Classe de doenças pulmonares difusas que normalmente afetam o interstício pulmonar, embora algumas também tenham um componente que afeta as vias aéreas (por exemplo, pneumonite em organização criptogênica).
Introdução
O que você precisa saber de cara
Classe de doenças pulmonares difusas que normalmente afetam o interstício pulmonar, embora algumas também tenham um componente que afeta as vias aéreas (por exemplo, pneumonite em organização criptogênica).
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Entender a doença
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Preparando trilha educativa...
Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Partes do corpo afetadas
+ 41 sintomas em outras categorias
Características mais comuns
Os sintomas variam de pessoa para pessoa. Abaixo estão as 97 características clínicas mais associadas, ordenadas por frequência.
Linha do tempo da pesquisa
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Genética e causas
O que está alterado no DNA e como passa nas famílias
Genes associados
14 genes identificados com associação a esta condição.
Pulmonary surfactant associated proteins promote alveolar stability by lowering the surface tension at the air-liquid interface in the peripheral air spaces
Secreted, extracellular space, surface film
Pulmonary surfactant metabolism dysfunction 2
A rare disease associated with progressive respiratory insufficiency and lung disease with a variable clinical course, due to impaired surfactant homeostasis. It is characterized by alveolar filling with floccular material that stains positive using the periodic acid-Schiff method and is derived from surfactant phospholipids and protein components. Excessive lipoproteins accumulation in the alveoli results in severe respiratory distress.
Telomerase is a ribonucleoprotein enzyme essential for the replication of chromosome termini in most eukaryotes. Active in progenitor and cancer cells. Inactive, or very low activity, in normal somatic cells. Catalytic component of the teleromerase holoenzyme complex whose main activity is the elongation of telomeres by acting as a reverse transcriptase that adds simple sequence repeats to chromosome ends by copying a template sequence within the RNA component of the enzyme. Catalyzes the RNA-de
Nucleus, nucleolusNucleus, nucleoplasmNucleusChromosome, telomereCytoplasmNucleus, PML body
3'-exoribonuclease that has a preference for poly(A) tails of mRNAs, thereby efficiently degrading poly(A) tails. Exonucleolytic degradation of the poly(A) tail is often the first step in the decay of eukaryotic mRNAs and is also used to silence certain maternal mRNAs translationally during oocyte maturation and early embryonic development. Interacts with both the 3'-end poly(A) tail and the 5'-end cap structure during degradation, the interaction with the cap structure being required for an eff
NucleusCytoplasmNucleus, nucleolus
Dyskeratosis congenita, autosomal recessive, 6
A form of dyskeratosis congenita, a rare multisystem disorder caused by defective telomere maintenance. It is characterized by progressive bone marrow failure, and the clinical triad of reticulated skin hyperpigmentation, nail dystrophy, and mucosal leukoplakia. Common but variable features include premature graying, aplastic anemia, low platelets, osteoporosis, pulmonary fibrosis, and liver fibrosis among others. Early mortality is often associated with bone marrow failure, infections, fatal pulmonary complications, or malignancy.
Dipeptidyl peptidase that cleaves off N-terminal dipeptides from proteins having a Pro or Ala residue at position 2 (PubMed:12662155, PubMed:16475979, PubMed:19667070, PubMed:29382749, PubMed:30291141, PubMed:33731929, PubMed:36112693). Acts as a key inhibitor of caspase-1-dependent monocyte and macrophage pyroptosis in resting cells by preventing activation of NLRP1 and CARD8 (PubMed:27820798, PubMed:29967349, PubMed:30291141, PubMed:31525884, PubMed:32796818, PubMed:36112693, PubMed:36357533).
Cytoplasm, cytosolNucleus
Hatipoglu immunodeficiency syndrome
An autosomal recessive immunologic disorder manifesting in infancy or early childhood, and characterized by failure to thrive, short stature, skin pigmentation abnormalities, pancytopenia, and susceptibility to recurrent infections.
In presence of calcium ions, it binds to surfactant phospholipids and contributes to lower the surface tension at the air-liquid interface in the alveoli of the mammalian lung and is essential for normal respiration
SecretedSecreted, extracellular space, extracellular matrixSecreted, extracellular space, surface film
Interstitial lung disease 2
A form of interstitial lung disease, a heterogeneous group of diseases affecting the distal part of the lung and characterized by a progressive remodeling of the alveolar interstitium. The disease spectrum ranges from idiopathic interstitial pneumonia or pneumonitis to idiopathic pulmonary fibrosis, that is associated with an increased risk of developing lung cancer. Clinical features of interstitial lung disease include dyspnea, clubbing of the fingers, and restrictive lung capacity. ILD2 inheritance is autosomal dominant.
Gel-forming mucin that is thought to contribute to the lubricating and viscoelastic properties of whole saliva and cervical mucus
Secreted
Interstitial lung disease 2
A form of interstitial lung disease, a heterogeneous group of diseases affecting the distal part of the lung and characterized by a progressive remodeling of the alveolar interstitium. The disease spectrum ranges from idiopathic interstitial pneumonia or pneumonitis to idiopathic pulmonary fibrosis, that is associated with an increased risk of developing lung cancer. Clinical features of interstitial lung disease include dyspnea, clubbing of the fingers, and restrictive lung capacity. ILD2 inheritance is autosomal dominant.
A component of desmosome cell-cell junctions which are required for positive regulation of cellular adhesion (PubMed:25733715). Critical for cell-cell adhesion in early stage blastocysts and progression through proamniotic cavity formation (By similarity). Not required for preimplantation morphogenic process in blastocysts (By similarity). Required for keratin filament anchoring at the desmosome junction and subsequent organization of the keratin intermediate filament network within the cytoplas
Cell projection, axonCell junction, desmosomeCell membraneCytoplasmNucleus
Keratoderma, palmoplantar, striate 2
A dermatological disorder characterized by thickening of the skin on the palms (linear pattern) and the soles (island-like pattern) and flexor aspect of the fingers. Abnormalities of the nails, the teeth and the hair are rarely present.
In presence of calcium ions, it binds to surfactant phospholipids and contributes to lower the surface tension at the air-liquid interface in the alveoli of the mammalian lung and is essential for normal respiration. Enhances the expression of MYO18A/SP-R210 on alveolar macrophages (By similarity) (Microbial infection) Recognition of M.tuberculosis by dendritic cells may occur partially via this molecule (PubMed:17158455, PubMed:21203928). Can recognize, bind, and opsonize pathogens to enhance t
SecretedSecreted, extracellular space, extracellular matrixSecreted, extracellular space, surface film
Interstitial lung disease 1
A form of interstitial lung disease, a heterogeneous group of diseases affecting the distal part of the lung and characterized by a progressive remodeling of the alveolar interstitium. The disease spectrum ranges from idiopathic interstitial pneumonia or pneumonitis to idiopathic pulmonary fibrosis, that is associated with an increased risk of developing lung cancer. Clinical features of interstitial lung disease include dyspnea, clubbing of the fingers, and restrictive lung capacity. ILD1 inheritance can be autosomal dominant with incomplete penetrance, and autosomal recessive.
Component of the CST complex proposed to act as a specialized replication factor promoting DNA replication under conditions of replication stress or natural replication barriers such as the telomere duplex. The CST complex binds single-stranded DNA with high affinity in a sequence-independent manner, while isolated subunits bind DNA with low affinity by themselves. Initially the CST complex has been proposed to protect telomeres from DNA degradation (PubMed:19854130). However, the CST complex ha
NucleusChromosome, telomere
Cerebroretinal microangiopathy with calcifications and cysts 2
An autosomal recessive, multisystemic disorder characterized by intrauterine growth retardation and, later in life, premature aging symptoms, including poor growth, graying hair, liver fibrosis, portal hypertension, esophageal varices, osteopenia, pancytopenia, hypocellular bone marrow, and vascular telangiectasia resulting in gastrointestinal bleeding. Brain calcifications and white matter changes are responsible for signs including spasticity, ataxia, or dystonia observed in some patients.
Catalyzes the ATP-dependent transport of phospholipids such as phosphatidylcholine and phosphoglycerol from the cytoplasm into the lumen side of lamellar bodies, in turn participates in the lamellar bodies biogenesis and homeostasis of pulmonary surfactant (PubMed:16959783, PubMed:17574245, PubMed:27177387, PubMed:28887056, PubMed:31473345). Transports preferentially phosphatidylcholine containing short acyl chains (PubMed:27177387). In addition plays a role as an efflux transporter of miltefosi
Endosome, multivesicular body membraneCytoplasmic vesicle membraneLate endosome membraneLysosome membrane
Pulmonary surfactant metabolism dysfunction 3
A rare lung disorder due to impaired surfactant homeostasis. It is characterized by alveolar filling with floccular material that stains positive using the periodic acid-Schiff method and is derived from surfactant phospholipids and protein components. Excessive lipoproteins accumulation in the alveoli results in severe respiratory distress.
A probable ATP-dependent DNA helicase implicated in telomere-length regulation, DNA repair and the maintenance of genomic stability. Acts as an anti-recombinase to counteract toxic recombination and limit crossover during meiosis. Regulates meiotic recombination and crossover homeostasis by physically dissociating strand invasion events and thereby promotes noncrossover repair by meiotic synthesis dependent strand annealing (SDSA) as well as disassembly of D loop recombination intermediates. Als
Nucleus
Dyskeratosis congenita, autosomal recessive, 5
A form of dyskeratosis congenita, a rare multisystem disorder caused by defective telomere maintenance. It is characterized by progressive bone marrow failure, and the clinical triad of reticulated skin hyperpigmentation, nail dystrophy, and mucosal leukoplakia. Common but variable features include premature graying, aplastic anemia, low platelets, osteoporosis, pulmonary fibrosis, and liver fibrosis among others. Early mortality is often associated with bone marrow failure, infections, fatal pulmonary complications, or malignancy. DKCB5 is characterized by onset of bone marrow failure and immunodeficiency in early childhood. Most patients also have growth and developmental delay and cerebellar hypoplasia, consistent with a clinical diagnosis of Hoyeraal-Hreidarsson syndrome.
Catalytic component of a P4-ATPase flippase complex which catalyzes the hydrolysis of ATP coupled to the transport of aminophospholipids, phosphatidylserines (PS) and phosphatidylethanolamines (PE), from the outer to the inner leaflet of the plasma membrane (PubMed:25315773, PubMed:25947375, PubMed:26567335, PubMed:29799007, PubMed:30018401, PubMed:36300302). Does not show flippase activity toward phosphatidylcholine (PC) (PubMed:34403372). Contributes to the maintenance of membrane lipid asymme
Cell membraneEarly endosomeRecycling endosomeEndoplasmic reticulum membrane
Deafness, autosomal dominant, 84
A form of non-syndromic, sensorineural hearing loss. Sensorineural hearing loss results from damage to the neural receptors of the inner ear, the nerve pathways to the brain, or the area of the brain that receives sound information. DFNA84 is characterized by slowly progressive, postlingual hearing loss.
Medicamentos aprovados (FDA)
1 medicamento encontrado nos registros da FDA americana.
Variantes genéticas (ClinVar)
832 variantes patogênicas registradas no ClinVar.
Vias biológicas (Reactome)
38 vias biológicas associadas aos genes desta condição.
Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
Remédios, cuidados de apoio e o que precisa acompanhar
Onde tratar no SUS
Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)
🇧🇷 Atendimento SUS — Pneumonia intersticial idiopática
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Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.
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Outros ensaios clínicos
31 ensaios clínicos encontrados, 5 ativos.
Publicações mais relevantes
Isolated antineutrophil cytoplasmic antibody-associated interstitial lung disease: A systematic review of an emerging condition.
To summarise the clinical characteristics, radiological and histopathological features, treatment approaches, and outcomes of isolated antineutrophil cytoplasmic antibody-associated interstitial lung disease (ANCA-ILD). A systematic literature review conducted according to the PRISMA statement. Twenty-four studies comprising 794 patients were included. Isolated ANCA-ILD predominantly affected older adults, between 50 and 70 years of age, with a slight male predominance (57%). MPO-ANCA positivity was observed in approximately 70% of patients, whereas PR3-ANCA positivity accounted for 10-15%. Fibrotic patterns predominated, with usual interstitial pneumonia (UIP) or UIP-like changes reported in 45-65% of cases, followed by NSIP in 15-30%. Glucocorticoids were prescribed in 58% of patients, immunosuppressive therapies in 31%, and antifibrotic treatment in approximately 26% of those reported in more recent cohorts. Functional decline occurred in approximately 30-50% of patients, and radiological progression in 30-45%. Acute exacerbations were reported in 19-25%, and up to 40% fulfilled criteria for progressive pulmonary fibrosis during follow-up. Progression to systemic ANCA-associated vasculitis (AAV) occurred in approximately 10-40% of cases, with timing ranging from the first year to several years later. This evolution occurred mainly toward microscopic polyangiitis (MPA), whereas granulomatosis with polyangiitis was infrequent, representing ≤10-20% of cases. Survival was generally comparable to ANCA-negative idiopathic interstitial pneumonia and AAV-ILD. Isolated ANCA-ILD is an emerging, increasingly recognised fibrotic interstitial lung disease phenotype characterised by frequent MPO-ANCA positivity and two partly independent trajectories: (1) an IPF-like fibrotic course and (2) progression to systemic AAV, most commonly MPA.
Nocturnal hypercapnia in the patients with idiopathic interstitial pneumonia registered for lung transplantation.
Respiratory failure in idiopathic interstitial pneumonia (IIP) is mainly non-hypercapnic hypoxia, although hypercapnia also occurs in advanced stages. Although sleep-disordered breathing in IIPs is drawing attention, the role of nocturnal hypercapnia remains largely unknown. In this study, we aimed to clarify whether nocturnal hypercapnia in patients with advanced IIPs is associated with the clinical characteristics. We retrospectively analyzed 41 patients with IIPs who underwent nocturnal transcutaneous carbon dioxide partial pressure (PtcCO2) monitoring during the evaluation for lung transplantation eligibility. Nocturnal hypercapnia was diagnosed according to the American Academy of Sleep Medicine criteria. Associations between nocturnal hypercapnia and clinical features including comorbidities such as PH, radiographic features, and pulmonary function tests were assessed. Fourteen patients (34.1%) met the criteria for nocturnal hypercapnia, exhibiting decreased normal lung volume and frequent use of long-term oxygen therapy (LTOT) during sleep. Lower percent predicted vital capacity (%VC) correlated with mean PtcCO2 and PtcCO2>55 mmHg time during sleep. Nocturnal hypercapnia was significantly associated with increased PH complications, higher pulmonary vascular resistance (PVR), and higher mean pulmonary artery pressure (P = 0.010, P = 0.023, and P = 0.045, respectively). Pleuroparenchymal fibroelastosis-like CT features were associated with daytime hypercapnia; however, the frequency of nocturnal hypercapnia among these patients was not significantly higher compared with other patients. Nocturnal hypercapnia is prevalent in advanced IIPs and is linked to reduced normal lung volume, LTOT during sleep, and low %VC. PH was observed more frequently in these patients. Further studies should elucidate the therapeutic potential of nocturnal hypercapnia in IIPs.
Impact of flat chest on waitlist mortality in adult patients with pleuroparenchymal fibroelastosis listed for lung transplantation.
Pleuroparenchymal fibroelastosis (PPFE) is a distinct subtype of idiopathic interstitial pneumonia, and progressive cases require lung transplantation (LT). Some patients with PPFE develop chest flattening; however, its impact on waitlist mortality for LT remains unclear. We retrospectively analyzed adult patients with PPFE listed for LT from donation after brain death (DBD) between January 2014 and July 2024. Chest flatness was quantified as the ratio of the anteroposterior diameter of the thoracic cage to its transverse diameter (APDT/TDT). An APDT/TDT cut-off for waitlist mortality was determined by receiver operating characteristic curve analysis. The primary objective was to investigate the prognostic significance of APDT/TDT on waitlist mortality. Among 36 listed patients, 19 (52.8%) underwent LT, 14 (38.9%) died while awaiting LT, and 3 (8.3%) remained on the waitlist. Patients were classified into high and low APDT/TDT groups: 11 (30.6%) and 25 (69.4%), respectively. The low APDT/TDT group demonstrated shorter 6-minute walk distance (6MWD; P = 0.002), lower percentage forced vital capacity (P = 0.015), and higher pCO2 (P = 0.035). Waitlist survival was shorter in the low APDT/TDT group than in the high group (P = 0.010). Univariate analyses identified low APDT/TDT (P = 0.033), smoking history (P = 0.012), and 6MWD < 400 m (P = 0.007) as risk factors for waitlist mortality. The APDT /TDT, an index of a flat chest, may serve as a prognostic factor for waitlist mortality in patients with PPFE awaiting LT. Acute interstitial pneumonia (AIP, also known as Hamman–Rich syndrome) is an acute, rapidly progressive idiopathic pulmonary disease that often leads to fulminant respiratory failure and acute respiratory distress syndrome (ARDS). AIP can be distinguished clinically from other types of interstitial pneumonia by the rapid onset of respiratory failure in a patient without preexisting lung disease. Louis Hamman and Arnold Rich first described AIP in 1935 as a fulminating diffuse interstitial fibrosis of the lungs. In 1986, Katzenstein introduced the term AIP, differentiating it from the group of chronic interstitial pneumonias. The American Thoracic Society and European Respiratory Society classify AIP as a major idiopathic interstitial pneumonia, compared with other rare or unclassified idiopathic interstitial pneumonias.
Postoperative pleurodesis using OK-432 for pulmonary air leak in lung cancer patients with idiopathic interstitial pneumonia: A retrospective study.
To evaluate the efficacy and safety of postoperative pleurodesis using OK-432, focusing on patients with idiopathic interstitial pneumonia (IIP). This retrospective cohort study included patients who underwent OK-432 pleurodesis following pulmonary resection. We reviewed clinical characteristics, radiological evidence of IIP, operative findings, postoperative air leak volume, pleurodesis details, morbidity, and mortality; then we compared the outcomes of patients with vs. those without IIP, and analyzed the predictors of ≥Grade II complications. Pleurodesis was performed in 361 patients, including 67 (19%) with IIP. No significant differences were observed in the incidence of fever or in postpleurodesis parameters. The initial success rate was 58.2% for IIP patients and 70.4% for non-IIP patients. Recurrence developed in 7.5% of patients and surgical intervention was required in 4.1%. Risk factors for ≥Grade II complications included older age, IIP, pleurodesis within 3 postoperative days (PODs), and pre-pleurodesis WBC > 7000/µL. Pneumonia after pleurodesis was more frequent in the IIP patients (11.9% vs. 2.4%, p < 0.01). There were no treatment-related deaths following OK-432 pleurodesis in IIP patients; however, IIP remained a significant risk factor for pleurodesis-related complications, particularly pneumonia. Early intervention and elevated WBC levels may increase the complication risk. Delaying pleurodesis until the WBC count normalizes is advisable to reduce adverse events.
Upfront combination therapy with nintedanib and anti-inflammatory agents for progressive pulmonary fibrosis: a multicentre, single-arm phase 2 study (TOP-ILD).
Progressive pulmonary fibrosis (PPF) is a chronic interstitial lung disease (ILD) characterised by fibrotic progression and poor prognosis, with effective treatment strategies for previously untreated patients remaining unclear. This study evaluated the efficacy and safety of upfront combination therapy with anti-inflammatory and antifibrotic agents in previously untreated PPF patients. This multicentre, single-arm phase 2 study enrolled 34 patients with ILD (including unclassifiable idiopathic interstitial pneumonia, idiopathic nonspecific interstitial pneumonia, fibrotic hypersensitivity pneumonitis and rheumatoid arthritis-associated ILD) all with evidence of PPF. Tacrolimus (0.0375 mg·kg-1 twice daily) and prednisolone (10 mg once daily) were initiated on day 1, with nintedanib (150 mg twice daily) added on day 8. The tacrolimus dosage was adjusted to maintain blood trough levels. The primary end-point was the change in the relative decline slope for forced vital capacity % predicted (%FVC) between before and after treatment. The protocol treatment was associated with a substantial improvement in the relative %FVC decline slope, from -20.9% per year before to +11.2% per year after treatment. Subgroup analysis revealed greater improvement in patients with an increased lymphocyte percentage in bronchoalveolar lavage fluid or elevated blood biomarkers. Adverse events, such as diarrhoea (67.6%) and hepatic dysfunction (29.4%), were manageable, with no severe cases or treatment discontinuations. Early combination therapy with tacrolimus, prednisolone and nintedanib was associated with improved pulmonary function and was well tolerated in previously untreated PPF patients. Our findings suggest the potential of this regimen as an initial treatment strategy, but further validation in larger randomised controlled trials is warranted.
Publicações recentes
Prognostic impact of thyroid transcription factor-1 expression and the efficacy of carboplatin plus (nab-) paclitaxel in non-squamous non-small cell lung cancer complicated with idiopathic interstitial pneumonias.
Subset binding enables detection of multimodal patient subgroup patterns and drug target discovery in idiopathic pulmonary fibrosis.
The role of S100A8/A9 in the pathogenesis of acute exacerbations of pulmonary fibrosis.
Clinical spectrum and profile of interstitial lung disease: an ambispective study from a tertiary center in North India.
Risk Factors for Pneumonitis in Patients with Unresectable Advanced Non-small Cell Lung Cancer Treated with Immune Checkpoint Inhibitors.
📚 EuropePMC369 artigos no totalmostrando 198
Isolated antineutrophil cytoplasmic antibody-associated interstitial lung disease: A systematic review of an emerging condition.
Autoimmunity reviewsNocturnal hypercapnia in the patients with idiopathic interstitial pneumonia registered for lung transplantation.
Respiratory investigationImpact of flat chest on waitlist mortality in adult patients with pleuroparenchymal fibroelastosis listed for lung transplantation.
JHLT openPostoperative pleurodesis using OK-432 for pulmonary air leak in lung cancer patients with idiopathic interstitial pneumonia: A retrospective study.
Surgery todayUpfront combination therapy with nintedanib and anti-inflammatory agents for progressive pulmonary fibrosis: a multicentre, single-arm phase 2 study (TOP-ILD).
ERJ open researchSex-specific phenotypes and outcomes in non‑IPF interstitial lung disease: results from the INSIGHTS‑ILD registry.
Respiration; international review of thoracic diseasesSignificance of clinical parameters and biomarkers to predict nintedanib-induced diarrhea: an interview-based retrospective study.
Journal of thoracic diseaseInterstitial pneumonia with autoimmune features: A literature review.
Respiratory medicineOutcomes and Toxicity of Stereotactic Radiotherapy in Non-small Cell Lung Cancer Patients With Interstitial Lung Disease: A Multicentre Cohort Study.
CureusCXCL2-TLR4 axis activates NETs by accelerating autophagy through ATG7 to promote the progression of idiopathic interstitial pneumonia.
Molecular immunologyOscillometrically assessed higher respiratory reactance is associated with impaired lung function and poorer prognosis in patients with fibrotic idiopathic interstitial pneumonias.
Respiratory investigationEfficacy and safety of immune checkpoint inhibitors in advanced non-small cell lung cancer with idiopathic interstitial pneumonia or interstitial lung abnormalities: NJLCG2301.
Translational lung cancer researchThe Lung Mycobiome in Idiopathic Interstitial Pneumonia, Collagen Tissue Disease-related Interstitial Lung Disease, and Sarcoidosis.
Medical mycology journalSurgical outcomes of lung cancer associated with autoimmune disease-related interstitial pneumonia.
General thoracic and cardiovascular surgeryBroadening Our Understanding of Genetic Risk to Interstitial Lung Disease in Understudied Populations.
Respirology (Carlton, Vic.)Waiting List Mortality and Potential Risk Factors in Lung Transplant Candidates: A Single-Center Data.
Transplantation proceedingsPrognostic impact of muscle mass in idiopathic interstitial pneumonia: analysis of idiopathic pulmonary fibrosis and other idiopathic interstitial pneumonias.
BMC pulmonary medicineRisk stratification of acute exacerbations by autoantibodies in patients with idiopathic interstitial pneumonia.
Scientific reportsPrognostic comparison of acute exacerbations across idiopathic interstitial pneumonia subtypes: A nationwide observational study.
Respiratory investigationOnline home spirometry in national pulmonary fibrosis care: insights from daily practice.
ERJ open researchCryptogenic Organizing Pneumonia.
Seminars in respiratory and critical care medicineNative lung aspergilloma after single lung transplantation-a case series.
Journal of thoracic diseasePatterns of Idiopathic Interstitial Pneumonia and Their Correlation With Spirometry Findings: A Study at Tikur Anbessa Specialized Hospital, Addis Ababa, Ethiopia.
Radiology research and practicePathophysiological Insights and Clinical Management Strategies for Interstitial Lung Diseases.
Biomolecules & therapeuticsDevelopment of an enzyme-linked immunosorbent assay for the efficient detection of autoantibodies against nuclear valosin-containing protein-like protein (NVL) 2 using its manipulated cDNA.
RMD openUpdate of the international multidisciplinary classification of the interstitial pneumonias: an ERS/ATS statement.
The European respiratory journalHemodynamics and Phosphodiesterase-5 Inhibitor Treatment Associated with Survival in Pulmonary Hypertension in Interstitial Lung Disease: A PVRI GoDeep Meta-Registry Analysis.
American journal of respiratory and critical care medicineAnalysis of the relationship between bronchoalveolar lavage lymphocyte fraction and detailed autoimmune features in patients with idiopathic interstitial pneumonia.
Scientific reportsAlveolar Sarcoidosis Mimicking Idiopathic Interstitial Pneumonia Without Mediastinal Lymphadenopathy.
Respirology case reportsInterstitial lung disease biomarkers: a systematic review and meta-analysis.
Clinica chimica acta; international journal of clinical chemistryCOVID-19 outcomes in hospitalized patients with underlying connective tissue disease-related interstitial lung disease vs. idiopathic interstitial pneumonia: a nationwide analysis 2019-2020.
ARP rheumatologyBidirectional Mendelian Randomization Study: Unraveling the Link Between Idiopathic Pulmonary Fibrosis and Cardiovascular Disease.
Annals of human geneticsPhase II study of carboplatin + weekly paclitaxel for advanced lung squamous cell carcinoma with idiopathic interstitial pneumonia (Hanshin Cancer Group IP001).
Medical oncology (Northwood, London, England)Prognosis and prognostic factors for chronic fibrosing idiopathic interstitial pneumonias.
Respiratory investigation[Target organ the lungs: diversity of fibrotic pulmonary diseases].
Innere Medizin (Heidelberg, Germany)A Case of Synovitis Acne Pustulosis Hyperostosis Osteitis (SAPHO) Syndrome With Myeloperoxidase Anti-neutrophil Cytoplasmic Antibody: Exploring an Association or Coincidence.
CureusEvaluation and management of rheumatoid arthritis-associated interstitial lung disease.
Respiratory investigationKorean Guidelines for Diagnosis and Management of Interstitial Lung Diseases.
Tuberculosis and respiratory diseasesClinical significance of anti-neutrophil cytoplasmic antibody in idiopathic interstitial pneumonia: a retrospective observational study.
BMC pulmonary medicineThe role of lung cancer in mortality rate in chronic fibrosing idiopathic interstitial pneumonia.
Scientific reportsAdvances in Concept and Imaging of Interstitial Lung Disease.
RadiologyRheumatoid arthritis development and survival in idiopathic interstitial pneumonia patients with anti-citrullinated protein antibodies.
Respiratory investigationCharacteristics, clinical findings, and treatment of idiopathic pulmonary fibrosis in Japanese patients registered with a medical subsidy system for intractable diseases.
Respiratory investigationAnti-annexin A4 antibody as a biomarker for desquamative interstitial pneumonia.
Journal of autoimmunityEvaluation of Autoimmune Features in Patients with Idiopathic Pulmonary Fibrosis and Pathologic Usual Interstitial Pneumonia: Implications for CT Patterns and Prognosis.
RadiologyAnti-neutrophil cytoplasmic antibodies associated interstitial pneumonia: A possible new clinical entity.
European journal of clinical investigationPrognostic prediction for newly diagnosed patients with idiopathic interstitial pneumonia: JIPS Registry (NEJ030).
Respiratory investigationEvaluating the efficacy of ethanolic extract of Tapak Liman (Elephantopus scaber L.) leaf in inhibiting pulmonary fibrosis: Mechanisms through anti-fibrotic cytokine promotion.
Open veterinary journalPleuroparenchymal Fibroelastosis: Update on CT and Histologic Findings.
Radiology. Cardiothoracic imagingComparison of interstitial lung disease diagnoses in urban and rural areas among participants in the pulmonary fibrosis foundation patient registry.
HeliyonCough monitoring systems in adults with chronic respiratory diseases: a systematic review.
European respiratory review : an official journal of the European Respiratory SocietyIdiopathic pulmonary fibrosis in the UK: findings from the British Thoracic Society UK Idiopathic Pulmonary Fibrosis Registry.
BMJ open respiratory researchAutomatic quantitative evaluation of high-resolution computed tomography scans of patients with interstitial lung diseases.
European journal of radiologyPrevalence and clinical features of progressive pulmonary fibrosis in patients with unclassifiable idiopathic interstitial pneumonia: A post hoc analysis of prospective multicenter registry.
Respiratory investigationEvaluating the Diagnostic Value of Lymphocyte Subsets in Bronchoalveolar Lavage Fluid and Peripheral Blood Across Various Diffuse Interstitial Lung Disease Subtypes.
BiomoleculesCarboplatin in combination with etoposide for advanced small cell lung cancer complicated with idiopathic interstitial pneumonia: a single-arm phase II study.
BMC pulmonary medicineAssociation between the HAL score and the development of progressive pulmonary fibrosis in idiopathic interstitial pneumonia: A prospective observational study.
Respiratory investigationIdiopathic pleuroparenchymal fibroelastosis: A review of the previous literature and current knowledge.
Respiratory investigationGut microbiota profiles of patients with idiopathic pulmonary fibrosis.
Experimental lung researchIntegrative Genomic and Transcriptomic Analysis in Acute Interstitial Pneumonia.
Journal of cellular and molecular medicineImmunological characteristics of bronchoalveolar lavage fluid and blood across connective tissue disease-associated interstitial lung diseases.
Frontiers in immunologyPulmonary wedge resection for lung cancer developing in a single transplanted lung: a case report.
General thoracic and cardiovascular surgery casesRecipient selection for lung transplantation: perspective in decision-making.
Postgraduate medical journalPrognostic value of myositis-specific antibodies in patients with idiopathic interstitial pneumonia.
BMC pulmonary medicineOpioids for the palliation of symptoms in people with serious respiratory illness: a systematic review and meta-analysis.
European respiratory review : an official journal of the European Respiratory SocietyAnti-interferon gamma-inducible protein 16 antibodies: Identification of a novel autoantigen in idiopathic interstitial pneumonia and its clinical characteristics based on a multicenter cohort study.
Clinical immunology (Orlando, Fla.)Objective measurement of cough in pulmonary fibrosis: a cohort study - ImpaCT.
ERJ open researchCXCL10 predicts autoimmune features and a favorable clinical course in patients with IIP: post hoc analysis of a prospective and multicenter cohort study.
Respiratory researchDurvalumab with etoposide and carboplatin for patients with extensive-stage small cell lung cancer and interstitial lung disease: A multicenter, open-label prospective trial.
Lung cancer (Amsterdam, Netherlands)Phase II study of carboplatin plus weekly paclitaxel with bevacizumab for non-squamous, non-small cell lung cancer with idiopathic interstitial pneumonia (Hanshin Cancer Group IP002).
Japanese journal of clinical oncologyClinical manifestations, treatment and prognosis of juvenile idiopathic arthritis with pulmonary involvement in China: a single centre study.
Clinical and experimental rheumatologyPost-lung transplant outcomes of connective tissue disease-related interstitial lung diseases compared with idiopathic interstitial pneumonia: a single-center experience in Japan.
General thoracic and cardiovascular surgeryReevaluating diagnosis in interstitial lung disease with a second multidisciplinary discussion.
Respiratory investigationUse of artificial intelligence algorithms to analyse systemic sclerosis-interstitial lung disease imaging features.
Rheumatology internationalThe burden of cough in idiopathic pulmonary fibrosis and other interstitial lung diseases: a systematic evidence synthesis.
Respiratory researchSignificance of Systemic Scleroderma-Specific Autoantibodies in Idiopathic Interstitial Pneumonia.
CureusAcute exacerbation of idiopathic pulmonary fibrosis a narrative review primary focus on treatments.
Journal of thoracic diseaseCase Report: Idiopathic pleuroparenchymal fibroelastosis.
F1000ResearchImprovement of diaphragmatic excursion in the supine position in a patient with idiopathic pleuroparenchymal fibroelastosis: A case report.
Respiratory medicine case reportsSuppression of OGN in lung myofibroblasts attenuates pulmonary fibrosis by inhibiting integrin αv-mediated TGF-β/Smad pathway activation.
Matrix biology : journal of the International Society for Matrix Biology18F-FDG accumulation at the early onset of acute exacerbation of idiopathic interstitial pneumonia on 18F-FDG PET/CT: A case report.
Respirology case reportsSingle-cell RNA sequencing reveals special basal cells and fibroblasts in idiopathic pulmonary fibrosis.
Scientific reportsImprovement in idiopathic interstitial pneumonia by adding macitentan to a patient unresponsive to nintedanib.
Respiratory medicine case reportsUsefulness of CT Quantification-Based Assessment in Defining Progressive Pulmonary Fibrosis.
Academic radiologyProgression to ANCA-associated vasculitis in patients with idiopathic interstitial pneumonia and positive ANCA.
Seminars in arthritis and rheumatismTrue predictor of postoperative acute exacerbation of idiopathic interstitial pneumonia in lung cancer patients.
Surgery todayInterstitial lung diseases associated with ANCA positivity: A different disease spectrum from interstitial pneumonia with autoimmune features.
Respiratory medicine and researchImpact of Controlling Nutritional Status Score on Mortality in Elderly Patients with Idiopathic Pulmonary Fibrosis.
Journal of clinical medicineAcute exacerbation predicting poor outcomes in idiopathic interstitial pneumonia and advanced lung cancer patients undergoing cytotoxic chemotherapy.
Scientific reportsNative lung surgery after single lung transplantation: clinical characteristics and outcomes.
Surgery todayIncidence, etiology, and outcome of hospital-acquired pneumonia in patients with acute exacerbation of fibrotic idiopathic interstitial pneumonia.
Respiratory investigationRelationship between idiopathic interstitial pneumonias (IIPs) and connective tissue disease-related interstitial lung disease (CTD-ILD): A narrative review.
Respiratory investigationPulmonary Hypertension in Idiopathic Interstitial Pneumonia Is Associated with Small Vessel Pruning.
American journal of respiratory and critical care medicineRadiological and histopathological features and treatment response by subtypes of interstitial pneumonia with autoimmune features: A prospective, multicentre cohort study.
Respiratory medicineRisk factors for progression of pulmonary fibrosis: a single-centered, retrospective study.
Frontiers in medicinePrevalence, incidence, and survival analysis of interstitial lung diseases in Hong Kong: a 16-year population-based cohort study.
The Lancet regional health. Western PacificThe Unveiled Triad: Clinical, Radiological and Pathological Insights into Hypersensitivity Pneumonitis.
Journal of clinical medicineHealth care costs and utilization of progressive fibrosing lung disease by underlying interstitial lung disease type.
Journal of managed care & specialty pharmacyHistopathological significance of connective tissue disease-associated interstitial lung disease in transbronchial lung cryobiopsy specimens.
Pathology, research and practiceHospitalization Rates in Interstitial Lung Disease: An Analysis of the Pulmonary Fibrosis Foundation Registry.
American journal of respiratory and critical care medicineIdentification of kynurenine and quinolinic acid as promising serum biomarkers for drug-induced interstitial lung diseases.
Respiratory researchOrganizing Pneumonia as a Pulmonary Sequela of Post-COVID-19 Syndrome in a Patient in Trinidad: A Case Report.
CureusAcute exacerbation of idiopathic pulmonary fibrosis after bivalent {tozinameran and famtozinameran} mRNA COVID-19 vaccination.
Respiratory medicine case reportsFrequency and characteristics of refractory dyspnea in idiopathic fibrosing interstitial pneumonia.
Respiratory medicineInterstitial lung disease associated with chronic liver disease.
Tuberkuloz ve toraksSurvival differences in rheumatoid arthritis interstitial lung disease and idiopathic pulmonary fibrosis may be explained by delays in presentation: results from multivariate analysis in a monocentric UK study.
Rheumatology internationalDisseminated cryptococcosis in a geriatric man following high-dose systemic steroid therapy for severe COVID-19 pneumonia.
Journal of general and family medicineIdiopathic interstitial pneumonia in a patient with von Hippel-Lindau syndrome: a first case.
ERJ open research[Chinese expert consensus on multidisciplinary discussion of interstitial lung disease].
Zhonghua jie he he hu xi za zhi = Zhonghua jiehe he huxi zazhi = Chinese journal of tuberculosis and respiratory diseasesCharacteristics of Interstitial Pneumonia With Autoimmune Features (IPAF): Protocol for a Multicenter Prospective Study.
JMIR research protocolsSurvival and acute exacerbation for patients with idiopathic pulmonary fibrosis (IPF) or non-IPF idiopathic interstitial pneumonias: 5-year follow-up analysis of a prospective multi-institutional patient registry.
BMJ open respiratory researchSalvianolic acid B protects against pulmonary fibrosis by attenuating stimulating protein 1-mediated macrophage and alveolar type 2 cell senescence.
Phytotherapy research : PTRAssociation of the lung immune prognostic index with the survival of patients with idiopathic interstitial pneumonias.
Respirology (Carlton, Vic.)SUCCESSFULLY TREATED ACUTE INTERSTITIAL PNEUMONIA.
Acta clinica CroaticaRo52/TRIM21 - From host defense to autoimmunity.
Cellular immunology＜Editors' Choice＞ Comparison of clinical features between patients with acute exacerbation of idiopathic interstitial pneumonia and collagen vascular disease-associated interstitial pneumonia.
Nagoya journal of medical sciencePotential Therapeutic Targets of Resveratrol in the Prevention and Treatment of Pulmonary Fibrosis.
Frontiers in bioscience (Landmark edition)Identifying potential biomarkers of idiopathic pulmonary fibrosis through machine learning analysis.
Scientific reportsSlowly Progressive ANCA-associated Glomerulonephritis with Strong Mesangial MPO Deposits Following a Diagnosis of Interstitial Lung Disease.
Internal medicine (Tokyo, Japan)Holistic management of patients with progressive pulmonary fibrosis.
Breathe (Sheffield, England)Design of a phase III, double-blind, randomised, placebo-controlled trial of BI 1015550 in patients with progressive pulmonary fibrosis (FIBRONEER-ILD).
BMJ open respiratory researchDiagnoses and treatments for participants with interstitial lung abnormalities detected in the Yorkshire Lung Screening Trial.
BMJ open respiratory researchDesign of a phase III, double-blind, randomised, placebo-controlled trial of BI 1015550 in patients with idiopathic pulmonary fibrosis (FIBRONEER-IPF).
BMJ open respiratory researchPalliative care in COPD and ILD: a call for action.
The European respiratory journalI-PreFer Study: A Discrete Choice Experiment to Explore Patient, Caregiver and Pulmonologist Preferences of Idiopathic Pulmonary Fibrosis Pharmacological Treatment Options.
Patient preference and adherenceZingiber officinale-Derived Extracellular Vesicles Attenuate Bleomycin-Induced Pulmonary Fibrosis Trough Antioxidant, Anti-Inflammatory and Protease Activity in a Mouse Model.
CellsNailfold capillaroscopy findings of interstitial pneumonia with autoimmune features.
The Korean journal of internal medicineRetracted: Classification and Pathological Diagnosis of Idiopathic Interstitial Pneumonia.
Computational intelligence and neuroscienceCarboplatin and weekly paclitaxel in combination with bevacizumab for the treatment of advanced non-small cell lung cancer complicated by idiopathic interstitial pneumonias: A feasibility study.
Respiratory investigationSpontaneous resolution of cryptogenic organizing pneumonia: Observational study.
MedicineDevelopment of microscopic polyangiitis following idiopathic pleuroparenchymal l fibroelastosis: A case report.
Modern rheumatology case reportsPulmonary hypertension secondary to interstitial fibrosis with pulmonary venous lesions masquerading pulmonary veno-occlusive disease.
Respirology case reportsImpact of partial pressure of arterial oxygen and radiologic findings on postoperative acute exacerbation of idiopathic interstitial pneumonia in patients with lung cancer.
Surgery todayA Real-World Prognosis in Idiopathic Pulmonary Fibrosis: A Special Reference to the Role of Antifibrotic Agents for the Elderly.
Journal of clinical medicineRituximab and mycophenolate mofetil combination in patients with interstitial lung disease (EVER-ILD): a double-blind, randomised, placebo-controlled trial.
The European respiratory journalUpdate on cryptogenic organizing pneumonia.
Frontiers in medicinePleuroparenchymal fibroelastosis secondary to autologous peripheral blood stem cell transplantation: A case report.
Respiratory medicine case reportsImaging of Pulmonary Fibrosis: An Update, From the AJR Special Series on Imaging of Fibrosis.
AJR. American journal of roentgenologyERS International Congress 2022: highlights from the Interstitial Lung Diseases Assembly.
ERJ open researchAcute exacerbation of pleuroparenchymal fibroelastosis with lower lobe usual interstitial pneumonia: An autopsy case.
Respiratory medicine case reportsPleuroparenchymal Fibroelastosis: A Review with a Focus on a Non-Infectious Complications after Hematopoietic Stem Cell Transplant.
BiomedicinesPrognostic role of CHA2DS2-VASc score for mortality risk assessment in non-advanced idiopathic pulmonary fibrosis: a preliminary observation.
Internal and emergency medicineHoneycomb lung is a major risk factor for preoperative radiological tumor size underestimation in patients with primary lung cancer.
Journal of thoracic diseaseGuselkumab-Associated Pulmonary Disease and Diffuse Alveolar Hemorrhage with Drug Rash with Eosinophilia and Systemic Symptoms.
CureusGenomic Fingerprint Associated with Familial Idiopathic Pulmonary Fibrosis: A Review.
International journal of medical sciencesThe balance between lung regulatory T cells and Th17 cells is a risk indicator for the acute exacerbation of interstitial lung disease after surgery: a case-control study.
BMC pulmonary medicineThe flare of care for rare: per aspera ad astra for rare lung diseases!
European respiratory review : an official journal of the European Respiratory SocietyInterstitial disease associated with connective tissue disease and vasculitis.
RadiologiaStudy protocol of an international patient-led registry in patients with pulmonary fibrosis using online home monitoring: I-FILE.
BMC pulmonary medicineClinical spectrum of Chinese hospitalized lung cancer patients with concomitant interstitial lung disease: before and after the new era of LC treatment.
Clinical and experimental medicineWhat Do We Need to Know About Rising Rates of Idiopathic Pulmonary Fibrosis? A Narrative Review and Update.
Advances in therapyMagnetic liposome as a dual-targeting delivery system for idiopathic pulmonary fibrosis treatment.
Journal of colloid and interface sciencePulmonary manifestations in VEXAS (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic) syndrome: a systematic review.
Rheumatology internationalAutomated Classification of Idiopathic Pulmonary Fibrosis in Pathological Images Using Convolutional Neural Network and Generative Adversarial Networks.
Diagnostics (Basel, Switzerland)Sensitivity of transbronchial lung cryobiopsy in the diagnosis of different interstitial lung diseases.
Scientific reportsChemotherapy versus best supportive care in advanced lung cancer and idiopathic interstitial pneumonias: A retrospective multi-centre cohort study.
Respiratory investigationThe impact of prognostic nutrition index on the waitlist mortality of lung transplantation.
General thoracic and cardiovascular surgeryRole of High-Resolution CT Thorax in Diagnosing Interstitial Lung Disease and Its Association With Smoking and Connective Tissue Disorder.
CureusIdentification and characterization of lysophosphatidylcholine 14:0 as a biomarker for drug-induced lung disease.
Scientific reportsDevelopment of an Artificial Intelligence Model for Analyzing the Relationship between Imaging Features and Glucocorticoid Sensitivity in Idiopathic Interstitial Pneumonia.
International journal of environmental research and public healthPositive Autoantibody Is Associated with Malignancies in Patients with Idiopathic Interstitial Pneumonias.
BiomedicinesA Retrospective Study of the Clinical, Radiological, and Pathological Characteristics of Patients with Interstitial Pneumonia Preceding Rheumatoid Arthritis.
Internal medicine (Tokyo, Japan)Efficacy of initial high- versus low-dose intravenous corticosteroid therapy in patients with acute exacerbation of idiopathic interstitial pneumonia: A nationwide observational study.
Annals of clinical epidemiologyPleuroparenchymal Fibroelastosis: A Case Report.
CureusDiagnostic value and safety of medical thoracoscopy under local anesthesia for unexplained diffuse interstitial lung disease: A retrospective study.
Chronic respiratory diseaseEvaluation of the potential complication of interstitial lung disease associated with antifibrotic drugs using data from databases reporting spontaneous adverse effects.
Clinical and translational science[Host factors and characteristics of hospitalized patients with pneumocystis jirovecii pneumonia].
Zhonghua jie he he hu xi za zhi = Zhonghua jiehe he huxi zazhi = Chinese journal of tuberculosis and respiratory diseasesNon-coding RNA in idiopathic interstitial pneumonia and Covid-19 pulmonary fibrosis.
Molecular biology reports[Clinical characteristics of 6 children with idiopathic interstitial pneumonia].
Zhonghua er ke za zhi = Chinese journal of pediatricsRadiological unilateral pleuroparenchymal fibroelastosis as a notable late complication after lung cancer surgery: incidence and perioperative associated factors.
Interactive cardiovascular and thoracic surgerySolitary Ground-Glass Nodule Mimicking Lung Cancer due to Focal Progression of Usual Interstitial Pneumonia.
International journal of surgical pathologyValidation of Proposed Criteria for Progressive Pulmonary Fibrosis.
American journal of respiratory and critical care medicineAssessment of diagnostic utility of serum hemeoxygenase-1 measurement for acute exacerbation of interstitial pneumonias.
Scientific reportsForced Oscillation Measurements in Patients with Idiopathic Interstitial Pneumonia Subjected to Pulmonary Rehabilitation.
Journal of clinical medicineThe Antifibrotic Effects of Inhaled Treprostinil: An Emerging Option for ILD.
Advances in therapyAtezolizumab for Pretreated Non-Small Cell Lung Cancer with Idiopathic Interstitial Pneumonia: Final Analysis of Phase II AMBITIOUS Study.
The oncologistMPO-ANCA-positive conversion and microscopic polyangiitis development in idiopathic interstitial pneumonia: a case report.
CEN case reportsAntisynthetase syndrome with rare EJ-1 antibodies with antiphospholipid syndrome.
Respirology case reportsClassification and Pathological Diagnosis of Idiopathic Interstitial Pneumonia.
Computational intelligence and neuroscienceMannan-Binding Lectin Reduces Epithelial-Mesenchymal Transition in Pulmonary Fibrosis via Inactivating the Store-Operated Calcium Entry Machinery.
Journal of innate immunityPrognostic implication of IgG4 and IgG1-positive cell infiltration in the lung in patients with idiopathic interstitial pneumonia.
Scientific reportsThe Use of Intraoperative Extracorporeal Membrane Oxygenation in Lung Transplantation: Initial Institutional Experience.
Brazilian journal of cardiovascular surgeryIdiopathic Pleuroparenchymal Fibroelastosis.
Journal of medical casesERS International Congress 2021: highlights from the Interstitial Lung Diseases Assembly.
ERJ open researchEvaluation of Proteasome Inhibitors in the Treatment of Idiopathic Pulmonary Fibrosis.
CellsAutoimmune pulmonary alveolar proteinosis with features similar to nonspecific interstitial pneumonia.
Respiratory medicine case reportsDeveloping a conceptual model of symptoms and impacts in progressive fibrosing interstitial lung disease to evaluate patient-reported outcome measures.
ERJ open researchConnective tissue disease-related interstitial lung disease (CTD-ILD) and interstitial lung abnormality (ILA): Evolving concept of CT findings, pathology and management.
European journal of radiology openA case of apixaban-associated idiopathic interstitial pneumonia.
Cardiology journalImpact of Palliative Care in End-of-Life of Fibrotic Interstitial Lung Disease Patients.
The American journal of hospice & palliative careChronic dyspnea with Raynaud's phenomenon and elevated ANA: A diagnosis of systemic sclerosis sine scleroderma.
The American journal of the medical sciences[Computed tomography lung density and small vessel quantification in pulmonary hypertension associated with progressive fibrosing interstitial lung disease (PF-ILD)].
Revue des maladies respiratoiresIs Thoracic Radiotherapy an Absolute Contraindication for Treatment of Lung Cancer Patients With Interstitial Lung Disease? A Systematic Review.
Clinical oncology (Royal College of Radiologists (Great Britain))Utility of Telomerase Gene Mutation Testing in Patients with Idiopathic Pulmonary Fibrosis in Routine Practice.
CellsSurvival after surgery for clinical stage I non-small-cell lung cancer with interstitial pneumonia.
Lung cancer (Amsterdam, Netherlands)Demystifying idiopathic interstitial pneumonia: time for more etiology-focused nomenclature in interstitial lung disease.
Expert review of respiratory medicineInterstitial lung diseases associated with mutations of poly(A)-specific ribonuclease: A multicentre retrospective study.
Respirology (Carlton, Vic.)Outcomes and Incidence of PF-ILD According to Different Definitions in a Real-World Setting.
Frontiers in pharmacologyAssociações
Organizações que acompanham esta doença — pra ter apoio e orientação
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Isolated antineutrophil cytoplasmic antibody-associated interstitial lung disease: A systematic review of an emerging condition.
- Nocturnal hypercapnia in the patients with idiopathic interstitial pneumonia registered for lung transplantation.
- Impact of flat chest on waitlist mortality in adult patients with pleuroparenchymal fibroelastosis listed for lung transplantation.
- Postoperative pleurodesis using OK-432 for pulmonary air leak in lung cancer patients with idiopathic interstitial pneumonia: A retrospective study.
- Upfront combination therapy with nintedanib and anti-inflammatory agents for progressive pulmonary fibrosis: a multicentre, single-arm phase 2 study (TOP-ILD).
- Prognostic impact of thyroid transcription factor-1 expression and the efficacy of carboplatin plus (nab-) paclitaxel in non-squamous non-small cell lung cancer complicated with idiopathic interstitial pneumonias.
- Subset binding enables detection of multimodal patient subgroup patterns and drug target discovery in idiopathic pulmonary fibrosis.
- The role of S100A8/A9 in the pathogenesis of acute exacerbations of pulmonary fibrosis.
- Clinical spectrum and profile of interstitial lung disease: an ambispective study from a tertiary center in North India.
- Risk Factors for Pneumonitis in Patients with Unresectable Advanced Non-small Cell Lung Cancer Treated with Immune Checkpoint Inhibitors.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:98300(Orphanet)
- MONDO:0002429(MONDO)
- GARD:13337(GARD (NIH))
- Variantes catalogadas(ClinVar)
- Busca completa no PubMed(PubMed)
- Artigo Wikipedia(Wikipedia)
- Q1790424(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
