A dermatomiosite (DM) é um tipo de miopatia inflamatória idiopática caracterizada por lesões cutâneas evocativas e fraqueza muscular proximal simétrica.
Introdução
O que você precisa saber de cara
A dermatomiosite (DM) é um tipo de miopatia inflamatória idiopática caracterizada por lesões cutâneas evocativas e fraqueza muscular proximal simétrica.
Escala de raridade
<1/50kMuito rara
1/20kRara
1/10kPouco freq.
1/5kIncomum
1/2k
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Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Partes do corpo afetadas
+ 47 sintomas em outras categorias
Características mais comuns
Os sintomas variam de pessoa para pessoa. Abaixo estão as 97 características clínicas mais associadas, ordenadas por frequência.
Linha do tempo da pesquisa
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Genética e causas
O que está alterado no DNA e como passa nas famílias
Nenhum gene associado encontrado
Os dados genéticos desta condição ainda estão sendo catalogados.
Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
Remédios, cuidados de apoio e o que precisa acompanhar
Onde tratar no SUS
Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)
🇧🇷 Atendimento SUS — Dermatomiosite
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Ensaios clínicos abertos e novidades científicas recentes
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Outros ensaios clínicos
Publicações mais relevantes
Mostrando amostra de 200 publicações de um total de 5.814
Reliability of durometry to assess firmness of calcinosis lesions in Juvenile and adult dermatomyositis.
A calcinose é uma complicação debilitante da dermatomiosite que carece de ferramentas de avaliação. Este estudo demonstra que a durômetria, que mede a firmeza das lesões, é um método novo e confiável para quantificar e caracterizar essas lesões. Isso oferece a médicos uma ferramenta objetiva e padronizada para monitorar a calcinose, potencialmente otimizando o manejo e o acompanhamento dos pacientes.
🇧🇷 traduzidoDermatomyositis masquerading as angioedema: a crucial differential not to overlook.
A dermatomiosite é uma doença autoimune rara que exige tratamento imunossupressor imediato para evitar danos multiorgânicos. Este artigo alerta que ela pode se manifestar de forma atípica, como inchaço grave no pescoço, mimetizando angioedema, o que pode atrasar o diagnóstico. É crucial que médicos considerem a dermatomiosite em casos de edema incomum, especialmente com alterações na pele e elevação da creatina quinase (CK), para garantir um tratamento urgente e eficaz.
🇧🇷 traduzidoSpatial transcriptomics reveals mechanism of autoimmunity driven by internalized autoantibodies.
Esta pesquisa revela que, na dermatomiosite e em outras doenças autoimunes, os autoanticorpos não apenas circulam, mas são *internalizados* pelas células (do músculo e de outros tecidos). Uma vez dentro, esses autoanticorpos ativam programas genéticos específicos que levam a danos celulares e inflamação (como a ativação do interferon). Este achado estabelece a internalização de autoanticorros como um mecanismo fundamental e compartilhado em diversas doenças autoimunes, oferecendo a médicos e pesquisadores uma nova perspectiva para entender a patogênese e desenvolver tratamentos mais eficazes.
🇧🇷 traduzidoAnti-CD19 CAR T cells for pediatric patients with treatment-refractory autoimmune diseases.
Uma nova terapia com células CAR T anti-CD19 demonstrou resultados promissores em crianças com doenças autoimunes graves e refratárias a tratamentos convencionais, incluindo a dermatomiosite. Todos os oito pacientes neste estudo (três com dermatomiosite) apresentaram melhora clínica substancial ou resolução da doença, permitindo a descontinuação sustentada de outros imunomoduladores, com efeitos adversos geralmente leves e manejáveis. Embora estes resultados preliminares sejam encorajadores, são urgentemente necessários ensaios clínicos formais para confirmar a segurança e eficácia a longo prazo desta abordagem para doenças como a dermatomiosite.
🇧🇷 traduzidoIdentification of common genes and biomarkers between Dermatomyositis and rheumatoid arthritis through integrated bioinformatics.
Este estudo revelou mecanismos moleculares e imunológicos comuns entre a Dermatomiosite (DM) e a Artrite Reumatoide (AR), explicando parcialmente sua comorbidade. Foram identificados os genes HCP5 e RARRES3 como potenciais biomarcadores de diagnóstico, validados em dados externos, e vias como IL-17 e alterações em células imunes (macrófagos e células T) em ambas as doenças. Estes achados abrem caminho para o desenvolvimento de ferramentas de diagnóstico mais precisas e terapias direcionadas para pacientes que sofrem de DM e AR.
🇧🇷 traduzidoPublicações recentes
Association between IL1B rs16944 polymorphism and the risk of idiopathic inflammatory myopathies.
Systematic literature review informing PReS/CARRA-endorsed recommendations for the treat-to-target strategy in juvenile dermatomyositis.
📖 RevisãoRemission rates and predictors in idiopathic inflammatory myopathy subgroups: Insights from a single-center cohort.
Lung transplant outcomes in myositis, systemic sclerosis and idiopathic pulmonary fibrosis: a multicenter retrospective analysis.
Upadacitinib Versus Tofacitinib in Anti-MDA5-Positive Dermatomyositis With Interstitial Lung Disease: A Multi-Centre Cohort Study Emulating a Target Trial.
📚 EuropePMC8.206 artigos no totalmostrando 193
Dermatomyositis with Anti-MDA5 Autoantibodies After SARS-CoV-2 mRNA Vaccination Treated with Tofacitinib: Integrating Literature Evidence and a Novel Observation.
Antibodies (Basel, Switzerland)A challenging case of facial oedemas revealing a systemic peripheral T-cell lymphoma, not otherwise specified.
European journal of dermatology : EJDReliability of durometry to assess firmness of calcinosis lesions in Juvenile and adult dermatomyositis.
PloS oneDistinct Interferon and Intracellular Signaling Signatures in Systemic Lupus Erythematosus and Dermatomyositis by Integrative Transcriptomic and Proteomic Analysis.
ACR open rheumatologyAdverse pregnancy outcomes in adult patients with idiopathic inflammatory myopathy: a systematic review and meta-analysis.
Arthritis care & researchClinical Findings, Antibody Panel and Pathology of Patients with Inflammatory Myopathies in Isfahan Province, Iran.
Advanced biomedical researchRelapse of Juvenile Dermatomyositis following Eight Years in Remission: A Case Report.
Case reports in dermatologyPrevalence and Risk of Falls and Fractures in the Idiopathic Inflammatory Myopathies: A Cross-Sectional Study of 470 Patients.
Rheumatology and therapySevere Juvenile Dermatomyositis With Peripheral Nervous System Involvement: A Case Report.
CureusSemi-quantitative analyses of muscle magnetic resonance imaging for pattern recognition in early idiopathic inflammatory myopathies.
Journal of neuromuscular diseasesThe role of extracorporeal membrane oxygenation in the management of rapidly progressive interstitial lung disease due to anti-melanoma differentiation-associated gene 5 antibody dermatomyositis: A case series and brief literature review.
JHLT openInhibition of the type I interferon receptor pathway protects against muscle weakness induced by dermatomyositis serum.
Annals of the rheumatic diseasesCheckerboard Hyperkeratosis With Apoptotic Keratinocytes as Features of Mechanic's Hands and Review of the Literature.
The American Journal of dermatopathologyDegos-Like-Skin Lesions in the Setting of Dermatomyositis: A Case Series and Literature Review.
Indian dermatology online journalA Study of Cutaneous Manifestations in Patients During the Post-COVID Period in A Tertiary Care Center.
Journal of pharmacy & bioallied sciencesDiagnosis of a patient with pulmonary and skeletal cryptococcosis: A case report and literature review.
The Journal of international medical researchFatal Cardiomyopathy Secondary to Seronegative Immune-Mediated Necrotizing Myopathy: A Case Report.
The American journal of case reportsPalmar Cutaneous Erythematous Macules: A Case Report of an Atypical Presentation of Chilblain Lupus Erythematosus.
Cureus"The Cancer that Carried the Chalk"-NXP2+ Paraneoplastic Dermatomyositis Unleashing Calcinosis Cutis and Peripheral Neuropathy.
The Journal of the Association of Physicians of IndiaElevated Serum Levels of β1,4-Galactosyltransferase 1 Have Diagnostic Value in Patients With Dermatomyositis.
International journal of rheumatic diseasesImmune dysregulation and infection susceptibility in Anti-MDA5 dermatomyositis.
Seminars in arthritis and rheumatismLinear and streaky rash in a young female.
Journal der Deutschen Dermatologischen Gesellschaft = Journal of the German Society of Dermatology : JDDGAnti-PM/Scl Antibody-Positive Dermatomyositis With Rapidly Progressive Interstitial Lung Disease in a 19-Year-Old Male: Clinical Implications of a Presumptive Diagnosis Based on Line Immunoassay Positivity.
CureusAssociation of diagnostic delay with disease activity and cumulative damage in Hispanic patients with idiopathic inflammatory myopathies: a cross-sectional study.
Clinical rheumatologyGlobal landscape of juvenile dermatomyositis research: a bibliometric analysis.
Pediatric researchClinical Value of Bronchiectasis and Airspace Enlargement Depicted on Iodine Map in Patients With Interstitial Lung Disease: A Pilot Study.
CureusComprehensive Analysis Reveals Potential Molecular Targets in Juvenile Dermatomyositis.
Biochemistry research internationalEvaluating the value of lactic dehydrogenase in anti-MDA5-positive Dermatomyositis associated with interstitial lung disease.
Frontiers in medicineA case of anti-nuclear matrix protein 2 antibody-positive dermatomyositis sine dermatitis with a challenging diagnosis due to the absence of typical skin manifestations.
Modern rheumatology case reportsCooccurrence of Anterior Cruciate Ligament Rupture and Ganglion Cyst: Clinical Complexity and Ultrasound-Guided Tailored Management.
Pain practice : the official journal of World Institute of PainAmyopathic dermatomyositis associated with anti-MDA5 antibodies and rapidly progressive interstitial pneumonia: 2 cases with different clinical evolution.
Medicina clinicaParallel course of calcinosis and cancer in a patient with anti-NXP2-positive dermatomyositis: A case report.
Modern rheumatology case reportsClinical characteristics and risk factors associated with objective flares in patients with dermatomyositis.
Seminars in arthritis and rheumatismDermatomyositis masquerading as angioedema: a crucial differential not to overlook.
BMJ case reportsRecurrent anti-TIF1γ-positive dermatomyositis coexisting with postoperative parotid lymphoepithelial carcinoma: a case report with pathogenesis analysis.
Frontiers in immunologyFlagellate erythema and breast infiltration.
JAAD case reportsOverfitting, sparse data bias, and variable selection in the predictive model for rapidly progressive interstitial lung disease in dermatomyositis.
Respiratory medicineEvaluating the Diagnostic Potential of Myxovirus Resistance Protein 1 (MX1) and Myxovirus Resistance Protein 2 (MX2) As Biomarkers in Idiopathic Inflammatory Myopathies.
CureusDermatomyositis: Prevalence, Clinical Spectrum, Diagnostic Approach, and Management Strategies.
Archives of internal medicine researchNailfold video capillaroscopy as a non-invasive biomarker in juvenile dermatomyositis: A longitudinal analysis of microvascular changes and clinical relevance over one year.
Seminars in arthritis and rheumatismRethinking rituximab in neuroimmunology: Real-world efficacy, cost-effectiveness, and long-term remission.
Journal of neuroimmunologyPeriorbital heliotrope erythema with edema as a potential clinical marker of paraneoplastic Dermatomyositis - a case series.
Journal der Deutschen Dermatologischen Gesellschaft = Journal of the German Society of Dermatology : JDDGDistinct by Design: Unraveling the Unique Clinical and Transcriptomic Identity of Juvenile Scleromyositis Overlap Compared to Juvenile Systemic Sclerosis and Juvenile Dermatomyositis: Implications for Care and Pathogenesis.
ACR open rheumatologySpatial transcriptomics reveals mechanism of autoimmunity driven by internalized autoantibodies.
medRxiv : the preprint server for health sciencesClinical features, treatment, and outcomes of anti-PD-1/PD-L1 immune checkpoint inhibitors induced dermatomyositis.
Immunopharmacology and immunotoxicologyTransition From Juvenile Dermatomyositis to Spondyloarthritis: A Novel Overlapping Inflammatory Phenotype.
ACR open rheumatologyFitbit as an activity monitor in idiopathic inflammatory myopathy: results from a real-world cohort.
Clinical and experimental rheumatologyNeutrophil-to-lymphocyte ratio as a prognostic indicator in anti-MDA5 dermatomyositis with interstitial lung disease and its link to IFN-α and IL-6.
Clinical and experimental rheumatologyAcquired generalised lipodystrophy as an uncommon complication of anti-Mi-2 dermatomyositis: a case report.
Clinical and experimental rheumatologyTemporal Dissociation Between Clinical Remission and Microvascular Improvement Assessed by AI-Assisted Capillaroscopy in Anti-Mi-2 Dermatomyositis: Potential Therapeutic Implications.
Arthritis & rheumatology (Hoboken, N.J.)A Case of Anti-SAE Antibody-Positive Dermatomyositis Coexisting With Sjögren's Disease.
The Journal of dermatologyGenetic Whispers in Hyperphosphataemic: Tumor Calcinosis in a 30-year-old.
Irish medical journalImproved Detection of Myositis-Specific Autoantibodies Using Luciferase Immunoprecipitation Systems Assay: Comparison with Line Blot and Conventional Immunoprecipitation.
Arthritis & rheumatology (Hoboken, N.J.)Long-term management challenges in postmyopathic dermatomyositis.
Dermatology online journalErythematous rash and proximal muscle weakness in a 59-year-old woman: Delayed diagnosis of dermatomyositis in a patient with skin of color.
Journal of the National Medical AssociationDevelopment and validation of a multi-institutional electronic juvenile idiopathic arthritis phenotype.
Seminars in arthritis and rheumatismAssociation between Oropharyngeal Dysphagia and Subgroups of Patients with Idiopathic Inflammatory Myopathy: A Cross-Sectional Study.
DysphagiaThe efficacy of transbronchial lung cryobiopsy for chronic progressive changes after remission of anti-MDA5 antibody-positive interstitial lung disease: a report of two cases.
Respiratory investigationAnti-MDA5 monoclonal antibodies from patients with dermatomyositis - B cell characteristics and differential targeting of the helicase domains.
Journal of autoimmunityAtypical dermatomyositis with positive anti-nuclear matrix protein 2 antibodies complicated by rhabdomyolysis syndrome: a case report and literature review.
Frontiers in immunologyPretreatment Cytokine Signatures as Candidate Biomarkers for JAK Inhibitor Response in Anti-MDA5 Dermatomyositis-Related Interstitial Lung Disease: A Pilot Study.
ACR open rheumatologyElevated serum interleukin-38 levels in polymyositis and dermatomyositis: diagnostic implications and correlations with inflammatory markers.
Frontiers in immunologyInterferon-Driven Tryptophan Metabolism Links Inflammation and Mental Health in Juvenile Dermatomyositis.
InflammationAcute muscle injury and subcutaneous edema in a patient with anti-nuclear matrix protein-2 antibody positive dermatomyositis sine dermatitis: A Case Report.
Internal medicine (Tokyo, Japan)Complement activation and M2-like macrophage accumulation in anti-MDA5 monoclonal antibody-induced hepatic injury in mice.
Frontiers in immunologyAnti-MDA5 Antibody-Positive Dermatomyositis in Emirati Patients: A Case Series Highlighting Clinical Variability.
The American journal of case reportsA case study of delayed-diagnosed leprosy: advancing diagnosis through MetaPath.
International journal of infectious diseases : IJID : official publication of the International Society for Infectious DiseasesHow loss-of-function mutations in IFIH1 contribute to infectious and/or inflammatory disease - a systematic review.
Journal of translational autoimmunityAnti-SAE Antibody-Positive Dermatomyositis Presenting With Widespread Erythema Complicated by Rosai-Dorfman Disease.
The Journal of dermatologyPrognostic value of HRCT-based risk stratification for acute/subacute progression in polymyositis/dermatomyositis-associated interstitial lung disease.
Frontiers in immunologyPostpartum-Onset Dermatomyositis Presenting With Malignant Pleural Effusion: A Case Report.
CureusCalcinosis Cutis Universalis: A Review of Therapeutic Strategies and Surgical Management.
Journal of clinical medicineDistinct anti-MDA5 antibody trajectories associated with long-term outcomes in 6-month survivors of anti-MDA5 dermatomyositis with interstitial lung disease.
Respiratory researchValidation of simplified scoring systems for assessing cutaneous disease activity in dermatomyositis.
Clinical and experimental rheumatologyPresence of Multiple Muscle Specific Autoantibodies (MSAs) in a Young Child with Juvenile Dermatomyositis.
Indian journal of pediatricsDetection of dermatomyositis skin rashes in skin of color: Addressing critical training gaps.
The American journal of medicineMulticentre development and validation of data-driven claims-based algorithms for identifying dermatomyositis and polymyositis in Japan.
Modern rheumatologyDermatomyositis Mimicking Statin-Induced Myopathy in A 62-Year-Old Woman.
European journal of case reports in internal medicineIntegrated proteomic and transcriptomic profiles reveals the role of OAS3 in dermatomyositis pathogenesis.
Frontiers in immunologyMonocyte-driven vasculopathy distinguishes dermatomyositis from CLE.
Nature reviews. RheumatologyEarly detection and intervention in dermatomyositis: current evidence and clinical implications.
Clinical rheumatologyDevelopment of enzyme-linked immunosorbent assays for the detection of myositis-specific autoantibodies against signal recognition particle, nuclear matrix protein 2, and small ubiquitin-like modifier activating enzyme.
Modern rheumatologyElbow Gottron's Sign as a Predictor of Dermatomyositis With Respiratory System as the Initial Manifestation: A Retrospective Study.
The Journal of dermatologyCytomegalovirus DNAemia in patients with anti-melanoma differentiation-associated gene 5 positive dermatomyositis from southern China.
BMC infectious diseasesAnti-Melanoma Differentiation-Associated Gene 5 Antibody-Positive Interstitial Lung Disease, Induced by Enfortumab Vedotin Plus Pembrolizumab for Advanced Urothelial Carcinoma.
IJU case reportsLung Involvement in MDA5-Positive Juvenile Dermatomyositis: A Case of Misdiagnosed Pneumonia in a Toddler.
Pediatric pulmonologyIdentifying cutaneous dermatomyositis disease area and severity index thresholds of disease severity in alignment with patient perspectives on quality of life: A retrospective analysis.
Journal of the American Academy of DermatologyPulmonary alveolar proteinosis developing during tofacitinib treatment for anti-MDA5 antibody-positive dermatomyositis-associated interstitial lung disease: a case report and review of the literature.
Immunological medicineCritical illness with fatal muscle weakness and gastrointestinal perforation after COVID-19.
Modern rheumatology case reportsAnti-CD19 CAR T cells for pediatric patients with treatment-refractory autoimmune diseases.
Nature medicineProteomic profiles in inclusion body myositis and polymyositis with mitochondrial pathology.
Acta neuropathologica communicationsClinically validated assay for rapid determination of type I and type II interferon activity in systemic inflammatory diseases.
The Journal of allergy and clinical immunologyIdentification of common genes and biomarkers between Dermatomyositis and rheumatoid arthritis through integrated bioinformatics.
PloS oneAtypical Interplay of Dermatomyositis, Metastatic Caecal Carcinoma, and Connective Tissue Disease.
Cureus[Expression of the melanoma 2-mediated pyroptosis pathway in peripheral blood mononuclear cells of patients with idiopathic inflammatory myopathies].
Beijing da xue xue bao. Yi xue ban = Journal of Peking University. Health sciencesPhospho-MLKL Upregulation in Immune-Mediated Necrotizing Myopathy: Implications for Disease Pathophysiology and Diagnosis.
Neuropathology : official journal of the Japanese Society of NeuropathologyPrognostic and Functional Trajectories in Idiopathic Pulmonary Fibrosis and Systemic Autoimmune Rheumatic Disease-Associated Interstitial Lung Disease: Insights From an Italian Multicenter Cohort.
The Journal of rheumatologyParaneoplastic dermatomyositis with atypical features associated with a solid pseudopapillary pancreatic neoplasm.
Clinical rheumatologyThrombotic microangiopathy in a patient with anti-signal recognition particle antibody-positive immune-mediated necrotising myopathy: a case report.
Modern rheumatology case reportsExtracellular Vesicular Proteins in Plasma from Patients with Cutaneous Lupus Correlate with Disease Activity.
Current issues in molecular biologyIdiopathic Inflammatory Myopathy With Normal Creatine Kinase Levels in an Elderly Patient: A Diagnostic Challenge.
CureusClinical Characteristics and Evolution of Interstitial Lung Disease in Subtypes of Idiopathic Inflammatory Myositis With Prevalent Lung Manifestation: A Retrospective Analysis.
ACR open rheumatologyMuscle RING finger-1 facilitates skeletal muscle regeneration via regulating myoblast proliferation and differentiation.
Journal of translational medicineHyperglycemia-A Driver of Cutaneous Severity in Dermatomyositis: A Narrative Review.
Journal of clinical medicineTowards New Strategies: Case Report and Review of the Literature-Effective Use of JAK Inhibitor Baricitinib in a 4-Year-Old Boy with Anti-MDA5 Antibody-Positive Juvenile Dermatomyositis.
Journal of clinical medicineCharacteristics, treatments and outcomes of patients with dermatomyositis using real-world data.
RMD openA Diagnostic Delay: Respiratory Muscle Weakness in Dermatomyositis Masquerading as Pneumonia.
CureusAn Overview of Small-Molecule Agents for the Treatment of Dermatomyositis.
Current topics in medicinal chemistryKikuchi-Fujimoto Disease as the Initial Presentation of Dermatomyositis.
Current rheumatology reviewsDifferent faces of anti-melanoma differentiation-associated gene 5 antibody-positive myositis.
ReumatologiaDysregulation of YTHDF2 promotes the over expression of interferon beta in anti-MDA5 antibody-positive dermatomyositis.
Arthritis research & therapyComparison of disease severity and activity between juvenile- and adult-onset dermatomyositis: a multicentre cohort study.
Rheumatology (Oxford, England)Serum interferon-λ3 as a short-term biomarker of disease control in anti-MDA5-positive dermatomyositis-associated ILD.
Scientific reportsIgG from anti-MDA5⁺ CADM patients impairs NK cell function via CD16 in RP-ILD.
Translational research : the journal of laboratory and clinical medicineIntravitreal Clindamycin for Multifocal Toxoplasma Retinochoroiditis in Immunocompromised Patients: A Case Series with Aqueous Humor PCR Confirmation.
Ocular immunology and inflammationWhen viral infections meet the anti-MDA5 antibody-positive dermatomyositis.
Frontiers in immunologyFrom Rhabdomyolysis to a Lymphoproliferative Disorder: A Long Diagnostic Work-Up.
CureusSerum ferritin trajectories predict mortality risk in anti-melanoma differentiation-associated protein 5 antibody-positive dermatomyositis: a longitudinal cohort study.
The European respiratory journalAn Unusual Case of Juvenile Dermatomyositis Complicated by Macrophage Activation Syndrome.
International journal of dermatologyAlterations of mucosal-associated invariant T cells in dermatomyositis.
Clinical and experimental rheumatologyComparison of pre- and post-natal environmental exposures in United States versus Brazilian patients with juvenile dermatomyositis.
Clinical and experimental rheumatologyMarked Long-Term Improvement in Lung Function in Melanoma Differentiation-Associated Protein 5 Antibody-Positive Dermatomyositis Patients: Experience of a Single-Center Longitudinal Cohort in North America.
Arthritis care & researchPost-COVID-19 Inflammatory Myopathy With Dermatomyositis-Mixed Connective Tissue Disease (MCTD) Overlap Features and Epiglottitis: A Case Report.
CureusStevens-Johnson syndrome/toxic epidermal necrolysis as the initial presentation of paraneoplastic anti-TIF1-γ dermatomyositis.
SAGE open medical case reportsDermatomyositis and Polymyositis: Are Both Ends of a Same Spectrum?
Journal of cosmetic dermatologyClinical prognosis and cancer risk assessment in autoimmune diseases with anti-TIF1γ alone or concurrent with anti-Ro52 antibodies in a Taiwanese cohort.
Clinical immunology (Orlando, Fla.)Lenabasum, a cannabinoid type 2 receptor agonist, exerts anti-inflammatory effects in dermatomyositis.
The Journal of investigative dermatologyA Case of Antinuclear Antibody-Negative Dermatomyositis with Interstitial Lung Disease.
Clinical laboratoryJAK Inhibition Restores Epidermal Homeostasis and Modulates Immune Responses in Dermatomyositis Skin: A Spatial Transcriptomic Pilot Study.
The Journal of dermatologySex Differences in PROMIS Pediatric Depressive Symptoms, Anxiety, and Psychological Stress Among Children and Adolescents Living With Pediatric Rheumatic Diseases.
The Journal of rheumatologyThe clinical values of laboratory inflammatory and composite indices in predicting rapidly progressive interstitial lung disease and prognosis in anti-MDA5 dermatomyositis patients.
Clinical rheumatologyThe Refractory DermatoMyositis Index (ReDMI): a clinical tool to predict refractory disease in patients with dermatomyositis.
Clinical and experimental rheumatologyAssociation of NXP2 autoantibodies with a more severe clinical phenotype of juvenile dermatomyositis.
Clinical and experimental rheumatologyDermatomyositis following COVID-19 Vaccination: A Case Report and Review of Vaccine-associated Autoimmune Phenomena.
Acta medica Philippina[Interferon scores in the management of rheumatic systemic diseases].
Zeitschrift fur RheumatologieImmunotherapies in autoimmune inflammatory myopathies: Rationale and therapeutic updates.
Handbook of clinical neurologyIntravenous immunoglobulin use in neurology.
Handbook of clinical neurologySemiquantitative HRCT scoring: a reliable predictor of rapidly progressive interstitial lung disease in patients with anti-MDA5 positive dermatomyositis.
Quantitative imaging in medicine and surgeryEvaluating heterogeneity in MDA-5+ dermatomyositis through cluster analyses.
Journal of the European Academy of Dermatology and Venereology : JEADVEnergy-Based Devices for the Treatment of Cutaneous Lesions in Patients With Lupus Erythematosus and Dermatomyositis.
Journal of cosmetic dermatologySera from patients with dermatomyositis and antisynthetase syndrome mediate muscle weakness, impair mitochondrial respiration and induce local cytokine production in muscle tissue.
Journal of autoimmunityRisk Factors Associated with the Development of Thrombotic Microangiopathy in Patients with Dermatomyositis.
International journal of molecular sciencesPeripheral blood immunophenotypic diversity in patients with anti-MDA5+ dermatomyositis and its impact on prognosis.
Clinical and experimental rheumatologyNXP-2-positive dermatomyositis presenting with pronounced unilateral lower extremity subcutaneous edema.
JAAD case reportsProlonged remission of dermatomyositis and autoantibody negativization following SARS-CoV-2 infection in an elderly patient.
AutoimmunityValidation of International Classification of Diseases Codes for Dermatologic Conditions: A Systematic Review.
JAMA dermatologyInterferon-β Triggers Z-DNA Binding Protein 1-Mediated PANoptosis in T Cells of Anti-Melanoma Differentiation-Associated Protein 5 Antibody-Positive Dermatomyositis.
ImmunologyUnmasking inflammation in juvenile dermatomyositis: myokine profiles of patients and bioengineered human muscle.
Frontiers in immunologyPregnancy outcomes in idiopathic inflammatory myopathies: a Portuguese multicentre study.
Frontiers in medicineNailfold videocapillaroscopy in the assessment of juvenile connective tissue diseases.
Clinical and experimental rheumatologyCTRP1 regulates skeletal muscle differentiation through quality control of mitochondrial dynamics and function.
Molecular therapy : the journal of the American Society of Gene TherapyAnti-MDA5 antibody-positive interstitial lung disease without prominent skin or muscle manifestations: A high-risk and potentially overlooked subgroup.
Respiratory medicineBaricitinib alleviates myositis-associated interstitial lung disease in mice by inhibiting the NETs-cGAS-STING-EMT axis.
International immunopharmacologyRituximab for Early-Onset Juvenile Dermatomyositis Complicated by Interstitial Lung Disease.
Case reports in pediatricsIdentifying immunostimulatory herbal supplements that may flare autoimmune skin diseases: a systematic scoping review.
Lupus science & medicineParaneoplastic dermatomyositis with Kaposi's sarcoma: A case report.
SAGE open medical case reportsGenetic Association Between Polymyositis/Dermatomyositis and Epilepsy: Insights From Mendelian Randomization and Bioinformatic Analyses.
Brain and behaviorParaneoplastic Amyopathic Dermatomyositis Suspect by Nailfold Capillaroscopy in a Patient With Breast Carcinoma.
International journal of rheumatic diseasesFlagellate Erythema: An Indicator of Underlying Malignancy in Dermatomyositis.
International journal of rheumatic diseasesTranscriptomic signatures in different tissues of anti-MDA5 positive dermatomyositis: Uncovering genes with predictive potential for RP-ILD.
Journal der Deutschen Dermatologischen Gesellschaft = Journal of the German Society of Dermatology : JDDGConcurrent paraneoplastic dermatomyositis and Sweet syndrome.
JAAD case reportsDermatomyositis is characterized by JAK1-mediated monocyte-driven vasculopathy and inflammation.
Science translational medicineAn Update on Dermatomyositis and Related Inflammatory Myopathies: Cutaneous Clues, Skeletal Muscle Involvement, and Advances in Pathogenesis and Treatment.
Muscles (Basel, Switzerland)Exhaustion of NK cells and interferon activation in anti-MDA5+ dermatomyositis are associated and determine the development of ILD.
Frontiers in immunologyMacrophage activation syndrome and rapidly progressive lung disease as life-threatening manifestations of anti-MDA5 antibody disease. A case report.
ReumatismoUnraveling the genetic association between autoimmune thyroid diseases and idiopathic inflammatory myopathies in the European population.
MedicineSit to stand and timed up and go in idiopathic inflammatory myopathies.
Scientific reportsDermatomyositis in women: a 15-year retrospective analysis of clinical patterns, malignancy risk, and long-term outcomes at a tertiary center.
Acta dermatovenerologica Alpina, Pannonica, et AdriaticaCase Report: Low-Dose Tofacitinib Reverses Progressive Interstitial Lung Disease in Anti-MDA5 Dermatomyositis After Failure of Traditional Immunosuppression.
International journal of rheumatic diseasesA Comparative Bibliometric Analysis of Pediatric Interstitial Lung Disease Treatment: Global Trends, Advances, and Future Directions (2004-2024).
Pediatric pulmonologyConcomitant IgA nephropathy and dermatomyositis: a case-based review.
Rheumatology internationalSerum Autoantibodies in Dermatomyositis and Systemic Lupus Erythematosus: A Systematic Review and Meta-Analysis.
Journal of cutaneous medicine and surgeryJuvenile dermatomyositis as a rare paraneoplastic manifestation of nasopharyngeal carcinoma.
Rheumatology (Oxford, England)Critical Limb Ischaemia in a Patient With Subcutaneous Nodules: Clues to a Hidden Systemic Disease.
CureusReal-world experience of anifrolumab in 30 patients with refractory DM: a multicentre-multidisciplinary retrospective study.
Rheumatology (Oxford, England)[Clinical characteristics, efficacy and safety of antifibrotic agents in elderly patients with connective tissue disease-associated interstitial lung disease].
Beijing da xue xue bao. Yi xue ban = Journal of Peking University. Health sciences[Rheumatic disease spectrum and immunological profile of anti-PM/Scl antibodies in idiopathic inflammatory myopathies].
Beijing da xue xue bao. Yi xue ban = Journal of Peking University. Health sciencesCorrigendum to "Diagnosis of neuropsychiatry disorder in patients with anti-MDA5 antibody dermatomyositis: A case report" [Heliyon Volume 9, Issue 12, December 2023, Article e22935].
HeliyonEfficacy of anifrolumab on skin, joint and lung involvement in anti-MDA5 positive dermatomyositis: a case report.
Frontiers in immunologyClinical use of intravenous immunoglobulin in juvenile dermatomyositis: indications, treatment course, and clinical outcomes.
Expert opinion on biological therapyAssociation of dermatological manifestations with in fertility: A systematic review of literature.
JPMA. The Journal of the Pakistan Medical AssociationDrooling as a Red Flag: Insights From a Case Series in Severe Dermatomyositis With Literature Review.
Clinical case reportsCaNO and eCO Might Be Potential Non-Invasive Biomarkers for Disease Severity and Exacerbations in Interstitial Lung Disease.
Journal of clinical medicineNew-onset anti-melanoma differentiation-associated gene 5 antibody positive clinically amyopathic dermatomyositis following COVID-19: A case report.
Internal medicine (Tokyo, Japan)RF-New Treatments in Dermatomyositis: Present and Future.
Actas dermo-sifiliograficasMDA5 Antibody Associated Juvenile Dermatomyositis Presenting as Rapidly Progressive Pulmonary Fibrosis-Case Report.
Journal of paediatrics and child healthArtifactual hypoglycemia caused by Raynaud's phenomenon: A case report with literature review.
Frontiers in endocrinologyUnilateral Facial Swelling as the Inaugural Sign of Anti-NPX2 Dermatomyositis: A Diagnostic Challenge in Oral Medicine.
Case reports in dentistryCardiac involvement in patients with anti-MDA5 Ab+ dermatomyositis: a cross-sectional study with cardiac magnetic resonance.
Quantitative imaging in medicine and surgeryPrognostic factors and a nomogram for survival in anti-MDA5 antibody-positive dermatomyositis-associated interstitial lung disease.
BMC pulmonary medicineMuscle mitochondrial changes in antisynthetase syndrome and other idiopathic inflammatory myopathies.
Journal of neuropathology and experimental neurologyMusculoskeletal Diseases: Mechanisms and Therapeutic Advances.
MedCommPredictive role of muscle MRI in juvenile dermatomyositis: A tertiary center experience.
European journal of radiologyAssociações
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Reliability of durometry to assess firmness of calcinosis lesions in Juvenile and adult dermatomyositis.
- Dermatomyositis masquerading as angioedema: a crucial differential not to overlook.
- Spatial transcriptomics reveals mechanism of autoimmunity driven by internalized autoantibodies.
- Anti-CD19 CAR T cells for pediatric patients with treatment-refractory autoimmune diseases.
- Identification of common genes and biomarkers between Dermatomyositis and rheumatoid arthritis through integrated bioinformatics.
- Association between IL1B rs16944 polymorphism and the risk of idiopathic inflammatory myopathies.
- Systematic literature review informing PReS/CARRA-endorsed recommendations for the treat-to-target strategy in juvenile dermatomyositis.
- Remission rates and predictors in idiopathic inflammatory myopathy subgroups: Insights from a single-center cohort.
- Lung transplant outcomes in myositis, systemic sclerosis and idiopathic pulmonary fibrosis: a multicenter retrospective analysis.
- Upadacitinib Versus Tofacitinib in Anti-MDA5-Positive Dermatomyositis With Interstitial Lung Disease: A Multi-Centre Cohort Study Emulating a Target Trial.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:221(Orphanet)
- MONDO:0016367(MONDO)
- Dermatomiosite e Polimiosite(PCDT · Ministério da Saúde)
- GARD:6263(GARD (NIH))
- Busca completa no PubMed(PubMed)
- Artigo Wikipedia(Wikipedia)
- Q681160(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
