Tumor maligno que surge das células endoteliais dos vasos sanguíneos. Microscopicamente, é caracterizado por canais vasculares frequentemente abertos, anastomosados e ramificados. As células malignas que revestem os canais vasculares são fusiformes ou epitelióides e frequentemente apresentam núcleos hipercromáticos. Os angiossarcomas ocorrem com mais frequência na pele e na mama. Pacientes com linfedema de longa data apresentam risco aumentado de desenvolver angiossarcoma.
Introdução
O que você precisa saber de cara
Tumor maligno que surge das células endoteliais dos vasos sanguíneos. Microscopicamente, é caracterizado por canais vasculares frequentemente abertos, anastomosados e ramificados. As células malignas que revestem os canais vasculares são fusiformes ou epitelióides e frequentemente apresentam núcleos hipercromáticos. Os angiossarcomas ocorrem com mais frequência na pele e na mama. Pacientes com linfedema de longa data apresentam risco aumentado de desenvolver angiossarcoma.
Escala de raridade
<1/50kMuito rara
1/20kRara
1/10kPouco freq.
1/5kIncomum
1/2k
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Características mais comuns
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Os sinais que médicos procuram e os exames que confirmam
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Mostrando amostra de 200 publicações de um total de 3.365
Primary low-grade breast angiosarcoma initially misdiagnosed as a benign vascular lesion.
Primary breast angiosarcoma is an exceptionally rare malignancy, particularly in elderly patients, and may closely resemble benign vascular lesions on imaging and core needle biopsy. We report a case of low-grade primary angiosarcoma in a woman in her late 70s, initially misdiagnosed as a haemangioma despite interval tumour growth. A definitive diagnosis was achieved only after wide local excision, which demonstrated well to intermediately differentiated angiosarcoma with clear margins. Given the limited evidence supporting adjuvant therapy in low-grade disease, surgery alone was appropriate, and the patient remains recurrence-free at 2.5 years. This case highlights the diagnostic challenges and importance of maintaining suspicion in older adults.
Primary cerebellar angiosarcoma: A rare case of posterior fossa vascular tumor with hemorrhagic presentation and favorable surgical outcome.
Primary cerebellar angiosarcoma is an exceptionally rare intracranial malignancy, with only 22 cases reported in the literature. We report the case of a 67-year-old male who presented with a severe headache, unsteady gait, and giddiness. Computed tomography of the brain demonstrated a hemorrhagic lesion in the right cerebellar hemisphere with associated vasogenic edema and early hydrocephalus. Magnetic resonance imaging revealed a right cerebellar intra-axial lesion with mixed signal intensities and a characteristic peripheral "bull's eye" enhancement pattern. Histopathological evaluation showed a vasoformative neoplasm with atypical endothelial cells, high mitotic activity, and immunopositivity for CD31 and erythroblast transformation specific (ETS)-related gene (ERG), consistent with low-grade angiosarcoma. The patient underwent gross total resection and remained recurrence-free 16 months postoperatively. This case underscores the importance of multi-modality imaging in the early recognition of hemorrhagic cerebellar tumors and reinforces the role of radiological-pathological correlation in diagnosis and treatment planning. Given its rarity, diagnosis of cerebellar angiosarcoma requires a high index of suspicion, supported by advanced imaging and immunohistochemical profiling. Multidisciplinary management is essential, and further case documentation is necessary to guide therapeutic strategies and prognostication.
Hepatic Angiosarcoma Associated with Chronic Schistosomiasis in a Patient with Decompensated Cirrhosis: A Rare Case Report.
Hepatic angiosarcoma (HA) is a rare endothelial malignancy with poor prognosis. Chronic Schistosoma infection causes periportal fibrosis and portal hypertension, but has not been established as a risk factor for hepatic vascular tumors. We report a case of high-grade HA coexisting with chronic schistosomiasis in a patient presenting with acute decompensated cirrhosis. A 64-year-old Filipino woman with no known chemical exposures presented with progressive abdominal pain, jaundice, ascites, and hepatic encephalopathy. Doppler ultrasound initially suggested Budd-Chiari syndrome, later excluded on advanced imaging. MRI showed multifocal hepatic lesions, and CT demonstrated multiple intra-abdominal hematomas without active bleeding. Liver biopsy confirmed poorly differentiated HA (CD31+/CD34+) and revealed calcified Schistosoma eggs. Her course was complicated by hemorrhagic shock after biopsy and paracentesis, spontaneous bacterial peritonitis, acute kidney injury, and worsening hepatic encephalopathy. She died despite aggressive supportive care. This case illustrates the diagnostic challenges and rapid progression of HA, especially in coagulopathic patients where biopsy carries significant risk. The coexistence of chronic schistosomiasis raises the possibility of parasitic inflammation contributing to hepatic vascular tumorigenesis. HA should be considered among unexplained hepatic masses with atypical imaging and clinical features.
Primary splenic angiosarcoma with diffuse intrasinusoidal hepatic metastasis mimicking lymphoma: a diagnostic challenge.
Primary splenic angiosarcoma is a rare aggressive vascular neoplasm. Although hepatic metastases are common, diffuse intrasinusoidal hepatic involvement is extremely rare and poses a significant diagnostic challenge. A 60-year-old woman presented with bilateral lower extremity edema, hypoalbuminemia, and thrombocytopenia. Contrast-enhanced computed tomography revealed marked splenomegaly, but no distinct hepatic lesions. Gadoxetic acid-enhanced magnetic resonance imaging revealed reduced hepatic uptake without focal abnormalities. 1⁸F-fluorodeoxyglucose positron emission tomography-computed tomography revealed diffuse radiotracer uptake in both the liver and spleen, raising the suspicion of an infiltrative malignant process, such as lymphoma. Liver biopsy revealed sinusoidal infiltration by atypical cells positive for cluster of differentiation 31 and ETS-related gene, but lacked architectural features diagnostic of angiosarcoma. Due to diagnostic uncertainty and concerns regarding splenic rupture, splenectomy was performed. Histopathological examination confirmed a primary splenic angiosarcoma with diffuse intrasinusoidal hepatic metastasis. Primary splenic angiosarcoma rarely presents with non-nodular intrasinusoidal hepatic metastasis, mimicking infiltrative liver diseases. Liver biopsy may fail to yield a definitive diagnosis. Therefore, a splenectomy may be required to establish a definitive diagnosis and guiding appropriate management when liver biopsy is inconclusive. Recognizing this uncommon metastatic pattern is crucial to avoid misdiagnosis and ensure timely treatment.
Spinal epithelioid angiosarcoma: a diagnostically and therapeutically challenging entity treated with chemoradiotherapy.
Primary spinal angiosarcoma is extremely rare with few reported cases globally. While en bloc resection is the only definitive and curative treatment modality, this case highlights the potential for curative-intent, non-surgical management of spinal epithelioid angiosarcoma using taxane-based chemoradiotherapy, especially in anatomically challenging and surgically unresectable locations. It also emphasises the role of multimodal imaging and histopathological correlation in the diagnosis and monitoring of rare spinal tumours.
Publicações recentes
Case Report of Primary Splenic Angiosarcoma in a Young Patient: A Very Rare and Challenging Disease.
📖 RevisãoBreast Angiosarcoma: 15-Years Experience.
🥉 Relato de casoLiposomal Versus Conventional Doxorubicin as First-Line Therapy in Advanced Soft Tissue Sarcomas: Observational Multi-Institutional Cohort of 8.5-Year Experience.
Surgical Management of Primary and Metastatic Cardiac Malignancies: A 20-Year Single-Center Experience.
📖 RevisãoDiagnostic Pitfalls and Imaging-Pathologic Correlation in Benign Breast Vascular Lesions Mimicking Malignancy: A Case-Based Systematic Review.
📚 EuropePMC5.021 artigos no totalmostrando 196
Primary low-grade breast angiosarcoma initially misdiagnosed as a benign vascular lesion.
BMJ case reportsImmune cell clustering identifies a CD163⁺/CSF1R⁺ macrophage and neutrophil-enriched phenotype with distinct biological signatures and poor prognosis in angiosarcoma.
OncoimmunologyPrimary cardiac angiosarcoma with isolated superior vena cava syndrome: a case report.
Journal of medical case reportsAcross borders and histologies: Rethinking endpoints for vascular sarcoma trials.
Clinical cancer research : an official journal of the American Association for Cancer ResearchLife-Threatening Lower GI Bleeding From Sigmoid Colon Metastasis of Cutaneous Angiosarcoma: A Case Report.
CureusNonconventional MYC-Positive Primary Cutaneous Angiosarcoma: Novel or Untested.
The American Journal of dermatopathologyRevisiting the Immune Frontier in Soft Tissue Sarcomas.
Current oncology reportsA rare pulmonary epithelioid angiosarcoma with ALK rearrangement: a case report and literature review.
Frontiers in oncologyDeceptive Thyroid Pathologies: Anaplastic Thyroid Carcinoma Mimics and Clinical Implications.
Head & neckAtypical Postradiation Vascular Proliferation: A Rare Dermatologic Sequela of Breast Cancer Therapy.
Clinical breast cancerRadiation-Induced Angiosarcoma of the Breast With Diffuse GATA-3 Positivity: A Possible Diagnostic Pitfall.
The American Journal of dermatopathologyDiagnosis and treatment of primary orbital angiosarcoma - a case study and review of the literature.
Orbit (Amsterdam, Netherlands)Overcoming Diagnostic and Therapeutic Challenges in Primary Cardiac Angiosarcoma.
JACC. Case reportsTissue Is Not the Only Issue in Multimodality, Multidisciplinary Cardiac Mass Evaluation.
JACC. Case reportsGenome agnostic, multi-level non-oncogene addiction-based systems pharmacology for rescuing metastatic relapsed/refractory neoplasias.
Frontiers in pharmacologyRare Angiosarcoma in the Postauricular Region-A Diagnostic Challenge and Treatment.
Clinical case reportsAnastomosing hemangioma of the renal pelvis: The first case report from Vietnam.
Urology case reports18F-FDG Outperforms 18F-FAPI-04 in Detecting Primary Splenic Angiosarcoma and Its Metastatic Lesions in Liver.
Clinical nuclear medicinePrimary epithelioid angiosarcoma of the vulva: A rare tumor at an unusual site.
Rare tumorsRadiation-Induced Angiosarcoma Following Breast Surgery: A Case Report.
Surgical case reportsPrimary Pericardial Angiosarcoma Demonstrating Initial Response Followed by Progression on First-Line Chemotherapy: A Case Report.
Clinical case reportsA Rare Case of Primary Breast Angiosarcoma: Diagnostic Challenges and Findings.
Journal of clinical ultrasound : JCUHemangiosarcoma: A Systematic Review of Biomarkers in Diagnosis, Prognosis, and Therapeutic Strategies.
Veterinary and comparative oncologyClinical Characteristics and Prognostic Factors of Renal Sarcoma: A Japanese National Cancer Registry Study.
Cancer investigationEfficacy and safety of pazopanib in patients with paclitaxel-pretreated primary cutaneous angiosarcoma in Japan: Results of the Japan Clinical Oncology Group single-arm confirmatory trial (JCOG1605).
The British journal of dermatologyEvaluation of Radiotherapy Dose in Secondary Breast Angiosarcoma: Implications for Pathogenesis.
Anticancer researchLarge atypical cells with foamy cytoplasm in bone marrow in primary splenic angiosarcoma: a case report.
International journal of hematologyVascular bone tumors of the pelvis and extremities: an 18-case clinical and radiological analysis.
Archives of orthopaedic and trauma surgeryGenomic Landscape and Therapeutic Implications of Metaplastic Breast Carcinoma: Insights from a Nationwide Database Including Diagnostic Mimickers.
Pharmaceuticals (Basel, Switzerland)Primary Angiosarcoma of Breast: Surgery Alone Versus Chemotherapy and/or Radiotherapy-A Systematic Review and Meta-Analysis.
CancersIncidence and Survival of Thoracic Angiosarcoma: Epidemiologic Evidence from a Population-Based Cancer Registry.
CancersCanonical microRNA loss drives tumor development implicating therapeutic efficacy of enoxacin in angiosarcoma.
RNA (New York, N.Y.)Expanded Radiologic Characterization and Long-Term Imaging Follow-Up of Sclerosing Angiomatoid Nodular Transformation (SANT): A Case Report.
CureusAn Atypical Presentation of Cutaneous Angiosarcoma: A Diagnostic Challenge in an End-Stage Renal Disease Patient.
CureusPrimary angiosarcoma of the seminal vesicle: a detailed case report and literature review of an extremely rare urological malignancy.
BMC urologyAngiosarcoma Presenting as Hemifacial Edema.
Ophthalmic plastic and reconstructive surgerySilent Invader: The Enigmatic Case of Cardiac Angiosarcoma.
CureusPostradiation angiosarcoma of the breast: a 25-year single-institution analysis of clinicopathological characteristics and immunohistochemical biomarker study.
Biotechnic & histochemistry : official publication of the Biological Stain CommissionPresentation, management, and outcomes of malignant vascular sarcomas: a National Cancer Database comparison of pediatrics and adults.
American journal of surgeryStewart-Treves syndrome: A fatal complication of rheumatoid arthritis-associated massive lymphedema.
JAAD case reportsRight Atrial Mass in a 63-Year-Old Woman.
ChestLow Subcutaneous Adipose Tissue is Associated with Poor Prognosis for Aged Patients with Cutaneous Angiosarcoma: A Retrospective Cohort Study.
Acta dermato-venereologicaUnique advantages of contrast-enhanced ultrasound in identifying extremely rare hepatic angiosarcoma with sinusoidal growth patterns.
Quantitative imaging in medicine and surgeryRight Atrial Angiosarcoma Presenting With Cardiac Tamponade, Hemorrhagic Pericardial Effusion, and Pulmonary Embolism: A Case Report.
CureusMultidisciplinary Management of a Rare Primary Cardiac Angiosarcoma.
JACC. Case reportsPost-Traumatic Intravascular Papillary Endothelial Hyperplasia (Masson Tumor) of the Eyelid.
The Journal of craniofacial surgeryCustomized Non-invasive Brachytherapy With Tailored Surface Moulds: An Experience From a Tertiary Care Centre.
Clinical oncology (Royal College of Radiologists (Great Britain))The anti-apoptotic protein lifeguard is expressed in osteosarcoma, chondrosarcoma and soft tissue sarcoma.
OncologyClinicopathological features and survival disparities between axial and appendicular skeletal Angiosarcoma: A SEER-based analysis using competing risk models.
Journal of bone oncologyPrimary renal angiosarcoma with renal vein thrombus: Case report and Review of literature.
Urology case reportsPrimary cerebellar angiosarcoma: A rare case of posterior fossa vascular tumor with hemorrhagic presentation and favorable surgical outcome.
Journal of clinical imaging scienceTreatment Beyond Progressive Disease With Pazopanib for Cutaneous Angiosarcoma: A Case Report.
The Journal of dermatologyCircumferential Resection of the Right Atrium to Excise Angiosarcoma.
JACC. Case reportsHepatic Angiosarcoma Mimicking Sinusoidal Obstruction Syndrome: A Case Report.
CureusMalignant vascular neoplasms of the distal female genital tract: a series of 19 cases emphasizing unusual features and diagnostic challenges.
HistopathologyPrimary Hepatic Angiosarcoma: Distinct Imaging Phenotypes Mirroring Histopathologic Growth Patterns in a Retrospective Human Study.
Diagnostics (Basel, Switzerland)Selective MYC 5' amplification in postirradiation/lymphedema-associated angiosarcoma.
Virchows Archiv : an international journal of pathologyHepatic Angiosarcoma Associated with Chronic Schistosomiasis in a Patient with Decompensated Cirrhosis: A Rare Case Report.
Case reports in gastroenterologyHypopyon Sign in Acral Lesions: Dermoscopic Findings of a Patient with Palmoplantar Pustulosis.
Current health sciences journalAwake mastectomy in a patient with severe cardio-respiratory disease.
Anaesthesia reportsDiagnostic Utility of Contrast-Enhanced Ultrasound and Multimodal Imaging in Splenic Angiosarcoma: A Pathologically Confirmed Case Report.
Journal of clinical ultrasound : JCUPhase II trial, multicenter, first-line paclitaxel-avelumab treatment of inoperable angiosarcoma (KCSG UN 18-15).
ESMO openPrimary epithelioid angiosarcoma of the jejunum presenting with severe anemia and distant metastasis: a case report and literature review.
Frontiers in oncologyBreast Hemangioma with Slow Growth over 11 Years: A Case Report.
Reports (MDPI)Exploring the enigma within: a retrospective study of primary cardiac sarcomas from a tertiary care centre.
EcancermedicalscienceAtypical Vulvovaginal Postradiation Vascular Lesion: A Distinctive, Benign Mimic of Angiosarcoma Characterized in a Series of 15 Patients.
The American journal of surgical pathologyPrimary aortic angiosarcoma following endovascular aneurysm repair: Case report and review of the literature.
Journal of vascular surgery cases and innovative techniquesA rare vascular puzzle: Portal hypertension and hepatic lesions.
Journal of hepatology[Radiation-Associated Angiosarcoma of the Breast-A Case Report].
Gan to kagaku ryoho. Cancer & chemotherapyOne case of left atrial arterial intimal sarcoma.
International journal of surgery case reportsAngiosarcoma developing in an ovarian fibroma: A case report.
Revista espanola de patologia : publicacion oficial de la Sociedad Espanola de Anatomia Patologica y de la Sociedad Espanola de CitologiaClinical and Pathological Significance of GLUT-1 Expression in Angiosarcoma and Other Vascular Tumors.
The Journal of dermatologyPrimary splenic angiosarcoma with diffuse intrasinusoidal hepatic metastasis mimicking lymphoma: a diagnostic challenge.
Clinical journal of gastroenterologySurgical resection of a primary cardiac angiosarcoma and reconstruction of involved right atrium.
Journal of surgical case reportsAdvances in Clinical Trials of Boron Neutron Capture Therapy.
Research (Washington, D.C.)CT findings of primary hepatic angiosarcoma complicated with hepatic sinusoidal obstruction syndrome: a case description.
Quantitative imaging in medicine and surgeryDiagnosis, treatment, and prognosis of scalp angiosarcoma: A case report.
MedicineContributors of All-Causes Mortality in Patients With Primary and Secondary Cutaneous Angiosarcoma.
Dermatologic surgery : official publication for American Society for Dermatologic Surgery [et al.]Multimodal Therapy in Cutaneous Angiosarcoma: A National Cancer Database Study of Treatment Patterns and Survival.
Annals of surgical oncologyAdult urologic sarcomas: a single institution experience over 25 years.
The Canadian journal of urologyMultimodal treatment of radiation-associated laryngeal angiosarcoma: A case report and literature review.
MedicineSpinal epithelioid angiosarcoma: a diagnostically and therapeutically challenging entity treated with chemoradiotherapy.
BMJ case reportsCardiac epithelioid hemangioendothelioma with WWTR1::ACTL6A fusion and atypical histology mimicking cardiac angiosarcoma.
HistopathologyPseudoangiomatous Stromal Hyperplasia in the Breast: A Report of a Rare Case.
CureusCongenital lumbosacral meningocele with malignant transformation to epithelioid angiosarcoma: A case report of complex spinal anomalies.
Radiology case reportsPrimary Angiosarcoma of Bone of the Skull Base: A Case Report and Literature Review.
CureusAtypical presentation of angiosarcoma detected by 18F-FDG PET/CT as a solitary mediastinal lesion.
Revista espanola de medicina nuclear e imagen molecularPeritoneal Post-Radiation Angiosarcoma in a Patient With a History of Radiation for Cervical Cancer.
The American journal of case reportsA Phase 2 Study of the Eribulin in Patients with Metastatic Angiosarcoma and Epithelioid Hemangioendothelioma (EHE).
Clinical cancer research : an official journal of the American Association for Cancer ResearchFive Cases of Hepatic Mesenchymal Tumors Diagnosed by Endoscopic Ultrasound-Guided Tissue Acquisition.
DEN openPreoperative Embolization for Sinonasal Angiosarcoma Optimized Intraoperative and Postoperative Outcomes: A Case Report.
The Annals of otology, rhinology, and laryngologyNasal Angiosarcoma Mimicking Common Sinonasal Tumors.
The Journal of craniofacial surgeryPrimary Cardiac Sarcomas: Clinical Characteristics, Management, and Outcomes at a Spanish National Reference Center.
CancersAngiosarcoma Arising in 1 of 2 Adolescent Twins With Cryptogenic Cirrhosis and MAF Gene Mutation.
Pediatric and developmental pathology : the official journal of the Society for Pediatric Pathology and the Paediatric Pathology SocietyDiagnostic pitfalls: soft-tissue sarcomas initially misdiagnosed as benign vascular anomalies-a case report and systematic review.
Oncology reviewsPrimary adrenal angiosarcoma: a rare case presentation.
Journal of surgical case reportsRecent advances in chemotherapy and targeted therapies for breast sarcoma.
Expert review of anticancer therapyThyroid angiosarcoma: a comprehensive review.
Seminars in diagnostic pathologyCardiac Angiosarcoma as an Unexpected Cause of Palpitations: Case Report, Differential Diagnosis, and Current Therapeutic Approach to Cardiac Tumors.
CureusRESOLVING DIFFICULT HISTOLOGICAL DIAGNOSIS OF THE RARE ACANTHOLYTIC SQUAMOUS CELL CARCINOMA USING IMMUNOHISTOCHEMISTRY: A CASE REPORT.
Annals of Ibadan postgraduate medicineThe "silent assassin" of the liver: angiosarcoma with portal hypertension.
Medical ultrasonographyRadiation-Induced Epithelioid Angiosarcoma of the Urinary Bladder Mimicking Sarcomatoid Carcinoma: A Rare Entity and Literature Review.
International journal of surgical pathologyAristolochic Acid and Alternative Lengthening of Telomeres Mechanisms Underlie Liver Angiosarcoma Pathogenesis.
Liver cancerLeft Atrial Epithelioid Angiosarcoma Presenting As Recurrent Stroke: A Case Report.
CureusImaging approach to retroperitoneal vascular tumors: a narrative review.
Abdominal radiology (New York)Concomitant gastric carcinoma and primary hepatic angiosarcoma in a patient: A case report.
Open life sciencesThe diagnostic dilemma of sinusoidal-type primary hepatic angiosarcoma: A case report and literature review.
Frontiers in oncologyAngiomatosis of the Breast: Unveiling a Rare and Unusual Vascular Puzzle.
CureusMalignant Right Atrial Mass With Inferior Vena Cava Extension Presenting as Budd-Chiari Syndrome: A Multimodality Imaging Case Report.
CureusEvolution of retiform hemangioendothelioma into angiosarcoma.
JAAD case reports99m Tc-RBC SPECT/CT Scintigraphy for Diagnosis of Small Intestinal Angiosarcoma : A Case Report.
Clinical nuclear medicineCardiac Angiosarcoma With Lung Metastasis Presenting as Granuloma-Like Lesions: One Case Report and Literature Review.
Respirology case reportsMultiple Pulmonary Cavernous Hemangioma: A Case Report.
Surgical case reportsPrimary breast angiosarcoma with diagnostic pitfalls and management challenges.
BMJ case reportsSpontaneous hepatic rupture: A catastrophic complication in a patient with primary splenic angiosarcoma and hepatic metastasis: case report and literature review.
Frontiers in oncologySignet ring cell cutaneous angiosarcoma with ATM deletion mutation on scalp.
JAAD case reportsPotential characteristic image findings of primary angiosarcoma of the breast: A case report.
Radiology case reportsPrimary Epithelioid Angiosarcoma of the Penis With Aberrant Expression of Synaptophysin: A Case Report and Review of Diagnostic Pitfalls.
Journal of cutaneous pathologyMolecular Characterization of Primary Ovarian Angiosarcoma in a Patient With a History of Mature Ovarian Teratoma.
CureusPrimary Cardiac Osteosarcoma: Epidemiology, Diagnosis, and Management - A Narrative Review.
Orthopedic reviewsGenomic and Demographic Characteristics of Angiosarcoma as Described in the AACR Project GENIE Registry.
CancersPrimary non-Hodgkin's lymphoma of the right atrium presenting as a cardiac mass: surgical debulking followed by chemotherapy.
Indian journal of thoracic and cardiovascular surgeryClinicopathological Features and Therapeutic Outcomes of Head and Neck Sarcomas: A 14-Year Retrospective Study.
CureusRare Indications of Splenectomy: A Case Series and Literature Review.
CureusPrimary cerebellar angiosarcoma: a rare case report and literature review.
BMC surgeryA Case Report of Surgical and Postoperative Treatment for Thyroid Angiosarcoma with Pulmonary Metastasis.
Surgical case reportsSoft-Tissue Chest Wall Reconstruction for Secondary Angiosarcoma: Systematic Review and Case Series.
Annals of plastic surgeryA Discovery of Potentially Hereditary Cardiac Angiosarcoma.
JACC. Case reportsUtility of 18F-FDG PET/CT for diagnosing and staging solitary malignant tumors of the spleen.
Frontiers in medicineSarcoma: Cardiovascular and Oncologic Considerations: JACC: CardioOncology State-of-the-Art Review.
JACC. CardioOncologyMulti-omics analysis revealed potential use of immunotherapy and CDK4/6 inhibitors in intimal sarcoma.
Frontiers in immunologyConcurrent MYC-Amplified Secondary Angiosarcoma and Recurrent Carcinoma in the Breast: A Rare Presentation With Unique Clinical Features and Distinct MYC Amplification Patterns.
International journal of surgical pathologyPrimary pulmonary angiosarcoma: A case study with genetic insights and potential therapeutic targets.
Oncology lettersMultidisciplinary treatment for primary cardiac angiosarcoma: a case report and overview of the literature.
BMC cardiovascular disordersSeeking out the primary tumour: multi-modality imaging of metastatic cardiac angiosarcoma.
European heart journal. Imaging methods and practiceMyeloid Sarcoma Versus Epithelioid Angiosarcoma: A Case Report of a Potential Diagnostic Pitfall.
International journal of surgical pathologySplenic angiosarcoma with hepatic and cardiac metastases: a case report and literature review.
Frontiers in oncologySecondary Lower-Body Sarcomas in Cervical Cancer Survivors Following Surgery, Radiotherapy, or Both: A Population-Based Study.
Cancer science[Primary duodenal epithelioid angiosarcoma:a case report].
Nihon Shokakibyo Gakkai zasshi = The Japanese journal of gastro-enterologyPrimary Pulmonary Epithelioid Angiosarcoma With Partial Response to Paclitaxel Treatment: A Case Report.
CureusCutaneous Angiosarcoma Mimicking Masson's Tumor in an Elderly Male: A Diagnostic Challenge and Treatment Failure.
CureusRavulizumab as an alternative for gemcitabine related trombotic microangiopathy: A case report.
NefrologiaCorrespondence: Prognostic significance of positive surgical margins for scalp angiosarcoma.
Journal of the Formosan Medical Association = Taiwan yi zhiRadiation-induced angiosarcoma of the breast - experience from clinical practice.
Ceska gynekologiePulmonary artery angiosarcoma.
ThoraxAn exceedingly rare case of de novo hepatic angiosarcoma in a transplanted liver.
Radiology case reportsSimply the (B)EST: what the interventionalist needs to know about (bleomycin) electrosclerotherapy for vascular anomalies.
European radiologyAcute rupture of primary hepatic angiosarcoma with Kasabach-Merritt syndrome: a rare case report and literature review.
World journal of surgical oncologyPrimary epithelioid angiosarcoma of the liver.
Clinical journal of gastroenterologyHigh-Grade Angiosarcoma Transformation in Schwannoma and SMARCB1 Mutation: A Case Report.
The American journal of case reportsCharacteristics, Outcomes, and Risk Factors in Primary and Secondary Angiosarcoma: A Retrospective Cohort Study.
The breast journalClinicopathologic and radio-genomic insights into hepatic epithelioid hemangioma: An illustrated review.
Human pathologyThe RANK-RANKL-OPG axis in dermatological malignancies: A systematic review.
International immunopharmacologyAngiosarcoma Revisited: Diagnostic Challenges and a 16-Year Retrospective Analysis from a Single Institution.
Iranian journal of pathologyNovel Therapeutic Approaches for Cutaneous Angiosarcoma, Particularly Focusing on Immune Checkpoint Inhibitors.
CancersPulmonary metastatic paraganglioma with angiosarcomatous differentiation: a rare case report and literature review.
The Pan African medical journalIntravascular organizing thrombus in the forearm: a unique imaging presentation.
Skeletal radiologyContrast-Enhanced Ultrasound-Guided Liver Tumor Biopsy for Primary Hepatic Angiosarcoma: A Case Series.
CureusDestructive upper limb malignant ulcer: A case report of angiosarcoma.
International journal of surgery case reportsANGIOSARCOMA ASSOCIATED WITH RADIATION THERAPY IN PATIENTS WITH A HISTORY OF INVASIVE BREAST CARCINOMA. A CASE REPORT AND REVIEW OF THE LITERATURE.
Experimental oncologyPrimary Uterine Angiosarcoma Presenting With Omental Metastasis, Lymph Node Involvement, and Demonstrating a Null p53 Mutational Staining Pattern.
International journal of surgical pathologyDiffuse Alveolar Haemorrhage Complicated by Pulmonary Metastasis of Cardiac Angiosarcoma and Kasabach-Merritt Syndrome: A Case Report.
Respirology case reportsEfficacy and Safety of Helical Tomotherapy Combined With Paclitaxel in Cutaneous Angiosarcoma.
The Journal of dermatologyPrimary Breast Angiosarcoma: A Case Report.
CureusPrimary cardiac angiosarcoma with right atrial rupture.
Interdisciplinary cardiovascular and thoracic surgeryA synthetic cohort analysis of postoperative management of primary cardiac angiosarcoma and a case report.
Frontiers in oncologySinonasal Sarcomas Management: An International Consensus Statement.
International forum of allergy & rhinologyVaccination Against Extracellular Vimentin Plus Doxorubicin for Canine Hemangiosarcoma.
International journal of molecular sciencesTriangulating Timing, Tropism and Burden of Sarcoma Metastases: Toward Precision Surveillance and Therapy in a Real-World-Time Cohort.
CancersPlasminogen Activator Inhibitor-1 in Skin Malignancies: Therapeutic Implications of Its Inhibition.
BiomoleculesPAI-1 in Skin Malignancies: a Central Regulator of Tumor Progression and Therapeutic Resistance.
Current treatment options in oncologyRadiation-Associated Breast Angiosarcoma Versus Recurrent Invasive Ductal Carcinoma After Partial Mastectomy: A Diagnostic Dilemma.
Clinical case reportsMultimodal Imaging in the Diagnosis of Primary Aortic Epithelioid Angiosarcoma.
CureusSurvival Outcomes in Cutaneous Angiosarcoma: A Meta Analysis.
Dermatologic surgery : official publication for American Society for Dermatologic Surgery [et al.]Outcome of 1773 superficial non-dermatofibrosarcoma sarcomas A French Sarcoma Group study (FSG) from the NETSARC database.
European journal of cancer (Oxford, England : 1990)[Vascular neoplasms of the liver].
Pathologie (Heidelberg, Germany)A case of cutaneous angiosarcoma with intradermal metastases responding to PD-1 inhibition-based immunotherapy.
JAAD case reportsImmunotherapy and Targeted Therapies in Sarcoma: Proposed Synergy with Combination Treatment.
Journal of immunotherapy and precision oncologyRare Metastases to Liver and Spleen form a Seldom Case of Facial Angiosarcoma Demonstrated on Staging FDG PET-CT.
Indian journal of nuclear medicine : IJNM : the official journal of the Society of Nuclear Medicine, IndiaSplit Facies with Destructive and Leonine Appearance: An Atypical Presentation of Angiosarcoma.
Indian dermatology online journalIntramuscular hematomas as the first presentation of angiosarcoma.
Polish archives of internal medicinePreclinical Investigations Toward Gd-free Molecularly Targeted Dual-Modal, MRI Dynamic (DCE-MRI)/Optical Imaging Contrast Agent for Cardiac Angiosarcoma.
Topics in magnetic resonance imaging : TMRIComparison of clinical features between patients with bone and soft tissue angiosarcomas.
Journal of orthopaedic science : official journal of the Japanese Orthopaedic AssociationOutcome of systemic therapy in patients with advanced rare skin cancers: A retrospective multicenter DeCOG study of 209 patients.
European journal of cancer (Oxford, England : 1990)Updating the genomic and clinicopathologic features of thoracic SMARCA4-deficient undifferentiated tumor: a mini-series including a long-term survivor.
Frontiers in oncologyCase Report: Hepatic infantile hemangioma malignantly transformed into hemangiosarcoma.
Frontiers in oncologyBrain Metastasis From Angiosarcoma of the Scalp: Report of Three Cases.
The Journal of dermatologyComparison of 68Ga-FAPI-04 and 18F-FDG in Primary Splenic Angiosarcoma.
Clinical nuclear medicineDiffuse Cutaneous Angiosarcoma Involving Scalp and Face on 18 F-FDG and 68 Ga-NODAGA-RGD PET/CT.
Clinical nuclear medicinePulmonary angiosarcoma in an HIV-positive patient presenting with hemoptysis and multisystem involvement: Report of a rare case.
Medicine internationalCardiac Angiosarcoma in a 17-Year-Old Female: A Rare Case Report and Literature Review.
CureusSecondary Angiosarcoma of the Thigh Arising From Lymphedema After Post-Operative Radiotherapy for Extramammary Paget's Disease: A Case Report.
The Journal of dermatologyCoexistence of a Rare Giant Right Ventricular Angiosarcoma with Right Coronary Artery Pseudoaneurysm and Unilateral Pleural Effusion: A Case Report.
RoFo : Fortschritte auf dem Gebiete der Rontgenstrahlen und der NuklearmedizinSplenic hamartoma mimicking angiosarcoma: A case report.
World journal of clinical casesPrimary Jejunal Angiosarcoma.
ACG case reports journalPrimary pulmonary artery sarcoma treated with simultaneous pulmonary valve replacement, artificial vessel replacement, and total right pneumonectomy: a case report.
General thoracic and cardiovascular surgery casesAssociações
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Referências e fontes
Bases de dados externas citadas neste artigo
Publicações científicas
Artigos indexados no PubMed ligados a esta doença no grafo RarasNet — título, periódico e PMID direto da fonte, sem intermediação de IA.
- Primary low-grade breast angiosarcoma initially misdiagnosed as a benign vascular lesion.
- Primary cerebellar angiosarcoma: A rare case of posterior fossa vascular tumor with hemorrhagic presentation and favorable surgical outcome.
- Hepatic Angiosarcoma Associated with Chronic Schistosomiasis in a Patient with Decompensated Cirrhosis: A Rare Case Report.
- Primary splenic angiosarcoma with diffuse intrasinusoidal hepatic metastasis mimicking lymphoma: a diagnostic challenge.
- Spinal epithelioid angiosarcoma: a diagnostically and therapeutically challenging entity treated with chemoradiotherapy.
- Case Report of Primary Splenic Angiosarcoma in a Young Patient: A Very Rare and Challenging Disease.
- Breast Angiosarcoma: 15-Years Experience.
- Liposomal Versus Conventional Doxorubicin as First-Line Therapy in Advanced Soft Tissue Sarcomas: Observational Multi-Institutional Cohort of 8.5-Year Experience.
- Surgical Management of Primary and Metastatic Cardiac Malignancies: A 20-Year Single-Center Experience.
- Diagnostic Pitfalls and Imaging-Pathologic Correlation in Benign Breast Vascular Lesions Mimicking Malignancy: A Case-Based Systematic Review.
Bases de dados e fontes oficiais
Identificadores e referências canônicas usadas para montar este verbete.
- ORPHA:263413(Orphanet)
- MONDO:0016982(MONDO)
- GARD:20900(GARD (NIH))
- Busca completa no PubMed(PubMed)
- Artigo Wikipedia(Wikipedia)
- Q2619091(Wikidata)
Dados compilados pelo RarasNet a partir de fontes abertas (Orphanet, OMIM, MONDO, PubMed/EuropePMC, ClinicalTrials.gov, DATASUS, PCDT/MS). Este conteúdo é informativo e não substitui avaliação médica.
Conteúdo mantido por Agente Raras · Médicos e pesquisadores podem colaborar
