LAMCAK pilot study: urinary cathepsin K as a potential biomarker in lymphangioleiomyomatosis.

Tuberous sclerosis complex.

A case description: lymphangioleiomyomatosis mimicking ovarian cyst.

A Case Series of Lymphangioleiomyomatosis, a Rare Cystic Lung Disease.

High Prevalence of TSC2 Mutations in Lung Tissue Samples from Patients with Sporadic Lymphangioleiomyomatosis (LAM).

Three cases of whole breast irradiation for breast cancer in patients with Lymphangioleiomyomatosis (LAM).

Uterine PEComa With Lymphangioleiomyomatosis (LAM)-Like Features: A Case Report.

Diagnostic Value of Serum VEGF-D in Lymphangioleiomyomatosis: Results of the First Prospective Study in the Russian Federation.

Cystic lung diseases in the daily routine: a comprehensive step-wise algorithm for the radiological diagnosis of cystic lung lesions and diffuse cystic lung diseases.

Visualization analysis of the use of traditional Chinese medicine in the diagnosis and treatment of rare diseases in mainland China based on CiteSpace.

Choriocarcinoma presenting with cystic lung metastasis mimicking diffuse cystic lung disease.

Educational attainment of individuals with lymphangioleiomyomatosis is a determinant of timely diagnosis and treatment uptake.

Determinants of adherence to sirolimus among lymphangioleiomyomatosis patients.

Tuberous sclerosis complex with multisystem involvement: A case report.

Dual renal pathologies in tuberous sclerosis complex: bilateral renal angiomyolipomas and concurrent left renal cell carcinoma.

Human blood cell traits and sporadic lymphangioleiomyomatosis: results from mediation joint multi-omics and eQTL Mendelian randomization analysis.

CCL14, identified by multi-omics approach, serves as a novel indicator of disease severity and progression in lymphangioleiomyomatosis.

Renal Angiomyolipoma in a Young Woman With Tuberous Sclerosis: A Case Report.

Selective embolization of a renal angiomyolipoma using n-butyl-2-cyanoacrylate‒lipiodol‒iopamidol mixture under microballoon occlusion resulting in tumor reduction and preservation of normal renal blood flow: A case report.

Radiologic Approach to Cystic Lung Diseases: From Cyst Definition to Diagnosis.

Recent advances in understanding the pathogenesis, diagnosis, and treatment of tuberous sclerosis complex (TSC)-associated Lymphangioleiomyomatosis.

Six-minute walk distance predicting the risk of mortality in lymphangioleiomyomatosis patients.

A successful pregnancy in advanced lymphangioleiomyomatosis: A case report and review of pregnancy management in LAM.

[Analysis of the protective effects of low-dose sirolimus on lung function in patients with lymphangioleiomyomatosis].

High-Throughput Proteomics in Lymphangioleiomyomatosis: Premelanosome Protein as a Diagnostic Biomarker, Construction of a Diagnosis Score, and Evidence of Neutrophil Involvement.

Recurrent Pneumothorax Revealing Lymphangioleiomyomatosis in a Young Woman: A Case Report.

Extracellular Matrix Deposition Drives Disease Progression and Reduces Rapamycin Response in LAM.

[Clinicopathological and molecular genetic characteristics of multifocal micronodular pneumocyte hyperplasia (MMPH)].

Rare co-existence of 15q26 deletion syndrome and lymphangioleiomyomatosis: diagnostic and therapeutic challenge.

Curious Coexistence of Perivascula Epitheloid Cell Tumour (PEComa) Systemic Sclerosis-Associated Interstitial Lung Disease and Biopsy-Proven Lymphangioleiomyomatosis in a Middle-Aged Female: A Case Report.

Spontaneous Pneumothorax: A Review of Underlying Etiologies and Diagnostic Imaging Modalities.

Extracellular vesicles modulate integrin signaling and subcellular energetics to promote pulmonary lymphangioleiomyomatosis metastasis.

[A case of diffuse cystic lung disease with severe pulmonary hypertension in a reproductive-aged female].

Robot-assisted laparoscopic resection of giant left renal angiomyolipoma and multiple left retroperitoneal angiomyolipomas: a case report of lymphangioleiomyomatosis.

Prevalence and assessment of exercise-induced desaturation in lymphangioleiomyomatosis.

PEComas of the colon and rectum: a case report of a 15-year-old girl and a review of the pertinent literature.

Nanomedicine for lymphangioleiomyomatosis: toward targeted and durable anti-fibrotic therapy.

GPNMB immunohistochemistry is a useful ancillary tool for the diagnosis of pulmonary lymphangioleiomyomatosis.

[Retroperitoneal lymph node lymphangioleiomyomatosis: tumor with an ambiguous clinical course].

Current Perspectives on The Diagnosis and Management of Lymphangioleiomyomatosis.

mTOR dysregulation induces IL-6 and paracrine AT2 cell senescence impeding lung repair in lymphangioleiomyomatosis.

Direct modulation of TRPM8 ion channels by rapamycin and analog macrolide immunosuppressants.

Beyond the uterus: diagnostic puzzle unravelled as benign metastasising leiomyomatosis with retroperitoneal and pulmonary involvement.

Emerging Concepts in Pathogenesis, Multiomics Applications, and Clinical Research in Lymphangioleiomyomatosis.

Mediastinal lymphangioleiomyomatosis: a case report and literature review.

An Unusual Case of Primary Sjögren's Syndrome and Lymphangioleiomyomatosis Diagnosed From Refractory Cough.

Extrapulmonary lymphangioleiomyomatosis: an incidental finding detected in surgery for gynecological malignancies.

Extracellular Matrix and Fibroblast Activation in Lymphangioleiomyomatosis.

Sporadic lymphangioleiomyomatosis in young female patient: A case report and review of the literature.

Inflammatory, Functional, and Compositional Changes of the Uterine Immune Microenvironment in a Lymphangioleiomyomatosis Mouse Model.

Exploring the uncharted role of cell senescence in rare diseases.

LAM-CAM: In Vivo Model for Rapid Analysis of Lymphangioleiomyomatosis Tumor Formation and Inhibition.

Successful live birth via in vitro fertilization in a patient with lymphangioleiomyomatosis: a case report.

Giant renal angiomyolipoma unmasks underlying lymphangioleiomyomatosis: a case report and literature review.

Mortality in Tuberous sclerosis Complex: Current understandings.

FGFR4 p.Gly388Arg polymorphism in PBMCs of LAM patients: findings of a pilot study.

Novel treatment strategies for lymphangioleiomyomatosis: a narrative review.

Sporadic Lymphangioleiomyomatosis in a 35-Year-Old Female Patient: A Rare Cause of Spontaneous Pneumothorax.

Radiological Manifestations of Lymphangioleiomyomatosis: A Local Patient Cohort Analysis.

A potential new entity pending further validation of pulmonary primary interstitial Tumor: Lymphangioleiomyomatosis-like.

Small extracellular vesicles and induction of epithelial-to-mesenchymal transition in lymphangioleiomyomatosis.

Exhaled Breath Analysis in Lymphangioleiomyomatosis by Real-Time Proton Mass Spectrometry.

Diagnostic Challenges in Lymphangioleiomyomatosis: From Ovarian Mass to Systemic Diagnosis.

Modulation of infiltrating CD206+ macrophages restricts progression of pulmonary lymphangioleiomyomatosis.

Genetic analysis of a novel TSC1 splice mutation causing tuberous sclerosis without neurological phenotypes.

Disease Classification of Pulmonary Xenon Ventilation MRI Using Artificial Intelligence.

Expanding the radiological spectrum of Lymphangioleiomyomatosis: A case with Unique imaging findings.

Neutrophil and neutrophil-lymphocyte ratios as predictors of clinical characteristics in patients with Lymphangioleiomyomatosis.

Sirolimus Use During Pregnancy in Women with Lymphangioleiomyomatosis.

Rare pulmonary diseases and pulmonary hypertension.

Cystic Lung Phantom to Validate Clinical CT Protocols.

Multifocal micronodular pneumocyte hyperplasia and splenic hamartomas in tuberous sclerosis complex: A case report.

Spectrum of Renal Angiomyolipoma with Radiologic-Pathologic Correlation.

Current concepts in the pathogenesis and clinical management of lymphangioleiomyomatosis.

[Evaluation of 18F-fibroblast activation protein inhibitor-42 PET/CT in lymphangioleiomyomatosis and its correlation with vascular endothelial growth factor-D].

Autocrine Transforming Growth Factor-β Signaling Promotes Cell Motility and Chemokine Secretion in an Angiomyolipoma-Derived Cell Model of Lymphangioleiomyomatosis.

Increased malignancy risk in patients with lymphangioleiomyomatosis: findings from a Chinese cohort.

Iron metabolism disorder and artesunate inhibiting tumor growth by inducing ferroptosis in Lymphangioleiomyomatosis.

Pulmonary lymphangioleiomyomatosis (LAM) having no extra-pulmonary manifestations with chemical and mechanical pleurodesis: A case report and review of literature.

Associations of VEGF-D levels with clinical manifestations in lymphangioleiomyomatosis: a cross-sectional analysis of 631 cases.

[Radiology of cysts: Analysis and classification of pulmonary and hepato-pancreatic cysts on imaging].

Inhibition of NAMPT as a therapeutic strategy to suppress tumor growth in lymphangioleiomyomatosis.

[Pulmonary cystic lesions in a young female patient].

PEComa-its clinical features, histopathology, and current therapy.

Mechanisms of exercise limitation and pulmonary rehabilitation in patients with cystic lung diseases.

Real-Time Identification of Lymph Vessels Using Indocyanine Green in a Patient With Chylothorax Associated With Lymphangioleiomyomatosis.

[Lymphangioleiomyomatosis: Update on Pathophysiology, Diagnosis, and Treatment].

A Gain-of-Function Mutation in Mechanistic Target of Rapamycin Results in a Tuberous Sclerosis Complex-Like Manifestation of Parenchymal Lung Disease.

Late living-donor kidney transplantation from the same donor after living-donor lobar lung transplantation.

A challenging convergence of conditions in a patient with thalassemia major presenting with thymoma and lymphangioleiomyomatosis: a case report.

Lung Transplantation Outcomes and Peritransplant Sirolimus Use in Lymphangioleiomyomatosis.

Pediatric reference values of VEGF-D derived from a German population-based cohort of healthy children.

Genetic Mutations and Post-Lung Transplant Complications: A Case of Hereditary Transthyretin Amyloidosis.

Beyond the Graft: Recurrence of Interstitial Lung Diseases Post Transplant.

Illness cognition, illness perception and related factors in patients with lymphangioleiomyomatosis.

Brazilian Thoracic Association recommendations for the management of lymphangioleiomyomatosis.

Prevalence and recurrence rates of spontaneous pneumothorax in patients with diffuse cystic lung diseases in China.

[Incidental diagnosis of lymphangioleiomyomatosis in gynecological surgery-a case series].

Targeting fibroblast-endothelial cell interactions in LAM pathogenesis using 3D spheroid models and spatial transcriptomics.

Synergistic effects of mTOR inhibitors with VEGFR3 inhibitors on the interaction between TSC2-mutated cells and lymphatic endothelial cells.

Lymphangioleiomyomatosis and Pregnancy-Do We Have All the Answers for a Woman Who Desires to Conceive?-Literature Review.

Characteristics and outcomes of patients with LAM receiving sirolimus in France based on real-life data.

Thirty years of lung transplantation: development of postoperative outcome and survival over three decades.

Immature Smooth Muscle Infiltration in Sporadic Lymphangioleiomyomatosis: A Case Study.

A Novel Case of Pulmonary Sclerosing Diffuse PEComatosis With Neuroendocrine Cell Hyperplasia.

Abdominal lymphangioleiomyomatosis in a man presenting with gastrointestinal hemorrhage as the first manifestation: a case report.

Lymphangioleiomyomatosis of the Pelvic Lymph Nodes Detected Incidentally During Surgical Staging of Gynecological Malignancies: Comprehensive Clinicopathological Analysis of 17 Consecutive Cases from a Single Institution.

Tuberous sclerosis: a survey in the canton of Vaud, Switzerland.

STAT1 Promotes PD-L1 Activation and Tumor Growth in Lymphangioleiomyomatosis.

Adrenal PEComa Treated by Surgical Resection and Postoperative Radiotherapy: A Case Report.

Pericardial Effusion as a Presentation of Lymphangioleiomyomatosis.

Tuberous Sclerosis Complex Demonstrated on 18 F-FDG PET/CT.

Primary thymic mucosa-associated lymphoid tissue (MALT) lymphoma with Sjogren's syndrome and diffuse cystic lung disease: a complex respiratory presentation of a multifaceted autoimmune disease.

Unlocking the clinical potential of paired inspiratory and expiratory CT scans in the differential diagnosis of cystic lung diseases: A systematic review.

The development for emerging biomarkers of lymphangioleiomyomatosis.

Evolution of Diffusing Capacity of the Lungs for Carbon Monoxide in Lymphangioleiomyomatosis: Historical Perspectives and the Role of Advanced Imaging.

The Bi-steric Inhibitor RMC-5552 Reduces mTORC1 Signaling and Growth in Lymphangioleiomyomatosis.

Lymphangioleiomyomatosis: A Review.

Enhanced Gαq Signaling in TSC2-Deficient Cells Is Required for Their Neoplastic Behavior.

The challenge of therapeutic options for patients with lymphangioleiomyomatosis.

Nintedanib for patients with lymphangioleiomyomatosis: a phase 2, open-label, single-arm study.

Hereditary Renal Tumor Syndromes and the Use of mTOR Inhibitors.

Repurposing Nitazoxanide for Potential Treatment of Rare Disease Lymphangioleiomyomatosis.

Tuberous sclerosis-associated pulmonary lymphangioleiomyomatosis: The role of pulmonary rehabilitation - A case report.

PEComas: A review of imaging and clinical features.

Quantifying Spatial Distribution of Ventilation Defects in Multiple Pulmonary Diseases With Hyperpolarized 129Xenon MRI.

Successful Treatment of Postmenopausal Exacerbation of Abdominal Lymphangioleiomyomatosis With Sirolimus: A Report of a Rare Case.

Pulmonary Lymphatics History, Anatomy, and Pathophysiology: Emerging Knowledge and a Look to the Future.

Clinical and Functional Outcomes Associated with Quality of Life in Patients with Lymphangioleiomyomatosis: A Cross-Sectional Study.

Surgical Management of Solitary Extrapulmonary Lymphangioleiomyomatosis in the Mesentery: A Case Report.

A case report and review of rheumatoid arthritis co-occurring with tuberous sclerosis complex, a rare occurrence.

Lymphangioleiomyomatosis and its Treatment: When to Start?

Uterine lymphangioleiomyomatosis in a premenopausal woman with tuberous sclerosis: A case report.

Extracellular vesicles regulate metastable phenotypes of lymphangioleiomyomatosis cells via shuttling ATP synthesis to pseudopodia and activation of integrin adhesion complexes.

Diagnostic Accuracy of Computed Tomography in Lymphangioleiomyomatosis.

Management of a rare case of lymphangioleiomyomatosis complicated by recurrent pneumothorax.

Omics research in lymphangioleiomyomatosis: status and challenges.

A Comparison of Clinical and Radiological Presentations of Sporadic and Tuberous Sclerosis Complex-Associated Lymphangioleiomyomatosis.

Surgical management of pleural complications in lymphangioleiomyomatosis.

Diffuse Cystic Lung Disease: A Clinical Guide to Recognition and Management.

Hemoptysis Associated with Sexual Activity in Lymphangioleiomyomatosis.

Spontaneous Hydropneumothorax After Pleurodesis in a Patient With Pulmonary Lymphangioleiomyomatosis With Associated Endometrial Cancer.

Diagnostic value of serum vascular endothelial growth factor-D in Korean patients with lymphangioleiomyomatosis.

Long-term safety and influence on growth in patients receiving sirolimus: a pooled analysis.

Multisystem Lymphangioleiomyomatosis.

[Clinical features of pulmonary hypertension in lymphangioleiomyomatosis].

Clinical Trial Validation of Automated Segmentation and Scoring of Pulmonary Cysts in Thoracic CT Scans.

Unsupervised Exercise in Interstitial Lung Disease: A Delphi Study to Develop a Consensus Preparticipation Screening Tool for Lymphangioleiomyomatosis.

Plasmacytoid Dendritic Cells: Bring a Glimmer of Hope for Patients with Lymphangioleiomyomatosis.

Plasmacytoid Dendritic Cells Mediate CpG-ODN-induced Increase in Survival in a Mouse Model of Lymphangioleiomyomatosis.

Development and internal validation of a clinical risk score to predict incident renal and pulmonary tumours in people with tuberous sclerosis complex.

Improved Diffusion-Weighted Hyperpolarized 129Xe Lung MRI with Patch-Based Higher-Order, Singular Value Decomposition Denoising.

Safety and efficacy of COVID-19 vaccination in the Chinese population with pulmonary lymphangioleiomyomatosis: a single-center retrospective study.

Genetic background of pulmonary (vascular) diseases - how much is written in the codes?

A 20-year-old woman with chronic cough and dyspnea.

Novel developments in the study of estrogen in the pathogenesis and therapeutic intervention of lymphangioleiomyomatosis.

Lung cancer and lymphangioleiomyomatosis: A common complication in an uncommon condition.

Single Lung Transplantation After Open Window Thoracotomy for Empyema: A Case Report.

Stepwise Incremental Dose Schedule of Sirolimus Is Successfully Tolerated by a Patient With Lymphangioleiomyomatosis Who Was Initially Allergic to mTOR Inhibitors.

Hepatic perivascular epithelioid cell tumors: Benign, malignant, and uncertain malignant potential.

A Study on the Psychological Profile and Coping With the Disease in Patients With Lymphangioleiomyomatosis.

Effect of mTOR inhibitors on the mortality and safety of patients with lymphangioleiomyomatosis on the lung transplantation waitlist: A retrospective cohort study.

Giant Renal Angiomyolipomas and Pulmonary Lymphangioleiomyomatosis: Follow-up Report after More than a Decade.

Giant Retinal Astrocytoma: A Case Report of an Uncommon Presentation of Tuberous Sclerosis in a Young Female.

Native lung surgery after single lung transplantation: clinical characteristics and outcomes.

[Diffuse cystic lung disease].

Lymphangioleiomyomatosis as a potent lung cancer risk factor: Insights from a Japanese large cohort study.

A Case Report of Malignant Perivascular Epithelioid Cell Tumors of the Uterus and Literature Review.

Glycoprotein non-metastatic melanoma protein B promotes tumor growth and is a biomarker for lymphangioleiomyomatosis.

Case report: Response to everolimus in a patient with platinum resistant, high grade serous ovarian carcinoma with biallelic TSC2 inactivation.

Lymphangioleiomyomatosis: Rapidly Progressive Retroperitoneal Cystic Tumor Mimicking Malignancy.

A 24-year-Old woman with recurrent pneumothoraces.

Tuberous sclerosis complex associated lymphangioleiomyomatosis caused by de novo mutation of TSC2 gene in Vietnam: A case report.

Lymphangioleiomyomatosis and pregnancy: a mini-review.

Epidemiology of patients with lymphangioleiomyomatosis: A descriptive study using the national database of health insurance claims and specific health checkups of Japan.

An Uncommon Presentation of Renal Angiomyolipoma: A Case Report.

An elderly woman with Birt-Hogg-Dubé syndrome having multiple pulmonary cysts mimicking lymphangioleiomyomatosis.

[Lymphangioleiomyomatosis].

Perivascular Epithelioid Cell-Family Tumors in Children, Adolescents, and Young Adults: Clinicopathologic Features in 70 Cases.

Desquamative interstitial pneumonia: A case report.

Lymphangioleiomyomatosis in patients with tuberous sclerosis: a national centre audit.

Intraoperative mechanical ventilation and incidence of pneumothorax in lymphangioleiomyomatosis.

Increasing the scan-efficiency of pulmonary imaging at 0.55 T using iterative concomitant field and motion-corrected reconstruction.

Bayesian two-stage modeling of longitudinal and time-to-event data with an integrated fractional Brownian motion covariance structure.

Clinical, tomographic and functional comparison of sporadic and tuberous sclerosis complex-associated forms of lymphangioleiomyomatosis: a retrospective cohort study.

Case report: If it is not asthma-think of lymphangioleiomyomatosis in younger female patients.

An unusual case of metastatic trophoblastic neoplasm presenting with diffuse cystic lung disease and pulmonary artery pseudoaneurysms in a teenager.

Ultra-low dose chest CT with silver filter and deep learning reconstruction significantly reduces radiation dose and retains quantitative information in the investigation and monitoring of lymphangioleiomyomatosis (LAM).

A chylothorax in a young woman: The difficulties of medical management.

Complications of lymphangioleiomyomatosis in pregnancy: a case report and review of the literature.

Identification of Lymphangioleiomyomatosis-associated Serum MicroRNAs.

Soft Tissue Perivascular Epithelioid Cell Tumors.

The role of moesin in diagnosing and assessing severity of lymphangioleiomyomatosis.

Case of the Month from the Peter MacCallum Cancer Centre, Melbourne, Australia: an operative approach to large renal angiomyolipoma associated with lymphangioleiomyomatosis.

TFEB drives mTORC1 hyperactivation and kidney disease in Tuberous Sclerosis Complex.

Small airways morphological alterations associated with functional impairment in lymphangioleiomyomatosis.

Lymphangioleiomyomatosis: No Longer Ultra-rare.

A case report of lymphangioleiomyomatosis with retroperitoneal masses in pregnancy.