Polineuropatia desmielinizante inflamatória crônica

A Study Evaluating the Safety and Efficacy of KITE-363 in Relapsed/Refractory Autoimmune Neurologic Diseases

NCT07304154

A Study to Evaluate the Efficacy and Safety of DNTH103 in Adults With Chronic Inflammatory Demyelinating Polyneuropathy (CAPTIVATE)

NCT06858579

A Study to Test the Efficacy and Safety of Riliprubart Against the Usual Treatment of Intravenous Immunoglobulin (IVIg) in People With Chronic Inflammatory Demyelinating Polyneuropathy (CIDP)

NCT06290141

A Study to Assess Efficacy and Safety of Empasiprubart Versus IVIg in Adults With CIDP

NCT06920004

A Study to Evaluate the Pharmacokinetics and Safety of XEMBIFY Versus Gamunex-C in Participants With Chronic Inflammatory Demyelinating Polyradiculoneuropathy

NCT07540221

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Timeline de publicações

1.256 papers (10 anos)

Mostrando amostra de 200 publicações de um total de 1.256

#1

Clinical features of chronic inflammatory demyelinating polyneuropathy: a single-center experience with 33 patients.

Frontiers in neurology2026

Chronic inflammatory demyelinating polyneuropathy (CIDP) is an immune-mediated neuropathy with heterogeneous clinical presentations. Although several clinical subtypes, including typical and variants, have been described, evidence regarding their distribution and treatment outcomes remains limited, particularly for CIDP variants. We retrospectively analyzed 33 consecutive patients diagnosed with CIDP at Kumamoto University Hospital between January 2020 and March 2025. Clinical data included demographic characteristics, disease duration, subtype classification, electrophysiological and cerebrospinal fluid (CSF) findings, imaging findings, treatment details, and treatment responsiveness. Subtypes were classified according to the 2021 EAN/PNS diagnostic criteria. Treatment responsiveness was defined as objective improvement confirmed by at least two neurologists. Among the 33 patients, 36.4% had typical CIDP and 63.6% had CIDP variants, including distal (39.4%), multifocal (15.2%), motor (3.0%), and sensory (6.0%) subtypes. Distal CIDP was the most frequent subtype. Patients with multifocal CIDP experienced the longest diagnostic delays (mean, 4.6 years) due to fewer demyelinating findings on electrophysiological studies. The MRC sum score was lowest in typical CIDP, suggesting greater disease severity. Intravenous immunoglobulin (IVIg) demonstrated high efficacy across all subtypes, including multifocal CIDP, in contrast to previous reports of lower responsiveness. During a mean follow-up period of 5.1 years, 78.8% of patients required maintenance therapy, most commonly IVIg and corticosteroids. No changes in clinical subtypes were observed during follow-up. In this single-center study, variants outnumbered typical CIDP, reflecting the case mix at a specialized tertiary referral center. Multifocal CIDP showed the longest diagnostic delays. IVIg demonstrated high efficacy across subtypes, including multifocal CIDP, contrasting with previous reports. These findings highlight the importance of improving diagnostic accuracy and establishing individualized long-term treatment strategies for CIDP.

#2

Clinical and laboratory features of juvenile-onset anti-NF155 autoimmune nodopathy.

Journal of neurology, neurosurgery, and psychiatry2026 Mar 03

Neurofascin 155 autoimmune nodopathy (NF155 AN) is a recently recognised immune-mediated neuropathy distinct from chronic inflammatory demyelinating polyneuropathy. While adult-onset cases have been increasingly reported, the juvenile-onset form remains poorly characterised. We retrospectively analysed 36 patients with NF155 AN, focusing on detailed characterisation of 16 juvenile-onset cases. Their clinical and laboratory data were reviewed. Juvenile-onset patients presented with sensorimotor neuropathy characterised by distal predominant weakness, tremor and sensory ataxia. Motor symptoms were the presenting feature in 75% of patients, which significantly differed from the adult cases (p=0.0015). Postural tremor was more frequent in juvenile patients (94%), while cranial nerve involvement was less common (19%). Electrophysiologically, absent compound muscle action potentials in lower limbs were significantly more prevalent in juvenile patients (peroneal: 78%; tibial: 66%; p<0.001 for both). Symmetrical spinal root/plexus hypertrophy on MR neurography and characteristic pathological findings were observed in both groups. Intravenous immunoglobulin response was generally poor, while delayed rituximab initiation still led to clinical improvement in the juvenile-onset group. Juvenile patients showed trends towards better functional outcomes. Juvenile-onset NF155 AN is distinguished by motor-predominant onset, frequent tremor and characteristic electrophysiological abnormalities, yet demonstrates favourable prognosis with B-cell targeted therapy. Early recognition and timely diagnosis are essential for optimal outcomes.

#3

Non-sensorimotor symptoms in chronic inflammatory demyelinating polyneuropathy.

Journal of neurology2026 Mar 03

Chronic inflammatory demyelinating polyneuropathy (CIDP) is defined as a dysimmune disorder of the peripheral nervous system (PNS) resulting in sensorimotor deficits. However, an increasing body of data suggests that CIDP also goes along with features, such as autonomic, circadian, fatigue, mood, and subtle cognitive dysfunctions. Some of these non-sensorimotor symptoms (NSMS) challenge the concept of an exclusive PNS disease. Pragmatically, the high prevalence of NSMS calls for a more holistic disease assessment and surveillance to achieve optimal therapeutic results.

#4

The actual usefulness of culturing apheresis products in hematopoietic stem cell autotransplants.

Transfusion and apheresis science : official journal of the World Apheresis Association : official journal of the European Society for Haemapheresis2026 Apr

Bacterial cultures of apheresis products are mandated by FACT-JACIE standards as a safety measure in autologous hematopoietic stem cell transplantation (aHSCT). However, results are often available only after reinfusion, raising questions about their clinical utility, particularly in programs that use fresh, non-cryopreserved products. To evaluate the incidence, microbiological profile, and clinical relevance of positive bacterial cultures in apheresis products used for aHSCT in autoimmune diseases. This prospective study included 629 apheresis products administered to 586 patients with MS or CIDP who underwent outpatient, non-cryopreserved aHSCT between July 2021 and March 2025. Bacterial cultures were performed from product aliquots using the BACTEC system (aerobic and anaerobic bottles). Positive isolates underwent antibiotic susceptibility testing. Culture results, timing of positivity, and 28-day post-infusion outcomes were analyzed. Bacterial contamination was detected in 8 of 629 products (1.3 %). In one case, Escherichia coli was isolated within 24 h, leading to identification of a urinary tract infection and fatal sepsis in the patient; the contaminated product was discarded. The remaining seven cases became positive after 2-11 days (median: 6), when products had already been infused. Isolates included Cutibacterium acnes (n = 6), Staphylococcus capitis (n = 1), and Coryneform bacteria (n = 1). All were considered contamination during aliquot handling. No clinical complications occurred in these patients during the 28-day follow-up. Routine bacterial cultures of apheresis products yielded clinically relevant information in only 1 of 629 procedures. Most positive results reflected contamination of aliquots rather than true product infection, suggesting that the value of routine cultures in fresh aHSCT for autoimmune diseases may be limited and warrants re-evaluation.

#5

Benefits and challenges in everyday life for patients performing subcutaneous immunoglobulin treatment at home: a qualitative interview study.

BMJ open2026 Jan 30

Across medicine, new therapies are shifting treatment from clinic to home settings. At-home subcutaneous immunoglobulin treatment for immunodeficiency is an example of one such therapy. In this qualitative interview study, we investigated experiences of patients living an everyday life with subcutaneous immunoglobulin at-home treatment. 24 Danish patients participated in semistructured interviews. Six patients were interviewed in individual home-visit interviews, while the remaining 18 participated in one of six subsequent group interviews using an online video format. Participants represented three patient groups: patients with primary immunodeficiency, patients with secondary immunodeficiency, and patients with chronic inflammatory demyelinating polyneuropathy or multifocal motor neuropathy. According to the interviewed patients, at-home treatment provided a high degree of flexibility and freedom in everyday life. When transitioning to at-home treatment, a sense of security had been achieved through individualised training and access to healthcare professionals. Some patients experienced uncertainty or insecurity during the initial period of administering treatment at home; however, this typically receded over time. For the patients, at-home treatment had become embedded in everyday life either through incorporation into existing everyday routines or through the development of new routines. The time-related and place-related flexibility of the at-home treatment had benefits for several arenas of everyday life: work, family, and leisure. Patients associated at-home treatment with a sense of freedom, which they ascribed both to independence from the hospital and to not being confronted with medical conditions and other patients in the hospital setting. A small minority of the patients viewed the reduced contact with healthcare professionals as a disadvantage, describing feelings of being alone and responsible for their treatment. Patients who had established at-home treatment routines in their everyday lives found the benefits of at-home treatment to outweigh the challenges.

Publicações recentes

CRE26-073: A Case of Bortezomib-Induced Demyelinating Polyneuropathy Resembling Chronic Inflammatory Demyelinating Polyneuropathy.

📖 Revisão

J Natl Compr Canc Netw2026 Mar 31

Quality of Life in Patients With Chronic Inflammatory Demyelinating Polyneuropathy.

🥈 Ensaio clínico

Muscle Nerve2026 Apr 14

Ultrasonographic, Electrophysiological and Clinical Profiles of Motor and Motor Predominant Chronic Inflammatory Demyelinating Polyneuropathy.

Muscle Nerve2026 Apr 14

Causal effects of Epstein-Barr virus antibodies on autoimmune neuroinflammatory diseases: A generalised summary data-based Mendelian randomisation study.

Medicine (Baltimore)2026 Apr 10

Leprosy neuropathy and demyelinating impairment: How should we interpret this neurophysiological pattern?

PLoS One2026

Ver todas no PubMed

📚 EuropePMC1.138 artigos no totalmostrando 196

When Foot Drop Tells a Bigger Story: POEMS (Polyneuropathy, Organomegaly, Endocrinopathy, Monoclonal Plasma Cell Disorder, and Skin Changes) Syndrome Revealed by Femoral Plasmacytoma.

Neuro-ophthalmology (Aeolus Press)

Clinical Features and Management of Optic Neuritis in a Cohort of Patients with Combined Central and Peripheral Demyelination.

Clinical features of chronic inflammatory demyelinating polyneuropathy: a single-center experience with 33 patients.

Distinct cerebrospinal fluid profiles of astrocytic aquaporin-4 and GFAP in neuroinflammatory disorders.

Neurobiology of disease

CIDP With and Without Monoclonal Gammopathy of Undetermined Significance (MGUS): Comparison of Clinical Phenotype, Diagnostic Features, and Treatment Response.

Biallelic Variants in RNU6ATAC Result in a Minor Spliceopathy Characterized by Transcriptome-Wide Minor Intron Retention Events and Short Stature with Variable Multisystem Manifestations.

HGG advances

Journal of neurology, neurosurgery, and psychiatry

Clinical and laboratory features of juvenile-onset anti-NF155 autoimmune nodopathy.

Non-sensorimotor symptoms in chronic inflammatory demyelinating polyneuropathy.

Journal of neuroimmunology

Rethinking rituximab in neuroimmunology: Real-world efficacy, cost-effectiveness, and long-term remission.

Case reports in neurological medicine

Familial Occurrence of Anti-NF155 Autoimmune Nodopathy in Father and Son: Expanding the Spectrum of IgG4-Related Nodopathies.

A case report of arsenic-induced peripheral neuropathy misdiagnosed as Guillain-Barré syndrome.

Frontiers in toxicology

Plasma neurofilament light chain is associated with clinical instability in chronic autoimmune neuropathies.

Scientific reports

Genetic risk of chronic pain conditions associated with risk of suicide death through an integrative analysis of EHR and genomics data.

Translational psychiatry

Real-world treatment utilization in adults with chronic inflammatory demyelinating polyneuropathy in the United States.

CAR-T manufacturing reduces heterogeneity between CIDP and multiple myeloma patient-derived T cells.

Theranostics

Journal of central nervous system disease

Case-Based Lessons on Remote Patient Monitoring in Neurology Using Consumer-Grade Wearables.

Frontiers in cardiovascular medicine

POEMS syndrome with cardiovascular lesions as the initial manifestation: a case report and literature review.

Transfusion and apheresis science : official journal of the World Apheresis Association : official journal of the European Society for Haemapheresis

The actual usefulness of culturing apheresis products in hematopoietic stem cell autotransplants.

Subacute cutaneous lupus erythematosus secondary to intravenous immunoglobulin therapy for chronic inflammatory demyelinating polyneuropathy: A case report.

JAAD case reports

Elucidating Causal Associations Between Immune Cells, Circulating Inflammatory Proteins, and Chronic Inflammatory Demyelinating Polyneuropathy: A Two-Sample Two-Step Mendelian Randomization Study.

Digestive diseases and sciences

Chronic Inflammatory Demyelinating Polyneuropathy Following Adalimumab Therapy for a Patient with Intestinal Behçet's Disease.

The American journal of case reports

Successful Treatment of Multifocal Demyelinating Sensory-Motor Neuropathy (Lewis-Sumner Syndrome) With Rituximab: A Case Report.

Benefits and challenges in everyday life for patients performing subcutaneous immunoglobulin treatment at home: a qualitative interview study.

BMJ open

Combined Central and Peripheral Demyelination with a Favorable Outcome: A Case with 10-Year Follow-up.

Noro psikiyatri arsivi

The British journal of ophthalmology

Corneal confocal microscopy as a paraclinical test in neurodegenerative disease: a scoping review.

Frontiers in molecular neuroscience

Genetic and metabolic inflammation signatures in chronic inflammatory demyelinating polyneuropathy: the role of IL18 polymorphisms and short-chain fatty acids.

Case report: Efgartigimod treatment in two pediatric patients with chronic inflammatory demyelinating polyneuropathy.

International journal of molecular sciences

Blood-Nerve Barrier Breakdown Induced by Immunoglobulin G in Typical and Multifocal Chronic Inflammatory Demyelinating Polyneuropathy and Multifocal Motor Neuropathy.

Practical Approach to Managing SCIg Treatment in Patients With Chronic Inflammatory Demyelinating Polyneuropathy.

Conduction Block Detection in Dysimmune Neuropathy: Hypothetical Pathophysiological 'Truth' Versus Clinical Pragmatism.

Characteristics of adverse events and clinical risks of intravenous immunoglobulin: a pharmacovigilance study based on FDA Adverse Event Reporting System (FAERS).

Frontiers in medicine

Evaluating the short-term and long-term therapeutic effects of immunoadsorption compared with plasma exchange in chronic inflammatory demyelinating polyneuropathy: a long-term, prospective, observational study.

EClinicalMedicine

Neurological Complications Associated With COVID-19 Compared to Other Viral Infections: A Systematic Review of Current Evidence.

Cost Analysis of Immunoglobulin Maintenance Treatment of Patients with Chronic Inflammatory Demyelinating Polyneuropathy in Spain.

PharmacoEconomics - open

Handbook of clinical neurology

Immunotherapies on Guillain-Barré syndrome and other acute autoimmune neuropathies.

Handbook of clinical neurology

FcRn inhibitors: A new era in neurotherapeutics.

Incidence, Prevalence, and Treatment Patterns in Chronic Inflammatory Demyelinating Polyneuropathy: Data Analysis of US Claims.

Neuroepidemiology

Amyloid : the international journal of experimental and clinical investigation : the official journal of the International Society of Amyloidosis

Significance of aberrant nerve conduction in hereditary transthyretin amyloidosis.

Biopsy of the Superficial Sensory Radial Nerve in the Distal Forearm: A Technical Note.

DISTRICTS trial: enhancing carpal tunnel syndrome treatment - Authors' reply.

Lancet (London, England)

Journal of clinical neurology (Seoul, Korea)

Efficacy, Safety, and Tolerability of Subcutaneous Efgartigimod PH20 in Chinese Patients With Chronic Inflammatory Demyelinating Polyneuropathy: A Prespecified Subpopulation Analysis of the Multicentre, Randomised-Withdrawal, Double-Blind, Placebo-Controlled, Phase II ADHERE Trial.

Journal of clinical neurology (Seoul, Korea)

Immunotherapy in Chronic Inflammatory Demyelinating Polyneuropathy and the Emerging Role of Efgartigimod.

Paraneoplastic neurological syndrome with Guillain-Barré syndrome overlap in small-cell lung carcinoma: A case report from a primary care hospital in China.

Medicine

Aberrant Complement Activation Is a Prominent Feature of Chronic Inflammatory Demyelinating Polyneuropathy.

Journal of investigative medicine high impact case reports

Persistent COVID-19 Pneumonia in a Patient on Rituximab.

Therapeutic advances in neurological disorders

Shaping the role of plasma exchange in autoimmune neurology: lessons learned from 67 years and over 90,000 procedures.

Therapeutic advances in neurological disorders

Efficacy of intravenous immunoglobulin in patients with chronic inflammatory demyelinating polyneuropathy with or without diabetes: insights from a multicenter prospective comparative study.

Chronic Inflammatory Demyelinating Polyneuropathy Presenting With Isolated Distal Fingertip Paresthesia in a Factory Worker With Ulcerative Colitis: A Case Report.

International ophthalmology clinics

Ocular and Neuro-Ophthalmic Manifestations of Chronic Inflammatory Demyelinating Polyneuropathy.

Highly Immunoresistant Acute Motor and Sensory Axonal Neuropathy With Concomitant Anti-NF155 Axonal Nodopathy: A Case Report.

Patient preference and adherence

Experiences of Immunoglobulin Therapy for Those with a Confirmed Diagnosis of Chronic Inflammatory Demyelinating Polyneuropathy: A Mixed-Methods Study with a Qualitative Patient Perspective Focus.

Intermittent immunoadsorption in critically ill patients with neuroimmunological disorders: a retrospective study.

International journal of molecular sciences

Autoimmune Neuromuscular Disorders at a Molecular Crossroad: Linking Pathogenesis to Targeted Immunotherapy.

Journal of the neurological sciences

A combined approach of Interleukin-8 and magnetic resonance neurography to differentiate Guillain-Barré syndrome and chronic inflammatory demyelinating polyneuropathy.

Case Report: Secondary myelodysplastic syndrome following autologous stem cell transplantation in a patient with POEMS syndrome.

Characterizing Treatment Patterns and Healthcare Use in Patients and Subgroups with Chronic Inflammatory Demyelinating Polyradiculoneuropathy: A Real-World Study.

Journal of the neurological sciences

Autoimmune neuropathies: New guidelines and expert insights into clinical decision making.

Neurologia i neurochirurgia polska

Clinical, serological, and electrophysiological differences in chronic inflammatory demyelinating polyradiculoneuropathy patients with and without malignancy - real-life evidence.

Frontiers in veterinary science

Case Report: Staged bilateral pancarpal arthrodesis using 3D-printed patient specific guides and customized hybrid plate for severe carpal joint instability associated with chronic inflammatory demyelinating polyneuropathy in a miniature dachshund.

Annals of clinical and translational neurology

Deep Learning-Assisted Differentiation of Four Peripheral Neuropathies Using Corneal Confocal Microscopy.

Journal of neuroimmunology

Efficacy and safety of intravenous efgartigimod for chronic inflammatory demyelinating polyneuropathy: A case series real-world study.

Clinical Utility of Serum Neurofilament Light Chain in Peripheral Neuropathy.

Wearable Monitoring Captures Sleep Disturbances in Patients With Chronic Inflammatory Demyelinating Polyneuropathy.

Zhurnal nevrologii i psikhiatrii imeni S.S. Korsakova

[POEMS syndrome: A complex diagnostic case under the guise of chronic polyneuropathy].

Very High Dose Immunoglobulin Treatment for Chronic Inflammatory Demyelinating Polyneuropathy: A Multicentre UK Study.

Switch from Intravenous to Subcutaneous Immunoglobulin in CIDP and MMN: 12 Months Results from an Observational Study.

An Evaluation of the Real-World Effectiveness of Immunoglobulin Therapy in Chronic Inflammatory Demyelinating Polyneuropathy.

Cognitive impairment in chronic inflammatory demyelinating polyneuropathy.

Recurrent Guillain-Barré Syndrome: A Case Report and Literature Review.

Asian journal of transfusion science

Effectiveness and safety of therapeutic plasma exchange in neurological disorders; measuring the response to treatment using Modified Rankin Scale - A single-center study.

AXIN1, STAMBP, ST1A1, CDCP1, and SIRT2 Validated as Myasthenia Gravis Biomarkers: A Comparative Proteomic Study With MS, CIDP, and Controls.

Journal of neuroimaging : official journal of the American Society of Neuroimaging

Diffusion Tensor Imaging Reveals Altered Centrality of Pain-Related Regions in SCN9A-Associated Small Fiber Neuropathy.

Surgical neurology international

BurstDR spinal cord stimulation for chronic inflammatory demyelinating polyneuropathy.

Delayed treatment and diagnostic challenges in differentiating multifocal acquired demyelinating sensory and motor neuropathy from lupus: a case report and literature review.

AME case reports

Abnormal Sleep in Chronic Inflammatory Demyelinating Polyneuropathy.

Transfusion medicine (Oxford, England)

Intravenous immunoglobulin weaning evaluation with zero-shot large language model classification.

The potential role of IgG subclass in NF155-associated nodopathy for targeting therapy: a pediatric case report highlighting the efficacy of pulsed oral corticosteroids.

Immune-Mediated Neuropathies Other Than Typical Chronic Inflammatory Demyelinating Polyradiculoneuropathy-Multifocal Motor Neuropathy, Autoimmune Nodopathies, Anti-Myelin Associated Glycoprotein Neuropathy, Chronic Inflammatory Sensory Polyradiculoneuropathy, and Chronic Ataxic Neuropathy with Ophthalmoplegia, M-Protein, Agglutinin, and Disialosyl Antibodies.

Neurologic clinics

Chronic Inflammatory Demyelinating Polyneuropathy and Variants.

Neurologic clinics

Journal of clinical medicine

Innate Immunity in the Pathogenesis of Selected Autoimmune Neurological Diseases.

Motor and Cognitive Fatigue in Chronic Inflammatory Demyelinating Polyneuropathy.

Nerve Ultrasound in Pediatric Polyneuropathies: A Systematic Review.

Neuropediatrics

Chimeric Antigen Receptor (CAR) T Cell Therapy for Neuromuscular Disorders: A Systematic Review.

Case reports in neurological medicine

Coexistence of Acute Demyelinating Polyneuropathy and LRP4-Positive Myasthenia Gravis.

A Rare Case of Concomitant Fibrillary Glomerulonephritis and Membranous Nephropathy in a Patient With Chronic Inflammatory Demyelinating Polyneuropathy.

Chronic inflammatory demyelinating polyneuropathy (CIDP) after cilta-cel therapy.

Blood cancer journal

Rinsho shinkeigaku = Clinical neurology

[A case of adult-onset Krabbe disease diagnosed by galactocerebrosidase gene mutations, presenting with an atypical phenotype].

Arquivos de neuro-psiquiatria

Anti-pan-neurofascin IgG3: insights about an emerging autoimmune nodoparanodopathy.

Clinical Spectrum, Pathology, and Mechanisms of Anti-LGI4 Antibody-Positive Autoimmune Nodopathy.

Exacerbation of demyelinating polyneuropathy after adoptive cell therapy with tumour-infiltrating lymphocytes by metastatic melanoma.

Swiss medical weekly

ImmunoTargets and therapy

Efficacy of Tacrolimus Plus Prednisone as Long-Term Immunosuppressive Therapy for Chronic Inflammatory Demyelinating Polyneuropathy: A Retrospective Cohort Study.

Temporal Association Between Dengue Outbreaks and Neurologic Autoimmune Diseases in French Guiana.

Internal medicine (Tokyo, Japan)

Hereditary Neuropathy with Liability to Pressure Palsies Mimicking a Chronic Inflammatory Demyelinating Polyneuropathy Variant: A Case Report Highlighting Diagnostic Challenges.

Comparison of the presentation and electrophysiological characteristics of autoimmune nodopathies in patients with antibody-negative CIDP and CMT1.

Archives of physical medicine and rehabilitation

Impact of Physical Exercise Programs on Fatigue and Functional Capacity in People With Guillain-Barré Syndrome and Chronic Inflammatory Demyelinating Polyneuropathy: A Systematic Review.

Journal of clinical immunology

A Novel Cause of CIDP: Homozygous Hotspot Mutation, c.793 C > T in CASP8 Gene.

Health and quality of life outcomes

Development of a PROM set for patients with Guillain-Barré syndrome (GBS) and chronic inflammatory demyelinating polyneuropathy (CIDP): study protocol.

BMJ (Clinical research ed.)

Atypical diabetic neuropathies.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology

Polyradiculoneuropathies associated with immune checkpoint inhibitors: are we facing a new nosological entity?

Epidemiology, Presentation, Management and Outcomes in Chronic Inflammatory Demyelinating Polyneuropathy in Birmingham, UK: The Impact of Ethnicity.

Case reports in hematology

POEMS Syndrome Without a Detectable Monoclonal Peak: The Critical Role of VEGF and Bone Marrow Biopsy in Diagnosis.

Humoral Immune Response Following COVID-19 Vaccination in Multifocal Motor Neuropathy and Chronic Inflammatory Demyelinating Polyneuropathy.

Vaccines

Orbit (Amsterdam, Netherlands)

Orbital apex-like syndrome with multiple cranial neuropathies secondary to chronic inflammatory demyelinating polyneuropathy.

Feasibility of Outpatient Transforaminal Lumbar Interbody Fusion (TLIF) in Chronic Inflammatory Demyelinating Polyneuropathy: A Case Report.

Journal of lipid research

Plasma lipidomic patterns associated with disease activity in chronic inflammatory demyelinating polyradiculoneuropathy (LIPID-CIDP).

Complement profiling of sural nerves in chronic-inflammatory demyelinating polyneuropathy.

Acta neuropathologica

The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiques

Feasibility of Subcutaneous Immunoglobulin Therapy as the Maintenance Therapy in Patients with Autoimmune Neuromuscular Disease: A Prospective Study.

Natural Pregnancy Following Oocyte Retrieval in a Luteal-Phase Progestin-Primed Ovarian Stimulation (PPOS) Protocol With Concurrent Blastocyst Cryopreservation: A Case Report.

Journal of neuroimmunology

Neuronal inflammation-associated biomarkers in cerebrospinal fluid of patients with acute and chronic inflammatory demyelinating polyneuropathies.

Targeting BCMA in CIDP: Valuable insights gained through multi-omics immune monitoring.

Med (New York, N.Y.)

Multiple sclerosis and related disorders

Autologous haematopoietic stem cell transplantation in non-MS neuroimmunological diseases.

International journal of molecular sciences

5-Aminolevulinic Acid Ameliorates Chronic Experimental Autoimmune Neuritis Through a Dual Mechanism of Mitochondrial Protection and Immunomodulation.

Case reports in hematology

POEMS Syndrome Masquerading as Metastatic Prostate Cancer Based on PSMA Avid Lesions.

A new screening tool for early recognition of ATTRv polyneuropathy in clinical practice: AmyloScan®.

The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiques

Quality of Life in Patients with Chronic Inflammatory Demyelinating Neuropathies Treated with Subcutaneous Immunoglobulin.

Rinsho shinkeigaku = Clinical neurology

[AQP4 positive neuromyelitis optica spectrum disorder: an atypical pathology with nerve root enlargement and peripheral nervous system damage in demyelination].

Journal of the neurological sciences

Outcome measures in CIDP: A scoping and mapping review.

bioRxiv : the preprint server for biology

B Cell Tolerance and BCR Signaling Dysregulation in NF155-Mediated Autoimmune Nodopathies.

Real-World Multinational Survey of Chronic Inflammatory Demyelinating Polyneuropathy: Disease Characteristics and Therapeutic Landscape.

Brain : a journal of neurology

Tipping the balance: the PD1-axis as a modulator in chronic inflammatory demyelinating polyneuropathy.

Molecular genetics and metabolism

Childhood POLG-related disorders: Focus on polyradiculoneuropathy.

Impact of Social Deprivation on Diagnosis, Management and Outcome of Chronic Inflammatory Demyelinating Polyneuropathy at a Tertiary UK Centre.

Case reports in women's health

Chronic inflammatory demyelinating polyneuropathy complicated by pre-eclampsia progressing to HELLP syndrome and pulmonary embolism: A case report.

Random X chromosome inactivation in female Charcot-Marie-Tooth disease type X1: insights from sural nerve biopsy analysis.

CAR T-cells meet autoimmune neurological diseases: a new dawn for therapy.

Clinical and Genetic Reassessment in Patients With Clinically Diagnosed Hereditary Polyneuropathy.

Current opinion in neurology

Controversies in the diagnosis of chronic inflammatory demyelinating polyneuropathy.

An auxiliary diagnostic strategy for distinguishing Guillain-Barré syndrome and chronic inflammatory demyelinating polyneuropathy: combining platelet-to-lymphocyte ratio and cerebrospinal fluid interleukin-8 levels.

Genetic susceptibility of human leukocyte antigen alleles in chronic inflammatory demyelinating polyneuropathy in Korean patients : Short title: HLA alleles and CIDP in Korea.

Minimal Clinically Important Differences in Measuring Treatment Effects in CIDP: History, Current Use, Limitations, and Prospects.

Exploring Ultrasonographic Atypical Aspects in Drug-Resistant Multifocal Chronic Inflammatory Demyelinating Polyneuropathy.

Brain and behavior

Extracorporeal therapy procedures (plasma exchange and immunoadsorption) in chronic inflammatory demyelinating polyneuropathies (CIDP)- a database analysis.

Journal of neuroengineering and rehabilitation

Digital biomechanical assessment of gait in patients with peripheral neuropathies.

Clinica chimica acta; international journal of clinical chemistry

Blood bile acid profiles in chronic inflammatory demyelinating polyneuropathy.

Digestive diseases and sciences

Nervous Breakdown: Chronic Inflammatory Demyelinating Polyneuropathy as an Extra-Intestinal Manifestation of Ulcerative Colitis.

Annals of clinical and translational neurology

Digital Activity Markers in Chronic Inflammatory Demyelinating Polyneuropathy.

Nerve conduction study and nerve ultrasound as biomarkers for steroid dependence in chronic inflammatory demyelinating polyneuropathy.

Neurological research

Journal of neuroengineering and rehabilitation

Electrophysiological-based automatic subgroups diagnosis of patients with chronic dysimmune polyneuropathies.

Magnetic resonance imaging clinics of North America

Whole-Body Magnetic Resonance Neurography-Technique, Current Perspectives, and Future Directions.

Where Does It All Itch? Exploring the Characteristics of Pruritus in Small Fiber Neuropathy.

Therapeutic advances in neurological disorders

Comparison of imaging markers of nerve ultrasound and MR-neurography in a longitudinal course in chronic inflammatory demyelinating polyneuropathy.

Case Report: Post-surgical Guillain-Barré syndrome as a rare differential diagnosis of flaccid paralysis of the lower extremities in an infant after cardiac surgery.

Frontiers in pediatrics

Stiff tongue syndrome and multifocal immune neuropathy in a young man with anti-glutamic acid decarboxylase and unclassified antibodies.

BMJ case reports

Chronic Inflammatory Demyelinating Polyneuropathy and Concurrent Membranous Nephropathy Associated With Anti-Contactin-1 Autoantibodies: A Rare Case Report With a Review of the Literature.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology

Chronic inflammatory demyelinating polyneuropathy in end-stage renal disease patients: a case series study.

The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiques

Nerve Ultrasound of Multifocal Motor Neuropathy and Motor and Typical Chronic Inflammatory Demyelinating Neuropathy.

The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiques

Systematic Review: Mental Health Outcomes in Guillain-Barré Syndrome and Chronic Inflammatory Demyelinating Polyneuropathy.

Serum Neurofilament Light Chain as a Biomarker for CIDP Diagnosis, Severity, and Treatment Outcome.

Inverse relation between serum neurofilament light chain and cognitive function in chronic inflammatory demyelinating polyneuropathy.

Severe Worsening of Neuropathy Associated With Antibodies Against Myelin-Associated Glycoprotein by Rituximab Resembling Chronic Inflammatory Demyelinating Polyneuropathy.

Role of Imaging in Chronic Inflammatory Demyelinating Polyneuropathy: A Systematic Review.

Peripheral neuropathies associated with anti-tnf-α treatments: a systematic review and proposed recommendations.

A highly sensitive quantitative method of polysialic acid reveals its unique changes in brain aging and neuropsychiatric disorders.

Scientific reports

Sulfatide antibody-mediated neuropathy: an analysis of clinical characteristics and immunotherapeutic responses.

Neurological research

Disability and rehabilitation. Assistive technology

Objective assessments for walking aid prescription in balance impairment and falls risk: a scoping review of current evidence.

Anti-BCMA CAR-T cell therapy in relapsed/refractory chronic inflammatory demyelinating polyneuropathy.

Med (New York, N.Y.)

Validity and Responsiveness of Balance Measurements Using Posturography in Patients With Immune-Mediated Neuropathies.

International journal of surgical pathology

Whipple Disease Initial Presentation as Supraclavicular Lymphadenopathy in a Patient With Rheumatoid Arthritis: A Diagnostic Challenge.

Acta neurologica Taiwanica

Focal Chronic Inflammatory Demyelinating Polyneuropathy - A Case Report with Clinical Application and Validation of 2021 European Academy of Neurology/Peripheral Nerve Society Criteria.

Chronic Inflammatory Demyelinating Polyneuropathy: How Pathophysiology Can Guide Treatment.

Case Report: A case of subacute combined degeneration of the spinal cord associated with chronic atrophic gastritis, macrocytic anemia, and positive anti-sulfatide IgM and IgG antibodies.

Chronic Inflammation: A Multidisciplinary Analysis of Shared Pathways in Autoimmune, Infectious, and Degenerative Diseases.

The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiques

Reviewer Comment on Li et al.: "Systematic review: mental health outcomes in Guillain-Barre syndrome and chronic inflammatory demyelinating polyneuropathy".

Patient-Reported Outcome Measures for Assessing Health-Related Quality of Life in Patients With Polyneuropathies, Focusing on Guillain-Barré Syndrome and Chronic Inflammatory Demyelinating Polyneuropathy: A Systematic Review of Measurement Properties.

Case reports in neurological medicine

Chronic Inflammatory Demyelinating Polyneuropathy Following Natural Influenza A Infection in a Pediatric Patient: A Case Report and Literature Review.

Syncope and New-Onset Bifascicular Block Associated With Intravenous Immunoglobulin in a Patient With Chronic Inflammatory Demyelinating Polyneuropathy.

Patient Experience of Chronic Inflammatory Demyelinating Polyneuropathy (CIDP): A Qualitative Exploration of Signs, Symptoms, and Health-Related Quality of Life Impacts.

Incomplete Presentations in Typical Chronic Inflammatory Demyelinating Polyneuropathy: A Single-Center, Retrospective Study.

Plasma cell myeloma with an evolving diagnostic complexity: A case report.

Oncology letters

Case reports in critical care

A Rare Presentation of Patient With CIDP Found to Have Respiratory Failure and Encephalopathy.

Neurosciences (Riyadh, Saudi Arabia)

Unmasking the mimic: Leprosy neuropathy misdiagnosed as chronic inflammatory demyelinating polyneuropathy: A case report from Saudi Arabia.

Current research in translational medicine

Acute-onset chronic inflammatory demyelinating polyneuropathy in a 23-year-old male exacerbated by an asymptomatic COVID-19 infection.

Ultrasound Shear Wave Velocity of Peripheral Nerves: A Possible Non-Invasive Biomarker for Demyelinating Neuropathies.

Dantrolene for the Treatment of Chronic Inflammatory Demyelinating Polyneuropathy-Induced Painful Muscle Spasms: A Case Report.

A&A practice

Rinsho shinkeigaku = Clinical neurology

[Rapidly progressive muscle weakness in anti-myelin associated glycoprotein (MAG) neuropathy successfully treated with intravenous immunoglobulin].

Successfully salvaging a HIV-positive patient with mixed CIDP and meningoencephalitis: a case report.

Frontiers in medicine

Repeated clear benefits of immunotherapy in a patient with Charcot-Marie-Tooth disease carrying a rare point mutation in PMP22.

Neurogenetics

Journal of pediatric hematology/oncology

Tracing a Rare Genetic Disease: Familial Congenital CD59 Deficiency and Carrier Cases Identified Through Village Screening.

Annals of Indian Academy of Neurology

Rare Case of Sjögren's Syndrome with Chronic Inflammatory Demyelinating Polyneuropathy and Atrioventricular Block.

Journal of clinical medicine research

Evaluating Grasp Function in Patients With Chronic Inflammatory Demyelinating Polyneuropathy Using Dynamometers: A Comprehensive Review.

Feasibility and Reliability of a Monitoring App for Chronic Inflammatory Neuropathies.

Utility of Median Nerve Electrophysiological Parameters in Differentiating Immune-Mediated Demyelination From Compressive Median Neuropathy at the Wrist.

Impact of the COVID-19 pandemic on the mental and physical wellbeing of patients with motor neuron disease and other neuromuscular disease.

Orphanet journal of rare diseases

Diagnosis of hereditary transthyretin amyloidosis in patients with suspected chronic inflammatory demyelinating polyneuropathy unresponsive to intravenous immunoglobulins: results of a retrospective study.

Eculizumab as a Disease-Modifying Therapy in Chronic Inflammatory Demyelinating Polyneuropathy (CIDP): A Case Report.

Clinical characteristics of Guillain-Barré syndrome in Shenzhen: a retrospective study.

European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society

Spinal cord stimulation (SCS) induced favorable neuromodulative outcome in the treatment of chronic neuropathic pain syndrome in children.

Unique Nerve Tissue-Restricted T-Cell Clones in Chronic Inflammatory Demyelinating Polyneuropathy.

Chronic Inflammatory Demyelinating Polyneuropathy: A Narrative Review of a Systematic Diagnostic Approach to Avoid Misdiagnosis.

Association Between MScanFit Motor Unit Number Estimation and Clinical Function and Response to Immunoglobulin Therapy in Chronic Inflammatory Demyelinating Polyneuropathy.

Chronic inflammatory demyelinating polyneuropathy associated with active systemic lupus erythematous: Anifrolumab as a potentially successful add-on therapy to intravenous immunoglobulins.

Lupus

[Neurology: what's new in 2024].

Revue medicale suisse

Distinguishing Chronic Inflammatory Demyelinating Polyneuropathy From Mimic Disorders: The Role of Statistical Modeling.

Clinical neurology and neurosurgery

The overlap of diabetic and inflammatory neuropathies: Epidemiology, possible mechanisms, and treatment implications.

Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia

Magnetic resonance imaging in chronic inflammatory demyelinating polyneuropathy (CIDP): Brachial plexus, lumbosacral plexus, and cranial nerve involvement.

Clinical and Electrophysiological Characteristics of 23 French Patients With Neurolymphomatosis.

Ver todos os 1.138 no EuropePMC

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