Papillon-Lefèvre syndrome with excellent response to risankizumab.

Differences in Inflammatory Genetic Profiles in Periodontitis Associated with Genetic and Immunological Disorders: A Systematic Review.

Atypical Presentation of Papillon-Lefèvre Syndrome: A Case of Isolated Cutaneous Manifestations Without Dental Involvement.

Papillon-Lefèvre Syndrome: Case Report of Two Sisters.

Papillon-Lefèvre Syndrome Unmasked by Atypical Cat Scratch Disease.

Periodontal Manifestations of Systemic Diseases.

Dipeptidyl peptidase 1 inhibitors for inflammatory respiratory diseases: mechanisms, clinical trials, and therapeutic prospects.

Clinical characteristics of Papillon-Lefèvre syndrome: A KSA perspective.

Secukinumab and Upadacitinib Treatment for Papillon-Lefèvre Syndrome in 2 Cases.

Inhibition of CTSC contributes to psoriasis inflammation and keratinocyte hyperproliferation by NF-κB signaling pathway.

Triangular Lunulae in Papillon-Lefèvre Syndrome: A Case Report.

Dental management of a young patient with Papillon-Lefèvre syndrome.

Papillon-Lefèvre syndrome: palmoplantar keratoderma with teeth abnormalities.

Papillon-Lefevre syndrome: Case series.

A Japanese case of Papillon-Lefèvre syndrome diagnosed by pyogenic liver abscess.

The di-leucine motif in the host defense peptide LL-37 is essential for initiation of autophagy in human macrophages.

Pharmacological inhibition of cathepsin S and of NSPs-AAP-1 (a novel, alternative protease driving the activation of neutrophil serine proteases).

Cathepsin C in health and disease: from structural insights to therapeutic prospects.

Skeletal indicators of pathology in the context of early tooth loss in children: A systematic literature review.

Papillon-Lefèvre syndrome in dental pediatric patient: A comprehensive review.

Self-reported clinical features and treatment effectiveness of Papillon-Lefèvre syndrome patients from five Latin American countries: A cross-sectional online survey study.

The oral microbiome of a family including Papillon-Lefèvre-syndrome patients and clinically healthy members.

Papillon-Lefevre syndrome in twelve Egyptian patients: Five novel CTSC variants and functional characterization of a missense variant and its effect on splicing.

Recalcitrant skin ulcers in a patient with Papillon-Lefèvre syndrome: an unusual novel presentation.

Identification of a novel frameshift mutation in cathepsin C gene in a patient with coexisting Papillon-Lefevre syndrome and rheumatoid arthritis.

Role of the NLRP1 inflammasome in skin cancer and inflammatory skin diseases.

Cathepsin C role in inflammatory gastroenterological, renal, rheumatic, and pulmonary disorders.

Possible relation of cathepsin C activity and seasonal fluctuation of skin lesions in Papillon-Lefèvre syndrome.

Diagnosis and Management of Papillon-Lefevre Syndrome: A Rare Case Report and a Brief Review of Literature.

Recent developments in the diagnosis, treatment, and management of Papillon-Lefèvre Syndrome.

Oral Rehabilitation of a Patient with Papillon Lefèvre Syndrome Using Fixed Full-Arch Hybrid Prostheses Supported by Four Axially Loaded Implants: A Case Report with Four-Year Follow-up.

Multidisciplinary management of Papillon-Lefevre syndrome as a result of consanguineous marriage.

Subsiding of Periodontitis in the Permanent Dentition in Individuals with Papillon-Lefèvre Syndrome through Specific Periodontal Treatment: A Systematic Review.

Oral Juvenile Xanthogranuloma: a case report of gingival hyperplasia and osteolysis in male adult patient.

Dimethyl fumarate for treating Papillon-Lefèvre syndrome.

Case report: Corticosteroids as an adjunct treatment for the management of liver abscess in Papillon-Lefèvre syndrome: A report on two cases.

Abnormal profiles of cathepsin C secreted in urine of Papillon Lefevre syndrome patients.

Papillon-Lefévre Syndrome: A Rare Case Report and a Brief Review of Literature.

Fixed prosthetic rehabilitation of a patient with Papillon-Lefevre syndrome supported by a Quad Zygoma Approach: A clinical report.

Long-Term Results after Placing Dental Implants in Patients with Papillon-Lefèvre Syndrome: Results 2.5-20 Years after Implant Insertion.

Premature Loss of Deciduous Teeth as a Symptom of Systemic Disease: A Narrative Literature Review.

Targeting Cathepsin C in PR3-ANCA Vasculitis.

A rare CTSC mutation in Papillon-Lefèvre Syndrome results in abolished serine protease activity and reduced NET formation but otherwise normal neutrophil function.

Papillon-Lefevre syndrome treated by acitretin: case report and cytokine profile.

The first case report of Haim Munk disease with neurological manifestations and literature review.

Oral Phenotype and Salivary Microbiome of Individuals With Papillon-Lefèvre Syndrome.

Novel Compound Heterozygous Mutations in CTSC Gene in a Chinese Family with Papillon-Lefevre Syndrome.

Survival Rates of Dental Implants in Patients with Papillon-Lefévre Syndrome: A Systematic Review.

A novel mutation in the cathepsin C (CTSC) gene in Iranian family with Papillon-Lefevre syndrome.

Two patients with Papillon-Lefèvre syndrome without periodontal involvement of the permanent dentition.

Potential Role of the Mitochondria for the Dermatological Treatment of Papillon-Lefèvre.

Diagnosis of Papillon-Lefèvre syndrome: review of the literature and a case report.

Dental prosthetic rehabilitation of Papillon-Lefèvre syndrome: a case report.

Oral rehabilitation of Papillon-Lefèvre syndrome patients by dental implants: a systematic review.

Cathepsin G and its Dichotomous Role in Modulating Levels of MHC Class I Molecules.

Lung Protection by Cathepsin C Inhibition: A New Hope for COVID-19 and ARDS?

Papillon-Lefèvre syndrome (PLS) with novel compound heterozygous mutation in the exclusion and Peptidase C1A domains of Cathepsin C gene.

Japanese case of Papillon-Lefèvre syndrome with novel compound heterozygous mutations.

Papillon-Lefèvre syndrome: Oral aspects and treatment.

Missense Mutations in the CTSC Gene in Saudi Families Segregating Papillon-Lefèvre Syndrome.

A Mutation in Cathepsin C Gene Causing Papillon-Lefèvre Syndrome in a Saudi Patient: A Case Report.

Identification of putative genetic modifying factors that influence the development of Papillon-Lefévre or Haim-Munk syndrome phenotypes.

Papillon Lefevre Syndrome.

Palmoplantar keratoderma, oral involvement, and homozygous CTSC mutation in two brothers from Cambodia.

A New Terminal Nonsense Mutation of the Cathepsin C Gene in a Patient With Atypical Papillon-Lefèvre Syndrome.

Cu-sil dentures: A novel approach of Papillon-Lefèvre syndrome management.

Digital prosthodontic management of a young patient with Papillon-Lefèvre syndrome: A clinical report.

Clinical and molecular analysis in Papillon-Lefèvre syndrome.

Papillon-Lefèvre Syndrome and Basal Cell Carcinoma: A Case Study.

Papillon-Lefèvre Syndrome: Diagnosis, Dental Management, and a Case Report.

Exome sequencing identifies a novel missense variant in CTSC causing nonsyndromic aggressive periodontitis.

CTSC compound heterozygous mutations in two Chinese patients with Papillon-Lefèvre syndrome.

[Gene mutational analyses of cathepsin C gene in a family with Papillon-Lefèvre syndrome].

Papillon-Lefèvre Syndrome: A Rare Case Report of Two Brothers and Review of the Literature.

Case Report: Clinical manifestation and dental management of Papillon-Lefèvre syndrome.

[Papillon-Lefevre syndrome complicated with liver abscess].

Papillon-Lefèvre syndrome.

Aggregated neutrophil extracellular traps resolve inflammation by proteolysis of cytokines and chemokines and protection from antiproteases.

A Rare Presentation of Psychotic Depression with Suicidality in a Case of Papillon-Lefèvre Syndrome.

Periodontal manifestations of systemic diseases and developmental and acquired conditions: Consensus report of workgroup 3 of the 2017 World Workshop on the Classification of Periodontal and Peri-Implant Diseases and Conditions.

Consequences of cathepsin C inactivation for membrane exposure of proteinase 3, the target antigen in autoimmune vasculitis.

Therapeutic targeting of cathepsin C: from pathophysiology to treatment.

Papillon-Lefevre Syndrome: A case report.

Autophagic dysfunction in patients with Papillon-Lefèvre syndrome is restored by recombinant cathepsin C treatment.

A Highlighted Case for Emphasizing on Clinical Diagnosis for Rare Syndrome in Third World.

Could Congenital Insensitivity to Pain with Anhidrosis Be Misdiagnosed as Papillon-Lefèvre Syndrome?

Full-Mouth Rehabilitation with Calvarium Bone Grafts and Dental Implants for a Papillon-Lefèvre Syndrome Patient: Case Report.

Janus-Faced Neutrophil Extracellular Traps in Periodontitis.

Papillon-Lefèvre syndrome: A series of three cases in the same family and a literature review.

Anesthesia Management of a Patient with Papillon-Lefevre Syndrome: A Case Report.

Ocular Surface Squamous Neoplasia in Papillon-Lefèvre Syndrome: Outcome at Long-Term Follow-Up of 12 Years.

Phenol-Soluble Modulin α Peptide Toxins from Aggressive Staphylococcus aureus Induce Rapid Formation of Neutrophil Extracellular Traps through a Reactive Oxygen Species-Independent Pathway.

[Gene mutational analyses of the cathepsin C gene in families with Papillon-Lefèvre syndrome].

[Papillon-Lefèvre syndrome: A new case].

Prolonged pharmacological inhibition of cathepsin C results in elimination of neutrophil serine proteases.

Oro-dental characteristics of three siblings with Papillon-Lefevre syndrome.

Inherited diseases caused by mutations in cathepsin protease genes.

Papillon-Lefevre Syndrome: Prosthodontic Rehabilitation of Oral Function.

Stimulus-dependent NETosis by neutrophils from a Papillon-Lefèvre Syndrome patient.

Papillon-Lefèvre syndrome: a series of five cases among siblings.

Whole-exome sequencing reveals a recurrent mutation in the cathepsin C gene that causes Papillon-Lefevre syndrome in a Saudi family.

[Oral status of a child with Papillon-Lefevre syndrome: over 10-year follow-up].

Primary immunodeficiencies associated with eosinophilia.

Papillon-Lefèvre syndrome: report of six patients and identification of a novel mutation.

[Screening of CTSC gene mutations in a Chinese pedigree affected with Papillon-Lefevre syndrome].

Characterization of neutrophil function in Papillon-Lefèvre syndrome.

Papillon-Lèfevre syndrome with palmoplantar keratoderma and periodontitis, a rare cause of pyrexia of unknown origin: a case report.

Analysis of urinary cathepsin C for diagnosing Papillon-Lefèvre syndrome.

A novel large deletion combined with a nonsense mutation in a Chinese child with Papillon-Lefèvre syndrome.

Periodontal Manifestations of Chronic Atypical Neutrophilic Dermatosis With Lipodystrophy and Elevated Temperature (CANDLE) Syndrome in an 11-Year-Old Patient.

Combined orthodontic and periodontic treatment in a child with Papillon Lefèvre syndrome.

One mutation, two phenotypes: a single nonsense mutation of the CTSC gene causes two clinically distinct phenotypes.

Papillon-Lefèvre syndrome: clinical presentation and management options.

Papillon-Lefevre Syndrome In An Adolescent Female: A Case Study.

Processing of Neutrophil α-Defensins Does Not Rely on Serine Proteases In Vivo.

Papillon-lefevre syndrome: review of literature and report of three cases in the same family.

Proxy molecular diagnosis from whole-exome sequencing reveals Papillon-Lefevre syndrome caused by a missense mutation in CTSC.