A Dissecting Pulmonary Aneurysm Complicating Eisenmenger Syndrome.

Protocol for an open-label, randomised, controlled trial to evaluate the efficacy and safety of sotatercept add-on therapy compared with pulmonary vasodilator-based standard of care for pulmonary vasodilator-resistant pulmonary arterial hypertension associated with unrepaired congenital shunts (atrial septal defect, ventricular septal defect or patent ductus arteriosus), including Eisenmenger syndrome: the SuMILE trial.

Sotatercept in Patients With Eisenmenger Syndrome.

Unrepaired Truncus Arteriosus Type 1 With Eisenmenger Syndrome and Recurrent Embolic Strokes: An Adult Case Report.

Risk stratification for adult patients with pulmonary arterial hypertension associated with congenital heart disease. A scientific statement of the ESC Working Group on Pulmonary Circulation & Right Ventricular Function, the ESC Working Group on Adult Congenital Heart Disease, and the Association of Cardiovascular Nursing & Allied Professions of the ESC.

Treatment of Brain Abscess in Patient with Eisenmenger Syndrome.

Maternal and Perinatal Outcome in Women with Congenital Heart Disease: An Observational Study.

Heart-Lung transplantation: Meeting allocation challenges in France.

Lung Retransplantation after Heart-lung Transplantation: A Case Report.

Management of Acute Cholecystitis in a Patient With Eisenmenger Syndrome and Abdominal Heterotaxy: A Case Report.

Pneumonia or something more? Eisenmenger syndrome in a resource-limited setting.

[A Case of Bilateral Breast Mastectomy Performed under Local Anesthesia with Ultrasound Guided Nerve Blocks].

Extracorporeal membrane oxygenation for pulmonary arterial hypertension complicating pregnancy: case series and literature review.

Treat-and-Repair Strategy for Atrial Septal Defect with Eisenmenger Syndrome due to Pulmonary Arterial Hypertension: A Case Report.

Standardized mortality ratio in adults with congenital heart disease.

Influence of gestational history on neural tube defects and Eisenmenger syndrome: associations with intellectual disability and visual impairment in children and adults - a systematic review.

Dyslipidemia Patterns in Adults with Congenital Heart Disease: Focus on HDL Cholesterol.

Case Report: Concurrent atrial and ventricular septal defect in a young Sphynx cat.

Bridge to recovery: A case of V-V ECMO following V-A ECMO in Eisenmenger syndrome.

Acute Decompensated Heart Failure in a Woman With Eisenmenger Syndrome: A Case Report.

Long-term outcome of patients with Eisenmenger syndrome receiving pulmonary arterial hypertension-targeted therapy.

Predictive Insights From the 6-Minute Walk Test in the Eisenmenger Syndrome.

Atrial Septal Defects: From Embryology to Pediatric Pulmonary Hypertension.

Prevalence of Pulmonary Arterial Thrombosis in Adults With Eisenmenger Syndrome.

Secondary hyperparathyroidism in adult congenital heart disease: the CHD-HYPER-study.

Treatment options for children with pulmonary arterial hypertension associated with congenital heart disease.

Unrepaired Dextro-Transposition of the Great Arteries: Eisenmenger Syndrome with Giant Pulmonary Artery Aneurysm.

[Initial care and stabilization of ACHD patients : Teamwork improves outcomes].

Specific risk factors for heart-lung transplantation.

Long-term outcomes of Eisenmenger syndrome in the era of targeted pulmonary vasodilator therapy.

Pulmonary arterial compliance as a long-term prognostic indicator in pulmonary arterial hypertension associated with adult congenital heart disease: results from a National multicenter prospective registry.

A Rare Eisenmenger Syndrome Presentation in the Intensive Care.

Cardiopulmonary Exercise Testing in Congenital Heart Disease: A Never-Ending Story from Paediatrics to Adult Life.

Continuous spinal anesthesia in a case of Eisenmenger syndrome undergoing TURBT- A case report.

A Rare Case of Chronic Thromboembolic Pulmonary Hypertension in an Elderly With Atrial Septal Defect and Eisenmenger Syndrome.

Analysis of Clinical Characteristics of 54 Dead Pregnant Patients With Pulmonary Hypertension.

Critical Care of the Adult With Congenital Heart Disease.

Large Patent Ductus Arteriosus in an Adult With Severe Pulmonary Hypertension and Polycythemia: PDA With Severe Pulmonary Hypertension.

Pregnancy in patients with pulmonary hypertension: a systematic review and meta-analysis with meta-regression.

Fatal Congenital Heart Disease in a Postpartum Woman.

Refractory hypoxaemia in the presence of two common conditions: a case report.

Extended Use of Central Veno-Arterial Extracorporeal Membrane Oxygenation in Lung Transplantation for Patients with Pulmonary Arterial Hypertension.

A Giant Pulmonary Artery Aneurysm in a Young Male With Eisenmenger Syndrome.

Successful interventional closure of patent ductus arteriosus in three pediatric cases with congenital heart disease and severe pulmonary hypertension: a case series and literature review.

Active Surveillance of Papillary Thyroid Cancer-A Feasibility Experience from a Tertiary Care Centre.

Is transplantation an option for adult Eisenmenger syndrome?Is the grass on the other side of fence greener?

Maternal outcomes among pregnant women with shunt-related congenital heart disease-associated pulmonary hypertension: a retrospective study.

Perioperative Risk in Adults with Congenital Heart Disease Undergoing Non-Cardiac Surgery: Challenges and Tailored Strategies.

Common shunt lesions with pulmonary hypertension-who will benefit from surgery?

Group D of pulmonary arterial hypertension and its relationship to congenital heart disease: Is there a non-invasive way to predict the unpredictable?

Novel Use of MitraClip for Treatment of Severe Aortic Regurgitation.

Meta-analysis of targeted drugs for pulmonary hypertension to improve exercise tolerance and associated factors in eisenmenger syndrome.

Utilization of the flow ratio measured by echocardiography (FRecho) compared to the flow ratio by right heart catheterization (FRrhc) for detecting Eisenmenger syndrome in uncorrected acyanotic adult congenital heart disease (ACHD).

Interventional Management of a Rare Case of Complex Congenital Heart Disease in an Adult Patient: A Case Report.

Isolated Pulmonary Arterial Thrombosis in Patient with Eisenmenger Syndrome Treated with Catheter-directed Thrombolysis: A Case Report and Literature Review.

A 19-year-old male with truncus arteriosus type I: a rare case report from Syria.

Risk stratification in Eisenmenger syndrome.

High Altitude May Protect Against the Early Development of Irreversible Pulmonary Hypertension in Patients With Congenital Heart Disease.

Challenging Perioperative Management of a MEN2A Syndrome Patient Complicated by Eisenmenger Syndrome.

Massive Hemoptysis in a Patient With Eisenmenger Syndrome, Polysplenia and Transverse Liver.

Advances in Atrial Septal Defect Closure: Managing Pulmonary Hypertension and Expanding Treatment Criteria Applicability.

Replacement of the systemic tricuspid valve in a patient with corrected transposition of the great arteries, ventricular septal defect, and Eisenmenger syndrome.

[Adult congenital heart disease misdiagnosed as Eisenmenger syndrome: a case report].

Author Correction: Contemporary survival outcomes of congenital systemic-to-pulmonary shunt in children with borderline pulmonary vascular resistant index compared to Eisenmenger syndrome.

Aortopulmonary Window in Adult Patient Operated on With Echocardiography Assessment.

Safety, tolerability, and efficacy of an in-class combination therapy switch from bosentan plus sildenafil to ambrisentan plus tadalafil in children with pulmonary arterial hypertension.

Eisenmenger syndrome during pregnancy: A true anesthetic challenge.

Intraoperative Hemodynamic Instability in a Patient With Ebstein's Anomaly Complicated With Eisenmenger Syndrome.

Pulmonary arterial hypertension with left to right shunts: When to treat and/or close?

Update on Eisenmenger syndrome - Review of pathophysiology and recent progress in risk assessment and management.

Multimodality Evaluation of Turner Syndrome With Right Ventricular Dilation and Partial Anomalous Pulmonary Venous Return.

Survival prospects of pulmonary arterial hypertension associated with congenital heart disease: Insights from the HOPE registry.

Survival comparison in adults with congenital systemic to pulmonary shunt and borderline elevated pulmonary vascular resistance versus Eisenmenger syndrome.

Macitentan in Pulmonary Arterial Hypertension Due to Congenital Heart Disease (CHD-PAH): Real-World Evidence from the OPUS/OrPHeUS Studies.

Operative strategies and outcomes for patients with severe pulmonary artery hypertension and intestinal obstruction: case series from single institution-sharing lessons to improve surgical outcomes.

[Implantation of leadless pacemaker in complex congenital heart disease with Eisenmenger syndrome and high-degree atrioventricular block: a case report].

Case report: Eisenmenger syndrome in a dog with ventricular septal defect: long term management and complications.

Pulmonary hypertension in adults with congenital heart defects (ACHDs) in light of the 2022 ESC PAH guidelines-part II: supportive therapy, special situations (pregnancy, contraception, non-cardiac surgery), targeted pharmacotherapy, organ transplantation, special management (shunt lesion, left ventricular disease, univentricular hearts), interventions, intensive care, ACHD follow-up, future perspective.

Pulmonary hypertension in adults with congenital heart defects (ACHDs)-in light of the 2022 ESC PAH guidelines-part I: definition, epidemiology, classification, diagnostics, genetics, risk stratification and follow-up, gender aspects.

Biventricular longitudinal strain analysis using cardiovascular magnetic resonance feature-tracking: Prognostic value in Eisenmenger syndrome.

Evaluation of Outcomes of Pregnancy in Women with Eisenmenger Syndrome: Is There Any Prognostic Criterion?

Bronchial Atresia with Eisenmenger Syndrome in a Complex Congenital Heart Disease-A Rare Coexistence: A Case Report.

Unexpected Origins: A Case Report of Escherichia coli-Linked Cerebral Abscess in an Adult.

Swyer-James-MacLeod Syndrome in a Patient with Eisenmenger Syndrome.

Cutting the Gordian knot of diuretic resistance using continuous ultrafiltration in a Holt-Oram patient with decompensated heart failure and Eisenmenger syndrome: a case report.

Eisenmenger Syndrome Combined with Pulmonary Artery Aneurysm and Dissection.

Erythrocytosis in congenital heart defects: hints for diagnosis and therapy from a clinical case.

Giant right pulmonary artery aneurysm in Eisenmenger syndrome.

Septal Defects: Unveiling Sex-Based Disparities and Screening Challenges for Timely Intervention Through a Case Report and Systematic Literature Review.

Pseudo-subarachnoid haemorrhage: An unusual presentation of hyperviscosity syndrome.

Contemporary survival outcomes of congenital systemic-to-pulmonary shunt in children with borderline pulmonary vascular resistant index compared to Eisenmenger syndrome.

Eisenmenger syndrome complicated by the presence of an aneurysm of the pulmonary trunk and compression of the left main coronary artery.

Atrial Septal Defect (ASD) Repair Unveiling an Unusual Conduction Conundrum: A Wenckebach Case Report.

Perioperative Management of an Obstetric Patient with Eisenmenger Syndrome and Pre-Eclampsia Using Milrinone.

Right ventricular fibrosis in adults with uncorrected secundum atrial septal defect and pulmonary hypertension: a cardiovascular magnetic resonance study with late gadolinium enhancement, native T1 and extracellular volume.

Successful Cardiac Surgical Management in a Trisomy 21 Child After Long-Term Hospitalization Associated With Bronchopneumonia and Hepatitis C Virus Seropositivity: A Case Report.

How severity and classification of pulmonary hypertension affect pregnancy outcomes: a systematic review and timeline.

Survival and outcomes of isolated neonatal ventricular septal defects: A population-based study from a middle-income country.

Complex Cardiovascular Morbidities in Prader-Willi Syndrome: A Multidisciplinary Approach.

Development and Validation of a Nomogram of Persistent Pulmonary Hypertension in Adult Pretricuspid Shunts After Correction.

The Anesthetic Complexity of Eisenmenger Syndrome: A Clinical Case.

Medical Therapy and Monitoring in Adult Congenital Heart Disease Heart Failure.

Cyanotic Nephropathy in an Adult Patient with Eisenmenger Syndrome: A Case Report and Literature Review.

Successful intraoperative management of laparoscopic hysterectomy in a patient with Eisenmenger syndrome: a case report.

Management of Unrepaired Tetralogy of Fallot in an 86-Year-Old Patient Undergoing Transcatheter Aortic Valve Replacement.

Acquired Cardiovascular Diseases in Patients with Pulmonary Hypertension Due to Congenital Heart Disease: A Case Report.

The Unrepaired Tetralogy of Fallot: A Tale of Delayed Presentation and Limited Access to Care.

Application of a modified clinical classification for pulmonary arterial hypertension associated with congenital heart disease in children: emphasis on atrial septal defects and transposition of the great arteries. An analysis from the TOPP registry.

Remimazolam in perioperative management of Eisenmenger syndrome: a case report.

Noncardiac surgery in Eisenmenger syndrome.

Thirty years of surgical management of pediatric pulmonary hypertension: Mid-term outcomes following reverse Potts shunt and transplantation.

A case of atrial septal defect with right-to-left shunting without pulmonary hypertension.

Prognosis factors in heart-lung transplantation: 30 years experience in a reference center.

Triple vasodilator therapy in pulmonary arterial hypertension associated with congenital heart disease.

Clinical features and pregnancy outcomes in women with aortopulmonary window defect: case series.

Intravascular Ultrasound-Guided Stent Implantation in the Left Main Coronary Artery Extrinsic Compression by Pulmonary Artery Aneurysm Due to Eisenmenger Syndrome.

Eisenmenger Syndrome: A Revisit of a Hidden but Catastrophic Disease.

Evaluating the role of serum uric acid in the risk stratification and therapeutic response of patients with pulmonary arterial hypertension associated with congenital heart disease (PAH-CHD).

Metabolomics in Pulmonary Hypertension-A Useful Tool to Provide Insights into the Dark Side of a Tricky Pathology.

Outcomes of pregnancy in women with different types of pulmonary hypertension.

Pseudoaneurysm after aortopulmonary window repair and bilateral lung transplantation for eisenmenger syndrome: a case report.

One-minute sit-to-stand test in patients with pulmonary arterial hypertension associated with congenital heart disease: A single-center prospective study.

Pulmonary vascular disease as a complication of pediatric congenital heart diseases.

Heart-lung transplantation in Eisenmenger syndrome with pulmonary embolisms.

Risk Assessment Tool Implementation in Congenital Heart Disease-Associated Pulmonary Arterial Hypertension.

Fatal Association of Eisenmenger Syndrome and Severe Preeclampsia.

De novo progressive dural arteriovenous fistula with putamen hemorrhage associated with long-term Down syndrome: A case report and literature review.

Eisenmenger syndrome combined with pulmonary artery dissecting aneurysm.

Management and outcomes of pulmonary artery hypertension and Eisenmenger syndrome during pregnancy: a prospective observational cohort study.

Atrial fibrillation ablation in a single atrium with inferior vena cava interruption.

Characteristics, treatments and survival of pulmonary arterial hypertension associated with congenital heart disease in China: Insights from a national multicenter prospective registry.

Common congenital heart problems in acute and intensive care.

Advanced heart failure in adult congenital heart disease: the role of renal dysfunction in management and outcomes.

Outcome of Down patients with repaired versus unrepaired atrioventricular septal defect.

Impact of current targeted drug therapy on the prognosis of Eisenmenger syndrome: A large-scale retrospective analysis.

Successful delivery in a woman with ventricular septal defect complicated with Eisenmenger syndrome: case report.

An Unusual Presentation of Eisenmenger Syndrome in a Middle-Aged Woman Without Known Cardiac History.

Univentricular hearts not undergoing Fontan: the type of palliation matters.

A Caseating Tricuspid Mass in an Adult With Eisenmenger Syndrome Secondary to Aorto-Pulmonary Window.

Congenital unilateral absence of right pulmonary artery with VSD and wide aortopulmonary window in an adult patient: a case report.

Successful Eisenmenger syndrome-targeted drug therapy in pregnant women: a case series and literature review.

[Nacimiento anómalo de arteria pulmonar derecha en un paciente joven con síndrome de eisenmenger].

Case report: Thoughts on two cases of total anomalous pulmonary venous connection complicated with pulmonary artery hypertension.

Cyanotic Congenital Heart Disease in Pregnancy: A Review of Pathophysiology and Management.

Outcomes of heart-lung transplantation in Eisenmenger syndrome compared to primary pulmonary hypertension.

Multidisciplinary approach for the management of term pregnancy complicated by Eisenmenger syndrome.

Pregnancy in Eisenmenger syndrome: a case series from a tertiary care hospital of Northern India.

Characteristics of exercise intolerance in different subgroups of pulmonary arterial hypertension associated with congenital heart disease.

Novel Hybrid Treatment for Pulmonary Arterial Hypertension with or without Eisenmenger Syndrome: Double Lung Transplantation with Simultaneous Endovascular or Classic Surgical Closure of the Patent Ductus Arteriosus (PDA).

Pregnancy outcomes of women with Eisenmenger syndrome: A single-center study.

Undiagnosed ventricular septal defect with resultant Eisenmenger syndrome presenting with diplopia.

Survival of patients with congenital ventricular septal defect.

Partial anomalous pulmonary venous return in adults: Insight into pulmonary hypertension.

Detection and evaluation of myocardial fibrosis in Eisenmenger syndrome using cardiovascular magnetic resonance late gadolinium enhancement and T1 mapping.

Long-term course of pulmonary arterial hypertension in adults with congenital heart disease under targeted therapy: a retrospective analysis of a single tertiary center.

Evolving Indications for Heart-Lung Transplant in Spain.

[Evidence base for specific pulmonary vasodilators in adults with congenital heart disease].

Leadless pacemaker implantation in Eisenmenger syndrome.

Risk of pulmonary artery dissection in adults with congenital heart disease.

Monitored anesthesia care for craniotomy in a patient with Eisenmenger syndrome: A case report.

Targeted Therapies in Patients with Pulmonary Arterial Hypertension Due to Congenital Heart Disease.

Cerebral abscess as a neurosurgical emergency in Eisenmenger syndrome: illustrative case.

Successful Control of Heavy Menstrual Bleeding Using High-Intensity Focused Ultrasound Ablation of Fibroid Uterus in a Woman With Eisenmenger Syndrome.

Long-Term Study on Therapeutic Strategy for Treatment of Eisenmenger Syndrome Patients: A Case Series Study.

Status of adult outpatients with congenital heart disease in Japan: The Japanese Network of Cardiovascular Departments for Adult Congenital Heart Disease Registry.

Successful Bronchial Artery Embolization after Stabilization with Nitric Oxide for the Treatment of Haemoptysis in a Patient with Eisenmenger Syndrome.

Case Report: Artifactual Hypoglycemia: A Condition That Should Not Be Forgotten.

Transcatheter closure of secundum atrial septal defect using Cocoon septal occluder: immediate and long-term results.

Thrombosis of aneurysmal pulmonary arteries in patent ductus arteriosus with Eisenmenger syndrome.

Late presentation of aortopulmonary window: a contemporary series.

Eisenmenger Syndrome in Case of Extended Goldenhar Complex Treated With Heart-Lung Transplantation.

A case series describing the multidisciplinary management of pulmonary arterial hypertension in pregnancy: Time for optimism.

Challenges in managing a critically ill patient with decompensated Eisenmenger syndrome.

Long-Term Survival of Adult Patients With Atrial Septal Defect With Regards to Defect Closure and Pulmonary Hypertension.

Successful bronchial artery embolization in a patient with Eisenmenger syndrome and recurrent haemoptysis.

Eisenmenger Syndrome Among Children with Unrepaired Congenital Heart Defects in Yunnan, China.

Maternal and fetal outcomes of pregnant women with pulmonary arterial hypertension associated with congenital heart disease in Beijing, China: A retrospective study.

Spontaneous hyphema from iris microhemangioma in Eisenmenger syndrome.

Inferior sinus venosus defect and anomalous hepatic venous return to the coronary sinus leading to an Eisenmenger syndrome.

Pregnancy in Congenital Heart Disease, Complicated by Pulmonary Arterial Hypertension-A Challenging Issue for the Pregnant Woman, the Foetus, and Healthcare Professionals.

Evaluation of Liver Stiffness After Atrial Septal Defect Closure.

Pheochromocytoma and multiple paragangliomas associated with Eisenmenger syndrome: An autopsy case.

Transcatheter leadless permanent pacemaker in complex congenital heart disease with interrupted inferior vena cava: A challenging implantation.

Role of high-flow nasal oxygen therapy in COVID-19 pneumonia with Eisenmenger syndrome: A case report.

A Case of Multifocal Extramedullary and Non-Hepatosplenic Extramedullary Hematopoiesis in a 43-Year-Old Man with a History of Congenital Eisenmenger Syndrome.

Eisenmenger Syndrome: JACC State-of-the-Art Review.

Pulmonary Hypertension in Adult Congenital Heart Disease in Asia: A Distinctive Feature of Complex Congenital Heart Disease.

Eisenmenger syndrome with left main compression syndrome: a case report.

Central retinal artery occlusion with cilioretinal sparing in a patient with Eisenmenger syndrome.

Anaesthetic management in neurosurgery in a patient with Eisenmenger syndrome and Down syndrome. A case report.

Haemoptysis in Pulmonary Arterial Hypertension Associated with Congenital Heart Disease: Insights on Pathophysiology, Diagnosis and Management.

Fruitful Pregnancy Outcome in a Case of Eisenmenger Syndrome With Severe Pulmonary Hypertension: A Rare Case Report.

Catheter Ablation of Atrioventricular Nodal Reentrant Tachycardia in Patients With Congenital Heart Disease.

Medical treatment of pulmonary hypertension in adults with congenital heart disease: updated and extended results from the International COMPERA-CHD Registry.

Exercise ventilatory reserve predicts survival in adult congenital heart disease associated pulmonary arterial hypertension with Eisenmenger physiology.

Current Situation and Prognostic Evolution of Combined Heart-lung Transplantation in a European Union Country.

The use of pulmonary arterial hypertension therapies in Eisenmenger syndrome.

Venovenous Extracorporeal Membrane Oxygenation During Bilateral Lung Transplantation for a Patient With Eisenmenger Syndrome Complicated With Giant Pulmonary Artery Aneurysm, Azygos Continuation, and Central Airway Obstruction.

Angiography-guided mid/high septal implantation of ventricular leads in patients with congenital heart disease.

Effect of oxygen therapy on exercise performance in patients with cyanotic congenital heart disease: Randomized-controlled trial.