A Retrospective Analysis of Dengue-associated Hemophagocytic Lymphohistiocytosis in a Dengue-endemic Country.

Retrospective study: clinical analysis of Kawasaki disease complicated with macrophage activation syndrome.

IL12-engineered human PSMA-CAR T cells for the treatment of advanced prostate cancer.

[Clinical Manifestations of Childhood Systemic Lupus Erythematosus-associated Acute Pancreatitis and Evaluation of the Efficacy of Plasma Exchange Combined With Glucocorticoids].

Clinical characteristics and diagnostic indicators of childhood-onset systemic lupus erythematosus complicated with macrophage activation syndrome.

Predictive value for intravenous immunoglobulin resistance of Kobayashi and Kawanet scores in 722 children with Kawasaki disease across diverse ethnic backgrounds (KIWI study): an international cohort study.

2016 sJIA-MAS criteria and a step-up therapeutic approach in KD-MAS: insights from a combined cohort and literature review.

Is a variant of uncertain significance always 'insignificant'? A systematic review on PRF1 A91V in Hemophagocytic Lymphohistocytosis and comparative analysis with Still's disease.

Adjunctive Therapeutic Plasma Exchange in Refractory Adult-Onset Still's Disease Complicated by Secondary Macrophage Activation Syndrome: A Single-Center Experience.

Frequency, Characteristics, Management, and Outcomes of Posttransplant Lymphoproliferative Disorder After Allogeneic Hematopoietic Stem Cell Transplantation in Children: A Multicentre Retrospective Study of the Turkish Pediatric BMT Study Group.

A case of VEXAS syndrome presenting as macrophage activation syndrome: from chronic inflammation to multi-organ failure.

Origin, diagnosis and treatment of periocular Histiocytic disorders- state-of-the-art review.

Childhood-Onset Systemic Lupus Erythematosus Research over the Past Decade in Japan.

Transition of serum-free IL-18 levels in systemic juvenile idiopathic arthritis measured by a novel detection method.

Serum calprotectin elevation and interferon-α-induced neutrophil priming in macrophage activation syndrome associated with systemic lupus erythematosus: clinical and experimental insights.

Drug-induced liver injury secondary to anakinra in a patient with systemic juvenile idiopathic arthritis-Case report and literature overview.

Diagnostic Complexity in Systemic Inflammation: Adult-Onset Still's Disease.

Refractory macrophage activation syndrome in adult-onset Still's disease: response to interferon-γ blockade and JAK inhibition.

A Case of Refractory Adult-Onset Still Disease With Macrophage Activation Syndrome and Pulmonary Alveolar Proteinosis.

Identifying novel biomarkers for systemic lupus erythematosus associated with macrophage activation syndrome.

[Macrophage activation syndrome in a young patient with polymyositis].

Adult-Onset Still's Disease(AOSD) With Features Suggestive of Macrophages Activation Syndrome in Young Female: A Rare Case Report From Nepal.

Hemophagocytic Lymphohistiocytosis and Infections in Children: An Update.

Type I Interferon Signature is Associated With Lung Disease, Drug-Associated Immune Reactions, and Genetic Variation in Interferon-Linked Pathways in Still Disease.

[Musculoskeletal Complications in Rheumatic Diseases].

Clinical features and comorbidities of Epstein-Barr virus infection in childhood-onset systemic lupus erythematosus with a focus on macrophage activation syndrome: a cross-sectional study of 200 patients.

Unmasking Hemophagocytic Lymphohistiocytosis After Minimal Tumor Necrosis Factor-Alpha (TNF-α) Blockade: An Interplay of Contributing Elements.

Clinically validated assay for rapid determination of type I and type II interferon activity in systemic inflammatory diseases.

Still's Disease and Autoinflammation: Positioning an Inflammatory Syndrome on the Autoinflammation-Autoimmunity Spectrum.

An Unprecedented Triad: Simultaneous Acute Pancreatitis, Axonal Polyneuropathy, and Type 1 Diabetes Mellitus in a Catastrophic Juvenile Lupus Flare.

Macrophage Activation Syndrome-Associated Proteins and Enhanced Interferon-γ Responsiveness in the Plasma Proteome of Patients With Multisystem Inflammatory Syndrome in Children in a Pretreatment Replication Single-Center Cohort.

Macrophage Activation Syndrome Associated with Adult-onset Still's Disease Successfully Treated with Plasma Exchange and Canakinumab: A Case Report.

Safety and Effectiveness of Canakinumab in Patients with Systemic Juvenile Idiopathic Arthritis in Japan: A Post-Marketing Surveillance Study.

Advancing Precision Medicine in Adult-Onset Still's Disease: Insights into Biomarkers, Therapies, and COVID-19 Impacts.

[Hemophagocytic lymphohistiocytosis].

An Unusual Case of Juvenile Dermatomyositis Complicated by Macrophage Activation Syndrome.

Spiroplasma infection complicated by macrophage activation syndrome and fulminant hepatitis in a kidney transplant recipient.

Association of NXP2 autoantibodies with a more severe clinical phenotype of juvenile dermatomyositis.

Adult-Onset Still's Disease Presenting with Atypical Kikuchi-Fujimoto Disease-Like Histiocytic Necrotizing Lymphadenitis: A Diagnostic Pitfall.

Utility of systemic score as a prognosis marker and biologic treatment indication in adults with Still's disease.

[Interferon scores in the management of rheumatic systemic diseases].

Macrophage Activation Syndrome Following Vaccination After HSCT.

[Unusual presentation of Crohn disease associated with hemophagocytic lymphohistiocytosis syndrome: a case report].

Unusual Cardiac Complication in Still's Disease: MAS-Induced Cardiogenic Shock.

Lupus mastitis heralding macrophage activation syndrome: Case report and systematic review of the literature.

Multisystem Inflammatory Syndrome in Children with tailored therapy and six-month outcome.

A Review of Adenosine Deaminase 2 (ADA2) as a Biomarker of Monocyte/Macrophage Activation.

Rescue Therapy With Continuous Intravenous Anakinra Infusion and Plasma Exchange in Refractory Cytokine Storm of Systemic JIA: A Case Report.

Hemophagocytic Lymphohistiocytosis (HLH) or Macrophage Activation Syndrome (MAS)? A Lethal Case of Malignancy-Associated Hemophagocytic Lymphohistiocytosis in a Patient With Concurrent Autoimmune Disease.

Clinical Practice Variation Among Pediatric Rheumatologists Treating Kawasaki Disease: Results of a North American Survey.

Not Just Sjögren's: A Rare Life-Threatening Manifestation in a Pediatric Patient.

TLR9 decreases FOXO3 expression to prevent excessive inflammation in macrophage activation syndrome.

Macrophage activation syndrome and rapidly progressive lung disease as life-threatening manifestations of anti-MDA5 antibody disease. A case report.

Vaccine-induced immune thrombotic thrombocytopenia in Tunisia following AstraZeneca COVID-19 vaccination: a case report.

Risk factors for macrophage activation syndrome in systemic juvenile idiopathic arthritis: a systematic review and meta-analysis.

Lysophosphatidic acid regulates macrophage polarization via LPAR1 by suppressing inflammatory responses and promoting M2-like characteristics.

Adult-Onset Still's Disease Complicated by Secondary Hemophagocytic Lymphohistiocytosis: A Case Report.

Macrophage activation syndrome in a child with varicella: a case report.

Interleukin-18 Levels Are Associated With Disease Course in Patients With Still Disease Treated With Interleukin-1 Inhibitors.

Hepatic Manifestations in Systemic Juvenile Idiopathic Arthritis and Macrophage Activation Syndrome.

Baseline Clinical Features and Biomarker Profiles of the Childhood Arthritis and Rheumatology Research Alliance Systemic Juvenile Idiopathic Arthritis-Associated Lung Disease Cohort.

Mevalonate kinase deficiency diagnosed in late adolescence presenting with macrophage activation syndrome.

Distinct Natural Killer Cell Signature in Still Disease: Insights From a Multinational Immunome Project Consortium for Autoinflammatory Disorders.

Precision Immunotherapy to Improve Sepsis Outcomes: The ImmunoSep Randomized Clinical Trial.

Hemophagocytic lymphohistiocytosis: do we have a solution for TMI (too much inflammation)?

Hyperinflammatory status associated with COVID-19: clinical features of a pediatric series.

Full recovery with left ventricular unloading via venoarterial extracorporeal membrane oxygenation and use of emapalumab in severe metapnomovirus myocarditis presenting with cardiogenic shock.

Case Report: Rare adverse events following CAR-T therapy in patients with relapsed/refractory diffuse large B-cell lymphoma.

Eculizumab as an adjunctive rescue treatment for life-threatening childhood onset of systemic lupus erythematosus.

Pharmacological and non-pharmacological treatments for refractory paediatric Still's disease: a scoping review.

Fatal Chronic Varicella-Zoster Viral Infection in a Young Man With Chediak-Higashi Syndrome.

Emapalumab as a Life-Saving Therapy for Macrophage Activation Syndrome in Refractory Systemic Juvenile Idiopathic Arthritis with Trisomy 21.

Shock in Adult-Onset Still's Disease Complicated by Macrophage Activation Syndrome: Clinical Characteristics and Prognosis of 14 Patients.

Etiologic spectrum and early mortality predictors in extreme hyperferritinemia: insights from rheumatology and hematology clinics.

Prediction nomogram of serum interferon-γ enable early identification of macrophage activation syndrome in children with Kawasaki disease.

Therapeutic plasma exchange in autoimmune diseases: a retrospective study in a tertiary pediatric hospital in Mexico.

Monocyte/macrophages may exert prominent roles in macrophage activation syndrome.

Kawasaki disease complicated with shock syndrome and macrophage activation syndrome in children: a case report.

Macrophage activation syndrome-like in multiple myeloma patients treated with the academic CAR-T against BCMA ARI0002h.

Hemophagocytic lymphohistiocytosis in 60 Mexican children with chronic granulomatous disease.

Sustained remission with eculizumab in refractory lupus nephritis with atypical haemolytic uraemic syndrome.

Distinct expression profiles of inflammasome-associated genes in systemic juvenile idiopathic arthritis.

Low-dose emapalumab treatment in refractory macrophage activation syndrome secondary to adult onset still's disease/systemic lupus erythematosus: insights from nine cases.

From Cough to Myocarditis: A Systemic Tale of Adult-Onset Still's Disease.

Clinical significance of non-infectious procalcitonin elevation in Still's disease: a predictor of macrophage activation syndrome.

Macrophage Activation in Lupus Nephritis: An Unknown Cause of Severe Hypercalcemia.

Clinical Analysis of Two Cases of Histiocytic Necrotizing Lymphadenitis Complicated with Macrophage Activation Syndrome.

Griscelli Syndrome Type 2 Revealed by Macrophage Activation Syndrome: Two Cases From the Same Family.

Long-term safety of canakinumab in patients with systemic juvenile idiopathic arthritis: 5-year results from the Childhood Arthritis and Rheumatology Research Alliance (CARRA) registry.

An animal model of NLRC4-associated autoinflammation and infantile enterocolitis reveals novel therapeutic strategies.

Recurrent macrophage activation syndrome in patients with refractory systemic lupus erythematosus treated with emapalumab: a case report.

Clinical characteristics and prognostic factors in adult macrophage activation syndrome: an observational study in a Chinese cohort.

Reassessing sepsis research: new clues for old players and new players for an old symptom to improve patient outcomes.

Still's disease: bridging the gap between guidelines and clinical practice.

Treating and triggering hyperinflammation: tackling hemophagocytic lymphohistiocytosis and HLH-like syndromes in the pediatric cell therapy and critical care setting.

Add in a virus: four cases of severe Kawasaki disease and concurrent adenovirus infection.

Hemophagocytic lymphohistiocytosis: an update in diagnostics, criteria, and treatment considerations.

Pruritic eruption in a young woman with fever.

Clinical Features and Outcome Measures Across Still Disease (Systemic Juvenile Idiopathic Arthritis and Adult-Onset Still Disease) Cohorts Worldwide: A Systematic Literature Review.

Unfolding dermatological spectrum of Still's disease: a cohort study from the International AIDA Network Still's Disease Registry.

In Vivo Immune Cell Responses and Long-Term Effects of Cold Atmospheric Plasma in the Upper Respiratory Tract.

Hyperferritinemia and Macrophage Activation Syndrome in Septic Shock: Recent Advances with a Pediatric Focus (2020-2025).

Adult-onset Still's disease following COVID-19: a case report and literature review.

[Emapalumab treatment for macrophage activation syndrome in a child with systemic lupus erythematosus].

Less is more: hematologic safety and sustained efficacy of a modified low-dose etoposide regimen in macrophage activation syndrome.

Macrophage activation syndrome associated with multi-system inflammatory syndrome in children: a case report and cytokine profile.

Should multisystem inflammatory syndrome in children be considered occult macrophage activation syndrome?

Allogeneic haematopoietic stem cell transplantation for severe Still's disease: a retrospective report of three paediatric patients.

Early-onset enterocolitis and concerning for macrophage activation syndrome in NLRC4 p.Val342Ala: IL-18 insights.

A diagnostic algorithm to evaluate elevated C-reactive protein levels in juvenile systemic lupus erythematosus.

Traditional laboratory parameters and IFNγ-related biomarkers in the diagnosis and management of MAS.

Systemic Lupus Erythematosus with Hemophagocytic Lymphohistiocytosis Mimicking Tuberculosis in a Young Male: A Diagnostic Challenge.

Epstein-Barr Virus Seropositivity, Immune Dysregulation, and Mortality in Pediatric Sepsis.

Efficacy, pharmacokinetics and safety of iscalimab (CFZ533) in patients with proliferative lupus nephritis: a randomised, double-blind, placebo-controlled, phase II study.

Progressive Disseminated Histoplasmosis with Dermatomyositis and Macrophage Activation Syndrome/Hemophagocytic Lymphohistiocytosis.

Successful management of Still's disease with severe liver injury through the administration of baricitinib: a case report.

Haemophagocytic Lymphohistiocytosis: An Uncommon Presentation in Systemic Lupus Erythematosus and Acute Leukaemia.

Serum Cytokine Profiling Differentiates Underlying Diseases in Cytokine Storm Syndrome.

Genetics of progressive multifocal leukoencephalopathy: update on case reports with an inborn error of immunity and risk variants found in drug-linked cases.

Targeting JAK-STAT in macrophage activation syndrome-no MAS!

Paradoxical hemoglobin drop Post-Transfusion: Hyperhemolysis in Delta-Beta thalassemia with macrophage activation syndrome.

Etiologies and long-term outcome of pediatric hemophagocytic lymphohistiocytosis and macrophage activation syndrome in Taiwan: a single-center retrospective study.

Managing the clinical heterogeneity of patients with Still's disease, from early diagnosis to timely treatment.

Utility of patient-reported outcomes for pulmonary symptoms and sleep disturbance and impairment in children with systemic juvenile idiopathic arthritis.

Haemophagocytic lymphohistiocytosis in pregnancy and the postpartum: A case series from the national HLH network.

Efficacy and safety of ruxolitinib in adult patients with refractory rheumatic disease-associated macrophage activation syndrome.

Subphenotypic Classification of Immune Response in Sepsis: Predicting Mortality and Guiding Future Personalized Immunotherapy.

nCD64 index as a new early predictive biomarker for macrophage activation syndrome in adult-onset still's disease.

Somatic Mosaic NLRC4 Variants in Autoinflammatory Diseases: Functional Characterization and Correlation of Mosaicism Levels with Disease Age of Onset and Severity.

Prolonged acyclovir therapy for Herpes simplex virus (HSV)-1-associated hepatitis in an immunocompetent man.

Investigation of the effect of serum gasdermin d levels on clinical course and mortality in patients with covid-19.

Phagocytes Out of Control: Macrophage Activation Syndrome After the Use of Biologic Agents in the Treatment of Systemic Juvenile Idiopathic Arthritis.

Refractory Sclerosing Mesenteritis/Mesenteric Panniculitis Presenting With Macrophage Activation Syndrome Treated With Rituximab.

A Cytokine Storm Unveiled: Diagnostic Challenges of Macrophage Activation Syndrome in the Context of Undiagnosed Systemic Lupus Erythematosus in an Adolescent.

Safety and Efficacy of Simultaneous Vaccination with Polysaccharide Conjugate Vaccines Against Pneumococcal (13-Valent Vaccine) and Haemophilus Type B Infections in Children with Systemic Juvenile Idiopathic Arthritis: Prospective Cohort Study.

Characteristics of 21 Patients with Secondary Hemophagocytic Lymphohistiocytosis-Insights from a Single-Center Retrospective Study.

Macrophage activation syndrome-associated adult onset Still disease treatment: a scoping review of case reports and case series.

Macrophage activation syndrome complicating adult-onset Still's disease: the case for standardized guidelines.

Tofacitinib in the Treatment of Refractory Adult-Onset Still's Disease Co-diagnosed With Celiac Disease: A Case Report.

C1q monogenic lupus: a case series and review.

Case Report: Two Cases of Kikuchi Disease in West Texas With Non-Self-Limited Disease.

[Systemic juvenile idiopathic arthritis. Pediatric-onset Still's disease].

French protocol for the diagnosis and management of juvenile idiopathic arthritis including pediatric-onset Still's disease.

Outcomes of children with juvenile idiopathic arthritis receiving biological disease-modifying anti-rheumatic drugs: a retrospective single-centre experience from India.

Turmeric and Eucalyptus Aqueous Extracts Reduced Inflammation in Macrophage Activation Syndrome (MAS) Mouse Model.

Anti-melanoma differentiation-associated gene 5 antibody associated rapidly progressive interstitial lung disease in a pediatric patient: a case report.

Life-Threatening Macrophage Activation Syndrome in Pregnancy: First Manifestation of SLE Induced by Parvovirus B19.

Unmasking the Masquerade: A Case Report of Adult-Onset Still's Disease.

Analysis of the clinical characteristics of five patients with Kawasaki disease complicated with macrophage activation syndrome in Baoding Hospital of Beijing Children's Hospital, Capital Medical University.

Trends and Hot Spots of Macrophages Linked to Metabolic Syndrome: A Comprehensive Bibliometric and Visualization Analysis (2014-2024).

Macrophage activation syndrome in a pediatric patient: Findings on PET/CT with 18F-FDG.

A retrospective study of long-term outcomes related with initial factors in childhood onset systemic lupus erythematosus.

The pathophysiology of hemophagocytic lympho-histiocytosis (HLH) syndrome and insights from animal models.

Macrophage activation syndrome with hypoplastic marrow and orbital myositis as a unique initial presentation of systemic lupus erythematosus: A case-based review.

Impact of Interleukin-1 Blockade on the Development of Macrophage Activation Syndrome in Still Disease: Incidence and Diagnostic Validity of the EULAR/ACR/PRINTO 2016 MAS Classification Criteria.

Macrophage Activation Syndrome Revealing Hodgkin Lymphoma: A Pediatric Case Report.

Macrophage activation syndrome associated with neonatal lupus erythematosus.

Ruxolitinib targets JAK-STAT signaling to modulate neutrophil activation in refractory macrophage activation syndrome.

Effective Treatment of Macrophage Activation Syndrome Linked to Systemic Lupus Erythematosus Using Interleukin-1 Inhibitor.

Pulmonary arterial hypertension in adults with Still's disease: another pulmonary manifestation associated with HLA-DRB1*15.

Advancing multidisciplinary management of pediatric hyperinflammatory disorders.

Endogenous Lipoid Pneumonia in Adult Autoinflammatory Disease.

[Epistaxis and weight loss in a 73-year-old man].

Modeling the HLH immune synapse uncovers critical roles for IS termination, cytokine intensity, and target cell death.

Haemophagocytic Lymphohistiocytosis as an Initial Presentation of Undiagnosed Systemic Lupus Erythematosus.

Tofacitinib as a possible treatment in macrophage activation syndrome: a pilot single-center study in China.

Long-term effectiveness and safety of baricitinib treatment on refractory or severe juvenile dermatomyositis.

Upregulation of Fcγ Receptor IV on Activated Monocytes and Macrophages Causes Nonspecific Binding of the PK136 Anti-NK1.1 Antibody in Murine Models of Toll-Like Receptor-Induced Inflammation.

Corrigendum: Early identification of macrophage activation syndrome in adult-onset Still's disease: a case report and literature review.

Unmet needs and research gaps in Still's disease across ages: proceedings from a pediatric and adult joint expert panel.

Case Report: Macrophage activation syndrome due to multifocal tuberculosis in an immunocompromised patient.

Fatal Acute Intestinal Obstruction with Hemophagocytic Lymphohistiocytosis and Multiple Organ Failure in Adult-Onset Still's Disease: A Rare Case Report.

Macrophage Activation Syndrome in Adult-Onset Still's Disease: Challenges in Early Detection and Management.

Management Challenge of Coexistence of Macrophage Activation Syndrome, Systemic Lupus Erythematosus, and Hepatitis B: Case Report.

Successful re-administration of tocilizumab in a patient with adult-onset Still's disease after improvement of macrophage activation syndrome.

Macrophage activation syndrome successfully treated with eculizumab and emapalumab: a case report.

Macrophage Activation Syndrome as an Atypical Manifestation of Mixed Connective Tissue Disease in a 14-Year-Old Girl: A Case Report.

Adult-Onset Still's Disease Presenting as Aseptic Meningitis: A Case Report and Literature Review.

First-line biological versus conventional synthetic disease-modifying antirheumatic drug therapy in adult-onset Still's disease: a multicentre, retrospective, propensity weighted cohort study.

Ηidradenitis suppurativa associated with autoimmunity in children and adolescents; a case-based review.

Macrophage Activation Syndrome in Kawasaki Disease: Insights from a Systematic Literature Review on Diagnosis, Clinical Features, and Treatment.

High Neutrophil Alkaline Phosphatase Activity in Adult-Onset Still's Disease.

Characterization of Patients with Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis.

Macrophage activation syndrome in Kawasaki disease: a literature review of Korean studies.

Macrophage Activation Syndrome: Not Just for Rheumatologists Anymore.

T-ing up the storm: pathogenic cycling lymphocytes in the biology of macrophage activation syndrome.

An Inflammatory Cascade: Still's Disease Complicated by Macrophage Activation Syndrome.

Treatment of systemic juvenile idiopathic arthritis: conventional treatment versus biologics.

[Fever and Pancytopenia - not Always a Case for Oncology].

[A rare differential diagnosis of fever of unknown origin].

Influence of CAR T-cell therapy associated complications.

Successful control of recurrent MAS by canakinumab in a Sjögren syndrome patient with homozygous MEFV P369S variants and review of literatures.

Development of anti-murine IL-18 binding protein antibodies to stimulate IL-18 bioactivity.

Systemic juvenile idiopathic arthritis and adult-onset Still's disease are the same disease and should now be designated by the same unique name, Still's disease.

Sustained remission after bispecific antibody anti-IL-1β/anti-IL-18 therapy in a severe childhood Still's disease with recurrent macrophage activation syndrome.

Marked exacerbation of resolving macrophage activation syndrome in a patient with adult-onset Still's disease following one dose of granulocyte colony-stimulating factor.

Mortality in children and adolescents with autoimmune inflammatory rheumatic diseases admitted to the pediatric intensive care unit.

Hyperferritinemia is Associated with Thrombocytopenia and Increased Mortality Risk in Adult Sepsis Patients: A Retrospective Study of Two Observational Cohorts.

Gastrointestinal system involvement characteristics in Covid -19 patients.

Tetrandrine alleviates macrophage activation syndrome after CAR-T cell therapy.