1H, 13C, and 15N backbone resonance assignments of the A2 domain of human von Willebrand factor.

A Retrospective Analysis of ADAMTS13 Enzymatic Activity Results in a Population With Thrombotic Thrombocytopenic Purpura Disease in the Arabian Gulf and Colombia (APOLO Study).

Beyond HELLP: An Unusual Cause of Severe Thrombocytopenia in Pregnancy.

Thrombotic thrombocytopenic purpura in pregnancy: Lessons from a case series of three patients.

Thrombotic microangiopathy with features of thrombotic thrombocytopenic purpura in a patient with Vibrio parahaemolyticus bacteremia: a rare case report.

A 35-year-old man with immune thrombotic thrombocytopenic purpura presenting with dark urine.

Thrombotic thrombocytopenic purpura following one anastomosis gastric bypass surgery: a rare case report.

Case Report: Endothelial-targeted bridging therapy for a TTP-like phenotype in fulminant iMCD-TAFRO.

Dynamic Monitoring of ADAMTS-13 Activity for Differential Diagnosis Across the Spectrum of Sepsis-Associated Thrombotic Microangiopathies.

Systematic Literature Review of the Economic and Quality of Life Burden of Congenital and Immune-Mediated Thrombotic Thrombocytopenic Purpura.

The interface of hemostasis and inflammation: endothelial-platelet dynamics in thrombosis.

A red blood cell-based antigen delivery system to facilitate T cell epitope presentation to promote peripheral tolerance to ADAMT S13 in immune-mediated thrombotic thrombocytopenic purpura.

Hereditary Thrombotic Thrombocytopenic Purpura Associated With Recurrent Strokes and Prominent Nervous System Involvement in a Young Chinese Female.

Multiphasic Infarcts in a Young Brain Secondary to Thrombotic Thrombocytopenic Purpura: Looking Beyond the Usual Suspects.

Thrombotic thrombocytopenic purpura: celebrating 25 years of ADAMTS13.

Measuring the neuropsychological consequences of thrombotic thrombocytopenic purpura: a rapid literature review.

Effectiveness of caplacizumab in the first-line treatment for acquired thrombotic thrombocytopenic purpura: single center experience.

Triple therapy with caplacizumab and rituximab for refractory systemic lupus erythematosus-associated thrombotic thrombocytopenic purpura achieves rapid, durable remission: A case report.

Reinventing the wheel in ischemic stroke: Novel aspects in ADAMTS13 and von Willebrand axis.

Thrombotic thrombocytopenic purpura as a complication of pembrolizumab: a case report and literature Review.

Pregnancy-Associated Thrombotic Thrombocytopenic Purpura: Diagnostic Pitfalls, Therapeutic Strategies, and Emerging Paradigms.

Cerebral Fat Embolism Syndrome in Homozygous Sickle Cell Disease Treated With Therapeutic Plasma Exchange and Simple Transfusions.

Late Onset of Congenital TTP: Case Presentation and Review of the Literature.

Recombinant ADAMTS13: An Enzyme Replacement Therapy for the Management of Congenital Thrombotic Thrombocytopenic Purpura.

Genetics of thrombotic thrombocytopenic purpura: systematic review in immune and congenital thrombotic thrombocytopenic purpura.

Caplacizumab resistance in immune thrombotic thrombocytopenic purpura is associated with a von Willebrand factor A1 domain missense variant.

Hematologic safety of caplacizumab in immune-mediated thrombotic thrombocytopenic purpura: insights from platelet-related signal detection in the FAERS database.

Is congenital thrombotic thrombocytopenic purpura a risk factor for ischemic osteonecrosis of the hip joint (Legg-Calvé-Perthes disease)?

C3 mutation-associated atypical hemolytic uremic syndrome with severe renal dysfunction and hypertensive emergency successfully treated with ravulizumab and sacubitril/valsartan: a case report.

Linking preclinical models to clinical realities: VEGF/VEGFR inhibitors and thrombotic microangiopathy in cancer therapy.

Impact of Day of Hospital Admission and Hospital Characteristics on Mortality in Thrombotic Thrombocytopenic Purpura.

Revisiting Clinical Response and Refractoriness in Immune Thrombotic Thrombocytopenic Purpura.

Hypertensive Havoc: When Malignant Hypertension Mimics Thrombotic Thrombocytopenic Purpura.

Optimizing the management of congenital thrombotic thrombocytopenic purpura.

Efficacy of Plasma Exchange in Secondary Thrombotic Microangiopathy: A Case Report and Literature Review.

Acute kidney injury requiring temporary hemodialysis due to HELLP syndrome: a case report.

[Immune-mediated thrombotic thrombocytopenic purpura successfully diagnosed and treated through repeated ADAMTS13 inhibitor testing].

Pathogen-reduced plasma, cryoprecipitate reduced for therapeutic plasma exchange.

Bone marrow proteomic profiling reveals TMEM109 as a biomarker for relapse in thrombotic thrombocytopenic purpura.

Experience in emergency management of first-episode immune thrombotic thrombocytopenic purpura over the past 21 years: a single-center retrospective study.

[Management of thrombotic microangiopathy].

[Microangiopathies thrombotiques].

Monitoring ADAMTS-13 conformation in immune-mediated thrombotic thrombocytopenic purpura: toward personalized management.

Endothelial injury to cognitive decline: a 12-month follow-up using computed tomography perfusion and diffusion magnetic resonance imaging in immune-mediated thrombotic thrombocytopenic purpura.

Thrombotic thrombocytopenic purpura in a patient with systemic lupus erythematosus after anifrolumab: a possible association.

Thrombotic thrombocytopenic purpura: a Trojan horse of acute leukemia?: a case report.

Acquired thrombotic thrombocytopenic purpura and HIV infection: a case report and review of the literature.

Health-related quality of life and mental health in autoimmune thrombotic thrombocytopenic purpura patients in the caplacizumab era.

Caplacizumab as an Emerging Treatment for Patients With Thrombotic Thrombocytopenic Purpura Presenting With Acute Ischemic Stroke.

Brazilian Registry of Thrombotic Thrombocytopenic Purpura: A prospective cohort study of diagnosis, management and outcomes in Brazil.

Postpartum Readmission for Pregnancy-Associated Thrombotic Microangiopathy Is Associated With Poor Maternal Outcomes.

Bilious Pleural Effusion Following Cholecystostomy in an Immunocompromised Elderly Male.

Thrombotic Microangiopathy Secondary to Capnocytophaga Sepsis: A Case Report.

Diagnostic and therapeutic challenges into snakebite-induced thrombotic microangiopathy: a case report and review of the literature.

Diagnostic Challenges in Atypical Hemolytic Uremic Syndrome: A Case of Artificial Mitral Valve Dysfunction as a Possible Trigger for Severe Thrombotic Microangiopathy.

Ethnicity affects relapse-free survival in immune-mediated thrombotic thrombocytopenic purpura.

Acute Kidney Injury in Immune-Mediated Thrombotic Thrombocytopenic Purpura - Solving the Puzzle?

Mechanisms of immune modulation by therapeutic plasma exchange.

Lyme disease as a rare trigger for autoimmune hemolytic anemia.

Therapeutic plasma exchangerelated complications in patients with immune-mediated thrombotic thrombocytopenic purpura.

An updated systematic review and meta-analysis of Caplacizumab for immune thrombotic thrombocytopenic purpura: Insights into efficacy and safety.

Atypical Hemolytic Uremic Syndrome After Post-Abortion Infection: Case Report and Literature Review.

Caplacizumab in Lupus-Associated Thrombotic Thrombocytopenic Purpura (TTP): Navigating Autoimmunity and Microangiopathy.

Genotype-Phenotype Variability in Congenital Thrombotic Thrombocytopenic Purpura (TTP): Two Novel ADAMTS13 Variants.

Rituximab in the Intensive Care Unit: A Review of Indications and Clinical Considerations.

Babesiosis precipitating immune thrombotic thrombocytopenic purpura.

Post-miscarriage Complement-Mediated Thrombotic Microangiopathy in a 27-Year-Old Woman: A Case Highlighting Diagnostic and Therapeutic Gaps in Brazil.

Improving the PLASMIC score with the use of RDW-SD in the differential diagnosis for thrombotic thrombocytopenic purpura in Chinese patients.

Thrombotic thrombocytopenic purpura following allogeneic hematopoietic stem cell transplantation: a rare but fatal complication.

In patients with suspected thrombotic thrombocytopenic purpura, what is the optimal time to therapeutic plasma exchange?

Hemolytic Uremic Syndrome Complicated by Severe Neuropsychiatric Symptoms: A Case Report and Review of the Literature.

Risk factors for silent cerebral infarction in immune-mediated thrombotic thrombocytopenic survivors.

Continuity of care in immune thrombotic thrombocytopenic purpura (iTTP): A visual roadmap for survivorship beyond acute management.

Tailored treatment of acute immune-mediated thrombotic thrombocytopenic purpura.

Challenges and opportunities in the long-term management of immune-mediated TTP.

Modern management of congenital thrombotic thrombocytopenic purpura (cTTP).

Update in the diagnosis of complement-mediated thrombotic microangiopathy/atypical hemolytic uremic syndrome.

A practical approach to immune thrombocytopenia in pregnancy.

EASIX, a new tool to predict response and refractoriness in immune-mediated thrombotic thrombocytopenic purpura.

Immune-mediated thrombotic thrombocytopenic purpura as a model of systemic microvascular dysfunction: moving from an acute to a chronic disorder.

Predicting Outcomes and Optimizing Therapy in Thrombotic Thrombocytopenic Purpura: Insights on Caplacizumab Use from a Romanian Hematology Center.

Thrombotic Thrombocytopenic Purpura During Anti-Tuberculosis Therapy: A Case Report and Literature Review.

Bicytopenia with haemolysis: Think severe vitamin B12 deficiency-associated thrombotic microangiopathy.

Ocular manifestations of primary thrombotic microangiopathies : a descriptive systematic review.

Severe thrombocytopenia and neurological symptoms in pregnancy: a diagnostic challenge between hemolysis, elevated liver enzymes, and low platelet syndrome and thrombotic thrombocytopenic purpura-what is your diagnosis?

Novel cryptic ADAMTS13 epitopes uncover a distinct open ADAMTS13 conformation in immune-mediated TTP.

IKAROS Associated Immunodeficiency and Thrombotic Thrombocytopenic Purpura.

"Recombinant a disintegrin-like and metalloproteinase with thrombospondin type 1 motifs 13 (ADAMTS-13) for acute and prophylactic treatment of congenital thrombotic thrombocytopenic purpura in pregnancy": comment.

von Willebrand factor and fibrin monomer - induced septic shock coagulation typing: Clinical comparison between thrombotic thrombocytopenic purpura - like syndrome and sepsis - induced coagulopathy with prognostic implications.

Malignant Hypertension-Induced Thrombotic Microangiopathy Mimicking Atypical Hemolytic Uremic Syndrome and Thrombotic Thrombocytopenic Purpura.

Common features of rare disease patients in the emergency department: a systematised literature review.

Recurrent Thrombocytopenia During Caplacizumab Therapy in Acute Immune-Mediated Thrombotic Thrombocytopenic Purpura.

A Case Report of Thrombotic Thrombocytopenic Purpura.

A Case of Piperacillin-Induced Immune Thrombocytopenia: Diagnostic Challenges and Management.

An Unusual Case of Nonneutropenic Fever Associated With Myelodysplasia and Sweet's Syndrome.

Danazol and cost-savings in immune thrombocytopenia and in immune thrombotic thrombocytopenic purpura.

Successful use of recombinant ADAMTS13 in a pregnant patient with immune-mediated thrombotic thrombocytopenic purpura.

Brain volumetric reductions in patients with thrombotic thrombocytopenic purpura.

An Unexpected Journey: Thrombotic Thrombocytopenic Purpura Unveiling Hidden HIV Infection.

Severe ADAMTS-13 deficiency without hemolysis as a cause of cryptogenic stroke: A single center case series.

Systemic immune inflammation index guides machine learning for rapid TTP diagnosis: a retrospective cohort study.

Pregnancy-Triggered Hereditary Thrombotic Thrombocytopenic Purpura: A Case Report.

Case report: post-delivery thrombotic thrombocytopenic purpura complicated by malignant catatonia.

Characteristics and Management of Patients With Immune Thrombotic Thrombocytopenic Purpura Admitted to the Intensive Care Unit: A Multicenter Retrospective Analysis.

Association of Cognitive Impairment with Reduced Health-Related Quality of Life and Depression Among Survivors of Thrombotic Thrombocytopenic Purpura.

Reduced half-life of recombinant ADAMTS13 in a patient with cTTP undergoing total hip arthroplasty.

Atypical hemolytic uremic syndrome treated with anti-C5 antibody agent eculizumab, without genetic complement abnormalities.

Updated ISTH thrombotic thrombocytopenic purpura guidelines 2025-a bridge to the future for congenital thrombotic thrombocytopenic purpura.

A rare case of hemolytic-uremic syndrome due to a Capnocytophaga canimorsus sepsis: Case report.

Pathogenic cytokines in thrombotic microangiopathies: molecular insights and therapeutic targets.

Recombinant ADAMTS-13 for congenital and immune thrombotic thrombocytopenic purpura in pregnancy.

Unmasking hidden shapes: unusual red cell morphologies in urine sediment.

Argatroban-Associated Adverse Events: An Analysis Based on FDA Adverse Event Reporting System (FAERS).

Resolution of thrombotic thrombocytopenic purpura serous retinal detachment following rituximab therapy.

Facing the bleeding risk of caplacizumab in postpartum immune thrombotic thrombocytopenic purpura in constrained resource settings.

Relapsing Chronic Immune Thrombocytopenia and Thrombosis: A Case Report.

Identification of HLA alleles involved in immune thrombotic thrombocytopenic purpura patients from Turkey: Erratum.

Fetal and maternal morbidity in pregnant patients with thrombotic thrombocytopenic purpura: A Nationwide analysis.

Zebrafish model reveals developmental and hematopoietic functions of ADAMTS13.

Real-world safety and efficacy of rADAMTS13 prophylaxis in congenital thrombotic thrombocytopenic purpura: experience from Polish patients previously treated with fresh frozen plasma.

[Advances in the diagnosis and treatment of thrombotic thrombocytopenic purpura].

Arterial Thrombotic Event in Thrombotic Thrombocytopenic Purpura Predating the Development of Microangiopathic Hemolytic Anemia and Thrombocytopenia.

Clinical characteristics and treatment response of patients with SLE complicated with thrombotic thrombocytopenic purpura.

Reference Range for the Automated Fragmented Red Cell Parameter and Its Diagnostic Utility in Red Blood Cell (RBC) Fragment Quantification: A Prospective Study.

[Exploring critical thinking in the management of diagnosis and treatment of fulminant pregnancy-associated atypical haemolytic uraemic syndrome].

Thrombotic microangiopathy multidisciplinary assessment team: demographics, final diagnosis, treatment, and outcomes.

Posterior reversible encephalopathy syndrome due to thrombotic thrombocytopenic purpura in a liver-transplant patient treated with tacrolimus.

ADAMTS13 Activity Testing: Evaluation of Two Automated Platforms for Diagnosis and Follow-Up of Thrombotic Thrombocytopenic Purpura.

Standard cardiovascular risk prediction scores underestimate risk in immune-mediated thrombotic thrombocytopenic purpura survivors.

The impact of the COVID-19 pandemic on incidence and clinical presentation of thrombotic microangiopathies: data from a laboratory centralizing ADAMTS-13 testing in Quebec.

The Differential Diagnosis of Thromobocytopenia.

New Insights Into Renal Involvement During Immune-Mediated Thrombotic Thrombocytopenic Purpura.

Pregnancy-Induced Thrombotic Thrombocytopenic Purpura Complicated by Atypical Posterior Reversible Encephalopathy Syndrome and Acute Pancreatitis: A Rare Presentation.

Regarding "Challenges in diagnosing thrombotic thrombocytopenic purpura".

Fetal Hereditary Thrombotic Thrombocytopenic Purpura.

Therapeutic plasma exchange in immune thrombotic thrombocytopenic purpura: A six-year prospective study on clinical efficacy, laboratory trends, and sex-based differences.

Can COVID-19 Lead to Refractory Thrombotic Thrombocytopenic Purpura (TTP) During Pregnancy and Postpartum? A Case Report and a Review of the Literature.

A Clever Stroke Mimic: Thrombotic Thrombocytopenic Purpura Without Schistocytes - A Case Report and Literature Review.

Evaluation of different platelet-dependent von Willebrand factor activity assays to assess the in vivo inhibitory effect of caplacizumab on the von Willebrand factor-platelet interaction.

Cytokine storm and microvascular fate: mechanistic insights into endothelial injury in thrombotic microangiopathies.

Prognostic value of laboratory biomarkers for mortality risk stratification in thrombotic thrombocytopenic purpura.

[Personalised treatment of patients with immune thrombotic thrombocytopenic purpura].

Optimizing ADAMTS13 prophylaxis to reduce relapse and organ failure in congenital thrombotic thrombocytopenic purpura.

Association of Therapeutic Plasma Exchange-Treated Thrombotic Thrombocytopenic Purpura with Improved Mortality Outcome in End-Stage Renal Disease.

Long-term follow-up outcomes in congenital thrombotic thrombocytopenic purpura.

Implementation of a fully automated ADAMTS13 activity assay utilizing fluorescence resonance energy transfer with a practical approach to address high background fluorescence interference.

COVID-19 Microangiopathy: Insights into plasma exchange as a therapeutic strategy.

High anti-ADAMTS13 IgG Levels after Plasma Exchange Predict Delayed ADAMTS13 Normalization in Immune-mediated Thrombotic Thrombocytopenic Purpura.

Rare onset of congenital thrombotic thrombocytopenic purpura during pregnancy: A novel ADAMTS13 gene variant.

Severe Plasmodium Falciparum Malaria Mimicking Thrombotic Thrombocytopenic Purpura (TTP): A Case Report From China.

Progression From Early Multiterritorial Punctate Infarcts to Massive Stroke in Fulminant Thrombotic Thrombocytopenic Purpura Despite Aggressive Therapy: A Therapeutic Dilemma in Initiating Antithrombotic Therapy.

Prognostic relevance of early clinical and laboratory findings in immune-mediated thrombotic thrombocytopenic purpura.

Recurrent Thrombotic Thrombocytopenic Purpura Associated With Helicobacter pylori: More Than a Gut Feeling.

Kidney transplantation in congenital thrombotic thrombocytopaenic purpura: using recombinant ADAMTS13 to balance relapse and rejection.

Thrombotic Thrombocytopenic Purpura in Pregnancy.

Progressive silent cerebral infarction is associated with stroke and persistent cognitive impairment in survivors of iTTP.

Severe congenital thrombotic thrombocytopenic purpura in pregnancy complicated by eclampsia.

Trp1250, Lys1252, and Arg1367 of ADAMTS13 comprise a hot spot for anti-CUB domain antibodies in patients with iTTP.

Novel prognostic factor in thrombotic thrombocytopenic purpura: human leukocyte antigen class II.

Seasonal variation in immune thrombotic thrombocytopenic purpura in New England.

Rising total leukocyte counts correspond with rising platelet counts in thrombotic thrombocytopenic purpura.

Genetic variants contribute to modulation of renal function in patients with immune thrombotic thrombocytopenic purpura.

A rare complication of thrombotic microangiopathy induced by chemotherapy for second breast cancer in a Hodgkin lymphoma survivor: a case report.

Characterization of autopsy findings including multivisceral glomeruloid vascular bodies in hereditary thrombotic thrombocytopenic purpura with two new variants in ADAMTS13 gene.

A peculiar case report of primary iTTP in a previously healthy Saudi man.

Differential Diagnosis of Thrombotic Microangiopathy: Overlapping Features of Thrombotic Thrombocytopenic Purpura and Complement-Mediated Thrombotic Microangiopathy in a Dengue-Infected Patient.

Caplacizumab for pediatric immune thrombotic thrombocytopenic Purpura: A scoping review of current evidence.

Investigating the impact of platelet transfusions on adverse outcomes in patients with thrombotic thrombocytopenic purpura: A systematic review of published studies.

Thrombotic Thrombocytopenic Purpura Triggered by Chronic Lymphocytic Leukemia: A Case Report.

Immune-mediated thrombotic thrombocytopenic purpura with systemic lupus erythematosus: clinical features and outcome.

Open or closed? Understanding the molecular mechanisms and clinical implications of ADAMTS13's conformation.

[Translated article] Caplacizumab in acute thrombotic thrombocytopenic purpura refractory to standard treatment.

Thrombotic Thrombocytopenic Purpura as a Rare Stroke Mimic.

Longitudinal analysis of arterial pressure and its impact on outcomes in patients with thrombotic thrombocytopenic purpura.

Clinical Manifestations, Treatment Characteristics, and Clinical Outcomes in Patients with Immune Thrombotic Thrombocytopenic Purpura (iTTP) in a Real-World Setting: An Interim Analysis of the Turkish iTTP Registry.

Thrombotic thrombocytopenic purpura: Description and analysis of 23 cases treated in Chile between 2017 and 2022.

Splenectomy for immune thrombotic thrombocytopenic purpura: a systematic review and meta-analysis.

Fulminant myocarditis in immune-mediated thrombotic thrombocytopenic purpura: A case report.

The Hideous Side of Acute Pancreatitis: A Case of Pancreatitis-Induced Atypical Hemolytic Uremic Syndrome.

Potentially reversible severe cardiac involvement in thrombotic microangiopathies with malignant hypertension.

Anti-ADAMTS13 Antibodies Trajectory is Associated With ADAMTS13 Recovery in Immune-Mediated TTP.

Proof-of-Concept in a Murine Model of Treatment of Thrombotic Thrombocytopenic Purpura Using Engineered Red Blood Cells.

Novel ADAMTS13 Mutation in a Patient With Congenital TTP Diagnosed in Pregnancy.

Congenital thrombotic thrombocytopenic purpura: a rare cause of severe neonatal jaundice and hypoxic respiratory failure - a case report.

A microfluidic approach reveals ongoing disease activity in thrombotic thrombocytopenic purpura patients despite clinical remission.

Preferences of Patients With cTTP and Other Chronic Conditions for At-Home Prophylactic Infusions: A Discrete Choice Experiment.

Diagnostic Value of Biological Parameters in Biopsy-Confirmed Thrombotic Microangiopathy-MATRIX Consortium Group.

Systemic Lupus Erythematosus-Associated Thrombotic Thrombocytopenic Purpura: A Case Report.

[Plasma exchange-free therapeutic management of immune-mediated thrombotic thrombocytopenic purpura].

Navigating recurrent immune-mediated thrombotic thrombocytopenic purpura (iTTP) in pregnancy: A case report and literature review.

Quantitative Systems Pharmacology Modeling of Platelet Responses to Recombinant ADAMTS13 in Patients With Congenital Thrombotic Thrombocytopenic Purpura.

Microangiopathic Hemolytic Anemia in Pregnancy.

Thrombotic Microangiopathies.

Thrombotic thrombocytopenic purpura: early diagnosis and effective treatment in 2025.

Immunotherapy-associated hemostatic abnormalities: bleeding and thrombotic complications.

Early Recognition of Atypical Thrombotic Thrombocytopenic Purpura (TTP) in Severe Asymptomatic Thrombocytopenia Using the PLASMIC Score and Peripheral Blood Smear.

A predictive algorithm involving lactate dehydrogenase to serum creatinine ratio may assist in identifying patients with thrombotic thrombocytopenic purpura.