A poliarterite nodosa (PAN) é uma doença reumatológica rara, com sintomas variados, caracterizada por lesões inflamatórias que destroem o tecido e afetam os vasos sanguíneos pequenos e médios. A PAN afeta mais comumente a pele, as articulações, os nervos periféricos, o intestino e os rins.
Introdução
O que você precisa saber de cara
A poliarterite nodosa (PAN) é uma doença reumatológica rara, com sintomas variados, caracterizada por lesões inflamatórias que destroem o tecido e afetam os vasos sanguíneos pequenos e médios. A PAN afeta mais comumente a pele, as articulações, os nervos periféricos, o intestino e os rins.
Escala de raridade
<1/50kMuito rara
1/20kRara
1/10kPouco freq.
1/5kIncomum
1/2k
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Entender a doença
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Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Partes do corpo afetadas
+ 11 sintomas em outras categorias
Características mais comuns
Os sintomas variam de pessoa para pessoa. Abaixo estão as 28 características clínicas mais associadas, ordenadas por frequência.
Linha do tempo da pesquisa
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Genética e causas
O que está alterado no DNA e como passa nas famílias
Nenhum gene associado encontrado
Os dados genéticos desta condição ainda estão sendo catalogados.
Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
Remédios, cuidados de apoio e o que precisa acompanhar
Onde tratar no SUS
Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)
🇧🇷 Atendimento SUS — Poliarterite nodosa
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Publicações mais relevantes
Mostrando amostra de 200 publicações de um total de 956
Systemic Arterial Aneurysms With Limb Ischemia in a 3-Month-Old Infant: An Unusual Presentation of Incomplete Kawasaki Disease.
Kawasaki disease (KD) is an acute systemic vasculitis predominantly affecting children under 5 years old, characterized by inflammation of medium-sized arteries. The most serious complication is the development of coronary artery aneurysms (CAAs), which can lead to significant cardiovascular morbidity and mortality. Although coronary artery aneurysms (CAAs) are well-documented in KD, the occurrence of systemic arterial aneurysms (SAAs) is rare and less understood. This report describes a 3-month-old male infant with probable/incomplete Kawasaki disease (KD), who presented with bilateral lower limb ischemia due to multiple systemic arterial aneurysms (SAAs) and coronary involvement. Treatment with intravenous immunoglobulin (IVIG) and aspirin led to clinical improvement. This case emphasizes the importance of recognizing incomplete forms of KD and considering differential diagnoses such as infantile polyarteritis nodosa and MIS-C.
Hypertensive crisis due to secondary aldosteronism from polyarteritis nodosa.
Primary aldosteronism is common in those diagnosed with hypertension and distinguishing primary aldosteronism from its mimics allows tailored management. A woman in her 30s presented to an Australian hospital with hypertensive crisis (209/100 mm Hg) and spontaneous hypokalaemia (2.9 mmol/L). Laboratory tests revealed hyperreninaemic hyperaldosteronism with a normal aldosterone-renin ratio. CT imaging showed focal areas of soft tissue encasement and enhancement surrounding multiple arteries, including the left renal artery, raising suspicion of a medium-vessel vasculitis. Further investigation led to a final diagnosis of polyarteritis nodosa with secondary aldosteronism.
Think Out of the Box-A Rare Case of Intestinal Polyarteritis Nodosa.
Systemic Necrotizing Medium-Vessel Vasculitis Clinically Consistent With Polyarteritis Nodosa: A Detailed Case Report.
Polyarteritis nodosa (PAN) is a rare necrotizing vasculitis of medium-sized arteries presenting with heterogeneous multisystem involvement. Diagnosis is challenging due to the absence of specific biomarkers, frequent anti-neutrophil cytoplasmic antibodies (ANCA) negativity, variable early imaging findings, and low diagnostic yield of superficial biopsies. We report the case of a 33-year-old man experiencing a four-month evolution of recurrent inflammatory episodes involving abdominal, neurological, cutaneous, and cardiopulmonary systems. He developed dusky necrotizing vasculitic lesions, mononeuritis multiplex-type neuropathy, constitutional symptoms, markedly elevated inflammatory markers, and demonstrated a dramatic response to corticosteroid therapy. Computed tomography angiography was normal, and a superficial punch biopsy performed after steroid initiation was nondiagnostic, reflecting known limitations of sampling depth and timing. Despite this, clinical features, disease trajectory, exclusion of alternative vasculitides, and classical steroid responsiveness strongly supported systemic PAN. This case highlights the diagnostic limitations of biopsy and imaging in early PAN and emphasizes the need for clinical judgment and timely treatment.
Clinical manifestations, prognostic impact, and relapse in polyarteritis nodosa: a systematic review and meta-analysis.
Polyarteritis Nodosa is a rare necrotizing vasculitis with a broad and variable clinical presentation, driven by its ability to affect multiple organs and systems. This heterogeneity influences disease severity, relapse risk, and mortality, highlighting the prognostic importance of its diverse manifestations. This systematic review and meta-analysis synthesize the available evidence to define the clinical profile of Polyarteritis Nodosa and highlight key prognostic factors. A systematic search of electronic databases was conducted to identify studies reporting clinical manifestations and outcomes of patients diagnosed with Polyarteritis Nodosa. Pooled prevalence summary estimates were calculated using R software, including subgroup analyses by age group. Case Fatality Rate was calculated to determine the clinical severity of the manifestations. Across adult and pediatric groups, the most common manifestations were fever (~ 52%), myalgia (~ 53%), and cutaneous involvement (~ 56%). Age significantly moderated the prevalence of fever, arthralgia, hypertension, and peripheral neuropathy. Several symptoms were frequently observed among patients who experienced relapse, particularly cutaneous involvement (~ 66%) and myalgia (~ 64%). While cardiac involvement was associated with higher case fatality, gastrointestinal manifestations accounted for a greater proportion of reported deaths overall. Total mortality was approximately 13%, relapse occurred in about 27% of patients, while roughly 65% of patients achieved remission. This systematic review with meta-analysis provides crucial information to clinical physicians, regarding the clinical profile and the prognostic factors of Polyarteritis Nodosa. Thus, these insights could guide management strategies and increase the survival and remission rate of these patients. PROSPERO: https://www.crd.york.ac.uk/PROSPERO/view/CRD420251249274. The online version contains supplementary material available at 10.1007/s00296-026-06082-8.
Publicações recentes
[(18)F]FDG PET/CT value in the diagnostic evaluation of patients with polyarteritis nodosa.
Catastrophic Brain Hemorrhage in a Teenager With Immune Thrombocytopenia and Polyarteritis Nodosa.
Paraneoplastic necrotizing medium-vessel vasculitis mimicking polyarteritis nodosa with large-vessel involvement.
Myeloperoxidase anti-neutrophil cytoplasmic antibody vasculitis mimicking renal polyarteritis nodosa.
[Polyarteritis nodosa: an etiology of myelitis that should not be ignored in subsaharansub-Saharan Africa].
📚 EuropePMC2.134 artigos no totalmostrando 195
Myeloperoxidase anti-neutrophil cytoplasmic antibody vasculitis mimicking renal polyarteritis nodosa.
Journal of nephrology[Polyarteritis nodosa: an etiology of myelitis that should not be ignored in subsaharansub-Saharan Africa].
Medecine tropicale et sante internationaleSystemic Necrotizing Medium-Vessel Vasculitis Clinically Consistent With Polyarteritis Nodosa: A Detailed Case Report.
CureusClinical manifestations, prognostic impact, and relapse in polyarteritis nodosa: a systematic review and meta-analysis.
Rheumatology internationalDrug-induced renal function deterioration in a patient with polyarteritis nodosa.
Farmaceuticos comunitariosSystemic Arterial Aneurysms With Limb Ischemia in a 3-Month-Old Infant: An Unusual Presentation of Incomplete Kawasaki Disease.
Sage open pediatricsMaternal and perinatal outcomes in vasculitis: a 15-year study at a Portuguese tertiary multidisciplinary centre.
Rheumatology advances in practiceTherapeutic management of inflammatory heart diseases.
Pharmacology & therapeuticsNavigating clinical overlap: A case of polyarteritis nodosa in the setting of antiphospholipid syndrome.
Modern rheumatology case reportsSuccessful treatment of aneurysmal subarachnoid hemorrhage in polyarteritis nodosa with immunosuppressive therapy: illustrative case.
Journal of neurosurgery. Case lessonsPolyarteritis nodosa with isolated organ involvement requiring resection in the genitourinary system.
Annals of diagnostic pathologyHypertensive crisis due to secondary aldosteronism from polyarteritis nodosa.
BMJ case reportsBilateral spontaneous kidney rupture in a patient with polyarteritis nodosa disguising as granulomatosis with polyangiitis.
Polish archives of internal medicineLocalized Immune-Complex Small-Vessel Vasculitis Presenting as Unilateral Myositis After Hepatitis A.
CureusFever of unknown origin, muscle weakness, and an adrenal nodule-the cat we chased like a hare: a case report.
Journal of medical case reportsVasculitic fasciitis characterizes a distinct subset of vasculitic myopathy with interferon-gamma signature.
Acta neuropathologicaMRI-guided muscle biopsy improves diagnostic yield in small- to medium-vessel vasculitis: a retrospective single-center study.
Rheumatology internationalClinical Implications of Vasculitis Associated with Familial Mediterranean Fever: A Comparative Study in Childhood.
Modern rheumatologyPolyarteritis nodosa associated with VEXAS syndrome and chronic myelomonocytic leukemia: a case-control study.
Rheumatology (Oxford, England)A Case of Challenging Polyarteritis Nodosa With Critical Limb Ischemia.
CureusPolyarteritis Nodosa With Mesenteric, Hepatic, and Musculoskeletal Manifestations in a 36-Year-Old Nigerian Male Patient: A Case Report.
CureusPolyarteritis nodosa with abdominal pain as the main symptoms: A case report.
MedicineTocilizumab for refractory and/or relapsing polyarteritis nodosa.
Journal of the American Academy of DermatologyClinical and laboratory predictors of diagnostic delay in childhood Takayasu arteritis and PAN: a retrospective cohort study.
Rheumatology (Oxford, England)Adenosine deaminase 2 (ADA2) deficiency masquerading as polyarteritis nodosa.
JAAD case reportsNonspecific Interstitial Pneumonia Pattern as an Atypical Pulmonary Manifestation of Polyarteritis Nodosa.
CureusCanine Cardiac and Cardiovascular Pathology: Four Major Life-Threatening Non-Degenerative, Non-Hereditary Conditions.
Veterinary sciencesClinical Spectrum and One-Year Outcomes of Central Nervous System Vasculitis Secondary to Systemic Autoimmune Disorders: A Retrospective Cohort Study.
CureusSevere relapse of cutaneous polyarteritis nodosa triggered by bacterial cellulitis.
European journal of dermatology : EJDDiagnostic yield of biopsy in cutaneous polyarteritis nodosa: A retrospective cohort study from 2 academic centers.
Journal of the American Academy of DermatologyDiverse Phenotypic Expressions of ADA2 Deficiency: Two Case Studies.
Iranian journal of allergy, asthma, and immunologyPolyarteritis nodosa presenting with TAFRO signs following COVID-19 infection: case report.
Modern rheumatology case reportsA visual guide for emergency radiologists navigating the complexity of abdominal vasculitis: part 1 - true vasculitis.
Emergency radiologyTumor Necrosis Factor Inhibitor Therapy in Polyarteritis Nodosa: Expanding Evidence From Systemic to Cutaneous Disease.
The Journal of rheumatologyRole of F-18 FDG-PET CT scan in the evaluation of medium vessel vasculitis.
Seminars in arthritis and rheumatismDiagnostic Implications and Correlates of Plasma Adenosine Deaminase 2 Activity and ADA2 Variants.
Arthritis & rheumatology (Hoboken, N.J.)Nodular Polyarteritis With Superior Mesenteric Artery Involvement: A Report of a Complex Case.
British journal of hospital medicine (London, England : 2005)Coronary Arteritis in Polyarteritis Nodosa.
QJM : monthly journal of the Association of PhysiciansPolyarteritis nodosa presenting with pancreatic-artery rupture and co-existing MEFV and ADA2 mutation: clinicopathological and genomic insights from a case report.
Virchows Archiv : an international journal of pathologyEfficacy and safety of tocilizumab in polyarteritis nodosa and adenosine deaminase 2 deficiency: a systematic literature review.
Clinical and experimental rheumatologyPolyarteritis nodosa: a tale of two atypical presentations.
BMJ case reportsNew avenues in childhood vasculitis.
Pediatric rheumatology online journalCotton-Wool Appearance of Muscular Polyarteritis Nodosa on Contrast Magnetic Resonance Imaging.
The Journal of rheumatologyMuscular polyarteritis nodosa.
Internal and emergency medicineThe Case | A patient with malignant hypertension, thrombotic microangiopathy, and perinephric hematoma after a biopsy.
Kidney internationalPolyarteritis nodosa with cutaneous manifestations localized to the upper limb, possibly caused by trauma.
European journal of dermatology : EJDSuccessful Treatment of Polyarteritis Nodosa With Multifocal Intracranial and Mesenteric Stenoses Using Endovascular Stenting and Tocilizumab.
CureusA Clinical Case Report of Deficiency of Adenosine Deaminase 2 Syndrome (DADA 2) Presenting as a Brachial Artery Aneurysm.
Mediterranean journal of rheumatologyPolyarteritis Nodosa with Concurrent CMV Infection: A Case Report and Brief Literature Review.
South Dakota medicine : the journal of the South Dakota State Medical AssociationVasculitis as an indicator of disease severity in familial Mediterranean fever.
Frontiers in immunologyCardiac disease in patients with vasculitis.
Clinical research in cardiology : official journal of the German Cardiac SocietyClinical value of biomarkers in relation to artery size in eosinophilic granulomatosis with polyangiitis: findings from an inception cohort at a Japanese City Hospital.
Clinical rheumatologyPediatric-Onset Polyarteritis Nodosa and Deficiency of Adenosine Deaminase 2: Clinical Overlap and Divergence.
Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseasesCognitive impairment and other neuropsychiatric manifestations in patients with primary vasculitis: a systematic review.
Seminars in arthritis and rheumatismReticulated violaceous patches in a 10-year-old boy.
JAAD case reportsC4d Immunoreactivity in Autoimmune and HBV-Induced Hepatitis: Implications for Complement-Mediated Hepatocellular Injury.
Pathophysiology : the official journal of the International Society for PathophysiologyDiagnosis and outcomes of fever of unknown origin cases with an erythrocyte sedimentation rate of 100 mm/h or more: An International ID-IRI (Infectious Diseases - International Research Initiative) Observational Retrospective Cohort Study.
MedicineCoronary Polyarteritis Nodosa: Clinical Dilemmas in Diagnosis and Management.
JACC. Case reportsTemporal arteritis and vasculitic myopathy in polyarteritis nodosa.
Journal of neurologyPolyarteritis nodosa with testicular involvement: a rare case report highlighting the role of nuclear imaging and angiography in diagnosis.
BJR case reportsTeaching NeuroImage: Vasculitic Neuropathy With Cutaneous Polyarteritis Nodosa.
Neurology[Abnormal renal arteriography].
La Revue de medecine interneMuscular polyarteritis nodosa: a diagnostic and therapeutic challenge.
BMJ case reportsNET Proteomic Profiling Reveals New Pathways Potentially Implicated in Dendritic Cell-Mediated Inflammation in DADA2 Patients.
Journal of clinical immunologyReversible Cardiomyopathy in Polyarteritis Nodosa: A Case Report.
CureusCutaneous Polyarteritis Nodosa-Like Vasculitis Possibly Induced by Osimertinib.
International journal of dermatologySpontaneous accessory renal artery aneurysm rupture as a first presentation of polyarteritis nodosa: a case report and review of literature.
Annals of medicine and surgery (2012)Effective Pain Management in Polyarteritis Nodosa (PAN) Utilizing Lumbar Sympathetic Blocks: A Case Report.
Anesthesiology and pain medicineSuccessful treatment with tocilizumab in a case of familial Mediterranean fever with Takayasu arteritis.
Modern rheumatology case reportsVasculitis in an Infant Born to a Mother With Longstanding Cutaneous Polyarteritis Nodosa: A Case Report and Review of Literature.
Pediatric dermatologyBeyond Ulcerations: A Case of Cutaneous Polyarteritis Nodosa in a Middle-Aged Woman.
CureusThink Out of the Box-A Rare Case of Intestinal Polyarteritis Nodosa.
The American journal of gastroenterologyEfficacy of Tumor Necrosis Factor Inhibitors for Refractory Leg Ulcers in Cutaneous Polyarteritis Nodosa: A Case Series.
The Journal of rheumatologyF18-FDG PET-CT Findings in Juvenile-Onset Polyarteritis Nodosa: A First Series and Literature Review.
Journal of clinical medicineDirect immunofluorescence testing for panniculitis offers negligible diagnostic utility: A retrospective single-center cohort study of 87 specimens.
Journal of the American Academy of DermatologyIgA vasculitis associated with chronic myelomonocytic leukemia.
BMC rheumatologyMinocycline-induced Polyarteritis Nodosa Manifesting as Tenosynovitis, Edema, and Rash: A Case Report.
The Israel Medical Association journal : IMAJCase Report: A case of cutaneous polyarteritis nodosa in a child following a streptococcal infection.
Frontiers in pediatricsSupplementation with Pycnogenol® relieves symptoms of chronic inflammatory diseases with a significant vasculitis component: a pilot registry study.
Minerva medicaComplex presentation of polyarteritis nodosa: Renal pseudoaneurysm rupture and bowel ischemia: A case report.
International journal of surgery case reportsMimics and challenging presentations of DADA2.
Clinical and experimental immunologyArtificial intelligence challenge of discriminating cutaneous arteritis and polyarteritis nodosa based on hematoxylin-and-eosin images of skin biopsy specimens.
Pathology, research and practiceCutaneous Arteritis Complicated by Crohn's Disease.
Internal medicine (Tokyo, Japan)Idiopathic polyarteritis nodosa - does it still exist? Viewpoint 1: as our knowledge makes progress, idiopathic polyarteritis nodosa is fading away.
Rheumatology (Oxford, England)Idiopathic polyarteritis nodosa-does it still exist? Viewpoint 2: idiopathic polyarteritis nodosa is rare, but still exists.
Rheumatology (Oxford, England)Clinical characterization of aortitis and periaortitis: study of 134 patients from a single university hospital.
Internal and emergency medicineEfficacy of Upadacitinib in refractory Polyarteritis Nodosa: a case report.
Oxford medical case reportsFasciitis-panniculitis syndrome with autoantibodies reacting to adipocyte pericellular fibers: a case report.
Pediatric rheumatology online journalIdentifcation of candidate biomarkers for polyarteritis nodosa using data-independent acquisition mass spectrometry.
American journal of translational researchPolyarteritis nodosa initially presenting as ocular motility impairment and diplopia with subsequent development of bilateral central retinal artery occlusion: A case report.
American journal of ophthalmology case reportsEffect of trace elements and nutrients on 21 autoimmune diseases: a Mendelian randomization study.
Frontiers in immunologyA Rare Case of Goodpasture's Syndrome Combined with Polyarteritis Nodosa.
Internal medicine (Tokyo, Japan)Incidence of ANCA-associated vasculitis and polyarteritis nodosa in Norfolk, UK, from 2011 to 2020.
Rheumatology (Oxford, England)Radiological insights into fibromuscular dysplasia unveiled by intracranial aneurysms and iliac vein hypoplasia in suspected DVT.
Radiology case reportsAnalysis of macular retinal thickness in polyarteritis nodosa using spectral domain optical coherence tomography.
Journal of ophthalmic inflammation and infectionPolyarteritis nodosa with life-threatening intracranial aneurysms in a child, and treatment with infliximab.
The Turkish journal of pediatricsThe clinical characteristics and treatment outcomes of patients with systemic polyarteritis nodosa: a single-centre study from India.
Rheumatology (Oxford, England)Coronary polyarteritis nodosa in a young adult - Authors' reply.
The Lancet. RheumatologyCoronary polyarteritis nodosa in a young adult.
The Lancet. RheumatologyA case of renovascular hypertension due to polyarteritis nodosa.
Journal of hypertensionRapidly progressive digital necrosis in polyarteritis nodosa.
Rheumatology advances in practiceExtreme Phenotypic Variation in Siblings with Identical Homozygous Mutations Causing ADA2 Deficiency: A Case Series.
Turkish journal of haematology : official journal of Turkish Society of HaematologyLethal Gastrointestinal Manifestation and 3D-Reconstructive CT in Systemic Polyarteritis Nodosa (PAN).
International journal of rheumatic diseasesPolyangiitis Overlap Syndrome: Polyarteritis Nodosa with Leukocytoclastic Vasculitis Associated with Left Ventricular Thrombus and Vocal Cord Palsy: A Case Report.
Oman medical journalEffectiveness of the combined therapy in the treatment of chronic non-healing wounds in patients with autoimmune diseases.
Journal of plastic, reconstructive & aesthetic surgery : JPRASPolyarteritis nodosa presenting with severe upper gastrointestinal bleeding: a case report.
Journal of medical case reportsA case of polyarteritis nodosa with severe lower limb ulcer that was treated with prednisolone and tocilizumab.
Modern rheumatology case reportsAn autopsy of a patient with polyarteritis nodosa who developed fatal intestinal perforation accompanied by systemic multiple aneurysms and arterial thrombosis.
Modern rheumatology case reportsComparison of [18F]FAPI-42 and [18F]FDG PET/CT in the evaluation of systemic vasculitis.
European journal of nuclear medicine and molecular imagingMisdiagnosed for 14 Years: Adenosine Deaminase 2 (ADA2) Deficiency in a Teen Mimicking Polyarteritis Nodosa.
Clinical case reportsCoronary polyarteritis nodosa.
The Lancet. RheumatologyMechanisms and Screening for Atherosclerosis in Adults With Vasculitis.
Arteriosclerosis, thrombosis, and vascular biologyAngiographic imaging of the testicular arteries with polyarteritis nodosa: A case report.
Radiology case reportsLong-term follow-up of anti-TNF treatment in adult and pediatric DADA2 patients: Insights from real-world data.
International journal of rheumatic diseasesRenovascular hypertension - a primer for the radiologist.
Abdominal radiology (New York)Hospitalist-performed skin biopsy in the diagnosis of skin disease.
Archives of dermatological researchDeficiency of adenosine deaminase 2 (DADA2) presented with bilateral renal subcapsular hematoma: a case report and literature review.
Annals of medicine and surgery (2012)Successful treatment of cutaneous polyarteritis nodosa with baricitinib.
The Journal of dermatological treatmentResilience and Beyond the Acute Phase Challenges: Case Series on Prolonged COVID-19 Infection in Immunocompromised Individuals.
Infection and drug resistance18 F-FDG PET/CT in the Evaluation of Polyarteritis Nodosa.
Clinical nuclear medicineFrench protocol for diagnosis and management of Cogan's syndrome.
La Revue de medecine internePage kidney in a case of polyarteritis nodosa.
Forensic science, medicine, and pathologyPolyarteritis nodosa mimics Kawasaki disease.
BMJ case reportsUncommon triple vessel spontaneous coronary artery dissection in the setting of polyarteritis nodosa: a case report.
Journal of medical case reportsSudden cardiac death caused by Kawasaki coronary artery vasculitis in a child with Hodgkin's lymphoma. Case report and literature review.
Cardiovascular pathology : the official journal of the Society for Cardiovascular PathologyCritical Limb Threatening Ischemia Due to Severe Polyarteritis Nodosa.
Internal medicine (Tokyo, Japan)Immunosuppression Therapy for Chronic Limb-threatening Ischemia in a Patient with Severe Polyarteritis Nodosa.
Internal medicine (Tokyo, Japan)Clinical Outcomes After Distal Bypass in Patients With Chronic Limb-Threatening Ischemia due to Connective Tissue Disease.
Vascular and endovascular surgeryTop 10 Clinical Pearls in Vasculitic Neuropathies.
Seminars in neurologyConstitutional symptoms of severe childhood-onset polyarteritis nodosa.
The Lancet. RheumatologyDiagnostic Value of Whole-Body MRI in Pediatric Patients with Suspected Rheumatic Diseases.
Medicina (Kaunas, Lithuania)[Vasculitic involvement of the skeletal muscle and the peripheral nervous system: clinical and neuropathologic perspective].
Zeitschrift fur RheumatologieRheumatoid Vasculitis Involving Gastrointestinal Tract Pre-dating Rheumatoid Arthritis: A Case Study and Literature Review.
CureusMuscular polyarteritis nodosa detected by FDG-PET/CT.
International journal of rheumatic diseasesClinical spectrum of and outcomes for Indian children with deficiency of adenosine deaminase 2 (DADA2): a multicentric study.
Rheumatology (Oxford, England)The coincidence of multiple sclerosis and primary vasculitis; from the bench of pathology to the bedside of treatment: a systematic review of case reports.
Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical NeurophysiologyPolyarteritis nodosa complicated by renal aneurysm and intestinal perforation: A case report.
MedicineCase report: Cutaneous polyarteritis nodosa presenting with ulcers in atypical localizations and atypical skin rashes: A report of a rare case.
International journal of rheumatic diseasesEarly skeletal muscle manifestations in polyarteritis nodosa and ANCA-associated vasculitis.
Autoimmunity reviewsPolyarteritis nodosa with abdominal bleeding: imaging with PET/CT and angiography on the same day.
Rheumatology advances in practicePossible usefulness of fluorodeoxyglucose positron emission tomography in diagnosing polyarteritis nodosa: A case report and literature review.
Modern rheumatology case reportsAdalimumab-induced leukocytoclastic vasculitis in a patient with ankylosing spondylitis: A case report.
Clinical case reports[Allogeneic haematopoietic stem cell transplantation induced remission of periarteritis nodosa associated with azacytidine-refractory myelodysplastic syndrome].
La Revue de medecine interneMuscular polyarteritis nodosa with fasciitis and upper extremity involvement.
Rheumatology advances in practiceKidney involvement in myelodysplastic syndromes.
Clinical kidney journalAutoimmune inner ear disease associated with antiphospholipid antibodies.
Clinical and experimental rheumatologyCOVID-19 associated cutaneous polyarteritis nodosa.
The American journal of the medical sciencesA great simulator in clinical practice: mononeuritis multiplex in HIV infection.
Autopsy & case reportsAutoimmunity in patients with inborn errors of immunity: A case series.
Reumatologia clinicaSpontaneous hepatic artery pseudoaneurysm rupture as a first presentation of polyarteritis nodosa.
BMJ case reportsUlcerative colitis: a diagnostic odyssey through cutaneous polyarteritis nodosa and granulomatous hepatitis.
BMJ case reportsHistopathological Confirmation of Axonal Sprouting in Regenerative Peripheral Nerve Interface.
Plastic and reconstructive surgery. Global openApremilast successfully treats cutaneous polyarteritis nodosa associated with SAPHO syndrome.
Rheumatology (Oxford, England)Case report of streptococcal infection as a potential precipitating factor in cutaneous polyarteritis nodosa in pediatric patients.
Clinical case reportsSevere infections in systemic necrotizing vasculitis.
Reumatologia clinicaKidney rupture in a patient with polyarteritis nodosa.
Polish archives of internal medicineRapidly Progressive, Symmetrical, Acute Cutaneous Necrosis of Bilateral Lower Limbs: A Rare Presentation of Polyarteritis Nodosa.
CureusDeficiency of adenosine deaminase 2: a genetic autoinflammatory disorder mimicking childhood polyarteritis nodosa.
BMJ case reportsClinical and laboratory findings characterizing the need for systemic corticosteroids and nonsteroidal systemic therapies and the predicted outcomes in cutaneous polyarteritis nodosa: a single-centre retrospective analysis.
Clinical and experimental dermatologyOphthalmic vascular manifestations in eosinophil-associated diseases: a comprehensive analysis of 57 patients from the CEREO and EESG networks and a literature review.
Frontiers in immunologyEosinophilic granulomatosis with polyangiitis and its association with montelukast: a case-based review.
Clinical rheumatologyGastroduodenal artery aneurysm - an extremely rare but insidious cause of abdominal pain: a case report.
The Pan African medical journalMulti-Modality Imaging in Vasculitis.
Diagnostics (Basel, Switzerland)Coinciding Crohn's disease and polyarteritis nodosa: A sign of medically refractory disease?
International journal of rheumatic diseasesVisualization of intradermal blood vessel structures by dual-wavelength photoacoustic microscopy and characterization of three-dimensional construction of livedo-racemosa in cutaneous polyarteritis nodosa.
Journal of dermatological scienceAnti-LAMP-2 Antibody Seropositivity in Children with Primary Systemic Vasculitis Affecting Medium- and Large-Sized Vessels.
International journal of molecular sciencesCutaneous polyarteritis nodosa: it is not always erythema nodosum.
Anales de pediatriaNeuro-ophthalmic challenges and multi-morbidity in vasculitis among the older adults.
Expert review of clinical immunologyShifting perspectives in coronary involvement of polyarteritis nodosa: case of 3-vessel occlusion treated with 4-vessel CABG and review of literature.
BMC cardiovascular disordersA Rare Presentation of Polyarteritis Nodosa (PAN).
CureusThe Extinction of Primary Polyarteritis Nodosa: A Modern Science Success Story?
Arthritis & rheumatology (Hoboken, N.J.)Wunderlich syndrome as a rare complication of polyarteritis nodosa: a case report.
ReumatismoComparison of characteristics of muscle magnetic resonance imaging findings in patients with antineutrophilic cytoplasmic antibody-associated vasculitis and polyarteritis nodosa.
International journal of rheumatic diseasesPost COVID-19 vaccination medium vessel vasculitis: a systematic review of case reports.
InfectionStroke frequency, associated factors, and clinical features in primary systemic vasculitis: a multicentric observational study.
Journal of neurologyAPDS patients with immune-complex vasculitis and resolution with leniolisib.
Clinical immunology (Orlando, Fla.)Polyarteritis nodosa with superior mesenteric artery dissection.
The American journal of the medical sciencesPolyarteritis nodosa with splenic rupture and multiple cerebral infarctions.
The Journal of dermatologyNew-onset autoimmune disease after COVID-19.
Frontiers in immunologyImages in Vascular Medicine: The large PANeurysm - A rare case of hepatic artery aneurysm in a 25-year-old woman with polyarteritis nodosa.
Vascular medicine (London, England)Clinical Characteristics and Outcomes of Polyarteritis Nodosa: An International Study.
Arthritis & rheumatology (Hoboken, N.J.)Nationwide epidemiological survey of polyarteritis nodosa in Japan in 2020.
Modern rheumatologyVon Willebrand factor: a possible biomarker for disease activity in vasculitis.
Scandinavian journal of rheumatologyRuptured Saccular Aneurysm Caused by Necrotizing Arteritis of the Polyarteritis Nodosa Type in Primary Angiitis of Central Nervous System.
International journal of surgical pathology[Immunoglobulin A vasculitis].
Innere Medizin (Heidelberg, Germany)Vasculitis-panniculitis mimicking unresolved diabetic foot ulcer.
Endocrinology, diabetes & metabolism case reportsLeft main and three vessels spontaneous coronary artery dissection as an incidental finding in young man with history of Hodgkin's lymphoma-a case report.
BMC cardiovascular disorders[Polyarteritis nodosa and Kawasaki syndrome : Vasculitis predominantly of medium size and small vessels].
Innere Medizin (Heidelberg, Germany)VEXAS syndrome: Clinical manifestations, diagnosis, and treatment.
Reumatologia clinicaSpontaneous Hepatic Rupture in the Setting of Peliosis Hepatis and End-Stage Renal Disease.
CureusRelapsing Hepatitis B-associated Vasculitis with Features of Polyarteritis Nodosa and c-Antineutrophilic Cytoplasmic Antibodies-associated Vasculitis.
Saudi journal of kidney diseases and transplantation : an official publication of the Saudi Center for Organ Transplantation, Saudi Arabia[Vasculitis as a cause of stroke].
Zhurnal nevrologii i psikhiatrii imeni S.S. KorsakovaComparison of EULAR/PRINTO/PReS Ankara 2008 and 2022 ACR/EULAR classification criteria for granulomatosis with polyangiitis in children.
Rheumatology (Oxford, England)Clinical characteristics, disease trajectories and management of vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic (VEXAS) syndrome: a systematic review.
Rheumatology internationalCutaneous polyarteritis nodosa and pulmonary arterial hypertension: An unexpected liaison. A case report.
MedicineAssociações
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Systemic Arterial Aneurysms With Limb Ischemia in a 3-Month-Old Infant: An Unusual Presentation of Incomplete Kawasaki Disease.
- Hypertensive crisis due to secondary aldosteronism from polyarteritis nodosa.
- Think Out of the Box-A Rare Case of Intestinal Polyarteritis Nodosa.
- Systemic Necrotizing Medium-Vessel Vasculitis Clinically Consistent With Polyarteritis Nodosa: A Detailed Case Report.
- Clinical manifestations, prognostic impact, and relapse in polyarteritis nodosa: a systematic review and meta-analysis.
- [(18)F]FDG PET/CT value in the diagnostic evaluation of patients with polyarteritis nodosa.
- Catastrophic Brain Hemorrhage in a Teenager With Immune Thrombocytopenia and Polyarteritis Nodosa.
- Paraneoplastic necrotizing medium-vessel vasculitis mimicking polyarteritis nodosa with large-vessel involvement.
- Myeloperoxidase anti-neutrophil cytoplasmic antibody vasculitis mimicking renal polyarteritis nodosa.
- [Polyarteritis nodosa: an etiology of myelitis that should not be ignored in subsaharansub-Saharan Africa].
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:767(Orphanet)
- MONDO:0019170(MONDO)
- GARD:7360(GARD (NIH))
- Busca completa no PubMed(PubMed)
- Artigo Wikipedia(Wikipedia)
- Q745162(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
