Ventrículo direito de dupla saída (DORV) é uma condição cardíaca rara em que a aorta e a artéria pulmonar — os dois grandes vasos que saem do coração — se originam, total ou em sua maior parte, do ventrículo direito.
Introdução
O que você precisa saber de cara
Ventrículo direito de dupla saída (DORV) é uma condição cardíaca rara em que a aorta e a artéria pulmonar — os dois grandes vasos que saem do coração — se originam, total ou em sua maior parte, do ventrículo direito.
Tem tratamento?
Escala de raridade
<1/50kMuito rara
1/20kRara
1/10kPouco freq.
1/5kIncomum
1/2k
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Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Partes do corpo afetadas
+ 11 sintomas em outras categorias
Características mais comuns
Os sintomas variam de pessoa para pessoa. Abaixo estão as 28 características clínicas mais associadas, ordenadas por frequência.
Linha do tempo da pesquisa
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Genética e causas
O que está alterado no DNA e como passa nas famílias
Nenhum gene associado encontrado
Os dados genéticos desta condição ainda estão sendo catalogados.
Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
Remédios, cuidados de apoio e o que precisa acompanhar
Onde tratar no SUS
Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)
🇧🇷 Atendimento SUS — Ventrículo direito com dupla saída
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Outros ensaios clínicos
7 ensaios clínicos encontrados, 2 ativos.
Publicações mais relevantes
Mostrando amostra de 200 publicações de um total de 709
Neurodevelopmental outcomes in preschool children with congenital heart defects: A case-control study using Ages & Stages Questionnaire.
Um estudo comparando o neurodesenvolvimento de crianças pré-escolares com doenças cardíacas congênitas que exigiram cirurgia (incluindo o Dupla Saída do Ventrículo Direito - DORV) e controles saudáveis, revelou que, embora a pontuação média geral fosse comparável, as crianças com defeitos cardíacos tinham cinco vezes mais chances de obter uma pontuação baixa no questionário ASQ. Este risco aumentado foi impulsionado principalmente por casos de Defeito do Septo Ventricular (DSV) não detectado prenatalmente, e uma tendência de pontuações mais baixas em Transposição das Grandes Artérias (TGA), especialmente quando não detectada antes do nascimento, sem diferenças específicas reportadas para o DORV isoladamente. Esses achados são cruciais para médicos e pais, sublinhando a importância do acompanhamento de todas as crianças com cardiopatia congênita cirúrgica, incluindo aquelas com DORV, para identificar precocemente e intervir em potenciais atrasos no desenvolvimento.
🇧🇷 traduzidoAnaesthetic management in a neonate with a double-outlet right ventricle undergoing repair of leaking myelomeningocele.
Este artigo destaca a extrema complexidade do manejo anestésico em recém-nascidos com múltiplos defeitos congênitos graves, como a Dupla Via de Saída do Ventrículo Direito (DORV) e mielomeningocele. Para médicos, o relato demonstra que uma estratégia de anestesia intravenosa total, utilizando dexmedetomidina e fentanil, pode ser uma opção segura e eficaz para manter a estabilidade hemodinâmica e oferecer neuroproteção em cirurgias de alto risco nestes pacientes pediátricos.
🇧🇷 traduzidoSustained remission of post-Fontan protein-losing enteropathy achieved by combination therapy with high-dose spironolactone and the somatostatin analogue octreotide: a case report.
Este relato de caso demonstrou o tratamento bem-sucedido de enteropatia perdedora de proteínas (EPP) pós-Fontan, grave e refratária, em uma criança com cardiopatia congênita complexa (incluindo ventrículo direito de dupla saída). Após falha da terapia padrão, a combinação de espironolactona em dose alta com octreotide induziu remissão completa da condição. Notavelmente, o octreotide pôde ser descontinuado com a manutenção da remissão a longo prazo, sugerindo que a espironolactona em doses elevadas pode ser uma opção eficaz para pacientes e médicos, especialmente para reduzir a exposição prolongada ao octreotide e seus potenciais efeitos adversos.
🇧🇷 traduzidoYoung-onset hepatocellular carcinoma following double outlet right ventricle surgery without liver congestion: a case report with genetic analysis.
Este artigo descreve o caso incomum de uma jovem de 16 anos que desenvolveu câncer de fígado (HCC) anos após uma cirurgia para cardiopatia congênita (DORV), sem as habituais complicações hepáticas como congestão ou cirrose. A análise genética aponta para fatores genéticos subjacentes, sugerindo um mecanismo diferente de desenvolvimento do câncer. Para médicos e pacientes, isso significa que o rastreamento para câncer de fígado deve ser considerado em indivíduos de alto risco com cardiopatias congênitas, mesmo na ausência de problemas hepáticos visíveis ou função hepática alterada.
🇧🇷 traduzidoLong-term Outcomes of Standardized Strategy in Arterial Switch Operation: An 18-Year Review in a Single Center.
Este estudo avaliou os resultados a longo prazo da Cirurgia de Switch Arterial (ASO) utilizando uma estratégia cirúrgica padronizada, mostrando desfechos geralmente favoráveis com baixa mortalidade operatória e tardia. No entanto, desafios significativos a longo prazo incluem a necessidade de reintervenção em cerca de um quarto dos pacientes e uma alta incidência de dilatação da raiz neo-aórtica (em 63% dos pacientes em 15 anos). Pacientes com subtipos mais complexos de Transposição das Grandes Artérias (TGA) têm maior risco dessas complicações e de reoperações, o que requer monitoramento contínuo.
🇧🇷 traduzidoPublicações recentes
Half-turned truncal switch for transposition of the great arteries with left ventricular outflow tract obstruction.
In vitro construction of handmade polytetrafluoroethylene right ventricle-to-pulmonary artery valved conduit using a modification of the Ozaki technique.
Aortic root replacement after repaired congenital conotruncal defects: A surgical challenge.
Ultrasound-Guided Superficial Temporal Artery Cannulation for Proximal Arterial Pressure Monitoring During Coarctation Repair With an Aberrant Right Subclavian Artery in a Low-Birth-Weight Neonate.
Double-inlet double-outlet right ventricle: a case report and systematic review of the literature with cluster analysis.
📚 EuropePMC719 artigos no totalmostrando 199
Half-turned truncal switch for transposition of the great arteries with left ventricular outflow tract obstruction.
JTCVS techniquesIn vitro construction of handmade polytetrafluoroethylene right ventricle-to-pulmonary artery valved conduit using a modification of the Ozaki technique.
JTCVS techniquesAortic root replacement after repaired congenital conotruncal defects: A surgical challenge.
JTCVS openSwitch-back Ross, Bentall/Konno and valve-sparing root replacement: three cutting-edge solutions to complex left ventricular outflow tract obstruction post arterial switch in Taussig-Bing anomaly.
Multimedia manual of cardiothoracic surgery : MMCTSUltrasound-Guided Superficial Temporal Artery Cannulation for Proximal Arterial Pressure Monitoring During Coarctation Repair With an Aberrant Right Subclavian Artery in a Low-Birth-Weight Neonate.
CureusDouble-inlet double-outlet right ventricle: a case report and systematic review of the literature with cluster analysis.
Cardiology in the youngSingle Ventricle: Radiology Primer for Preprocedural Evaluation.
Radiographics : a review publication of the Radiological Society of North America, IncEnhancer of zeste homolog 2 (Ezh2) is required in mouse Isl1-expressing progenitors for proper development of cardiac and skeletal hindlimb structures.
Biology openNeurodevelopmental outcomes in preschool children with congenital heart defects: A case-control study using Ages & Stages Questionnaire.
PloS oneA Case of Restrictive Dermopathy With Atypical Cardiac Anomalies and a Novel ZMPSTE24 Variant.
American journal of medical genetics. Part ASuccessful palliation and Fontan completion in a patient with double outlet right ventricle and intact ventricular septum.
Cardiology in the youngNorwood procedure with left coronary artery reimplantation for hypoplastic left heart syndrome combined with Anomalous left coronary artery from the right pulmonary artery: a case report.
General thoracic and cardiovascular surgery casesDurability of the Arterial Switch Operation: Long-Term Survival and Structural Sequelae in a Multicentre Cohort.
The Canadian journal of cardiologyInfective endocarditis in an adult male patient with tetralogy of Fallot physiology secondary to double outlet right ventricle presenting with stroke: a complex presentation with multiorgan dysfunction-a case report.
Journal of medical case reportsAnaesthetic management in a neonate with a double-outlet right ventricle undergoing repair of leaking myelomeningocele.
BMJ case reportsCase Report: Parachute tricuspid valve in association with cyanotic congenital heart disease and juxtaposed atrial appendages in a 1-year-old boy-a rare anatomical association.
Frontiers in cardiovascular medicineSustained remission of post-Fontan protein-losing enteropathy achieved by combination therapy with high-dose spironolactone and the somatostatin analogue octreotide: a case report.
BMC pediatricsOne-stage repair of Taussig-Bing anomaly in a neonate with aortic arch hypoplasia and single coronary artery.
Multimedia manual of cardiothoracic surgery : MMCTSSurgical management of double outlet right ventricle with outflow obstruction: a systematic review of biventricular strategies.
Cardiology in the youngPhysics-Informed Emulation of Systemic Circulation for Fast Parameter Estimation and Uncertainty Quantification.
International journal for numerical methods in biomedical engineeringReference standards and diagnosis-specific trends in cardiorespiratory fitness in paediatric patients with repaired CHD.
Cardiology in the youngDouble-outlet Right Ventricle with Subaortic Ventricular Septal Defect and Severe Pulmonary Valve Stenosis, but Only Minimal Cyanosis and No Murmur: A Paradox?
Journal of cardiovascular echographyHorseshoe Lung Associated with Left-sided Scimitar Syndrome in an Infant with Complex Congenital Heart Disease.
Journal of cardiovascular echographyReversal of Glenn-associated diffuse pulmonary arteriovenous malformations after total cavopulmonary connection: a case report.
Frontiers in cardiovascular medicineAccuracy of fetal echocardiography in detecting lesions associated with, and predicting surgical plan for, dextro-transposition of the great arteries and double outlet right ventricle with subpulmonary ventricular septal defect and predicted transposition physiology.
Ultrasound in obstetrics & gynecology : the official journal of the International Society of Ultrasound in Obstetrics and GynecologyInfant with Complex Congenital Cardiac Anomalies: A Case Report and Review of Literature.
Annals of African medicineDouble-Drainage Levoatrial Cardinal Vein: Cardiac CT Evaluation of Compensatory Pulmonary Venous Pathway in Univentricular Heart.
JACC. Case reportsPulmonary Vein-Triggered Atrial Fibrillation in Unrepaired Double-Outlet Right Ventricle With Pulmonary Atresia.
JACC. Case reportsA One-Dimensional (1D) Computational Fluid Dynamics Study of Fontan-Associated Liver Disease (FALD).
International journal for numerical methods in biomedical engineeringHaploinsufficiency of Endothelial Nitric Oxide Synthase Mitigates Beneficial Effects of Maternal Exercise on Fetal Heart Development During Pregestational Diabetes.
Journal of the American Heart AssociationTranscatheter pulmonary valve replacement with the venusP-valve system in a patient with double outlet right ventricle and transposition of the great arteries a first-in-human case report.
Frontiers in cardiovascular medicineThe 24-Segment Global Sphericity Index Is Useful for Assessing Fetal Cardiac Function and as an Indicator of Fetal Well-Being.
CureusDouble Outlet Right Ventricle With a Not-Directly-Committed Ventricular Septal Defect.
Korean circulation journalMultimodality Imaging of Double-Outlet Right Ventricle, Superior-Inferior Ventricles, and Malposed Great Arteries.
JACC. Case reportsA Novel STAG2 Frameshift Variant in Mullegama-Klein-Martinez Syndrome with Complex Conotruncal Heart Defect.
GenesCriss cross heart: an outflow tract defect?
Orphanet journal of rare diseasesRight Ventricular Myocardial Strain and Proteomic Analysis of Fetuses With Left Ventricular Hypoplasia: A Cross-Sectional Study.
Health science reportsYoung-onset hepatocellular carcinoma following double outlet right ventricle surgery without liver congestion: a case report with genetic analysis.
Clinical journal of gastroenterologyLong-term Outcomes of Standardized Strategy in Arterial Switch Operation: An 18-Year Review in a Single Center.
Korean circulation journalIdentifying Pathogenic Variants in Vietnamese Children with Functional Single Ventricle Based on Whole-Exome Sequencing.
Diagnostics (Basel, Switzerland)Balloon dilation of the para-device space to alleviate severe flow restriction in an oversized pulmonary flow restrictor: a case report.
BMC cardiovascular disordersSuccessful Transcatheter Pulmonary Valve Replacement Via the Azygous Vein in a Patient With Interrupted Inferior Vena Cava.
JACC. Case reportsLong-Term Surgical Outcomes in Double Outlet Right Ventricle Based on Detailed Anatomical Sub-Typology.
European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic SurgeryClarifying the Cardiovascular Morphology and Associated Abnormalities in Patients with Double Inlet Left Ventricle Using Multidetector CT Angiography.
Pediatric cardiologyOptimising pre-operative assessment in double-outlet right ventricle: the complementary role of echocardiography and CT angiography.
Cardiology in the youngMultisystem Phenotypic Spectrum in Pediatric Heterotaxy Syndrome: A Case Series.
CureusAnterior Pulmonary Artery Translocation with the Damus-Kaye-Stansel and Rastelli Procedures for Multilevel Tracheobronchomalacia with Double-Outlet Right Ventricle (S, D, L) and Right Pulmonary Agenesis.
European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic SurgeryEndoscopic Third Ventriculostomy in Hydrocephalus Due to Complex Congenital Heart Disease: A Case Report.
CureusIatrogenic aorto-right ventricular fistula after transcatheter pulmonary valvuloplasty.
Asian cardiovascular & thoracic annalsDouble-Outlet Right Ventricular Malformation in a Two-Year-Old Aberdeen Angus Cow.
Animals : an open access journal from MDPIComparison for Long-Term Results of the Modified Réparation à l´étage Ventriculaire and Rastelli Repair.
World journal for pediatric & congenital heart surgeryAcute stent placement for dynamic airway collapse after cardiac surgery in congenital heart disease with bronchial stenosis: A case report.
MedicineConotruncal Anomalies of the Fetus.
Ultraschall in der Medizin (Stuttgart, Germany : 1980)Successful ablation of ventricular tachycardia in which resected infundibular septum served as a critical isthmus in a patient with double-outlet right ventricle after Rastelli surgery.
HeartRhythm case reportsClassification of Fetal Congenital Heart Disease by Prenatal Ultrasound and Its Diagnostic Value.
International journal of general medicineTechnical Advances and Outcomes of Fetal Atrial Septal Intervention for Restrictive or Intact Atrial Septum.
Circulation. Cardiovascular interventionsGenetic Variants Associated With Congenital Heart Disease: A Meta-Analysis of Ethnicity and Subtype-Specific Susceptibility.
Circulation. Genomic and precision medicineFirst-Trimester Detection of Conotruncal Anomalies Using Transabdominal SlowflowHD: A Case Series and Proof-of-Concept Study.
Journal of ultrasound in medicine : official journal of the American Institute of Ultrasound in MedicineUtility of inhaled nitric oxide for pulmonary hypertension in cyanotic congenital heart disease: a cohort study with propensity score matching.
Medical gas researchOutcomes of Fontan patients undergoing combined heart-liver transplantation in pediatric hospitals across the United States.
The Journal of thoracic and cardiovascular surgeryKRAS4B is required for placental development.
Cellular and molecular life sciences : CMLSInfective endocarditis leading to pulmonary pseudoaneurysm and severe pulmonary valve regurgitation: A case report.
MedicineReaching consensus as to how knowledge of development underscores our understanding of deficient ventricular septation.
Cardiology in the youngStraddling of the mitral valve in the set of situs solitus in dextrocardia with atrio-ventricular connection discordance and double-outlet right-ventricle: a rare case report.
Archivos de cardiologia de MexicoHeterotaxy syndrome with biliary atresia: a case report.
The Pan African medical journalA rare complication of cyanotic CHD: brain abscess.
Cardiology in the youngThe Ultrasound and Genetic Characteristics of Fetuses With Laterality Defects-A Prenatal Cohort in Asian Population.
Prenatal diagnosisIncidence, Associated Abnormalities, and Outcomes of Dextrocardia: A Registry-based Study in Saudi Arabia.
Journal of the Saudi Heart AssociationDouble-Outlet Right Ventricle in an Adult With a Univentricular Heart and Total Situs Inversus.
JACC. Case reportsPostpartum ischemic stroke due to persistent left superior vena cava to left atrium after DORV repair: a case report and literature review.
BMC cardiovascular disordersCongenital Conundrum: Unraveling the Puzzle of Double Outlet Right Ventricle for the Neonatologist.
NeoReviewsUsing Multimodality Imaging and 3-Dimensional Printed Models to Guide Decision-Making for Complex Congenital Biventricular Repair.
JACC. Case reportsMortality Associated With Viral Bronchiolitis in a Pediatric Department: A Retrospective Analysis.
CureusSignificance of Papillary and Trabecular Muscular Volume in Right Ventricular Volumetry with Cardiac MR Imaging.
Magnetic resonance in medical sciences : MRMS : an official journal of Japan Society of Magnetic Resonance in MedicineNavigating Complexity: Advanced Visualization for Müllerian Anomalies and its Implications for Diagnoses and Surgical Planning.
Journal of pediatric and adolescent gynecologyA Retrospective Study on the Imaging Spectrum of Functional Single Ventricle and Its Associations.
The Indian journal of radiology & imagingAortic Disturbed Flow Is Associated with Aortic Angle in Patients with Tetralogy of Fallot or Double-Outlet Right Ventricle.
Magnetic resonance in medical sciences : MRMS : an official journal of Japan Society of Magnetic Resonance in MedicineCoarctation Stenting When Origin of Aberrant Right Subclavian Artery Is Before Stenotic Segment.
JACC. Case reportsValve-preserving technique for tetralogy of fallot by transannular delamination.
Asian cardiovascular & thoracic annalsUnraveling the complexities of double outlet right ventricle (DORV): A rare case of congenital heart disease with bidirectional shunting in a young girl.
Radiology case reportsHemodynamics of a right ventricular outflow tract aneurysm assessed with 4D flow MRI before and after unilateral pulmonary artery balloon angioplasty: A case report.
Radiology case reportsProminent Chiari Network as a Cause of Cyanosis in Infants: A Case Report and Implications for Pediatric Cardiology Practice.
Journal of clinical ultrasound : JCUA new association between Kleefstra syndrome and Panayiotopoulos epilepsy.
Italian journal of pediatricsLongitudinal Trends in Pediatric Survival by Congenital Heart Defect in Texas, 1999 to 2017.
JACC. AdvancesAn isolated double-inlet right ventricular malformation: a case report and review of the literature.
Journal of medical case reportsSingle and Double Root Translocation for Transposition and Malposition of the Great Arteries.
Seminars in thoracic and cardiovascular surgery. Pediatric cardiac surgery annualCan We Better Understand the Anatomy of Channels Between the Ventricles on the Basis of Knowledge of Their Development?
World journal for pediatric & congenital heart surgeryAspirin Use Following the Arterial Switch Operation in the United States: Variability, Trends, and Perioperative Outcomes.
World journal for pediatric & congenital heart surgeryHemodynamic rounds: Transcatheter creation of ventricular septal defect in pulmonary arterial hypertension with suprasystemic pressures.
Annals of pediatric cardiologyManagement dilemma of a child with long-segment tracheal stenosis, double outlet right ventricle, and left pulmonary artery sling: For single or staged repair?
Annals of pediatric cardiologyTotal anomalous pulmonary venous connection - prenatal echocardiography and neonatal follow-up.
Journal of ultrasonography[MÖB-03] Extra-Pericardial Modified Blalock-Taussig Shunt Via Sternotomy in Patients with A Right Aortic Arch.
Turk gogus kalp damar cerrahisi dergisiBorn to be Bad: Combination of Aorticopulmonary Window With Double-Outlet Right Ventricle-Pulmonary Atresia.
Echocardiography (Mount Kisco, N.Y.)Complex Management of Thromboembolism in Double-Outlet Right Ventricle.
JACC. Case reportsAn extreme case of Raghib syndrome: combination of mirror-image dextrocardia, single atrium, double-outlet right ventricle, and patent ductus arteriosus.
European heart journalPractical approach to using cardiac magnetic resonance imaging for pre-surgical planning in complex paediatric congenital heart disease.
Pediatric radiologyEnhancing management of double outlet right ventricle when the interventricular communication is remote from the arterial roots through three-dimensional printing.
3D printing in medicineCriss-cross heart with complex cardiac malformation, situs inversus totalis and bronchial dysplasia.
BMC cardiovascular disordersCumulative radiation dose in children with congenital heart disease: national data 2000-2021, stratified by diagnosis, age, and imaging modality.
Acta radiologica (Stockholm, Sweden : 1987)Criss-cross heart with double-outlet right ventricle and interrupted aortic arch in a rare adult survivor: computed tomography insights.
European heart journalUtility of 3-Dimensional Echocardiography in Patients With Complex Intracardiac Connections and Ventricular Septal Defects.
JACC. Case reportsRepeated Systolic Anterior Motion of the Mitral Valve After Double Outlet Right Ventricle Repair.
Annals of thoracic surgery short reportsOutcomes of Fontan operation in patients with conotruncal anomalies from Australia and New Zealand Fontan Registry: a review of 1835 patients†.
European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic SurgeryPregnancy in ACHD women: crucial role of multidisciplinary clinical roadmap.
The journal of maternal-fetal & neonatal medicine : the official journal of the European Association of Perinatal Medicine, the Federation of Asia and Oceania Perinatal Societies, the International Society of Perinatal ObstetriciansParameter selection and optimization of a computational network model of blood flow in single-ventricle patients.
Journal of the Royal Society, Interface[Double Outlet Right Ventricle (DORV)].
The Thoracic and cardiovascular surgeonPediatric Three-dimensional Transesophageal Echocardiography: A Game Changer in Congenital Heart Disease.
Journal of cardiovascular echographySurgical Repair of Double Outlet Right Ventricle Infants Guided by Three Dimensional-Computed Tomography Cardiac Modeling and Printing.
World journal for pediatric & congenital heart surgeryA De Novo Frameshift Variant in SMC1A Causes Non-Classic Cornelia de Lange Syndrome With Epilepsy: A Case Report and Literature Review.
Molecular genetics & genomic medicinePrevalence of immunological aberrations and 22q11.2 deletion in children with conotruncal anomalies: A cross-sectional study.
Annals of pediatric cardiologyDouble Outlet Right Ventricle: A Rare Finding in a 15-Month-Old Female With Failure to Thrive.
Clinical case reportsPrinted Models for Better Prediction of Surgery in Patients with Double Outlet Right Ventricle.
Pediatric cardiologyClarifying the Cardiovascular Morphology and Associated Abnormalities in Patients with Double Inlet Right Ventricle Using Multidetector CT Angiography.
Pediatric cardiologyDouble-outlet right ventricle in a patient with Takenouchi-Kosaki syndrome.
Pediatrics and neonatologyInterventional Treatment of Acute Right Ventricular Outflow Tract Infectious Endocarditis: A Bridge to Surgical or Percutaneous Pulmonary Valve Replacement.
Catheterization and cardiovascular interventions : official journal of the Society for Cardiac Angiography & InterventionsTechnique for staged biventricular repair of heterotaxy, double-outlet right ventricle, unbalanced atrioventricular canal defect, and transposition.
JTCVS techniquesCongenital heart defects differ following left versus right avian cardiac neural crest ablation.
Developmental biologyCyclin-dependent kinase 13 is indispensable for normal mouse heart development.
Journal of anatomyRelating normal human cardiac development to the anatomical findings in the congenitally malformed heart.
Clinical anatomy (New York, N.Y.)Successful surgical repair of Taussig Bing anomaly with pulmonary artery and pulmonary valve stenosis in a neonate patient: A case report.
International journal of surgery case reportsContemporary prenatal diagnosis of congenital heart disease in a regional perinatal center lacking onsite pediatric cardiac surgery: obstetrical and neonatal outcomes.
Journal of perinatal medicineA Prevalent TMEM260 Deletion Causes Conotruncal Heart Defects, Including Truncus Arteriosus.
American journal of medical genetics. Part ASuccessful repair of infracardiac total anomalous pulmonary venous connection with nonconfluent bilateral pulmonary veins.
Asian cardiovascular & thoracic annalsVery high take-off the right coronary artery with double outlet right ventricle.
Cardiology in the youngPrenatally Diagnosed Case of Successful Survival of an Unguarded Mitral Valve Orifice.
JACC. Case reportsInvestigation of the Clinical Value of Four Visualization Modalities for Congenital Heart Disease.
Journal of cardiovascular development and diseaseDouble-Outlet Right Ventricle With Intact Ventricular Septum and Left Atrioventricular Valve Regurgitation in a Patient With Right Atrial Isomerism.
World journal for pediatric & congenital heart surgeryHigh-resolution three-dimensional atlas of congenital heart defects based on micro-CT images of human postmortem wax-infiltrated heart specimens.
Cardiovascular pathology : the official journal of the Society for Cardiovascular PathologyNationwide Birth Prevalence of Crucial Congenital Heart Defects From 2014 to 2018 in Korea.
Korean circulation journalSpectrum of Heart Diseases in Children in a National Cardiac Referral Center Tanzania, Eastern Africa: A Six-Year Overview.
Global heartSurgical correction of total anomalous pulmonary venous connection to persistent left-sided superior vena cava: a case report.
European heart journal. Case reportsLeft ventricular apical pacing-induced heart failure in a child after congenital heart surgery: a case report.
European heart journal. Case reportsLong-term Outcome After Repair of Transposition of the Great Arteries With Aortic Arch Obstruction.
The Annals of thoracic surgeryApplication of array comparative genomic hybridization on the DNA extracted from cultured amniocytes for rapid diagnosis of 22q11.2 microdeletion in a pregnancy with a normal karyotype at amniocentesis and double outlet right ventricle and transposition of great arteries on level II ultrasound.
Taiwanese journal of obstetrics & gynecology[Analysis of Prenatal Ultrasound Manifestations in 15 Cases of Cantrell Syndrome].
Sichuan da xue xue bao. Yi xue ban = Journal of Sichuan University. Medical science editionFollow-up of a Term Infant with a Prenatal Diagnosis of Double-Outlet Right Ventricle.
NeoReviewsArterial Switch Operation for Transposition of the Great Arteries: Can We Do it Better?
JACC. AdvancesClinical Course of TGA After Arterial Switch Operation in the Current Era.
JACC. AdvancesLong-term Outcomes of Surgical Repair for Corrected Transposition of the Great Arteries.
The Annals of thoracic surgeryClinical Course of Residual Ventricular Septal Defects After Congenital Heart Disease Repair.
Pediatric cardiologyA new approach to surgical correction of double-outlet right ventricle with remote interventricular communication.
JTCVS techniquesHuman Genetics of Defects of Situs.
Advances in experimental medicine and biologyMolecular Pathways and Animal Models of Tetralogy of Fallot and Double Outlet Right Ventricle.
Advances in experimental medicine and biologyHuman Genetics of Tetralogy of Fallot and Double-Outlet Right Ventricle.
Advances in experimental medicine and biologyClinical Presentation and Therapy of Tetralogy of Fallot and Double-Outlet Right Ventricle.
Advances in experimental medicine and biologyCardiac Transcription Factors and Regulatory Networks.
Advances in experimental medicine and biologyCardiac Development and Animal Models of Congenital Heart Defects.
Advances in experimental medicine and biologyReoperations in Adolescents and Adults After Prior Arterial Switch Operation: The Society of Thoracic Surgeons Congenital Heart Surgery Database Analysis.
The Annals of thoracic surgerySurgical repair of unusual variant of double-outlet right ventricle with discordant atrioventricular connections and superior-inferior ventricles.
JTCVS techniquesRelationship between diagnosis of conus arteriosus malformation and genetic diagnosis results in fetal cardiac axis abnormalities by echocardiography during middle pregnancy.
Frontiers in cardiovascular medicineThe developmental processes of ventricular septal defects with outflow tract malalignment.
Annals of anatomy = Anatomischer Anzeiger : official organ of the Anatomische GesellschaftClinical implications of dextrocardia based on four visceroatrial situs studies.
Pediatrics and neonatologyRecent advances in multimodal imaging in tetralogy of fallot and double outlet right ventricle.
Current opinion in cardiologyImpact of right ventriculotomy on cardiac function after pulmonary valve sparing repair of tetralogy of Fallot and double outlet right ventricle with pulmonary stenosis.
Cardiology in the youngRepair of the complete atrioventricular septal defect-impact of postoperative moderate or more regurgitation.
Interdisciplinary cardiovascular and thoracic surgeryAtrioventricular valve surgery in patients with univentricular heart and two separate atrioventricular valves.
Cardiology in the youngEn Bloc Rotation of the Outflow Tracts - Double Root Translocation.
Seminars in thoracic and cardiovascular surgery. Pediatric cardiac surgery annualTwo-Dimensional and Doppler trans-thoracic echocardiographic patterns of suspected pediatric heart diseases at Tibebe--Ghion specialized Teaching Hospital and Adinas General Hospital, Bahir Dar, North-west Ethiopia:-An experience from an LMIC.
PloS oneNavigating the spectrum of double-outlet right ventricle presentations: Outcomes from a contemporary cohort based on subtypes.
Echocardiography (Mount Kisco, N.Y.)Three-dimensional printed moulds to obtain silicone hearts with congenital defects for paediatric heart-surgeon training.
European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic SurgeryPreoperative surgical planning for biventricular repair of double outlet right ventricle by using a 3D heart model.
Quantitative imaging in medicine and surgeryDouble outlet right ventricle - the 50% rule has always been about the conus.
Current opinion in cardiologyAntifungal medication use during early pregnancy and the risk of congenital heart defects in the National Birth Defects Prevention Study, 1997-2011.
Birth defects researchWhat are the conotruncal malformations?
The Journal of thoracic and cardiovascular surgeryGaming on an Immersive Virtual Reality Platform to Ameliorate the Level of Anxiety in Patients Undergoing Congenital Heart Disease.
CureusDifferent leadless pacemakers working in harmony (Aveir in the atrium/Micra AV2 in the ventricle) in a patient with dextrocardia and double outlet right ventricle after high-risk infected device extraction.
Journal of cardiovascular electrophysiologyLong-term results after the réparation à l'étage ventriculaire procedure for transposition of the great arteries and double-outlet right ventricle with pulmonary stenosis.
European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic SurgeryMulticentre study on late outcomes of biventricular repair of double outlet right ventricle.
European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic SurgeryPersistent neo-aortic root dilatation and aortic valve insufficiency after arterial switch operation following prior pulmonary artery banding.
Indian journal of thoracic and cardiovascular surgeryComprehensive Multiomics Analysis of Monozygotic Twin Discordant for Double Outlet Right Ventricle.
Twin research and human genetics : the official journal of the International Society for Twin StudiesHow best can we name the channels seen in the setting of deficient ventricular septation?
Cardiology in the youngIntracardiac Three-Dimensional Image as Surgical Decision-Making Tool of Congenital Heart Disease.
Pediatric cardiology3D Printed Cardiac Models as an Adjunct to Traditional Teaching of Anatomy in Congenital Heart Disease-A Randomised Controlled Study.
Heart, lung & circulationRecanalized vein of marshall following bidirectional glenn surgery.
The Journal of invasive cardiologyA Rare Entity: Double Outlet of Both Ventricles.
World journal for pediatric & congenital heart surgeryGrowth of the Neo-Aortic Root and Prognosis of Transposition of the Great Arteries.
Journal of the American College of CardiologyCardiovascular anomalies in patients with Tessier syndrome: a systematic review.
European journal of pediatricsTrans-aortic DORV repair.
Indian journal of thoracic and cardiovascular surgeryLower Socioeconomic Status is Associated with an Increased Incidence and Spectrum of Major Congenital Heart Disease and Associated Extracardiac Pathology.
Pediatric cardiologyComplex cyanotic congenital heart disease and cervical spine surgery: Ticking all the right boxes.
Annals of cardiac anaesthesiaImproved Surgical Outcomes in Adults with Congenital Heart Disease and Decompensated Heart Failure: The Role of Perioperative Medical Optimization.
The American journal of case reportsDouble outlet right ventricle.
Frontiers in pediatricsOptimizing Surgical Selection for Transposition With Left Ventricular Outflow Tract Obstruction.
The Annals of thoracic surgeryOutcomes of neo-aortic valve and root surgery late after arterial switch operation.
The Journal of thoracic and cardiovascular surgeryEarly Outcomes of Pulmonary Valve Replacement With the Edwards Inspiris Resilia Pericardial Bioprosthesis.
World journal for pediatric & congenital heart surgeryStenting for Left Ventricular Outflow Tract Stenosis after Double Outlet Right Ventricle Repair.
Acta Cardiologica SinicaOutcomes of atrioventricular septal defects with and without down syndrome: analysis of the national inpatient database.
Cardiology in the youngA 20-year follow-up of successful surgical management for a complex case of pentalogy of fallot and dextrocardia with systemic and pulmonary venous anomalies: A rare case report.
International journal of surgery case reportsThe Arterial Switch Operation in the Developing World: Risk Factors and Current Outcomes.
The Annals of thoracic surgeryExploring the Role of Modified Vascular Anatomical Molding (MVAM) in Prenatal Diagnosis Teaching and Prognosis Prediction of Fetal Complex Congenital Heart Disease (CCHD): A Preliminary Study.
International journal of general medicineAtrioventricular conduction recovery immediately after the re-operation in a repaired CHD patient.
Cardiology in the youngPerioperative Management of Emergency Craniotomes in Children With Cyanotic Congenital Heart Disease: A Case Series.
CureusCharacterization of ultrasound and postnatal pathology in fetuses with heterotaxy syndrome.
Frontiers in cardiovascular medicineA rare case of diagnosed absent aortic valve and severely hypoplastic pulmonary valve with double outlet right ventricle: A case report.
HeliyonThe retirement years of Doctor Helen B. Taussig: an intersection of art and medicine.
Cardiology in the youngOutcomes after implantation of right-sided mechanical valve prostheses in congenital heart disease.
Heart (British Cardiac Society)Ten-year follow-up of dilatation of aortic structures in Fallot-type anomalies.
Pediatric cardiologySinus of Valsalva Aneurysm in a Preschooler With Schuurs-Hoeijmakers Syndrome.
Annals of thoracic surgery short reportsRight Aortic Arch with Isolated Left Subclavian Artery in Association with Double Outlet Right Ventricle and Cor Triatriatum Sinister: Hitherto Unreported Association.
The Indian journal of radiology & imagingAssociações
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Neurodevelopmental outcomes in preschool children with congenital heart defects: A case-control study using Ages & Stages Questionnaire.
- Anaesthetic management in a neonate with a double-outlet right ventricle undergoing repair of leaking myelomeningocele.
- Sustained remission of post-Fontan protein-losing enteropathy achieved by combination therapy with high-dose spironolactone and the somatostatin analogue octreotide: a case report.
- Young-onset hepatocellular carcinoma following double outlet right ventricle surgery without liver congestion: a case report with genetic analysis.
- Long-term Outcomes of Standardized Strategy in Arterial Switch Operation: An 18-Year Review in a Single Center.
- Half-turned truncal switch for transposition of the great arteries with left ventricular outflow tract obstruction.
- In vitro construction of handmade polytetrafluoroethylene right ventricle-to-pulmonary artery valved conduit using a modification of the Ozaki technique.
- Aortic root replacement after repaired congenital conotruncal defects: A surgical challenge.
- Ultrasound-Guided Superficial Temporal Artery Cannulation for Proximal Arterial Pressure Monitoring During Coarctation Repair With an Aberrant Right Subclavian Artery in a Low-Birth-Weight Neonate.
- Double-inlet double-outlet right ventricle: a case report and systematic review of the literature with cluster analysis.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:3426(Orphanet)
- MONDO:0018089(MONDO)
- GARD:1908(GARD (NIH))
- Busca completa no PubMed(PubMed)
- Q361648(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
