Distúrbio neurológico raro em que há inflamação das raízes nervosas e nervos periféricos e destruição da cobertura protetora gordurosa (bainha de mielina) sobre os nervos. Isso afeta a rapidez com que os sinais nervosos são transmitidos e leva à perda de fibras nervosas. Isto causa fraqueza, paralisia e/ou comprometimento da função motora, especialmente dos braços e pernas (membros). Distúrbios sensoriais também podem estar presentes. As deficiências motoras e sensoriais geralmente afetam ambos os lados do corpo (simétricas), e o grau de gravidade e o curso da doença podem variar de caso para caso. Alguns indivíduos afetados podem seguir um padrão lento e constante de sintomas, enquanto outros podem apresentar sintomas que se estabilizam e depois recaem.
Introdução
O que você precisa saber de cara
Distúrbio neurológico raro em que há inflamação das raízes nervosas e nervos periféricos e destruição da cobertura protetora gordurosa (bainha de mielina) sobre os nervos. Isso afeta a rapidez com que os sinais nervosos são transmitidos e leva à perda de fibras nervosas. Isto causa fraqueza, paralisia e/ou comprometimento da função motora, especialmente dos braços e pernas (membros). Distúrbios sensoriais também podem estar presentes. As deficiências motoras e sensoriais geralmente afetam ambos os lados do corpo (simétricas), e o grau de gravidade e o curso da doença podem variar de caso para caso. Alguns indivíduos afetados podem seguir um padrão lento e constante de sintomas, enquanto outros podem apresentar sintomas que se estabilizam e depois recaem.
Escala de raridade
<1/50kMuito rara
1/20kRara
1/10kPouco freq.
1/5kIncomum
1/2k
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Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Partes do corpo afetadas
+ 13 sintomas em outras categorias
Características mais comuns
Os sintomas variam de pessoa para pessoa. Abaixo estão as 21 características clínicas mais associadas, ordenadas por frequência.
Linha do tempo da pesquisa
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Genética e causas
O que está alterado no DNA e como passa nas famílias
Nenhum gene associado encontrado
Os dados genéticos desta condição ainda estão sendo catalogados.
Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
Remédios, cuidados de apoio e o que precisa acompanhar
Onde tratar no SUS
Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)
🇧🇷 Atendimento SUS — Polineuropatia desmielinizante inflamatória crônica
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Publicações mais relevantes
Mostrando amostra de 200 publicações de um total de 1.256
Clinical features of chronic inflammatory demyelinating polyneuropathy: a single-center experience with 33 patients.
Chronic inflammatory demyelinating polyneuropathy (CIDP) is an immune-mediated neuropathy with heterogeneous clinical presentations. Although several clinical subtypes, including typical and variants, have been described, evidence regarding their distribution and treatment outcomes remains limited, particularly for CIDP variants. We retrospectively analyzed 33 consecutive patients diagnosed with CIDP at Kumamoto University Hospital between January 2020 and March 2025. Clinical data included demographic characteristics, disease duration, subtype classification, electrophysiological and cerebrospinal fluid (CSF) findings, imaging findings, treatment details, and treatment responsiveness. Subtypes were classified according to the 2021 EAN/PNS diagnostic criteria. Treatment responsiveness was defined as objective improvement confirmed by at least two neurologists. Among the 33 patients, 36.4% had typical CIDP and 63.6% had CIDP variants, including distal (39.4%), multifocal (15.2%), motor (3.0%), and sensory (6.0%) subtypes. Distal CIDP was the most frequent subtype. Patients with multifocal CIDP experienced the longest diagnostic delays (mean, 4.6 years) due to fewer demyelinating findings on electrophysiological studies. The MRC sum score was lowest in typical CIDP, suggesting greater disease severity. Intravenous immunoglobulin (IVIg) demonstrated high efficacy across all subtypes, including multifocal CIDP, in contrast to previous reports of lower responsiveness. During a mean follow-up period of 5.1 years, 78.8% of patients required maintenance therapy, most commonly IVIg and corticosteroids. No changes in clinical subtypes were observed during follow-up. In this single-center study, variants outnumbered typical CIDP, reflecting the case mix at a specialized tertiary referral center. Multifocal CIDP showed the longest diagnostic delays. IVIg demonstrated high efficacy across subtypes, including multifocal CIDP, contrasting with previous reports. These findings highlight the importance of improving diagnostic accuracy and establishing individualized long-term treatment strategies for CIDP.
Clinical and laboratory features of juvenile-onset anti-NF155 autoimmune nodopathy.
Neurofascin 155 autoimmune nodopathy (NF155 AN) is a recently recognised immune-mediated neuropathy distinct from chronic inflammatory demyelinating polyneuropathy. While adult-onset cases have been increasingly reported, the juvenile-onset form remains poorly characterised. We retrospectively analysed 36 patients with NF155 AN, focusing on detailed characterisation of 16 juvenile-onset cases. Their clinical and laboratory data were reviewed. Juvenile-onset patients presented with sensorimotor neuropathy characterised by distal predominant weakness, tremor and sensory ataxia. Motor symptoms were the presenting feature in 75% of patients, which significantly differed from the adult cases (p=0.0015). Postural tremor was more frequent in juvenile patients (94%), while cranial nerve involvement was less common (19%). Electrophysiologically, absent compound muscle action potentials in lower limbs were significantly more prevalent in juvenile patients (peroneal: 78%; tibial: 66%; p<0.001 for both). Symmetrical spinal root/plexus hypertrophy on MR neurography and characteristic pathological findings were observed in both groups. Intravenous immunoglobulin response was generally poor, while delayed rituximab initiation still led to clinical improvement in the juvenile-onset group. Juvenile patients showed trends towards better functional outcomes. Juvenile-onset NF155 AN is distinguished by motor-predominant onset, frequent tremor and characteristic electrophysiological abnormalities, yet demonstrates favourable prognosis with B-cell targeted therapy. Early recognition and timely diagnosis are essential for optimal outcomes.
Non-sensorimotor symptoms in chronic inflammatory demyelinating polyneuropathy.
Chronic inflammatory demyelinating polyneuropathy (CIDP) is defined as a dysimmune disorder of the peripheral nervous system (PNS) resulting in sensorimotor deficits. However, an increasing body of data suggests that CIDP also goes along with features, such as autonomic, circadian, fatigue, mood, and subtle cognitive dysfunctions. Some of these non-sensorimotor symptoms (NSMS) challenge the concept of an exclusive PNS disease. Pragmatically, the high prevalence of NSMS calls for a more holistic disease assessment and surveillance to achieve optimal therapeutic results.
The actual usefulness of culturing apheresis products in hematopoietic stem cell autotransplants.
Bacterial cultures of apheresis products are mandated by FACT-JACIE standards as a safety measure in autologous hematopoietic stem cell transplantation (aHSCT). However, results are often available only after reinfusion, raising questions about their clinical utility, particularly in programs that use fresh, non-cryopreserved products. To evaluate the incidence, microbiological profile, and clinical relevance of positive bacterial cultures in apheresis products used for aHSCT in autoimmune diseases. This prospective study included 629 apheresis products administered to 586 patients with MS or CIDP who underwent outpatient, non-cryopreserved aHSCT between July 2021 and March 2025. Bacterial cultures were performed from product aliquots using the BACTEC system (aerobic and anaerobic bottles). Positive isolates underwent antibiotic susceptibility testing. Culture results, timing of positivity, and 28-day post-infusion outcomes were analyzed. Bacterial contamination was detected in 8 of 629 products (1.3 %). In one case, Escherichia coli was isolated within 24 h, leading to identification of a urinary tract infection and fatal sepsis in the patient; the contaminated product was discarded. The remaining seven cases became positive after 2-11 days (median: 6), when products had already been infused. Isolates included Cutibacterium acnes (n = 6), Staphylococcus capitis (n = 1), and Coryneform bacteria (n = 1). All were considered contamination during aliquot handling. No clinical complications occurred in these patients during the 28-day follow-up. Routine bacterial cultures of apheresis products yielded clinically relevant information in only 1 of 629 procedures. Most positive results reflected contamination of aliquots rather than true product infection, suggesting that the value of routine cultures in fresh aHSCT for autoimmune diseases may be limited and warrants re-evaluation.
Benefits and challenges in everyday life for patients performing subcutaneous immunoglobulin treatment at home: a qualitative interview study.
Across medicine, new therapies are shifting treatment from clinic to home settings. At-home subcutaneous immunoglobulin treatment for immunodeficiency is an example of one such therapy. In this qualitative interview study, we investigated experiences of patients living an everyday life with subcutaneous immunoglobulin at-home treatment. 24 Danish patients participated in semistructured interviews. Six patients were interviewed in individual home-visit interviews, while the remaining 18 participated in one of six subsequent group interviews using an online video format. Participants represented three patient groups: patients with primary immunodeficiency, patients with secondary immunodeficiency, and patients with chronic inflammatory demyelinating polyneuropathy or multifocal motor neuropathy. According to the interviewed patients, at-home treatment provided a high degree of flexibility and freedom in everyday life. When transitioning to at-home treatment, a sense of security had been achieved through individualised training and access to healthcare professionals. Some patients experienced uncertainty or insecurity during the initial period of administering treatment at home; however, this typically receded over time. For the patients, at-home treatment had become embedded in everyday life either through incorporation into existing everyday routines or through the development of new routines. The time-related and place-related flexibility of the at-home treatment had benefits for several arenas of everyday life: work, family, and leisure. Patients associated at-home treatment with a sense of freedom, which they ascribed both to independence from the hospital and to not being confronted with medical conditions and other patients in the hospital setting. A small minority of the patients viewed the reduced contact with healthcare professionals as a disadvantage, describing feelings of being alone and responsible for their treatment. Patients who had established at-home treatment routines in their everyday lives found the benefits of at-home treatment to outweigh the challenges.
Publicações recentes
CRE26-073: A Case of Bortezomib-Induced Demyelinating Polyneuropathy Resembling Chronic Inflammatory Demyelinating Polyneuropathy.
📖 RevisãoQuality of Life in Patients With Chronic Inflammatory Demyelinating Polyneuropathy.
🥈 Ensaio clínicoUltrasonographic, Electrophysiological and Clinical Profiles of Motor and Motor Predominant Chronic Inflammatory Demyelinating Polyneuropathy.
Causal effects of Epstein-Barr virus antibodies on autoimmune neuroinflammatory diseases: A generalised summary data-based Mendelian randomisation study.
Leprosy neuropathy and demyelinating impairment: How should we interpret this neurophysiological pattern?
📚 EuropePMC1.138 artigos no totalmostrando 196
When Foot Drop Tells a Bigger Story: POEMS (Polyneuropathy, Organomegaly, Endocrinopathy, Monoclonal Plasma Cell Disorder, and Skin Changes) Syndrome Revealed by Femoral Plasmacytoma.
CureusClinical Features and Management of Optic Neuritis in a Cohort of Patients with Combined Central and Peripheral Demyelination.
Neuro-ophthalmology (Aeolus Press)Clinical features of chronic inflammatory demyelinating polyneuropathy: a single-center experience with 33 patients.
Frontiers in neurologyDistinct cerebrospinal fluid profiles of astrocytic aquaporin-4 and GFAP in neuroinflammatory disorders.
Neurobiology of diseaseCIDP With and Without Monoclonal Gammopathy of Undetermined Significance (MGUS): Comparison of Clinical Phenotype, Diagnostic Features, and Treatment Response.
Journal of the peripheral nervous system : JPNSBiallelic Variants in RNU6ATAC Result in a Minor Spliceopathy Characterized by Transcriptome-Wide Minor Intron Retention Events and Short Stature with Variable Multisystem Manifestations.
HGG advancesClinical and laboratory features of juvenile-onset anti-NF155 autoimmune nodopathy.
Journal of neurology, neurosurgery, and psychiatryNon-sensorimotor symptoms in chronic inflammatory demyelinating polyneuropathy.
Journal of neurologyRethinking rituximab in neuroimmunology: Real-world efficacy, cost-effectiveness, and long-term remission.
Journal of neuroimmunologyFamilial Occurrence of Anti-NF155 Autoimmune Nodopathy in Father and Son: Expanding the Spectrum of IgG4-Related Nodopathies.
Case reports in neurological medicineA case report of arsenic-induced peripheral neuropathy misdiagnosed as Guillain-Barré syndrome.
Frontiers in toxicologyPlasma neurofilament light chain is associated with clinical instability in chronic autoimmune neuropathies.
Scientific reportsGenetic risk of chronic pain conditions associated with risk of suicide death through an integrative analysis of EHR and genomics data.
Translational psychiatryReal-world treatment utilization in adults with chronic inflammatory demyelinating polyneuropathy in the United States.
Frontiers in neurologyCAR-T manufacturing reduces heterogeneity between CIDP and multiple myeloma patient-derived T cells.
TheranosticsCase-Based Lessons on Remote Patient Monitoring in Neurology Using Consumer-Grade Wearables.
Journal of central nervous system diseasePOEMS syndrome with cardiovascular lesions as the initial manifestation: a case report and literature review.
Frontiers in cardiovascular medicineThe actual usefulness of culturing apheresis products in hematopoietic stem cell autotransplants.
Transfusion and apheresis science : official journal of the World Apheresis Association : official journal of the European Society for HaemapheresisSubacute cutaneous lupus erythematosus secondary to intravenous immunoglobulin therapy for chronic inflammatory demyelinating polyneuropathy: A case report.
JAAD case reportsElucidating Causal Associations Between Immune Cells, Circulating Inflammatory Proteins, and Chronic Inflammatory Demyelinating Polyneuropathy: A Two-Sample Two-Step Mendelian Randomization Study.
Journal of the peripheral nervous system : JPNSChronic Inflammatory Demyelinating Polyneuropathy Following Adalimumab Therapy for a Patient with Intestinal Behçet's Disease.
Digestive diseases and sciencesSuccessful Treatment of Multifocal Demyelinating Sensory-Motor Neuropathy (Lewis-Sumner Syndrome) With Rituximab: A Case Report.
The American journal of case reportsBenefits and challenges in everyday life for patients performing subcutaneous immunoglobulin treatment at home: a qualitative interview study.
BMJ openCombined Central and Peripheral Demyelination with a Favorable Outcome: A Case with 10-Year Follow-up.
Noro psikiyatri arsiviCorneal confocal microscopy as a paraclinical test in neurodegenerative disease: a scoping review.
The British journal of ophthalmologyGenetic and metabolic inflammation signatures in chronic inflammatory demyelinating polyneuropathy: the role of IL18 polymorphisms and short-chain fatty acids.
Frontiers in molecular neuroscienceCase report: Efgartigimod treatment in two pediatric patients with chronic inflammatory demyelinating polyneuropathy.
Frontiers in immunologyBlood-Nerve Barrier Breakdown Induced by Immunoglobulin G in Typical and Multifocal Chronic Inflammatory Demyelinating Polyneuropathy and Multifocal Motor Neuropathy.
International journal of molecular sciencesPractical Approach to Managing SCIg Treatment in Patients With Chronic Inflammatory Demyelinating Polyneuropathy.
Muscle & nerveConduction Block Detection in Dysimmune Neuropathy: Hypothetical Pathophysiological 'Truth' Versus Clinical Pragmatism.
European journal of neurologyCharacteristics of adverse events and clinical risks of intravenous immunoglobulin: a pharmacovigilance study based on FDA Adverse Event Reporting System (FAERS).
Frontiers in medicineEvaluating the short-term and long-term therapeutic effects of immunoadsorption compared with plasma exchange in chronic inflammatory demyelinating polyneuropathy: a long-term, prospective, observational study.
EClinicalMedicineNeurological Complications Associated With COVID-19 Compared to Other Viral Infections: A Systematic Review of Current Evidence.
CureusCost Analysis of Immunoglobulin Maintenance Treatment of Patients with Chronic Inflammatory Demyelinating Polyneuropathy in Spain.
PharmacoEconomics - openImmunotherapies on Guillain-Barré syndrome and other acute autoimmune neuropathies.
Handbook of clinical neurologyFcRn inhibitors: A new era in neurotherapeutics.
Handbook of clinical neurologyIncidence, Prevalence, and Treatment Patterns in Chronic Inflammatory Demyelinating Polyneuropathy: Data Analysis of US Claims.
NeuroepidemiologySignificance of aberrant nerve conduction in hereditary transthyretin amyloidosis.
Amyloid : the international journal of experimental and clinical investigation : the official journal of the International Society of AmyloidosisBiopsy of the Superficial Sensory Radial Nerve in the Distal Forearm: A Technical Note.
CureusDISTRICTS trial: enhancing carpal tunnel syndrome treatment - Authors' reply.
Lancet (London, England)Efficacy, Safety, and Tolerability of Subcutaneous Efgartigimod PH20 in Chinese Patients With Chronic Inflammatory Demyelinating Polyneuropathy: A Prespecified Subpopulation Analysis of the Multicentre, Randomised-Withdrawal, Double-Blind, Placebo-Controlled, Phase II ADHERE Trial.
Journal of clinical neurology (Seoul, Korea)Immunotherapy in Chronic Inflammatory Demyelinating Polyneuropathy and the Emerging Role of Efgartigimod.
Journal of clinical neurology (Seoul, Korea)Paraneoplastic neurological syndrome with Guillain-Barré syndrome overlap in small-cell lung carcinoma: A case report from a primary care hospital in China.
MedicineAberrant Complement Activation Is a Prominent Feature of Chronic Inflammatory Demyelinating Polyneuropathy.
Neurology(R) neuroimmunology & neuroinflammationPersistent COVID-19 Pneumonia in a Patient on Rituximab.
Journal of investigative medicine high impact case reportsShaping the role of plasma exchange in autoimmune neurology: lessons learned from 67 years and over 90,000 procedures.
Therapeutic advances in neurological disordersEfficacy of intravenous immunoglobulin in patients with chronic inflammatory demyelinating polyneuropathy with or without diabetes: insights from a multicenter prospective comparative study.
Therapeutic advances in neurological disordersChronic Inflammatory Demyelinating Polyneuropathy Presenting With Isolated Distal Fingertip Paresthesia in a Factory Worker With Ulcerative Colitis: A Case Report.
CureusOcular and Neuro-Ophthalmic Manifestations of Chronic Inflammatory Demyelinating Polyneuropathy.
International ophthalmology clinicsHighly Immunoresistant Acute Motor and Sensory Axonal Neuropathy With Concomitant Anti-NF155 Axonal Nodopathy: A Case Report.
CureusExperiences of Immunoglobulin Therapy for Those with a Confirmed Diagnosis of Chronic Inflammatory Demyelinating Polyneuropathy: A Mixed-Methods Study with a Qualitative Patient Perspective Focus.
Patient preference and adherenceIntermittent immunoadsorption in critically ill patients with neuroimmunological disorders: a retrospective study.
Frontiers in neurologyAutoimmune Neuromuscular Disorders at a Molecular Crossroad: Linking Pathogenesis to Targeted Immunotherapy.
International journal of molecular sciencesA combined approach of Interleukin-8 and magnetic resonance neurography to differentiate Guillain-Barré syndrome and chronic inflammatory demyelinating polyneuropathy.
Journal of the neurological sciencesCase Report: Secondary myelodysplastic syndrome following autologous stem cell transplantation in a patient with POEMS syndrome.
Frontiers in immunologyCharacterizing Treatment Patterns and Healthcare Use in Patients and Subgroups with Chronic Inflammatory Demyelinating Polyradiculoneuropathy: A Real-World Study.
Neurology and therapyAutoimmune neuropathies: New guidelines and expert insights into clinical decision making.
Journal of the neurological sciencesClinical, serological, and electrophysiological differences in chronic inflammatory demyelinating polyradiculoneuropathy patients with and without malignancy - real-life evidence.
Neurologia i neurochirurgia polskaCase Report: Staged bilateral pancarpal arthrodesis using 3D-printed patient specific guides and customized hybrid plate for severe carpal joint instability associated with chronic inflammatory demyelinating polyneuropathy in a miniature dachshund.
Frontiers in veterinary scienceDeep Learning-Assisted Differentiation of Four Peripheral Neuropathies Using Corneal Confocal Microscopy.
Annals of clinical and translational neurologyEfficacy and safety of intravenous efgartigimod for chronic inflammatory demyelinating polyneuropathy: A case series real-world study.
Journal of neuroimmunologyClinical Utility of Serum Neurofilament Light Chain in Peripheral Neuropathy.
Muscle & nerveWearable Monitoring Captures Sleep Disturbances in Patients With Chronic Inflammatory Demyelinating Polyneuropathy.
Journal of the peripheral nervous system : JPNS[POEMS syndrome: A complex diagnostic case under the guise of chronic polyneuropathy].
Zhurnal nevrologii i psikhiatrii imeni S.S. KorsakovaVery High Dose Immunoglobulin Treatment for Chronic Inflammatory Demyelinating Polyneuropathy: A Multicentre UK Study.
European journal of neurologySwitch from Intravenous to Subcutaneous Immunoglobulin in CIDP and MMN: 12 Months Results from an Observational Study.
Neurology and therapyAn Evaluation of the Real-World Effectiveness of Immunoglobulin Therapy in Chronic Inflammatory Demyelinating Polyneuropathy.
Neurology and therapyCognitive impairment in chronic inflammatory demyelinating polyneuropathy.
Journal of neurologyRecurrent Guillain-Barré Syndrome: A Case Report and Literature Review.
CureusEffectiveness and safety of therapeutic plasma exchange in neurological disorders; measuring the response to treatment using Modified Rankin Scale - A single-center study.
Asian journal of transfusion scienceAXIN1, STAMBP, ST1A1, CDCP1, and SIRT2 Validated as Myasthenia Gravis Biomarkers: A Comparative Proteomic Study With MS, CIDP, and Controls.
European journal of neurologyDiffusion Tensor Imaging Reveals Altered Centrality of Pain-Related Regions in SCN9A-Associated Small Fiber Neuropathy.
Journal of neuroimaging : official journal of the American Society of NeuroimagingBurstDR spinal cord stimulation for chronic inflammatory demyelinating polyneuropathy.
Surgical neurology internationalDelayed treatment and diagnostic challenges in differentiating multifocal acquired demyelinating sensory and motor neuropathy from lupus: a case report and literature review.
AME case reportsAbnormal Sleep in Chronic Inflammatory Demyelinating Polyneuropathy.
European journal of neurologyIntravenous immunoglobulin weaning evaluation with zero-shot large language model classification.
Transfusion medicine (Oxford, England)The potential role of IgG subclass in NF155-associated nodopathy for targeting therapy: a pediatric case report highlighting the efficacy of pulsed oral corticosteroids.
BMC neurologyImmune-Mediated Neuropathies Other Than Typical Chronic Inflammatory Demyelinating Polyradiculoneuropathy-Multifocal Motor Neuropathy, Autoimmune Nodopathies, Anti-Myelin Associated Glycoprotein Neuropathy, Chronic Inflammatory Sensory Polyradiculoneuropathy, and Chronic Ataxic Neuropathy with Ophthalmoplegia, M-Protein, Agglutinin, and Disialosyl Antibodies.
Neurologic clinicsChronic Inflammatory Demyelinating Polyneuropathy and Variants.
Neurologic clinicsInnate Immunity in the Pathogenesis of Selected Autoimmune Neurological Diseases.
Journal of clinical medicineMotor and Cognitive Fatigue in Chronic Inflammatory Demyelinating Polyneuropathy.
European journal of neurologyNerve Ultrasound in Pediatric Polyneuropathies: A Systematic Review.
NeuropediatricsChimeric Antigen Receptor (CAR) T Cell Therapy for Neuromuscular Disorders: A Systematic Review.
CureusCoexistence of Acute Demyelinating Polyneuropathy and LRP4-Positive Myasthenia Gravis.
Case reports in neurological medicineA Rare Case of Concomitant Fibrillary Glomerulonephritis and Membranous Nephropathy in a Patient With Chronic Inflammatory Demyelinating Polyneuropathy.
CureusChronic inflammatory demyelinating polyneuropathy (CIDP) after cilta-cel therapy.
Blood cancer journal[A case of adult-onset Krabbe disease diagnosed by galactocerebrosidase gene mutations, presenting with an atypical phenotype].
Rinsho shinkeigaku = Clinical neurologyAnti-pan-neurofascin IgG3: insights about an emerging autoimmune nodoparanodopathy.
Arquivos de neuro-psiquiatriaClinical Spectrum, Pathology, and Mechanisms of Anti-LGI4 Antibody-Positive Autoimmune Nodopathy.
Neurology(R) neuroimmunology & neuroinflammationExacerbation of demyelinating polyneuropathy after adoptive cell therapy with tumour-infiltrating lymphocytes by metastatic melanoma.
Swiss medical weeklyEfficacy of Tacrolimus Plus Prednisone as Long-Term Immunosuppressive Therapy for Chronic Inflammatory Demyelinating Polyneuropathy: A Retrospective Cohort Study.
ImmunoTargets and therapyTemporal Association Between Dengue Outbreaks and Neurologic Autoimmune Diseases in French Guiana.
Neurology(R) neuroimmunology & neuroinflammationHereditary Neuropathy with Liability to Pressure Palsies Mimicking a Chronic Inflammatory Demyelinating Polyneuropathy Variant: A Case Report Highlighting Diagnostic Challenges.
Internal medicine (Tokyo, Japan)Comparison of the presentation and electrophysiological characteristics of autoimmune nodopathies in patients with antibody-negative CIDP and CMT1.
Frontiers in neurologyImpact of Physical Exercise Programs on Fatigue and Functional Capacity in People With Guillain-Barré Syndrome and Chronic Inflammatory Demyelinating Polyneuropathy: A Systematic Review.
Archives of physical medicine and rehabilitationA Novel Cause of CIDP: Homozygous Hotspot Mutation, c.793 C > T in CASP8 Gene.
Journal of clinical immunologyDevelopment of a PROM set for patients with Guillain-Barré syndrome (GBS) and chronic inflammatory demyelinating polyneuropathy (CIDP): study protocol.
Health and quality of life outcomesAtypical diabetic neuropathies.
BMJ (Clinical research ed.)Polyradiculoneuropathies associated with immune checkpoint inhibitors: are we facing a new nosological entity?
Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical NeurophysiologyEpidemiology, Presentation, Management and Outcomes in Chronic Inflammatory Demyelinating Polyneuropathy in Birmingham, UK: The Impact of Ethnicity.
Journal of the peripheral nervous system : JPNSPOEMS Syndrome Without a Detectable Monoclonal Peak: The Critical Role of VEGF and Bone Marrow Biopsy in Diagnosis.
Case reports in hematologyHumoral Immune Response Following COVID-19 Vaccination in Multifocal Motor Neuropathy and Chronic Inflammatory Demyelinating Polyneuropathy.
VaccinesOrbital apex-like syndrome with multiple cranial neuropathies secondary to chronic inflammatory demyelinating polyneuropathy.
Orbit (Amsterdam, Netherlands)Feasibility of Outpatient Transforaminal Lumbar Interbody Fusion (TLIF) in Chronic Inflammatory Demyelinating Polyneuropathy: A Case Report.
CureusPlasma lipidomic patterns associated with disease activity in chronic inflammatory demyelinating polyradiculoneuropathy (LIPID-CIDP).
Journal of lipid researchComplement profiling of sural nerves in chronic-inflammatory demyelinating polyneuropathy.
Acta neuropathologicaFeasibility of Subcutaneous Immunoglobulin Therapy as the Maintenance Therapy in Patients with Autoimmune Neuromuscular Disease: A Prospective Study.
The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiquesNatural Pregnancy Following Oocyte Retrieval in a Luteal-Phase Progestin-Primed Ovarian Stimulation (PPOS) Protocol With Concurrent Blastocyst Cryopreservation: A Case Report.
CureusNeuronal inflammation-associated biomarkers in cerebrospinal fluid of patients with acute and chronic inflammatory demyelinating polyneuropathies.
Journal of neuroimmunologyTargeting BCMA in CIDP: Valuable insights gained through multi-omics immune monitoring.
Med (New York, N.Y.)Autologous haematopoietic stem cell transplantation in non-MS neuroimmunological diseases.
Multiple sclerosis and related disorders5-Aminolevulinic Acid Ameliorates Chronic Experimental Autoimmune Neuritis Through a Dual Mechanism of Mitochondrial Protection and Immunomodulation.
International journal of molecular sciencesPOEMS Syndrome Masquerading as Metastatic Prostate Cancer Based on PSMA Avid Lesions.
Case reports in hematologyA new screening tool for early recognition of ATTRv polyneuropathy in clinical practice: AmyloScan®.
Journal of neurologyQuality of Life in Patients with Chronic Inflammatory Demyelinating Neuropathies Treated with Subcutaneous Immunoglobulin.
The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiques[AQP4 positive neuromyelitis optica spectrum disorder: an atypical pathology with nerve root enlargement and peripheral nervous system damage in demyelination].
Rinsho shinkeigaku = Clinical neurologyOutcome measures in CIDP: A scoping and mapping review.
Journal of the neurological sciencesB Cell Tolerance and BCR Signaling Dysregulation in NF155-Mediated Autoimmune Nodopathies.
bioRxiv : the preprint server for biologyReal-World Multinational Survey of Chronic Inflammatory Demyelinating Polyneuropathy: Disease Characteristics and Therapeutic Landscape.
Journal of the peripheral nervous system : JPNSTipping the balance: the PD1-axis as a modulator in chronic inflammatory demyelinating polyneuropathy.
Brain : a journal of neurologyChildhood POLG-related disorders: Focus on polyradiculoneuropathy.
Molecular genetics and metabolismImpact of Social Deprivation on Diagnosis, Management and Outcome of Chronic Inflammatory Demyelinating Polyneuropathy at a Tertiary UK Centre.
Journal of the peripheral nervous system : JPNSChronic inflammatory demyelinating polyneuropathy complicated by pre-eclampsia progressing to HELLP syndrome and pulmonary embolism: A case report.
Case reports in women's healthRandom X chromosome inactivation in female Charcot-Marie-Tooth disease type X1: insights from sural nerve biopsy analysis.
BMC neurologyCAR T-cells meet autoimmune neurological diseases: a new dawn for therapy.
Frontiers in immunologyClinical and Genetic Reassessment in Patients With Clinically Diagnosed Hereditary Polyneuropathy.
European journal of neurologyControversies in the diagnosis of chronic inflammatory demyelinating polyneuropathy.
Current opinion in neurologyAn auxiliary diagnostic strategy for distinguishing Guillain-Barré syndrome and chronic inflammatory demyelinating polyneuropathy: combining platelet-to-lymphocyte ratio and cerebrospinal fluid interleukin-8 levels.
BMC neurologyGenetic susceptibility of human leukocyte antigen alleles in chronic inflammatory demyelinating polyneuropathy in Korean patients : Short title: HLA alleles and CIDP in Korea.
BMC neurologyMinimal Clinically Important Differences in Measuring Treatment Effects in CIDP: History, Current Use, Limitations, and Prospects.
Muscle & nerveExploring Ultrasonographic Atypical Aspects in Drug-Resistant Multifocal Chronic Inflammatory Demyelinating Polyneuropathy.
Brain and behaviorExtracorporeal therapy procedures (plasma exchange and immunoadsorption) in chronic inflammatory demyelinating polyneuropathies (CIDP)- a database analysis.
BMC neurologyDigital biomechanical assessment of gait in patients with peripheral neuropathies.
Journal of neuroengineering and rehabilitationBlood bile acid profiles in chronic inflammatory demyelinating polyneuropathy.
Clinica chimica acta; international journal of clinical chemistryNervous Breakdown: Chronic Inflammatory Demyelinating Polyneuropathy as an Extra-Intestinal Manifestation of Ulcerative Colitis.
Digestive diseases and sciencesDigital Activity Markers in Chronic Inflammatory Demyelinating Polyneuropathy.
Annals of clinical and translational neurologyNerve conduction study and nerve ultrasound as biomarkers for steroid dependence in chronic inflammatory demyelinating polyneuropathy.
Neurological researchElectrophysiological-based automatic subgroups diagnosis of patients with chronic dysimmune polyneuropathies.
Journal of neuroengineering and rehabilitationWhole-Body Magnetic Resonance Neurography-Technique, Current Perspectives, and Future Directions.
Magnetic resonance imaging clinics of North AmericaWhere Does It All Itch? Exploring the Characteristics of Pruritus in Small Fiber Neuropathy.
Journal of the peripheral nervous system : JPNSComparison of imaging markers of nerve ultrasound and MR-neurography in a longitudinal course in chronic inflammatory demyelinating polyneuropathy.
Therapeutic advances in neurological disordersCase Report: Post-surgical Guillain-Barré syndrome as a rare differential diagnosis of flaccid paralysis of the lower extremities in an infant after cardiac surgery.
Frontiers in pediatricsStiff tongue syndrome and multifocal immune neuropathy in a young man with anti-glutamic acid decarboxylase and unclassified antibodies.
BMJ case reportsChronic Inflammatory Demyelinating Polyneuropathy and Concurrent Membranous Nephropathy Associated With Anti-Contactin-1 Autoantibodies: A Rare Case Report With a Review of the Literature.
CureusChronic inflammatory demyelinating polyneuropathy in end-stage renal disease patients: a case series study.
Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical NeurophysiologyNerve Ultrasound of Multifocal Motor Neuropathy and Motor and Typical Chronic Inflammatory Demyelinating Neuropathy.
The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiquesSystematic Review: Mental Health Outcomes in Guillain-Barré Syndrome and Chronic Inflammatory Demyelinating Polyneuropathy.
The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiquesSerum Neurofilament Light Chain as a Biomarker for CIDP Diagnosis, Severity, and Treatment Outcome.
Neurology(R) neuroimmunology & neuroinflammationInverse relation between serum neurofilament light chain and cognitive function in chronic inflammatory demyelinating polyneuropathy.
Journal of neurologySevere Worsening of Neuropathy Associated With Antibodies Against Myelin-Associated Glycoprotein by Rituximab Resembling Chronic Inflammatory Demyelinating Polyneuropathy.
CureusRole of Imaging in Chronic Inflammatory Demyelinating Polyneuropathy: A Systematic Review.
European journal of neurologyPeripheral neuropathies associated with anti-tnf-α treatments: a systematic review and proposed recommendations.
Journal of neurologyA highly sensitive quantitative method of polysialic acid reveals its unique changes in brain aging and neuropsychiatric disorders.
Scientific reportsSulfatide antibody-mediated neuropathy: an analysis of clinical characteristics and immunotherapeutic responses.
Neurological researchObjective assessments for walking aid prescription in balance impairment and falls risk: a scoping review of current evidence.
Disability and rehabilitation. Assistive technologyAnti-BCMA CAR-T cell therapy in relapsed/refractory chronic inflammatory demyelinating polyneuropathy.
Med (New York, N.Y.)Validity and Responsiveness of Balance Measurements Using Posturography in Patients With Immune-Mediated Neuropathies.
Journal of the peripheral nervous system : JPNSWhipple Disease Initial Presentation as Supraclavicular Lymphadenopathy in a Patient With Rheumatoid Arthritis: A Diagnostic Challenge.
International journal of surgical pathologyFocal Chronic Inflammatory Demyelinating Polyneuropathy - A Case Report with Clinical Application and Validation of 2021 European Academy of Neurology/Peripheral Nerve Society Criteria.
Acta neurologica TaiwanicaChronic Inflammatory Demyelinating Polyneuropathy: How Pathophysiology Can Guide Treatment.
Muscle & nerveCase Report: A case of subacute combined degeneration of the spinal cord associated with chronic atrophic gastritis, macrocytic anemia, and positive anti-sulfatide IgM and IgG antibodies.
Frontiers in immunologyChronic Inflammation: A Multidisciplinary Analysis of Shared Pathways in Autoimmune, Infectious, and Degenerative Diseases.
CureusReviewer Comment on Li et al.: "Systematic review: mental health outcomes in Guillain-Barre syndrome and chronic inflammatory demyelinating polyneuropathy".
The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiquesPatient-Reported Outcome Measures for Assessing Health-Related Quality of Life in Patients With Polyneuropathies, Focusing on Guillain-Barré Syndrome and Chronic Inflammatory Demyelinating Polyneuropathy: A Systematic Review of Measurement Properties.
Journal of the peripheral nervous system : JPNSChronic Inflammatory Demyelinating Polyneuropathy Following Natural Influenza A Infection in a Pediatric Patient: A Case Report and Literature Review.
Case reports in neurological medicineSyncope and New-Onset Bifascicular Block Associated With Intravenous Immunoglobulin in a Patient With Chronic Inflammatory Demyelinating Polyneuropathy.
CureusPatient Experience of Chronic Inflammatory Demyelinating Polyneuropathy (CIDP): A Qualitative Exploration of Signs, Symptoms, and Health-Related Quality of Life Impacts.
Neurology and therapyIncomplete Presentations in Typical Chronic Inflammatory Demyelinating Polyneuropathy: A Single-Center, Retrospective Study.
Muscle & nervePlasma cell myeloma with an evolving diagnostic complexity: A case report.
Oncology lettersA Rare Presentation of Patient With CIDP Found to Have Respiratory Failure and Encephalopathy.
Case reports in critical careUnmasking the mimic: Leprosy neuropathy misdiagnosed as chronic inflammatory demyelinating polyneuropathy: A case report from Saudi Arabia.
Neurosciences (Riyadh, Saudi Arabia)Acute-onset chronic inflammatory demyelinating polyneuropathy in a 23-year-old male exacerbated by an asymptomatic COVID-19 infection.
Current research in translational medicineUltrasound Shear Wave Velocity of Peripheral Nerves: A Possible Non-Invasive Biomarker for Demyelinating Neuropathies.
Journal of the peripheral nervous system : JPNSDantrolene for the Treatment of Chronic Inflammatory Demyelinating Polyneuropathy-Induced Painful Muscle Spasms: A Case Report.
A&A practice[Rapidly progressive muscle weakness in anti-myelin associated glycoprotein (MAG) neuropathy successfully treated with intravenous immunoglobulin].
Rinsho shinkeigaku = Clinical neurologySuccessfully salvaging a HIV-positive patient with mixed CIDP and meningoencephalitis: a case report.
Frontiers in medicineRepeated clear benefits of immunotherapy in a patient with Charcot-Marie-Tooth disease carrying a rare point mutation in PMP22.
NeurogeneticsTracing a Rare Genetic Disease: Familial Congenital CD59 Deficiency and Carrier Cases Identified Through Village Screening.
Journal of pediatric hematology/oncologyRare Case of Sjögren's Syndrome with Chronic Inflammatory Demyelinating Polyneuropathy and Atrioventricular Block.
Annals of Indian Academy of NeurologyEvaluating Grasp Function in Patients With Chronic Inflammatory Demyelinating Polyneuropathy Using Dynamometers: A Comprehensive Review.
Journal of clinical medicine researchFeasibility and Reliability of a Monitoring App for Chronic Inflammatory Neuropathies.
Journal of the peripheral nervous system : JPNSUtility of Median Nerve Electrophysiological Parameters in Differentiating Immune-Mediated Demyelination From Compressive Median Neuropathy at the Wrist.
Muscle & nerveImpact of the COVID-19 pandemic on the mental and physical wellbeing of patients with motor neuron disease and other neuromuscular disease.
Frontiers in neurologyDiagnosis of hereditary transthyretin amyloidosis in patients with suspected chronic inflammatory demyelinating polyneuropathy unresponsive to intravenous immunoglobulins: results of a retrospective study.
Orphanet journal of rare diseasesEculizumab as a Disease-Modifying Therapy in Chronic Inflammatory Demyelinating Polyneuropathy (CIDP): A Case Report.
Journal of the peripheral nervous system : JPNSClinical characteristics of Guillain-Barré syndrome in Shenzhen: a retrospective study.
BMC neurologySpinal cord stimulation (SCS) induced favorable neuromodulative outcome in the treatment of chronic neuropathic pain syndrome in children.
European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology SocietyUnique Nerve Tissue-Restricted T-Cell Clones in Chronic Inflammatory Demyelinating Polyneuropathy.
Journal of the peripheral nervous system : JPNSChronic Inflammatory Demyelinating Polyneuropathy: A Narrative Review of a Systematic Diagnostic Approach to Avoid Misdiagnosis.
CureusAssociation Between MScanFit Motor Unit Number Estimation and Clinical Function and Response to Immunoglobulin Therapy in Chronic Inflammatory Demyelinating Polyneuropathy.
Journal of the peripheral nervous system : JPNSChronic inflammatory demyelinating polyneuropathy associated with active systemic lupus erythematous: Anifrolumab as a potentially successful add-on therapy to intravenous immunoglobulins.
Lupus[Neurology: what's new in 2024].
Revue medicale suisseDistinguishing Chronic Inflammatory Demyelinating Polyneuropathy From Mimic Disorders: The Role of Statistical Modeling.
Journal of the peripheral nervous system : JPNSThe overlap of diabetic and inflammatory neuropathies: Epidemiology, possible mechanisms, and treatment implications.
Clinical neurology and neurosurgeryMagnetic resonance imaging in chronic inflammatory demyelinating polyneuropathy (CIDP): Brachial plexus, lumbosacral plexus, and cranial nerve involvement.
Journal of clinical neuroscience : official journal of the Neurosurgical Society of AustralasiaClinical and Electrophysiological Characteristics of 23 French Patients With Neurolymphomatosis.
Muscle & nerveAssociações
Organizações que acompanham esta doença — pra ter apoio e orientação
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Clinical features of chronic inflammatory demyelinating polyneuropathy: a single-center experience with 33 patients.
- Clinical and laboratory features of juvenile-onset anti-NF155 autoimmune nodopathy.
- Non-sensorimotor symptoms in chronic inflammatory demyelinating polyneuropathy.
- The actual usefulness of culturing apheresis products in hematopoietic stem cell autotransplants.Transfusion and apheresis science : official journal of the World Apheresis Association : official journal of the European Society for Haemapheresis· 2026· PMID 41687157mais citado
- Benefits and challenges in everyday life for patients performing subcutaneous immunoglobulin treatment at home: a qualitative interview study.
- CRE26-073: A Case of Bortezomib-Induced Demyelinating Polyneuropathy Resembling Chronic Inflammatory Demyelinating Polyneuropathy.
- Quality of Life in Patients With Chronic Inflammatory Demyelinating Polyneuropathy.
- Ultrasonographic, Electrophysiological and Clinical Profiles of Motor and Motor Predominant Chronic Inflammatory Demyelinating Polyneuropathy.
- Causal effects of Epstein-Barr virus antibodies on autoimmune neuroinflammatory diseases: A generalised summary data-based Mendelian randomisation study.
- Leprosy neuropathy and demyelinating impairment: How should we interpret this neurophysiological pattern?
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:2932(Orphanet)
- MONDO:0006702(MONDO)
- GARD:6102(GARD (NIH))
- Busca completa no PubMed(PubMed)
- Q1088030(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
