OBSOLETO. A malformação arteriovenosa pulmonar (MAVP) descreve uma comunicação anatômica entre uma artéria pulmonar e uma veia pulmonar levando a um shunt extracardíaco direito-esquerdo que pode ser assintomático ou levar a manifestações variadas, como dispneia, hemoptise e sintomas neurológicos.
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OBSOLETO. A malformação arteriovenosa pulmonar (MAVP) descreve uma comunicação anatômica entre uma artéria pulmonar e uma veia pulmonar levando a um shunt extracardíaco direito-esquerdo que pode ser assintomático ou levar a manifestações variadas, como dispneia, hemoptise e sintomas neurológicos.
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Sinais e sintomas
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Partes do corpo afetadas
+ 13 sintomas em outras categorias
Características mais comuns
Os sintomas variam de pessoa para pessoa. Abaixo estão as 30 características clínicas mais associadas, ordenadas por frequência.
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O que está alterado no DNA e como passa nas famílias
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Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
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Onde tratar no SUS
Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)
🇧🇷 Atendimento SUS — Malformação arteriovenosa pulmonar
Centros de Referência SUS
24 centros habilitados pelo SUS para Malformação arteriovenosa pulmonar
Centros para Malformação arteriovenosa pulmonar
Detalhes dos centros
Hospital Universitário Prof. Edgard Santos (HUPES)
R. Dr. Augusto Viana, s/n - Canela, Salvador - BA, 40110-060 · CNES 0003808
Serviço de Referência
Hospital Infantil Albert Sabin
R. Tertuliano Sales, 544 - Vila União, Fortaleza - CE, 60410-794 · CNES 2407876
Serviço de Referência
Hospital de Apoio de Brasília (HAB)
AENW 3 Lote A Setor Noroeste - Plano Piloto, Brasília - DF, 70684-831 · CNES 0010456
Serviço de Referência
Hospital Estadual Infantil e Maternidade Alzir Bernardino Alves (HIABA)
Av. Min. Salgado Filho, 918 - Soteco, Vila Velha - ES, 29106-010 · CNES 6631207
Serviço de Referência
Hospital das Clínicas da UFG
Rua 235 QD. 68 Lote Área, Nº 285, s/nº - Setor Leste Universitário, Goiânia - GO, 74605-050 · CNES 2338424
Serviço de Referência
Hospital Universitário da UFJF
R. Catulo Breviglieri, Bairro - s/n - Santa Catarina, Juiz de Fora - MG, 36036-110 · CNES 2297442
Atenção Especializada
Hospital das Clínicas da UFMG
Av. Prof. Alfredo Balena, 110 - Santa Efigênia, Belo Horizonte - MG, 30130-100 · CNES 2280167
Serviço de Referência
Hospital Universitário Julio Müller (HUJM)
R. Luis Philippe Pereira Leite, s/n - Alvorada, Cuiabá - MT, 78048-902 · CNES 2726092
Atenção Especializada
Hospital Universitário João de Barros Barreto
R. dos Mundurucus, 4487 - Guamá, Belém - PA, 66073-000 · CNES 2337878
Serviço de Referência
Hospital Universitário Lauro Wanderley (HULW)
R. Tabeliao Estanislau Eloy, 585 - Castelo Branco, João Pessoa - PB, 58050-585 · CNES 0002470
Atenção Especializada
Instituto de Medicina Integral Prof. Fernando Figueira (IMIP)
R. dos Coelhos, 300 - Boa Vista, Recife - PE, 50070-902 · CNES 0000647
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Hospital Pequeno Príncipe
R. Des. Motta, 1070 - Água Verde, Curitiba - PR, 80250-060 · CNES 3143805
Serviço de Referência
Hospital Universitário Regional de Maringá (HUM)
Av. Mandacaru, 1590 - Parque das Laranjeiras, Maringá - PR, 87083-240 · CNES 2216108
Atenção Especializada
Hospital de Clínicas da UFPR
R. Gen. Carneiro, 181 - Alto da Glória, Curitiba - PR, 80060-900 · CNES 2364980
Serviço de Referência
Hospital Universitário Pedro Ernesto (HUPE-UERJ)
Blvd. 28 de Setembro, 77 - Vila Isabel, Rio de Janeiro - RJ, 20551-030 · CNES 2280221
Serviço de Referência
Instituto Nacional de Saúde da Mulher, da Criança e do Adolescente Fernandes Figueira (IFF/Fiocruz)
Av. Rui Barbosa, 716 - Flamengo, Rio de Janeiro - RJ, 22250-020 · CNES 2269988
Serviço de Referência
Hospital São Lucas da PUCRS
Av. Ipiranga, 6690 - Jardim Botânico, Porto Alegre - RS, 90610-000 · CNES 2232928
Serviço de Referência
Hospital de Clínicas de Porto Alegre (HCPA)
Rua Ramiro Barcelos, 2350 Bloco A - Av. Protásio Alves, 211 - Bloco B e C - Santa Cecília, Porto Alegre - RS, 90035-903 · CNES 2237601
Serviço de Referência
Hospital Universitário da UFSC (HU-UFSC)
R. Profa. Maria Flora Pausewang - Trindade, Florianópolis - SC, 88036-800 · CNES 2560356
Serviço de Referência
Hospital das Clínicas da FMUSP
R. Dr. Ovídio Pires de Campos, 225 - Cerqueira César, São Paulo - SP, 05403-010 · CNES 2077485
Serviço de Referência
Hospital de Base de São José do Rio Preto
Av. Brg. Faria Lima, 5544 - Vila Sao Jose, São José do Rio Preto - SP, 15090-000 · CNES 2079798
Atenção Especializada
Hospital de Clínicas da UNICAMP
R. Vital Brasil, 251 - Cidade Universitária, Campinas - SP, 13083-888 · CNES 2748223
Serviço de Referência
Hospital de Clínicas de Ribeirão Preto (HCRP-USP)
R. Ten. Catão Roxo, 3900 - Vila Monte Alegre, Ribeirão Preto - SP, 14015-010 · CNES 2082187
Serviço de Referência
UNIFESP / Hospital São Paulo
R. Napoleão de Barros, 715 - Vila Clementino, São Paulo - SP, 04024-002 · CNES 2688689
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Publicações mais relevantes
Safety and Efficacy of the LOBO Vascular Occlusion Device for Embolization of Pulmonary Arteriovenous Malformations (PAVM): A Single-Center Retrospective Experience.
To evaluate the safety, technical success, and short-term clinical efficacy of the Low-profile Braided Occluder (LOBO) device for embolization of pulmonary arteriovenous malformations (PAVMs). A single-center retrospective study of 23 consecutive patients (mean 42.3 + 19 years; 82% female) with PAVMs underwent transcatheter embolization using LOBO devices. Clinical efficacy was defined as the absence of PAVM recanalization/persistence and ≥70% reduction in sac size on 6-month follow-up CT angiography (CTA). Adverse events were also assessed following embolization. Of the twenty-three patients treated, 87% had Hereditary Hemorrhagic Telangiectasia. Fifty-nine feeding arteries were embolized using a single device per feeder (LOBO-3, n=37; LOBO-5, n=18; LOBO-7, n=3; LOBO-9, n=1) with no additional coils or other embolic devices required. Mean feeding-artery diameter was 2.93+1.05 mm. The mean fluoroscopy time was 29.19 + 20 minutes (Median:24.9 minutes; Range: 4.6-106.9 minutes), and mean radiation dose was 623.5 + 598 mGy (Median:404 mGy; Range: 18-3135 mGy). Technical success was 100%, with no intraprocedural device mal-deployment or migration. At imaging follow-up of approximately 6 months (Mean 251+74.55 days, Median 266 days, Range 154 - 474 days), there was no recanalization of treated arterial feeders and nopersistence or recanalization of the PAVM sac. No device-related adverse events or major procedure-related adverse events were observed. In this single-center experience, the LOBO device appears to be a safe and effective option for PAVM embolization, with promising short-term results.
BMPR2 Splice-Site Variant in a Patient With Pulmonary Arteriovenous Malformation and Delayed-Onset Pulmonary Arterial Hypertension: A Case Report and Mechanistic Phenocopy Hypothesis.
Pulmonary arteriovenous malformations (PAVMs) are rare vascular anomalies most commonly seen in hereditary hemorrhagic telangiectasia (HHT), a condition associated with mutations in ENG, ACVRL1, SMAD4, or GDF2. In contrast, BMPR2 variants are well-established in heritable pulmonary arterial hypertension (PAH), but their relationship to PAVMs remains poorly understood. We report the case of a 41-year-old woman with an incidentally discovered PAVM, initially treated with embolization and subsequent surgical resection. She remained asymptomatic for several years until progressive exertional dyspnea led to a diagnosis of severe precapillary PAH. Genetic testing identified a heterozygous BMPR2 splice-site variant (c.967 + 5G>A), previously reported in a PAH cohort but currently classified as a variant of uncertain significance. This report is notable for the delayed evolution from isolated PAVM to PAH in the context of a BMPR2 variant, raising the possibility of a mechanistic link outside the canonical HHT pathway. We review published reports of BMPR2-associated PAVMs, some of which include subtle HHT-like features, such as mucocutaneous telangiectases and epistaxis, despite negative testing for classical HHT genes. These observations suggest a potential phenocopy vascular syndrome driven by disruption of the shared bone morphogenetic protein 9 (BMP9)-ALK1 signaling axis. We also discuss the implications of sotatercept, a transforming growth factor-beta (TGF-β) superfamily ligand trap, which in this case was associated with symptomatic improvement and stable shunt burden. These findings contribute to the emerging recognition of atypical vascular phenotypes in BMPR2 variant carriers, particularly those presenting with PAVMs in the absence of HHT. It highlights the importance of considering genetic testing in isolated AVM presentations, as well as the need for longitudinal surveillance and mechanistic investigation into overlapping TGF-β/BMP signaling disorders.
Four-Dimensional Computed Tomography Differentiates Congenital Right Pulmonary Vein Atresia From Suspected Arteriovenous Malformation: A Case Report.
Congenital pulmonary vein atresia (PVA) is a rare condition often associated with vascular anomalies and complex pulmonary hemodynamics. A 54-year-old woman was referred for evaluation of a nodular shadow in the right upper lobe, initially suspected to represent a pulmonary arteriovenous malformation (PAVM). Four-dimensional enhanced computed tomography (4D-CT) revealed no abnormal vessels, suggesting a PAVM in the pulmonary arterial phase. However, in the venous phase, the pulmonary vein of the right upper lobe was occluded at the trunk, with reflux via a pulmonary vein varix and an abnormal vein draining into the pulmonary vein of the right middle lobe. Due to the risk of pulmonary hypertension, thromboembolism, or varix rupture, the patient underwent right upper lobectomy. 4D-CT effectively delineates the vascular morphology by separating the pulmonary arterial and venous phases. Congenital PVA may involve pulmonary vein varices and abnormal vascular formation; 4D-CT may be valuable for diagnosis and treatment planning.
Pulmonary arteriovenous malformation in pregnancy: a case report and literature review.
Pulmonary arteriovenous malformations (PAVMs) are rare vascular anomalies often linked to hereditary hemorrhagic telangiectasia (HHT). Pregnancy-related hemodynamic and hormonal changes may exacerbate PAVMs and lead to serious maternal and fetal complications. A 26-year-old multipara at 25 weeks’ gestation presented with fever, cough, progressive dyspnea and left chest pain. Imaging demonstrated bilateral PAVMs with a loculated left pleural effusion. She was managed conservatively (intercostal drainage, transfusion, thromboprophylaxis) and monitored closely. Embolization was discussed but deferred after multidisciplinary discussion because of insufficient finances and the patient’s clinical stability; elective cesarean section at 39 weeks resulted in a healthy newborn. The patient was referred to interventional radiology for planned postpartum embolization. To report an unusual presentation of bilateral large PAVMs in pregnancy and to review the literature on diagnostic strategies, antenatal management (embolotherapy vs. surgery vs. conservative), and maternal–fetal outcomes. We searched PubMed/MEDLINE, Embase and Scopus (Jan 1, 1997–Sep 30, 2025) using combinations of MeSH/keywords: “pulmonary arteriovenous malformation”, “PAVM”, “pulmonary AVM”, “pregnancy”, “pregnant”, “embolization”, “embolotherapy”, “hemothorax” (English, human). Case reports, case series and observational studies reporting PAVM in pregnancy were included; reviews and animal studies were excluded. Bibliographies of included articles were hand searched. A total of 21 published cases of PAVM in pregnancy were identified; after excluding the cases summarized in the earlier review up to 1997, we focused on 12 subsequent reports (Table 1). Dyspnea and chest pain were the most frequent presentations. Antenatal embolization was performed in several cases with generally favorable outcomes, though recanalization/persistence has been reported. No maternal deaths were reported among the cases included in our review. PAVM in pregnancy can present emergently and requires individualized, multidisciplinary management. Transcatheter embolization is the preferred treatment when feasible, but case-by-case decisions — accounting for clinical stability, gestation, and patient factors — are essential.
An Uncommon Cause of Massive Hemothorax: Pulmonary Arteriovenous Malformation in the Right Middle Lobe.
Pulmonary arteriovenous malformations (PAVMs) are rare vascular anomalies that can lead to severe complications when ruptured. We report the case of a 65-year-old active smoker who presented to the emergency department with acute pleuritic chest pain, severe dyspnea, and hypoxemia. Chest CT revealed a large PAVM in the right middle lobe, associated with massive hemothorax and a small pneumothorax. The patient had no history of hereditary hemorrhagic telangiectasia. Initial management included pleural drainage and endovascular embolization with a 16 mm Amplatzer™ device. Due to persistent respiratory failure and high risk of rebleeding, a right middle lobectomy was subsequently performed. Intraoperative findings confirmed a partially thrombosed AVM and correct device placement. Postoperative recovery was uneventful, with no recurrent bleeding. This case highlights a rare cause of spontaneous massive hemothorax requiring combined endovascular and surgical management, emphasizing the importance of early diagnosis and multidisciplinary care in idiopathic PAVMs. Las malformaciones arteriovenosas pulmonares (MAVPs) son anomalías vasculares poco frecuentes que pueden originar complicaciones graves cuando se rompen. Se trata de un paciente varón de 65 años y fumador activo que acudió al servicio de Urgencias con disnea intensa, dolor torácico de características pleuríticas e hipoxemia. La TC de tórax mostró una gran MAVP en el lóbulo medio derecho, asociada a hemotórax masivo y un pequeño neumotórax. El paciente no tenía antecedentes de telangiectasia hemorrágica hereditaria (THH). Se colocó un drenaje pleural y se realizó una embolización endovascular con dispositivo Amplatzer™ de 16 mm. Además, debido a la persistencia de insuficiencia respiratoria y riesgo elevado de resangrado, se realizó una lobectomía media derecha. Durante la intervención se confirmó una MAV parcialmente trombosada y la adecuada ubicación del dispositivo. La evolución posoperatoria fue favorable, sin nuevos sangrados. Este caso destaca una causa infrecuente de hemotórax espontáneo masivo que puede requerir tratamiento combinado endovascular y quirúrgico, resaltando la importancia de una sospecha clínica precoz y el manejo multidisciplinar en las MAVPs idiopáticas.
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Safety and Efficacy of the LOBO Vascular Occlusion Device for Embolization of Pulmonary Arteriovenous Malformations (PAVM): A Single-Center Retrospective Experience.
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Polish archives of internal medicineDiffuse pulmonary arteriovenous malformation presenting with secondary polycythemia and headaches: a case report.
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Journal of vascular and interventional radiology : JVIRThe trade-off dilemma between radiation dose and image resolution.
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Radiology case reportsA mediastinum-tumour-like pulmonary arteriovenous malformation with association to the pulmonary artery treated with surgical resection.
Respirology case reportsCase of Prenatal Diagnosis of a Fetal Pulmonary Arteriovenous Malformation at Term.
Diagnostics (Basel, Switzerland)Angiographic tool to detect pulmonary arteriovenous malformations in single ventricle physiology.
Cardiology in the youngRecurrence of Pulmonary Arteriovenous Malformation after Embolization in Patients with Pulmonary Hypertension.
Journal of vascular and interventional radiology : JVIR[Ischemic stroke due to paradoxical embolism through pulmonary arteriovenous malformation in a young patient].
MedicinaUltra-low dose chest CT for the diagnosis of pulmonary arteriovenous malformation in patients with hereditary hemorrhagic telangiectasia.
Diagnostic and interventional imagingSuccessful embolization of a clinically significant pulmonary arteriovenous malformation.
Respirology case reportsAn Alternative Endovascular Technique for Treatment of Pulmonary Arteriovenous Malformation: Microballoon-occluded Transcatheter Embolization Using n-butyl-2-cyanoacrylate.
Cardiovascular and interventional radiologyHereditary hemorrhagic telangiectasia diagnosis: A case report.
Journal of pediatric nursingLife-threatening hemothorax due to rupture of pulmonary arteriovenous malformation during pregnancy.
Journal of surgical case reportsComplex pulmonary arteriovenous malformation in a boy aged 18 months.
Anales de pediatriaFusion imaging for guidance of pulmonary arteriovenous malformation embolisation with minimal radiation and contrast exposure.
Cardiology in the youngMassive Pulmonary Arteriovenous Malformation as a Cause of Fetal Heart Failure.
CureusEvaluation of a gradually enlarging complex pulmonary arteriovenous malformation consisting of innumerable small fistulae using four-dimensional computed tomography.
BMJ case reportsEmbolization of De Novo Pulmonary Arteriovenous Malformations Using High-Volume Detachable Non-Fibered Coils: Propensity-Matched Comparison to Traditional Coils.
Journal of clinical medicineCoil Embolization of a Large Recurrent Pulmonary Arteriovenous Malformation by Retrograde Transseptal Pulmonary Vein Access.
Journal of vascular and interventional radiology : JVIRUse of Polyurethane-Covered Stents for Exclusion of Pulmonary Arteriovenous Malformations.
Cardiovascular and interventional radiologySpontaneous Hemothorax by Pulmonary Arteriovenous Malformation during Pregnancy.
The Thoracic and cardiovascular surgeon reportsPulmonary arteriovenous malformations in patients with previous brain abscess: a cross-sectional population-based study.
European journal of neurologyA Congenital Portosystemic Shunt in a Child With Heterotaxy, Situs Inversus, Polysplenia, and Interrupted Inferior Vena Cava With Azygous Continuation.
ACG case reports journalCase report: video-assisted thoracoscopic surgery for pulmonary arteriovenous malformation using near-infrared fluorescence with indocyanine green.
Journal of cardiothoracic surgeryPregnancy and delivery after percutaneous embolization with a combination of microvascular plugs and hydrogel-coated coils for unilateral diffuse pulmonary arteriovenous malformations: a case report.
European heart journal. Case reportsPulmonary arteriovenous malformation and a concurrent patent ductus arteriosus in a Doberman.
Journal of veterinary cardiology : the official journal of the European Society of Veterinary CardiologyCine MRI in the Evaluation of Pulmonary Arteriovenous Malformations.
CureusA case of hemoptysis unveiling the unlikely culprit - pulmonary arteriovenous malformation.
Radiology case reportsPulmonary arteriovenous malformation: Challenging diagnosis: A case report.
Radiology case reportsIncidental radiological findings during clinical tuberculosis screening in Lesotho and South Africa: a case series.
Journal of medical case reportsAn Update on Embolization for Pulmonary Arteriovenous Malformations.
Interventional radiology (Higashimatsuyama-shi (Japan)An analysis of sex differences in pulmonary arteriovenous malformation presentation, complications and management in a large, multinational registry of patients with hereditary haemorrhagic telangiectasia.
ERJ open researchRetrospective single-arm cohort study of video-assisted thoracic surgery for treatment of idiopathic peripherally located simple type pulmonary arteriovenous malformation in 23 consecutive patients.
Journal of cardiothoracic surgeryPearls and Pitfalls in the Transesophageal Echocardiographic Diagnosis of Patent Foramen Ovale.
Journal of the American Society of Echocardiography : official publication of the American Society of EchocardiographyComparison of Transthoracic Contrast Echocardiography with High-Resolution Chest CT after Embolization of Pulmonary Arteriovenous Malformation.
Journal of vascular and interventional radiology : JVIRCT chest-cerebral angiography for basilar artery occlusion caused by pulmonary arteriovenous malformation.
BMJ case reports[Hereditary hemorrhagic telangiectasia].
Revue des maladies respiratoiresTwenty-Seven-Year Retrospective Review of Hemoptysis from Systemic Collaterals Following Pulmonary Arteriovenous Malformation Embolization.
Cardiovascular and interventional radiologyPulmonary Arteriovenous Malformation Unmasked by Pregnancy: A Review of Pulmonary Arteriovenous Malformations and Cardiovascular and Respiratory Changes in Pregnancy.
Case reports in pulmonologyPulmonary arteriovenous fistula in a rare location: The importance of excluding patent foramen ovale.
Journal of cardiology casesPulmonary Arteriovenous Malformation (With Secondary Erythrocytosis): A Diagnosis Hastened by COVID-19 Pandemic.
Mayo Clinic proceedingsGiant complex pulmonary arteriovenous malformation treated with coil embolisation under general anaesthesia with a history of contrast media allergy.
BMJ case reportsDouble anterograde/retrograde approach for embolization of pulmonary arteriovenous malformation presenting with acute respiratory failure.
European heart journalAbernethy Malformation Masquerading as Congenital Heart Disease: A Boy With Cyanosis, Clubbing, and Hypoxia.
CureusMechanical thrombectomy for acute paradoxical cerebral embolism due to pulmonary arteriovenous malformation: A case report and review of literature.
Surgical neurology internationalPulmonary Arteriovenous Malformation in a Rare Case of Hereditary Hemorrhagic Telangiectasia.
CureusSpontaneous hemothorax in pregnant patient with pulmonary arteriovenous malformation.
Radiology case reportsRisk factors for cerebral complications in patients with pulmonary arteriovenous malformations: A multicenter retrospective cohort study.
PloS onePyogenic brain abscess associated with an incidental pulmonary arteriovenous malformation.
BMJ case reportsEvolution of Pulmonary Arteriovenous Malformations: The Role of Contrast Echocardiography.
ChestAcute Ischemic Stroke in Patients With Pulmonary Arteriovenous Malformations: Paradoxical Embolism or Epiphenomenon?
Stroke (Hoboken, N.J.)Telangiectatic pulmonary arteriovenous malformation presenting as a suspected malignant part-solid nodule.
British journal of hospital medicine (London, England : 2005)Haemothorax in a Pregnant Woman Secondary to Rupture of a Pulmonary Arteriovenous Malformation.
European journal of case reports in internal medicineRecurrent pulmonary arteriovenous malformation in a patient with Sjögren syndrome: A case report.
MedicineTranscatheter closure of congenital portosystemic shunts - A multicenter experience.
Annals of pediatric cardiologyPercutaneous Puncture Embolization for Recurrent Pulmonary Arteriovenous Malformation After Failed Initial Treatment: A Case Report.
Vascular and endovascular surgeryUnexpected Complications 25 Years after Coil Embolization for Pulmonary Arteriovenous Fistula.
Internal medicine (Tokyo, Japan)Significance of transesophageal contrast echocardiography with the agitated saline test for diagnosing pulmonary arteriovenous malformations.
Frontiers in cardiovascular medicineHepatic factor may not originate from hepatocytes.
Frontiers in cardiovascular medicineNoncontrast time-resolved pulmonary magnetic resonance angiography with consecutive beam saturation pulse and variable flip angles using three-dimensional fast spin echo: A preliminary study.
Magnetic resonance imagingDiagnosis and Management of Persistent Pulmonary Arterio-venous Malformations following Embolotherapy.
Academic radiologyAdvancements in Interventional Oncology of the Chest: Transarterial Chemoembolization and Related Therapies.
Seminars in interventional radiologyPulmonary Arteriovenous Malformations: What the Interventional Radiologist Should Know.
Seminars in interventional radiologyTranscatheter management of life-threatening pulmonary arteriovenous fistula with extracorporeal membrane oxygenation support in an infant.
Cardiology in the youngA Frameshift RBM10 Variant Associated With TARP Syndrome.
Frontiers in geneticsPostembolization Persistence of Pulmonary Arteriovenous Malformations: A Retrospective Comparison of Coils and Amplatzer and Micro Vascular Plugs Using Propensity Score Weighting.
AJR. American journal of roentgenologyFeasibility of Single-Shot Whole Thoracic Time-Resolved MR Angiography to Evaluate Patients with Multiple Pulmonary Arteriovenous Malformations.
Korean journal of radiologyBronchoscopy-guided removal of intrabronchial coil migration after coil embolization of pulmonary arteriovenous malformation.
Radiology case reportsBrain abscess associated with Mycoplasma faucium - The initial presentation of pulmonary arteriovenous malformation.
IDCasesCurrent trends in image-guided chest interventions.
Respirology (Carlton, Vic.)Neurologic Complications in Hereditary Hemorrhagic Telangiectasia with Pulmonary Arteriovenous Malformations: A Systematic Review.
The Canadian journal of neurological sciences. Le journal canadien des sciences neurologiquesEndovascular Embolisation of Pulmonary Arteriovenous Malformation Using Amplatzer Vascular Plugs.
CureusPulmonary arteriovenous malformation and inherent complications with solitary lung nodule biopsy-literature overview and case report.
Radiology case reportsThree-dimensional rotational angiography utility in imaging and intervention in a case of pulmonary arteriovenous malformation.
Annals of pediatric cardiologyManagement of pulmonary arteriovenous malformations involves additional factors aside from the diameter of feeding arteries: a 3-year case-case retrospective analysis.
Respiratory researchHemoptysis after coil embolization for pulmonary arteriovenous malformation: Histopathological confirmation of bronchial epithelium extension.
Radiology case reportsNeurovascular Complications and Pulmonary Arteriovenous Malformation Feeding Artery Size.
Annals of the American Thoracic SocietyHypoxia and Polycythemia: A Pediatric Emergency Department Point of Care Ultrasound Diagnosis of Pulmonary Arteriovenous Malformation.
Pediatric emergency carePulmonary arteriovenous malformations: A case of missed diagnosis in a neonate.
The Medical journal of MalaysiaHemodynamic Assessment of a Large Pulmonary Arteriovenous Malformation in a Neonate: Case Report and Review of Literature.
Pediatric cardiologyIntracardiac versus extracardiac shunt in a young man with ischaemic stroke.
BMJ case reportsVenous thrombosis via pulmonary arteriovenous malformation causing acute myocardial infarction in a relatively young female patient.
BMJ case reportsRetrograde Transseptal Pulmonary Vein Transcatheter Plug Closure for Pulmonary Arteriovenous Malformation.
JACC. Case reportsMultimodality imaging of Abernethy malformation.
Echocardiography (Mount Kisco, N.Y.)Treatment of a rare recurrent pulmonary arteriovenous malformation after multiple embolization by robotic-assisted thoracoscopic surgery.
Journal of surgical case reportsIatrogenic pulmonary artery perforation associated with 5-Fr catheter manipulation during pulmonary arteriovenous malformation embolization with a vascular plug.
Radiology case reportsRacemose hemangioma revealed by massive intraoperative hemorrhage: A case report.
International journal of surgery case reportsPulmonary arteriovenous malformation revealing Osler-Weber-Rendu disease: A case report.
Clinical case reportsAcquired pulmonary arteriovenous malformation associated with bronchiectasis: a case report.
Journal of medical case reportsOccult lung metastases of papillary thyroid cancer detected in a resected pulmonary arteriovenous malformation specimen.
Respiratory medicine case reportsPulmonary Arteriovenous Malformation and Its Vascular Mimickers.
Korean journal of radiologyAssessment of pulmonary arteriovenous malformation with ultra-short echo time magnetic resonance imaging.
European journal of radiologyCT Appearance of Pulmonary Arteriovenous Malformations and Mimics.
Radiographics : a review publication of the Radiological Society of North America, IncConcurrent pulmonary arteriovenous malformation and pulmonary embolism causing stroke: a therapeutic dilemma.
CVIR endovascularCongenital pulmonary varix: Two case reports.
MedicineSevere Hypoxemia Caused by High-Output Heart Failure and Pulmonary Arteriovenous Malformations in Hereditary Hemorrhagic Telangiectasia.
JACC. Case reportsPearls & Oy-sters: Cerebral Abscess Secondary to Pulmonary Arteriovenous Malformation in Hereditary Hemorrhagic Telangiectasia.
NeurologyPulmonary multifocal arteriovenous malformations lead to ischemic stroke in young adults: a case report and literature review.
Annals of palliative medicinePulmonary Arteriovenous Malformations Incidentalloma in a 10-Years-Old Child.
Global pediatric healthA massive pulmonary arteriovenous malformation with platypnoea-orthodeoxia: an important and reversible cause of refractory hypoxaemia.
The Medical journal of AustraliaComplex, Isolated Pulmonary Arteriovenous Malformation in Two Children With Severe Cyanosis.
World journal for pediatric & congenital heart surgeryCommentary: sVEGFR1 Is Enriched in Hepatic Vein Blood-Evidence for a Provisional Hepatic Factor Candidate?
Frontiers in pediatrics[A case of pulmonary arteriovenous malformation treated surgically].
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Safety and Efficacy of the LOBO Vascular Occlusion Device for Embolization of Pulmonary Arteriovenous Malformations (PAVM): A Single-Center Retrospective Experience.
- BMPR2 Splice-Site Variant in a Patient With Pulmonary Arteriovenous Malformation and Delayed-Onset Pulmonary Arterial Hypertension: A Case Report and Mechanistic Phenocopy Hypothesis.
- Four-Dimensional Computed Tomography Differentiates Congenital Right Pulmonary Vein Atresia From Suspected Arteriovenous Malformation: A Case Report.
- Pulmonary arteriovenous malformation in pregnancy: a case report and literature review.
- An Uncommon Cause of Massive Hemothorax: Pulmonary Arteriovenous Malformation in the Right Middle Lobe.
- The Benefits of an Intracardiac Conduit in the Fontan Operation for Complex Systemic Venous Anomalies in Patients with Single Ventricle Physiology.
- Concurrent Patent Foramen Ovale and Pulmonary Arteriovenous Malformation Etiology: Complex Case of Cryptogenic Stroke.
- Multifactorial Hypercoagulability Causing Simultaneous STEMI and Pulmonary Embolism in Young Adults With Prothrombin G20210A Mutation.
- Role of the Transcranial Doppler Bubble Test in the Diagnostic Pathway of a Patent Foramen Ovale in Embolic Stroke of Undetermined Source.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:2038(Orphanet)
- OMIM OMIM:265140(OMIM)
- MONDO:0009930(MONDO)
- Busca completa no PubMed(PubMed)
- Q52775754(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
