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Síndrome de opsoclonia-mioclonia
ORPHA:1183CID-10 · G25.3CID-11 · 9C85.02DOENÇA RARA

A síndrome opsoclonia mioclonia (OMS) é uma doença neuroinflamatória rara de origem paraneoplásica, parainfecciosa ou idiopática, caracterizada por opsoclonia, mioclonia, ataxia e distúrbios comportamentais e do sono.

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Introdução

O que você precisa saber de cara

📋

A síndrome opsoclonia mioclonia (OMS) é uma doença neuroinflamatória rara de origem paraneoplásica, parainfecciosa ou idiopática, caracterizada por opsoclonia, mioclonia, ataxia e distúrbios comportamentais e do sono.

Pesquisas ativas
1 ensaio
6 total registrados no ClinicalTrials.gov
Publicações científicas
491 artigos
Último publicado: 2026 Apr 14

Escala de raridade

CLASSIFICAÇÃO ORPHANET · BRASIL 2024
Unknown
Ultra-rara
<1/50k
Muito rara
1/20k
Rara
1/10k
Pouco freq.
1/5k
Incomum
1/2k
Prevalência
0.0
Worldwide
Início
Childhood
+ infancy
🏥
SUS: Cobertura mínimaScore: 15%
CID-10: G25.3
🇧🇷Dados SUS / DATASUS
PROCEDIMENTOS SIGTAP (2)
0202010694
Sequenciamento completo do exoma (WES)genetic_test
0301070040
Atendimento em reabilitação — doenças rarasrehabilitation
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Sinais e sintomas

O que aparece no corpo e com que frequência cada sintoma acontece

Partes do corpo afetadas

🧠
Neurológico
5 sintomas
🫁
Pulmão
2 sintomas
💪
Músculos
2 sintomas
🛡️
Imunológico
2 sintomas
🦴
Ossos e articulações
1 sintomas
👁️
Olhos
1 sintomas

+ 9 sintomas em outras categorias

Características mais comuns

90%prev.
Opsoclonia
Muito frequente (99-80%)
90%prev.
Anormalidade do sono
Muito frequente (99-80%)
90%prev.
Ataxia
Muito frequente (99-80%)
90%prev.
Movimentos sacádicos oculares anormais
Muito frequente (99-80%)
90%prev.
Mioclonias
Muito frequente (99-80%)
55%prev.
Neuroblastoma
Frequente (79-30%)
22sintomas
Muito frequente (5)
Frequente (8)
Ocasional (9)

Os sintomas variam de pessoa para pessoa. Abaixo estão as 22 características clínicas mais associadas, ordenadas por frequência.

OpsocloniaOpsoclonus
Muito frequente (99-80%)90%
Anormalidade do sonoSleep abnormality
Muito frequente (99-80%)90%
Ataxia
Muito frequente (99-80%)90%
Movimentos sacádicos oculares anormaisAbnormal saccadic eye movements
Muito frequente (99-80%)90%
MiocloniasMyoclonus
Muito frequente (99-80%)90%

Linha do tempo da pesquisa

Publicações por ano — veja quando o interesse científico cresceu
Anos de pesquisa1desde 2026
Total histórico491PubMed
Últimos 10 anos200publicações
Pico202141 papers
Linha do tempo
2026Hoje · 2026🧪 2004Primeiro ensaio clínico📈 2021Ano de pico
Publicações por ano (últimos 10 anos)

Encontrou um erro ou informação desatualizada? Sugira uma correção →

Genética e causas

O que está alterado no DNA e como passa nas famílias

🧬

Nenhum gene associado encontrado

Os dados genéticos desta condição ainda estão sendo catalogados.

Diagnóstico

Os sinais que médicos procuram e os exames que confirmam

Carregando...

Tratamento e manejo

Remédios, cuidados de apoio e o que precisa acompanhar

Pipeline de tratamentos
Pipeline regulatório — de medicamentos já aprovados a drogas em pesquisa exploratória.
3Fase 31
2Fase 23
·Pré-clínico1
Medicamentos catalogadosEnsaios clínicos· 0 medicamentos · 5 ensaios
Carregando informações de tratamento...

Onde tratar no SUS

Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

🇧🇷 Atendimento SUS — Síndrome de opsoclonia-mioclonia

🗺️

Selecione um estado ou use sua localização para ver resultados.

Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.

Pesquisa ativa

Ensaios clínicos abertos e novidades científicas recentes

Pesquisa e ensaios clínicos

6 ensaios clínicos encontrados, 1 ativos.

Distribuição por fase
Ver todos no ClinicalTrials.gov
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Publicações mais relevantes

Timeline de publicações
235 papers (10 anos)
#1

Neuroblastoma-associated opsoclonus-myoclonus-ataxia syndrome: an important yet overlooked diagnosis in pediatric ataxia.

The Turkish journal of pediatrics2026 Feb 27

Opsoclonus-myoclonus-ataxia syndrome (OMAS) is a rare, immune-mediated neurological disorder, often associated with neuroblastoma (NB) in children. This study aimed to describe the clinical features, diagnostic challenges, treatment, and outcomes of pediatric patients with NB-associated OMAS. We retrospectively reviewed medical records of seven children diagnosed with NB-associated OMAS between November 1, 2015 and January 31, 2025. Data on demographics, clinical presentation, tumor characteristics, treatment protocols, relapses, and outcomes were collected. The Mitchell-Pike OMS Rating Scale was used to assess severity. The cohort included four girls and three boys, aged 18-36 months (median 31). All had a history of infection and/or vaccination preceding symptom onset. Ataxia was the most common initial symptom (6/7, 85.7%), followed by behavioral disturbances and sleep disorders (5/7, 71.4% each). At presentation, opsoclonus was present in two patients, which was initially misdiagnosed as nystagmus. All but one patient had opsoclonus during the disease course. Neuroblastomas were located in abdominal (n=4), thoracic (n=1), and sacral (n=2) regions; all tumors measured.

#2

HLA and T-Cell Receptor Investigations in Idiopathic and Paraneoplastic Opsoclonus-Myoclonus in Children.

Neurology(R) neuroimmunology &amp; neuroinflammation2026 Mar

Opsoclonus-myoclonus-ataxia syndrome (OMAS) is a rare pediatric autoimmune neurologic disorder, with 40%-50% of cases occurring as a paraneoplastic syndrome in the setting of neuroblastoma or other neuroblastic tumors. The strong clinical similarities between idiopathic and paraneoplastic OMAS have led to the hypothesis that neuroblastoma may initially be present in idiopathic cases but spontaneously regress before OMAS onset. Both B- and T-cell mechanisms appear to contribute to OMAS autoimmunity, although their precise roles remain unknown. The aim of this study was to investigate similarities and differences between idiopathic and paraneoplastic OMAS by analyzing HLA profiles and T-cell receptor (TCR) repertoires in a Spanish pediatric cohort. Children with OMAS were enrolled in a nationwide prospective study (2013-2024). Neural autoantibody testing was performed in all patients. HLA genotyping was performed using next-generation sequencing (GenDx/Illumina) and compared with a reference Spanish population (n = 4,335). The Benjamini-Hochberg false discovery rate method was used to control for multiple comparisons across HLA antigens. TCR repertoires were analyzed in peripheral blood samples of 12 patients using the Adaptive Biotechnologies immunoSEQ assay. The bioinformatics tool Grouping of Lymphocyte Interactions by Paratope Hotspots (GLIPH2) was used to identify shared motifs within CDR3β-TCR sequences. Among 25 children with OMAS (median age 22 months [interquartile range (IQR): 15-38]), 12 (48%) had neuroblastoma and 3 (12%) had neuronal antibodies (one with anti-Hu, one with anti-myelin oligodendrocyte glycoprotein, one against unknown neuronal surface antigens). Some HLA class II antigens (DRB1*08, DRB1*10, and DQB1*04) were consistently overrepresented in patients with OMAS compared with Spanish controls (all p-adjusted <0.05). Distinct HLA antigens were associated with idiopathic OMAS (HLA-DRB1*08, HLA-DQB1*04), while paraneoplastic OMAS was linked to HLA-DRB1*10 (all p-adjusted <0.05), suggesting subgroup-specific genetic risks. TCR analysis revealed that patients with paraneoplastic OMAS showed greater TCR repertoire similarity, whereas shared sequences were rare in idiopathic OMAS. Despite similar clinical presentations, idiopathic and paraneoplastic OMASs appear to have distinct immunopathogenic mechanisms. In paraneoplastic OMAS, enrichment of specific HLA antigens and convergent TCR profiles supports antigen-driven T cell-mediated autoimmunity.

#3

Opsoclonus-myoclonus syndrome with anti-SOX1 antibodies.

BMJ case reports2026 Feb 02
#4

High Expression of CCL2 Correlated With Dendritic Cell Recruitment in Neuroblastomas Associated With Opsoclonus-Myoclonus Syndrome.

Laboratory investigation; a journal of technical methods and pathology2026 Jan

Neuroblastoma (NB) accounts for 10% to 15% of cancer-related deaths among children. In rare cases, NB is associated with opsoclonus-myoclonus syndrome (OMS), a neurological paraneoplastic syndrome. These low-risk (LR) NBs with OMS have a favorable prognosis and an immune-enriched microenvironment. The recruitment of dendritic cells (DCs) and T lymphocytes into tumors is known to be mediated by CCL2 and CXCL12, respectively. We investigated whether intratumor CCL2 and CXCL12 promote DC recruitment within the microenvironment of OMS-associated LR-NBs. We conducted a multicentric retrospective case-control study on 44 pediatric patients with NBs associated or not with OMS. The non-OMS population was subdivided into an LR-NB group versus a high-risk (HR)-NB group, with or without MYCN amplification. Immunohistochemistry was performed using anti-CCL2 and anti-CXCL12 antibodies. DC subpopulations were stained using OPAL spectral multiplex immunofluorescence. Immunostaining scores were established by semiquantitative optical analysis. Gene signatures of DC, as well as CCL2 and CXCL12 mRNA expressions, were also analyzed on a public RNA-Seq data set of NB. We observed a significantly higher protein expression of CCL2 in OMS-associated LR-NBs compared with MYCN-amplified HR-NBs, whereas CXCL12 was not preferentially expressed by any of the NB groups. Furthermore, DC infiltrate was more abundant in OMS-associated LR-NBs compared with any other NB risk groups and positively correlated with CCL2 expression. In silico analysis of public RNA-Seq data demonstrated a higher CCL2 expression in LR-NB with or without OMS compared with HR groups, and that the DC transcriptomic signature was higher in OMS-associated LR-NBs compared with HR-NB groups. We also observed a positive correlation between the DC gene signature and CCL2 or CXCL12 mRNA expression, to a lesser extent. Our results suggest that a DC-prone microenvironment might explain the favorable oncologic outcome of OMS-associated LR-NBs. CCL2 could be a therapeutic target to mobilize DCs in HR-NBs or in tumors characterized by a paucity of tumor-infiltrating DCs.

#5

Prolonged Diagnostic Latency and Long-term Surveillance in Anti-Ri Antibody-positive Opsoclonus-myoclonus Syndrome with Carcinoma of Unknown Primary.

Internal medicine (Tokyo, Japan)2026 Feb 15

Opsoclonus-myoclonus syndrome (OMS) is a rare paraneoplastic neurological disorder that is usually associated with breast cancer or small-cell lung carcinoma. We report the case of a 71-year-old woman with anti-Ri antibody-positive OMS, in whom no malignancy was initially identified. Thirty months later, carcinoma of an unknown primary tumor with supraclavicular and liver metastases was diagnosed. Neurological symptoms remained stable with immunosuppressive therapy, but the overall outcome was poor owing to progressive malignancy. This case underscores the fact that neurological stability does not necessarily equate to a favorable prognosis, and highlights the need for long-term surveillance in cases involving paraneoplastic syndromes.

Publicações recentes

Ver todas no PubMed

📚 EuropePMC329 artigos no totalmostrando 196

2026

Neuroblastoma-associated opsoclonus-myoclonus-ataxia syndrome: an important yet overlooked diagnosis in pediatric ataxia.

The Turkish journal of pediatrics
2026

Opsoclonus-myoclonus syndrome with anti-SOX1 antibodies.

BMJ case reports
2025

[A Case of Breast Cancer Initially Presenting with Opsoclonus-Myoclonus Syndrome].

Gan to kagaku ryoho. Cancer &amp; chemotherapy
2026

HLA and T-Cell Receptor Investigations in Idiopathic and Paraneoplastic Opsoclonus-Myoclonus in Children.

Neurology(R) neuroimmunology &amp; neuroinflammation
2025

Through the Lens of Experience: A Case Series on Pediatric Neuroblastic Tumors.

Indian journal of surgical oncology
2025

Transmitter and ion channel profiles of saccadic omnipause neurons and cholinergic non-omnipause neurons in human nucleus raphe interpositus.

Frontiers in neuroanatomy
2025

[Opsoclonus-myoclonus-ataxia syndrome associated with St Louis virus infection in Argentina].

Medicina
2026

High Expression of CCL2 Correlated With Dendritic Cell Recruitment in Neuroblastomas Associated With Opsoclonus-Myoclonus Syndrome.

Laboratory investigation; a journal of technical methods and pathology
2025

Diagnostic odyssey of opsoclonus-myoclonus syndrome and barriers to early detection.

Brain &amp; development
2025

Identification and Verification of Immune Metabolism-Related Biomarkers and Immune Infiltration Landscape for Pediatric Opsoclonus Myoclonus Ataxia Syndrome in Neuroblastoma.

CNS neuroscience &amp; therapeutics
2025

Movement Disorders in West Nile Virus Infection: A Systematic Review of Reported Cases and Conference Abstracts.

Movement disorders clinical practice
2025

Motor, cognitive, affective, and communication outcomes in patients with sustained remission of opsoclonus-myoclonus-ataxia syndrome.

European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society
2026

Prolonged Diagnostic Latency and Long-term Surveillance in Anti-Ri Antibody-positive Opsoclonus-myoclonus Syndrome with Carcinoma of Unknown Primary.

Internal medicine (Tokyo, Japan)
2025

Cancer-Associated Retinopathy and Optic Neuropathy in a Patient with Lung Adenocarcinoma.

Case reports in ophthalmology
2025

Anti-Ri Paraneoplastic Neurologic Syndrome in a Patient With Untreated Breast Cancer.

Cureus
2025

Genetic Landscape of Opsoclonus-Myoclonus-Ataxia Syndrome in Children.

Pediatric neurology
2025

Whether the Opsoclonus Myoclonus Syndrome Is Paraneoplastic or SARS-CoV-2-Related Can Be Clarified.

IJU case reports
2025

Opsoclonus-myoclonus Syndrome in a Female Breast Cancer Patient: A Case Report and Literature Review.

Anticancer research
2025

Bridging the Gap: Opsoclonus-Myoclonus Syndrome: Human Pegivirus Encephalomyelitis Diagnosed Through Metagenomic Next-Generation Sequencing.

Neurology
2025

Seronegative Paraneoplastic Opsoclonus-Myoclonus-Ataxia Syndrome Secondary to Low Volume Endocrine-Sensitive Malignancy of Likely Breast Origin.

Current oncology (Toronto, Ont.)
2025

Opsoclonus-Myoclonus-Ataxia Syndrome in a Patient With West Nile Virus: Case Report and a Patient's Experience.

The Neurohospitalist
2025

Opsoclonus in Children: Diagnosis, Etiology, and Ophthalmologic Assessment of Patients at a Tertiary Children's Hospital.

Pediatric neurology
2025

Challenges in Diagnosing Opsoclonus-Myoclonus Syndrome in Adults.

Cureus
2025

A comprehensive and critical narrative review on movement disorders linked through dengue virus based infection.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology
2025

Pediatric Opsoclonus-Myoclonus-Ataxia Syndrome can Lead to Long-Term Neurological, Neuropsychological, and Cognitive Sequelae Associated with Cerebellar Atrophy.

Cerebellum (London, England)
2025

Scrub typhus-associated movement and gait disorders: A systematic review with principal component analysis and in silico mechanistic modelling.

Tropical medicine &amp; international health : TM &amp; IH
2025

Review of Paraneoplastic Syndromes in Children with Malignancy.

Medical science monitor : international medical journal of experimental and clinical research
2025

Scrub Saccadomania: An Enigma of Eye Movement in the Tropics.

The Journal of the Association of Physicians of India
2025

A case of suspected paraneoplastic nerve syndrome associated with prostate cancer or opsoclonus-myoclonus syndrome associated with COVID-19 infection, but symptoms improved after treatment of both.

IJU case reports
2025

Para-infective opsoclonus-myoclonus syndrome due to malaria in a returning traveller.

Practical neurology
2025

The utilization of the multimodal immunotherapy for the opsoclonus-myoclonus syndrome can reduce relapses and permanent neurological sequelae.

Italian journal of pediatrics
2024

Opsoclonus-myoclonus syndrome in the course of teratoma: a case report.

Frontiers in medicine
2025

Zellweger spectrum disorder presenting with opsoclonus-myoclonus-ataxia syndrome: a case report on immunotherapy.

Acta neurologica Belgica
2025

Opsoclonus Myoclonus Ataxia Syndrome: An Atypical Presentation of Tuberculous Meningitis.

The American journal of tropical medicine and hygiene
2024

[Paraneoplastic opsoclonus-myoclonus syndrome].

Zhurnal nevrologii i psikhiatrii imeni S.S. Korsakova
2024

Paraneoplastic Syndromes of the Nervous System in Patients Suffering from SCLC. A Review of the Recent Literature.

Acta medica academica
2024

Immune-mediated neurological syndromes associated with childhood cancers.

European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society
2024

Unique Magnetic Resonance Imaging Findings in Opsoclonus-Myoclonus Syndrome Secondary to the West Nile Virus.

Cureus
2024

[Opsoclonus-myoclonus syndrome associated with West Nile virus].

Zhurnal nevrologii i psikhiatrii imeni S.S. Korsakova
2024

An unusual case of early onset opsoclonus-myoclonus syndrome: Case report and literature review.

SAGE open medical case reports
2024

Opsoclonus-myoclonus-ataxia syndrome associated with bacterial urinary tract infection.

BMJ case reports
2024

Pediatric Autoimmune Neurologic Disorders.

Continuum (Minneapolis, Minn.)
2024

Autoimmune Movement Disorders.

Continuum (Minneapolis, Minn.)
2024

Recent advances in diagnosis of immune-mediated cerebellar ataxias: novel concepts and fundamental questions on autoimmune mechanisms.

Journal of neurology
2024

Inaugural Patient-Reported Registry of Pediatric Opsoclonus-Myoclonus-Ataxia Syndrome: Presentation, Diagnosis, and Treatment of 194 Patients.

Pediatric neurology
2024

Opsoclonus-Ataxia Syndrome in a Patient With Small-Cell Lung Cancer Treated With Immune Checkpoint Inhibitors.

Neurology(R) neuroimmunology &amp; neuroinflammation
2024

Opsoclonus-Myoclonus With Anti-YO Antibodies Revealing Breast Cancer: A Case Report.

Cureus
2024

Dengue Fever Associated Opsoclonus Myoclonus Ataxia Syndrome.

Movement disorders clinical practice
2024

Drug- and Toxin-Induced Opsoclonus - a Systematized Review, including a Case Report on Amantadine-Induced Opsoclonus in Multiple System Atrophy.

Tremor and other hyperkinetic movements (New York, N.Y.)
2024

Late cognitive and adaptive outcomes of patients with neuroblastoma-associated opsoclonus-myoclonus-ataxia-syndrome: A report from the Children's Oncology Group.

Pediatric blood &amp; cancer
2024

Immune Ataxias: The Continuum of Latent Ataxia, Primary Ataxia and Clinical Ataxia.

Journal of integrative neuroscience
2024

Clinical Presentation, Management, and Diagnostic Performance of 2021 Criteria for Paraneoplastic Neurologic Syndromes in Childhood.

Neurology(R) neuroimmunology &amp; neuroinflammation
2024

Diagnostic value of 18F-fluorodeoxyglucose positron emission tomography/computed tomography imaging in pediatric opsoclonus myoclonus ataxia syndrome presenting with neuroblastoma.

Pediatric radiology
2024

Brain Volumes in Opsoclonus-Myoclonus Ataxia Syndrome: A Longitudinal Study.

Journal of child neurology
2024

Paraneoplastic antibodies targeting intracellular antigens.

Handbook of clinical neurology
2024

A rare clinical presentation of COVID 19: opsoclonus-myoclonus ataxia syndrome.

Journal of infection in developing countries
2024

Characteristics of Opsoclonus-Myoclonus Syndrome in Patients of the Largest Pediatric Hospital in Latin America.

Pediatric neurology
2024

Benign paraspinal ganglioneuroma with paraneoplastic opsoclonus myoclonus syndrome.

BMJ case reports
2025

Opsoclonus-myoclonus syndrome and prostate cancer. An entity to be aware of.

Neurologia
2024

[Clinical and prognostic analysis of opsoclonus-myoclonus-ataxia syndrome in children].

Zhonghua er ke za zhi = Chinese journal of pediatrics
2024

Successful use of tacrolimus for treatment-refractory neuroblastoma-associated opsoclonus-myoclonus-ataxia syndrome: A case series.

Pediatric blood &amp; cancer
2023

Paraneoplastic Opsoclonus-Myoclonus Syndrome Associated with Non-Small Cell Lung Cancer.

The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiques
2023

Recent Advances in Immune-Mediated Cerebellar Ataxias: Pathogenesis, Diagnostic Approaches, Therapies, and Future Challenges-Editorial.

Brain sciences
2023

A Case of Paraneoplastic Neurological Syndrome Leading to the Diagnosis of Large Cell Neuroendocrine Carcinoma From Opsoclonus-Myoclonus Syndrome.

Cureus
2023

Metabolic Opsoclonus Myoclonus Syndrome in a Patient of Crohn's Disease: Lessons Learnt.

Annals of Indian Academy of Neurology
2023

[Clinical analysis of adult oculomoclonus-myoclonus syndrome with vertigo].

Zhonghua nei ke za zhi
2024

Opsoclonus-Myoclonus-Ataxia Syndrome Due to Covid-19.

Cerebellum (London, England)
2023

Immune-mediated ataxias: Guide to clinicians.

Parkinsonism &amp; related disorders
2023

An International Pediatric-Onset Opsoclonus-Myoclonus Ataxia Syndrome Registry and Clinical Research Network: Development, Progress, and Vision.

Pediatric neurology
2023

Cervical Ganglioneuroblastoma Diagnosed by 68Ga-DOTATOC PET/CT in a Child with Opsoclonus Myoclonus Syndrome.

Journal of nuclear medicine technology
2024

Powassan Virus Encephalitis: A Tertiary Center Experience.

Clinical infectious diseases : an official publication of the Infectious Diseases Society of America
2023

Polyclonal lymphoid expansion drives paraneoplastic autoimmunity in neuroblastoma.

Cell reports
2024

Retrospective analysis of COVID-19 patients with Guillain-Barre, Miller-Fisher, and opsoclonus-myoclonus-ataxia syndromes-a case series.

Wiener medizinische Wochenschrift (1946)
2023

[Immune-Mediated Cerebellar Ataxias].

Brain and nerve = Shinkei kenkyu no shinpo
2023

Combined neuraxial-general anesthesia in opsoclonus-myoclonus syndrome: A case report.

Saudi journal of anaesthesia
2024

Five Years Follow-up of Opsoclonus-Myoclonus-Ataxia Syndrome-Associated Neurogenic Tumors in Children.

Neuropediatrics
2023

Adult-onset idiopathic opsoclonus-myoclonus syndrome.

Arquivos brasileiros de oftalmologia
2023

Neuroblastic Tumor Recurrence Associated With Opsoclonus Myoclonus Ataxia Syndrome Relapse a Decade After Initial Resection and Treatments.

Journal of pediatric hematology/oncology
2024

Anti-Ri paraneoplastic neurological syndrome presenting with bilateral cranial nerve VI palsy and jaw dystonia-a distinctive syndrome within the anti-Ri spectrum? : Case report and literature review.

Wiener medizinische Wochenschrift (1946)
2023

Opsoclonus Myoclonus Ataxia Syndrome Due to SARS-CoV-2.

Neuro-ophthalmology (Aeolus Press)
2023

Probable association between mRNA COVID-19 vaccine and opsoclonus-myoclonus-ataxia syndrome.

Journal of AAPOS : the official publication of the American Association for Pediatric Ophthalmology and Strabismus
2022

Opsoclonus Myoclonus Syndrome in a Case of Severe Acute Malnutrition in Children: A Case Report.

Cureus
2023

Sensory trick in patients with opsoclonus-myoclonus syndrome.

Acta neurologica Belgica
2023

Neuroblastoma-related severe hypoperfusion in the cerebellum of an infant: A case of opsoclonus-myoclonus syndrome.

Asia Oceania journal of nuclear medicine &amp; biology
2023

Opsoclonus-myoclonus syndrome caused by organophosphate poisoning.

Practical neurology
2022

Paraneoplastic Opsoclonus-Myoclonus Syndrome as a Rare Presentation of Small-Cell Lung Cancer.

Cureus
2022

Opsoclonus-myoclonus syndrome associated with pancreatic neuroendocrine tumor: a case report.

BMC neurology
2023

"Pediatrician's Approach to Recognizing Neuroblastoma With Opsoclonus-Myoclonus-Ataxia Syndrome".

Clinical pediatrics
2023

Opsoclonus-myoclonus syndrome: Clinical characteristics, therapeutic considerations, and prognostic factors in a Spanish paediatric cohort.

Neurologia
2022

Comparison of mediastinal and non-mediastinal neuroblastoma and ganglioneuroblastoma associated with opsoclonus-myoclonus syndrome: a systematic review and meta-analysis.

Translational cancer research
2022

A review of the neurological complications of breast cancer.

Journal of family medicine and primary care
2022

Opsoclonus-myoclonus paraneoplastic syndrome in nasopharyngeal carcinoma.

BMJ case reports
2022

Clinical features and outcomes of opsoclonus myoclonus ataxia syndrome.

European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society
2022

Rare Etiologies in Immune-Mediated Cerebellar Ataxias: Diagnostic Challenges.

Brain sciences
2023

Presence of identical B-cell clone in both cerebrospinal fluid and tumor tissue in a patient with opsoclonus-myoclonus syndrome associated with neuroblastoma.

Pediatric hematology and oncology
2022

Opsoclonus-myoclonus syndrome associated with neuroblastoma: Insights into antitumor immunity.

Pediatric blood &amp; cancer
2023

Covid-19 vaccines and neurological complications: a systematic review.

Zeitschrift fur Naturforschung. C, Journal of biosciences
2022

Breast Cancer Presenting As Onconeural Antibody Negative Opsoclonus-Myoclonus Syndrome.

Cureus
2023

Anti-SOX1 Antibody-positive Small-cell Lung Cancer That Triggered Opsoclonus.

Internal medicine (Tokyo, Japan)
2022

Para-Infectious Opsoclonus Myoclonus Syndrome with COVID-19.

Annals of Indian Academy of Neurology
2022

Opsoclonus-myoclonus Syndrome with Neuroblastoma in Children and their Anaesthetic Management.

Journal of the College of Physicians and Surgeons--Pakistan : JCPSP
2022

Monocentric retrospective clinical outcome in a group of 13 patients with opsoclonus myoclonus syndrome, proposal of diagnostic algorithm and review of the literature.

European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society
2023

Opsoclonus myoclonus ataxia syndrome following COVID-19 infection.

Acta neurologica Belgica
2022

Paraneoplastic syndrome in neuroophthalmology.

Journal of neurology
2022

Neurological Manifestations of Scrub Typhus.

Current neurology and neuroscience reports
2022

Ovarian Teratoma-Related Paraneoplastic Neurological Syndromes.

Frontiers in oncology
2023

Autoimmune Cerebellar Ataxia: Etiology and Clinical Characteristics of a Case Series from China.

Cerebellum (London, England)
2022

A Case of Opsoclonus-Myoclonus-Ataxia With Neuronal Intermediate Filament IgG Detected in Cerebrospinal Fluid.

Journal of neuro-ophthalmology : the official journal of the North American Neuro-Ophthalmology Society
2022

Opsoclonus-Myoclonus in COVID-19 Infection. A Known Clinical Presentation in New Disease.

Journal of neuro-ophthalmology : the official journal of the North American Neuro-Ophthalmology Society
2022

Long-term neurological outcomes of children with neuroblastoma with opsoclonus-myoclonus syndrome.

Translational pediatrics
2022

Central nervous system adverse events after ChAdOx1 vaccination.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology
2022

Diagnosis and Management of Opsoclonus-Myoclonus-Ataxia Syndrome in Children: An International Perspective.

Neurology(R) neuroimmunology &amp; neuroinflammation
2022

Anti-Ri-Associated Paraneoplastic Neurological Syndrome Revealing Breast Cancer: A Case Report.

Cureus
2022

Temporal Changes in Brain Perfusion in a Patient with Myoclonus and Ataxia Syndrome Associated with COVID-19.

Internal medicine (Tokyo, Japan)
2022

Paraneoplastic Opsoclonus-myoclonus Syndrome with Anti-Hu and Anti-SOX-1 Antibodies after Immune-checkpoint Inhibitor Treatment Combined with Chemotherapy in a Patient with Small-cell Lung Cancer.

Internal medicine (Tokyo, Japan)
2022

Postinfectious SARS-CoV-2 Opsoclonus-Myoclonus-Ataxia Syndrome.

Journal of neuro-ophthalmology : the official journal of the North American Neuro-Ophthalmology Society
2022

Case Report: Opsoclonus-Myoclonus Syndrome Associated With Contactin-Associated Protein-Like 2 and Acetylcholine Receptor Autoantibodies in the Setting of Non-Small Cell Lung Carcinoma.

The Neurohospitalist
2021

Opsoclonus-Myoclonus Syndrome in Children and Adolescents: A Therapeutic Challenge.

Children (Basel, Switzerland)
2021

Breast cancer-associated opsoclonus-myoclonus syndrome: a case report.

World journal of surgical oncology
2021

Clinical Analysis of Pediatric Opsoclonus-Myoclonus Syndrome in One of the National Children's Medical Center in China.

Frontiers in neurology
2021

Opsoclonus-Myoclonus-Associated Neuroblastoma With Bone Marrow Metastases: What Would Be the Best Treatment Option?

Oncology (Williston Park, N.Y.)
2021

Opsoclonus myoclonus ataxia may differentiate postinfectious autoimmune encephalitis from infectious encephalitis.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology
2022

Opsoclonus-myoclonus syndrome in HIV encephalitis: Treatment and PET/MRI functional changes.

Revue neurologique
2022

Surgical considerations for neuroblastoma-associated opsoclonus-myoclonus-ataxia syndrome: a series of 14 patients from a single institution.

Pediatric surgery international
2021

Post-COVID-19 opsoclonus-myoclonus syndrome and encephalopathy associated with leucine-rich glioma-inactivated 1 (LGI-1) antibodies.

Journal of the neurological sciences
2021

Atypical Presentation of Enterovirus D68 Infection as Opsoclonus-Myoclonus Syndrome.

Pediatric neurology
2021

Increased Prevalence of Familial Autoimmune Disease in Children With Opsoclonus-Myoclonus Syndrome.

Neurology(R) neuroimmunology &amp; neuroinflammation
2021

Acute Movement Disorders in Childhood: A Cohort Study and Review of the Literature.

Pediatric emergency care
2022

Delayed Opsoclonus-Myoclonus Syndrome After Ovarian Teratoma Resection.

Journal of neuro-ophthalmology : the official journal of the North American Neuro-Ophthalmology Society
2021

Low-dose intrathecal rituximab is a safe and potentially effective treatment for pediatric neuroimmunologic disorders.

Journal of neuroimmunology
2022

Scrub typhus meningoencephalitis presenting as opsoclonus myoclonus syndrome: A video-based case.

Tropical doctor
2021

New-Onset Refractory Status Epilepticus (NORSE) as a Recurrence of Anti-Neuronal Nuclear Antibody 2 (ANNA-2) Encephalitis After Immune Checkpoint Inhibition Therapy.

Cureus
2021

Opsoclonus myoclonus induced by lamotrigine toxicity.

Seizure
2021

Recurrent angiosarcoma of scalp with opsoclonus myoclonus syndrome: role of salvage treatment.

BMJ case reports
2021

Post-COVID Opsoclonus Myoclonus Syndrome: A Case Report From Pakistan.

Frontiers in neurology
2021

Opsoclonus-myoclonus in Aicardi-Goutières syndrome.

Developmental medicine and child neurology
2021

Paraneoplastic opsoclonus-myoclonus syndrome with positive anti-Yo antibody: A case report and literature review.

Revue neurologique
2021

Two COVID-19-related video-accompanied cases of severe ataxia-myoclonus syndrome.

Neurologia i neurochirurgia polska
2021

78-year-old woman with opsoclonus myoclonus ataxia syndrome secondary to COVID-19.

BMJ case reports
2021

Paraneoplastic opsoclonus-myoclonus-ataxia syndrome secondary to ovarian cancer.

Practical neurology
2021

Anti-Ma paraneoplastic opsoclonus-myoclonus syndrome.

BMJ case reports
2022

Opsoclonus-Myoclonus Syndrome as a Heralding Feature of Scrub Typhus: An Illustrative Case with a Video Vignette.

Journal of movement disorders
2021

Opsoclonus-myoclonus syndrome associated with anti Kelch-like protein-11 antibodies in a young female patient without cancer.

Journal of neuroimmunology
2021

Opsoclonus-myoclonus syndrome with severe clinical course and beneficial outcome: A case report.

Medicine
2021

Voltage-Gated Calcium Channel Antibody-Induced Oropharyngeal Dysphagia Presenting as a Paraneoplastic Neurological Complication in Breast Cancer.

Cureus
2021

Opsoclonus myoclonus ataxia syndrome in severe acute respiratory syndrome coronavirus-2.

Journal of neurovirology
2022

Opsoclonus-myoclonus-ataxia syndrome in children.

Journal of neurology
2021

Neuroblastoma With Opsoclonus-Myoclonus-Ataxia Syndrome: Role of Chemotherapy in the Management: Experience From a Tertiary Care Center in a Resource-limited Setting.

Journal of pediatric hematology/oncology
2021

Autoimmune Movement Disorders: A Video-Based Case Series of 11 Patients.

European neurology
2021

Serum Biomarkers in Neuro-Ophthalmology: When to Test.

Seminars in ophthalmology
2021

Immunotherapy responsive SARS-CoV-2 infection exacerbating opsoclonus myoclonus syndrome.

Multiple sclerosis and related disorders
2021

Opsoclonus After COVID-19 in an Infant.

Pediatric neurology
2021

Opsoclonus myoclonus syndrome in a postpartum period.

Multiple sclerosis and related disorders
2021

Opsoclonus-Myoclonus-Ataxia Syndrome (OMAS) Associated with SARS-CoV-2 Infection: Post-Infectious Neurological Complication with Benign Prognosis.

Tremor and other hyperkinetic movements (New York, N.Y.)
2021

Acute cerebellar ataxia and myoclonus with or without opsoclonus: a para-infectious syndrome associated with COVID-19.

European journal of neurology
2021

Opsoclonus-myoclonus syndrome, a post-infectious neurologic complication of COVID-19: case series and review of literature.

Journal of neurovirology
2021

Absence of GluD2 Antibodies in Patients With Opsoclonus-Myoclonus Syndrome.

Neurology
2021

Immune-Mediated Cerebellar Ataxias: Clinical Diagnosis and Treatment Based on Immunological and Physiological Mechanisms.

Journal of movement disorders
2021

Diagnostic values of 68Ga-labelled DOTANOC PET/CT imaging in pediatric patients presenting with paraneoplastic opsoclonus myoclonus ataxia syndrome.

European radiology
2020

Opsoclonus-myoclonus-ataxia syndrome associated with central nervous system HIV-1 escape phenomenon.

Revista de neurologia
2021

NK Cell-mediated Neuroblastoma Cell Lysis is Enhanced by IgG From Patients With Pediatric Opsoclonus-Myoclonus Syndrome.

Journal of pediatric hematology/oncology
2021

Opsoclonus Myoclonus Ataxia Syndrome in the Setting of COVID-19 Infection.

Neurology
2020

Factors influencing cognitive outcome in opsoclonus-myoclonus syndrome.

Developmental medicine and child neurology
2021

Opsoclonus-Myoclonus-Ataxia Syndrome Related to the Novel Coronavirus (COVID-19).

Journal of neuro-ophthalmology : the official journal of the North American Neuro-Ophthalmology Society
2020

Evolving Cognitive Dysfunction in Children with Neurologically Stable Opsoclonus-Myoclonus Syndrome.

Children (Basel, Switzerland)
2020

The Treatment of Opsoclonus-Myoclonus Syndrome Secondary to Neuroblastic Tumours-Single-Centre Experience and Literature Review.

Medicina (Kaunas, Lithuania)
2020

An unusual case of opsoclonus-myoclonus-ataxia syndrome associated neuroblastoma: High-risk disease requiring immunotherapy.

Pediatric blood &amp; cancer
2020

IQ predictors in pediatric opsoclonus myoclonus syndrome: a large international cohort study.

Developmental medicine and child neurology
2021

Opsoclonus-myoclonus syndrome secondary to duloxetine poisoning.

Neurologia
2020

Clinical Reasoning: An adolescent girl presenting with worsening vertigo, headache, and ataxia.

Neurology
2020

[Virus-induced opsoclonus-myoclonus syndrome during pregnancy].

Zhurnal nevrologii i psikhiatrii imeni S.S. Korsakova
2020

A rare case of Opsoclonus-Myoclonus associated with SCLC.

Acta neurologica Belgica
2020

Serum IgG-induced microglial activation enhances neuronal cytolysis via the NO/sGC/PKG pathway in children with opsoclonus-myoclonus syndrome and neuroblastoma.

Journal of neuroinflammation
2020

Treatment and revaccination of children with paraneoplastic opsoclonus-myoclonus-ataxia syndrome and neuroblastoma: The Memorial Sloan Kettering experience.

Pediatric blood &amp; cancer
2020

Anti-Ri-associated paraneoplastic ophthalmoplegia-ataxia syndrome in a woman with breast cancer: a case report and review of the literature.

Journal of medical case reports
2020

Paraneoplastic opsoclonus myoclonus syndrome associated with inflammatory myofibroblastic tumor in a pediatric patient.

Pediatric blood &amp; cancer
2020

Tumors masquerading as neurological diseases: A caution for clinicians in planning diagnosis and treatment.

Neurology India
2020

Dancing eyes syndrome from West Nile virus encephalitis.

Postgraduate medical journal
2020

Opsoclonus-myoclonus as a presentation of post-malaria neurological syndrome.

Journal of travel medicine
2020

Clinical Reasoning: A 16-year-old girl with ataxia, oscillopsia, and behavioral changes.

Neurology
2021

Opsoclonus-myoclonus syndrome associated with herpes simplex virus infection: a case report.

The International journal of neuroscience
2020

[Opsoclonus-myoclonus syndrome: Experience in a tertiary hospital in the last 12 years].

Anales de pediatria
2020

Neurological complications of pediatric cancer.

Cancer metastasis reviews
2020

Paraneoplastic opsoclonus-myoclonus syndrome in a patient with oesophageal adenocarcinoma.

Neurologia
2020

Therapeutic results in three cases of ganglioneuroblastoma associated with opsoclonus myoclonus ataxia syndrome.

Indian journal of cancer
2020

Pediatric whole body MRI detects causative ovarian teratoma in opsoclonus myoclonus syndrome.

Radiology case reports
2020

Serial change of opsoclonus associated with Mycoplasma pneumoniae infection.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology
2019

Paraneoplastic opsoclonus-myoclonus syndrome as a presentation of high grade serous ovarian cancer.

Gynecologic oncology reports
2019

[Opsoclonus myoclonus syndrome secondary to abdominal neuroblastoma. Presentation of a pediatric clinical case].

Archivos argentinos de pediatria
2019

Paraneoplastic opsoclonus-myoclonus syndrome secondary to melanoma metastasis form occult primary cancer.

Case reports in neurology
2019

Neurovascular compression syndrome of the brain stem with opsoclonus-myoclonus syndrome combined with vestibular paroxysmia and autonomic symptoms.

Drug discoveries &amp; therapeutics
2019

Childhood-onset cerebellar ataxia in Japan: A questionnaire-based survey.

Brain and behavior
2019

Diagnostic value of whole-body MRI in Opsoclonus-myoclonus syndrome: a clinical case series (3 case reports).

BMC medical imaging
2019

Clinical Profile, Prognostic Indicators, and Therapeutic Outcomes of Pediatric Opsoclonus-Myoclonus-Ataxia Syndrome: A Single-Center Experience from South India.

Annals of Indian Academy of Neurology
2019

[Neurological complications associated with dengue virus infection].

Revista de neurologia
2019

Paraneoplastic Opsoclonus Myoclonus in a Patient with Pancreatic Adenocarcinoma.

Case reports in neurological medicine
Ver todos os 329 no EuropePMC

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Referências e fontes

Bases de dados externas citadas neste artigo

Publicações científicas

Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.

  1. Neuroblastoma-associated opsoclonus-myoclonus-ataxia syndrome: an important yet overlooked diagnosis in pediatric ataxia.
    The Turkish journal of pediatrics· 2026· PMID 41871563mais citado
  2. HLA and T-Cell Receptor Investigations in Idiopathic and Paraneoplastic Opsoclonus-Myoclonus in Children.
    Neurology(R) neuroimmunology &amp; neuroinflammation· 2026· PMID 41499722mais citado
  3. Opsoclonus-myoclonus syndrome with anti-SOX1 antibodies.
    BMJ case reports· 2026· PMID 41629114mais citado
  4. High Expression of CCL2 Correlated With Dendritic Cell Recruitment in Neuroblastomas Associated With Opsoclonus-Myoclonus Syndrome.
    Laboratory investigation; a journal of technical methods and pathology· 2026· PMID 41270903mais citado
  5. Prolonged Diagnostic Latency and Long-term Surveillance in Anti-Ri Antibody-positive Opsoclonus-myoclonus Syndrome with Carcinoma of Unknown Primary.
    Internal medicine (Tokyo, Japan)· 2026· PMID 41093557mais citado
  6. Ophthalmological manifestations of neuroblastoma - A retrospective multicenter study.
    Pediatr Hematol Oncol· 2026· PMID 41979173recente
  7. CCL2: A double-edged sword in neuroblastoma, with a critical role in MYCN-amplified tumors.
    Transl Oncol· 2026· PMID 41936749recente
  8. Clinical features of paraneoplastic neurologic syndromes with anti-Ri antibodies: PRISMA systematic review.
    J Neurol· 2026· PMID 41894019recente

Bases de dados e fontes oficiais

Identificadores e referências canônicas usadas para montar este verbete.

  1. ORPHA:1183(Orphanet)
  2. MONDO:0015247(MONDO)
  3. GARD:10009(GARD (NIH))
  4. Busca completa no PubMed(PubMed)
  5. Artigo Wikipedia(Wikipedia)
  6. Q1424706(Wikidata)

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Síndrome de opsoclonia-mioclonia
Compêndio · Raras BR

Síndrome de opsoclonia-mioclonia

ORPHA:1183 · MONDO:0015247
Prevalência
Unknown
Herança
Not applicable
CID-10
G25.3 · Mioclonia
CID-11
Ensaios
1 ativos
Início
Childhood, Infancy
Prevalência
0.0 (Worldwide)
MedGen
UMLS
C0393626
EuropePMC
Wikidata
Wikipedia
Papers 10a
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