Doença congênita caracterizada por uma conexão anormal entre uma ou mais artérias coronárias e uma câmara cardíaca ou grande vaso.
Introdução
O que você precisa saber de cara
Doença congênita caracterizada por uma conexão anormal entre uma ou mais artérias coronárias e uma câmara cardíaca ou grande vaso.
Escala de raridade
<1/50kMuito rara
1/20kRara
1/10kPouco freq.
1/5kIncomum
1/2k
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Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Partes do corpo afetadas
+ 12 sintomas em outras categorias
Características mais comuns
Os sintomas variam de pessoa para pessoa. Abaixo estão as 27 características clínicas mais associadas, ordenadas por frequência.
Linha do tempo da pesquisa
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Genética e causas
O que está alterado no DNA e como passa nas famílias
Nenhum gene associado encontrado
Os dados genéticos desta condição ainda estão sendo catalogados.
Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
Remédios, cuidados de apoio e o que precisa acompanhar
Onde tratar no SUS
Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)
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Publicações mais relevantes
Surgical Management of a Right Coronary Artery Fistula After Failed Transcatheter Closure: A Case Report.
A coronary artery fistula (CAF) is an abnormal communication between a coronary artery and a great vessel or cardiac chamber. CAFs are very rare and are mostly of congenital origin, but they can also be acquired. Patients are usually asymptomatic since the majority of CAFs are small in size; hence, most cases are usually discovered incidentally during routine angiographic investigations. Moderate or large CAFs can be symptomatic, causing angina pectoris due to coronary steal phenomenon, and can carry a high risk of serious complications such as myocardial infarction, heart failure, or even sudden cardiac death. Consequently, prompt management with the appropriate choice of intervention - surgical versus transcatheter closure - is essential to prevent such complications. We present a case of a 52-year-old male patient with a right coronary artery-coronary sinus fistula managed with surgical closure.
Percutaneous Coronary Intervention-Related Iatrogenic Fistula in Acute Coronary Syndrome.
Iatrogenic coronary artery fistula (CAF) can occur following acute myocardial infarction, percutaneous coronary intervention (PCI) procedures, and heart surgery. Iatrogenic CAF linked to PCI has a low incidence rate. Early diagnosis and treatment are crucial when an iatrogenic fistula develops, as it may lead to cardiac tamponade, myocardial infarction, or death. In this report, we present a case of iatrogenic CAF secondary to coronary perforation caused by guidewire-induced trauma, followed by stent implantation and balloon inflation in the context of acute coronary syndrome (ACS). It was successfully managed through prolonged balloon inflation within the previously implanted stent just prior to the rupture zone.
Right Coronary Artery to Left Ventricular Fistula Complicated by Symptomatic Arrhythmia.
Coronary cameral fistulas (CCFs) are rare and are characterized by an abnormal connection between a coronary artery and any of the four chambers of the heart. Most cases of CCFs are asymptomatic. The most common presentation in symptomatic patients includes chest pain or heart failure; however, arrhythmias are rarely associated. We report the case of a 32-year-old male previously unknown to have any medical illnesses. He presented to the clinic with complaints of frequent palpitations, necessitating recurrent admissions. His electrocardiograms revealed regular wide complex tachycardia with a right bundle branch block pattern, suggestive of fascicular ventricular tachycardia. During hospitalization, an elective coronary angiography showed a large CCF originating from the right posterior descending coronary artery and draining into the left ventricle. Moreover, cardiac magnetic resonance imaging did not show any scar or evidence of cardiomyopathies. The patient underwent a successful catheter-based right coronary artery to left ventricular fistula occlusion with coils. In addition, the patient underwent a complex electrophysiological study with three-dimensional mapping and ablation. The presented case underscores the rarity and complexity of such clinical presentations. It also highlights the importance of a multidisciplinary approach in addressing this unique cardiac anomaly.
Unlocking the Hidden Pathway: A Rare Encounter With Right Coronary Artery Fistula to Coronary Sinus and Right Ventricle.
Coronary artery fistulas (CAFs) are rare vascular anomalies characterized by abnormal connections between coronary arteries and cardiac chambers or adjacent structures. Advances in cardiac interventions have led to an increasing recognition of acquired CAFs, which are typically congenital. We present a case of a 62-year-old male with a complex medical history, including hypertension, atrial fibrillation, and heart failure, who presented with exertional chest pain and palpitations. Diagnostic evaluation revealed a significant CAF originating from the right coronary artery (RCA) and terminating into the coronary sinus and right ventricle. Despite the absence of significant coronary artery occlusions, the fistula was deemed clinically significant due to its potential to cause myocardial ischemia. Management involved guideline-directed medical therapy and lifestyle modifications. This case underscores the importance of early recognition and appropriate management of CAFs to optimize patient outcomes. Further research is needed to better understand the natural history and optimal management strategies of CAFs.
Right Coronary Artery-to-Right Atrial Fistula Accompanied by Multiple Right Coronary Artery Aneurysms: A Case Report.
A coronary artery aneurysm (CAA) denotes a localized dilation of the coronary artery, while a coronary artery fistula signifies an aberrant connection between a coronary artery and a cardiac chamber or adjacent vessel. Here, we present a case study of a 68-year-old female with a previously diagnosed right coronary artery-to-right atrial fistula concomitant with multiple right coronary artery aneurysms. Initially asymptomatic, the patient subsequently manifested atrial fibrillation. Management involved augmenting the patient's home regimen with metoprolol tartrate, followed by successful cardioversion and restoration of sinus rhythm. Given the stability of the fistula and the absence of symptomatic exacerbation, no further interventional measures were undertaken. The patient was discharged with an adjusted metoprolol regimen and scheduled follow-up with her cardiologist. Subsequent imaging assessments unveiled progressive fistula expansion alongside the development of concurrent CAA, inciting deliberations concerning optimal treatment modalities.
Publicações recentes
Surgical Management of a Right Coronary Artery Fistula After Failed Transcatheter Closure: A Case Report.
Percutaneous Coronary Intervention-Related Iatrogenic Fistula in Acute Coronary Syndrome.
Right Coronary Artery to Left Ventricular Fistula Complicated by Symptomatic Arrhythmia.
Unlocking the Hidden Pathway: A Rare Encounter With Right Coronary Artery Fistula to Coronary Sinus and Right Ventricle.
Right Coronary Artery-to-Right Atrial Fistula Accompanied by Multiple Right Coronary Artery Aneurysms: A Case Report.
📚 EuropePMC36 artigos no totalmostrando 14
Surgical Management of a Right Coronary Artery Fistula After Failed Transcatheter Closure: A Case Report.
CureusPercutaneous Coronary Intervention-Related Iatrogenic Fistula in Acute Coronary Syndrome.
CureusRight Coronary Artery to Left Ventricular Fistula Complicated by Symptomatic Arrhythmia.
CureusUnlocking the Hidden Pathway: A Rare Encounter With Right Coronary Artery Fistula to Coronary Sinus and Right Ventricle.
CureusRight Coronary Artery-to-Right Atrial Fistula Accompanied by Multiple Right Coronary Artery Aneurysms: A Case Report.
CureusGiant left coronary artery diagonal branch left ventricular fistula: A case report and review of literature.
Frontiers in cardiovascular medicineRight Atrial Thrombus Presenting as Platypnea-Orthodeoxia Secondary to Reverse Lutembacher Syndrome: A Case Report.
CureusRole of Occlusion Position in Coronary Artery Fistulas with Terminal Aneurysms: A Hemodynamic Perspective.
Cardiovascular engineering and technologyNatural Coronary Bypass: A Rare Case of Aortocoronary Fistula in a Patient with Three-Vessel Disease.
CureusAortic atresia with the interrupted aortic arch and an pulmonary-coronary fistula: the unique constellation for survival.
Interactive cardiovascular and thoracic surgeryExtensively Thrombosed Ectatic Circumflex Coronary Artery Fistula Presenting as Acute Coronary Syndrome.
Current cardiology reviewsPrenatally Diagnosed Isolated Coronary Arterial Fistula Leading to Severe Complications at Birth.
Case reports in cardiologyCovered Stent for Large Coronary Arterial Fistula and Adjacent Atherosclerotic Plaque With Stenosis in a Patient With Non-ST-Segment Elevation Myocardial Infarction.
JACC. Cardiovascular interventions[Congenital coronary artery fistulas: clinical and therapeutic consideration].
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Surgical Management of a Right Coronary Artery Fistula After Failed Transcatheter Closure: A Case Report.
- Percutaneous Coronary Intervention-Related Iatrogenic Fistula in Acute Coronary Syndrome.
- Right Coronary Artery to Left Ventricular Fistula Complicated by Symptomatic Arrhythmia.
- Unlocking the Hidden Pathway: A Rare Encounter With Right Coronary Artery Fistula to Coronary Sinus and Right Ventricle.
- Right Coronary Artery-to-Right Atrial Fistula Accompanied by Multiple Right Coronary Artery Aneurysms: A Case Report.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:2041(Orphanet)
- MONDO:0016081(MONDO)
- GARD:1533(GARD (NIH))
- Busca completa no PubMed(PubMed)
- Q11829260(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
