Raras
Buscar doenças, sintomas, genes...
Miopatia e fasciite inflamatórias adquiridas
ORPHA:98482CID-11 · 4A41DOENÇA RARA

Termo genérico para doenças que apresentam inflamação muscular crônica e fraqueza de etiologia desconhecida. Os tipos de miopatia inflamatória idiopática são ainda definidos por critérios clinicopatológicos ou pela presença de certos autoanticorpos.

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Introdução

O que você precisa saber de cara

📋

Termo genérico para doenças que apresentam inflamação muscular crônica e fraqueza de etiologia desconhecida. Os tipos de miopatia inflamatória idiopática são ainda definidos por critérios clinicopatológicos ou pela presença de certos autoanticorpos.

Pesquisas ativas
14 ensaios
416 total registrados no ClinicalTrials.gov
Publicações científicas
1.217 artigos
Último publicado: 2026 Apr 15
Medicamentos
14 registrados
PREDNISOLONE, CORTISONE ACETATE, PREDNISONE

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14 medicamentos registrados
Ver detalhes, fases e interações →
PREDNISOLONECORTISONE ACETATEPREDNISONEABATACEPTBARICITINIBANIFROLUMABMETHOTREXATEALDESLEUKINUSTEKINUMABBREPOCITINIB

Escala de raridade

CLASSIFICAÇÃO ORPHANET · BRASIL 2024
Unknown
Ultra-rara
<1/50k
Muito rara
1/20k
Rara
1/10k
Pouco freq.
1/5k
Incomum
1/2k
Prevalência
0.0
Worldwide
🏥
SUS: Sem cobertura SUSScore: 0%
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Sinais e sintomas

O que aparece no corpo e com que frequência cada sintoma acontece

Partes do corpo afetadas

💪
Músculos
19 sintomas
🧬
Pele e cabelo
14 sintomas
❤️
Coração
14 sintomas
🫁
Pulmão
9 sintomas
🩸
Sangue
8 sintomas
🫃
Digestivo
8 sintomas

+ 85 sintomas em outras categorias

Características mais comuns

Aplasia/Hipoplasia da pele
Camptocormia
Aperto no peito
Condução atrioventricular anormal
Trombose venosa
Cardiomiopatia dilatada
183sintomas
Sem dados (183)

Os sintomas variam de pessoa para pessoa. Abaixo estão as 183 características clínicas mais associadas, ordenadas por frequência.

Aplasia/Hipoplasia da peleAplasia/Hypoplasia of the skin
Camptocormia
Aperto no peitoChest tightness
Condução atrioventricular anormalAbnormal atrioventricular conduction
Trombose venosaVenous thrombosis

Linha do tempo da pesquisa

Publicações por ano — veja quando o interesse científico cresceu
Anos de pesquisa1desde 2026
Total histórico1.217PubMed
Últimos 10 anos200publicações
Pico2025151 papers
Linha do tempo
2026Hoje · 2026🧪 1992Primeiro ensaio clínico📈 2025Ano de pico
Publicações por ano (últimos 10 anos)

Encontrou um erro ou informação desatualizada? Sugira uma correção →

Genética e causas

O que está alterado no DNA e como passa nas famílias

🧬

Nenhum gene associado encontrado

Os dados genéticos desta condição ainda estão sendo catalogados.

Diagnóstico

Os sinais que médicos procuram e os exames que confirmam

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Tratamento e manejo

Remédios, cuidados de apoio e o que precisa acompanhar

Pipeline de tratamentos
Pipeline regulatório — de medicamentos já aprovados a drogas em pesquisa exploratória.
Aprovado4
3Fase 310
2Fase 21
1Fase 18
·Pré-clínico6
Medicamentos catalogadosEnsaios clínicos· 10 medicamentos · 19 ensaios
✓ Aprovados — podem ser usados hoje
PREDNISOLONECORTISONE ACETATEPREDNISONE
Carregando informações de tratamento...

Onde tratar no SUS

Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

🇧🇷 Atendimento SUS — Miopatia e fasciite inflamatórias adquiridas

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Selecione um estado ou use sua localização para ver resultados.

Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.

Pesquisa ativa

Ensaios clínicos abertos e novidades científicas recentes

🟢 Recrutando agora

13 pesquisas recrutando participantes. Converse com seu médico sobre a possibilidade de participar.

Outros ensaios clínicos

416 ensaios clínicos encontrados, 14 ativos.

Distribuição por fase
Ver todos no ClinicalTrials.gov
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Publicações mais relevantes

Timeline de publicações
953 papers (10 anos)

Mostrando amostra de 200 publicações de um total de 953

#1

[Expression of the melanoma 2-mediated pyroptosis pathway in peripheral blood mononuclear cells of patients with idiopathic inflammatory myopathies].

Beijing da xue xue bao. Yi xue ban = Journal of Peking University. Health sciences2026 Feb 18

To detect the expression levels of absence in melanoma 2 (AIM2), cysteine aspartate-specific protease-1 (caspase-1), and gasdermin D (GSDMD) in peripheral blood mononuclear cell (PBMC) of patients with idiopathic inflammatory myopathy (IIM) and to explore their role in the pathogenesis of IIM. A total of 30 IIM patients (IIM group) who visited the Department of Rheumatology and Immunology, General Hospital of Northern Theater Command from May 2020 to June 2022 were recruited. Concurrently, 30 healthy volunteers matched by gender and age were recruited from the hospital's Health Examination Center. Clinical information, biochemical and immunological mar-kers, and venous blood samples were collected from the study subjects. Serum double-stranded DNA (dsDNA) levels were detected by fluorescence quantitative method, and the mRNA expression levels of AIM2, caspase-1, GSDMD, interleukin 1β (IL-1β), and IL-18 in PBMC were detected by reverse transcription quantitative real-time PCR (RT-qPCR). The protein expression levels of AIM2, caspase-1, GSDMD, IL-1β, and IL-18 in PBMC were detected using the Western blot (WB) method, and the serum levels of IL-1β and IL-18 were detected by enzyme-linked immunosorbent assay (ELISA). The IIM group included 10 cases of dermatomyositis (DM), 5 cases of polymyositis (PM), 11 cases of overlap syndrome (OM), and 4 cases of immune-mediated necrotizing myopathy (IMNM). Compared with the healthy control group, the serum levels of dsDNA, IL-1β, and IL-18 were significantly increased in the IIM group and its subgroups (P < 0.05). Except for the fact that there was no statistically significant difference in AIM2 mRNA levels in PBMC of the IMNM subgroup compared to the healthy control group, the expression of AIM2, caspase-1, and GSDMD mRNA was significantly increased in the IIM group and other subgroups (P < 0.05); Except for the comparison of IL-1β mRNA levels in PBMC of the IMNM and OM subgroups with the healthy control group showing no statistical difference, the expression of IL-1β and IL-18 mRNA was significantly increased in the IIM group and other subgroups (P < 0.05); Comparisons between subgroups indicated that the expression of IL-1β mRNA in the DM subgroup was significantly higher than that in the OM and IMNM subgroups, and the expression of IL-18 mRNA in the PM subgroup was significantly higher than that in the DM and OM subgroups (P < 0.05). The expression levels of AIM2, caspase-1, GSDMD, IL-1β, and IL-18 proteins in PBMC of the IIM group and its subgroups were significantly higher than those in the healthy control group (P < 0.05); Comparisons among subgroups revealed that the expression of IL-18 protein in the OM subgroup was significantly higher than that in the PM subgroup (P < 0.05). In the IIM group, the mRNA of caspase-1, GSDMD, and IL-18 showed a positive correlation with AIM2 mRNA, and the protein expression of caspase-1, GSDMD, IL-1β, and IL-18 also showed a positive correlation with AIM2 protein expression. The AIM2 inflammasome-mediated pyroptosis pathway may be involved in the pathogenesis of IIM, providing a theoretical basis for further research on the etiology of IIM and the development of new therapies. 检测特发性炎性肌病(idiopathic inflammatory myopathy,IIM)患者外周血单个核细胞(peripheral blood mononuclear cell,PBMC)中黑色素瘤缺失因子2(absent in melanoma 2,AIM2)及其介导的细胞焦亡通路关键组分——半胱氨酸天冬氨酸蛋白酶1(cysteine aspartate-specific protease-1,caspase-1)和焦孔素蛋白D(gasdermin D,GSDMD)的表达,并探讨其在IIM发病机制中的作用。 招募2020年5月至2022年6月于中国人民解放军北部战区总医院风湿免疫科就诊的30例IIM患者(IIM组),同期于医院体检中心招募30名性别和年龄与IIM患者相匹配的健康志愿者(健康对照组),收集研究对象临床信息、血液生化和免疫标志物,以及静脉血样本。通过荧光定量法检测血清双链DNA(double-stranded DNA,dsDNA)水平,通过实时荧光定量逆转录PCR(reverse transcription quantitative real-time PCR,RT-qPCR)检测PBMC中AIM2、caspase-1、GSDMD、白细胞介素1β(interleukin 1β,IL-1β)和IL-18的mRNA表达水平,应用蛋白免疫印迹法检测PBMC中AIM2、caspase-1、GSDMD、IL-1β和IL-18的蛋白表达水平,应用酶联免疫吸附(enzyme-linked immuno-sorbent assay,ELISA)法检测血清中IL-1β和IL-18的表达水平。 IIM组包含皮肌炎(dermatomyositis,DM,n=10)、多发性肌炎(polymyositis,PM,n=5)、重叠性肌炎(overlap syndrome,OM,n=11)和免疫介导的坏死性肌病(immune-mediated necrotizing myopathy,IMNM,n=4)4个亚组。与健康对照组相比,IIM组及其各亚组的血清中dsDNA、IL-1β和IL-18水平均显著增加(P<0.05)。除IMNM亚组PBMC中AIM2 mRNA与健康对照组差异无统计学意义外,IIM组及其他亚组AIM2、caspase-1和GSDMD mRNA表达均显著增加(P<0.05);除IMNM和OM亚组PBMC中IL-1β mRNA与健康对照组比较差异无统计学意义外,IIM组及其他亚组IL-1β和IL-18 mRNA表达均显著增加(P<0.05);亚组间比较表明,DM亚组PBMC中IL-1β mRNA表达明显高于OM和IMNM亚组,PM亚组IL-18 mRNA表达明显高于DM和OM亚组(P<0.05)。IIM及其各亚组的PBMC中,AIM2、caspase-1、GSDMD、IL-1β和IL-18蛋白的表达水平均显著高于健康对照组(P<0.05);各亚组间比较发现,OM亚组的IL-18蛋白表达显著高于PM亚组(P<0.05)。相关性分析表明,IIM组caspase-1、GSDMD和IL-18 mRNA与AIM2 mRNA呈正相关,caspase-1、GSDMD、IL-1β和IL-18蛋白与AIM2蛋白表达也呈正相关。 AIM2炎性小体介导的细胞焦亡通路可能参与IIM的发病机制,这一结论可以为研究IIM的病因及开发新的治疗方法提供理论基础。

#2

Adverse pregnancy outcomes in adult patients with idiopathic inflammatory myopathy: a systematic review and meta-analysis.

Arthritis care &amp; research2026 Mar 23

Studies of the impact of idiopathic inflammatory myopathy (IIM) and its pregnancy complications have yielded controversial results. The purpose of this study was to perform a systematic literature review and meta-analysis to evaluate the association between IIM and adverse pregnancy outcomes. PubMed, Embase, and Web of Science databases were searched to identify reports of interest. The databases were searched from establishment to May 15, 2025.Two investigators independently screened literature and extracted data according to inclusion and exclusion criteria. Newcastle-Ottawa Scale was used for quality assessment. A random effects model with inverse-variance weighting was selected to estimate the pooled odds ratio (OR) and 95% confidence interval (CI). Data analysis was carried out using RevMan 5.3. This analysis included five population-based retrospective cohorts, predominantly comprising patients with dermatomyositis or polymyositis; thus, the pooled estimates primarily reflect these subtypes. Compared to non-IIM pregnant women, IIM patients had significantly higher risks of hypertensive disorders of pregnancy (OR: 2.73, 95% CI: 1.76-4.23; I2=70%, Q P=0.01; overall effect P<0.00001) and cesarean section (OR: 2.03, 95% CI: 1.37-3.00; I2=79%, Q P=0.002; overall effect P=0.004). Infants born to IIM mothers also had notably higher rates of preterm birth (OR: 3.71, 95% CI: 2.35-5.85; I2=60%, Q P=0.06; overall effect P<0.00001) and small for gestational age/intrauterine growth restriction (OR: 1.90, 95% CI: 1.03-3.51; I2=43%, Q P=0.15; overall effect P=0.04). Our meta-analysis showed IIM to be associated with increased risk of hypertensive disorders of pregnancy, caesarean section, preterm birth and small for gestational age/intrauterine growth restriction birth, though residual confounding by disease activity and treatment may contribute.

#3

Semi-quantitative analyses of muscle magnetic resonance imaging for pattern recognition in early idiopathic inflammatory myopathies.

Journal of neuromuscular diseases2026 Mar 19

Idiopathic inflammatory myopathies (IIM) are a group of autoimmune diseases characterized by skeletal muscle inflammation. Magnetic resonance imaging (MRI) is increasingly used in IIM diagnosis, yet standardized protocols and comprehensive datasets remain limited. This study aimed to characterize MRI findings across IIM subtypes, identify muscle involvement patterns, and assess correlations between imaging abnormalities and clinical severity. In this retrospective cohort study, 34 patients with IIM evaluated between 2012 and 2020 in Düsseldorf and Halle (Germany) were included: Inclusion Body Myositis (IBM, n = 9), Dermatomyositis (DM, n = 5), Polymyositis (PM, n = 6), Anti-Synthetase Syndrome (ASYS, n = 5), and Immune-mediated Necrotizing Myopathy (IMNM, n = 9). Clinical data (autoantibody status, creatine kinase [CK] levels, and muscle strength via Manual-Muscle-Testing-8 [MMT-8]) and muscle MRI findings were analysed. Muscle involvement patterns were characterized, and associations with clinical severity were evaluated using univariate linear regression. MRI abnormalities were evident even in early disease stages (median disease duration: 7 months [IQR: 2-18]). Patterns of muscle involvement differed markedly across IIM subtypes; notably, ASYS and IBM showed minimal involvement of upper extremities. A significant correlation was found between MRI-visible pathology and MMT-8 scores (p = 0.027) as well as CK levels (p = 0.028). MRI reveals subclinical muscle involvement in early IIM and uncovers subtype-specific patterns. Given the heterogeneity of MRI findings, individualized imaging approaches are warranted. While MRI serves as a valuable adjunct in diagnosis and management of IIM, its utility depends on standardized protocols and integration with clinical and laboratory data to enable accurate interpretation and informed decision-making in clinical practice.

#4

Muscle MR Radiomics for Evaluation of Idiopathic Inflammatory Myopathies.

Current medical imaging2026 Mar 12

This study aimed to establish a prediction model for Idiopathic Inflammatory Myopathies (IIM) based on the radiomics of verasimus intermedius. 43 IIM patients and 48 control cases were analyzed in the retrospective study. By using the 3D slicer software, 107 radiomics features were obtained for each case. The selection of variables was performed using a two-sample t-test or the Mann-Whitney U test, followed by maximum correlation minimum redundancy (mRMR). Least Absolute Shrinkage and Selection Operator (LASSO) regression was used for dimension reduction. To assess the model performance, the receiver operating characteristic (ROC) curve was plotted. The results showed that 67 features were varying between the IIM cases and control groups (p < 0.05). With the mRMR and LASSO methods, seven features were finally determined. Regarding the radiomics model's performance, it achieved an AUC of 0.983 in the validation data. Muscle MR radiomics is feasible for identifying idiopathic inflammatory myopathy and has the potential to serve as a non-invasive alternative to muscle biopsy.

#5

Global landscape of juvenile dermatomyositis research: a bibliometric analysis.

Pediatric research2026 Mar 09

Juvenile dermatomyositis (JDM) is the most common and severe form of juvenile idiopathic inflammatory myopathy. We conducted a global mapping of the JDM scientific literature to assess publication trends, collaboration patterns, intellectual structure, and emerging priorities. We identified English-language original articles on JDM published between 1976 and 2024 in the Web of Science Core Collection (Science Citation Index Expanded), limited to clinically relevant categories. Bibliometrix and VOSviewer were used to generate key bibliometric indicators. Disruption Index was applied to distinguish disruptive from consolidating work. A total of 1113 articles were published in 201 journals by 5626 researchers. Publication output peaked in 2024, with an annual growth rate of 7.8%. The United States produced the largest number of publications, whereas the United Kingdom achieved the highest time-normalized citation rate. Recent research has increasingly focused on immunological endotyping, myositis-specific antibodies (MSAs), disease activity indices, and registry-based studies. Disruption Index analysis showed that disruptive contributions clustered around epidemiologic baselines, core outcome sets, treatment strategies, and clinical definitions. JDM research has evolved into a measurement-driven, collaborative field focused on immunological profiling and standardized assessment. Strengthening international networks and registry-based designs may further accelerate progress in this rare disease domain. This study presents a comprehensive bibliometric analysis of juvenile dermatomyositis research spanning nearly five decades. The study identifies key publication trends, intellectual structures, and disruptive contributions shaping the field. The findings demonstrate that international collaboration and standardization efforts significantly enhance citation impact and field-wide influence. The study provides a strategic roadmap for future research, emphasizing endotype-based classification, registry integration, and cross-specialty dissemination to accelerate progress in this rare disease.

Publicações recentes

Ver todas no PubMed

📚 EuropePMC406 artigos no totalmostrando 198

2026

Adverse pregnancy outcomes in adult patients with idiopathic inflammatory myopathy: a systematic review and meta-analysis.

Arthritis care &amp; research
2026

Semi-quantitative analyses of muscle magnetic resonance imaging for pattern recognition in early idiopathic inflammatory myopathies.

Journal of neuromuscular diseases
2026

Muscle MR Radiomics for Evaluation of Idiopathic Inflammatory Myopathies.

Current medical imaging
2026

Validating the effectiveness of The International Myositis Assessment and Clinical Studies Group (IMACS) idiopathic inflammatory myopathy cancer screening guidelines in a Singapore cohort.

Clinical and experimental rheumatology
2026

Global landscape of juvenile dermatomyositis research: a bibliometric analysis.

Pediatric research
2026

A case of anti-nuclear matrix protein 2 antibody-positive dermatomyositis sine dermatitis with a challenging diagnosis due to the absence of typical skin manifestations.

Modern rheumatology case reports
2026

CAR-T therapy for autoimmune rheumatic diseases: navigating clinical frontiers between breakthroughs and uncertainties.

Clinical and experimental medicine
2026

Nerandomilast attenuates idiopathic inflammatory myopathy-associated interstitial lung disease via inhibiting proliferation and differentiation of B cells.

Frontiers in immunology
2026

An interpretable machine learning model integrating clinical and CT radiomic features for the detection of interstitial lung disease in idiopathic inflammatory myopathies.

Arthritis research &amp; therapy
2026

HLA variation analysis and autoantigen epitope prediction in idiopathic inflammatory myopathies.

Rheumatology (Oxford, England)
2026

Antisynthetase Syndrome Mimicking Pulmonary Infection: A Diagnostic Lesson From County-Managed Hospital.

Clinical case reports
2026

Fitbit as an activity monitor in idiopathic inflammatory myopathy: results from a real-world cohort.

Clinical and experimental rheumatology
2026

Prophylactic Effect of Trimethoprim-sulfamethoxazole on Severe Infections in Idiopathic Inflammatory Myopathy.

Journal of clinical rheumatology : practical reports on rheumatic &amp; musculoskeletal diseases
2026

Erythematous rash and proximal muscle weakness in a 59-year-old woman: Delayed diagnosis of dermatomyositis in a patient with skin of color.

Journal of the National Medical Association
2026

Association between Oropharyngeal Dysphagia and Subgroups of Patients with Idiopathic Inflammatory Myopathy: A Cross-Sectional Study.

Dysphagia
2026

A Rare Case Report of Antisynthetase Syndrome With Progressive Myopathy and Interstitial Lung Disease in a 38-Year-Old Male.

Clinical case reports
2026

Anlotinib ameliorates myositis-associated interstitial lung disease (MAILD) via suppression of the NETs-PI3K/Akt-driven epithelial-mesenchymal transition.

RMD open
2026

Interstitial lung disease in systemic autoimmune rheumatic diseases: radiologic and histologic correlations.

Rheumatology advances in practice
2026

Development of enzyme-linked immunosorbent assays for the detection of myositis-specific autoantibodies against signal recognition particle, nuclear matrix protein 2, and small ubiquitin-like modifier activating enzyme.

Modern rheumatology
2026

The impact of vertebral fractures on pulmonary function tests in patients with interstitial lung disease: a cross-sectional study.

Respiratory research
2026

Identification of immune-related genes and serum miR-100-5p in idiopathic inflammatory myopathy-related heart failure by integrated bioinformatics analysis and clinical validation.

European journal of medical research
2026

Kinematic features of dysphagia in inclusion body myositis.

Neuromuscular disorders : NMD
2026

Spontaneous remission in statin-associated HMGCR-positive immune-mediated necrotizing myopathy after statin withdrawal.

Neuromuscular disorders : NMD
2026

[Expression of the melanoma 2-mediated pyroptosis pathway in peripheral blood mononuclear cells of patients with idiopathic inflammatory myopathies].

Beijing da xue xue bao. Yi xue ban = Journal of Peking University. Health sciences
2025

Idiopathic Inflammatory Myopathy With Normal Creatine Kinase Levels in an Elderly Patient: A Diagnostic Challenge.

Cureus
2026

Clinical Characteristics and Evolution of Interstitial Lung Disease in Subtypes of Idiopathic Inflammatory Myositis With Prevalent Lung Manifestation: A Retrospective Analysis.

ACR open rheumatology
2026

Hyperglycemia-A Driver of Cutaneous Severity in Dermatomyositis: A Narrative Review.

Journal of clinical medicine
2025

A Diagnostic Delay: Respiratory Muscle Weakness in Dermatomyositis Masquerading as Pneumonia.

Cureus
2025

Different faces of anti-melanoma differentiation-associated gene 5 antibody-positive myositis.

Reumatologia
2026

Lung ultrasound B-line quantification in CTD-ILD: a cross-sectional single-center observational study.

Scientific reports
2026

Addressing cohort reliance in rare diseases literature: a scoping review of myositis research.

Rheumatology (Oxford, England)
2026

Prevalence and early detection of myocarditis in idiopathic inflammatory myopathies: a prospective single-centre study.

Clinical and experimental rheumatology
2026

The distribution and clinical significance of anti-nuclear antibodies in patients with idiopathic inflammatory myopathy in Southwest China.

Medicina clinica
2026

Multi-kingdom gut microbiota characterization in Chinese patients with idiopathic inflammatory myopathies.

Scientific reports
2026

Baricitinib alleviates myositis-associated interstitial lung disease in mice by inhibiting the NETs-cGAS-STING-EMT axis.

International immunopharmacology
2025

An Update on Dermatomyositis and Related Inflammatory Myopathies: Cutaneous Clues, Skeletal Muscle Involvement, and Advances in Pathogenesis and Treatment.

Muscles (Basel, Switzerland)
2025

CT characterization of idiopathic inflammatory myopathy-associated interstitial lung disease: frontiers to strengthen diagnostic accuracyAuthors' ReplyA Review of Myositis-Associated Interstitial Lung Disease2023 American College of Rheumatology (ACR)/American College of Chest Physicians (CHEST) Guideline for the Screening and Monitoring of Interstitial Lung Disease in People with Systemic Autoimmune Rheumatic Diseases2022 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension.

Jornal brasileiro de pneumologia : publicacao oficial da Sociedade Brasileira de Pneumologia e Tisilogia
2025

[Rheumatic disease spectrum and immunological profile of anti-PM/Scl antibodies in idiopathic inflammatory myopathies].

Beijing da xue xue bao. Yi xue ban = Journal of Peking University. Health sciences
2026

Anti-SRP antibody-positive polymyositis complicated by neuromyelitis optica spectrum disorder: a case report and literature review.

Modern rheumatology case reports
2025

A pilot study of telitacicept in predominantly immune-mediated necrotizing myopathy, retrospective analysis of a monocentric Chinese cohort.

Journal of neurology
2025

Targeted Therapy for Idiopathic Inflammatory Myopathy.

Journal of cachexia, sarcopenia and muscle
2025

Inhibition of NOX4 attenuates muscle damage and mitochondrial dysfunction in inflammatory myopathy.

Arthritis research &amp; therapy
2025

Rapidly Progressive Polymyositis With Vasculitis: The Pivotal Role of Histopathology in Diagnosis and Management.

Cureus
2026

Clinical features and prognosis of idiopathic inflammatory myopathy complicated by heart failure with preserved ejection fraction.

Rheumatology (Oxford, England)
2025

Circular RNAs and their emerging roles in muscular immune-related diseases.

Frontiers in immunology
2025

Prognostic value of pulmonary vessel-related structures in rapid progression of idiopathic inflammatory myopathy-associated interstitial lung disease: a retrospective study from two centres.

BMJ open respiratory research
2025

Clinical Significance of Fractional Exhaled Nitric Oxide (FeNO) Measurements in Juvenile Idiopathic Inflammatory Myopathy-Associated Interstitial Lung Disease.

Pediatric pulmonology
2026

Retrospective analysis of myositis-specific antibody-positive veteran survival between 2011 and 2023.

Clinical rheumatology
2025

Interleukin-33 Promotes Interstitial Lung Disease in Idiopathic Inflammatory Myopathy Via ERK-Mediated Epithelial-Mesenchymal Transition: ERK as a Potential Therapeutic Target.

Arthritis &amp; rheumatology (Hoboken, N.J.)
2025

Association of clinical features and myositis-specific antibodies in idiopathic inflammatory myopathy: a retrospective study from southern China.

Frontiers in immunology
2025

Juvenile idiopathic inflammatory myopathies assessment by magnetic resonance imaging: a scoping review of protocols, scoring systems, and applications.

Advances in rheumatology (London, England)
2026

Increased prevalence and incidence of statin-associated immune-mediated necrotizing myopathy in Native Americans.

Rheumatology (Oxford, England)
2025

Cellular Therapy for Systemic Autoimmune Diseases: New Opportunities for Future Research and Interdisciplinary Collaboration.

ACR open rheumatology
2025

Integrated metabolomic profiling identifies citrate as novel diagnostic biomarker for Anti-MDA5-Positive dermatomyositis.

Arthritis research &amp; therapy
2026

Serum carcinoembryonic antigen levels correlate with disease severity and 1-year survival across different interstitial lung diseases subtypes.

Rheumatology (Oxford, England)
2025

Unmasking Idiopathic Inflammatory Myopathy: A Case of Proximal Weakness in a Young Male With Co-Occurring Vitamin D Deficiency.

Clinical case reports
2026

Distinct cytokine signature in juvenile dermatomyositis: linking myositis-specific antibodies and clinical manifestations.

Cytokine
2025

Progressive myalgia as the sole manifestation of cancer-associated myositis: A case report and review of the literature.

Medicine
2025

[Frequency of hypogonadism and clinical features of systemic sclerosis and idiopathic inflammatory myopathies in men depending on testosterone levels].

Terapevticheskii arkhiv
2025

Antisynthetase syndrome causing progressive gait disturbance.

Practical neurology
2025

Emerging therapies in idiopathic inflammatory myopathies: Advances in treatment and future directions.

Best practice &amp; research. Clinical rheumatology
2025

Relapse Rate After Glucocorticoid-Free Remission in Patients With Idiopathic Inflammatory Myopathies and Validation of the International Myositis Assessment and Clinical Studies Group Criteria for Complete Clinical Response and Worsening.

Arthritis &amp; rheumatology (Hoboken, N.J.)
2025

Statin-Associated Immune-Mediated Necrotizing Myopathy With Dual Anti-3-Hydroxy-3-Methylglutaryl-Coenzyme A Reductase (Anti-HMGCR) and Anti-OJ Positivity: A Case Report of Fulminant Weakness and Respiratory Failure.

Cureus
2025

The SCRIM score: a clinical tool for cancer risk-stratification in patients with idiopathic inflammatory myopathy.

Arthritis research &amp; therapy
2025

Longitudinal change of idiopathic inflammatory myopathy-associated interstitial lung disease on high-resolution computed tomography, a prospective cohort study.

BMC pulmonary medicine
2025

Clinical, functional, and computed tomographic characterization of idiopathic inflammatory myopathy-associated interstitial lung disease: a retrospective cohort study.

Jornal brasileiro de pneumologia : publicacao oficial da Sociedade Brasileira de Pneumologia e Tisilogia
2025

Altered Iron Regulation and the Role of Ferritin Heavy Chain in Dermatomyositis Patients.

Journal of inflammation research
2025

Chimeric Antigen Receptor (CAR) T Cell Therapy for Neuromuscular Disorders: A Systematic Review.

Cureus
2025

Emerging therapies in idiopathic inflammatory myopathies.

Journal of neuromuscular diseases
2025

Mixed Multiple Autoimmune Syndrome Type 3 With Coexistence of Primary Biliary Cholangitis, Inflammatory Myopathy, and Chronic Thyroiditis: A Case Report.

Cureus
2025

The Clinical Features and Prognosis of Idiopathic and Infection-Triggered Acute Exacerbation of Idiopathic Inflammatory Myopathy-Associated Interstitial Lung Disease: A Preliminary Study.

Diagnostics (Basel, Switzerland)
2025

Regaining Gait Independence in Idiopathic Inflammatory Myopathy Patients With Inability to Ambulate.

The Journal of dermatology
2026

Association of diastolic dysfunction with myocardial tissue characteristics assessed by multi-parameter cardiac magnetic resonance in patients with idiopathic inflammatory myopathy.

Rheumatology (Oxford, England)
2025

Discordance in Patient and Physician's Perception of Disease Activity Among Idiopathic Inflammatory Myopathy Patients: Insights From the COVAD Study.

International journal of rheumatic diseases
2025

When Sepsis Is Not Sepsis: A Case Report of Autoimmune Myopathy Masquerading as Postoperative Infection.

Cureus
2025

Clinical-pathologic classification of anti-HMGCR-positive immune-mediated necrotizing myopathy.

Scientific reports
2025

Cardiac Magnetic Resonance Imaging Markers in Idiopathic Inflammatory Myopathy: Correspondence.

Annals of Indian Academy of Neurology
2026

Clinical characteristics and prognostic analysis of concurrent Pneumocystis jirovecii pneumonia in patients with connective tissue diseases: a retrospective study.

Clinical and experimental rheumatology
2025

Diagnostic challenges of dermatomyositis in a resource-limited setting: a case report.

Journal of medical case reports
2025

Identification of idiopathic inflammatory myopathy research cohorts using international classification of disease (ICD) codes: A systematic review.

Seminars in arthritis and rheumatism
2025

Clinical features and recurrence risk prediction model in patients with idiopathic inflammatory myopathies-associated interstitial lung disease: a retrospective study from Ningbo.

Frontiers in medicine
2025

Idiopathic inflammatory myopathy associated with Sjögren's disease: features of a distinct clinical entity.

Frontiers in immunology
2025

Antisynthetase Syndrome Masquerading As Psoriasis and Psoriatic Arthritis: A Case Report.

Cureus
2025

Anti-Melanoma Differentiation-Associated Gene 5 Dermatomyositis With Rapidly Progressive Interstitial Lung Disease Complicated by Pneumothorax, Pneumomediastinum, and Subcutaneous Emphysema: Clinical Course Compared With Reported Cases Worldwide.

Cureus
2025

Idiopathic Inflammatory Myopathy-Molecular Mechanisms Underlying Its Pathogenesis and Physical Therapy Effects.

International journal of molecular sciences
2025

Isolated Rapidly Progressive Interstitial Lung Disease Without Muscle or Skin Involvement in Idiopathic Inflammatory Myopathy: An Unusual Anti-Mi-2 Antibody Phenotype.

Cureus
2025

Myopathology and Immune Profile of Granulomatous Myositis in Sarcoid Myopathy.

Neuropathology and applied neurobiology
2025

A Scoping Review of Respiratory Dysfunction in Inclusion Body Myositis.

International journal of rheumatic diseases
2025

Biased Usage of V/D/J Genes and Clonal Diversity in IgG Repertoires Correlates with Disease Activity and Clinical Features in Systemic Autoimmune Diseases.

Immunological investigations
2025

[Experiences after CD19-CAR T-cell therapy in non-SLE connective tissue diseases].

Zeitschrift fur Rheumatologie
2025

Characterization of Muscle Tissue Cell Diversity and Clinical Implications in Idiopathic Inflammatory Myopathy.

Journal of cachexia, sarcopenia and muscle
2026

Pathogenesis and Treatment of Interstitial Lung Disease Accompanied by Anti-melanoma Differentiation-associated Gene 5-positive Idiopathic Inflammatory Myopathies.

Internal medicine (Tokyo, Japan)
2025

Quantitative Imaging Markers on HRCT Predict Rapid Progression and Adverse Events of Patients with Idiopathic Inflammatory Myopathies-Related Interstitial Lung Disease.

International journal of general medicine
2025

Associated factors in the development of rapidly progressive interstitial lung disease in patients with idiopathic inflammatory myopathies: a systematic review and meta-analysis.

Frontiers in immunology
2025

Performance of sit-to-stand, timed up-and-go, and six-minute walk tests in home and office settings in patients with idiopathic inflammatory myopathy.

Seminars in arthritis and rheumatism
2025

Complementary and alternative medicine in dermatomyositis: A scoping review.

JAAD international
2025

Utilization of Rehabilitation Services After Idiopathic Inflammatory Myopathy Diagnosis: A Retrospective Cohort Assessment in the United States.

The Journal of rheumatology
2025

Using serum cTnT/CK combined with anti-Ro52 antibodies to screen for myocardial involvement and assess prognosis in idiopathic inflammatory myopathy.

Modern rheumatology
2025

Pulmonary Involvement in Patients with Positive Myositis Antibodies in Rheumatology: A Retrospective Monocentric Analysis.

Journal of clinical medicine
2025

Co-Occurrence of Anti-Synthetase Syndrome and Sjögren Disease: A Case-Based Review.

Journal of clinical medicine
2025

Non-targeted immunosuppressive and immunomodulatory therapies for idiopathic inflammatory myopathies.

The Cochrane database of systematic reviews
2025

Dermatomyositis: focus on cutaneous features, etiopathogenetic mechanisms and their implications for treatment.

Seminars in immunopathology
2026

Clinical significance of cytoplasmic discrete dots (AC-18) patterns in HEp-2 cell indirect Immunofluorescence: insights from a Taiwanese multicenter study.

Clinica chimica acta; international journal of clinical chemistry
2025

The value of myositis-specific autoantibodies in the diagnosis of idiopathic inflammatory myopathy and tumor risk prediction.

The Journal of international medical research
2025

Targeted immunosuppressive and immunomodulatory therapies for idiopathic inflammatory myopathies.

The Cochrane database of systematic reviews
2025

Genetics of myositis - distinct backgrounds of subtypes.

Journal of human genetics
2026

Muscle strength recovery in patients with idiopathic inflammatory myopathy with different myositis-specific autoantibodies.

Immunological medicine
2025

Clinicopathological profiling and prognosis of idiopathic inflammatory myopathy overlapping with myasthenia gravis: a retrospective cohort study.

Journal of neurology
2025

Validation of the MCK model for predicting outcomes in myopathy-associated interstitial lung disease: a multicentre MYKO cohort study.

Modern rheumatology
2025

Advances in the Regulation by Immune Cells of Skeletal Myositis Outcomes.

Aging and disease
2025

Anti-nuclear matrix protein 2 antibody-positive dermatomyositis associated with smouldering myeloma mimicking anti-melanoma differentiation-associated gene 5 antibody-positive dermatomyositis: A case of digital gangrene, palmar papules, and scrotal rash.

Modern rheumatology case reports
2026

Anifrolumab in Refractory Juvenile Dermatomyositis.

Pediatric dermatology
2025

Clinical Significance and Correlation of Plasma D-Dimer, Fibrinogen, and Cytokines in Idiopathic Inflammatory Myopathy.

International journal of general medicine
2025

Coexistence of anti-melanoma differentiation-associated protein 5 and anti-Ro52 antibodies in patients with idiopathic inflammatory myopathy: a retrospective cohort study.

Clinical rheumatology
2025

NXP-2-positive polymyositis associated with scrub typhus.

BMJ case reports
2025

Polymyositis-Induced Atrial Flutter: A Rare and Unexpected Arrhythmia in an Idiopathic Inflammatory Myopathy.

Journal of investigative medicine high impact case reports
2025

The Prospective Registry Of MyositIS (PROMIS): II. Temporal shifts in causes of death among patients with idiopathic inflammatory myopathies.

Journal of the American Academy of Dermatology
2025

N-glycosylation patterns of plasma immunoglobulin G in anti-synthetase syndrome disease.

Frontiers in immunology
2025

The clinical features and mortality predictors for idiopathic inflammatory myopathies: a retrospective study of 572 patients and the "AIRMT" Score.

Clinical rheumatology
2025

Chimeric Antigen Receptor T-cell therapy in systemic autoimmune rheumatic diseases: current insights and future prospects.

Journal of rheumatic diseases
2025

Expert consensus on interstitial lung disease associated with systemic autoimmune diseases. Executive summary.

Revista clinica espanola
2025

Idiopathic Inflammatory Myopathies and Malignancy Screening: A Survey of Current Practices Amongst Canadian Neurologists and Rheumatologists.

Muscle &amp; nerve
2025

Ruxolitinib in adult dermatomyositis with anti-TIF1γ antibody: a case report and literature review.

Frontiers in immunology
2025

Risk, risk factors, and screening of malignancies in dermatomyositis: current status and future perspectives.

Frontiers in oncology
2025

Muscle Vasculitis: A Novel Delineation of Distinct Subsets of Disease.

ACR open rheumatology
2025

Immune Characterization of a Vietnamese Cohort With Idiopathic Inflammatory Myopathies.

Muscle &amp; nerve
2025

Cardiac involvement in established idiopathic inflammatory myopathy assessed by cardiac magnetic resonance mapping.

Clinical rheumatology
2025

Activated Dendritic Cell Subsets Characterize Muscle of Inclusion Body Myositis Patients and Correlate with KLRG1+ and TBX21+ CD8+ T cells.

medRxiv : the preprint server for health sciences
2025

Diagnostic value of bronchoalveolar lavage fluid metagenomic next-generation sequencing for pulmonary infections in patients with connective tissue disease: A retrospective study.

Scientific reports
2025

Cardiac Magnetic Resonance Imaging Markers in Idiopathic Inflammatory Myopathy - A Prospective Observational Study.

Annals of Indian Academy of Neurology
2025

Application of a Growth-Rate Model to Enhance Subgroup Identification in Heterogeneous Clinical Courses of the Idiopathic Inflammatory Myopathy-Associated Interstitial Lung Disease and Its Prognostic Implication.

International journal of rheumatic diseases
2025

Myositis Due to Parvovirus B19: A Case Report and Literature Review.

Cureus
2025

Ageing Signatures and Disturbed Muscle Regeneration in Muscle Proteome of Inclusion Body Myositis.

Journal of cachexia, sarcopenia and muscle
2025

A case of myositis associated with mixed connective tissue disease mimicking bilateral posterior interosseous nerve palsy.

Ideggyogyaszati szemle
2026

Analysis of clinical features and risk factors for patients with idiopathic inflammatory myopathy complicated by Pneumocystis jirovecii pneumonia.

Clinical and experimental rheumatology
2025

Association of Cancer and Anti-Synthetase Syndrome: A Retrospective Multicenter Study.

The American journal of medicine
2025

High levels of EPSTI1 enhance IFN-β-mediated HLA-A expression and chemokine secretion in myoblasts in dermatomyositis.

Rheumatology (Oxford, England)
2025

Immunoadsorption as a novel therapy for refractory idiopathic inflammatory myopathies: a retrospective observational study.

Rheumatology (Oxford, England)
2025

Characterizing local antibody responses in the muscle of inclusion body myositis patients.

Journal of autoimmunity
2025

Anti-HMGCR myopathy: a first case report from North Africa and literature insights.

Frontiers in immunology
2025

Polymyositis Presenting With Respiratory Failure and Cardiac Arrest: A Case Report.

Cureus
2025

Beyond the Generalized Weakness: A Rare Case of Statin-Induced Immune-Mediated Necrotizing Myopathy.

Journal of investigative medicine high impact case reports
2025

Investigating the profile of patients with idiopathic inflammatory myopathies in the post-COVID-19 period.

Microbiology spectrum
2025

Diagnostic performance of particle-based multi-analyte technology compared to indirect immunofluorescence in screening for anti-nuclear antibodies in patients with autoimmune rheumatic diseases.

Clinical and experimental rheumatology
2025

Serum connective tissue growth factor is aberrantly expressed in idiopathic inflammatory myopathy.

Clinical and experimental rheumatology
2025

Differences in Organ Damage Based on Age at Onset in Idiopathic Inflammatory Myopathies: A Retrospective Multicenter MYKO Study.

Internal medicine (Tokyo, Japan)
2025

Modeling Idiopathic Inflammatory Myopathy in the Bioinspired Muscle Tissue on Chip.

Advanced healthcare materials
2025

Shared and Distinctive Inflammation-Related Protein Profiling in Idiopathic Inflammatory Myopathy with/without Anti-MDA5 Autoantibodies.

Journal of inflammation research
2025

Long-term outcomes of idiopathic inflammatory myopathies: a large-scale longitudinal cohort study.

Journal of autoimmunity
2025

Microvascular abnormalities between anti-TIF1-γ-associated dermatomyositis with and without malignancy.

BMC rheumatology
2025

Inclusion Body Myositis: A Case Report.

Cureus
2025

Local immune effector cell-associated toxicity syndrome in CAR T-cell treated patients with autoimmune disease: an observational study.

The Lancet. Rheumatology
2025

Anti-TIF1-beta autoantibody-positive dermatomyositis: a case-based review.

Rheumatology international
2025

Imaging assessment of calcinosis in juvenile dermatomyositis: a narrative review.

Pediatric rheumatology online journal
2025

Abatacept for the treatment of myositis-associated interstitial lung disease.

Rheumatology (Oxford, England)
2025

Recruitment rate comparison between a virtual tele-research cohort and a traditional centre-based cohort in idiopathic inflammatory myopathy.

Rheumatology (Oxford, England)
2025

A novel approach to refractory idiopathic inflammatory myopathy: CD19 CAR T-cell therapy-case report and literature review.

Rheumatology (Oxford, England)
2025

MRI patterns of thigh muscle involvement in immune-mediated necrotizing myopathy and dermatomyositis.

BMC rheumatology
2025

Prevalence of Elevated CK Levels, Myositis-Specific and Myositis-Associated Antibodies, Myositis, and Other Neuromuscular Diseases in Myasthenia Gravis Patients-Experience from an Eastern European Tertiary Center.

Journal of clinical medicine
2025

Targeting B Cells for the Treatment of Idiopathic Inflammatory Myopathy.

Clinical reviews in allergy &amp; immunology
2025

Polymorphisms of HSP70 genes are involved in the pathogenesis of idiopathic inflammatory myopathy.

Reumatologia
2025

Mitochondrial damage is associated with an early immune response in inclusion body myositis.

Brain : a journal of neurology
2025

The role of monocytes and macrophages in idiopathic inflammatory myopathies: insights into pathogenesis and potential targets.

Frontiers in immunology
2025

Successful treatment of rheumatoid arthritis complicated by anti-Jo-1 antibody-positive myopathy with abatacept: A case report.

Fukushima journal of medical science
2025

Risk factors and predictive model for pulmonary arterial hypertension in adult idiopathic-inflammatory-myopathy patients: A cross-sectional study.

Clinics (Sao Paulo, Brazil)
2025

International Guideline for Idiopathic Inflammatory Myopathy-Associated Cancer Screening recommendations detect most malignancies in patients with dermatomyositis: Retrospective performance in a tertiary-care center cohort.

Journal of the American Academy of Dermatology
2025

MDA5 protein mediating persistent ER stress/unfolded protein response contributes to endothelial-mesenchymal-transition of lung microvascular endothelial cell in dermatomyositis.

Cell communication and signaling : CCS
2025

Effectiveness and safety of anti-CD20 monoclonal antibodies versus csDMARDs in anti-Jo-1 antisynthetase syndrome: A retrospective cohort study.

Seminars in arthritis and rheumatism
2025

Pirfenidone alleviates interstitial lung disease in mice by inhibiting neutrophil extracellular trap formation and NLRP3 inflammasome activation.

Clinical and experimental immunology
2025

Nailfold videocapillaroscopy findings are associated with IIM subtypes and IFN activation.

Arthritis research &amp; therapy
2025

Pseudoangioedema as a presenting symptom of dermatomyositis with antinuclear matrix protein 2 autoantibodies.

JAAD case reports
2025

Human epididymis secretory protein 4 in idiopathic inflammatory myopathy-associated interstitial lung disease.

Clinical rheumatology
2025

Anti-nuclear Matrix Protein 2 Antibody-Positive Dermatomyositis Relapse With Preceding Panniculitis.

Cureus
2025

External validation of the 2017 EULAR/ACR classification criteria for idiopathic inflammatory myopathies in anti-MDA5 antibody-positive interstitial lung disease patients: A multicenter retrospective cohort study in China.

Seminars in arthritis and rheumatism
2025

Plasma levels of adhesion molecules are elevated in dermatomyositis-interstitial lung disease and associated with low paraoxonase-1 activity.

Arthritis research &amp; therapy
2024

Interleukin 6 inhibition in refractory antisynthetase syndrome: case-based literature review.

Acta clinica Belgica
2025

[Sequential autoimmunity? The rare case of MDA5 dermatomyositis and sarcoidosis].

Zeitschrift fur Rheumatologie
2025

Corrigendum: Applicability of a serodiagnostic line blot for idiopathic inflammatory myopathy: the muscle biopsy is not all.

Frontiers in neurology
2025

Treatment guidelines for idiopathic inflammatory myopathies in adults: a comparative review.

Rheumatology (Oxford, England)
2025

Clinical Features of Dermatomyositis Associated with Myositis-Specific Antibodies in Moroccan Patients.

Clinics and practice
2025

Characteristics of Overlap Syndrome in a Large Cohort of Brazilian Patients With Systemic Sclerosis: A Retrospective Analysis.

The Journal of rheumatology
2025

Patients with anti-PM/Scl-positive and idiopathic inflammatory myopathy resemble anti-synthetase syndrome.

Advances in rheumatology (London, England)
2025

Emerging mechanisms and therapeutics in inflammatory muscle diseases.

Trends in pharmacological sciences
2025

Outcome of COVID-19 in patients with idiopathic inflammatory myopathy during the Omicron wave in China: A longitudinal observational study.

PloS one
2025

Mortality Risk Prediction in Patients With Antimelanoma Differentiation-Associated, Gene 5 Antibody-Positive, Dermatomyositis-Associated Interstitial Lung Disease: Algorithm Development and Validation.

Journal of medical Internet research
2025

Dermatomyositis following resection of thyroid and breast cancer: a case report and literature review.

Frontiers in oncology
2025

cGAS-STING mediates neutrophil extracellular traps-induced EMT in myositis-associated interstitial lung disease: STING as a potential therapeutic target.

International immunopharmacology
2025

Mitochondrial transplantation as a novel therapeutic approach in idiopathic inflammatory myopathy.

Annals of the rheumatic diseases
2024

Clinical Characteristics and Outcomes of Patients with Anti-MDA5 Antibody Associated Rapidly Progressive Interstitial Lung Disease (RP-ILD): A Case Series.

Mediterranean journal of rheumatology
2025

Retrospective analysis of US veterans with inclusion body myositis: initial findings from the Veterans Affairs Corporate Data Warehouse.

Military Medical Research
2025

Idiopathic inflammatory myopathy.

Medicina clinica
2025

30-Color Longitudinal Full-Spectrum Immunophenotyping and Sorting of Human Circulating Immune Cell Subsets Implicated in Systemic Autoimmune Rheumatic Diseases.

bioRxiv : the preprint server for biology
2025

Validity of Diagnosis Codes to Identify a Dermatomyositis Cohort from Electronic Health Records.

Dermatology (Basel, Switzerland)
2025

Recalcitrant Dermatomyositis Treated With Anifrolumab.

ACR open rheumatology
2024

Applicability of a serodiagnostic line blot for idiopathic inflammatory myopathy: the muscle biopsy is not all.

Frontiers in neurology
2024

Anti-SRP myositis: a diagnostic and therapeutic challenge.

The Turkish journal of pediatrics
2025

Interstitial Lung Disease Associated with Anti-Ku Antibodies: A Case Series of 19 Patients.

Journal of clinical medicine
2025

Disease activity in patients with idiopathic inflammatory myopathy according to time since diagnosis and positivity to antisynthetase autoantibodies: data from the Myo-Spain registry.

Arthritis research &amp; therapy
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Doenças relacionadas

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Referências e fontes

Bases de dados externas citadas neste artigo

Publicações científicas

Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.

  1. [Expression of the melanoma 2-mediated pyroptosis pathway in peripheral blood mononuclear cells of patients with idiopathic inflammatory myopathies].
    Beijing da xue xue bao. Yi xue ban = Journal of Peking University. Health sciences· 2026· PMID 41633601mais citado
  2. Adverse pregnancy outcomes in adult patients with idiopathic inflammatory myopathy: a systematic review and meta-analysis.
    Arthritis care &amp; research· 2026· PMID 41869994mais citado
  3. Semi-quantitative analyses of muscle magnetic resonance imaging for pattern recognition in early idiopathic inflammatory myopathies.
    Journal of neuromuscular diseases· 2026· PMID 41854350mais citado
  4. Muscle MR Radiomics for Evaluation of Idiopathic Inflammatory Myopathies.
    Current medical imaging· 2026· PMID 41832724mais citado
  5. Global landscape of juvenile dermatomyositis research: a bibliometric analysis.
    Pediatric research· 2026· PMID 41803247mais citado
  6. Remission rates and predictors in idiopathic inflammatory myopathy subgroups: Insights from a single-center cohort.
    J Rheumatol· 2026· PMID 41985918recente
  7. Quantitative spectral computed tomography biomarkers for idiopathic inflammatory myopathy-associated interstitial lung disease: a dual-layer detector computed tomography study.
    Quant Imaging Med Surg· 2026· PMID 41972046recente
  8. Efficacy and safety of upadacitinib in refractory interstitial lung disease with idiopathic inflammatory myopathies: a retrospective study.
    Rheumatology (Oxford)· 2026· PMID 41967849recente
  9. Immunoprecipitation-mass spectrometry reveals known and novel (NatC, BCS1L) antinuclear antibodies in rheumatoid arthritis.
    RMD Open· 2026· PMID 41963076recente
  10. Clinical characteristics and factors associated with dysphagia in idiopathic inflammatory myopathy: A cross-sectional observational study.
    Med Clin (Barc)· 2026· PMID 41946117recente

Bases de dados e fontes oficiais

Identificadores e referências canônicas usadas para montar este verbete.

  1. ORPHA:98482(Orphanet)
  2. MONDO:0020122(MONDO)
  3. GARD:9128(GARD (NIH))
  4. Busca completa no PubMed(PubMed)
  5. Q55789135(Wikidata)

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Miopatia e fasciite inflamatórias adquiridas
Compêndio · Raras BR

Miopatia e fasciite inflamatórias adquiridas

ORPHA:98482 · MONDO:0020122
Prevalência
Unknown
CID-11
Ensaios
14 ativos
Medicamentos
14 registrados
Prevalência
0.0 (Worldwide)
MedGen
UMLS
C0751356
EuropePMC
Wikidata
Papers 10a
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