
2020

Delving Inside the Enigmatic Central Neurocytoma: Electronic Hospital Database Retrieval.

Acta informatica medica : AIM : journal of the Society for Medical Informatics of Bosnia &amp; Herzegovina : casopis Drustva za medicinsku informatiku BiH
2020

Cerebellar Neurocytoma with Excellent Response to Radiotherapy.

World neurosurgery
2020

[Unilateral Transcranial Endoscopic Surgical Removal for Large Intraventricular Tumor Assisted by Contralateral Neuroendoscope].

No shinkei geka. Neurological surgery
2020

Atypical central neurocytoma with aggressive features in a child.

BMJ case reports
2020

Neuroimaging diagnosis of intraventricular Central neurocytoma.

Neuroscience letters
2020

Central neurocytoma originating in third ventricle with expansion into the cerebral aqueduct and fourth ventricle: Case report and review of literature.

Neuro-Chirurgie
2020

Atypical central neurocytoma with leptomeningeal dissemination: a case report.

Journal of the Egyptian National Cancer Institute
2020

Endoscopic Intraventricular Atrial Adhesiolysis for the Treatment of Entrapped Temporal Horn after İntraventricular Tumor Surgery.

Journal of neurosciences in rural practice
2021

Stereotactic radiosurgery for central neurocytomas: an international multicenter retrospective cohort study.

Journal of neurosurgery
2020

[The role of SMARCE1 in the diagnosis of clear cell meningioma].

Zhonghua bing li xue za zhi = Chinese journal of pathology
2020

Unique Case of Atypical Central Neurocytoma with Craniospinal Metastases and Pituitary Adenoma.

Asian journal of neurosurgery
2020

Endoscopic approach and stereotactic radiosurgery for a posterior third ventricular Central Neurocytoma - case report and literature review.

International journal of surgery case reports
2020

Freiburg Neuropathology Case Conference : Intraventricular Mass Lesion in a Child.

Clinical neuroradiology
2019

[Central neurocytomas: surgical treatment outcomes and new trends and approaches in the treatment].

Zhurnal voprosy neirokhirurgii imeni N. N. Burdenko
2020

Central Neurocytoma Treatment Modalities: A Systematic Review Assessing the Outcomes of Combined Maximal Safe Resection and Radiotherapy with Gross Total Resection.

World neurosurgery
2020

Progeny in an Inhospitable Milieu-Solitary Intraventricular Metastasis From a Triple-Negative Breast Cancer Mimicking Central Neurocytoma: Case Report and Review of Diagnostic Pitfalls and Management Strategies.

World neurosurgery
2020

Application of diffusion-weighted imaging combined with apparent diffusion coefficient in differential diagnosis between central neurocytoma and ependymoma.

Neuroradiology
2019

Successful Treatment of Serious Meningitis Caused by Extremely Carbapenem-Resistant Enterobacter cloacae (MIC≥16mg/L) with i.v. Meropenem and i.v. Amikacin Plus Intraventricular Amikacin.

Infection and drug resistance
2019

The role of chemotherapy in the treatment of central neurocytoma.

CNS oncology
2019

Far-anterior Interhemispheric Transcallosal Approach for a Central Neurocytoma in the Lateral Ventricle.

Neurologia medico-chirurgica
2019

Extraventricular neurocytoma with ganglioid differentiation of the sellar and parasellar regions in an elderly patient: A case report.

Surgical neurology international
2019

Central neurocytoma in the posterior fossa.

BMJ case reports
2019

Central Neurocytoma Presenting with Bleed and Obstructive Hydrocephalus: A Rare Presentation.

Asian journal of neurosurgery
2019

Histogram Analysis Parameters ADC for Distinguishing Ventricular Neoplasms of Ependymoma, Choroid Plexus Papilloma, and Central Neurocytoma.

Medical science monitor : international medical journal of experimental and clinical research
2019

Uncal Herniation Due to External Hydrocephalus Post Intraventricular Surgery.

The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiques
2019

Radiosurgery for Central Neurocytoma.

Progress in neurological surgery
2019

Successful Central Neurocytoma Management: A Rare Brain Tumor.

Journal of the College of Physicians and Surgeons--Pakistan : JCPSP
2019

Central neurocytoma: SNP array analyses, subtel FISH, and review of the literature.

Pathology, research and practice
2019

Bifocal germinoma of the septum pellucidum and the sellar-supra-sellar region: An uncommon presentation for a rare tumor.

eNeurologicalSci
2019

The epidemiology of central and extraventricular neurocytoma in the United States between 2006 and 2014.

Journal of neuro-oncology
2019

Atypical central neurocytoma with novel EWSR1-ATF1 fusion and MUTYH mutation detected by next-generation sequencing.

BMJ case reports
2019

Central Neurocytoma: Rare Presentation in Fourth Ventricle and Review of Literature.

World neurosurgery
2018

Tumor control of third ventricular central neurocytoma after gamma knife radiosurgery in an elderly patient: A case report and literature review.

Medicine
2018

Combination of the tubular retractor and brain spatulas provides an adequate operative field in surgery for deep-seated lesions: Case series and technical note.

Surgical neurology international
2019

Tetraventricular Atypical Central Neurocytoma.

World neurosurgery
2018

Paranoid Syndrome as the First Sign of Central Neurocytoma: A Case Report.

Journal of psychiatric practice
2018

Central Neurocytoma - A Rare Brain Tumor.

The Journal of the Association of Physicians of India
2018

Prognosis and treatment outcomes of central neurocytomas: clinical interrogation based on a single center experience.

Journal of neuro-oncology
2018

MRI of intracranial intraventricular lesions.

Clinical imaging
2018

Stereotactic radiosurgery for hypervascular intracranial tumors.

Journal of neuro-oncology
2018

Oridonin inhibits growth and induces apoptosis of human neurocytoma cells via the Wnt/β-catenin pathway.

Oncology letters
2018

Relative survival of patients with central neurocytoma.

Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia
2018

Novel case of recurrent intraventricular atypical central neurocytoma with prominent gangliogliomatous differentiation in a 10-year-old boy with 10 years of follow up.

Neuropathology : official journal of the Japanese Society of Neuropathology
2019

Purely neuroendoscopic resection of intraventricular tumors with an endoscopic ultrasonic aspirator.

Neurosurgical review
2018

FGFR1:TACC1 fusion is a frequent event in molecularly defined extraventricular neurocytoma.

Acta neuropathologica
2018

Central neurocytoma represents a tumor consisting of diverse neuronal phenotypes.

Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia
2018

Diagnostic value of six MRI features for central neurocytoma.

European radiology
2018

The role of proton beam therapy in central neurocytoma: A single-institution experience.

Practical radiation oncology
2018

Central neurocytoma: Clinical characteristics, patterns of care, and survival.

Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia
2018

Intramedullary central neurocytoma of the thoracic spinal cord: A case report and literature review.

Molecular and clinical oncology
2018

Spontaneous intracerebral hemorrhage as presentation of atypical central neurocytoma: the role of angiogenesis through the characterization of tumor endothelial cells.

Histology and histopathology
2017

The painter from Sinaloa: artistic analysis of a case of spatial agnosia and neglect of visual shapes.

Neurocase
2017

[Central neurocytomas: clinical and radiopathological correlations: about 12 cases].

The Pan African medical journal
2018

Clinical Features, Treatment, and Long-term Outcomes of Central Neurocytoma: A 20-Year Experience at a Single Center.

World neurosurgery
2017

Clinical, radiological, pathological and prognostic aspects of intraventricular oligodendroglioma: comparison with central neurocytoma.

Journal of neuro-oncology
2017

Perfusion MR imaging of enhancing brain tumors: Comparison of arterial spin labeling technique with dynamic susceptibility contrast technique.

Neurology India
2017

Teaching NeuroImages: Central neurocytoma.

Neurology
2017

Systematic Analysis of Clinical Outcomes Following Stereotactic Radiosurgery for Central Neurocytoma.

Brain tumor research and treatment
2017

Intracranial intraventricular tumors: long-term surgical outcome of 25 patients.

Turkish journal of medical sciences
2016

Pediatric central neurocytoma: Case report and review of literature.

Journal of pediatric neurosciences
2017

Ventricular Central Neurocytoma: Rate of Shunting and Outcome 2 Years After Total and Subtotal Excision.

Acta neurochirurgica. Supplement
2016

Magnetic Resonance Imaging of a Case of Central Neurocytoma.

Acta informatica medica : AIM : journal of the Society for Medical Informatics of Bosnia &amp; Herzegovina : casopis Drustva za medicinsku informatiku BiH
2017

MR Spectroscopy to Distinguish between Supratentorial Intraventricular Subependymoma and Central Neurocytoma.

Magnetic resonance in medical sciences : MRMS : an official journal of Japan Society of Magnetic Resonance in Medicine
2016

Central Neurocytoma: A Review of Clinical Management and Histopathologic Features.

Brain tumor research and treatment
2017

Upfront Gamma Knife Surgery for Giant Central Neurocytoma.

World neurosurgery
2017

Pediatric Central Neurocytoma.

Journal of child neurology
2016

Glioneuronal tumors of cerebral hemisphere in children: correlation of surgical resection with seizure outcomes and tumor recurrences.

Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery
2016

Clinical characteristics and prognostic factors of brain central neurocytoma.

Oncotarget
2016

Atypical central neurocytoma with metastatic craniospinal dissemination: a case report.

Clinical imaging
2016

Extraventricular neurocytoma in the left temporal lobe: A case report and review of the literature.

Oncology letters
2016

Pre-operative Embolization of Intracranial and Extracranial Tumors: A Review of 37 Cases.

Journal of the Medical Association of Thailand = Chotmaihet thangphaet
2016

Rapid tumor growth with glial differentiation of central neurocytoma after stereotactic radiosurgery.

Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia
2016

Hypothalamic Extraventricular Neurocytoma (EVN) in a Pediatric Patient: A Case of EVN Treated with Subtotal Removal Followed by Adjuvant Radiotherapy.

Brain tumor research and treatment
2016

Treatment Results of Gamma Knife Radiosurgery for Central Neurocytoma: Report of a Japanese Multi-Institutional Cooperative Study.

World neurosurgery
2016

Intraoperative high-field MRI maximizes the extent of resection in intraventricular central neurocytoma surgery.

Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia
2015

Role of adjuvant radiation in the management of central neurocytoma: Experience from a tertiary cancer care center of India.

Indian journal of cancer
2016

Minimally Invasive Transsulcal Resection of Intraventricular and Periventricular Lesions Through a Tubular Retractor System: Multicentric Experience and Results.

World neurosurgery
2016

Operative Management of Intraventricular Central Neurocytomas: An Analysis of a Surgical Experience with 32 Cases.

Turkish neurosurgery
2015

Tetraventricular central neurocytoma: A rare presentation with imaging-pathologic correlation.

Journal of neurosciences in rural practice
2016

Clinical outcome and prognostic factors for central neurocytoma: twenty year institutional experience.

Journal of neuro-oncology
2015

Neurocytoma arising from a mature ovary teratoma: a case report.

Diagnostic pathology
2015

Primary intraventricular oligodendroglioma: A case report of the usefulness of Olig2 immunohistochemistry for diagnosis.

Neuropathology : official journal of the Japanese Society of Neuropathology
2015

Cerebral oligodendroglioma mimicking intraventricular neoplasia in three dogs.

Journal of veterinary diagnostic investigation : official publication of the American Association of Veterinary Laboratory Diagnosticians, Inc
2015

(P043) Central neurocytoma: impact of resection extent and adjuvant radiotherapy on survival outcomes.

Oncology (Williston Park, N.Y.)
2015

Atypical extraventricular neurocytoma in a 3-year-old girl: case report with radiological-pathological correlation.

Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery
2015

Pan ventricular neurocytoma.

Asian journal of neurosurgery
2015

Cavernoma of the septum pellucidum in the region of foramen of Monro.

Neurology India
2014

Intraventricular mass lesions at magnetic resonance imaging: iconographic essay - part 1.

Radiologia brasileira
2014

Atypical Neurocytoma: Dilemma in diagnosis and management.

Surgical neurology international
2014

Intraventricular hemorrhage--unusual presentation of central neurocytoma.

Neurology India
Ver todos os 349 no EuropePMC

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Comunidades

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Doenças relacionadas

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Referências e fontes

Bases de dados externas citadas neste artigo

Publicações científicas

Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.

  1. Epidemiology and Long-Term Treatment Outcome of Central Neurocytoma: A Retrospective National Study from Saudi Arabia.
    World neurosurgery· 2026· PMID 41475458mais citado
  2. Diffuse midline glioma, H3K27-altered, mimicking central neurocytoma on MRI: A case report.
    Radiology case reports· 2026· PMID 41234807mais citado
  3. Improved tumor control with adjuvant radiotherapy in patients with central neurocytoma: a multicenter study.
    Journal of neuro-oncology· 2026· PMID 41872623mais citado
  4. Transfrontal Endoscopic Endoport Approach for Gross Total Resection of a Panventricular Central Neurocytoma: 2-Dimensional Operative Video.
    Operative neurosurgery (Hagerstown, Md.)· 2026· PMID 40168511mais citado
  5. Central Neurocytoma in the Fourth Ventricle: A Case Report and Review of Cases With This Unusual Presentation Site.
    Cureus· 2025· PMID 41356891mais citado
  6. Case Report: Familial hCG syndrome with elevated hCG level concurrently in blood and cerebrospinal fluid.
    Front Endocrinol (Lausanne)· 2026· PMID 41970975recente

Bases de dados e fontes oficiais

Identificadores e referências canônicas usadas para montar este verbete.

  1. ORPHA:73256(Orphanet)
  2. MONDO:0019134(MONDO)
  3. GARD:10641(GARD (NIH))
  4. Busca completa no PubMed(PubMed)
  5. Q5062123(Wikidata)

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Neurocitoma central
Compêndio · Raras BR

Neurocitoma central

ORPHA:73256 · MONDO:0019134
Prevalência
Unknown
Casos
500 casos conhecidos
Herança
Not applicable
CID-10
D33.0 · Neoplasia benigna do encéfalo, supratentorial
CID-11
Ensaios
1 ativos
Início
Adolescent, Adult, Childhood
Prevalência
0.0 (Worldwide)
MedGen
UMLS
C0206719
EuropePMC
Wikidata
Papers 10a
DiscussaoAtiva

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