A Dermatomiosite Juvenil (DMJ) é a forma de dermatomiosite (DM) que começa mais cedo na vida. É uma doença autoimune e inflamatória que afeta os músculos e o corpo todo. Ela se caracteriza por fraqueza nos músculos próximos ao tronco (como ombros e quadris), lesões ou manchas típicas na pele, e outros problemas que podem surgir em diferentes partes do corpo.
Introdução
O que você precisa saber de cara
A Dermatomiosite Juvenil (DMJ) é a forma de dermatomiosite (DM) que começa mais cedo na vida. É uma doença autoimune e inflamatória que afeta os músculos e o corpo todo. Ela se caracteriza por fraqueza nos músculos próximos ao tronco (como ombros e quadris), lesões ou manchas típicas na pele, e outros problemas que podem surgir em diferentes partes do corpo.
Escala de raridade
<1/50kMuito rara
1/20kRara
1/10kPouco freq.
1/5kIncomum
1/2k
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Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Partes do corpo afetadas
+ 21 sintomas em outras categorias
Características mais comuns
Os sintomas variam de pessoa para pessoa. Abaixo estão as 45 características clínicas mais associadas, ordenadas por frequência.
Linha do tempo da pesquisa
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Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
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🇧🇷 Atendimento SUS — Dermatomiosite juvenil
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Publicações mais relevantes
Mostrando amostra de 200 publicações de um total de 908
Reliability of durometry to assess firmness of calcinosis lesions in Juvenile and adult dermatomyositis.
Dermatomyositis (DM) and juvenile dermatomyositis (JDM) are inflammatory myopathies affecting multiple organs, including muscle and skin. Calcinosis is a complication of DM/JDM that causes significant morbidity; however, few tools exist to assess calcinosis in DM/JDM patients This study aimed to evaluate the reliability of durometry measurements to assess the firmness of calcinosis lesions in DM and JDM patients. Calcinosis firmness was measured using a handheld digital durometer. Six investigators across 3 institutions examined DM/JDM calcinosis lesions by durometry, as well as control readings in healthy unaffected skin/subcutaneous tissue in similar anatomic areas, recording three readings per site. Intra-rater and inter-rater intraclass correlations were evaluated. We enrolled 57 patients and gathered 709 measurements (443 calcinosis lesions; 266 control lesions) over eleven anatomic regions. Intra-rater reliability was high across sites, while inter-rater reliability varied, being moderate to good in most areas, but poor in the thigh and anterior calf. Durometry readings were higher in calcinosis lesions than control sites overall. Measurements moderately correlated with qualitative physician assessments. Due to our study's cross-sectional nature, we could not assess calcinosis over time. Durometry is a novel, reliable, quantitative measure in assessing and characterizing targeted calcinosis lesions of DM/JDM patients.
Intermittent Glucocorticoid Pulse Combined With Mycophenolate Mofetil in Juvenile Dermatomyositis.
This cohort study reports the long-term clinical outcomes of the use of intermittent intravenous methylprednisolone pulse therapy combined with mycophenolate mofetil for patients with juvenile dermatomyositis.
Presence of Multiple Muscle Specific Autoantibodies (MSAs) in a Young Child with Juvenile Dermatomyositis.
Relapse of Juvenile Dermatomyositis following Eight Years in Remission: A Case Report.
Dermatomyositis is an autoimmune inflammatory condition that is characterized by proximal muscle weakness and a variety of cutaneous manifestations. In this report, we discuss the case of a 27-year-old white female who developed a relapse of juvenile dermatomyositis (JDM) 8 years after remission. The patient presented with a 4-month history of progressive proximal muscle weakness and rash, as well as a more recent onset of dysphagia. Severe cutaneous involvement was apparent on examination with ulcerated, pruritic plaques, violaceous papules, and diffuse erythema. Laboratories revealed elevated CK, aldolase, and CRP, with positive anti-NXP2, anti-U1 RNP, and anti-U2 RNP antibodies. Based on the clinical picture and diagnostic results, a relapse of JDM was diagnosed and various medication trials were initiated. Since initial presentation, the patient has improved and is currently stable on a regimen of hydroxychloroquine, IVIG, low-dose corticosteroids, tofacitinib, and gabapentin. Her myositis is in remission; however, she continues to experience burdensome cutaneous symptoms and overall significant disease impact. This case highlights the possibility of JDM relapse even after prolonged remission, underscoring the importance of maintaining a high index of suspicion for symptom recurrence. It also offers a thorough example of multimodal therapy use for refractory JDM.
Severe Juvenile Dermatomyositis With Peripheral Nervous System Involvement: A Case Report.
Juvenile dermatomyositis is the most common inflammatory myopathy of childhood. While many cases achieve favorable outcomes, severe forms may develop persistent disease activity, complications, and long-term disability. A five-year-old girl was admitted after 20 days of Gottron's papules and heliotrope rash, with intermittent fever during the first 10 days. She then developed mild proximal-predominant muscle weakness in all four limbs, rapidly progressing to severe generalized weakness with signs of axonal neuropathy over the subsequent 15 days. Despite aggressive immunosuppression with IV methotrexate, high-dose methylprednisolone pulses, IV immunoglobulin, oral prednisolone, and azathioprine, she demonstrated inadequate clinical response over four years of follow-up. Severe juvenile dermatomyositis with peripheral nervous system involvement may follow a refractory course despite guideline-directed aggressive immunosuppression. This case highlights the therapeutic challenges of rapidly progressive disease with atypical neurological complications and underscores the need for early recognition and intensified treatment strategies in high-risk presentations.
Publicações recentes
Systematic literature review informing PReS/CARRA-endorsed recommendations for the treat-to-target strategy in juvenile dermatomyositis.
Introducing a parent-centred composite disease activity score for remote monitoring in juvenile dermatomyositis.
📖 RevisãoUse of the EOS 2D/3D Imaging System for the Evaluation of Calcinosis in Juvenile Dermatomyositis: A Retrospective Case Series.
Wong-type juvenile dermatomyositis associated with anti-MDA5 and anti-PL-7 antibodies.
CAR T-cell therapy and indications for pediatric rheumatology: Structured overview of applications, risks, and considerations.
📚 EuropePMC1.328 artigos no totalmostrando 199
Novel use of anifrolumab in a young patient with Jo-1-positive juvenile dermatomyositis.
Rheumatology advances in practiceReliability of durometry to assess firmness of calcinosis lesions in Juvenile and adult dermatomyositis.
PloS oneRelapse of Juvenile Dermatomyositis following Eight Years in Remission: A Case Report.
Case reports in dermatologySevere Juvenile Dermatomyositis With Peripheral Nervous System Involvement: A Case Report.
CureusGlobal landscape of juvenile dermatomyositis research: a bibliometric analysis.
Pediatric researchComprehensive Analysis Reveals Potential Molecular Targets in Juvenile Dermatomyositis.
Biochemistry research internationalNailfold video capillaroscopy as a non-invasive biomarker in juvenile dermatomyositis: A longitudinal analysis of microvascular changes and clinical relevance over one year.
Seminars in arthritis and rheumatismDistinct by Design: Unraveling the Unique Clinical and Transcriptomic Identity of Juvenile Scleromyositis Overlap Compared to Juvenile Systemic Sclerosis and Juvenile Dermatomyositis: Implications for Care and Pathogenesis.
ACR open rheumatologyTransition From Juvenile Dermatomyositis to Spondyloarthritis: A Novel Overlapping Inflammatory Phenotype.
ACR open rheumatologyInterferon-Driven Tryptophan Metabolism Links Inflammation and Mental Health in Juvenile Dermatomyositis.
InflammationPresence of Multiple Muscle Specific Autoantibodies (MSAs) in a Young Child with Juvenile Dermatomyositis.
Indian journal of pediatricsLung Involvement in MDA5-Positive Juvenile Dermatomyositis: A Case of Misdiagnosed Pneumonia in a Toddler.
Pediatric pulmonologyClinically validated assay for rapid determination of type I and type II interferon activity in systemic inflammatory diseases.
The Journal of allergy and clinical immunologyTowards New Strategies: Case Report and Review of the Literature-Effective Use of JAK Inhibitor Baricitinib in a 4-Year-Old Boy with Anti-MDA5 Antibody-Positive Juvenile Dermatomyositis.
Journal of clinical medicineComparison of disease severity and activity between juvenile- and adult-onset dermatomyositis: a multicentre cohort study.
Rheumatology (Oxford, England)An Unusual Case of Juvenile Dermatomyositis Complicated by Macrophage Activation Syndrome.
International journal of dermatologyComparison of pre- and post-natal environmental exposures in United States versus Brazilian patients with juvenile dermatomyositis.
Clinical and experimental rheumatologySex Differences in PROMIS Pediatric Depressive Symptoms, Anxiety, and Psychological Stress Among Children and Adolescents Living With Pediatric Rheumatic Diseases.
The Journal of rheumatologyAssociation of NXP2 autoantibodies with a more severe clinical phenotype of juvenile dermatomyositis.
Clinical and experimental rheumatologyUnmasking inflammation in juvenile dermatomyositis: myokine profiles of patients and bioengineered human muscle.
Frontiers in immunologyRituximab for Early-Onset Juvenile Dermatomyositis Complicated by Interstitial Lung Disease.
Case reports in pediatricsA Comparative Bibliometric Analysis of Pediatric Interstitial Lung Disease Treatment: Global Trends, Advances, and Future Directions (2004-2024).
Pediatric pulmonologyJuvenile dermatomyositis as a rare paraneoplastic manifestation of nasopharyngeal carcinoma.
Rheumatology (Oxford, England)Clinical use of intravenous immunoglobulin in juvenile dermatomyositis: indications, treatment course, and clinical outcomes.
Expert opinion on biological therapyMDA5 Antibody Associated Juvenile Dermatomyositis Presenting as Rapidly Progressive Pulmonary Fibrosis-Case Report.
Journal of paediatrics and child healthPredictive role of muscle MRI in juvenile dermatomyositis: A tertiary center experience.
European journal of radiologySingle-Cell Transcriptomics Reveals CCL3+ Classical Monocyte Subset Linked to Autoimmune Pathogenesis.
Journal of inflammation researchNeutrophil lymphocyte ratio as a marker of skin disease activity in older children with juvenile dermatomyositis.
Pediatric rheumatology online journalJuvenile idiopathic inflammatory myopathies assessment by magnetic resonance imaging: a scoping review of protocols, scoring systems, and applications.
Advances in rheumatology (London, England)Intermittent Glucocorticoid Pulse Combined With Mycophenolate Mofetil in Juvenile Dermatomyositis.
JAMA dermatologyDistinct cytokine signature in juvenile dermatomyositis: linking myositis-specific antibodies and clinical manifestations.
CytokineJuvenile dermatomyositis: new insights into pathogenesis and clinical applications.
Pediatric rheumatology online journal[Clinical characteristics of juvenile dermatomyositis in anti-nuclear matrix protein 2 antibody-positive patients and risk factors for severity: a national multicenter retrospective study].
Zhonghua er ke za zhi = Chinese journal of pediatricsSuperimposed Segmental Juvenile Dermatomyositis: A Case Report.
CureusToward a Treat-to-Target Strategy in Juvenile Dermatomyositis: What Are the Suitable Targets and Optimal Timing of Their Achievement?
Arthritis & rheumatology (Hoboken, N.J.)Therapeutic plasma exchange in autoimmune diseases: a retrospective study in a tertiary pediatric hospital in Mexico.
Frontiers in pediatricsCongruence Between Child Self-Reported and Caregiver-Proxy-Reported Health-Related Quality of Life in Children With Juvenile Idiopathic Arthritis and Systemic Lupus Erythematosus.
The Journal of rheumatologyPromising Treatments in Juvenile Dermatomyositis.
Rheumatic diseases clinics of North AmericaPhysical Activity Monitors in Myositis: Bridging the Gap from Bedside to Clinical Trials.
Rheumatic diseases clinics of North AmericaCalcinosis in Adult and Juvenile Dermatomyositis: Pathogenesis and Potential Therapeutic Targets.
Rheumatic diseases clinics of North AmericaDiverse Joint Manifestations in Anti-MDA5 Antibody-Positive Juvenile Dermatomyositis: A Unique Case Report.
International journal of rheumatic diseasesAlternative polyadenylation and splicing regulation in refractory juvenile dermatomyositis: CELF2 at the crossroads.
Molecular therapy. Nucleic acidsIFN-α levels correlate with muscle disease activity only in juvenile dermatomyositis patients with anti-MDA5+ autoantibodies.
Rheumatology (Oxford, England)Neutrophil activation in juvenile dermatomyositis: associations with muscle function and disease progression.
Pediatric rheumatology online journalLong-term outcomes of juvenile dermatomyositis.
Journal of the European Academy of Dermatology and Venereology : JEADVValidation of the 2019 EULAR/ACR classification criteria and clinical characteristics of childhood-onset Japanese patients with systemic lupus erythematosus.
Modern rheumatologyThe effect of Rituximab on B cells in pediatric autoimmune rheumatic diseases.
Northern clinics of IstanbulIs Hydroxychloroquine Useful for the Treatment of Cutaneous Manifestations of Idiopathic Inflammatory Myopathies? A Systematic Review.
Pharmaceuticals (Basel, Switzerland)Impaired Brachial Artery Reactivity in Young Adults With Clinically Quiescent Juvenile Dermatomyositis.
ACR open rheumatologyPROMIS displays strong construct validity in pediatric and adult patients with idiopathic inflammatory myopathies.
Rheumatology (Oxford, England)[Relationship between common myositis-specific antibodies and clinical features in children with juvenile dermatomyositis].
Zhongguo dang dai er ke za zhi = Chinese journal of contemporary pediatricsTumoral Calcinosis of the Knee With Secondary Infection in a Patient With Juvenile Dermatomyositis: Management Approach and Pathophysiological and Therapeutic Review.
CureusAnti-TIF1-Gamma Autoantibodies-Positive Juvenile Dermatomyositis Associated With Interstitial Lung Disease: A Case Report.
CureusDazukibart for the treatment of severe TIF1γ-positive juvenile dermatomyositis.
Journal of the European Academy of Dermatology and Venereology : JEADVBanker Type of Juvenile Dermatomyositis.
Indian journal of dermatologyDiscovery of tissue-specific proteomic signatures in juvenile dermatomyositis highlights pathways reflecting persistent disease activity, clinical heterogeneity, and myositis-specific autoantibody subtype.
Annals of the rheumatic diseasesVitamin D Status in Paraguayan Children With Autoimmune Diseases.
International journal of rheumatic diseasesA possible role for immunogenetic factors in myositis developing after vaccination in the pre-covid-19 era.
Frontiers in immunologyA retrospective natural history study in adult and juvenile patients with incident dermatomyositis and polymyositis using real world data.
Clinical rheumatology[Clinical characteristics of anti-melanoma differentiation associated gene 5 antibody-positive juvenile dermatomyositis].
Zhonghua er ke za zhi = Chinese journal of pediatricsNon-targeted immunosuppressive and immunomodulatory therapies for idiopathic inflammatory myopathies.
The Cochrane database of systematic reviewsSpatial transcriptomic analysis of muscle biopsy from patients with treatment-naive juvenile dermatomyositis reveals mitochondrial abnormalities despite disease-related interferon-driven signature.
Annals of the rheumatic diseasesAnasarca in Juvenile Dermatomyositis: An Uncommon Presentation.
Indian journal of pediatricsLevel of CD4+ central memory T cells and its clinical correlation in childhood-onset systemic lupus erythematosus.
LupusCalcinosis Universalis: An Atypical Presentation of Mi-2 Positive Juvenile Dermatomyositis - A Case-Based Review.
Mediterranean journal of rheumatologyApplication of HRCT-based radiomics to predict interstitial lung disease for juvenile dermatomyositis.
BMC pediatricsTargeted immunosuppressive and immunomodulatory therapies for idiopathic inflammatory myopathies.
The Cochrane database of systematic reviewsTreatment outcomes in 63 cases of juvenile dermatomyositis-associated calcinosis.
Clinical and experimental rheumatologyCD68 + macrophage infiltrations in muscle tissue of juvenile dermatomyositis associated with the course of the disease, not with the severity.
Clinical rheumatologyUpdates in juvenile dermatomyositis: pathogenesis and therapy.
Current opinion in rheumatologyNailfold videocapillaroscopy in juvenile dermatomyositis: detailed correlations between microvascular abnormalities with clinical and laboratory parameters from an observational retrospective single-center study.
Clinical rheumatologyTransition of CELF2 PAS usage promotes recovery of refractory JDM through alternative splicing regulation of CTSB.
Molecular therapy. Nucleic acidsJuvenile dermatomyositis in Oman: clinical patterns and disease trajectory from a National cohort.
Pediatric rheumatology online journalAnifrolumab in Refractory Juvenile Dermatomyositis.
Pediatric dermatologyRemission and low disease activity definitions in adult idiopathic inflammatory myopathies: A narrative review by myositis clinical trials consortium (MCTC).
Autoimmunity reviewsForty-one Cytokine Profile and Interferon-I Score in Juvenile Dermatomyositis: A Case Series Study.
Recent advances in inflammation & allergy drug discoveryPanniculitis in Anti-MDA-5 Positive Juvenile Dermatomyositis: A Case Report.
JNMA; journal of the Nepal Medical AssociationJuvenile dermatomyositis: a severe and atypical presentation.
ARP rheumatologyEfficacy of hydroxychloroquine treatment for the skin manifestations of juvenile dermatomyositis.
Modern rheumatology case reportsCAR T cell therapy for children with rheumatic disease: the time is now.
Nature reviews. RheumatologyEpidemiology of Juvenile Dermatomyositis-What We Know and What More Is Needed?
International journal of rheumatic diseasesEfficacy and safety of rhGH in juvenile dermatomyositis children with glucocorticoid-related growth failure.
Rheumatology (Oxford, England)Muscle Spatial Transcriptomic Reveals Heterogeneous Profiles in Juvenile Dermatomyositis and Persistence of Abnormal Signature After Remission.
CellsLong-term outcome of juvenile dermatomyositis associated with lipodystrophy: experience of a University hospital.
Anais brasileiros de dermatologiaA novel presentation of calcinosis cutis of the scalp in adult dermatomyositis.
Dermatology online journalOral JAK inhibitors for pediatric inflammatory skin disease.
Current opinion in pediatrics[Clinical analysis of 4 cases of juvenile dermatomyositis complicated with massive hemorrhage of digestive tract].
Zhonghua er ke za zhi = Chinese journal of pediatricsAnti-melanoma differentiation-associated gene 5 antibody associated rapidly progressive interstitial lung disease in a pediatric patient: a case report.
Journal of medical case reportsPredictors of persistent active disease and the longitudinal development of organ damage, patient-reported outcomes and autoantibodies in long-term juvenile dermatomyositis.
RMD openMyositis-specific autoantibody subtypes are associated with response to Janus kinase inhibitors in patients with juvenile dermatomyositis.
Rheumatology (Oxford, England)Rheumatologic manifestations in children with underlying inborn errors of immunity.
BMC rheumatologyTreating juvenile dermatomyositis to target: Paediatric Rheumatology European Society/Childhood Arthritis and Rheumatology Research Alliance-endorsed recommendations from an international task force.
Annals of the rheumatic diseasesTofacitinib monotherapy as maintenance treatment in juvenile dermatomyositis: a case report.
RMD openEffect of graded nursing and feeding guidance based on water swallow test combined with enteral nutrition support in juvenile dermatomyositis children with swallowing dysfunction.
African journal of reproductive healthExploring the Association of Sociodemographic Factors and Primary Diagnosis With Transition Readiness in Adolescents With Rheumatic Disease.
ACR open rheumatologyJuvenile Dermatomyositis.
Journal of cutaneous medicine and surgeryWhy Recommended Visit Intervals Should Be Extracted When Conducting Longitudinal Analyses Using Electronic Health Record Data: Examining Visit Mechanism and Sensitivity to Assessment Not at Random.
Statistics in medicineEffects of Juvenile Idiopathic Inflammatory Myopathies on Growth, Development, and Maturation: A Systematic Review and Metaanalysis.
The Journal of rheumatologyTargeting interferon responses in juvenile dermatomyositis: Siglec-1 as an in vitro biomarker for JAK inhibitor efficacy.
Rheumatology (Oxford, England)Differences in Organ Damage Based on Age at Onset in Idiopathic Inflammatory Myopathies: A Retrospective Multicenter MYKO Study.
Internal medicine (Tokyo, Japan)F18-FDG PET-CT Findings in Juvenile-Onset Polyarteritis Nodosa: A First Series and Literature Review.
Journal of clinical medicineJuvenile Dermatomyositis and Hepatitis B Viral Infection.
European journal of case reports in internal medicineCAR-T cell therapy for juvenile-onset autoimmune diseases: a promising future?
Arthritis research & therapyJuvenile Dermatomyositis Triggered by Influenza B: A Case Report on Viral-Induced Autoimmunity.
Pediatric dermatologyLong-term effectiveness and safety of baricitinib treatment on refractory or severe juvenile dermatomyositis.
Rheumatology (Oxford, England)Interferon Response Gene Score in Juvenile Dermatomyositis.
The Journal of rheumatologyCannabinoids in the management of refractory juvenile dermatomyositis: a patient's perspective.
Clinical and experimental dermatologyImaging assessment of calcinosis in juvenile dermatomyositis: a narrative review.
Pediatric rheumatology online journalTofacitinib: a promising agent for the treatment of persistent rashes in juvenile dermatomyositis.
World journal of pediatrics : WJPRapid clinical and transcriptomic response to anifrolumab in refractory anti-TIF1γ-positive juvenile dermatomyositis.
Annals of the rheumatic diseasesJuvenile Dermatomyositis in a Two-Year-Old Yemeni Girl in a Resource-Limited Setting: A Case Report.
CureusInvolving young people in research investigating comorbidity associated with childhood-onset rheumatic disease: perspectives of a series of focus groups.
BMC rheumatologyPhysical Growth Dynamics of Children With Juvenile Dermatomyositis.
CureusA Case of Juvenile Dermatomyositis Presenting with Inverse Gottron's Papules: A Case Report.
Case reports in dermatologyPerspectives and experiences of parents of children with juvenile dermatomyositis: a semi-structured interview study.
Pediatric rheumatology online journalMonozygotic twins discordant for juvenile dermatomyositis: clinical, serological and gene expression studies.
Pediatric rheumatology online journalImaging features of juvenile dermatomyositis complicated by pyomyositis in a 12-year-old boy: A case report.
Radiology case reportsPhysical activity and quality of life of children and adolescents with juvenile idiopathic arthritis, juvenile systemic lupus erythematosus and juvenile dermatomyositis during the COVID-19 pandemic.
Jornal de pediatriaType I interferon signature: a quantitative standardized method for clinical application.
Clinical and experimental immunologyMonoclonal antibody targeting IFNβ for the treatment of NXP2-positive ulcerative juvenile dermatomyositis.
PediatricsPseudoangioedema as a presenting symptom of dermatomyositis with antinuclear matrix protein 2 autoantibodies.
JAAD case reportsCorrelation Between Interferon Response Gene Score and Disease Activity in Juvenile Dermatomyositis.
The Journal of rheumatologyTape strip expression profiling of juvenile dermatomyositis skin reveals mitochondrial dysfunction contributing to disease endotype.
JCI insightEffect of abatacept added to mycophenolate mofetil for refractory calcinosis in juvenile dermatomyositis.
Modern rheumatology case reportsSuccessful treatment of an anti-MDA5 antibody-positive Juvenile Dermatomyositis patient with refractory interstitial lung disease using tofacitinib.
Pediatric rheumatology online journalMortality in children and adolescents with autoimmune inflammatory rheumatic diseases admitted to the pediatric intensive care unit.
Pediatric rheumatology online journal[A case of vedolizumab treatment for refractory juvenile dermatomyositis with secondary intestinal perforation].
Zhonghua er ke za zhi = Chinese journal of pediatricsPsychometric properties of patient-reported outcomes measurement information system (PROMIS) fixed short forms in Juvenile Myositis.
Seminars in arthritis and rheumatismApproach to Janus kinase inhibition for juvenile dermatomyositis among CARRA and PReS providers.
Rheumatology (Oxford, England)Anti-nuclear matrix protein 2 antibody-associated juvenile dermatomyositis with gastrointestinal perforations was successfully treated with traditional therapeutic drugs combined with vedolizumab: a case report after a long-term follow-up and a review of the literature.
Frontiers in pediatricsExploring the clinical profiles and management of juvenile dermatomyositis in Africa: a survey of African rheumatology care providers.
Pediatric rheumatology online journalImmunobiologics in juvenile dermatomyositis: a systematic review of promising therapeutic advances.
ReumatologiaThe Role of Pyroptosis-Related Gene Signature and Immune Infiltration in Juvenile Dermatomyositis.
Clinical, cosmetic and investigational dermatologySafety and Efficacy of Long-term Use of Infliximab in Severe Juvenile Dermatomyositis - 12 Years of Follow-up.
Acta dermatovenerologica Croatica : ADCThromboembolic Risk in Juvenile Dermatomyositis Patients Treated With Intravenous Immunoglobulin.
Pediatric dermatologyAnti-MDA5 Positive Juvenile Dermatomyositis With Macrophage Activation Syndrome: A Case Report.
CureusJuvenile Dermatomyositis Associated Cholestatic Liver Disease With Normal Creatine Kinase.
Journal of paediatrics and child healthUnforeseen complication in juvenile dermatomyositis.
Rheumatology (Oxford, England)Achieving Medication-Free Remission in Patients With Juvenile Dermatomyositis.
ACR open rheumatologyThe value of quantitative muscle ultrasound in monitoring muscle and fascia inflammatory activity in juvenile dermatomyositis patients.
Quantitative imaging in medicine and surgeryRadiographs in Pediatric Rheumatology: Where Do We Stand?
The Indian journal of radiology & imagingTransient negativity for the anti-TIF1γ antibody before treatment in juvenile dermatomyositis.
Rheumatology advances in practiceA Bayesian latent class approach to causal inference with longitudinal data.
Statistical methods in medical researchSuccessful tocilizumab treatment for rapidly progressive interstitial lung disease with anti-MDA5-positive juvenile dermatomyositis: a case report and literature review.
Frontiers in pediatrics25 Years of Biologics for the Treatment of Pediatric Rheumatic Disease: Advances in Prognosis and Ongoing Challenges.
Arthritis care & researchCase Report: IVIG causing bilateral papilledema and increased intracranial hypertension in patients with anti-TIF-1γ antibody-positive JDM.
Frontiers in pediatricsAnasarca and Systemic Capillary Leak Syndrome as an Unusual Presentation of Juvenile Dermatomyositis: Report of Three Cases and Case-Based Review.
International journal of rheumatic diseasesAnti-lipoprotein lipase antibodies: A review.
Autoimmunity reviewsCalcinosis universalis in juvenile dermatomyositis.
The Pan African medical journalExpert Perspective: Diagnostic Approach to Differentiating Juvenile Dermatomyositis From Muscular Dystrophy.
Arthritis & rheumatology (Hoboken, N.J.)Anesthetic Challenges in Laparoscopic Surgery for a Child with Juvenile Dermatomyositis.
CureusRecent Advances in Juvenile Dermatomyositis: Moving toward Integration of Myositis-Specific Antibody Clinical Phenotypes, IFN-Driven Pathogenesis, and Targeted Therapies.
The Journal of investigative dermatologyPredictors of poor outcomes in juvenile dermatomyositis: what do we know? A narrative review.
ReumatismoNeutrophil and mononuclear leukocyte pathways and upstream regulators revealed by serum proteomics of adult and juvenile dermatomyositis.
Arthritis research & therapyRituximab Treatment in Adult Patients With Idiopathic Inflammatory Myositis: A Systematic Review and Meta-analysis.
Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseasesAnti-Sp4 and anti-CCAR1 autoantibodies in UK vs US patients with adult and juvenile-onset anti-TIF1γ-positive myositis.
Rheumatology (Oxford, England)Dyslipidemia in Juvenile Dermatomyositis.
Scientific reportsRinging in the Patient Voice: Measuring Patients' Lived Experience of Dermatomyositis Symptoms.
The Journal of rheumatologyGenome-wide identification of cell type-specific susceptibility genes for Juvenile dermatomyositis through the analysis of N6-methyladenosine-associated SNPs.
AutoimmunityInterferon-β-Induced Injury During Pediatric Muscle Differentiation: Insight Into Juvenile Dermatomyositis Pathogenesis.
ACR open rheumatologyJuvenile Dermatomyositis: Updates in Pathogenesis and Biomarkers, Current Treatment, and Emerging Targeted Therapies.
Paediatric drugsEpidemiological Characteristics of Patients With Juvenile Dermatomyositis in China: A Multicenter Study.
The Journal of rheumatologyLongitudinal assessment of disease activity and muscle strength in juvenile dermatomyositis: a multicentre registry study.
Clinical and experimental rheumatologyPenicillamine-Induced Juvenile Dermatomyositis: A Rare Clinical Encounter.
Indian dermatology online journalRare skin manifestation of juvenile dermatomyositis: peri-orbital oedema and facial swelling.
Paediatrics and international child healthNailfold Capillaroscopy Changes in Patients with Idiopathic Inflammatory Myopathies.
Journal of clinical medicineAdvances in Juvenile Dermatomyositis: Pathophysiology, Diagnosis, Treatment and Interstitial Lung Diseases-A Narrative Review.
Children (Basel, Switzerland)Profile of patients with Juvenile Dermatomyositis and Anti-MDA5 autoantibodies.
Pediatric research14-month-old female with anti-MDA5 juvenile dermatomyositis complicated by liver disease: a case report.
Pediatric rheumatology online journalJuvenile Dermatomyositis: Diagnosis and Management.
SkinmedMining for Gems: Early Detection of Calcinosis in Juvenile Dermatomyositis Using Low-Dose Computed Tomography.
The Journal of rheumatologyDouble-negative T cells in pediatric rheumatic diseases.
Clinical and experimental pediatricsThe influence of environmental factors related to Juvenile Dermatomyositis (JDM), its course and refractoriness to treatment.
Advances in rheumatology (London, England)Cutaneous Ulcers and Response to Treatment in a Child with Anti-MDA5 Dermatomyositis.
Mediterranean journal of rheumatologyAtherosclerotic cardiovascular disease following a diagnosis of idiopathic inflammatory myopathy: analysis from a retrospective cohort in the TriNetX registry.
Clinical rheumatologyPersonalised medicine in juvenile dermatomyositis: From novel insights in disease mechanisms to changes in clinical practice.
Best practice & research. Clinical rheumatologyParaneoplastic dermatomyositis and Hodgkin's lymphoma in a 14-year-old girl: a case report and literature review.
Frontiers in oncologyPrevalence and Clinical Implications of Autoantibodies in Juvenile Dermatomyositis: A Single-Center Experience From India.
Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseasesDifferences in the autoantibody phenotypes and long-term outcomes between juvenile- and adult-idiopathic inflammatory myopathies.
Seminars in arthritis and rheumatismCurrent evidence for janus kinase inhibitors in adult and juvenile dermatomyositis and key comparisons.
Expert opinion on pharmacotherapyCalcinosis in dermatomyositis.
Current opinion in rheumatologyIncreased vascular deposition of oxidized LDL in untreated juvenile dermatomyositis.
Pediatric rheumatology online journalAssay for interferon gamma release as a novel marker in pediatric patients with systemic lupus erythematosus.
Pediatric rheumatology online journalDecoding the genetic landscape of juvenile dermatomyositis: insights from phosphorylation-associated single nucleotide polymorphisms.
ImmunogeneticsElicitation of expert prior opinion to design the BARJDM trial in juvenile dermatomyositis.
Rheumatology (Oxford, England)Over Activation of IL-6/STAT3 Signaling Pathway in Juvenile Dermatomyositis.
Rheumatology and therapyJuvenile dermatomyositis complications: navigating gastrointestinal perforations and treatment challenges, a case report.
Frontiers in pediatricsClinical characteristics and prognostic factor in juvenile dermatomyositis: data of the Spanish registry.
Pediatric rheumatology online journalCapillaroscopy in the daily clinic of the pediatric rheumatologist.
Best practice & research. Clinical rheumatologyAn Adolescent Case of Anti-MDA5 Antibody-Positive Juvenile Dermatomyositis With Interstitial Lung Disease Successfully Treated by Multitarget Therapy Avoiding Cyclophosphamide: A Case Report and Literature Review.
CureusAutologous haematopoiesis stem cell transplantation (AHSCT) for treatment-refractory autoimmune diseases in children.
RMD openThe Diagnostic Role of Skin Manifestations in Rheumatic Diseases in Children: A Critical Review of Paediatric Vasculitis.
International journal of molecular sciencesDecreased Peripheral Blood Natural Killer Cell Count in Untreated Juvenile Dermatomyositis Is Associated with Muscle Weakness.
International journal of molecular sciencesFamilial clustering of dysbiotic oral and fecal microbiomes in juvenile dermatomyositis.
Scientific reportsUndercover lung damage in pediatrics - a hot spot in morbidity caused by collagenoses.
Frontiers in immunologyIncreased percentage of HLA-DR T cells in untreated juvenile dermatomyositis.
Clinical immunology communicationsCase Report: Contiguous presentation of anti-MDA5 juvenile dermatomyositis and anti-AQP4 neuromyelitis optica spectrum disorder in an adolescent patient.
Frontiers in pediatricsChildhood Arthritis and Rheumatology Research Alliance Biologic Disease-Modifying Antirheumatic Drug Consensus Treatment Plans for Refractory Moderately Severe Juvenile Dermatomyositis.
Arthritis care & researchAutologous CD19-Targeting CAR T Cells in a Patient With Refractory Juvenile Dermatomyositis.
Arthritis & rheumatology (Hoboken, N.J.)Associações
Organizações que acompanham esta doença — pra ter apoio e orientação
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Comunidades
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Ainda não existe comunidade no Raras para Dermatomiosite juvenil
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Reliability of durometry to assess firmness of calcinosis lesions in Juvenile and adult dermatomyositis.
- Intermittent Glucocorticoid Pulse Combined With Mycophenolate Mofetil in Juvenile Dermatomyositis.
- Presence of Multiple Muscle Specific Autoantibodies (MSAs) in a Young Child with Juvenile Dermatomyositis.
- Relapse of Juvenile Dermatomyositis following Eight Years in Remission: A Case Report.
- Severe Juvenile Dermatomyositis With Peripheral Nervous System Involvement: A Case Report.
- Systematic literature review informing PReS/CARRA-endorsed recommendations for the treat-to-target strategy in juvenile dermatomyositis.
- Introducing a parent-centred composite disease activity score for remote monitoring in juvenile dermatomyositis.
- Use of the EOS 2D/3D Imaging System for the Evaluation of Calcinosis in Juvenile Dermatomyositis: A Retrospective Case Series.
- Wong-type juvenile dermatomyositis associated with anti-MDA5 and anti-PL-7 antibodies.
- CAR T-cell therapy and indications for pediatric rheumatology: Structured overview of applications, risks, and considerations.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:93672(Orphanet)
- MONDO:0008054(MONDO)
- Dermatomiosite e Polimiosite(PCDT · Ministério da Saúde)
- GARD:6805(GARD (NIH))
- Busca completa no PubMed(PubMed)
- Artigo Wikipedia(Wikipedia)
- Q6318950(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
