Raras
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Lúpus eritematoso cutâneo crônico
ORPHA:163531CID-11 · EB51PCDT · SUSDOENÇA RARA

O Lúpus Eritematoso Cutâneo Crônico (CCLE) é um tipo de lúpus que afeta a pele de forma persistente. Ele faz parte de um grupo maior de condições conhecido como Lúpus Eritematoso Cutâneo (CLE), e inclui cinco formas diferentes: lúpus eritematoso discoide (DLE); lúpus tipo frieira (também conhecido como lúpus pérnio); lúpus eritematoso hipertrófico ou verrucoso (que causa lesões espessas ou parecidas com verrugas); lúpus eritematoso tumidus (que forma inchaços na pele); e lúpus eritematoso paniculite (que atinge a camada de gordura embaixo da pele).

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Introdução

O que você precisa saber de cara

📋

O Lúpus Eritematoso Cutâneo Crônico (CCLE) é um tipo de lúpus que afeta a pele de forma persistente. Ele faz parte de um grupo maior de condições conhecido como Lúpus Eritematoso Cutâneo (CLE), e inclui cinco formas diferentes: lúpus eritematoso discoide (DLE); lúpus tipo frieira (também conhecido como lúpus pérnio); lúpus eritematoso hipertrófico ou verrucoso (que causa lesões espessas ou parecidas com verrugas); lúpus eritematoso tumidus (que forma inchaços na pele); e lúpus eritematoso paniculite (que atinge a camada de gordura embaixo da pele).

Pesquisas ativas
8 ensaios
35 total registrados no ClinicalTrials.gov
Publicações científicas
224 artigos
Último publicado: 2026 Mar
🏥
SUS: Cobertura parcialScore: 50%
PCDT disponível1 medicamentos CEAF
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Sinais e sintomas

O que aparece no corpo e com que frequência cada sintoma acontece

Partes do corpo afetadas

🧬
Pele e cabelo
16 sintomas
🦴
Ossos e articulações
2 sintomas
👂
Ouvidos
1 sintomas
❤️
Coração
1 sintomas
🛡️
Imunológico
1 sintomas
😀
Face
1 sintomas

+ 19 sintomas em outras categorias

Características mais comuns

Edema dérmico papilar
Fotossensibilidade cutânea
Eritema pérnio
Autoamputação dos dedos
Artralgia
Morfologia anormal da unha
42sintomas
Sem dados (42)

Os sintomas variam de pessoa para pessoa. Abaixo estão as 42 características clínicas mais associadas, ordenadas por frequência.

Edema dérmico papilarPapillary dermal edema
Fotossensibilidade cutâneaCutaneous photosensitivity
Eritema pérnioChilblains
Autoamputação dos dedosAutoamputation of digits
ArtralgiaArthralgia

Linha do tempo da pesquisa

Publicações por ano — veja quando o interesse científico cresceu
Anos de pesquisa1desde 2026
Total histórico224PubMed
Últimos 10 anos124publicações
Pico202315 papers
Linha do tempo
2026Hoje · 2026🧪 1997Primeiro ensaio clínico📈 2023Ano de pico
Publicações por ano (últimos 10 anos)

Encontrou um erro ou informação desatualizada? Sugira uma correção →

Genética e causas

O que está alterado no DNA e como passa nas famílias

Genes associados

3 genes identificados com associação a esta condição.

Multigenic/multifactorial
TREX1Three-prime repair exonuclease 1Disease-causing germline mutation(s) inTolerante
FUNÇÃO

Major cellular 3'-to-5' DNA exonuclease which digests single-stranded DNA (ssDNA) and double-stranded DNA (dsDNA) with mismatched 3' termini (PubMed:10391904, PubMed:10393201, PubMed:17293595). Prevents cell-intrinsic initiation of autoimmunity (PubMed:10391904, PubMed:10393201, PubMed:17293595). Acts by metabolizing DNA fragments from endogenous retroelements, including L1, LTR and SINE elements (PubMed:10391904, PubMed:10393201, PubMed:17293595). Plays a key role in degradation of DNA fragment

LOCALIZAÇÃO

NucleusCytoplasm, cytosolEndoplasmic reticulum membrane

VIAS BIOLÓGICAS (2)
IRF3-mediated induction of type I IFNRegulation by TREX1
MECANISMO DE DOENÇA

Aicardi-Goutieres syndrome 1

A form of Aicardi-Goutieres syndrome, a genetically heterogeneous disease characterized by cerebral atrophy, leukoencephalopathy, intracranial calcifications, chronic cerebrospinal fluid (CSF) lymphocytosis, increased CSF alpha-interferon, and negative serologic investigations for common prenatal infection. Clinical features as thrombocytopenia, hepatosplenomegaly and elevated hepatic transaminases along with intermittent fever may erroneously suggest an infective process. Severe neurological dysfunctions manifest in infancy as progressive microcephaly, spasticity, dystonic posturing and profound psychomotor retardation. Death often occurs in early childhood.

EXPRESSÃO TECIDUAL(Ubíquo)
Linfócitos
80.6 TPM
Baço
45.2 TPM
Skin Sun Exposed Lower leg
42.6 TPM
Skin Not Sun Exposed Suprapubic
42.3 TPM
Pituitária
42.0 TPM
OUTRAS DOENÇAS (6)
retinal vasculopathy with cerebral leukoencephalopathy and systemic manifestationschilblain lupus 1Aicardi-Goutieres syndrome 1Aicardi-Goutieres syndrome
HGNC:12269UniProt:Q9NSU2
SAMHD1Deoxynucleoside triphosphate triphosphohydrolase SAMHD1Disease-causing germline mutation(s) inTolerante
FUNÇÃO

Protein that acts both as a host restriction factor involved in defense response to virus and as a regulator of DNA end resection at stalled replication forks (PubMed:19525956, PubMed:21613998, PubMed:21720370, PubMed:22056990, PubMed:23601106, PubMed:23602554, PubMed:24336198, PubMed:26294762, PubMed:26431200, PubMed:28229507, PubMed:28834754, PubMed:29670289). Has deoxynucleoside triphosphate (dNTPase) activity, which is required to restrict infection by viruses, such as HIV-1: dNTPase activit

LOCALIZAÇÃO

NucleusChromosome

VIAS BIOLÓGICAS (2)
Interferon alpha/beta signalingNucleotide catabolism
MECANISMO DE DOENÇA

Aicardi-Goutieres syndrome 5

A form of Aicardi-Goutieres syndrome, a genetically heterogeneous disease characterized by cerebral atrophy, leukoencephalopathy, intracranial calcifications, chronic cerebrospinal fluid (CSF) lymphocytosis, increased CSF alpha-interferon, and negative serologic investigations for common prenatal infection. Clinical features as thrombocytopenia, hepatosplenomegaly and elevated hepatic transaminases along with intermittent fever may erroneously suggest an infective process. Severe neurological dysfunctions manifest in infancy as progressive microcephaly, spasticity, dystonic posturing and profound psychomotor retardation. Death often occurs in early childhood.

EXPRESSÃO TECIDUAL(Ubíquo)
Nervo tibial
453.4 TPM
Esôfago - Muscular
225.4 TPM
Esôfago - Junção
209.5 TPM
Artéria coronária
194.4 TPM
Fallopian Tube
174.3 TPM
OUTRAS DOENÇAS (4)
chilblain lupus 2Aicardi-Goutieres syndrome 5familial chilblain lupusAicardi-Goutieres syndrome
HGNC:15925UniProt:Q9Y3Z3
STING1Stimulator of interferon genes proteinCandidate gene tested inTolerante
FUNÇÃO

Facilitator of innate immune signaling that acts as a sensor of cytosolic DNA from bacteria and viruses and promotes the production of type I interferon (IFN-alpha and IFN-beta) (PubMed:18724357, PubMed:18818105, PubMed:19433799, PubMed:19776740, PubMed:23027953, PubMed:23747010, PubMed:23910378, PubMed:27801882, PubMed:29973723, PubMed:30842659, PubMed:35045565, PubMed:35388221, PubMed:36808561, PubMed:37832545, PubMed:25704810, PubMed:39255680). Innate immune response is triggered in response

LOCALIZAÇÃO

Endoplasmic reticulum membraneCytoplasm, perinuclear regionEndoplasmic reticulum-Golgi intermediate compartment membraneGolgi apparatus membraneCytoplasmic vesicle, autophagosome membraneMitochondrion outer membraneCell membrane

VIAS BIOLÓGICAS (5)
SARS-CoV-2 activates/modulates innate and adaptive immune responsesSTING mediated induction of host immune responsesRegulation of innate immune responses to cytosolic DNASARS-CoV-1 activates/modulates innate immune responsesDengue virus activates/modulates innate and adaptive immune responses
MECANISMO DE DOENÇA

STING-associated vasculopathy, infantile-onset

An autoinflammatory disease characterized by early-onset systemic inflammation and cutaneous vasculopathy, resulting in severe skin lesions. Violaceous, scaling lesions of fingers, toes, nose, cheeks and ears progress to acral necrosis in most of the patients. Some patients have severe interstitial lung disease.

OUTRAS DOENÇAS (2)
STING-associated vasculopathy with onset in infancyfamilial chilblain lupus
HGNC:27962UniProt:Q86WV6

Variantes genéticas (ClinVar)

1,607 variantes patogênicas registradas no ClinVar.

🧬 STING1: NM_198282.4(STING1):c.473G>T (p.Gly158Val) ()
🧬 STING1: NM_198282.4(STING1):c.439G>A (p.Val147Met) ()
🧬 STING1: NM_198282.4(STING1):c.852G>C (p.Arg284Ser) ()
🧬 STING1: NM_198282.4(STING1):c.683A>G (p.Gln228Arg) ()
🧬 STING1: NM_198282.4(STING1):c.659G>T (p.Arg220Leu) ()
Ver todas no ClinVar

Diagnóstico

Os sinais que médicos procuram e os exames que confirmam

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Tratamento e manejo

Remédios, cuidados de apoio e o que precisa acompanhar

Pipeline de tratamentos
Pipeline regulatório — de medicamentos já aprovados a drogas em pesquisa exploratória.
3Fase 35
2Fase 26
1Fase 12
·Pré-clínico2
Medicamentos catalogadosEnsaios clínicos· 0 medicamentos · 15 ensaios
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Onde tratar no SUS

Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

🇧🇷 Atendimento SUS — Lúpus eritematoso cutâneo crônico

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Selecione um estado ou use sua localização para ver resultados.

Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.

Pesquisa ativa

Ensaios clínicos abertos e novidades científicas recentes

🟢 Recrutando agora

7 pesquisas recrutando participantes. Converse com seu médico sobre a possibilidade de participar.

Outros ensaios clínicos

35 ensaios clínicos encontrados, 8 ativos.

Distribuição por fase
Ver todos no ClinicalTrials.gov
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Publicações mais relevantes

Timeline de publicações
128 papers (10 anos)
#1

Prevalence and Risk Factors of Systemic Lupus Erythematosus in Patients With Chronic Cutaneous Lupus: A Bicentric Study Employing Three Classification Criteria.

International journal of dermatology2026 Mar 25

Chronic cutaneous lupus erythematosus (CCLE) is the most common form of cutaneous lupus erythematosus, accounting for about 80% of cases. While patients with CCLE can develop systemic lupus erythematosus (SLE), the prevalence and risk factors of this association remain poorly studied, especially in North African populations. We conducted a bicentric study including all patients with histologically confirmed CCLE in two tertiary referral hospitals in Tunis between 2013 and 2023. SLE was classified using three criteria sets: ACR 1997, SLICC 2012, and ACR/EULAR 2019. Univariate and multivariate analyses were performed. Ninety-five patients with CCLE (median age 48 years, 75% female) were included. The prevalence of SLE varied significantly depending on the classification criteria used: 24% with ACR 1997, 32% with SLICC 2012, and 21% with ACR/EULAR 2019. Independent risk factors for SLE included arthralgias consistently across all classification criteria. Other risk factors for SLE differed among classification systems. For instance, asthenia and elevated ESR were independent risk factors under the ACR 1997 criteria, while female sex and extensive skin involvement were unique to the SLICC 2012 criteria. This study, the largest in North Africa aiming to identify the prevalence and risk factors of SLE among CCLE patients, showed significant variability depending on the used classification criteria. Arthralgias represented an independent risk factor for SLE in CCLE patients. The findings of this study were used to develop a diagnostic algorithm to assist clinicians.

#2

Palmar Cutaneous Erythematous Macules: A Case Report of an Atypical Presentation of Chilblain Lupus Erythematosus.

Cureus2026 Feb

Systemic lupus erythematosus (SLE) manifests with a broad spectrum of cutaneous manifestations, including chilblain lupus erythematosus (CHLE), which typically presents as cold-induced, painful acral lesions with specific dermatoscopic and histopathologic features. We describe an unusual case of a 32-year-old woman with established SLE and stage IV lupus nephritis who presented with a five-year history of asymptomatic, recurrent erythematous macules on the palms.  The patient reported no cold sensitivity, pain, or Raynaud's phenomenon, which are hallmark features of classic CHLE. Physical examination revealed irregularly shaped pink macules and patches on the volar aspect of the fingers and thumb base and dorsal hands, sparing the palms. Dermoscopy showed well-demarcated, non-scaling pink macules with nonspecific white dots and sparing of palmar skin lines. Histopathological analysis demonstrated superficial and deep perivascular lymphocytic infiltrates with increased dermal mucin. Direct immunofluorescence revealed granular IgM and IgG deposits at the dermoepidermal junction, supporting a lupus-related process. Although the patient met the histopathologic and minor clinical criteria for CHLE, the absence of cold triggers and pain suggests an atypical presentation of CHLE or a distinct variant of lupus-associated palmar macules. Differential diagnoses, including dermatomyositis and small-vessel vasculitis, were excluded through clinical and laboratory evaluations. This case highlights the clinical variability of cutaneous lupus and the diagnostic challenges posed by palmar lesions that do not strictly adhere to established diagnostic criteria for CHLE. Lupus erythematosus is a multisystem disorder that predominantly affects the skin. There are many types of lupus, including systemic lupus erythematosus (SLE), drug-induced lupus erythematosus, neonatal lupus erythematosus, and cutaneous lupus erythematosus. The most common types of cutaneous lupus erythematosus include acute cutaneous lupus erythematosus, subacute cutaneous lupus erythematosus, and chronic cutaneous lupus erythematosus; discoid lupus erythematosus is a subtype of chronic cutaneous lupus erythematosus. Dr James Gilliam described the most commonly used classification of cutaneous lesions in lupus erythematosus. He distinguished lesions as either specific or nonspecific, based on the presence of interface dermatitis on histopathologic examination. Within the category of specific cutaneous lesions, he subdivided these into acute cutaneous lupus erythematosus, subacute cutaneous lupus erythematosus, and chronic cutaneous erythematosus. Discoid lupus erythematosus is the most common subset of chronic cutaneous lupus erythematosus. Patients may or may not report photosensitivity, but lesions are frequently photodistributed and often exhibit secondary atrophy or scarring. Most patients with discoid lupus erythematosus do not have significant systemic disease. Discoid lupus erythematosus can also occur as a manifestation of SLE in approximately 20% of patients. Other less common variants of chronic cutaneous lupus erythematosus include hypertrophic lupus erythematosus, tumid lupus erythematosus, lupus erythematosus panniculitis (also known as lupus profundus), chilblain lupus erythematosus, oral discoid lupus erythematosus, and discoid lupus erythematosus lesions on the palms and soles.

#3

Generalized verrucous discoid lupus erythematosus.

Journal of the European Academy of Dermatology and Venereology : JEADV2026 Jan 23
#4

Chronic Cutaneous Lupus Erythematosus Presenting as Acne Scars: A Case Report.

Case reports in dermatology2025

Chronic cutaneous lupus erythematosus (CCLE) is a subtype of lupus erythematosus that primarily affects sun-exposed areas, resulting in atrophic scarring and dyspigmentation. While its classic presentation involves erythematous, scaly plaques with follicular plugging, rare clinical variants have been described. Among these, acneiform or comedonal CCLE can closely mimic acne vulgaris, leading to delayed diagnosis and inappropriate management. A 49-year-old woman presented with multiple facial scars after more than 20 years of unsuccessful acne treatments. Physical examination revealed deep atrophic scars and pseudocomedones on the cheeks and chin, along with erythematous, scaly plaques on the ear, and an alopecic patch on the scalp. A skin biopsy showed a picture of CCLE. A diagnosis of CCLE presenting as acne scar was concluded. The patient responded well to hydroxychloroquine followed by successful surgical scar revision. Acneiform CCLE is a rare and often misdiagnosed variant. Dermatologists should consider it in patients with treatment-resistant "acne," particularly when lesions are scarring or involve sun-exposed sites, as early diagnosis and appropriate therapy can prevent irreversible disfigurement.

#5

Efficacy of Belimumab on Different Joint and Skin Manifestations of Systemic Lupus Erythematosus: Real-Life Data from a New Multicentric, Nationwide Italian Cohort (BeRLiSS-JS 2.0).

Biologics : targets & therapy2025

To evaluate the effectiveness of belimumab in different joint and skin phenotypes of systemic lupus erythematosus (SLE). The BeRLiSS-JS 2.0 is a decade-long observational study including adult SLE patients from 14 Italian Centers treated with belimumab (intravenous/subcutaneous) stratified by articular (nondeforming nonerosive arthritis -NDNE-, Jaccoud's arthropathy, Rhupus) and cutaneous phenotypes (acute -ACLE-, subacute -SCLE-, and chronic cutaneous lupus erythematosus -CCLE-, and nonspecific manifestations). Outcome variables measured every 6 months up to 36 months included Disease Activity Score-28 joints (DAS28) and Cutaneous Lupus Erythematosus Disease Area and Severity Index (CLASI) scores, remission rates (DAS28<2.6; CLASI-A=0), and prednisone intake (mg/day). Of 443 patients, 221 (49.9%) had NDNE, 30 (6.8%) Jaccoud's arthropathy, 21 (4.7%) rhupus, 112 (25.3%) had ACLE, 54 (12.2%) SCLE, and 18 (4.1%) CCLE. At 6 months a significant decrease of DAS28 was observed in NDNE (p<0.001) and by CLASI-A in ACLE and SCLE (both p<0.001). Non-specific cutaneous manifestations did not improve significantly. CLASI-D scores remained stable over 36 months. Remission rates were higher in NDNE and ACLE patients (at 6 months: NDNE 59.6%, Jaccoud's 18.8%, rhupus 30.3% - p=0.002; at 18 months: ACLE 75.9%, SCLE 56.4%, CCLE 33.3% - p=0.018). Daily prednisone dosage decreased in all organ-specific phenotypes, but more pronouncedly in patients with NDNE, ACLE, and SCLE. Higher baseline CLASI-A and DAS28 and CLASI-D were associated with lower remission rates. Treatment with belimumab was associated with reduced disease activity and increased remission especially in NDNE and ACLE patients. Glucocorticoid-sparing effect was also found. Belimumab is known to be an effective treatment for systemic lupus erythematosus (SLE), achieving the highest level of recommendation for non-responders to hydroxychloroquine/immunosuppressive agents (1a/A), while reaching a level B for active cutaneous involvement (1a/B) in the latest EULAR recommendations. On the other hand, belimumab effectiveness across different joint and skin phenotypes of SLE had not been thoroughly evaluated. This study was necessary to understand how belimumab performs in specific SLE phenotypes, such as nondeforming nonerosive arthritis (NDNE), Jaccoud’s arthropathy, rhupus, and various cutaneous manifestations (acute, subacute, chronic, and nonspecific) by using disease specific and validated clinimetric measures, such as DAS28 and CLASI. Belimumab significantly decreased disease activity and improved remission rates especially in NDNE and acute cutaneous lupus erythematosus (ACLE) patients while also highlighting a glucocorticoid-sparing effect particularly in NDNE, ACLE, and subacute cutaneous lupus erythematosus (SCLE) patients. Therefore, these findings suggest that belimumab could be more beneficial for patients with NDNE and ACLE than other phenotypes, potentially guiding more personalized treatment approaches in clinical practice.

Publicações recentes

Ver todas no PubMed

📚 EuropePMC81 artigos no totalmostrando 122

2026

Prevalence and Risk Factors of Systemic Lupus Erythematosus in Patients With Chronic Cutaneous Lupus: A Bicentric Study Employing Three Classification Criteria.

International journal of dermatology
2026

Palmar Cutaneous Erythematous Macules: A Case Report of an Atypical Presentation of Chilblain Lupus Erythematosus.

Cureus
2026

Generalized verrucous discoid lupus erythematosus.

Journal of the European Academy of Dermatology and Venereology : JEADV
2025

Chronic Cutaneous Lupus Erythematosus Presenting as Acne Scars: A Case Report.

Case reports in dermatology
2025

Efficacy of Belimumab on Different Joint and Skin Manifestations of Systemic Lupus Erythematosus: Real-Life Data from a New Multicentric, Nationwide Italian Cohort (BeRLiSS-JS 2.0).

Biologics : targets &amp; therapy
2025

Koebner Phenomenon Induced by Eyeglasses in a Patient With Discoid Lupus Erythematosus.

Case reports in dermatological medicine
2025

Erbium-doped nonablative fractional laser therapy for postinflammatory hyperpigmentation and atrophic scarring due to discoid lupus erythematosus in a patient with systemic lupus erythematosus.

JAAD case reports
2025

A Case Report of Atypical Presentation of Systemic Lupus Erythematosus in a Young Child.

International journal of rheumatic diseases
2025

Comedogenic Lupus in a 13-Year-Old Female: A Unique Pediatric Case.

Pediatric dermatology
2025

Anifrolumab for Nonsystemic Cutaneous Lupus Erythematosus: Clinical Experience, Immunologic Insights, and Review of the Literature.

Journal of clinical medicine
2025

High-Frequency Ultrasonography in Cutaneous Lupus Erythematosus.

Skin research and technology : official journal of International Society for Bioengineering and the Skin (ISBS) [and] International Society for Digital Imaging of Skin (ISDIS) [and] International Society for Skin Imaging (ISSI)
2024

A Case of Rowell Syndrome: Excellent Response to Oral Cyclosporine.

Acta dermatovenerologica Croatica : ADC
2025

Comedonal Plaques With Scarring Alopecia on the Scalp: A Case Report.

Cureus
2025

A20 haploinsufficiency diagnosis beyond systemic lupus erythematosus: A systematic review of the literature.

Autoimmunity reviews
2025

Immunohistochemical Expression of Immune Regulatory Proteins in Interface Dermatoses.

Journal of cutaneous pathology
2024

Trichoscopy of Discoid Lupus Erythematosus in the Black Scalp: A Literature Review.

Skin appendage disorders
2024

Impressive resolution of refractory hypertrophic discoid lupus erythematosus with anifrolumab.

BMJ case reports
2024

Lupus Erythematosus Tumidus as a Distinct Uncommon Subtype of Cutaneous Lupus Erythematosus: A Case Report and Review.

Cureus
2024

Tumid Lupus Erythematosus (TLE): A Review of a Rare Variant of Chronic Cutaneous Lupus Erythematosus (cCLE) with Emphasis on Differential Diagnosis.

Diagnostics (Basel, Switzerland)
2024

Efficacy of anifrolumab in long-term intractable alopecia due to discoid lupus erythematosus.

Modern rheumatology case reports
2024

A gyrate pattern of discoid lupus erythematosus.

The Journal of dermatology
2023

Case series of anifrolumab for treatment of cutaneous lupus erythematosus and lupus-related mucocutaneous manifestations in patients with SLE.

Lupus science &amp; medicine
2023

The realistic positioning of UVA1 phototherapy after 25 years of clinical experience and the availability of new biologics and small molecules: a retrospective clinical study.

Frontiers in medicine
2023

Lupus Erythematosus Profundus with Multiple Overlying Cutaneous Ulcerations: A Rare Case.

Clinical, cosmetic and investigational dermatology
2023

Lupus mastitis and antiphospholipid syndrome treated with anticoagulation and immunosuppression: a case report.

Journal of medical case reports
2023

Ocular Discoid Lupus Erythematosus: More Than what Meets The Eye.

Indian dermatology online journal
2023

Tumid Lupus Erythematosus Presenting as Patchy Alopecia: A Discussion of Alopecia Associated With Lupus Erythematosus.

Cureus
2023

Comedonic lupus, a rare variant of chronic cutaneous lupus erythematosus (CCLE): case series and literature review.

International journal of dermatology
2023

Scleroderma-Like Lupus Panniculitis: A Case Report and Literature Review.

Clinical, cosmetic and investigational dermatology
2023

Lupus panniculitis: a rare bilateral and symmetrical manifestation of cutaneous lupus erythematosus in an adolescent girl.

Dermatology reports
2023

Panoramic view of clinical features of lupus erythematosus: a cross-sectional multicentre study from China.

Lupus science &amp; medicine
2023

Autoimmune Skin Conditions: Cutaneous Lupus Erythematosus.

FP essentials
2023

Pigmented Macular Variant of Chronic Cutaneous Lupus Erythematosus: Clinico-dermoscopic Features of Three Patients With Skin of Color.

Dermatology practical &amp; conceptual
2023

Comedogenic lupus: a rare variant of chronic cutaneous lupus erythematosus - case series.

Anais brasileiros de dermatologia
2024

Exacerbation of Chronic Cutaneous Lupus Erythematosus Triggered by Vaccine Against COVID-19.

Actas dermo-sifiliograficas
2022

Drug-Induced Photosensitivity: Clinical Types of Phototoxicity and Photoallergy and Pathogenetic Mechanisms.

Frontiers in allergy
2023

Effective treatment of canine chronic cutaneous lupus erythematosus variants with oclacitinib: Seven cases.

Veterinary dermatology
2022

Identification of Significant Genes and Pathways for the Chronic and Subacute Cutaneous Lupus Erythematosus via Bioinformatics Analysis.

Disease markers
2023

Cutaneous Involvement in Systemic Lupus Erythematosus: A Review for the Rheumatologist.

The Journal of rheumatology
2022

Clinicopathological characteristics of cutaneous lupus erythematosus patients in Bangladesh.

Postepy dermatologii i alergologii
2022

Chronic Cutaneous Lupus Erythematosus in a White Population: Dermoscopic Characteristics by Clinical Subtype, Lesion Location and Disease Duration.

Dermatology and therapy
2022

Lupus Erythematosus Tumidus Clinical Characteristics and Treatment: A Retrospective Review of 25 Patients.

Cutis
2022

Depression, stigma and social isolation: the psychosocial trifecta of primary chronic cutaneous lupus erythematosus, a cross-sectional and path analysis.

Lupus science &amp; medicine
2022

Melanotic lupus erythematosus: A review of a newly described clinical form of chronic cutaneous lupus erythematosus.

Clinics in dermatology
2021

Discoid lupus erythematosus of eyelids - Diagnostic and therapeutic challenges.

Saudi journal of ophthalmology : official journal of the Saudi Ophthalmological Society
2022

Rituximab Used for the Treatment of Nonuremic Calciphylaxis: A Complication of Prolonged Steroid Use in Lupus Nephritis.

Cureus
2022

Linear Cutaneous Lupus Erythematosus Following Blaschko's Lines on the Scalp: Additional Cases and Review of the Literature.

HCA healthcare journal of medicine
2021

Postsurgical Appearance of Chilblains Lupus Erythematosus.

Journal of hand surgery global online
2022

Lupus Erythematosus Tumidus Associated With Hemophagocytosis.

The American Journal of dermatopathology
2021

Comedonal Lupus: An Unusual Presentation of Chronic Cutaneous Lupus Erythematosus.

Skinmed
2022

Treatment of Hyperpigmented Discoid Lupus Erythematosus With Jessner's Peel: A Case Report.

Journal of drugs in dermatology : JDD
2021

Koebner phenomenon in a patient with hypertrophic chronic cutaneous lupus erythematosus.

Postepy dermatologii i alergologii
2021

Gene Expression Profiling in the Skin Reveals Strong Similarities between Subacute and Chronic Cutaneous Lupus that Are Distinct from Lupus Nephritis.

The Journal of investigative dermatology
2021

Cutaneous Manifestations of "Lupus": Systemic Lupus Erythematosus and Beyond.

International journal of rheumatology
2021

B cell subset composition segments clinically and serologically distinct groups in chronic cutaneous lupus erythematosus.

Annals of the rheumatic diseases
2021

Clinical features of tumor necrosis factor-α-inhibitor induced chilblain lupus: A case series.

JAAD case reports
2021

Emerging Skin Toxicities in Patients with Breast Cancer Treated with New Cyclin-Dependent Kinase 4/6 Inhibitors: A Systematic Review.

Drug safety
2021

Comedonal plaque on the scalp.

JAAD case reports
2021

Bioinformatic analysis of key biomarkers and immune filtration of skin biopsy in discoid lupus erythematosus.

Lupus
2020

Nonisomorphic and Nonisotopic Multidermatomal Discoid Lupus Erythematosus - A Rare Subtype of Cutaneous Lupus Erythematosus.

Indian dermatology online journal
2021

Development of chronic cutaneous lupus erythematosus during biologic therapy: A systematic review.

Journal of the American Academy of Dermatology
2021

The combined role of clinical, reflectance confocal microscopy and dermoscopy applied to chronic discoid cutaneous lupus and subacutus lupus erythematosus: A case series and literature review.

Lupus
2020

Progression of Discoid Lupus to Lupus Panniculitis: An Unexplained and Likely Underreported Phenomenon.

Cureus
2020

Comedonal variant of chronic cutaneous lupus erythematosus causing mutilation of the earlobe.

JAAD case reports
2020

Reversibility of alopecia caused by chronic cutaneous lupus erythematosus.

International journal of dermatology
2020

Chronic cutaneous lupus erythematosus induced by 5-fluorouracil.

Expert review of clinical pharmacology
2020

Tumid Lupus Erythematosus: A Rare and Distinctive Variant of Cutaneous Lupus Erythematosus Masquerading as Urticarial Vasculitis.

Cureus
2020

Cutaneous lupus erythematosus: factors related to cutaneous activity and damage in a cohort of 260 patients from A Coruña, Spain.

Lupus
2020

Scarring alopecia in chronic cutaneous lupus erythematosus with neutrophils: A new scenario with therapeutic connotations.

Journal of cutaneous pathology
2020

Cosmetic treatment in patients with autoimmune connective tissue diseases: Best practices for patients with lupus erythematosus.

Journal of the American Academy of Dermatology
2020

Persistent Facial Oedema and Erythema in a Woman, An Uncommon Manifestation of Chronic Cutaneous Lupus Erythematosus.

European journal of case reports in internal medicine
2020

A Case of Tolosa-Hunt Syndrome With Discoid Lupus Erythematosus.

The Neurohospitalist
2020

Chronic cutaneous lupus erythematosus (discoid lupus) induced by palbociclib.

International journal of dermatology
2019

An atypical clinical presentation of alopecia in 2 patients with systemic lupus erythematosus.

JAAD case reports
2020

A secondary discoid lupus erythematosus induced by scald of edible oil: An illustration of Koebner phenomenon.

Journal of cosmetic dermatology
2019

Current Insights Into The Management Of Discoid Lupus Erythematosus.

Clinical, cosmetic and investigational dermatology
2019

A comedonal variant of chronic cutaneous lupus erythematosus: Case report and literature review.

JAAD case reports
2019

Spectrum of cutaneous lupus erythematosus in South Africans with systemic lupus erythematosus.

Lupus
2019

An Unusual Morphological and Distribution Pattern of Chronic Cutaneous Lupus Erythematosus.

Indian dermatology online journal
2019

In silico Analyses of Skin and Peripheral Blood Transcriptional Data in Cutaneous Lupus Reveals CCR2-A Novel Potential Therapeutic Target.

Frontiers in immunology
2019

Chronic Cutaneous Lupus Erythematosus: Depression Burden and Associated Factors.

American journal of clinical dermatology
2019

Intravenous immunoglobulin G use in patients with chronic inflammatory demyelinating polyneuropathy: An uncommon cause of drug-induced discoid lupus erythematosus.

The Australasian journal of dermatology
2018

Skin signs in juvenile- and adult-onset systemic lupus erythematosus: clues to different systemic involvement.

Lupus
2018

Chronic cutaneous lupus erythematosus and topical clindamycin.

BMJ case reports
2018

Fogo selvagem: endemic pemphigus foliaceus.

Anais brasileiros de dermatologia
2018

Lupus panniculitis: Clinicopathological features of a series of 12 patients.

Medicina clinica
2018

Periorbital erythema and swelling as a presenting sign of lupus erythematosus in tertiary referral centers and literature review.

Lupus
2018

A comprehensive review of immune-mediated dermatopathology in systemic lupus erythematosus.

Journal of autoimmunity
2018

Disease severity and prophylactic measures in patients with cutaneous lupus erythematosus: results of a worldwide questionnaire-based study.

Postepy dermatologii i alergologii
2018

CXCL13 is an activity marker for systemic, but not cutaneous lupus erythematosus: a longitudinal cohort study.

Archives of dermatological research
2018

Coexistence of chronic cutaneous lupus erythematosus and frontal fibrosing alopecia.

Anais brasileiros de dermatologia
2018

Chronic Cutaneous Lupus Erythematosus in a Blaschkoid Pattern over Face.

Indian journal of dermatology
2019

Racial Disparities in the Incidence of Primary Chronic Cutaneous Lupus Erythematosus in the Southeastern US: The Georgia Lupus Registry.

Arthritis care &amp; research
2018

Bizarre appearance of chronic cutaneous lupus erythematosus of face mimicking factitial dermatitis.

Journal of the European Academy of Dermatology and Venereology : JEADV
2018

The involvement of galectin-3 in skin injury in systemic lupus erythematosus patients.

Lupus
2017

Chronic cutaneous lupus erythematosus revealed by unilateral eyelid oedema.

European journal of dermatology : EJD
2017

Cutaneous Lupus: A Brief Review of Old and New Medical Therapeutic Options.

The journal of investigative dermatology. Symposium proceedings
2018

Chronic cutaneous lupus erythematosus presenting as atypical acneiform and comedonal plaque: case report and literature review.

Lupus
2017

Histologic features of chronic cutaneous lupus erythematosus of the scalp using horizontal sectioning: Emphasis on follicular findings.

Journal of the American Academy of Dermatology
2017

Pigmented macular variant of chronic cutaneous lupus erythematosus: an under-recognized subset in dark skin.

Clinical and experimental dermatology
2017

Lupus profundus limited to a site of trauma: Case report and review of the literature.

International journal of women's dermatology
2017

The Increased Expression of Toll-Like Receptor 4 in Renal and Skin Lesions in Lupus Erythematosus.

The journal of histochemistry and cytochemistry : official journal of the Histochemistry Society
2017

Lupus erythematosus tumidus of the scalp masquerading as alopecia areata.

Cutis
2016

Lupus tumidus: a report of two cases.

Anais brasileiros de dermatologia
2016

[Systemic lupus erythematosus : Unusual cutaneous manifestations].

Der Hautarzt; Zeitschrift fur Dermatologie, Venerologie, und verwandte Gebiete
2016

Primary cicatricial alopecia: Lymphocytic primary cicatricial alopecias, including chronic cutaneous lupus erythematosus, lichen planopilaris, frontal fibrosing alopecia, and Graham-Little syndrome.

Journal of the American Academy of Dermatology
2016

Clinical and microscopic features of generalized discoid lupus erythematosus in dogs (10 cases).

Veterinary dermatology
2016

Cutaneous sarcoidosis masquerading as chronic cutaneous lupus erythematosus - case report.

BMC dermatology
2016

Linear cutaneous lupus erythematosus following the lines of Blaschko - Case report.

Anais brasileiros de dermatologia
2017

Methimazole-induced chronic cutaneous lupus erythematosus.

Journal of the European Academy of Dermatology and Venereology : JEADV
2016

CD123 immunohistochemistry for plasmacytoid dendritic cells is useful in the diagnosis of scarring alopecia.

Journal of cutaneous pathology
2016

Lupus Panniculitis as an Initial Manifestation of Systemic Lupus Erythematosus: A Case Report.

Medicine
2016

Unilateral unique Lupus tumidus: pathogenetic mystery and diagnostic problem.

Wiener medizinische Wochenschrift (1946)
2015

Blisters and Loss of Epidermis in Patients With Lupus Erythematosus: A Clinicopathological Study of 22 Patients.

Medicine
2016

Differentiation of Jessner's Lymphocytic Infiltration of the Skin from Various Chronic Cutaneous Lupus Erythematosus Subtypes by Quantitative Computer-Aided Image Analysis.

Dermatology (Basel, Switzerland)
2015

Apoptosis in chronic cutaneous lupus erythematosus, discoid lupus, and lupus profundus.

International journal of clinical and experimental pathology
2015

Genome-wide transcriptional profiling data from skin of chronic cutaneous lupus erythematosus (CCLE) patients.

Data in brief
2015

Genome-wide transcriptional profiling data from chronic cutaneous lupus erythematosus (CCLE) peripheral blood.

Data in brief
2015

Treatment of Scarring Alopecia in Discoid Variant of Chronic Cutaneous Lupus Erythematosus With Tacrolimus Lotion, 0.3.

JAMA dermatology
2015

Cutaneous lupus erythematosus in skin of color.

Journal of drugs in dermatology : JDD
2015

Magnetic resonance imaging findings are useful for evaluating the three-dimensional development and follow-up of linear lupus erythematosus profundus.

Lupus
2015

Brief report: responses to rituximab suggest B cell-independent inflammation in cutaneous systemic lupus erythematosus.

Arthritis &amp; rheumatology (Hoboken, N.J.)

Associações

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Comunidades

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Doenças relacionadas

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Referências e fontes

Bases de dados externas citadas neste artigo

Publicações científicas

Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.

  1. Prevalence and Risk Factors of Systemic Lupus Erythematosus in Patients With Chronic Cutaneous Lupus: A Bicentric Study Employing Three Classification Criteria.
    International journal of dermatology· 2026· PMID 41877623mais citado
  2. Palmar Cutaneous Erythematous Macules: A Case Report of an Atypical Presentation of Chilblain Lupus Erythematosus.
    Cureus· 2026· PMID 41822629mais citado
  3. Generalized verrucous discoid lupus erythematosus.
    Journal of the European Academy of Dermatology and Venereology : JEADV· 2026· PMID 41575073mais citado
  4. Chronic Cutaneous Lupus Erythematosus Presenting as Acne Scars: A Case Report.
    Case reports in dermatology· 2025· PMID 41357617mais citado
  5. Efficacy of Belimumab on Different Joint and Skin Manifestations of Systemic Lupus Erythematosus: Real-Life Data from a New Multicentric, Nationwide Italian Cohort (BeRLiSS-JS 2.0).
    Biologics : targets &amp; therapy· 2025· PMID 41190171mais citado
  6. A Unique Case of Lupus Erythematosus Profundus Presenting With Localized Scarring Alopecia and Perioral Swelling in a Pediatric Patient.
    Cureus· 2026· PMID 41994712recente
  7. Cutaneous Squamous Cell Carcinoma Arising in Discoid Lupus Erythematosus: A Systematic Review and Meta-analysis.
    J Cutan Med Surg· 2026· PMID 41914714recente
  8. Discoid Lupus Erythematosus.
    · 2026· PMID 29630197recente

Bases de dados e fontes oficiais

Identificadores e referências canônicas usadas para montar este verbete.

  1. ORPHA:163531(Orphanet)
  2. MONDO:0015574(MONDO)
  3. Lupus Eritematoso Sistemico(PCDT · Ministério da Saúde)
  4. GARD:20043(GARD (NIH))
  5. Variantes catalogadas(ClinVar)
  6. Busca completa no PubMed(PubMed)
  7. Q55785567(Wikidata)

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Lúpus eritematoso cutâneo crônico
Compêndio · Raras BR

Lúpus eritematoso cutâneo crônico

ORPHA:163531 · MONDO:0015574
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CID-11
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Adolescent, Adult, Childhood, Elderly
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C0024138
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dexamethasoneglucocorticoid receptor agonist
dexamethasone-acetate
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