Raras
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Tumor de células germinativas extragonadal
ORPHA:363579DOENÇA RARA

Um tumor de células germinativas que surge em um local do corpo diferente dos testículos ou ovários (por exemplo, no sistema nervoso central, pulmão, mediastino e retroperitônio).

Mantido por Agente Raras·Colaborar como especialista →

Introdução

O que você precisa saber de cara

📋

Um tumor de células germinativas que surge em um local do corpo diferente dos testículos ou ovários (por exemplo, no sistema nervoso central, pulmão, mediastino e retroperitônio).

Publicações científicas
234 artigos
Último publicado: 2026 Mar-Apr

Escala de raridade

CLASSIFICAÇÃO ORPHANET · BRASIL 2024
1-9 / 1 000 000
Ultra-rara
<1/50k
Muito rara
1/20k
Rara
1/10k
Pouco freq.
1/5k
Incomum
1/2k
Prevalência
0.13
Europe
🏥
SUS: Sem cobertura SUSScore: 0%
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Entender a doença

Do básico ao detalhe, leia no seu ritmo

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Sinais e sintomas

O que aparece no corpo e com que frequência cada sintoma acontece

Partes do corpo afetadas

🫃
Digestivo
4 sintomas
📏
Crescimento
4 sintomas
🦴
Ossos e articulações
2 sintomas
🧠
Neurológico
2 sintomas
👁️
Olhos
1 sintomas
🩸
Sangue
1 sintomas

+ 17 sintomas em outras categorias

Características mais comuns

Diplopia
Teratoma
Morfologia anormal do abdome
Poliúria
Hemiparesia
Nistagmo
31sintomas
Sem dados (31)

Os sintomas variam de pessoa para pessoa. Abaixo estão as 31 características clínicas mais associadas, ordenadas por frequência.

Diplopia
Teratoma
Morfologia anormal do abdomeAbnormality of abdomen morphology
PoliúriaPolyuria
HemiparesiaHemiparesis

Linha do tempo da pesquisa

Publicações por ano — veja quando o interesse científico cresceu
Anos de pesquisa1desde 2026
Total histórico234PubMed
Últimos 10 anos111publicações
Pico202116 papers
Linha do tempo
2026Hoje · 2026🧪 1989Primeiro ensaio clínico📈 2021Ano de pico
Publicações por ano (últimos 10 anos)

Encontrou um erro ou informação desatualizada? Sugira uma correção →

Genética e causas

O que está alterado no DNA e como passa nas famílias

Genes associados

1 gene identificado com associação a esta condição.

JMJD1CJumonji domain-containing protein 1CCandidate gene tested inAltamente restrito
FUNÇÃO

Demethylates lysine in proteins, such as STAT3 or MDC1 (By similarity) (PubMed:24240613). Demethylates MDC1, thereby promoting MDC1-RNF8 interaction and facilitating RNF8-dependent MDC1 ubiquitination essential for double-strand break (DSB) repair (PubMed:24240613). Demethylation of STAT3 at 'Lys-140' facilitates its interactions with the phosphatase PTPN6 and restrains STAT3 activation (By similarity). It is uncertain whether JMJD1C removes methyl groups from histone proteins as the other JMJD1

LOCALIZAÇÃO

Nucleus

VIAS BIOLÓGICAS (1)
Factors involved in megakaryocyte development and platelet production
EXPRESSÃO TECIDUAL(Ubíquo)
Cerebelo
55.1 TPM
Cérebro - Hemisfério cerebelar
48.8 TPM
Cervix Endocervix
30.5 TPM
Linfócitos
30.3 TPM
Útero
29.5 TPM
OUTRAS DOENÇAS (2)
22q11.2 deletion syndromepineal region germinoma
HGNC:12313UniProt:Q15652

Variantes genéticas (ClinVar)

40 variantes patogênicas registradas no ClinVar.

🧬 JMJD1C: NM_032776.3(JMJD1C):c.103C>G (p.Arg35Gly) ()
🧬 JMJD1C: NM_032776.3(JMJD1C):c.6077-9C>G ()
🧬 JMJD1C: NM_032776.3(JMJD1C):c.6740-1del ()
🧬 JMJD1C: NM_032776.3(JMJD1C):c.5644+4G>A ()
🧬 JMJD1C: NM_032776.3(JMJD1C):c.1320T>G (p.Asp440Glu) ()
Ver todas no ClinVar

Vias biológicas (Reactome)

1 via biológica associada aos genes desta condição.

Diagnóstico

Os sinais que médicos procuram e os exames que confirmam

Carregando...

Tratamento e manejo

Remédios, cuidados de apoio e o que precisa acompanhar

Pipeline de tratamentos
Pipeline regulatório — de medicamentos já aprovados a drogas em pesquisa exploratória.
3Fase 35
2Fase 212
1Fase 13
Medicamentos catalogadosEnsaios clínicos· 0 medicamentos · 20 ensaios
Carregando informações de tratamento...

Onde tratar no SUS

Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

🇧🇷 Atendimento SUS — Tumor de células germinativas extragonadal

🗺️

Selecione um estado ou use sua localização para ver resultados.

Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.

Pesquisa ativa

Ensaios clínicos abertos e novidades científicas recentes

Pesquisa e ensaios clínicos

57 ensaios clínicos encontrados.

Distribuição por fase
NCT06940804 · A Clinical Study Investigating the Therapeutic Effects and S…Cancelado
PHASE2
NCT00638898 · Busulfan, Melphalan, Topotecan Hydrochloride, and a Stem Cel…Concluído
PHASE1
NCT00104676 · Combination Chemotherapy in Treating Patients With Stage II …Concluído
PHASE3
NCT00716976 · Sodium Thiosulfate in Preventing Hearing Loss in Young Patie…Concluído
PHASE3
NCT00788125 · Dasatinib, Ifosfamide, Carboplatin, and Etoposide in Treatin…Encerrado
PHASE1, PHASE2
NCT00432094 · Autologous Peripheral Blood Stem Cell Transplant for Germ Ce…Concluído
PHASE2
NCT00053352 · Surgery and Combination Chemotherapy in Treating Children Wi…Concluído
PHASE3
NCT01037790 · Phase II Trial of the Cyclin-Dependent Kinase Inhibitor PD 0…Concluído
PHASE2
NCT00002566 · Combination Chemotherapy With Bone Marrow Transplantation in…Concluído
PHASE3
NCT00007813 · Peripheral Stem Cell Transplantation Plus Chemotherapy in Tr…Concluído
PHASE1
NCT00002943 · Carboplatin, Etoposide, Cyclophosphamide, and Autologous Bon…Concluído
PHASE2
NCT00003926 · Amifostine to Protect From Side Effects of PSCT in Treating …Encerrado
PHASE1
NCT00470366 · Combination Chemotherapy and Pegfilgrastim in Treating Patie…Concluído
PHASE2
NCT00957905 · Alvocidib and Oxaliplatin With or Without Fluorouracil and L…Concluído
PHASE2
NCT00002931 · Combination Chemotherapy Plus Peripheral Stem Cell Transplan…Concluído
PHASE2
NCT00003657 · High-dose ICE With AmifostineConcluído
PHASE2
NCT00072215 · Cisplatin and Ifosfamide Combined With Either Paclitaxel or …Encerrado
PHASE3
NCT00003852 · Combination Chemotherapy Plus Peripheral Stem Cell Transplan…Encerrado
PHASE2
NCT00002558 · Combination Chemotherapy Plus Peripheral Stem Cell Transplan…Concluído
PHASE1, PHASE2
NCT00423852 · Paclitaxel, Ifosfamide, and Carboplatin Followed By Autologo…Concluído
PHASE1, PHASE2
Ver todos no ClinicalTrials.gov
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Publicações mais relevantes

🥉Melhor nível de evidência: Relato de caso
Timeline de publicações
114 papers (10 anos)
#1

Extracranial, Extragonadal Germ Cell Tumors: A Multicenter Australian Case Series.

Asia-Pacific journal of clinical oncology2026 Jan 29

To describe the treatment pattern and outcomes for patients with extracranial, extragonadal germ cell tumors (EGCTs). We conducted a retrospective analysis of male patients with EGCT prospectively registered in the Australian GCT clinical registry (iTestis) since its inception in 2018. Demographics, clinicopathologic features, treatment characteristics, and outcomes were recorded. Data were analyzed using descriptive statistics and the Kaplan-Meier method estimates of overall survival (OS). Of 1256 patients in the iTestis registry, 33 (3%) had EGCT including 18 (55%) with mediastinal, 14 (42%) with retroperitoneal, and 1 (3%) with a lung primary. The median age was 31 years (range: 24-38), ECOG performance status was 0-1 in 26 (79%), and 21 (64%) were non-seminoma. Chemotherapy was administered upfront in 27 (82%) patients, upfront surgery in four patients (12%), and treatment was unknown in two (6%) patients. The most common chemotherapy regimen was bleomycin/etoposide/cisplatin (BEP) (n = 20, 74%), followed by etoposide/ifosfamide/cisplatin (VIP) (n = 5, 19%) and EP (n = 2, 7%). Post-chemotherapy surgery was carried out in 16 (59%) patients, and 4 (15%) patients received second-line chemotherapy. At a median follow-up of 22.7 months (range: 0-126), no deaths were observed in individuals with retroperitoneal primary (n = 14), seminoma (n = 12), or International Germ Cell Cancer Collaborative Group (IGCCCG) good (n = 15) and intermediate risk (n = 3) disease. Three deaths occurred in patients with mediastinal non-seminoma. The estimated 24-month OS for mediastinal non-seminoma and IGCCCG poor risk disease was 71% (95% confidence interval [CI]: 27%-94%) and 79% (95% CI: 25%-95%), respectively. Incidence of EGCT in Australia is consistent with published literature. Treatment patterns reflect international practices. Primary mediastinal non-seminoma has the poorest outcomes. Primary retroperitoneal and primary mediastinal seminomas have excellent outcomes.

#2

Minimally Invasive Approach of Bile Duct Stricture after Laparoscopic Hepatectomy.

Journal of laparoendoscopic &amp; advanced surgical techniques. Part A2026 Feb 09

Extragonadal germ cell tumors in pediatric patients are rare, accounting for approximately 10 to 15% of all germ cell tumors. High-risk chemotherapy followed by surgical resection represents the standard of care. Post-hepatectomy biliary complications, such as hepatic duct stenosis, constitute a relevant clinical challenge. We present the case of a 10-year-old pediatric patient with a retroperitoneal and mediastinal extragonadal germ cell tumor treated with high-risk chemotherapy according to the GALOP 2017 protocol and multiple surgical procedures, including laparoscopic atypical left hepatectomy for residual disease. The patient subsequently developed stenosis of the main hepatic duct. Percutaneous biliary drainage and balloon cholangioplasty were performed, successfully restoring biliary patency and normalizing liver function tests, without immediate complications. Post-hepatectomy biliary complications in pediatric patients, although uncommon, may be related to mechanical trauma or metallic clip placement. Percutaneous management is effective and safe, allowing avoidance of open reintervention. Multidisciplinary planning is essential to optimize outcomes in high-risk pediatric germ cell tumors. Post-hepatectomy biliary stenosis should be considered in pediatric patients presenting with jaundice and cholestasis. Percutaneous management of biliary complications is a safe and effective alternative, highlighting the importance of early intervention and close follow-up to preserve liver function.

#3

Rectal adenocarcinoma with a yolk sac tumor component: A rare case report and review of the literature.

International cancer conference journal2026 Jan

Yolk sac tumor (YST) occurs primarily in the gonads but rarely outside the gonads. They typically arise in the midline location, and there are only a few reports describing the colon and rectum as the primary sites of YST. Additionally, colorectal cancers containing YST-like components are rare, and in other organs, including the stomach, it is more common to describe such lesions as " yolk sac tumor-like carcinoma". Here, we report a case of colorectal adenocarcinoma with a YST-like component arising in the rectum. This is the seventh reported case of colorectal YST-like carcinoma. A 66-year-old man presented to our hospital with the chief complaint of anal bleeding. Colonoscopy revealed a 25 × 20 mm tumor located 5 cm above the anal verge. Biopsy results showed moderately differentiated tubular adenocarcinoma, cT3, cN2b, cM0, and cStage IIIC (UICC 8th edition). Subsequently, a laparoscopic abdominoperineal resection was performed. A histopathological examination of the resected specimen revealed findings of adenocarcinoma and YST-like component. Immunostaining for mismatch repair proteins revealed no abnormalities. The tumor was positive for the KRAS G12S mutation, and negative for the BRAF mutation. The overall diagnosis was adenocarcinoma with a YST-like component, pT3, pN2a, cM0, and pStage IIIB (UICC 8th edition). Six months after the surgery, metastasis was found in the liver, but at the request of the patient and their family, the decision was made not to undergo any aggressive treatment. We describe the clinical and pathological features of colorectal YST-like carcinoma that aid in its accurate diagnosis and provide treatment suggestions.

#4

A rare entity in the retroperitoneum: Case report of a primary seminoma.

Urology case reports2026 Mar

Primary retroperitoneal seminoma is an extremely rare extragonadal germ cell tumor. A 61-year-old male was referred following the discovery of a retroperitoneal mass on routine physical examination. Computed tomography and PET-CT revealed a soft-tissue nodule near the left renal hilum, suggestive of a neoplasm. The patient underwent surgical resection, and histopathology confirmed seminoma. Scrotal ultrasound showed no testicular abnormalities, thereby excluding a metastatic origin and confirming the diagnosis of primary retroperitoneal seminoma. This case underscores the importance of considering this rare entity in the differential diagnosis of retroperitoneal masses.

#5

Hepatoduodenal ligament teratoma presenting with fever in a young adult.

Journal of surgical case reports2026 Jan

Hepatoduodenal ligament teratomas are very rare, and there are fewer than 20 cases reported in the literature. A 22-year-old woman with fever and acute abdominal pain due a mature cystic teratoma in the hepatoduodenal ligament. This occurrence when presented with acute cholangitis was the first case of this rare tumor. Previous cases seen in adults were asymptomatic and were diagnosed incidentally on investigations. The mass was successfully removed operation on this patient without affecting the portal triad structures. This case adds to our knowledge of how these rare tumors may present clinically. It also highlights the relevance of this diagnosis in young adults with acute febrile illness and appropriate imaging characteristics.

Publicações recentes

Ver todas no PubMed

📚 EuropePMC88 artigos no totalmostrando 111

2025

Survival outcomes and prognostic factors of extragonadal germ cell tumors: An institutional experience over a decade.

The Gulf journal of oncology
2026

Minimally Invasive Approach of Bile Duct Stricture after Laparoscopic Hepatectomy.

Journal of laparoendoscopic &amp; advanced surgical techniques. Part A
2026

Extracranial, Extragonadal Germ Cell Tumors: A Multicenter Australian Case Series.

Asia-Pacific journal of clinical oncology
2026

Rectal adenocarcinoma with a yolk sac tumor component: A rare case report and review of the literature.

International cancer conference journal
2026

A rare entity in the retroperitoneum: Case report of a primary seminoma.

Urology case reports
2025

Histopathologic diagnosis of mediastinal seminoma in a low-resource setting: A case report on navigating limited access to molecular testing.

International journal of surgery case reports
2026

Hepatoduodenal ligament teratoma presenting with fever in a young adult.

Journal of surgical case reports
2026

Extragonadal yolk sac tumor of the ureter with neuroendocrine differentiation: A case report.

Urology case reports
2025

Application of Negative Pressure Wound Therapy in Neonatal Bone-Exposed Wounds: Nursing Interventions and Clinical Outcomes.

Nursing in critical care
2025

Gross hematuria secondary to vesicular varices: an unusual long-term sequela of inferior vena cava ligation and resection case report.

Urology case reports
2025

Fetal sacrococcygeal immature teratoma: a case report and a literature review.

BMC pediatrics
2025

A endometrial malignant tumor with yolk sac tumor component: a case report and literature review.

Frontiers in oncology
2025

Primary Mediastinal Germ Cell Tumor With Bone Marrow Infiltration: A Case Report and Literature Review.

Cancer reports (Hoboken, N.J.)
2025

Extragonadal Urinary Tract Neoplasms With Yolk Sac Differentiation: Clinical, Histologic, and Molecular Evidence of Derivation From Underlying Urothelial Carcinoma.

Modern pathology : an official journal of the United States and Canadian Academy of Pathology, Inc
2025

Pulmonary teratoma masquerading as aspergilloma.

Indian journal of thoracic and cardiovascular surgery
2024

[A Case of Metastatic Extragonadal Germ Cell Tumor Treated by Surgical Resection after Chemotherapy and Follow-Up Time : A Case Report].

Hinyokika kiyo. Acta urologica Japonica
2024

Primary Retroperitoneal Seminoma-An Uncommon Presentation With Significant Implications.

Case reports in surgery
2024

A rare case of huge intracranial yolk sac tumor presenting as an orbital mass in an infant: case report and literature review.

Discover oncology
2024

Early Outcomes of the Surgical Treatment of Sacrococcygeal Tumors in a Tertiary Level Government Hospital.

Acta medica Philippina
2024

Primary mediastinal choriocarcinoma in a woman treated with VIP therapy instead of BEP therapy for the prevention of postoperative acute respiratory distress syndrome.

International cancer conference journal
2024

Primary Nonseminomatous Germ Cell Tumor of Kidney: An Uncommon Renal Neoplasm.

Journal of kidney cancer and VHL
2024

Diagnosis and management of a sacrococcygeal teratoma at a tertiary hospital in northern Tanzania: A case report.

International journal of surgery case reports
2024

Mediastinal Mature Cystic Teratoma With Intrapulmonary Extension Mimicking a Hydatid Cyst: Advantages of MRI in Diagnostics.

Cureus
2024

Extragonadal Germ Cell Tumor with Hepatic Infiltration in a Child: Aberrant Somatostatin Receptors and the Diagnostic Conundrum.

Journal of Indian Association of Pediatric Surgeons
2024

Spontaneous rupture‑induced life‑threatening mediastinal mixed germ cell tumor: A case report and therapeutic considerations.

Oncology letters
2024

Primary Yolk Sac Tumor of the Liver: A Rare Cause of Bile Duct Obstruction.

Case reports in gastrointestinal medicine
2024

Extragonadal germ-cell tumor presenting initially as a massive abdominal mass: A case report.

Asian journal of surgery
2024

Pulsatile giant sacrococcygeal teratoma appearing like 2nd head.

Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery
2023

Primary Undifferentiated Neoplasm of the Left Arm with Characteristics of Extragonadal Germ Cell Tumor and High-Grade Sarcoma.

Clinical oncology, case reports
2023

A Rare Case of Extragonadal Mixed Germ Cell Tumor of the Sacrococcygeal Region with Mature Thymic Tissue in the Teratoma Component.

Journal of Indian Association of Pediatric Surgeons
2023

Critical elements of pediatrics sacrococcygeal germ cell tumor surgery.

Seminars in pediatric surgery
2024

Extragonadal Germ Cell Tumors: A Single Institution Experience with Clinicopathological Correlation.

International journal of surgical pathology
2022

[Extragonadal germ cell tumor: A case report and review of the literature].

Zhonghua nan ke xue = National journal of andrology
2023

Analysis of microsatellite instability (MSI) in pediatric gonadal and extra-gonadal germ cell tumors.

Intractable &amp; rare diseases research
2023

Mediastinal seminoma in a pediatric patient managed with multi-modality treatment approach: A case report.

International journal of surgery case reports
2023

[A Case of Germ Cell Tumor in which Necrotic Tissue Revealed hCG-Positive in Surgical Specimen of Post-Chemotherapy Retroperitoneal Lymph Node Dissection].

Hinyokika kiyo. Acta urologica Japonica
2023

Case of extragonadal germ cell tumor mimicking left adrenal tumor.

Urology case reports
2023

Immune-related mechanisms and immunotherapy in extragonadal germ cell tumors.

Frontiers in immunology
2023

[Burned-out testicular germ cell tumors: a clinicopathological analysis of three cases].

Zhonghua bing li xue za zhi = Chinese journal of pathology
2023

A case of mediastinal teratoma with malignant transformation into angiosarcoma and relapse with multiple bone metastases that was cured by a multidisciplinary treatment.

IJU case reports
2024

Extragonadal germ cell tumor: A rare case in dorsal region.

Indian journal of cancer
2023

Upper gastrointestinal bleed as the initial presentation of seminoma involving the duodenum in an elderly patient with 9 year follow up: A case report and literature review.

Diagnostic cytopathology
2023

A Long-Term Outcome of the Patients with Sacrococcygeal Teratoma: A Bosnian Cohort.

Turkish archives of pediatrics
2023

Postoperative recurrence of mixed extragonadal germ cell tumor in the right shoulder: a case report.

Diagnostic pathology
2023

Case report: A unique case of benign teratoma in the posterior mediastinum associated with anterior meningomyelocele in a one-year-old child.

International journal of surgery case reports
2022

Yolk Sac Tumor of the Parotid Gland in a Child and its Differentials.

Journal of Indian Association of Pediatric Surgeons
2023

Teratoma of the Tongue in a Fetus: A Case Report and Review of the Literature.

Pediatric and developmental pathology : the official journal of the Society for Pediatric Pathology and the Paediatric Pathology Society
2022

Endodermal sinus tumor with pancreatic origin: A case report.

International journal of surgery case reports
2022

A Case of Sex Cord-Stromal Tumor Originating in the Retroperitoneal Space.

Cureus
2022

Posterior mediastinal teratoma presenting as an abdominal mass in a child: A case report.

Radiology case reports
2022

A 24-Year-Old Man Presenting with Lung Metastases from a Primary Retroperitoneal Extragonadal Choriocarcinoma.

The American journal of case reports
2022

An Unexpected Occurrence of Malignancy in a Patient After a Fontan Operation.

Cureus
2022

An Extremely Rare Case of a Primary Pancreatic Yolk Sac Tumor.

Cureus
2022

Yolk sac tumor presenting as a colonic mass in a post-menopausal woman: A case report.

Gynecologic oncology reports
2022

Early postoperative complications in pediatric abdominal solid tumor surgery according to Clavian-Dindo classification.

Pediatric surgery international
2022

Extragonadal mixed germ cell tumor of the seminal vesicle.

Indian journal of urology : IJU : journal of the Urological Society of India
2022

Retroperitoneal extragonadal germ cell tumor with duodenal infiltration: A challenging endo-luminal tissue diagnosis.

JGH open : an open access journal of gastroenterology and hepatology
2022

Gastric adenocarcinoma with germ cell tumor components: a rare case report.

The Journal of international medical research
2021

Cervical Cystic Teratoma: An Unusual Cause of Airway Obstruction in the Pediatric Population.

Cureus
2021

Uniportal video-assisted thoracoscopic surgery for complex mediastinal mature teratoma: A case report.

World journal of clinical cases
2022

18F-FDG PET/CT Findings in a Rare Case of Paraneoplastic Vestibulocerebellar Syndrome Associated With Isolated Antiamphiphysin Antibodies.

Clinical nuclear medicine
2021

A scoping review on the "burned out" or "burnt out" testicular cancer: When a rare phenomenon deserves more attention.

Critical reviews in oncology/hematology
2022

Cutaneous nonseminomatous mixed extragonadal germ cell tumor: a case report.

International journal of dermatology
2021

A presumed extragonadal germ cell tumor that turned out to be a gastric cancer-a case report.

Translational andrology and urology
2021

Pleural Effusion: A Rare Presentation of Mature Teratoma in a Young Patient.

Cureus
2021

Extragonadal germ cell tumor, a report of two cases presenting in the gastrointestinal tract.

Rare tumors
2021

To Be or Not to Be a Germ Cell: The Extragonadal Germ Cell Tumor Paradigm.

International journal of molecular sciences
2021

Laparoscopic Trachelectomy for Cervix Yolk Sac Tumor in 11-Month-Old Girl: The Youngest Case.

Journal of pediatric and adolescent gynecology
2021

A Case of Primary Mediastinal Seminoma Associated With Testicular Microlithiasis and Liver Injury.

Cureus
2021

Spontaneous regression of an extragonadal seminomatous germ cell tumor.

Cancer treatment and research communications
2021

Radiotherapy as a Single Modality in Primary Seminoma of the Prostate.

Cureus
2021

Sacrococcygeal Teratoma : A Tumor at the Center of Embryogenesis.

Journal of Korean Neurosurgical Society
2021

Yolk sac tumor of the endometrium in a post-menopausal woman: Case report and review of the literature.

Gynecologic oncology reports
2020

Primary Mediastinal Germ Cell Tumors-The University of Western Ontario Experience.

Current oncology (Toronto, Ont.)
2021

Mediastinal Germ Cell Tumor with Testicular Microlithiasis.

Cureus
2021

Late testicular relapse two decades after primary extragonadal germ cell tumor with uncommon metastases: a case report.

Journal of medical case reports
2021

[Pathological features of primary extragonadal germ cell tumor of the prostate with small round blue cell morphology].

Zhonghua bing li xue za zhi = Chinese journal of pathology
2020

[A Case of Extragonadal Germ Cell Tumor Treated by Induction Therapy with A Reduced Bep Regimen].

Hinyokika kiyo. Acta urologica Japonica
2020

Klinefelter syndrome and germ cell tumors: review of the literature.

International journal of pediatric endocrinology
2020

An extragonadal germ cell tumor with dermatomyositis: A case report and literature review.

Molecular and clinical oncology
2020

[A Case of Metachronous Testicular Tumor Developing Twenty Years after Treatment of Retroperitoneal Extragonadal Germ Cell Tumor].

Hinyokika kiyo. Acta urologica Japonica
2020

Nonseminomatous Extragonadal Germ Cell Tumor Presenting As Early Pericardial Tamponade.

Cureus
2020

Incidentally discovered primary mediastinal germ cell tumor.

JAAPA : official journal of the American Academy of Physician Assistants
2020

Primary malignant mediastinal germ cell tumors: A single institutional experience.

South Asian journal of cancer
2020

Retroperitoneal extragonadal germ cell tumor without distant metastasis: a case report.

International cancer conference journal
2019

A synchronous occurrence of bifocal intracranial germinoma and bilateral testicular epidermoid cyst in an adolescent patient with Klinefelter`s syndrome.

The Turkish journal of pediatrics
2020

An extragonadal yolk sac tumor presumed to be of postmeiotic germ cell origin by genetic zygosity analysis via single nucleotide polymorphism array.

Genes, chromosomes &amp; cancer
2019

Playing the long surveillance ball game: Metachronous testicular tumor developing after treatment and remission of extragonadal germ cell tumor.

Rare tumors
2019

Case of acute respiratory distress syndrome in a patient with an extragonadal germ cell tumor without lung metastasis in which choriocarcinoma syndrome was suspected.

IJU case reports
2019

Primary mediastinal germ cell tumors.

Seminars in oncology
2019

Japanese clinical practice guidelines for sacrococcygeal teratoma, 2017.

Pediatrics international : official journal of the Japan Pediatric Society
2019

Poor prognosis of retroperitoneal mixed extragonadal germ cell tumors in an HIV-infected man with severe immunosuppression and bilateral cryptorchidism: a case report.

BMC cancer
2019

Primary Malignant Thyroid Teratoma: An Institutional Experience.

Thyroid : official journal of the American Thyroid Association
2018

[A CASE WITH LATE RECURRENCE OF EXTRAGONADAL GERM CELL TUMOR].

Nihon Hinyokika Gakkai zasshi. The japanese journal of urology
2018

Therapy-related acute myeloid leukemia and myelodysplastic syndrome among refractory germ cell tumor patients.

International journal of urology : official journal of the Japanese Urological Association
2018

Extragonadal germ cell tumor of the posterior mediastinum in a child complicated with spinal cord compression: a case report.

BMC pediatrics
2017

Yolk sac tumor in the abdominal wall of an 18-month-old girl: a case report.

Journal of medical case reports
2017

Hypertestosteronemia and Infertility from a Mediastinal Extragonadal Germ Cell Tumor.

The American journal of medicine
2016

Comparison of the clinical features and hematopoietic stem cell transplantation outcomes of mediastinal malignant germ cell tumors with nonmediastinal extragonadal placements.

OncoTargets and therapy
2017

Klinefelter Syndrome with Poor Risk Extragonadal Germ Cell Tumor.

Urology case reports
2017

Primary Choriocarcinoma of the Bladder: A Case Report and Review of Literature.

Clinical genitourinary cancer
2016

Dislodgement and gastrointestinal tract penetration of bone cement used for spinal reconstruction after lumbosacral vertebral tumor excision: A case report.

Medicine
2017

Testicular Microlithiasis in the Setting of Primary Extragonadal Germ Cell Tumor: A Case Series.

Ultrasound quarterly
2016

Recovery from Choriocarcinoma Syndrome Associated with a Metastatic Extragonadal Germ Cell Tumor Hemorrhage.

Case reports in gastroenterology
2016

Modified Facial Translocation Approach in a One-Month Old With a Skullbase Tumor.

The Journal of craniofacial surgery
2016

Desperation surgery for a chemorefractory lung lesion in a patient with an extragonadal germ cell tumor.

International cancer conference journal
2016

A clinicopathological study of mediastinal masses operated in a tertiary care hospital in Eastern India in 3 years with special reference to thymoma.

Indian journal of pathology &amp; microbiology
2016

Clinical Features and Treatment Outcomes in Patients with Extragonadal Germ Cell Tumors: A Single-center Experience.

Anticancer research
2015

Primary extragonadal germ cell tumor: A case report on prostate seminoma.

Oncology letters
2015

[PRIMARY MEDIASTINAL GERM CELL TUMOR ARISING IN A PATIENT WITH NEUROFIBROMATOSIS TYPE 1].

Nihon Hinyokika Gakkai zasshi. The japanese journal of urology
2015

[A case of metachronal testicular tumor eight years after medical treatment of extragonadal germ cell tumor].

Hinyokika kiyo. Acta urologica Japonica

Associações

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Comunidades

Grupos ativos de quem convive com esta doença aqui no Raras

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Doenças relacionadas

Doenças com sintomas parecidos — ajudam quem ainda está buscando diagnóstico

Referências e fontes

Bases de dados externas citadas neste artigo

Publicações científicas

Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.

  1. Extracranial, Extragonadal Germ Cell Tumors: A Multicenter Australian Case Series.
    Asia-Pacific journal of clinical oncology· 2026· PMID 41607262mais citado
  2. Minimally Invasive Approach of Bile Duct Stricture after Laparoscopic Hepatectomy.
    Journal of laparoendoscopic &amp; advanced surgical techniques. Part A· 2026· PMID 41661109mais citado
  3. Rectal adenocarcinoma with a yolk sac tumor component: A rare case report and review of the literature.
    International cancer conference journal· 2026· PMID 41589237mais citado
  4. A rare entity in the retroperitoneum: Case report of a primary seminoma.
    Urology case reports· 2026· PMID 41551963mais citado
  5. Hepatoduodenal ligament teratoma presenting with fever in a young adult.
    Journal of surgical case reports· 2026· PMID 41523223mais citado
  6. Extragonadal Primary Mixed Germ Cell Tumor of the Stomach.
    J Indian Assoc Pediatr Surg· 2026· PMID 41958792recente
  7. Rapidly growing mediastinal mature cystic teratoma with increased FDG uptake: challenging the paradigm of indolent growth.
    J Cardiothorac Surg· 2026· PMID 41937160recente
  8. Survival outcomes and prognostic factors of extragonadal germ cell tumors: An institutional experience over a decade.
    Gulf J Oncolog· 2025· PMID 41733161recente

Bases de dados e fontes oficiais

Identificadores e referências canônicas usadas para montar este verbete.

  1. ORPHA:363579(Orphanet)
  2. MONDO:0018201(MONDO)
  3. GARD:9325(GARD (NIH))
  4. Variantes catalogadas(ClinVar)
  5. Busca completa no PubMed(PubMed)
  6. Q55787791(Wikidata)

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Tumor de células germinativas extragonadal
Compêndio · Raras BR

Tumor de células germinativas extragonadal

ORPHA:363579 · MONDO:0018201
Prevalência
1-9 / 1 000 000
Prevalência
0.13 (Europe)
MedGen
UMLS
C3544268
EuropePMC
Wikidata
Papers 10a
Evidência
🥉 Relato de caso
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