Pênfigo foliáceo

Autoimmune Blistering Diseases Study

NCT02753777

RECRUTANDO

A Study to Assess the Long-term Safety and Efficacy of a Subcutaneous Formulation of Efgartigimod PH20 SC in Adults With Pemphigus (Vulgaris or Foliaceus)

NCT04598477

DESCONHECIDO

A Study to Assess the Efficacy and Safety of a Subcutaneous Formulation of Efgartigimod PH20 SC in Adults With Pemphigus (Vulgaris or Foliaceus)

NCT04598451

CONCLUÍDO

Polyclonal Regulatory T Cells (PolyTregs) for Pemphigus

NCT03239470

DESCONHECIDO

A Study of PRN1008 in Patients With Pemphigus

NCT03762265

DESCONHECIDO

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Outros ensaios clínicos

8 ensaios clínicos encontrados, 1 ativos.

Distribuição por fase

NCT04598477 · A Study to Assess the Long-term Safety and Efficacy of a Sub…Encerrado

PHASE3

NCT04598451 · A Study to Assess the Efficacy and Safety of a Subcutaneous …Concluído

PHASE3

NCT03239470 · Polyclonal Regulatory T Cells (PolyTregs) for PemphigusEncerrado

PHASE1

NCT03762265 · A Study of PRN1008 in Patients With PemphigusEncerrado

PHASE3

NCT04117529 · Phenotypic and Functional Characterisation of Human B-cell R…UNKNOWN

NA

NCT03334058 · A Study to Evaluate the Safety, PD, PK and Efficacy of ARGX-…Concluído

PHASE2

NCT03075904 · A Safety and Dose-Finding Study of SYNT001 in Subjects With …Encerrado

PHASE1, PHASE2

Ver todos no ClinicalTrials.gov

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Publicações mais relevantes

Timeline de publicações

606 papers (10 anos)

Mostrando amostra de 200 publicações de um total de 606

#1

Species-Level Comparative Metagenomic Analysis of the Bacterial Abundance of the Gut Microbiome in Psoriasis, Hidradenitis Suppurativa, and Pemphigus Foliaceous Patients Using Shotgun Next-Generation Sequencing.

International journal of molecular sciences2026 Jan 14

Recent studies have revealed a specific relationship between gut bacteria and inflammatory skin profiles. We aimed to perform a species-level comparative metagenomic analysis of the gut microbiome in patients with psoriasis, hidradenitis suppurativa (HS), and pemphigus foliaceus (PF). We included omnivorous nonsmokers and nondrinkers with psoriasis (n = 24), HS (n = 10), and PF (n = 11), as well as healthy controls (n = 10). We collected faecal samples from all patients for classic parasitological analysis. Gut microbiome analysis was conducted using shotgun next-generation sequencing. We used the Deseq2, Limma_voom, LinDA, and MaAMaAsLin 2 bioinformatics tools to evaluate concordance and differential abundance between patients. Thirteen patients (23.64%) were diagnosed with active intestinal parasitosis. The presence of intestinal parasitosis was significantly related to immunosuppression (p = 0.009). The most abundant microorganism species found in the faeces of the patients evaluated was Escherichia coli. Psoriasis patients presented a greater abundance of bacteria from the Veillonellaceae family, whereas PF patients presented a greater abundance of Firmicutes bacteria. Patients with PF showed increased E. coli virulence and antibiotic resistance functional markers. Immunosuppression significantly influenced the presence of intestinal parasitosis as well as increased the virulence of functional markers in patients with PF receiving systemic corticosteroid therapy.

#2

A Single-Center Profile of Pemphigus in China: Significant Diagnostic Delay and Evolving Treatment Patterns.

Clinical, cosmetic and investigational dermatology2026

Pemphigus encompasses a group of rare and potentially life-threatening autoimmune bullous diseases. Epidemiological research on pemphigus in China remains limited. This study aimed to analyze the clinical characteristics, diagnostic delay, and initial treatment patterns of patients with newly diagnosed pemphigus at a tertiary center in China. This retrospective study included patients newly diagnosed with pemphigus between January 2020 and December 2024 at the outpatient department of Peking Union Medical College Hospital. Demographic and clinical data were collected and analyzed. A total of 138 patients were included. Pemphigus vulgaris was the most prevalent subtype (68 cases, 49.3%), followed by pemphigus erythematosus (34 cases, 24.6%), pemphigus foliaceus (13 cases, 9.4%), and pemphigus herpetiformis (11 cases, 8.0%). Notably, the diagnostic delay was substantial, with a median of 5.0 (2.0-12.0) months, and 106 patients (76.8%) had been misdiagnosed before a definitive diagnosis was made. Regarding initial treatment, the most frequently used drugs were corticosteroids (104/132, 78.8%), followed by mycophenolate mofetil (33/132, 25.0%), Tripterygium wilfordii Hook F (29/132, 22.0%), minocycline (28/132, 21.2%), and rituximab (24/132, 18.2%). There was no significant difference among the subtypes in the proportion of patients receiving non-steroidal therapies. These findings highlight a significant diagnostic delay and outline evolving treatment patterns for pemphigus in a contemporary Chinese cohort. This information may inform future research directions and health policy decisions for managing this rare disease.

#3

Diagnostic Accuracy of Anti-Desmoglein 1 and 3 Antibodies by Enzyme-Linked Immunosorbent Assay (ELISA) in Pemphigus Vulgaris.

Journal of the College of Physicians and Surgeons--Pakistan : JCPSP2026 Jan

To determine the diagnostic accuracy of anti-Desmoglein 1 (Dsg1) and anti-Desmoglein 3 (Dsg3) antibodies detected by the enzyme-linked immunosorbent assay (ELISA) in clinically suspected cases of pemphigus vulgaris (PV). A cross-sectional study. Place and Duration of the Study: Department of Immunology, the Armed Forces Institute of Pathology, Rawalpindi, Pakistan, from July to December 2024. A total of 105 clinically suspected PV patients were enrolled using a non-probability consecutive sampling technique. Serum was analysed for the detection of Dsg1 and Dsg3 antibodies by the ELISA, with histopathology and direct immunofluorescence used as the reference methods for skin biopsy examination. The diagnostic accuracy of the ELISA was assessed through sensitivity, specificity, positive and negative predictive values, and Cohen's kappa statistics. A total of 105 clinically suspected cases, comprising 50 (47.6%) males and 55 (52.4%) females (male-to-female ratio 10:11), were included. PV was detected in 82 (78%) cases by both Immunofluorescence and histopathology, while 23 (22%) were diagnosed as other (non-PV). Among the PV, 70 (85.4%) were positive for both Dsg1 and Dsg3 antibodies, while 12 (14.6%) were negative. Anti-Dsg1 and 3 positivity was observed in 10 (9.5%) and 5 (4.7%) non-PV cases, respectively, diagnosed as pemphigus foliaceus and bullous pemphigoid. Both anti-Dsg1 and anti-Dsg3 yielded equal sensitivity of 85.4%; however, the specificity of anti-Dsg1 was lower (56.5%) than that of anti-Dsg3 (78.3%) antibodies. Both anti-Dsg1 and anti-Dsg3 antibodies detected by the ELISA demonstrated good sensitivity; the comparatively lower specificity of anti-Dsg1 antibodies, however, restricted its applicability in PV in resource-limited settings. Pemphigus vulgaris, Desmoglein1, Desmoglein3, Enzyme-linked immunosorbent assay, Sensitivity, Specificity, Immuno-fluorescence.

#4

Case Report: Pemphigus following COVID-19 mRNA vaccination: two cases achieving long-term remission without relapse.

Frontiers in immunology2026

Autoimmune blistering diseases (AIBDs) are mediated by autoantibodies targeting structural proteins of the epidermis or dermo-epidermal junction. Since the introduction of COVID-19 mRNA vaccines, isolated cases of pemphigus temporally associated with vaccination have been described, although causal relationships remain uncertain. We report two patients who developed pemphigus following COVID-19 mRNA vaccination and showed an exceptionally favorable clinical course. A 66-year-old man developed pemphigus foliaceus one week after his second vaccine dose, and a 45-year-old woman developed pemphigus vulgaris two months after her second dose. Both patients responded promptly to corticosteroid therapy, with normalization of autoantibody titers and achievement of long-term complete remission lasting over two years without relapse or maintenance therapy. These outcomes stand in contrast to sporadic pemphigus, which usually follows a chronic relapsing course, and suggest that vaccine-related pemphigus may, in rare instances, represent a transient and self-limited immune dysregulation. Such cases are exceptional and should not discourage COVID-19 vaccination.

#5

Correlation of platelet-related parameters and autoantibodies in patients with autoimmune bullous diseases.

Laboratory medicine2026 Feb 09

Autoimmune bullous diseases (AIBDs) are rare, tissue-specific autoimmune diseases of the skin, and corresponding autoantibodies have been proved to be pathogenic. Recently, we reported that variations in platelet-related parameters may reflect the fluctuations of circulating AIBD-correlated antibody titers during the disease progression of 1 patient with AIBD. The purpose of this article is to further investigate the possible correlation between autoantibody titers and platelet-related parameters in patients with AIBD. This study collected data on autoantibody titers and platelet-related parameters from 136 patients with bullous pemphigoid positive for anti-BP180 antibodies, 54 patients with pemphigus foliaceus positive for anti-desmoglein (Dsg) 1 antibody, 55 patients with pemphigus vulgaris positive for both anti-Dsg1 and Dsg3 antibodies, and 16 patients with pemphigus vulgaris positive for anti-Dsg3 antibody alone. Two groups of healthy individuals served as controls. Comparative analyses revealed clinically significantly elevated platelet-related parameters, such as platelet count and thrombocytocrit, in the autoantibody-positive patient groups relative to control individuals. Correlation analyses demonstrated statistically significant positive associations between autoantibody titers and specific platelet-related parameters. These findings represent the first documented evidence of a positive correlation between autoantibody titers and platelet-related parameters in patients with AIBDs. The data implied that platelets may contribute to the disease pathophysiology and progression of AIBDs.

Publicações recentes

Long-Term Use of Oclacitinib Maleate for the Management of Pemphigus Foliaceus in a Miniature Donkey.

Vet Dermatol2026 Apr 10

Pemphigus Foliaceus. Reply.

N Engl J Med2026 Apr 2

Pemphigus Foliaceus in Skin of Color: A Challenging Clinical-Pathological Correlation.

Dermatol Pract Concept2026 Jan 30

Ver todas no PubMed

📚 EuropePMC985 artigos no totalmostrando 194

Clinical, cosmetic and investigational dermatology

A Single-Center Profile of Pemphigus in China: Significant Diagnostic Delay and Evolving Treatment Patterns.

Acta dermatovenerologica Croatica : ADC

What has Better Diagnostic Accuracy in Pemphigus? Direct Immunofluorescence of Plucked Hair, Oral Scrapes or Tzanck Smears!

Journal of the College of Physicians and Surgeons--Pakistan : JCPSP

Diagnostic Accuracy of Anti-Desmoglein 1 and 3 Antibodies by Enzyme-Linked Immunosorbent Assay (ELISA) in Pemphigus Vulgaris.

Case Report: Pemphigus following COVID-19 mRNA vaccination: two cases achieving long-term remission without relapse.

Correlation of platelet-related parameters and autoantibodies in patients with autoimmune bullous diseases.

Laboratory medicine

Pemphigus Foliaceus Mimicking Erythema Annulare Centrifugum: A Case Report.

A rare case of peristomal pemphigus foliaceus: possible involvement of the Koebner phenomenon.

International journal of molecular sciences

Species-Level Comparative Metagenomic Analysis of the Bacterial Abundance of the Gut Microbiome in Psoriasis, Hidradenitis Suppurativa, and Pemphigus Foliaceous Patients Using Shotgun Next-Generation Sequencing.

Dermatology (Basel, Switzerland)

Clinical Phenotype Transition in Pemphigus May Suggest Undertreatment with Rituximab: Findings from a Retrospective Single-Centre Analysis of Relapsed Patients.

Pemphigus foliaceus transforming to pemphigus vulgaris: a case report.

Comparing the genetic and serum expression of LL-37 Antimicrobial Peptide in pemphigus vulgaris and pemphigus foliaceus patients.

Localized nasal dermatosis in a healthy male.

B-cell-activating factor and A proliferation-inducing ligand (BAFF/APRIL) blockade with telitacicept in pemphigus foliaceus: two cases.

American journal of clinical dermatology

Emerging Treatments in Pemphigus: Is Healing an Achievable Goal?

Clinical correlation of anti-desmoglein antibody dynamics in pemphigus treated with rituximab.

Atypical Case of Pemphigus Erythematosus in a Previously Healthy Young Woman: Diagnostic Delay and Response to Rituximab.

An atypical case of pemphigus herpetiformis with erythroderma.

Successful Treatment of Refractory Severe Pemphigus With Telitacicept as Adjunctive Therapy: Two Case Reports.

Role of protein kinase C subtype-specific signalling in regulating adhesion in human keratinocytes and skin in pemphigus.

Autoantibodies against Components of Sensory Nerve Formations in the Intervertebral Disks and Adjacent Structures are Antigens Recognized by the Sera from Patients Affected by a New Variant of Endemic Pemphigus in El Bagre, Colombia.

Journal of dermatological science

Bead aggregation assays with desmoglein and desmocollin for the evaluation of disease activity in pemphigus.

Journal of clinical medicine

Eight Years of Follow-Up of Rituximab in Pemphigus Vulgaris and Foliaceus at a Single Center: Assessing Efficacy and Safety in Light of Several Factors.

Pemphigus Foliaceous With Secondary Herpes Simplex Infection.

JAMA dermatology

Introducing human 3D skin models as a new serological diagnostic tool for severe autoimmune bullous diseases.

Hypocomplementemic paraneoplastic vasculitis: a rare case of B-cell malignancy.

ARP rheumatology

Journal of the American Academy of Dermatology

Comparing combination and single-agent therapy for the treatment of pemphigus: A retrospective cohort study.

Anti-contactin-1 autoimmune nodopathy with thymoma: case report and literature review.

A case of erythrodermic pemphigus foliaceus and bullous pemphigoid.

Clinical and experimental dermatology

Clinico-demographic characteristics of pemphigus foliaceus: Retrospective analysis of clinic-based data of 103 patients in a non-endemic location.

Pemphigus Foliaceus in a Patient With Pre-existing Atopic Dermatitis: A Case Report.

Successful Treatment of Pemphigus Foliaceus With Dupilumab: A Case Report.

Post translational Modifications and Protein-Protein Interactome of Endemic Pemphigus in El Bagre, Colombia: A New Variant Analysis.

A Clinico-Epidemiological Study of Various Autoimmune Vesiculobullous Disorders in a Tertiary Care Center.

Correlation of Antimuscarinic Acetylcholine Receptor Antibody Titers With Pemphigus Disease Activity at Baseline and Following Phase I Pulse Therapy.

Drug-Induced Pemphigus Foliaceus Potentially Triggered by Piperacillin-Tazobactam, Linezolid, and Additional Factors: A Report of a Rare Case.

Rilzabrutinib-induced transition from pemphigus vulgaris to pemphigus foliaceous: a case report and literature review.

Dermatology reports

Echoes of infection: radial EBUS unveils invasive pulmonary aspergillosis.

BMJ case reports

A Multimodal Approach to Diagnosis of Immunobullous Diseases: Integrating Clinical, Histopathological, and Immunofluorescence Findings.

Inflammation research : official journal of the European Histamine Research Society ... [et al.]

Successful treatment of refractory erythrodermic pemphigus foliaceus with low-dose rituximab and intravenous immunoglobulin.

The Multikinase Inhibitor Midostaurin Mitigates Loss of Intercellular Adhesion and Skin Blistering in Pemphigus Vulgaris.

Is Tunisian Endemic Pemphigus Foliaceus A Real Entity, Or Should These Cases Be Reclassified With Other Autoimmune Blistering Disease?

Evaluation of the efficacy and safety of dapsone alone or associated with topical corticosteroids for pemphigus foliaceus: a retrospective multicentre study.

Journal of the American Academy of Dermatology

Efficacy, safety, and B-cell depletion capacity of 3 rituximab dosing regimens in the treatment of moderate-to-severe pemphigus vulgaris and pemphigus foliaceus: A 52-week clinical trial.

Diagnostics (Basel, Switzerland)

The Pericardium Cells Junctions Are a Target for Autoantibodies of Patients Affected by a Variant of Endemic Pemphigus Foliaceus in El Bagre and Surrounding Municipalities in Colombia, South America.

Outcome measurement in pemphigus clinical research: a scoping review on heterogeneity in outcome reporting and definitions.

Journal of inflammation research

Oral Prednisolone, Apremilast and Human Umbilical Cord Mesenchymal Stem Cells in the Management of Pemphigus Foliaceus.

Clinical outcomes and prognostic factors of pemphigus vulgaris and pemphigus foliaceus: A 20-year retrospective study.

Chinese medical journal

Interleukin (IL)-34 promotes the inflammatory role of IL-1β-producing myeloid cells in pemphigus lesions.

International immunopharmacology

MicroRNAs in patients with pemphigus: A systematic review.

Successful management of pemphigus foliaceus with mycophenolate mofetil as a steroid-sparing agent in a cat with corticosteroid-associated congestive heart failure.

JFMS open reports

Trichoscopy of Pemphigus Vulgaris and Foliaceus on Black Scalp.

Skin appendage disorders

Brazilian journal of veterinary medicine

Use of Oclacitinib in the treatment of pemphigus foliaceus in a dog: case report.

Evaluation of the Effects of systemic Therapy on Inflammatory Markers and Disease Severity in Patients with Pemphigus.

Persistent Nasal Skin Lesions in Pemphigus Patients and the Role of Methotrexate in Treatment: A Case Series Study.

Prurigo nodularis imitators unmasked.

Clinics in dermatology

Archives of Iranian medicine

Mortality Rates Among Individuals Diagnosed with Pemphigus: 12-Year Experience in Tehran, Iran.

Acta dermato-venereologica

Clinical Features, Diagnosis and Treatment of Different Types of Paediatric Pemphigus.

Pediatric Dermatology, Pruritic Annular Vesiculobullous Plaques in a 10-Year-Old Female.

Pediatric dermatology

Long-Term Efficacy and Safety of Rituximab in Patients With Pemphigus Foliaceus Compared With Pemphigus Vulgaris.

JAMA dermatology

Comparability of Randomized Controlled Trials Evaluating Pharmacological Interventions for Pemphigus Vulgaris and Pemphigus Foliaceus: A Systematic Mapping Review.

Advances in therapy

Archives of dermatological research

Distinct anti-microbial peptides expression patterns and microbiome profiles in skin of Tunisian endemic Pemphigus foliaceus patients.

Life (Basel, Switzerland)

Localization of Lesions in Autoimmune Blistering Diseases Is Independent of Site-Specific Target Antigen Expression.

Prevalence and pathogenic activity of anti-desmocollin-3 antibodies in patients with pemphigus vulgaris and pemphigus foliaceus.

Archives of dermatological research

Exploring the role of glucocorticoid receptors and co-chaperones in Pemphigus foliaceus stratification.

Optimizing Pemphigus Management With Rituximab and Short-Term Relapse Predictors.

JAMA dermatology

Journal of clinical medicine

Senear-Usher Syndrome or Coexistence of SLE with Pemphigus Vulgaris-A Case Report with Literature Review.

The American Journal of dermatopathology

Immunohistochemistry for Immunoglobulin G4 on Paraffin Sections as a Diagnostic Test for Pemphigus.

Indian dermatology online journal

Consensus Based Indian Guidelines for the Management of Pemphigus Vulgaris and Pemphigus Foliaceous.

Improvement of acute phase symptoms of pemphigus foliaceus with spesolimab.

Pemphigus and Bullous Pemphigoid Following COVID-19 Vaccination: A Systematic Review.

Viruses

Pemphigus Foliaceus Mimicking Ichthyosis: A Rare Clinical Presentation.

Dermatopathology (Basel, Switzerland)

Potential Pitfalls of IgG4 Immunohistochemical Staining on Lesional Tissue in Cutaneous Acantholytic Disorders.

Antibodies (Basel, Switzerland)

Clinical Characteristics, Comorbidities, and Treatment in Patients with Pemphigus-A Single-Center Retrospective Study.

The Veterinary clinics of North America. Small animal practice

Canine and Feline Pemphigus Foliaceus-an Update on Pathogenesis and Treatment.

Clinical, cosmetic and investigational dermatology

Coexistence of Pemphigus Foliaceus and Bullous Pemphigoid: A Case Report.

A Case of Recurrent Pemphigus Foliaceus Following Noncompliance to Medication.

Clinical case reports

Journal of the European Academy of Dermatology and Venereology : JEADV

Treatment of pemphigus foliaceus with upadacitinib.

A case of rapidly progressive hair loss due to azathioprine, and the prevalence of NUDT15 variants among Japanese patients with autoimmune blistering diseases: A single-center retrospective observational study.

Pemphigus relapse: Mechanisms, risk factors, and agents associated with disease recurrence.

A rare case of radiation-induced pemphigus foliaceus in a 70-year-old female.

SAGE open medical case reports

Localized facial pemphigus foliaceus presenting in a dermatomal distribution: A case report.

New complex cell junctions in and around the intervertebral discs discovered using autoantibodies from patients affected by endemic pemphigus foliaceus in El Bagre, Colombia, South America.

A Comprehensive Review on the Intricate Interplay between COVID-19 Immunization and the New Onset of Pemphigus Foliaceus.

Vaccines

Medicina (Kaunas, Lithuania)

Dapsone as a Current Option for the Treatment of Autoimmune Bullous Diseases with Autoimmunity to Non-Enzymes: A Retrospective Study from a Single Central European Referral Center.

Advances in rheumatology (London, England)

Targeting Bruton's tyrosine kinase (BTK) as a signaling pathway in immune-mediated diseases: from molecular mechanisms to leading treatments.

Case report: Managing pemphigus foliaceus using apremilast without systemic glucocorticosteroids or immunosuppressive agents.

A 3-year-old child with multiple superficial erosions and yellowish crusts on the scalp and seborrheic areas.

Radiotherapy-induced pemphigus foliaceus successfully treated with rituximab.

Immunohistopathological analyses of a case of pemphigus vegetans with antibodies against desmoglein 1 and desmocollins 1-3.

Clinical and experimental dermatology

Pemphigus foliaceus: a patient's perspective.

Establishing minimal clinically important differences for the Pemphigus Disease Area Index.

Serum interleukin-6 concentration in patients with pemphigus.

Dermatology reports

A Case Report on Senear-Usher Syndrome.

Journal of the European Academy of Dermatology and Venereology : JEADV

Pemphigus foliaceus successfully treated with upadacitinib.

Current molecular medicine

CD4+ T-cell Subsets and Cytokine Signature in Pemphigus Foliaceus Clinical Stratification beyond the th1/Th2 Paradigm.

State-of-the-art diagnosis of autoimmune blistering diseases.

Comparative study of efficacy and safety: Biosimilar rituximab versus originator rituximab in the treatment of pemphigus.

Factors associated with non-pathogenic antibodies against desmoglein-3 in pemphigus foliaceus.

Comparison of selected cytomorphological features of canine pemphigus foliaceus and superficial pyoderma.

The Veterinary clinics of North America. Equine practice

Autoimmune Dermatopathies of Horses.

Veterinary immunology and immunopathology

Re-evaluating the prevalence of anti-desmocollin-1 IgA autoantibodies in canine pemphigus foliaceus.

Diagnosis, treatment, and long-term outcomes of pediatric pemphigus: a retrospective study at tertiary medical centers.

Seborrheic Pemphigus: A Misunderstood Variant of Pemphigus Foliaceus.

New Onset and Exacerbation of Autoimmune Bullous Dermatosis Following COVID-19 Vaccination: A Systematic Review.

Vaccines

Clinical and experimental medicine

Epidemiology of malignant tumors in patients with pemphigus: an analysis of trends from 1955 to 2021.

The Journal of the Association of Physicians of India

Early Gestational Diabetes Mellitus: An Update.

The Journal of the Association of Physicians of India

Inappropriate Use of Steroids in Superficial Dermatophytosis: An Uncommon Case of Erythroderma.

Molecular biology reports

PDE4D and miR-203 are promising biomarkers for canine atopic dermatitis.

Superficial erosions in a pediatric patient.

Pediatric dermatology

The evolution of Pemphigus publications: A bibliometric analysis with research trends and global productivity.

Medicine

Onychoscopic Analysis of Cyclophosphamide-Induced Polydactylic Bluish-Gray Discoloration in a Case of Pemphigus Foliaceus.

EGFR Inhibition by Erlotinib Rescues Desmosome Ultrastructure and Keratin Anchorage and Protects against Pemphigus Vulgaris IgG-Induced Acantholysis in Human Epidermis.

Effectiveness and safety of immunoadsorption in the treatment of pemphigus vulgaris and pemphigus foliaceus.

COVID-19-associated pemphigus foliaceus exacerbated by toll-like receptor 7 agonist.

Dermatopathology (Basel, Switzerland)

Claudin-4 Upregulation in Acantholytic and Autoimmune-Mediated Bullous Disorders.

The Prevalence of Clinically Undiagnosed Depression in Patients With Autoimmune Bullous Diseases Seen at Inkosi Albert Luthuli Central Hospital, Durban, South Africa.

Efficacy and Safety of Rilzabrutinib in Pemphigus: PEGASUS Phase 3 Randomized Study.

Dermatology online journal

Red crusty plaques in a young man.

Eye and lid involvement as an uncommon feature of pemphigus foliaceus in a pediatric patient.

Pediatric dermatology

The Canadian veterinary journal = La revue veterinaire canadienne

Pemphigus foliaceus in cats.

Telemedicine journal and e-health : the official journal of the American Telemedicine Association

Evaluation of the Status of Patients with Autoimmune Bullous Diseases (Pemphigus and Bullous Pemphigoids) in Dermatology Clinics of Mashhad University of Medical Sciences During the COVID-19 Pandemic Using Telemedicine.

Case reports in dermatological medicine

Sporadic Pemphigus Foliaceus in a 3-Year-Old Vietnamese Girl: A Case Report and Literature Review.

Medicina (Kaunas, Lithuania)

Rituximab in the Management of Autoimmune Bullous Diseases: A Treatment-Resistant Case Series from a Single Central European Referral Center.

Microarray Gene Expression Analysis of Lesional Skin in Canine Pemphigus Foliaceus.

Veterinary sciences

Putative pemphigus-like reaction to oral fluralaner in a dog.

Desmoglein autoantibodies and disease severity in pemphigus patients - correlations and discrepancies.

Folia medica

Intractable pemphigus foliaceus after COVID-19 mRNA vaccination.

Clinical reviews in allergy & immunology

A Global View of Pemphigus: Geographical Variations.

HLA inherence as a potential parameter in checkpoint inhibitor-associated autoimmune adverse event assessment.

Life (Basel, Switzerland)

Genetic Association and Differential RNA Expression of Histone (De)Acetylation-Related Genes in Pemphigus Foliaceus-A Possible Epigenetic Effect in the Autoimmune Response.

Journal of the European Academy of Dermatology and Venereology : JEADV

De novo pemphigus vulgaris and pemphigus foliaceus development following COVID-19 infection and vaccination: Matched case-control study.

Efficacy and safety of adjuvant immunoadsorption in pemphigus vulgaris and pemphigus foliaceus (IA-Pem Study): a multicentre randomized controlled trial.

From the Cochrane Library: Interventions for Pemphigus Vulgaris and Pemphigus Foliaceus.

JMIR dermatology

The realistic positioning of UVA1 phototherapy after 25 years of clinical experience and the availability of new biologics and small molecules: a retrospective clinical study.

Pemphigus Foliaceus Possibly Associated with Excessive Intake of Spirulina.

Annals of dermatology

Efficacy of therapeutic plasma exchange in a case of severe, generalised canine pemphigus foliaceus.

Novel use of dupilumab in pemphigus vulgaris and pemphigus foliaceus.

A Recalcitrant Case of Senear-Usher Syndrome Treated With Rituximab.

Dermatologie (Heidelberg, Germany)

[Trigger factors associated with bullous autoimmune dermatoses].

Dermatologie (Heidelberg, Germany)

[Pemphigus: current and future treatment strategies].

Current biologics in treatment of pemphigus foliaceus: a systematic review.

Case reports in dermatological medicine

Pemphigus Foliaceus after COVID-19 Vaccination: A Report of Two Cases.

Retrospective analysis of autoimmune bullous diseases in Middle Franconia.

The Australasian journal of dermatology

A case of cytomegalovirus-induced haemorrhagic cystitis during treatment of pemphigus foliaceus with corticosteroids and azathioprine.

Raccoon eyes sign in pemphigus foliaceus.

Differential FCGR2A and FCGR3A Alleles/Genotypes in Pemphigus Vulgaris and Pemphigus Foliaceus in Southeastern Brazil.

Epidemiological and clinical study of cases of endemic pemphigus foliaceus and pemphigus vulgaris in a reference center in the state of Minas Gerais, Brazil.

Treatment of Pediatric Pemphigus Foliaceus.

Journal of medical case reports

Autoimmune bullous disorder flares following severe acute respiratory syndrome coronavirus 2 vaccination: a case series.

Successful treatment of erythrodermic pemphigus foliaceus with intravenous immunoglobulin.

The use of oclacitinib compared to azathioprine in the management of canine pemphigus foliaceus: A retrospective analysis.

Journal of cutaneous pathology

Correlation of desmoglein 1 and 3 immunohistochemistry with autoantibody levels and clinical severity in pemphigus.

The landscape of the immunoglobulin repertoire in endemic pemphigus foliaceus.

Journal of drugs in dermatology : JDD

Juvenile Pemphigus Foliaceus in a Patient With Psoriasis Receiving Narrow-Band Ultraviolet-B: Successful Treatment With Rituximab.

Journal of translational autoimmunity

Ultrastructural skin alterations of healthy subjects with anti-desmoglein 1 antibodies in endemic areas to pemphigus foliaceus: A case series.

Medicina (Kaunas, Lithuania)

Intravenous Immunoglobulin for Autoimmune Bullous Diseases: A Case Series from a Central European Referral Center.

Two cases of cutaneous-type pemphigus vulgaris and a case of pemphigus foliaceus without mucosal involvement despite high anti-desmoglein 3 autoantibody levels.

Veterinary immunology and immunopathology

Characterization of the serum and skin inflammatory profile in canine pemphigus foliaceus using multiplex assay and quantitative real-time polymerase chain reaction (qRT-PCR).

Pemphigus foliaceus complicated with Listeria monocytogenes infection and meningitis.

Skin-infiltrating T cells display distinct inflammatory signatures in lichen planus, bullous pemphigoid and pemphigus vulgaris.

Is transition between subtypes of pemphigus possible? A series of pemphigus vulgaris patients showing the transition to pemphigus foliaceus.

Dexamethasone-cyclophosphamide pulse therapy outcomes comparing pemphigus vulgaris and pemphigus foliaceus groups in a Brazilian cohort study.

Journal der Deutschen Dermatologischen Gesellschaft = Journal of the German Society of Dermatology : JDDG

Transformation eines Pemphigus foliaceus in einen Pemphigus herpetiformis.

Journal of medical virology

New-onset pemphigus foliaceus after COVID-19 infection.

The American Journal of dermatopathology

Persistent Symmetrical Erythema and Scaling of the Face and Scalp: Pemphigus Foliaceus: Answer.

Journal of the European Academy of Dermatology and Venereology : JEADV

New-onset pemphigus vulgaris and pemphigus foliaceus following COVID-19 infection and vaccination, systematic review of case reports and a causal hypothesis.

Histopathological characterisation of trunk-dominant canine pemphigus foliaceus, and comparison with classic facial and insecticide-triggered forms.

Measurement of pesticides in hair samples from pemphigus foliaceus and pemphigus vulgaris patients in Southeastern Brazil.

Clinical, cosmetic and investigational dermatology

Direct Immunofluorescence of IgG on Formalin-Fixed Paraffin-Embedded Tissue by Heat-Induced Antigen Retrieval as a Sensitive Method for the Diagnosis of Pemphigus.

Indian journal of dermatology

Localized Pemphigus Foliaceus: Diverse Presentations, Treatment, and Review of the Literature.

Dsg3 epitope-specific signalling in pemphigus.

Journal der Deutschen Dermatologischen Gesellschaft = Journal of the German Society of Dermatology : JDDG

Pemphigus foliaceus transforming into pemphigus herpetiformis.

miRNA implication in the pathogenesis and the outcome of Tunisian endemic pemphigus foliaceus.

Experimental dermatology

Case report: Dermatosis neglecta mimicking pemphigus foliaceus in association with obsessive-compulsive disorder.

Desmoglein-Specific B-Cell-Targeted Single-Cell Analysis Revealing Unique Gene Regulation in Patients with Pemphigus.

Dermoscopic approach for differential diagnosing of autoimmune bullous disease: pemphigus vulgaris, pemphigus foliaceus, and IgA pemphigus.

Case reports in dermatology

Six Cases of Erythrodermic Pemphigus Foliaceus: A Case Report.

Dermatopathology (Basel, Switzerland)

Post-Pemphigus Acanthomata Presenting as an Isolated, Hyperkeratotic Plaque.

Human vaccines & immunotherapeutics

The complicated use of dupilumab in the treatment of atypical generalized pemphigus Erythematous: A report of two cases.

Journal of cutaneous pathology

Lymphocyte-predominant lesional inflammatory infiltrates of the skin are associated with mucosal-dominant phenotype in pemphigus.

IL-31 and IL-31 receptor alpha in pemphigus: Contributors to more than just itch?

T cell autoimmunity and immune regulation to desmoglein 3, a pemphigus autoantigen.

Subtype transition from pemphigus vulgaris to pemphigus foliaceus.

Clinical course and outcomes of pemphigus vulgaris and foliaceus: A retrospective study using a nationwide database in Japan.

Molecular genetics & genomic medicine

Evaluation of X chromosome inactivation in endemic Tunisian pemphigus foliaceus.

Indian dermatology online journal

Rituximab in Pemphigus - An Observational Study from a Tertiary Care Center of North India.

Clinical manifestations and comorbidities of pemphigus: a retrospective case-control study in southern Finland.

Desmoglein compensation hypothesis fidelity assessment in Pemphigus.

Rituximab therapy for intractable pemphigus: A multicenter, open-label, single-arm, prospective study of 20 Japanese patients.

Case report: Documentation of cutaneous only pemphigus vulgaris without history of mucosal lesions in North America.

Frontiers in veterinary science

Case report: Uncommon immune-mediated skin disease involving systemic disorders in dogs.

Two cases with new onset of pemphigus foliaceus after SARS-CoV-2 vaccination.

Dermatologic therapy

New onset of pemphigus foliaceus following BBIBP COVID-19 vaccine.

Dermatologic therapy

Anti-desmoglein 1 antibody-positive mother and antibody-negative child with Darier's disease.

Ver todos os 985 no EuropePMC

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