O defeito pericárdico e diafragmático é uma combinação rara de pericárdio ausente com defeito diafragmático congênito.
Introdução
O que você precisa saber de cara
O defeito pericárdico e diafragmático é uma combinação rara de pericárdio ausente com defeito diafragmático congênito.
Escala de raridade
<1/50kMuito rara
1/20kRara
1/10kPouco freq.
1/5kIncomum
1/2k
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Sinais e sintomas
O que aparece no corpo e com que frequência cada sintoma acontece
Partes do corpo afetadas
+ 8 sintomas em outras categorias
Características mais comuns
Os sintomas variam de pessoa para pessoa. Abaixo estão as 20 características clínicas mais associadas, ordenadas por frequência.
Linha do tempo da pesquisa
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Genética e causas
O que está alterado no DNA e como passa nas famílias
Nenhum gene associado encontrado
Os dados genéticos desta condição ainda estão sendo catalogados.
Diagnóstico
Os sinais que médicos procuram e os exames que confirmam
Tratamento e manejo
Remédios, cuidados de apoio e o que precisa acompanhar
Onde tratar no SUS
Hospitais de referência no Brasil e o protocolo oficial do SUS (PCDT)
🇧🇷 Atendimento SUS — Defeito do pericárdio e diafragma
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Dados de DATASUS/CNES, SBGM, ABNeuro e Ministério da Saúde. Sempre confirme a disponibilidade diretamente com o estabelecimento.
Pesquisa ativa
Ensaios clínicos abertos e novidades científicas recentes
Pesquisa e ensaios clínicos
Nenhum ensaio clínico registrado para esta condição.
Publicações mais relevantes
Cantrell Syndrome and the One Health Perspective: A Unified Review of Human and Comparative Cases.
Cantrell syndrome (CS) is a rare congenital disorder involving defects in the thoraco-abdominal midline, the diaphragm, the pericardium, the sternum and the heart. Since the initial description of the syndrome, 165 well-documented cases in humans have been reported, demonstrating substantial heterogeneity ranging from complete pentalogy to partial or atypical variants. A systematic review classified body wall defects and associated anomalies into nine categories, which are fully described in the manuscript. The categories include midline defects (UThAb, SUThAb, UAb, SUAb, SUICD, and UH), lateral defects (ThLAb and StLAb), and special cases. Each case was reassessed for umbilical cord status, body wall morphology, cardiac anomalies and additional malformations. Midline defects predominated (153 out of 165 cases, 92.7%), with supraumbilical variants being the most frequent. Umbilical hernias formed a distinct subgroup of ten cases. Lateral defects were uncommon (9 cases, 5.5%) and typically presented as thoracogastroschisis or lateral thoracoabdominoschisis. These defects were often associated with normal umbilical cords. Cardiac anomalies were universal, with ventricular and atrial septal defects being the most common findings. Reclassification revealed that many cases originally labeled as 'classic pentalogy of Cantrell' were more accurately classified as partial or atypical forms. This unified framework improves epidemiological understanding and diagnostic precision. From a One Health perspective, it underscores CS as a shared developmental vulnerability across mammalian species.
An Incidental Necropsy Finding: Intrathoracic Ectopic Liver in a Cat.
Ectopic liver is a rare anomaly characterized by the presence of hepatic tissue outside its normal anatomical location without continuity with the main liver. Reports of this condition are sporadic in human medicine, and cases in veterinary species remain limited. This condition may arise as a congenital developmental defect or as a consequence of prior traumatic injury leading to fragmentation and displacement of hepatic tissue. This case study describes an incidental intrathoracic ectopic liver identified in a 6-year-old male cat that died of acute suppurative bacterial pneumonia. Necropsy revealed a well-demarcated, encapsulated, large mass within the middle of the caudal mediastinum, unattached to the diaphragm, lungs, or pericardium. Cytologic and histopathologic examinations confirmed the presence of hepatic tissue with preserved lobular architecture. No evidence of previous trauma or diaphragmatic defects was present, supporting the congenital origin. The accompanying severe bacterial pneumonia was unrelated to the mediastinal mass. This study highlights the diagnostic challenges associated with intrathoracic ectopic liver, which can mimic neoplastic or inflammatory masses. Awareness of this entity is essential for accurate diagnosis. Given the documented risk of malignant transformation in ectopic hepatic tissue, surgical excision and histopathological assessment should be considered whenever such lesions are detected.
Radiological insights into a voluminous left-sided Morgagni-Larrey hernia: A case report.
Morgagni-Larrey hernia is a rare condition, accounting for less than 5% of congenital diaphragmatic hernias, with a marked predominance on the right side. Left-sided localizations are encountered rarely due to the protection afforded by the heart and pericardium. We report the case of a 17-year-old patient admitted to the emergency department with acute abdominal pain and dyspnea. Chest X-ray revealed a left basithoracic opacity with air-fluid level, confirmed by thoracoabdominal-pelvic computed tomography as corresponding to a left sided Morgagni-Larrey hernia. The hernial contents were particularly extensive, including the stomach, spleen, transverse colon, omentum, and tail of the pancreas. The patient underwent surgical reduction of the viscera and closure of the diaphragmatic defect, with a favorable postoperative outcome. This case illustrates the rarity of large left-sided Morgagni-Larrey hernias and highlights the importance of imaging, particularly CT, for diagnosis and surgical planning.
Pentalogy of Cantrell: Comprehensive Multimodal Imaging Evaluation in an Adult With Ectopia Cordis.
Pentalogy of Cantrell (PC) is a rare congenital syndrome defined by 5 midline structural defects involving the heart, sternum, diaphragm, pericardium, and abdominal wall. Adult survival is exceptional, particularly in cases associated with ectopia cordis (EC). A 29-year-old asymptomatic man with ectopia cordis was evaluated using multimodal cardiac imaging, which demonstrated sternal, diaphragmatic, and pericardial defects consistent with PC, along with a large ventricular septal defect and patent ductus arteriosus causing pulmonary hypertension. Surgical correction was declined, and medical therapy was indicated with clinical stability. Comprehensive multimodal imaging allows accurate anatomic characterization and functional assessment of complex congenital malformations, while adult presentation underscores the variable spectrum of PC and the potential for survival in partial or less severe forms. PC rarely presents in adulthood. Multimodal imaging is essential for diagnosis and management. Survival depends on less severe intracardiac and thoracoabdominal defects.
Congenital peritoneo-pericardial hernia in a 4 years-old child: Case report of a rare type of congenital diaphragmatic hernia.
Congenital peritoneo-pericardial Hernia (CPPDH) occurs when a defect in the central tendon of the diaphragm allows communication between the peritoneal and pericardial cavities, leading to herniation of intra-abdominal organs into the pericardial cavity. It is an extremely rare form of congenital diaphragmatic hernia with only a few reported cases in the literature. We report a case of congenital peritoneo-pericardial hernia diagnosed in a 4-year-old female child after she presented with fast breathing and intermittent cough. The diagnosis was suspected during echocardiography,when a solid mass having similar echogenicity to the liver was seen in the pericardial cavity. Computed tomography (CT) scan demonstrated a central diaphragmatic defect and herniation of the left liver lobe and the stomach into the pericardial cavity. Currently, surgery is the only option of management, and a correct diagnosis is usually not made prior to surgery. Our report highlights the crucial imaging findings helpful in the preoperative diagnosis, and also the importance of considering CPPDH as a differential diagnosis for an unusual intra-pericardial lesion discovered during echocardiography.
Publicações recentes
A fatal case of gastropericardial fistula due to a benign gastric ulcer.
A novel technique for transdiaphragmatic latero-pericardial cardiophrenic lymph node excision using the minimally invasive surgical access procedure in patient with advanced stage ovarian cancer.
Anesthesia for Pentalogy of Cantrell with Surgical Repair of Tetralogy of Fallot Along with Absent Diaphragm: A Case Study.
Extended resection of a mediastinal tumour with diaphragm reconstruction.
Robotic left intrapericardial upper lobectomy, pericardial reconstruction and diaphragmatic plication.
📚 EuropePMCmostrando 136
An Incidental Necropsy Finding: Intrathoracic Ectopic Liver in a Cat.
Animals : an open access journal from MDPIRadiological insights into a voluminous left-sided Morgagni-Larrey hernia: A case report.
Radiology case reportsCantrell Syndrome and the One Health Perspective: A Unified Review of Human and Comparative Cases.
Veterinary sciencesPentalogy of Cantrell: Comprehensive Multimodal Imaging Evaluation in an Adult With Ectopia Cordis.
JACC. Case reportsCongenital peritoneo-pericardial hernia in a 4 years-old child: Case report of a rare type of congenital diaphragmatic hernia.
Radiology case reportsRobot-Assisted Laparoscopic Repair of Pericardial Hernia in a Heart Transplant Patient.
Annals of thoracic surgery short reportsMassive diaphragmectomy combined with pericardiectomy for ovarian cancer: a case report.
Gynecologic oncology reportsLaparoscopic Repair of Diaphragmatic Pericardial Hernia Following Blunt Trauma: A Case Report.
The American journal of case reportsPrenatal diagnosis and management challenges of Pentalogy of Cantrell at term in a resource-constrained setting: A rare case report.
International journal of surgery case reports[ Giant asymptomatic anterolateral diaphragmatic hernia in an adult: report of a rare case].
Revista de la Facultad de Ciencias Medicas (Cordoba, Argentina)Prenatal ultrasound diagnosis of pentalogy of Cantrell: A case report.
MedicineJugular Venous Doppler Ultrasound as a Non-Invasive Window to Right Heart Hemodynamics: A Narrative Review and Future Perspective.
Therapeutic advances in pulmonary and critical care medicineLong-term survival after extended resection combined with pericardiectomy for locally advanced intrahepatic cholangiocarcinoma: a case report.
Journal of surgical case reportsPeritoneo pericardial hernioplasty in a 2-month-old Shih Tzu.
Open veterinary journalNephrotic syndrome with concurrent effusion from a different cause: A case series.
Journal of family medicine and primary care[MEP-41] Management of Diaphgramatic Dehiscence and Wound Infection After Open Repair of Thoracoabdominal Aortic Aneurysm.
Turk gogus kalp damar cerrahisi dergisiAnesthesia for Pentalogy of Cantrell with Surgical Repair of Tetralogy of Fallot Along with Absent Diaphragm: A Case Study.
Annals of cardiac anaesthesiaMinimally invasive surgery for concomitant pericardial and diaphragmatic rupture after blunt trauma: a case report.
Journal of trauma and injuryReconstruction of a Sternal Cleft and Ventral Hernia in an Adolescent with Pentalogy of Cantrell Utilizing Titanium Plates.
The American surgeonImpact of diaphragm paralysis and its surgical interventions on outcomes after the staged Fontan procedure.
Interdisciplinary cardiovascular and thoracic surgerySubxiphoid hernia, definition and repair: an international delphi consensus.
Hernia : the journal of hernias and abdominal wall surgeryEndometriosis presenting as catamenial pneumothorax, pneumopericardium and pneumoperitoneum.
BMJ case reportsPericardial Hernia After Pericardial Window: A Rare Case.
CureusPiezo, Nephrocyte Function, and Slit Diaphragm Maintenance in Drosophila.
Journal of the American Society of Nephrology : JASNStrangulated pericardial hernia presenting as a case of STEMI; when the disease misleads the physician: a very rare case report.
Annals of medicine and surgery (2012)Multimodality Imaging of Congenital Intrapericardial Diaphragmatic Hernia.
Radiology. Cardiothoracic imagingCase Report: Surgical challenges and insights in a child with a blunt left diaphragmatic and pericardial rupture and heart subluxation.
Frontiers in surgeryDiaphragmatic and pericardial reconstruction using a Gore-Tex® patch in a patient with an invasive liver malignancy.
Clinical journal of gastroenterology[Analysis of Prenatal Ultrasound Manifestations in 15 Cases of Cantrell Syndrome].
Sichuan da xue xue bao. Yi xue ban = Journal of Sichuan University. Medical science editionAcellular Bovine Pericardial Patch for Difficult Abdominal Closure in the Pediatric Population: Our Experience with Review of Literature.
Journal of Indian Association of Pediatric SurgeonsPrimary pericardial synovial sarcoma requiring emergency salvage right atrial debulking: a case report.
Journal of surgical case reportsPulsating abdominal mass in a newborn - Pentalogy of Cantrell with left ventricular diverticulum.
Annals of pediatric cardiologyA Case of Incidentally Discovered Congenital Complete Pericardial Defect during Lobectomy for Lung Cancer: A Case Report and Literature Review.
Annals of thoracic and cardiovascular surgery : official journal of the Association of Thoracic and Cardiovascular Surgeons of AsiaA ventral diaphragmatic advancement technique to repair a large congenital peritoneopericardial diaphragmatic hernia in a dog.
Journal of the American Veterinary Medical AssociationA case of a peritoneal dialysis patient with left pleuroperitoneal communication caused by a pericardial defect after coronary artery bypass surgery.
CEN case reportsEvidence of Pneumopericardium after Elective Ovariectomy in a Peritoneopericardial Diaphragmatic Hernia-Affected Dog: A Case Report.
Animals : an open access journal from MDPIIntrapericardial Diaphragmatic Hernia Following the Convergence Procedure for Atrial Fibrillation.
CureusThe pentalogy of Cantrell: A rare and challenging prenatal diagnosis.
International journal of surgery case reportsGiant right atrial aneurysm associated with persistent left cranial vena cava in a cat.
Journal of veterinary cardiology : the official journal of the European Society of Veterinary CardiologyIatrogenic diaphragmatic herniation of the liver into the pericardium-a case report.
Journal of surgical case reportsSurgical treatment of neonatal Cantrell pentalogy: a case report and literature review.
AME case reportsPentalogy of Cantrell in Two Neonate Littermate Puppies: A Spontaneous Animal Model Suggesting Familial Inheritance.
Animals : an open access journal from MDPICongenital Diaphragmatic Hernia - Diagnosis After Intra-Thoracic Cholecystitis.
Portuguese journal of cardiac thoracic and vascular surgeryA case of a transient phrenic nerve paralysis after resection of a giant lymphangioma evaluated by dynamic digital radiography.
General thoracic and cardiovascular surgery casesIntrapericardial liver herniation after coronary artery bypass grafting: a case report of minimally invasive repair with 20-year follow-up.
Acta chirurgica BelgicaThe Combined Robotic-assisted Laparoscopic and Thoracic Approach in the Management of Diaphragmatic, Pleural, and Pericardial Endometriosis.
Journal of minimally invasive gynecologySingle-site laparoscopic ligation of the hernia sac in infants with congenital Morgagni hernia.
Frontiers in pediatricsSuccessful early diagnosis and surgical treatment of congenital caval foramen hernia in an 8-month-old mixed breed cat.
Brazilian journal of veterinary medicineHypogenetic right lung with partial anomalous pulmonary venous return and accessory diaphragm: a case of "scimitar lung".
Folia morphologicaTraumatic Diaphragmatic Rupture With Pericardial Tear and Transdiaphragmatic Herniation of the Stomach.
CureusSevere pericardial effusion in a cat with peritoneopericardial diaphragmatic hernia and incarcerated hepatic sarcoma.
JFMS open reportsLeft upper lobectomy in a patient with congenital pericardial defect.
Asian cardiovascular & thoracic annalsPentalogy of Cantrell Associated with Ectopia Cordis: A Case Report.
Pediatric health, medicine and therapeuticsRadiological findings of partial expression pentalogy of Cantrell and other multiple congenital anomalies: A rare case report.
Radiology case reportsThe way to a man's heart is through his stomach? A unique case report of transient constrictive pericarditis secondary to infarction of herniated omentum following bariatric surgery.
European heart journal. Case reportsCongenital biventricular cardiac diverticula as a part of class III Cantrell's syndrome: case report.
Cardiology in the youngThe use of biological membranes for correction of congenital malformations.
Cell and tissue banking[Ventricular diverticulum in Cantrell´s pentalogy: rare but not isolated entities].
Archivos peruanos de cardiologia y cirugia cardiovascularCombined Use of Electrocardiography and Ultrasound to Detect Cardiac and Pulmonary Involvement after Recovery from COVID-19 Pneumonia: A Case Series.
Journal of cardiovascular development and diseasePost-ablation Dyspnea a Case Report to Highlight the Differential Diagnoses.
CureusLaparoscopic liver resection with open partial resection of the thoracoabdominal wall for cancer along the transhepatic biliary drainage tract: A case report.
International journal of surgery case reportsPentalogy of Cantrell With a Left Ventricular Diverticulum and Muscular VSD.
The Annals of thoracic surgerySurgical Management of Total Sternal Cleft in a Pentalogy of Cantrell Neonate.
The Annals of thoracic surgeryMalposition of septum primum in isolated dextrocardia: unique and rare form of anomalous pulmonary venous return in association with partial absence of pericardium-case report.
Journal of cardiothoracic surgeryFrequency of sternal variations and anomalies in living individuals evaluated by MDCT.
European journal of radiologyPost-traumatic diaphragmatic rupture with pericardial denudation: A case report.
International journal of surgery case reportsThe complete spectrum of pentalogy of Cantrell in one of a set of dizygotic twins: A case report of a rare congenital anomaly.
MedicineRapidly involuting congenital hemangioma of the liver in a newborn with incomplete Pentalogy of Cantrell: description of a new association.
Journal of surgical case reportsPeritoneopericardial diaphragmatic hernia in a healthy adult feline (Felis catus domesticus): diagnosis to surgical treatment - Case report.
Brazilian journal of veterinary medicineTwin pregnancy in which both fetuses have Cantrell's pentalogy: A case report and literature review.
European journal of obstetrics, gynecology, and reproductive biologyPeritoneal-pericardial diaphragmatic hernia in a 6-year-old male intact pug dog.
The Canadian veterinary journal = La revue veterinaire canadienneLaparoscopic excision of pericardial and diaphragmatic endometriosis.
Fertility and sterilityRare complication after pericardial window: symptomatic diaphragmatic hernia containing bowel and liver.
BMJ case reportsConservative management of Cantrell syndrome: a case report.
Journal of surgical case reportsTransdiaphragmatic-pericardial Hernia: Case Report of an Unusual Condition Managed by Utilization of a Robotic Surgical System.
CureusCase report of traumatic intrapericardial diaphragmatic hernia: Laparoscopic composite mesh repair and literature review.
International journal of surgery case reportsAdult congenital diaphragmatic hernia with absent pericardium and liver heterotopia.
European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic SurgerySuccessful Surgical Separation of Thoraco-Omphalopagus Symmetrical Conjoined Twins in Iran: Two Case Reports.
Iranian journal of medical sciencesCantrell syndrome in the first trimester of pregnancy: imagistic findings and literature review.
Medical ultrasonographyPrenatal Diagnosis and Management of a Rare Central Tendon Defect Type of Congenital Diaphragmatic Hernia with a Massive Pericardial Effusion.
Case reports in obstetrics and gynecologyCantrell Syndrome (Thoracoabdominal Ectopia Cordis; Anomalous Umbilical Cord; Diaphragmatic, Pericardial and Intracardiac Defects) in the Pig (Sus scrofa domesticus).
Journal of comparative pathologyDiagnosis and management of congenital absence of pericardium: a case report.
European heart journal. Case reportsDelayed presentation of pericardio-diaphragmatic hernia following blunt trauma: A case report.
Trauma case reportsComplete and Incomplete Pentalogy of Cantrell.
Children (Basel, Switzerland)MDCT prior to median re-sternotomy in cardiovascular surgery: our experiences, infrequent findings and the crucial role of radiological report.
The British journal of radiologyPentalogy of Cantrell in Full Term Neonate.
AJP reportsFetal Intra-pericardial Morgagni Hernia with effusion affecting one member of a twin gestation.
Echocardiography (Mount Kisco, N.Y.)Ectopia Cordis Associated with Pentalogy of Cantrell-A Case Report.
Revista brasileira de ginecologia e obstetricia : revista da Federacao Brasileira das Sociedades de Ginecologia e ObstetriciaSuccessful treatment of late onset empyema after extrapleural pneumonectomy: A case report.
Respiratory medicine case reportsImaging of thoracic hernias: types and complications.
Insights into imaging[Anesthesia for surgical repair of the pentalogy of Cantrell: case report].
Brazilian journal of anesthesiology (Elsevier)The Usefulness of Magnetic Resonance Imaging of the Cardiovascular System in the Diagnostic Work-Up of Patients With Turner Syndrome.
Frontiers in endocrinologyFetal MRI in the Identification of a Fetal Ventral Wall Defect Spectrum.
AJP reportsA Diaphragmatic Hernia and Pericardial Rupture Caused by Blunt Injury of the Chest: A Case Review.
Journal of trauma nursing : the official journal of the Society of Trauma NursesMorgagni Hernia Causing Incarcerated Bowel and Contributing to Cardiac Arrest.
Current problems in diagnostic radiologyIntrapericardial diaphragmatic hernia into the pericardium after esophagectomy: a case report.
Surgical case reportsPentalogy of Cantrell associated with unilateral anophthalmia: Case report and literature review.
MedicineCantrell Syndrome-A Rare Complex Congenital Anomaly: A Case Report and Literature Review.
Frontiers in pediatricsManagement Challenges in an Infant With Pentalogy of Cantrell, Giant Anterior Encephalocele, and Craniofacial Anomalies: A Case Report.
A&A practiceAbrogation of TGF-beta signalling in TAGLN expressing cells recapitulates Pentalogy of Cantrell in the mouse.
Scientific reportsRepair of Morgagni hernia and ventricular septal defect through sternotomy.
Asian cardiovascular & thoracic annalsAn Autopsy Case of Mesenteric Panniculitis with Massive Pleural Effusions.
The American journal of case reportsLaparoscopic repair of a peritoneopericardial diaphragmatic hernia after a convergent procedure for the treatment of atrial fibrillation.
Journal of thoracic diseaseAsymptomatic adult intrapericardial diaphragmatic hernia detected on cardiac SPECT CT.
Journal of nuclear cardiology : official publication of the American Society of Nuclear CardiologySternal malformations and anesthetic management.
Paediatric anaesthesiaCongenital Diaphragmatic Hernia with Liver Herniation into the Pericardial Sac in a 30-Week Gestation Infant.
Pediatric and developmental pathology : the official journal of the Society for Pediatric Pathology and the Paediatric Pathology SocietySevere Intrauterine Amputations in One Dichorionic Twin With Pentalogy of Cantrell: Further Evidence and Consideration for Mechanical Teratogenesis.
Pediatric and developmental pathology : the official journal of the Society for Pediatric Pathology and the Paediatric Pathology SocietyIndentation in the Right Ventricle by an Incomplete Pericardium on 3-Dimensional Reconstructed Computed Tomography.
The Korean journal of thoracic and cardiovascular surgeryPericardial Herniation of Small Bowel Post Minimally Invasive Hybrid Maze of Atrial Fibrillation.
The Journal of emergency medicineRepair of Intrapericardial Diaphragmatic Hernia during Aortic Surgery in a 78-Year-Old Woman.
Texas Heart Institute journalAcquired transdiaphragmatic hernia: an unusual cause of cardiac tamponade.
Asian cardiovascular & thoracic annalsA Recurrent Case of Pentalogy of Cantrell: A Rare Case with Sonological Findings and Review of Literature.
Polish journal of radiologyPericardio-Amniotic Shunting for Incomplete Pentalogy of Cantrell.
Fetal diagnosis and therapyLaparoscopic repair of an iatrogenic intrapericardial diaphragmatic hernia using the falciform ligament flap.
Acta chirurgica BelgicaMorgagni hernia presenting with massive pericardial effusion and ascites: prenatal management by thoraco-amniotic shunting and fetal endoscopic tracheal occlusion (FETO) and review of the literature.
Archives of gynecology and obstetricsHepatic fibrosarcoma incarcerated in a peritoneopericardial diaphragmatic hernia in a cat.
JFMS open reportsIncomplete Pentalogy of Cantrell--A Case Report.
Mymensingh medical journal : MMJHepatoblastoma of the adult with pericardial metastasis: A case report.
International journal of surgery case reportsCharacterization of primary pulmonary adenosquamous carcinoma-associated pleural effusion.
Veterinary clinical pathologyUse of Unique Doppler Flow-Pattern for the Diagnosis of Left Ventricular Diverticulum.
Echocardiography (Mount Kisco, N.Y.)A case of Cantrell syndrome diagnosed in the first trimester.
Clinical and experimental obstetrics & gynecologyCongenital diaphragmatic hernia with concurrent aplasia of the pericardium in a foal.
BMC veterinary researchPreviously Complicated Nuss Procedure Does Not Preclude Blind Removal of the Bar.
The Thoracic and cardiovascular surgeonPentalogy of Cantrell: Case Report With Review of the Literature.
Advances in neonatal care : official journal of the National Association of Neonatal NursesClass II pentalogy of Cantrell.
BMC research notesCardiac malposition (ectopia cordis) in a cat.
Journal of veterinary emergency and critical care (San Antonio, Tex. : 2001)Pentalogy of Cantrell accompanied by scoliosis and pes equinovarus deformity at 12 weeks gestation.
Clinical and experimental obstetrics & gynecologyPentalogy of Cantrell: a case report.
BJR case reportsSternal Cleft Associated with Cantrell's Pentalogy in a German Shepherd Dog.
Journal of the American Animal Hospital AssociationLaparoscopic repair of Morgagni hernia by artificial pericardium patch in an adult obese patient.
Journal of thoracic disease5, 4, 3, 2, 1: embryologic variants of pentalogy of Cantrell.
The Journal of surgical researchThe hepatic buttress: A novel surgical technique to treat an intrapericardial diaphragmatic defect after hybrid myocardial ablation.
The Journal of thoracic and cardiovascular surgeryPentalogy of Cantrell with Ectopia Cordis: CT Findings.
Journal of radiology case reportsOne-stage surgical treatment for Cantrell syndrome without repairing the left ventricular diverticulum: a case report.
Cardiology in the youngGiant solitary fibrous tumor of the diaphragm: a case report and review of literature.
International journal of clinical and experimental pathologyCongenital peritoneopericardial diaphragmatic hernia in a terrier dog.
Veterinary research forum : an international quarterly journalAssociações
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Cantrell Syndrome and the One Health Perspective: A Unified Review of Human and Comparative Cases.
- An Incidental Necropsy Finding: Intrathoracic Ectopic Liver in a Cat.
- Radiological insights into a voluminous left-sided Morgagni-Larrey hernia: A case report.
- Pentalogy of Cantrell: Comprehensive Multimodal Imaging Evaluation in an Adult With Ectopia Cordis.
- Congenital peritoneo-pericardial hernia in a 4 years-old child: Case report of a rare type of congenital diaphragmatic hernia.
- A fatal case of gastropericardial fistula due to a benign gastric ulcer.
- A novel technique for transdiaphragmatic latero-pericardial cardiophrenic lymph node excision using the minimally invasive surgical access procedure in patient with advanced stage ovarian cancer.
- Anesthesia for Pentalogy of Cantrell with Surgical Repair of Tetralogy of Fallot Along with Absent Diaphragm: A Case Study.
- Extended resection of a mediastinal tumour with diaphragm reconstruction.
- Robotic left intrapericardial upper lobectomy, pericardial reconstruction and diaphragmatic plication.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:2847(Orphanet)
- MONDO:0017301(MONDO)
- GARD:18780(GARD (NIH))
- Busca completa no PubMed(PubMed)
- Q55786970(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
