Raras
Buscar doenças, sintomas, genes...
Síndrome do intestino curto secundário
ORPHA:95427CID-10 · K91.2CID-11 · DA96.04DOENÇA RARA

A síndrome do intestino curto secundária é uma insuficiência intestinal causada por qualquer condição que resulte em um intestino delgado funcional com menos de 200 cm de comprimento e é caracterizada por diarreia, má absorção de nutrientes, dilatação intestinal e dismobilidade.

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Introdução

O que você precisa saber de cara

📋

A síndrome do intestino curto secundária é uma insuficiência intestinal causada por qualquer condição que resulte em um intestino delgado funcional com menos de 200 cm de comprimento e é caracterizada por diarreia, má absorção de nutrientes, dilatação intestinal e dismobilidade.

Escala de raridade

CLASSIFICAÇÃO ORPHANET · BRASIL 2024
Unknown
Ultra-rara
<1/50k
Muito rara
1/20k
Rara
1/10k
Pouco freq.
1/5k
Incomum
1/2k
Prevalência
0.0
Worldwide
Início
All ages
🏥
SUS: Sem cobertura SUSScore: 0%
CID-10: K91.2
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Entender a doença

Do básico ao detalhe, leia no seu ritmo

Preparando trilha educativa...

Sinais e sintomas

O que aparece no corpo e com que frequência cada sintoma acontece

Partes do corpo afetadas

🫃
Digestivo
10 sintomas
📏
Crescimento
4 sintomas
🩸
Sangue
4 sintomas
🦴
Ossos e articulações
1 sintomas
🫘
Rins
1 sintomas

+ 12 sintomas em outras categorias

Características mais comuns

55%prev.
Perda de peso
Frequente (79-30%)
55%prev.
Anormalidade do intestino delgado
Frequente (79-30%)
55%prev.
Desnutrição
Frequente (79-30%)
55%prev.
Anormalidade do metabolismo vitamínico
Frequente (79-30%)
55%prev.
Má absorção
Frequente (79-30%)
17%prev.
Distensão abdominal
Ocasional (29-5%)
32sintomas
Frequente (5)
Ocasional (22)
Muito raro (5)

Os sintomas variam de pessoa para pessoa. Abaixo estão as 32 características clínicas mais associadas, ordenadas por frequência.

Perda de pesoWeight loss
Frequente (79-30%)55%
Anormalidade do intestino delgadoAbnormality of the small intestine
Frequente (79-30%)55%
DesnutriçãoMalnutrition
Frequente (79-30%)55%
Anormalidade do metabolismo vitamínicoAbnormality of vitamin metabolism
Frequente (79-30%)55%
Má absorçãoMalabsorption
Frequente (79-30%)55%

Linha do tempo da pesquisa

Publicações por ano — veja quando o interesse científico cresceu
Anos de pesquisa1desde 2026
Últimos 10 anos200publicações
Pico202236 papers
Linha do tempo
2026Hoje · 2026📈 2022Ano de pico
Publicações por ano (últimos 10 anos)

Encontrou um erro ou informação desatualizada? Sugira uma correção →

Genética e causas

O que está alterado no DNA e como passa nas famílias

🧬

Nenhum gene associado encontrado

Os dados genéticos desta condição ainda estão sendo catalogados.

Diagnóstico

Os sinais que médicos procuram e os exames que confirmam

Carregando...

Tratamento e manejo

Remédios, cuidados de apoio e o que precisa acompanhar

Carregando informações de tratamento...

Onde tratar no SUS

Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)

🇧🇷 Atendimento SUS — Síndrome do intestino curto secundário

🗺️

Selecione um estado ou use sua localização para ver resultados.

Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.

Pesquisa ativa

Ensaios clínicos abertos e novidades científicas recentes

Pesquisa e ensaios clínicos

Nenhum ensaio clínico registrado para esta condição.

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Publicações mais relevantes

Timeline de publicações
0 papers (10 anos)
#1

The role of mediterranean diet and highly processed foods in inflammatory bowel diseases.

Digestive and liver disease : official journal of the Italian Society of Gastroenterology and the Italian Association for the Study of the Liver2026 Feb 28

The Mediterranean Diet (MD) is considered a balanced dietary model, whereas high consumption of highly processed foods (HPF) may worsen metabolic health. We aimed to compare adherence to the MD and HPF consumption between patients with Crohn's Disease (CD) and Ulcerative Colitis (UC), and to assess their relationship with disease activity. A secondary objective was to explore the association between dietary patterns and metabolic parameters. Adherence to the MD was assessed using the Pyramid Mediterranean Diet Score (PyrMDS), while HPF intake was evaluated with the short questionnaire on highly processed foods (sQ-HPF). 193 consecutive IBD patients were included. CD patients showed significantly lower adherence to the MD compared with UC patients (median PyrMDS 9.3 vs 9.8, p = 0.02), while HPF consumption was similar in both groups (median sQ-HPF 3). In CD patients, a trend toward an inverse correlation was observed between MD adherence and disease activity (p = 0.07). Higher HPF consumption was positively associated with metabolic syndrome (median sQ-HPF 4 vs 3, p = 0.01). CD patients exhibit lower adherence to the MD, particularly during periods of higher disease activity, while greater HPF intake is linked to adverse metabolic profiles. Tailored nutritional counseling is important for supporting healthier dietary patterns in individuals with IBD.

#2

Teduglutide use in haemodialysis-dependent renal failure from secondary hyperoxaluria in short bowel syndrome and type 3 intestinal failure - A case report.

Intestinal Failure (New York, N.Y.)2026

Renal impairment is common in patients receiving long-term home parenteral nutrition (HPN) for short bowel syndrome-associated intestinal failure (SBS-IF). While glucagon-like peptide-2 (GLP-2) analogues like teduglutide are effective in reducing parenteral support (PS) requirements, data on their use in advanced stage chronic kidney disease (CKD) or haemodialysis are scarce. We describe a 66-year-old female with SBS-IF on HPN, complicated by hyperoxaluria and nephrocalcinosis contributing to stage 4 CKD. Initial renally-adjusted teduglutide dosing (0.025 mg/kg/day) enabled enteral autonomy, but was interrupted by intercurrent illness. As a result of progressive renal dysfunction, the patient was commenced on haemodialysis. Teduglutide was introduced post-dialysis at full dose (0.05 mg/kg), resulting in a sustained 36 % reduction in weekly PS requirements without adverse effects, despite recurrent sepsis. This case demonstrates a clinically significant teduglutide response in a haemodialysis-dependent SBS-IF patient, supporting post-dialysis dosing as a feasible strategy in this HPN cohort.

#3

Spontaneous transanal evisceration of the small bowel through perforation of the sigmoid colon: a case report and new surgical approach.

International journal of surgery case reports2026 Mar

Transanal evisceration of the small intestine is a rare surgical emergency that requires immediate intervention. Since its initial description in 1827, only three cases of evisceration secondary to perforation of the sigmoid colon have been documented. This case report describes the fourth case worldwide. An 85-year-old woman presented with transanal small bowel evisceration after straining during defecation. Examination revealed prolapsed, congested but viable small bowel loops through the anal canal, without uterine or rectal prolapse. Emergency laparotomy identified sigmoid perforation likely due to chronic diverticulitis. Initial surgery involved sigmoid segment resection and blind stapling, followed by ICU care. A second-look laparotomy required 290 cm small bowel resection, sigmoidectomy, colorectal anastomosis, and loop ileostomy. Recovery was prolonged due to age and short bowel syndrome. The patient was discharged to a nursing home 2 months postoperatively. Transanal evisceration involves small bowel herniation via rectal or sigmoid perforation, commonly due to rectal prolapse and sudden increase in intra-abdominal pressure. Surgical management includes emergency laparotomy, bowel viability assessment, resection, and repair. Hartmann's procedure is preferred in contaminated fields. Mortality has decreased significantly with improved techniques. Definitive care should address underlying pathology to prevent recurrence. Immediate surgical intervention is the mainstay of treatment in transanal evisceration of the small bowel. The choice of surgical approach depends on intraoperative findings. A staged surgical approach including second or even third look surgeries may improve small bowel preservation and improve clinical outcome.

#4

Case report: minimally invasive management of two major complications of colonic perforation and pseudoaneurysm formation following nephrostomy tube placement.

The Canadian journal of urology2026 Feb 28

We present a case of two major complications following insertion of a nephrostomy managed in a minimally invasive way. Our case is the first in the literature to describe this minimally invasive treatment technique for colon perforation in a completely asymptomatic patient. A 75-year-old female patient with a history of bilateral obstructive uropathy secondary to bilateral radiation-induced ureteric strictures attended for bilateral nephrostomy placement. The patient had a history of endometrial cancer, treated previously by total hysterectomy and bilateral salpingo-oophorectomy with adjuvant chemo-radiotherapy and brachytherapy. Her recovery had been further complicated by the development of radiation cystitis, small bowel resection, and short gut syndrome. The strictures had previously been managed with bilateral double J stents, which have now failed. A left-sided nephrostomy insertion was performed. A CT-scan prompted by a repeat deterioration in renal function revealed a right-sided hydronephrosis and suggested transcolic passage of the previously placed left-sided nephrostomy. She had remained clinically well and apyretic. A right-sided nephrostomy was inserted, and the left re-sited following a colonoscopy-guided nephrostomy removal and clip occlusion of the nephrostomy tract. The patient then developed a pseudoaneurysm, which was managed with embolization. The patient was able to return home with corrected kidney function. The three-monthly checks for changes in nephrostomy catheters did not reveal any complications. The patient therefore presented with two major complications of nephrostomy placement: colonic perforation and pseudoaneurysm, classified as Clavien IIIb and IIIa, respectively. Multidisciplinary management, including urologists, gastroenterologists, general surgeons, and radiologists, enabled a minimally invasive management. Minimally invasive management with endoscopic clip placement appears to be a safe alternative to directed fistula of colonic perforation.

#5

Pilot trial: 8.4% sodium bicarbonate locks for infection prevention in pediatric intestinal failure.

Nutrition in clinical practice : official publication of the American Society for Parenteral and Enteral Nutrition2026 Feb 25

Pediatric patients with intestinal failure (IF) require long-term central vascular catheters (CVCs) for parenteral nutrition, placing them at high risk for catheter-related bloodstream infections (CRBSIs). Sodium bicarbonate (NaHCO₃) locks have shown potential in reducing CRBSIs in adult populations, but data in pediatric patients with IF remain limited. We conducted an open-label prospective cohort study at a tertiary medical center to evaluate the impact of 8.4% NaHCO₃ locks on CRBSI and CVC replacement rates in pediatric patients with IF (ClinicalTrials.gov NCT05927484). The baseline period (heparin locks) was assessed retrospectively, whereas the intervention period (NaHCO₃ locks) was evaluated prospectively. Primary outcome was CRBSI rate; secondary outcomes included CVC replacement because of CRBSI and infection-related hospitalizations. In the per‑protocol analysis, six patients contributed 5733 total catheter days (3244 on heparin, 2489 on NaHCO₃). CRBSI rates decreased from a median of 8.2 to 3.0 per 1000 catheter days after switching to NaHCO₃ locks (P = 0.11). A similar downward trend was observed in the intent‑to‑treat analysis. A statistically significant reduction in CVC replacement because of CRBSI was observed (2.3 vs 0 per 1000 catheter days; P = 0.03). Trends toward reduced hospital and intensive care unit admissions were also noted in the intervention group. No serious adverse events were attributed to NaHCO₃ lock use. NaHCO₃ locks appear to be a safe and promising strategy for reducing CRBSI-related complications in pediatric patients with IF, especially where access to more effective lock solutions is limited. Larger prospective studies are needed to confirm these findings.

Publicações recentes

Ver todas no PubMed

📚 EuropePMCmostrando 200

2026

Teduglutide use in haemodialysis-dependent renal failure from secondary hyperoxaluria in short bowel syndrome and type 3 intestinal failure - A case report.

Intestinal Failure (New York, N.Y.)
2026

Spontaneous transanal evisceration of the small bowel through perforation of the sigmoid colon: a case report and new surgical approach.

International journal of surgery case reports
2026

Case report: minimally invasive management of two major complications of colonic perforation and pseudoaneurysm formation following nephrostomy tube placement.

The Canadian journal of urology
2026

The role of mediterranean diet and highly processed foods in inflammatory bowel diseases.

Digestive and liver disease : official journal of the Italian Society of Gastroenterology and the Italian Association for the Study of the Liver
2026

Pilot trial: 8.4% sodium bicarbonate locks for infection prevention in pediatric intestinal failure.

Nutrition in clinical practice : official publication of the American Society for Parenteral and Enteral Nutrition
2026

Mid-Term Results of the Multicenter CAMPARI Registry Using the E-Liac Iliac Branch Device for Aorto-Iliac Aneurysms.

Journal of cardiovascular development and disease
2026

Growth failure and early recurrence in congenital diaphragmatic hernia: An international cohort study.

Journal of pediatric surgery
2026

Pharmacokinetics and Safety of Single-Dose Apraglutide in Individuals with Normal and Impaired Hepatic Function: A Phase 1, Open-Label Trial.

Clinical pharmacology in drug development
2025

Impact of teduglutide on pediatric short bowel syndrome: A systematic review and trial sequential meta-analysis.

World journal of gastrointestinal surgery
2025

The molecular interplay between the gut microbiome and circadian rhythms: an integrated review.

Frontiers in microbiology
2025

Oxalate nephropathy precipitated by linaclotide in a high-risk patient.

Clinical nephrology. Case studies
2026

The impact of intervention timing, etiology, and revascularization strategy on acute mesenteric ischemia outcomes.

Journal of vascular surgery
2025

Idiopathic hypereosinophilic syndrome complicated by computed tomography-negative cerebral infarction, strangulated intestinal obstruction, and hepatic portal venous gas: a case report of multi-system involvement.

Quantitative imaging in medicine and surgery
2025

Geriatric syndromes in intestinal failure: An accelerated aging phenomenon in middle adulthood patients?

Clinical nutrition ESPEN
2025

A 2-year prospective study on the evolution of Low Anterior Resection Syndrome (LARS) following rectal cancer surgery.

International journal of colorectal disease
2025

Hypnotherapy self-exercises with audio files for children and adolescents with disorders of gut-brain interaction-a study of feasibility and preliminary effects in Sweden.

Therapeutic advances in gastroenterology
2025

Nyctalopia Due to Vitamin A Deficiency Secondary to Short Bowel Syndrome: When the Electroretinogram Is the Diagnostic Key.

Brain sciences
2025

A case of yogurt central line-associated bloodstream infection in a child with intestinal failure.

Nutrition in clinical practice : official publication of the American Society for Parenteral and Enteral Nutrition
2025

Resistant Starch and Microbiota-Derived Secondary Metabolites: A Focus on Postbiotic Pathways in Gut Health and Irritable Bowel Syndrome.

International journal of molecular sciences
2025

The Effect of Faecal Microbiota Transplantation on Cognitive Function in Cognitively Healthy Adults with Irritable Bowel Syndrome: Protocol for a Randomised, Placebo-Controlled, Double-Blinded Pilot Study.

Methods and protocols
2025

Techniques and procedures for advancing feeds for children with intestinal failure due to short bowel syndrome: A narrative review.

Nutrition in clinical practice : official publication of the American Society for Parenteral and Enteral Nutrition
2025

Outcomes of glepaglutide on intestinal absorption and parenteral support in patients with short bowel syndrome.

Clinical nutrition ESPEN
2025

Metastatic esophageal squamous cell carcinoma with paraneoplastic Raynaud phenomenon: a case report.

AME case reports
2025

Calcium butyrate efficacy in pediatric irritable bowel syndrome: Randomized placebo-controlled multiomics-based clinical trial.

Journal of pediatric gastroenterology and nutrition
2025

The interplay of gut microbiota and intestinal motility in gastrointestinal function.

Journal of smooth muscle research = Nihon Heikatsukin Gakkai kikanshi
2025

Ten-Year-Old Girl With Emesis, Abdominal Distention, Tenderness, Altered Mental Status, and Ataxia.

Pediatrics
2025

Small Intestinal Strangulation Secondary to Omental Adhesion Entrapment in a Dog.

Case reports in veterinary medicine
2025

Serial Transverse Duodenal Enteroplasty in Adults With Ultra-Short Bowel Syndrome: A Case Series.

Cureus
2025

Lactobacillus rhamnosus GG maintains gut microbiota stability and promotes intestinal adaptation via activated intestinal farnesoid X receptor signaling in short bowel syndrome.

Communications biology
2025

Clinical Trial: A Mediterranean Low-FODMAP Diet Alleviates Symptoms of Non-Constipation IBS-Randomized Controlled Study and Volatomics Analysis.

Nutrients
2025

Acute arterial mesenteric ischaemia: comparison of partial and complete occlusion of the superior mesenteric artery.

Insights into imaging
2025

Clinical outcomes in Crohn's disease patients with short bowel syndrome on home parenteral nutrition are comparable to those with short bowel syndrome from other etiologies.

Clinical nutrition (Edinburgh, Scotland)
2025

Salvage of stoma stenosis using a fenestrated ultrathin ALT perforator flap following Kock pouch ileostomy.

Case reports in plastic surgery &amp; hand surgery
2025

Glucagon-like peptide-2 pharmacotherapy activates hepatic Farnesoid X receptor-signaling to attenuate resection-associated bile acid loss in mice.

Molecular metabolism
2025

Congenital Diarrhea and Enteropathies.

NeoReviews
2025

Botulinum toxin improved intestinal adaptation to short gut in a twenty-one-day-old weanling rat.

Brazilian journal of medical and biological research = Revista brasileira de pesquisas medicas e biologicas
2025

A multicenter study on enteral autonomy outcome of pediatric intestinal failure patients from a middle-income country.

Clinical nutrition ESPEN
2024

Efficacy and Safety of a Mixture of Microencapsulated Sodium Butyrate, Probiotics, and Short Chain Fructooligosaccharides in Patients with Irritable Bowel Syndrome-A Randomized, Double-Blind, Placebo-Controlled Study.

Journal of clinical medicine
2025

Glepaglutide, a Long-Acting Glucagon-like Peptide-2 Analogue, Reduces Parenteral Support in Patients With Short Bowel Syndrome: A Phase 3 Randomized Controlled Trial.

Gastroenterology
2025

Quality and quantity of carbohydrates, faecal short-chain fatty acids and gastrointestinal symptoms - results from a randomised, controlled trial (CARBFUNC).

Clinical nutrition (Edinburgh, Scotland)
2024

Multimodal surgical strategy for mixed refractory hypertonia in a patient with cerebral palsy: C1-2 puncture and pectoral pocket for baclofen pump implantation following lumbosacral ventral-dorsal rhizotomy. Illustrative case.

Journal of neurosurgery. Case lessons
2024

Short Bowel Syndrome Is Not a Contraindication for Kidney Transplantation.

Pediatric transplantation
2024

Efficacy and safety of apraglutide in short bowel syndrome with intestinal failure and colon-in-continuity: A multicenter, open-label, metabolic balance study.

Clinical nutrition (Edinburgh, Scotland)
2024

Rapid identification of primary atopic disorders (PAD) by a clinical landmark-guided, upfront use of genomic sequencing.

Allergologie select
2025

Serial Transverse Enteroplasty (STEP) for Short Bowel Syndrome (SBS) in Children: A Multicenter Study on Long-term Outcomes.

Journal of pediatric surgery
2024

Complications resulting from an intragastric balloon in a patient without follow-up and monitoring.

BMJ case reports
2024

Protocol for a randomized controlled trial of an internet-based prevention intervention for young children at-risk for functional abdominal pain.

Trials
2024

Unplanned 30-Day Readmissions After Hospitalization for Irritable Bowel Syndrome.

Cureus
2024

Effect of parenteral lipids on essential fatty acid deficiency in pediatric intestinal failure: A retrospective cohort study.

JPEN. Journal of parenteral and enteral nutrition
2024

Endovascular revascularization vs open surgical revascularization as the first strategy for arterial acute mesenteric ischemia: A systematic review and meta-analysis.

Journal of vascular surgery
2024

Intestinal microbial and metabolite profile in infants with small bowel stomas after bowel resection.

Journal of pediatric gastroenterology and nutrition
2024

Achieving Digestive Autonomy and Gastrointestinal Continuity in a Patient with Short Bowel Syndrome Secondary to Concomitant Jejunal Atresia and Small Intestinal Hirschsprung's Disease.

European journal of pediatric surgery reports
2024

Characteristics and clinical outcomes of pediatric patients following massive bowel resection: A retrospective cohort study.

Intestinal Failure (New York, N.Y.)
2024

Association between Postoperative Adjuvant Vasodilator Therapy and In-Hospital Mortality for Non-Occlusive Mesenteric Ischemia: A Nationwide Observational Study.

Journal of Nippon Medical School = Nippon Ika Daigaku zasshi
2024

Plasma metabolomics changes comparing daytime to overnight infusions of home parenteral nutrition in adult patients with short bowel syndrome: Secondary analysis of a clinical trial.

Clinical nutrition ESPEN
2024

Early safety and efficiency outcomes of a novel interdisciplinary laparoscopic resection rectopexy combined with sacrocolpopexy for women with obstructive defecation syndrome and pelvic organ prolapse: a single center study.

BMC surgery
2024

Archaea influence composition of endoscopically visible ileocolonic biofilms.

Gut microbes
2024

Therapeutic effect of Wendan Decoction combined with mosapride on gastroesophageal reflux disease after esophageal cancer surgery.

World journal of clinical cases
2024

Long-term weight loss of distal gastric bypass is moderately superior compared to proximal gastric bypass in patients with a BMI of 37-44 Kg/m2.

Langenbeck's archives of surgery
2024

Effects of a low FODMAP diet on the symptom management of patients with irritable bowel syndrome: a systematic umbrella review with the meta-analysis of clinical trials.

Food &amp; function
2024

Home parenteral nutrition, sleep patterns, and depressive symptoms: Secondary analysis of cross-sectional data.

JPEN. Journal of parenteral and enteral nutrition
2024

Managing venous thrombosis in a pediatric patient with short bowel and congenital nephrotic syndromes: a case report emphasizing rivaroxaban level monitoring.

Frontiers in pediatrics
2024

Evaluation of the Effectiveness of Teduglutide Treatment in Patients with Short Bowel Syndrome in Slovakia-Multicenter Real-World Study.

Journal of clinical medicine
2024

Skipped Aganglionic Lengthening Transposition (SALT) is highly effective to achieve enteral autonomy in selected patients with intestinal failure secondary to total intestinal aganglionosis.

Pediatric surgery international
2024

A case report of lactobacillus bacteremia in a patient on chronic parenteral nutrition.

Clinical nutrition ESPEN
2024

Improved Outcomes Associated With Teduglutide Use in Patients With Both Short Bowel Syndrome and Crohn's Disease.

Crohn's &amp; colitis 360
2024

Abdominal cocoon syndrome (ACS): a case report of a Chinese male diagnosed idiopathic ACS with inborn short intestine.

Annals of medicine and surgery (2012)
2024

Iodine status in children with intestinal failure.

Journal of pediatric gastroenterology and nutrition
2025

Ogilvie, when medical and endoscopic treatment fail.

Revista espanola de enfermedades digestivas
2024

Specific probiotics and prebiotics to improve the quality of life of patients with chronic irritable bowel syndrome.

Minerva gastroenterology
2024

Small and large bowel anatomy is associated with enteral autonomy in infants with short bowel syndrome: A retrospective cohort study.

JPEN. Journal of parenteral and enteral nutrition
2023

Implications of COVID-19 in Acute Mesenteric Ischemia and Bowel Necrosis: A Case Report.

Cureus
2023

Anastomotic leakage and functional outcomes following total mesorectal excision with delayed and immediate colo-anal anastomosis for rectal cancer: Two single-arm phase II trials.

European journal of surgical oncology : the journal of the European Society of Surgical Oncology and the British Association of Surgical Oncology
2023

Emerging uses of glucagon-like peptide 1 (GLP-1) receptor agonists following ileal resection: literature review and case examples.

Frontline gastroenterology
2023

The Long-Term Effects of a Low-Fermentable Oligosaccharides, Disaccharides, Monosaccharides, and Polyols Diet for Irritable Bowel Syndrome Management.

Current developments in nutrition
2023

The Effect of the Flint Water Crisis Secondary to Increased Lead Levels in Drinking Water on Constipation in Children in the City of Flint, Michigan, USA.

Cureus
2023

Present state of intestinal transplantation in Japan.

Pediatric surgery international
2023

A multi-national survey of experience and attitudes towards managing catheter related blood stream infections for home parenteral nutrition.

Clinical nutrition ESPEN
2023

The role of delayed aortic surgery in type A aortic dissection and mesenteric ischemia: a systematic review and meta-analysis.

Journal of cardiothoracic surgery
2023

Possible role of the gut microbiome in mediating the beneficial effects of the six-herbal formulation STW 5-II on digestive health.

Phytomedicine : international journal of phytotherapy and phytopharmacology
2023

Probiotics for the management of irritable bowel syndrome: a systematic review and three-level meta-analysis.

International journal of surgery (London, England)
2023

Nutritional management of a patient with chronic intestinal failure and hemodialysis receiving teduglutide: A case report.

Nutrition (Burbank, Los Angeles County, Calif.)
2023

Oral antimicrobial agents in patients with short bowel syndrome: worth a try!

The Journal of antimicrobial chemotherapy
2023

[Oxalate: from physiology to pathology].

Nephrologie &amp; therapeutique
2023

Transanal irrigation in functional bowel disorders and LARS: short-term results from an Italian national study.

Techniques in coloproctology
2024

A CASE OF RETINAL ATHEROSCLEROTIC OXALOSIS DUE TO HYPEROXALURIA IN A PATIENT WITH SHORT GUT SYNDROME.

Retinal cases &amp; brief reports
2023

Small bowel ischemia secondary to gastric pacemaker wires-a case report.

Journal of surgical case reports
2023

Short-term clinical evaluation of teduglutide for patients with Crohn's disease on home parenteral support for postoperative short bowel syndrome with intestinal failure.

Clinical nutrition (Edinburgh, Scotland)
2023

Clinical Outcome of Ultrasound-Detected Perforated Necrotizing Enterocolitis without Radiographic Pneumoperitoneum in Very Preterm Infants.

Journal of clinical medicine
2023

Diet-microbial cross-talk underlying increased visceral perception.

Gut microbes
2022

Novel Therapeutic Approaches for Mitigating Complications in Short Bowel Syndrome.

Nutrients
2022

Effects of Microencapsulated Sodium Butyrate, Probiotics and Short Chain Fructooligosaccharides in Patients with Irritable Bowel Syndrome: A Study Protocol of a Randomized Double-Blind Placebo-Controlled Trial.

Journal of clinical medicine
2023

High Rate of Venous Thromboembolism in Severe Pediatric Intestinal Failure.

The Journal of pediatrics
2023

Bone marrow oxalosis with pancytopenia in a patient with short bowel syndrome: Report of a case and review of the literature.

JPEN. Journal of parenteral and enteral nutrition
2022

Real-world etiologies and treatments of pediatric short bowel syndrome in Japan.

Pediatrics international : official journal of the Japan Pediatric Society
2022

Tracking the physicochemical stability of teduglutide (Revestive®) clinical solutions over time in different storage containers.

Journal of pharmaceutical and biomedical analysis
2022

A rare case of eosinophilic gastrointestinal disorders with short bowel syndrome after strangulated bowel obstruction.

Surgical case reports
2022

Surgical strategies for intestinal Crohn's disease.

Zhong nan da xue xue bao. Yi xue ban = Journal of Central South University. Medical sciences
2023

Long-term home parenteral nutrition and profile of amino acids in serum and their loss in urine.

The British journal of nutrition
2022

The Role of Pelvic Floor Muscle Training on Low Anterior Resection Syndrome: A Multicenter Randomized Controlled Trial.

Annals of surgery
2022

Surgical Treatment of Short Bowel Syndrome-The Past, the Present and the Future, a Descriptive Review of the Literature.

Children (Basel, Switzerland)
2022

Seropositive Neuromyelitis Optica in a Case of Undiagnosed Ankylosing Spondylitis: A Neuro-Rheumatological Conundrum.

Qatar medical journal
2022

Carnitine Deficiency in an Adult With Short Bowel Syndrome After Surgical Resection.

ACG case reports journal
2022

[Growth of Children with Neonatal Short Bowel Syndrome: Its Relationship to Gestational Age].

Acta gastroenterologica Latinoamericana
2022

Management of pediatric intestinal failure related to short bowel syndrome.

Seminars in pediatric surgery
2023

Anastomotic Height Is a Valuable Indicator of Long-term Bowel Function Following Surgery for Rectal Cancer.

Diseases of the colon and rectum
2022

Safety of bariatric surgery in patients with previous acute coronary events or heart failure: nationwide cohort study.

BJS open
2022

Sodium Bicarbonate Locks May Be a Safe and Effective Alternative in Pediatric Intestinal Failure: A Pilot Study.

Journal of pediatric gastroenterology and nutrition
2022

Nonocclusive mesenteric ischemia caused by type B aortic dissection: a case report.

BMC surgery
2022

Bridging Liver Transplantation in the Treatment of Intestinal Failure Associated Liver Disease in Infants-A Bridge Too Far?

Children (Basel, Switzerland)
2022

Venous Thromboembolic Complications in Pediatric Gastrointestinal Diseases: Inflammatory Bowel Disease and Intestinal Failure.

Frontiers in pediatrics
2022

The dual GLP-1 and GLP-2 receptor agonist dapiglutide promotes barrier function in murine short bowel.

Annals of the New York Academy of Sciences
2023

Effects of glepaglutide, a long-acting glucagon-like peptide-2 analog, on intestinal morphology and perfusion in patients with short bowel syndrome: Findings from a randomized phase 2 trial.

JPEN. Journal of parenteral and enteral nutrition
2022

Autologous Intestinal Reconstruction Surgery in Short Bowel Syndrome: Which, When, and Why.

Frontiers in nutrition
2022

Dietary Management of Chronic Kidney Disease and Secondary Hyperoxaluria in Patients with Short Bowel Syndrome and Type 3 Intestinal Failure.

Nutrients
2022

Potential Roles of Enterochromaffin Cells in Early Life Stress-Induced Irritable Bowel Syndrome.

Frontiers in cellular neuroscience
2022

Evaluation of a Multidisciplinary Integrated Treatment Approach Versus Standard Model of Care for Functional Gastrointestinal Disorders (FGIDS): A Matched Cohort Study.

Digestive diseases and sciences
2022

Apraglutide, a novel once-weekly glucagon-like peptide-2 analog, improves intestinal fluid and energy absorption in patients with short bowel syndrome: An open-label phase 1 and 2 metabolic balance trial.

JPEN. Journal of parenteral and enteral nutrition
2022

Efficacy of Teduglutide for Parenteral Support Reduction in Patients with Short Bowel Syndrome: A Systematic Review and Meta-Analysis.

Nutrients
2022

Comparing bowel lengthening procedures: which, when, and why?

Current opinion in organ transplantation
2022

Operative, long-term and quality of life outcomes after salvage of failed re-do ileal pouch anal anastomosis.

Colorectal disease : the official journal of the Association of Coloproctology of Great Britain and Ireland
2022

Severe Coagulopathy in a Patient With Short Bowel Syndrome.

The Journal of emergency medicine
2022

Microbiomes in physiology: insights into 21st-century global medical challenges.

Experimental physiology
2021

Longitudinal Follow-Up With Radiologic Screening for Recurrence and Secondary Hiatal Hernia in Neonates With Open Repair of Congenital Diaphragmatic Hernia-A Large Prospective, Observational Cohort Study at One Referral Center.

Frontiers in pediatrics
2022

Small bowel intussusception and concurrent jejunal polyp with neoplastic transformation: a new diagnosis of Peutz-Jeghers syndrome.

Annals of the Royal College of Surgeons of England
2021

Short bowel syndrome in infancy: recent advances and practical management.

Frontline gastroenterology
2022

Fecal microbiome and bile acid metabolome in adult short bowel syndrome.

American journal of physiology. Gastrointestinal and liver physiology
2022

Predicting Factors of Protracted Intestinal Failure in Children with Gastroschisis.

The Journal of pediatrics
2022

Feasibility of open abdomen surgery treatment for near fatal necrotizing enterocolitis in preterm infants.

Journal of pediatric surgery
2021

Personalized exercise intervention in HPN patients - A feasibility study.

Clinical nutrition ESPEN
2021

Conservative management of malignant gastric outlet obstruction syndrome-evidence based evaluation of endoscopic ultrasound-guided gastroentero-anastomosis.

World journal of gastrointestinal oncology
2022

Prenatal ultrasonographic markers for prediction of complex gastroschisis and adverse perinatal outcomes: a systematic review and meta-analysis.

Archives of disease in childhood. Fetal and neonatal edition
2021

[Clinical guidelines for the managment of intestinal failure secondary to pediatric short bowel syndrome].

Archivos argentinos de pediatria
2021

Incidence of surgical procedures for gastrointestinal complications after abdominal wall closure in patients with gastroschisis and omphalocele.

Pediatric surgery international
2021

Intestinal iatrogenic hyperadaptation in patients with short bowel syndrome and Crohn's disease: Is this an indication for mandatory lifelong injections of teduglutide?

Nutrition (Burbank, Los Angeles County, Calif.)
2021

Laparoscopic Management of Congenital Intestinal Obstruction: Duodenal Atresia and Small Bowel Atresia.

Journal of laparoendoscopic &amp; advanced surgical techniques. Part A
2021

Intestinal gangrene secondary to congenital transmesenteric hernia in a child misdiagnosed with gastrointestinal bleeding: A case report.

World journal of clinical cases
2022

Apraglutide, a novel glucagon-like peptide-2 analog, improves fluid absorption in patients with short bowel syndrome intestinal failure: Findings from a placebo-controlled, randomized phase 2 trial.

JPEN. Journal of parenteral and enteral nutrition
2021

Intestinal Microbiota in the SARS-CoV-2 Infection: What Is Known?

Advances in experimental medicine and biology
2021

Expression, purification and molecular dynamics simulation of extracellular domain of glucagon-like peptide-2 receptor linked to teduglutide.

International journal of biological macromolecules
2021

Operational tolerance after pediatric composite liver-pancreas-intestine transplantation following severe graft-versus-host disease.

Pediatric transplantation
2021

Can an amino acid mixture alleviate gastrointestinal symptoms in neuroendocrine tumor patients?

BMC cancer
2021

D-lactic acidosis presenting as metabolic encephalopathy in a patient with short bowel syndrome.

BMJ case reports
2021

Spinal column shortening for secondary tethered cord syndrome: radiographic, clinical, patient-reported, and urodynamic short-term outcomes.

Journal of neurosurgery. Pediatrics
2022

Evaluation of the fibrosis-4 index for detection of advanced fibrosis among individuals at risk for intestinal failure-associated liver disease.

JPEN. Journal of parenteral and enteral nutrition
2022

Cost-effectiveness of ethanol lock prophylaxis to prevent central line-associated bloodstream infections in children with intestinal failure in the United States.

JPEN. Journal of parenteral and enteral nutrition
2021

Challenge of diagnosing splenic torsion in a paediatric patient with gastroschisis.

BMJ case reports
2021

Secondary Kwashiorkor Disease in a Patient with Gastric Bypass Surgery and Short Gut Syndrome.

The American journal of case reports
2021

One-year Experience With Composite Intravenous Lipid Emulsion in Children on Home Parenteral Nutrition.

Journal of pediatric gastroenterology and nutrition
2020

The pathophysiology of bile acid diarrhoea: differences in the colonic microbiome, metabolome and bile acids.

Scientific reports
2020

A Novel Case of Carcinoid Tumor in a Pediatric Patient With Short Bowel Syndrome Secondary to Gastroschisis.

JPGN reports
2020

Prospective analysis of tumor spread to the small bowel mesentery in cases of right-sided colon cancer.

Langenbeck's archives of surgery
2020

Short Bowel Syndrome and Kidney Transplantation: Challenges, Outcomes, and the Use of Teduglutide.

Case reports in transplantation
2021

Clinical Manifestations of Copper Deficiency: A Case Report and Review of the Literature.

Nutrition in clinical practice : official publication of the American Society for Parenteral and Enteral Nutrition
2020

Effectiveness and safety of light vegetarian diet and Qingjiang Tiaochang Recipe for functional constipation: An exploratory study protocol for randomized controlled trial.

Medicine
2020

Relationship between volume and outcome for gastroschisis: a systematic review protocol.

Systematic reviews
2020

Bone mineral density and vitamin D in paediatric intestinal failure patients receiving home parenteral nutrition.

Clinical nutrition ESPEN
2021

De novo hepatocellular carcinoma 18 years after liver and small bowel transplantation in a one-year-old pediatric patient.

Pediatric transplantation
2021

Hypophosphatemia in a Specialized Intestinal Failure Unit: An Observational Cohort Study.

JPEN. Journal of parenteral and enteral nutrition
2021

Reversal of Intestinal Failure-Associated Liver Disease in an Infant Treated With Mixed Lipid Emulsion and Multidisciplinary Intestinal Rehabilitation Program.

JPEN. Journal of parenteral and enteral nutrition
2020

Differential Diagnosis and Management of Diarrhea in Patients with Neuroendocrine Tumors.

Journal of clinical medicine
2020

Outcome associated with EPCAM founder mutation c.499dup in Qatar.

European journal of medical genetics
2021

Fecal Microbiota Transplantation Reduces Symptoms in Some Patients With Irritable Bowel Syndrome With Predominant Abdominal Bloating: Short- and Long-term Results From a Placebo-Controlled Randomized Trial.

Gastroenterology
2020

The Effectiveness of Synbiotic Preparation Containing Lactobacillus and Bifidobacterium Probiotic Strains and Short Chain Fructooligosaccharides in Patients with Diarrhea Predominant Irritable Bowel Syndrome-A Randomized Double-Blind, Placebo-Controlled Study.

Nutrients
2020

New onset severe right ventricular failure associated with COVID-19 in a young infant without previous heart disease.

Cardiology in the young
2020

Complex Abdominal Wound Healing After Multivisceral Retransplant: A Case Report on the Importance of Nutrition.

Transplantation proceedings
2020

β-Galactooligosaccharide in Conjunction With Low FODMAP Diet Improves Irritable Bowel Syndrome Symptoms but Reduces Fecal Bifidobacteria.

The American journal of gastroenterology
2020

Phenome-Wide Analysis of Short- and Long-Run Disease Incidence Following Recurrent Pregnancy Loss Using Data From a 39-Year Period.

Journal of the American Heart Association
2020

Efficacy and Safety of Probiotics, Prebiotics and Synbiotics in the Treatment of Irritable Bowel Syndrome: A systematic review and meta-analysis.

Sultan Qaboos University medical journal
2019

[A Case of Unresectable Sigmoid Colon Cancer with Peritoneal Dissemination Treated with Chemotherapy after an Unintended Emergency Jejunostomy Formation].

Gan to kagaku ryoho. Cancer &amp; chemotherapy
2020

Choledochal cyst mimicker-When small bowel length matters.

International journal of surgery case reports
2020

Multidisciplinary Management in Pediatric Ultrashort Bowel Syndrome.

Journal of multidisciplinary healthcare
2020

Evaluation of Fibrosis in Intestinal Failure-Associated Liver Disease in the Sustain Registry.

JPEN. Journal of parenteral and enteral nutrition
2020

Understanding short bowel syndrome: Current status and future perspectives.

Digestive and liver disease : official journal of the Italian Society of Gastroenterology and the Italian Association for the Study of the Liver
2020

Review of the management of diarrhea syndrome after a bariatric surgery.

Endocrinologia, diabetes y nutricion
2019

Longer small bowel segments are resected in emergency surgery for ileocaecal Crohn's disease with a higher ileostomy and complication rate.

Techniques in coloproctology
2019

Persistent physical symptoms reduction intervention: a system change and evaluation in secondary care (PRINCE secondary) - a CBT-based transdiagnostic approach: study protocol for a randomised controlled trial.

BMC psychiatry
2019

Kidney After Intestinal Transplantation Using Two Different Living Donors: A First Case Report.

Transplantation proceedings
2019

Thiamine Deficiency in a Child with Short Bowel Syndrome and Review.

Pediatric gastroenterology, hepatology &amp; nutrition
2019

Homeopathy for treatment of irritable bowel syndrome.

The Cochrane database of systematic reviews
2019

A Rare Case of Primary Midgut Volvulus Necessitating Extensive Bowel Resection in an Adult.

Cureus
2019

Effects of a Cod Protein Hydrolysate Supplement on Symptoms, Gut Integrity Markers and Fecal Fermentation in Patients with Irritable Bowel Syndrome.

Nutrients
2019

Diazoxide for the Treatment of Hypoglycemia Resulting From Dumping Syndrome in a Child.

Journal of the Endocrine Society
2019

Towards a Rational and Efficient Diagnostic Approach in Children Referred for Growth Failure to the General Paediatrician.

Hormone research in paediatrics
2019

A case of intraductal papillary neoplasm of the bile duct that developed 38 years after choledochoduodenostomy with invasive adenocarcinoma and lymph node metastasis.

Surgical case reports
2019

"Understand your illness and your needs": Assessment-informed patient education for people with multiple functional somatic syndromes.

Patient education and counseling
2019

FXR agonist GW4064 improves liver and intestinal pathology and alters bile acid metabolism in rats undergoing small intestinal resection.

American journal of physiology. Gastrointestinal and liver physiology
2019

Lymphatic network remodeling after small bowel resection.

Journal of pediatric surgery
2019

Persistent fecal incontinence into adulthood after repair of anorectal malformations.

International journal of colorectal disease
2018

Transcutaneous electric nerve stimulation over acupoints for patients with diarrhea-predominant irritable bowel syndrome: Protocol for systematic review and meta-analysis.

Medicine
2019

Retracing our STEPs: Four decades of progress in intestinal lengthening procedures for short bowel syndrome.

American journal of surgery
2018

The Association of Nil Per Os (NPO) Days with Necrotizing Enterocolitis.

Gastroenterology research and practice
2018

Real-World, Non-Interventional, Observational Study to Evaluate Effectiveness and Tolerability of Acotiamide Hydrochloride Hydrate in Treatment of Functional Dyspepsia.

Advances in therapy
2018

Organization and outcomes of multidisciplinary intestinal failure teams.

Seminars in pediatric surgery
2019

Long-term Oncological and Functional Outcomes of Chemoradiotherapy Followed by Organ-Sparing Transanal Endoscopic Microsurgery for Distal Rectal Cancer: The CARTS Study.

JAMA surgery
2019

Association of spontaneous labor onset with neonatal outcomes in pregnancies with fetal gastroschisis: A retrospective cohort analysis.

Acta obstetricia et gynecologica Scandinavica
2018

Aloe vera Is Effective and Safe in Short-term Treatment of Irritable Bowel Syndrome: A Systematic Review and Meta-analysis.

Journal of neurogastroenterology and motility
2018

The Brain-Gut-Microbiome Axis.

Cellular and molecular gastroenterology and hepatology
2018

Endovascular Repair of Superior Mesenteric Arteriovenous Fistula Causing Early Mesenteric Steal Syndrome Following Abdominal Gunshot Injury.

EJVES short reports
2018

The Intestinotrophic Effects of Glucagon-Like Peptide-2 in Relation to Intestinal Neoplasia.

The Journal of clinical endocrinology and metabolism

Associações

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Comunidades

Grupos ativos de quem convive com esta doença aqui no Raras

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Doenças relacionadas

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Referências e fontes

Bases de dados externas citadas neste artigo

Publicações científicas

Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.

  1. The role of mediterranean diet and highly processed foods in inflammatory bowel diseases.
    Digestive and liver disease : official journal of the Italian Society of Gastroenterology and the Italian Association for the Study of the Liver· 2026· PMID 41765700mais citado
  2. Teduglutide use in haemodialysis-dependent renal failure from secondary hyperoxaluria in short bowel syndrome and type 3 intestinal failure - A case report.
    Intestinal Failure (New York, N.Y.)· 2026· PMID 41852601mais citado
  3. Spontaneous transanal evisceration of the small bowel through perforation of the sigmoid colon: a case report and new surgical approach.
    International journal of surgery case reports· 2026· PMID 41836970mais citado
  4. Case report: minimally invasive management of two major complications of colonic perforation and pseudoaneurysm formation following nephrostomy tube placement.
    The Canadian journal of urology· 2026· PMID 41800519mais citado
  5. Pilot trial: 8.4% sodium bicarbonate locks for infection prevention in pediatric intestinal failure.
    Nutrition in clinical practice : official publication of the American Society for Parenteral and Enteral Nutrition· 2026· PMID 41741971mais citado
  6. Pharmacokinetics and Safety of Single-Dose Apraglutide in Individuals with Normal and Impaired Hepatic Function: A Phase 1, Open-Label Trial.
    Clin Pharmacol Drug Dev· 2026· PMID 41545784recente
  7. Techniques and procedures for advancing feeds for children with intestinal failure due to short bowel syndrome: A narrative review.
    Nutr Clin Pract· 2025· PMID 40826818recente
  8. Outcomes of glepaglutide on intestinal absorption and parenteral support in patients with short bowel syndrome.
    Clin Nutr ESPEN· 2025· PMID 40774623recente
  9. Lactobacillus rhamnosus GG maintains gut microbiota stability and promotes intestinal adaptation via activated intestinal farnesoid X receptor signaling in short bowel syndrome.
    Commun Biol· 2025· PMID 40425822recente
  10. Clinical outcomes in Crohn's disease patients with short bowel syndrome on home parenteral nutrition are comparable to those with short bowel syndrome from other etiologies.
    Clin Nutr· 2025· PMID 40305998recente

Bases de dados e fontes oficiais

Identificadores e referências canônicas usadas para montar este verbete.

  1. ORPHA:95427(Orphanet)
  2. MONDO:0019802(MONDO)
  3. GARD:19258(GARD (NIH))
  4. Busca completa no PubMed(PubMed)
  5. Q55788882(Wikidata)

Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.

Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar

Síndrome do intestino curto secundário
Compêndio · Raras BR

Síndrome do intestino curto secundário

ORPHA:95427 · MONDO:0019802
Prevalência
Unknown
Herança
Not applicable
CID-10
K91.2 · Má-absorção pós-cirúrgica não classificada em outra parte
CID-11
Início
All ages
Prevalência
0.0 (Worldwide)
MedGen
UMLS
C5681579
Wikidata
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